Ka taea e ngā pukupuku te puta ki ō io? Me kōrero tātou mō ngā pukupuku o te takotoranga io i roto i ngā kupu māmā noa iho!

He rite ngā io e rere ana puta noa i ō tātou tinana ki tētahi whatunga waea e kawe ana i ngā karere hiko. Koinei ngā mea e kawe ana i ngā kōrero mai i te roro ki te toenga o te tinana, mai i te tinana ki te roro. Whakaarohia ko ēnei pūtau io, ko ō rātou tautau, kua takaihia katoatia ki ngā kiriuhi tiaki motuhake, pērā i te takotoranga kirihou e karapoti ana i tētahi waea, hei tiaki i a rātou, hei āwhina hoki i te tere haere o ngā tohu hiko. I roto i ēnei kiriuhi tiaki ka puta ake ai ēnei pukupuku e kiia nei ko te takotoranga io.

He aha ngā pukupuku o te pūkahu io?

He whakarāpopototanga, ka puta ēnei pukupuku i roto i ngā "pūkahukahu" tiaki e karapoti ana i ō tātou io. He maha ngā paparanga o tēnei "pūkahukahu" e hipokina ana:

• Ngā pūtau Schwann: Koinei ngā pūtau e takai ana i te axon, te wāhanga roa o te pūtau io, he rite ki te whakamarumaru e takai ana i te waea.
• Endoneurium: Koinei te kiko honohono e karapoti ana i ia muka io, he rite tonu ki te takotoranga e karapoti ana i tētahi waea parahi kotahi i roto i te waea.
• Perineurium: Koinei te mea e karapoti ana i ngā paihere muka io.

E rua ngā wāhanga o tō tātou pūnaha io:

• Pūnaha io matua: Kei roto i tēnei ko tō tātou roro me te taurakira.
• Pūnaha io taha: Koinei te whatunga io e toro atu ana i te roro me te taurakira ki ngā wāhanga katoa o te tinana.

I te nuinga o te wā, ka puta ēnei neurofibromas i roto i te pūnaha io ā-taha .

He aha ngā momo nati kei reira?

He maha ngā momo matua o ngā neuromas. Me titiro tātou ki ērā momo.

Schwannomas

Ka puta ēnei pukupuku i roto i ngā pūtau Schwann i whakahuatia ake nei. Tata ki te 60% o ngā schwannomas ka puta i roto i te io vestibular i roto i tō tātou taringa o roto . Ka āwhina tēnei io i tō tātou tinana ki te pupuri i te taurite. Ka puta pea ētahi atu schwannomas i raro i tō tātou kiri, i roto rānei i ngā kiko me ngā okana o te tinana. Ko ngā wāhi e kitea whānuitia ana ēnei pukupuku ko:

• I roto i ngā ringa me ngā waewae
• I roto i te upoko
• I roto i te tinana (arā, te rohe i waenganui i ngā pakihiwi me ngā hope)

Ko ngā Schwannoma he momo pukupuku e kapi ana i tētahi paparanga kiko angiangi, e kiia ana he "kāpia". Ko ēnei pukupuku he kore-matepukupuku (pai). Heoi, he tino onge, ka taea e tētahi pukupuku roa te huri hei matepukupuku (kino).

Ngā neurofibromas

Kei roto i tēnei momo pukupuku ētahi momo kiko e kīia nei ko ngā pūtau Schwann, te endoneurium, me te perineurium e kapi ana i ngā io. He maha ngā wā ka puta mai ēnei hei puku i raro i te kiri, engari i ētahi wā ka puta ake i runga i ngā io i roto rawa i te tinana.

Kāore ngā neurofibromas i te rite ki ngā schwannomas, engari he rerekē ki ngā neurofibromas e kapi ana i ngā pūtau. Ka tipu i roto i ngā paihere io. Ko ngā neurofibromas Plexiform he momo pukupuku e horapa ana pērā i te mata, e karapoti ana i ngā paihere io maha, ā, ka horapa ki roto i ngā kiko e karapoti ana.

Ehara te nuinga o ngā neurofibromas i te mate pukupuku. Heoi, tata ki te 5% ki te 10% o ēnei pukupuku ka taea te huri hei mate pukupuku . Ka kiia ēnei he pukupuku pukupuku pukupuku io taha kino (MPNST) . Tata ki te haurua o te hunga whai pukupuku pukupuku kino kua horapa kē ki ētahi atu wāhanga o te tinana i te wā e kitea ai te mate.

He pēhea te noa o tēnei hua?

He tino onge ngā pukupuku o te pukupuku io kāore i te matepukupuku.

• Ko te nuinga o te wā ka kitea ngā Schwannoma i roto i te hunga i waenga i te 50 me te 60 tau te pakeke.
• Ko te nuinga o te wā ka puta ngā neurofibromas i roto i te hunga i waenga i te 20 me te 40 tau te pakeke.
• Ko ngā neurofibromas plexiform ka puta i mua i te 5 tau te pakeke.

He momo mate pukupuku tino onge ngā pukupuku kino o te pūkahu io taha , e pāngia ana e te kotahi i roto i te 10 miriona tāngata i ia tau.

