Kua kōrerotia koe e te tākuta mō te pokanga ū? He mea noa te mataku me te manukanuka ina rongo koe i tēnā. Kaua e manukanuka. I tēnei rā ka kōrero tātou mō tētahi o aua pokanga, arā, ko te "thymectomy". Me mārama noa tātou he aha te tikanga, he aha te take e mahia ai, me pēhea te mahi, me te aha ka tupu i muri i te pokanga.
Tuatahi, he aha te Thymectomy?
He whakarāpopototanga noa iho, ko te thymectomy he tango pokanga i tō repe thymus. Kei te uma o runga te repe thymus, kei mua tonu i te ngākau.
He repe tino motuhake tēnei. He tino āwhina ki te whakawhanake i tō tātou pūnaha ārai mate i a tātou e tamariki ana. Engari i a tātou e pakeke haere ana, ka mimiti tēnei repe. I ētahi wā, nā ētahi raruraru o tēnei repe, me tango e ngā tākuta. Ehara tēnei i te pokanga tino noa.
He aha ngā āhuatanga hauora e arahi ana ki tēnei pokanga?
He maha ngā take matua mō te tango i te repe thymus. Me titiro tātou ki ērā.
| Tūnga mate | He whakamārama māmā |
|---|---|
| Te Maistenia Gravis | He mate tēnei e pā ana ki ngā io me ngā uaua. Ko te tohu matua ko te ngoikore o ngā uaua o te tinana. Ka taea te whakahaere i ēnei tohu mā te tango i te repe thymus. |
| Timoma | He pukupuku tēnei e tupu ana i roto i te repe thymus. Tērā pea he matepukupuku (thymic carcinoma) he matepukupuku rānei (pai). Ka mahia tēnei pokanga hei tango i aua pukupuku. |
| Ētahi atu momo nati | Ka taea hoki e ētahi atu momo pukupuku onge, pērā i ngā pukupuku neuroendocrine, te whakawhanake i roto i te repe thymus. He otinga anō hoki tēnei pokanga mō rātou. |
Me pēhea te whakarite i mua i te pokanga?
Ki te whakatau koe kia tangohia tō manawa, ka tirotirohia koe e tō tākuta me te matapaki i tō hītori hauora. Hei tāpiri, tera pea ka tonoa koe kia mahi i ētahi atu whakamātautau.
- Whakamātautau mahi a ō pukahukahu: Tirohia te pai o te mahi a ō pukahukahu.
- EKG (Electrocardiogram): Akohia te mahi a te ngākau.
- Whakamātautau ahotea ngākau: Tirohia te urupare a tō ngākau ki te whakakori tinana.
- Matawai CT (Matawai Tomography Rorohiko) MRI rānei (Whakaahua Āhua Aukume): Hei tiro mārama i te repe thymus me ngā whekau e karapoti ana.
- Matawai PET (Matawai Tomography Tukunga Positron): Hei tirotiro mō ngā pūtau matepukupuku.
Ko te mea nui: Ki te mea kei te tango koe i ētahi rongoā (ina koa mō te Myasthenia Gravis), me pātai atu ki tō tākuta mēnā me mutu te tango i mua i te pokanga. Kaua e mutu te tango i tētahi rongoā me te kore āna tohutohu.
I te nuinga o te wā ka tohutohuhia koe kia mutu te kai me te inu mai i waenganui pō o te pō i mua i te pokanga.
Kia kite tātou me pēhea te mahi o te pokanga.
E rua ngā tikanga matua mō te mahi i te thymectomy. Ko tētahi mā te pokanga tuwhera, ko tētahi mā te raupapa o ngā tapahi iti me te kāmera. Mā tō tākuta e whakatau ko tēhea tikanga te mea pai mōu.
| Tikanga pokanga | Te āhua o te tupu |
|---|---|
| Pokanga Tuwhera (Huarahi Whakawhiti) | I tēnei, ka whakatuwheratia te uma mā te tapahi i te wheua waenga (sternum) kia roa, he rite ki te pokanga ngākau tuwhera. Kātahi ka tangohia te repe thymus me ngā kiko e karapoti ana. Hei whakamutunga, ka whakauruhia kia kotahi, kia rua rānei ngā ngongo uma hei tango i te wai mai i te kōhao o te uma, ka mau te wheua ki ngā waea, ā, ka tuia te kiri kia kati. |
| Pokanga Whakaekenga Iti (Pokanga Whakaekenga Iti - Robotic, VATS rānei) | Kāore tēnei tikanga e hiahia ana ki te tapahi nui i te uma. Engari, e toru ngā tapahi iti ka mahia ki te taha o te uma, tētahi me te kāmera, tētahi me ngā taputapu motuhake. Mā te whakamahi i ēnei taputapu (i ētahi wā me te āwhina o te ringa karetao), ka tangohia te repe, ka whakanohoia ki roto i tētahi putea iti, ka tangohia mā tētahi o ngā tapahi. He iti ake te mamae o tēnei tikanga, ā, he poto ake te wā whakaora. |
I te nuinga o te wā, ka roa pea tēnei pokanga mō te rua ki te whā hāora.
