He aha te mate MRKH (Mate Mayer-Rokitansky-Küster-Hauser)? Me kōrero tāua mō tēnei?

Kāore anō kia tīmata te paheketanga o tāu tamāhine, o tētahi tamaiti iti rānei e mōhio ana koe, i te tere e tika ana mō tōna tau? He mamae, he koretake rānei ia i ētahi wā ina ngana ana ki te moe tāne? I tēnei rā ka kōrero tātou mō tētahi āhuatanga hauora motuhake ka puta ai ēnei āhuatanga, engari kāore i te tino noa, ā, kāore i te maha ngā tāngata kua rongo mōna. Ko te ingoa o tēnei ko te Meyer-Rokitansky-Küster-Hauser syndrome , ko te "MRKH syndrome" rānei hei whakarāpopototanga. Ahakoa he roa te ingoa, he āhuatanga ira onge tēnei e pā ana ki ngā wāhine. Me kōrero noa iho, i roto i tētahi huarahi e mārama ai koe.

He aha tonu te mate MRKH?

Ki te whakarāpopototanga, ko te mate MRKH he āhuatanga e kore ai e tika te whanaketanga o te tara me te kōpū o te wahine, kāore rānei i tino hangaia i te whānautanga. Whakaarohia he rite ki tētahi whare e hangaia ana, kāore ētahi rūma i tika te hanganga. Heoi, i te nuinga o te wā, ka mahi noa ngā ovaries me ngā fallopian tubes o te hunga whai mate pēnei . Waihoki, he mea noa ngā ira tangata o waho, arā, te wāhanga o raro o te tara, te whakatuwheratanga tara, te labia, te clitoris, me te tupu o ngā huruhuru i te taha. Kāore te urethra e pāngia, nō reira kāore he raruraru ki te mimi.

Heoi, i roto i ētahi momo mate MRKH, tera pea ētahi raruraru whanaketanga i roto i ētahi atu okana, pērā i ngā whatukuhu me te tuaiwi.

I te nuinga o te wā, ka kitea tēnei mate i te wā taitamariki, arā, i te 15-16 tau te pakeke, i te wā kāore anō kia tīmata te paheketanga. Nā te mea kāore anō kia tino whanake te kōpū, nō reira kāore e puta te paheketanga. I ētahi wā, i te wā e ngana ana ki te moe tāne, ka mamae, ka uaua rānei te tara nā te mea he poto, he whaiti hoki.

Nā te mea kāore anō kia tino whanake te kōpū, kāore rānei i reira, kāore e taea te hapu me te whānau i te tamaiti me te kore he āwhina hauora i roto i tēnei āhuatanga. Heoi, ki te mahi ngā ovaries, ā, kei te puta ngā hua manu , ka taea te whakaaro ki ngā kōwhiringa pēnei i te "IVF - te whakatōnga in vitro" me te "surrogacy". Ki te mea kei te tumanako koe ki te whānau tamariki, he mea tino nui kia kōrero koe ki tō tākuta mō tēnei mea. Kātahi ka taea e rātou te tohutohu i a koe mō ngā kōwhiringa e tika ana māu.

He maha atu anō ngā ingoa e whakamahia ana mō te `(MRKH syndrome)`:

• Te ngaro o te kōpū me te tara i te whānautanga (CAUV)
• Te whakaputa uri o te tara
• Agenesis Müllerian
• Te āputa o Mullerian (MA)
• Te mate taringa whatukuhu ira tangata (GRES)

He momo mate MRKH anō kei reira?

Āe, e rua ngā momo matua o te `(MRKH syndrome)`:

• Momo 1:I tēnei momo, ka mahi noa ngā ovaries me ngā fallopian tubes, engari kua āraia, kua kore rānei e tū te wāhanga o runga o te tenetene, te cervix, me te kōpū. Heoi, kāore tēnei e pā ki ētahi atu okana o te tinana.

• Momo 2: I tēnei momo, haunga te aukati, te kore rānei e tū tika ana te wāhanga o runga o te tenetene, te kaki o te kōpū, me te kōpū, tera pea ētahi raruraru ki ngā ngongo fallopian, ngā ovaries, te tuaiwi, ngā whatukuhu, me ētahi atu whekau rānei.

E hia te auau o tēnei āhuatanga?

He tino onge te mate MRKH. Kotahi anake i roto i te 4,500 ngā kōtiro ka pāngia. Nō reira, ehara i te mea miharo kāore anō kia nui ngā kōrero mōna.

He aha ngā tohu o te MRKH?

Ka rerekē pea ngā tohu o te mate MRKH i runga i te momo kei a koe.

I te nuinga o te wā, ko te tohu matua ko te korenga o te paheketanga (amenorrhea) i te 16 tau te pakeke. He tohu tēnei kāore anō kia whanake tika te kōpū, te tara rānei. Heoi, nā te mea kei te mahi noa ngā ovaries, ka puta pea ētahi atu tohu e pā ana ki te paheketanga, pērā i te pupuhi me te hurihanga o te wairua, ahakoa kāore he toto.