He aha i pēnei ai te āhua o ngā pukupuku? He aha ngā take?

He pānga nui tō ngā huringa ira ki te whanaketanga o ēnei neurofibromas.

• E pā ana te whanaketanga o Schwannomas ki ngā huringa o te ira e kiia nei ko te NF2.
• E hono ana ngā neurofibromas ki tētahi ira e kiia nei ko (NF1).

I te nuinga o te wā, ka puta noa ēnei huringa ira, kāore he take e kitea ana . Heoi, he iti noa ngā schwannomas me ngā neurofibromas e puta mai ana i tētahi mate ira onge e kiia nei ko te neurofibromatosis , ka taea te whakaputa i roto i ngā whānau.

Ngā momo Neurofibromatosis

E toru ngā momo matua o tēnei mate:

• Neurofibromatosis momo 1 (NF1): He nui ngā neurofibromas ka pāngia e te hunga whai NF1. He nui ake hoki te mōrearea o te whakawhanake i ngā plexiform neuromas me ngā pukupuku pukupuku io peripheral malignant (MPNST). Ko ētahi atu āhuatanga e kitea ana i roto i te hunga whai NF1 ko te macrocephaly , te scoliosis, me ngā ngoikoretanga ako .

• Neurofibromatosis momo 2 (NF2):Tata ki te katoa e pāngia ana e te NF2 ka pāngia e te vestibular schwannomas i ngā taringa e rua i mua i te 30 tau te pakeke. Hei tāpiri, ka taea hoki e ētahi atu momo schwannomas me ngā pukupuku te pāngia e te kiri, ngā kanohi, me te pūnaha io matua.

• Schwannomatosis: I tēnei āhua, ka puta he maha ngā schwannoma i roto i te io vestibular (i ngā taringa e rua) kaua i roto i te io vestibular.

He aha ngā tohu o ēnei pukupuku?

Ko te nuinga o te hunga whai pukupuku neuromastoid kāore e pāngia e te mamae, e ētahi atu tohu rānei . Heoi, ki te nui haere te pukupuku, ki te pēhi rānei i te io, ka puta ngā tohu pēnei i:

• He puku, he pukupuku rānei i raro i te kiri (tērā pea ka mamae ina pēhia).
• Te ngoikore o te uaua .
• Te ngoikore .
• Ngā mamae, ngā ngau kino, ngā mamae koi rānei .
• He kare ā-whatu, me te mea e pāngia ana e te hiko .

I runga anō i te wāhi o te puku, ka puta pea ētahi atu tohu motuhake. Anei ētahi tauira:

• Puku io sciatic: Mamae e haere ana mai i te tuara ki raro i te waewae (sciatica).
• He pukupuku i te ringaringa: He rite ngā tohu ki ērā o te Carpal Tunnel Syndrome.
• Puku io vestibular: Te ngaronga o te rongo, te tinnitus, ngā raruraru taurite.

I te nuinga o te wā, mēnā he neurofibromatosis te mate o te tangata, he kotahi noa te pukupuku. Heoi, i roto i te hunga whai neurofibromatosis kua whakahuatia ake nei, ka kitea ngā pukupuku maha (he maha ngā wā kei runga i te kiri).

Me pēhea koe e mōhio ai kei a koe ēnei nati?

Ka tirohia tō tinana e tō tākuta, ka aromatawaihia hoki tō hauora whānui. Ka uru atu ki tēnei te pātai mō tō hītori hauora, tō hītori hauora whānau, me ngā tohumate e pā ana ki a koe.

Hei tirotiro anō i tētahi pukupuku kua kitea kētia, he pukupuku whakapae rānei, ka tūtohu pea tō tākuta i ēnei whakamātautau e whai ake nei:

• Ngā whakamātautau whakaahua hauora: Kei roto i ēnei ko ngā matawai MRI, ngā matawai ultrasound, me ngā matawai PET hei kite mārama i te pukupuku.
• Biopsy: Ka tangohia he wahi iti o te kiko mai i te pukupuku, ka tirohia i raro i te karuārai hei whakatau i te momo pūtau kei roto. Mā tēnei ka taea te kī atu mēnā he matepukupuku te pukupuku, kāore rānei.

Mena he maha ō pukupuku, ka tūtohu pea tō tākuta kia whakamātauria he whakamātautau ira hei tirotiro mēnā kei a koe ngā mate e kiia nei ko (NF1), (NF2), me te Schwannomatosis.

He aha ngā maimoatanga mō tēnei?

Ki te kore he tohu o te neuromastoid, ka tūtohu pea tō tākuta kia "mātakitaki, tatari".Ka taea e koe te whakamahi i te tikanga e kīia nei ko te "aroturukitanga." Arā, me tirotiro pinepine te puku kia kite ai mēnā kei te nui haere, kei te rerekē haere rānei.

Mō ngā pukupuku e whakaatu ana i ngā tohu o te mate, ki te hiahia rānei koe ki te tango i te pukupuku mō ngā take whakapaipai, ko te pokanga anake te huarahi i te nuinga o te wā .