Ngā painga me ngā mōrearea o te pokanga
Ngā painga o tēnei pokanga
Ka taea e tēnei pokanga te whakarato i te oranga nui mō te tangata e pāngia ana e te Myasthenia Gravis.
- Kei te heke haere te maha o ngā tāngata e whakaurua ana ki te hōhipera nā te mate nei.
- Ka taea te whakaiti i ngā rongoā e tangohia ana e koe mō te mate (hei tauira, te Prednisone).
- Ka heke te ngoikore o te tinana.
- Ka tino ora ētahi o ngā tohumate, ā, ka taea e rātou te ora tonu me te kore rongoā.
Mena ka mahia te pokanga me te iti noa o te pokanga, ka iti ake te noho hōhipera, ka iti ake te toto e ngaro, ka iti ake te mamae, ā, ka taea e koe te hoki wawe ki tō oranga o mua.
Tata ki te 70% o te hunga e tangohia ana te manawa mō te myasthenia gravis ka kite i te hekenga o ngā tohu me te hiahia ki te rongoā. I waenga i te 30% me te 40% ka kite i te memeha katoa o ngā tohu.
Ngā tūponotanga pea (Ngā raruraru)
Pērā i ngā pokanga katoa, he tūponotanga kei reira, engari kāore ēnei e pā ki te katoa.
- Te kino ki te ngākau, ki te io, ki te oko toto tata rānei.
- Te toto.
- Te pūkahukahu.
- Ngā mate urutā pērā i te niumōnia.
- He āhuatanga ohorere onge te myasthenic crisis e puta mai ana i te ahotea o te pokanga.
Kia pēhea te roa o te wā e ora ai, ā, he aha ngā mea hei tūpato māu?
Ko te roa o te whakaoranga e whakawhirinaki ana ki te pokanga tuwhera, ki te pokanga iti rawa rānei. Heoi, me noho koe ki te hōhipera mō te iti rawa i te rā kotahi. Ka hoatu he rongoā ki a koe hei whakahaere i te mamae i muri i te pokanga, ā, ka ngaro katoa i roto i ngā wiki e rua.
Ko te roa o te wā e hoki ai koe ki te mahi, kei runga i te āhua o tō mahi. Mena he mahi tēpu tāu, ka taea e koe te hoki wawe ki te mahi. Heoi, ki te mea he mahi tāu e hiahia ana kia hiki taumaha, kia tū rānei mō te wā roa, me roa ake pea te wā e ora ai koe.
Ki te pā mai ēnei tohu ki a koe, waea atu ki tō tākuta tonu atu.
Ina hoki koe ki te kāinga i muri i te pokanga, me whakamōhio tonu koe ki tō tākuta mēnā ka pāngia koe e tētahi o ngā tohu e whai ake nei:
- Te uaua ki te manawa.
- Te mamae i te taha kotahi o te uma.
- Te pikinga ake o te tere o te manawa.
- Te pikinga o te tere o te ngakau.
- Te kirika.
- Maremare.
- Te turuturu toto, te turuturu wai rānei mai i te wāhi i tapahia ai te pokanga.
- Ka puta anō ngā tohu o te myasthenia gravis.
Hei whakamutunga, he mea noa te mataku i a koe e pokanga ana. Engari kia maumahara, he mahi tonu tēnei a ngā taote pokanga. Kei te ngana tonu rātou ki te hoatu i te hua pai rawa atu ki a koe. Nō reira kaua e wehi ki te pātai atu ki tō tākuta mō ngā pātai, ngā āwangawanga rānei kei a koe.
Karere Tangohia ki te Kāinga
- Ko te tango i te repe thymus te mahi pokanga. Ko te nuinga o te wā ka mahia hei rongoā mō ngā mate pēnei i te Myasthenia Gravis me te Thymoma.
- E rua ngā tikanga matua mō te mahi i te pokanga (tuwhera me te iti rawa te pokanga). Kōrero ki tō tākuta mō te tikanga pai rawa atu māu.
- He tino nui ngā painga o tēnei pokanga mō ngā tūroro Myasthenia Gravis, engari tera pea ka roa te wā ka kitea ngā hua.
- He ngāwari te whakaora i muri i te pokanga, ā, he mea tino nui te whai i ngā tohutohu hauora.
- Kia tūpato ki ngā tohu whakatūpato ka puta i muri i te pokanga, ā, me whakamōhio tonu atu ki tō tākuta mēnā ka kite koe i tētahi.











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