Nā te mea he chromosomes wahine me ngā homoni kei a koe, ka pāngia koe e te whanaketanga ā-ira tangata noa, pērā i te whanaketanga o te ū me te tupu o te huruhuru i roto i ngā kēkē me te wāhi ira tangata. Heoi, ka pāngia pea koe e te mamae, te kore rānei e pai i te wā tuatahi ka ngana koe ki te moe tāne. Nā te mea he angiangi ake, he whaiti ake, he poto ake hoki tō tenetene i te mea noa.

Mena kei a koe te Momo 2 MRKH, tera pea ka pāngia koe e ētahi atu tohu pēnei i:

• Ngā raruraru o te whatukuhu, te ngoikore rānei o tētahi, o ngā whatukuhu e rua rānei.
• Ngā raruraru ki ngā tuaiwi o te tuaiwi, ki ētahi atu āhua rerekē rānei o te pūnaha angaiwi.
• Te ngoikore o te whakarongo.
• Ko ētahi raruraru o te ngākau.

He aha te take o te MRKH?

Kāore anō kia mōhiotia e ngā kairangahau te tino take o te mate MRKH. Heoi, e mōhio ana rātou he raruraru kei roto i ngā ira me ngā chromosomes. Heoi, kāore anō kia taea e rātou te whakatau ko tētahi ira motuhake te take. Ko te mea nui , ehara i te mea i mahia, i kore rānei i mahia e te whaea i te wā e hapu ana . Nō reira kaua e manukanuka.

Ka tīmata te whanaketanga o te pūnaha whakaputa uri o te wahine i ngā wiki tuatahi o te hapūtanga. Ko ngā ngongo fallopian, te kōpū, te cervix, me te taha o runga o te tara i hangaia mai i tētahi mea e kiia nei ko ngā awa Müllerian . Mō te hunga whai mate MRKH, kāore ēnei awa Müllerian e tino whanake. Kāore anō kia mōhiotia he aha tēnei e tupu ai i roto i ētahi tāngata. Heoi, nā te mea ka whanake motuhake ngā ovaries mai i te toenga o te pūnaha whakaputa uri, kāore ngā ovaries e pāngia.

Me pēhea koe e mōhio ai mēnā kei a koe te MRKH?

He maha ngā wā ka tātaritatia e ngā tākuta te mate MRKH ina kore te paheketanga o tētahi kōtiro e puta tuatahi.

Ko te taahiraa tuatahi ki te tautuhi i tēnei mate ko te whakamātautau tinana . Ka whakaurua e tō tākuta he maihao karapu ki roto i tō tara, ka ine i tōna hohonutanga me tōna whānui. Ka taea e tēnei whakamātautau te kite i te MRKH nā te mea kua poto te tara. Kātahi ka tonoa pea koe ki te mahi i ngā whakamātautau whakaahua, pērā i te matawai ultrasound, i te matawai MRI rānei, kia kite ai mēnā kei te pāngia tō kōpū, ngā ngongo fallopian, ngā whatukuhu, me ētahi atu okana rānei. I ētahi wā, ka mahia pea ngā whakamātautau toto hei tirotiro i ō taumata homoni.

He aha ngā maimoatanga mō te MRKH?

He rerekē te maimoatanga mō te mate MRKH i runga i ō whāinga me ō tohu. He maimoatanga pokanga me ngā maimoatanga kore-pokanga. Ko ētahi o ēnei ko te vaginoplasty, te whakawhānui i te tara, me te whakawhitinga kōpū.

Te whakawhānui o te tara

Ko tētahi huarahi e whakamahia ana e ngā tākuta hei totoro i te tara ko ngā taputapu e kiia nei ko ngā whakawhanui tara . He mea hanga ēnei ki te kirihou, ki te silicone rānei, ā, he rerekē te roa me te whānui. Ka āwhina ēnei taputapu rite ki te ngongo ki te whakawhānui me te totoro i te tara mai i roto. Ma tō tākuta koe e whakamārama te huarahi pai ki te whakamahi i te whakawhanui tara mō tō āhuatanga.

Vaginoplasty (te hanga anō i te tara mā te pokanga)

He pokanga te Vaginoplasty hei hanga i tētahi tara . He maha ngā huarahi a ngā taote pokanga ki te mahi i tēnei mahi. I te nuinga o te wā, ka hangaia he kōhao ka hipokina ki te kiko i tangohia mai i tētahi atu wāhanga o tō tinana. Mā tēnei ka taea e koe te moe tāne noa.

Te whakawhitinga kōpū

Mā te whakawhitinga kōpū ka taea e te wahine whai mate MRKH te whai wāhi ki te whānau tamariki. He mahi nui tēnei. Kei roto ko te whakawhitinga i tētahi kōpū mai i tētahi kaituku ki tētahi wahine kāore anō kia whai. Mā tēnei ka taea e te hunga whai mate MRKH te whānau me te whānau i tā rātou ake tamaiti. Kāore anō kia whānuitia te mahi whakawhitinga kōpū i ngā wāhi katoa o te ao, engari he maimoatanga tino angitu pea ā muri ake nei.

Ka taea te ārai i tēnei āhuatanga?