He uaua ki te tango katoa i ētahi neurofibromas, inā koa ko ērā e kiia nei ko ngā plexiform neurofibromas, nā te mea ka tipu i roto i te io me waenganui i ngā paparanga o te hipoki. Mena kāore e taea te tango katoa i te pukupuku i muri i te pokanga, ka tirotirohia koe e tō tākuta, nā te mea ka taea e te pukupuku te tipu anō.

Te maimoatanga o ngā schwannomas i te upoko

Ko ngā schwannomas e puta mai ana i te mahunga, pērā i ngā schwannomas vestibular, ka pā ki ngā io e whakahaere ana i ngā mahi nui o tō tātou tinana. I ēnei wā, ka whakamahia e ngā tākuta tētahi tikanga e kiia nei ko te stereotactic radiosurgery (hei tauira, Gamma Knife®) hei ārai i te kino o ngā io.

Ehara tēnei i te pokanga tuku iho e hiahiatia ana he tapahi. Engari ko te tuku i tētahi hihi irahiko tino tika te arotahi mā roto i te kiri hei whakangaro, hei whakaiti rānei i te pukupuku.

Te rongoā i ngā pukupuku pukupuku o te pukupuku io ā-taha

Haunga te pokanga, ka taea hoki te whakamahi i ngā maimoatanga mate pukupuku pēnei i te radiotherapy me te chemotherapy hei rongoā i ngā pukupuku kino o te pukupuku io peripheral.

He aha ngā raruraru ka pā mai i te pokanga?

Pērā i ngā pokanga katoa, he maha ngā raruraru noa ka pā mai i ēnei pokanga:

• Te toto
• Mate pāwera
• Mamae
• Te whara

Hei tāpiritanga, he mōrearea te pakaru o te io me te hauātanga tuturu i roto i te pokanga io. Mā tō rōpū hauora koe e āwhina ki te whakahaere i tētahi hauātanga roa ka puta mai i muri i te pokanga. Tērā pea ka āwhina i a koe ki te ora mā te maha o ngā maimoatanga (te whakaora tinana, te whakaora mahi, me te whakaora kōrero).

Ka taea te ārai i te whanaketanga o ēnei pukupuku?

Kāore anō kia mōhiotia he huarahi hei ārai i te hanganga o ēnei pukupuku. Heoi anō, ka tūtohu pea tō tākuta kia whakamātauria he whakamātautau ira mēnā:

• Mena kei roto i tō whānau tētahi hītori o te whanaketanga o ngā neurofibromas.
• Mena he maha ō pukupuku o te pūkahu io (he tohu pea tēnei nō te mate neurofibromatosis).

He aha tā tātou whakaaro mō ēnei nati i ngā rā kei te heke mai? (Outlook)

Ko te nuinga o ngā neurofibromas ehara i te matepukupuku . Ka taea te whakaora mā te pokanga, ā, he onge te hokinga mai. Heoi, ki te kore e taea te tango katoa i tō pukupuku mā te pokanga, me noho tonu koe i raro i te tirotiro a te taote.

Tata ki te 3 i roto i te 4 o ngā tāngata e whiwhi maimoatanga ana mō te vestibular schwannoma ka taea e rātou te pupuri i ō rātou taringa whakarongo .

He tino iti te mōrearea o te mate pukupuku o te pukupuku io. Ko te mōrearea nui rawa atu ko te hunga whai mate pukupuku (NF1) e pāngia ana e te Plexiform neurofibroma. Kāore i te pai te matapae mō ngā pukupuku io kino o te pukupuku io (MPNST), inā koa he nui ake te pukupuku i te 2 inihi. He iti iho i te haurua o te hunga whai mate pukupuku e ora ana i te rima tau i muri i te tātaritanga.

Āhea koe me toro atu ki te tākuta?

Ki te kite koe i tētahi puku i raro i tō kiri, ki te pāngia rānei koe e ētahi tohu e whakaaro ana koe he neurofibromatosis , me toro atu ki te tākuta tonu . Me kōrero hoki ki tō tākuta mēnā kua pāngia tētahi o tō whānau e ēnei momo pukupuku.

Karere Whakamutunga mō te Tango ki te Kāinga

Kia maumahara, ko te nuinga o ngā pukupuku neuroendocrine he tipu pai, ehara i te matepukupuku, ā, he puhoi te tipu . Mēnā kāore he tohu, ka whakatau pea tō tākuta ki te tirotiro noa i a koe. Mēnā me tango he pukupuku, he tino angitu te pokanga. He tino onge te puta o ngā raruraru (pērā i te kore e taea te tango katoa i te pukupuku, te kino o te io), te huri rānei o te pukupuku hei matepukupuku. Ma tō tākuta koe e āwhina ki te whakawhanake i tētahi mahere maimoatanga me tētahi wātaka mō ngā whakamātautau a meake nei hei āwhina i a koe ki te whakahaere i tō āhua. Nō reira kaua e wehi ki te kōrero ki tō tākuta mō tetahi mea.

` ngā pukupuku o te pūkahu io, schwannoma, neurofibroma, neurofibromatosis, ngā pukupuku io, mate pukupuku, ngā mate ira, ngā pukupuku pūkahu io