Kāo, kāore he huarahi hei ārai i te mate MRKH . Ka pā pea tēnei ki te hunga kāore anō kia pāngia e tēnei mate i mua, he ira tuku iho rānei. E ai ki te kōrero i mua ake nei, ehara i te mea nā te ira kotahi anake i puta ai.

Ka taea e te hunga whai MRKH te whānau tamariki?

Ae, ka taea e te hunga whai `(MRKH syndrome)` te whānau tamariki!Mena kei te mahi ō ovaries, ka taea te whakakotahi i ō hua manu me te parāoa, ka whakamomonatia mā te whakamahi i te whakamomona in vitro (IVF). Kātahi ka whakawhitia te kukune ki tētahi whaea hāpu/whānau whakakapi . Ko te tikanga tēnei ka whānau he tamaiti me ō ake ira, e tipu ana i roto i te kōpū o tētahi atu wahine hauora.

He aha atu ngā raruraru hauora ka puta mai i te MRKH?

Kua kōrerohia e tātou i mua ko te hunga whai "Momo 2" MRKH ka pāngia e ngā raruraru ki ētahi atu okana, pērā i ngā whatukuhu, te tuaiwi, te ngākau rānei. Hei tāpiri, ko ētahi atu raruraru hauora e kitea whānuitia ana i roto i te hunga whai "Momo 2" MRKH ko:

• Ngā raruraru e pā ana ki ngā vertebrae o te tuaiwi.
• Te korokoro.
• Ngā āhua hē o te whatukuhu, pērā i te honoa o ngā whatukuhu, te ngaro rānei o tētahi, o ngā whatukuhu e rua rānei (renal agenesis).
• Te pikinga ake o te mōrearea o ngā kohatu tākihi, ngā mate mimi, me te aukati i te ara mimi.
• Te ngoikore o te whakarongo.
• Mate ngakau.

He mea noa ngā raruraru o te pūnaha whakaputa uri i roto i te hunga whai MRKH. Haunga te kore e taea te hapu, te whānau rānei i tā rātou ake tamaiti, ka taea hoki e te hunga kāore i te tino whanake te kōpū te whakawhanake i ngā āhuatanga pēnei i te endometriosis.

Ahakoa ēnei āhuatanga katoa, he mea noa te pāngia e te ahotea kare ā-roto . Tērā pea ka tūtohu tō tākuta kia uru atu koe ki tētahi rōpū tautoko, kia rapu rānei i tētahi ratonga tohutohu hinengaro, pērā i te rongoā hinengaro-whanonga (CBT), hei āwhina i a koe ki te whakatau i te āhuatanga. He tino āwhina ēnei mea.

Kāore he mea miharo ko te mōhio kei a koe te mate Mayer-Rokitansky-Küster-Hauser (MRKH) he tino ohorere. Mena i whānau mai koe me te kōpū, te tara rānei kāore i tino whanake, kāore pea koe e mōhio tae noa ki te tamarikitanga, ā, kua tīmata noa te paheketanga. Ahakoa ehara i te mate morearea, ka taea e ia te whakararu i te ahotea nui, te pā ki te kaha o te wahine ki te hapu me te moe tāne. I ētahi wā, ka pā ki ētahi atu okana, ā, ka piki ake te mōrearea o ētahi mate hauora.

Ngā mea tino nui hei maumahara (Karere hei kawe ki te kāinga)

Āe, kua mārama ake koe ināianei ki tā tātou i kōrero ai, arā, te "syndrome MRKH". Ko te mea nui kia maumahara koe, ehara i te mea ko koe anake . He tāngata anō kei te ao e noho tahi ana me ēnei mate.

• Mena kei a koe ēnei tohu, he mea nui kia toro atu koe ki tētahi tākuta pai, kia tika ai te tautuhi i te mate .
• He maimoatanga kei te wātea. Kōrero ki tō tākuta, ā, whiriwhiria te maimoatanga e pai ana mōu.
• Kaua e mutu te tumanako mō ngā tamariki. Mā ngā hangarau pēnei i te `(IVF)` me te `(surrogacy)`, kei reira ngā huarahi hei whakatutuki i taua moemoeā.
• Kia tiakina hoki tō hauora hinengaro.Ki te mea e tika ana, rapua he tohutohu, ā, uru atu ki ngā rōpū tautoko me te hunga kua pāngia e ngā wheako rite. Mā tēnei ka nui te kaha e hoatu ki a koe.
• Ehara tēnei i tōu he. He āhuatanga tūturu tēnei ka pā ki te tangata katoa.

Mā tō tākuta, me tētahi rōpū tohunga pea, koe e tautoko me te ārahi hei āwhina i a koe ki te anga whakamua me tēnei `(MRKH syndrome)`. Whakawhirinaki ki a rātou. Mena he pātai anō āu mō tēnei, kaua e wehi ki te pātai atu. Kia ora!

Te mate MRKH, te mate Mayer-Rokitansky-Küster-Hauser, te mate tara, te mate kōpū, te hauora o ngā wāhine, te hauora uri, te korenga o te hapūtanga