I ētahi wā ka tino ngenge koe, ka ngoikore rānei, kāore he take? He kōwhai te āhua o tō kiri? Kāore rānei te kiri kōwhai o tō pēpi hou e memeha i muri i ngā wiki e rua? Ko te take o ēnei mea pea he ngoikore o te whākōkī e kiia nei ko te G6PD i roto i tō tinana. Kaua e manukanuka, he mate tino noa tēnei. I tēnei rā, ka kōrero māmā noa tātou mō te G6PD, he aha te mea ka puta ina iti, me te whakamātautau G6PD.
He aha te G6PD?
Whakaarohia ngā toto whero i roto i ō tātou tinana he rite ki ngā hōia e mahi ana. He 'kaitiaki' kei reira e tiaki ana i ēnei hōia mai i ngā momo mea kino. Ko taua kaitiaki he whākōkī e kiia nei ko te G6PD.
He whakarāpopototanga noa iho, he whākōkī tino nui te G6PD (Glucose-6-Phosphate Dehydrogenase) e tiaki ana i ō tātou pūtau, inā koa ngā pūtau toto whero i roto i ō tātou toto, mai i ngā matū kino. Ka whakaputahia e tō tātou tinana ngā matū kino (e kiia ana ko 'Free Radicals' 'Reactive Oxygen Species' rānei) e whakaputaina ana i te wā e mahi noa ana. Ka mahi te whākōkī G6PD i tēnei mā te aukati i ēnei matū kino kei kohikohi me te kino i ngā pūtau.
Ka aha mēnā he iti te G6PD?
Whakaarohia te mea ka tupu mēnā he iti te 'kaitiaki' (G6PD) i roto i te tinana? Kātahi ka puta mai aua mea kino ka tīmata ki te whakangaro i ō tātou toto whero. Ko tēnei tukanga o te pakaru tere o ngā toto whero i te mea ka taea te hanga ka kiia ko te hemolysis .
Ina ngaro te nui o ngā toto whero i tēnei ara, kāore tō tinana e whiwhi i te hāora e hiahiatia ana. Koinei te mea e kīia nei ko te anemia, he anemia hemolytic rānei. Koinei te take e ngenge ai koe, e ngoikore ai, e mā ai hoki i ngā wā katoa.
Me pēhea te puta o te ngoikore o te G6PD?
He mate ira tuku iho te ngoikore o te G6PD. Ko te tikanga he mea tuku iho i ō mātua. Ina puta he whakarerekētanga ira i roto i te ira e whakahau ana i a koe ki te hanga i te whākōkī G6PD, ka heke te nui o tēnei whākōkī e hangaia ana i roto i te tinana.
Engari ko te mea nui i konei, ehara i te mea ka puta ngā tohu ki te hunga katoa he ngoikore te G6PD. He maha ngā tāngata e noho noa ana, kāore he raruraru. Heoi anō, ka taea e ētahi āhuatanga o waho (e kiia ana ēnei e mātou he 'mea whakaoho') te puta ohorere mai o ngā tohu.
Ngā mea e whakaoho ana i ngā tohu G6PD
Mā ēnei mea whakaoho ka piki ake te nui o ngā 'rauropi kore utu' kino i kōrerotia e te tinana. Kāore e taea e te tangata he ngoikore te G6PD te whakahaere i ēnei matū kino e piki haere ana. Ko te wā tēnā ka tīmata te pakaru o ngā pūtau toto whero, ka puta ai ngā tohu.
| Momo Whakaoho | Whakaahuatanga |
|---|---|
| ētahi kai | Tērā pea ko ngā pīni fava . Ka pā mai ngā tohu mā te kai i a rātou, mā te hongi rānei i te hae. Ka kiia hoki tēnei mate ko te 'Favism'. |
| Ētahi rongoā | Ko ētahi rongoā mamae pēnei i te Aspirin, te Acetaminophen (Paracetamol), ētahi rongoā Sulfa, ētahi rongoā paturopi me ngā rongoā malaria ngā mea matua. Kaua e tango i tētahi rongoā me te kore he tohutohu a te taote. |
| Ngā mate huaketo me ngā mate kitakita | Ka taea e ngā mate katoa, mai i te makariri noa ki ngā mate kino, te whakaoho i ngā tohumate G6PD. |
He nui ake te kitea o te korenga o te G6PD i roto i ngā tāne i ngā wāhine, ā, he nui ake te kitea o te hunga o Āwherika, Āhia, me te Moana-nui-a-Kiwa.
Ko wai me whakamātautau i te G6PD?
Tērā pea ka tūtohu tō tākuta i tētahi whakamātautau toto noa iho (G6PD), ina koa mēnā kei a koe ētahi o ēnei tohu e whai ake nei:
- Te ngenge me te ngoikore kāore i te whakamāramahia
- Kiri mā
- Te uaua ki te manawa, te wheezing rānei
- Ngā tere o te ngakau
- Te kōwhai o te kiri me ngā kanohi (jaundice)
- Mimi pouri (tae kōra)
- Mamae tuara, mamae puku rānei
- Te āhua o te rangirua i nāianei
Kia tino tiakina ngā pēpi whānau hou.
He mea noa te pāngia o te pēpi hou e te jaundice. Engari, ki te roa atu i te rua wiki te roa , ka pōuri te mimi o te pēpi, ka mā te paru, ka whakapae pea te tākuta kei te ngoikore te G6PD, ā, ka whakahaerehia tēnei whakamātautau.
Me pēhea te mārama ki te pūrongo whakamātautau?
Ka rerekē pea ngā hua o te whakamātautau G6PD i ia taiwhanga, nō reira ko tō tākuta anake ka taea te hoatu i ngā mōhiohio tino tika . Heoi, e toru ngā momo hua i te nuinga o te wā.
- Noa: He nui te whākōkī G6PD i roto i tō tinana. Kāore he ngoikore o te G6PD i a koe.
- Te ngoikore o te tinana: Kei waenga i te 10% me te 60% o te taumata noa ngā taumata whākōkī. Ko te tikanga ka pāngia ēnei tāngata e te mate pāwera, ina rānei ka pāngia rātou e te uruparenga kino ki te rongoā.
- Te ngoikore nui: Kei raro iho i te 10% o ngā taumata noa te whākōkī. Tērā pea ka pāngia ēnei tāngata e te anemia pumau, e ngā tohumate auau rānei.
Te maimoatanga me te whakahaere i te ngoikore o te G6PD
Ehara te ngoikore o te G6PD i te mate e kore e taea te rongoā katoa, nā te mea he mate ira. Heoi, ki te whakahaeretia tika, ka taea e koe te noho ora me te kore raruraru .
Ko te mea pai ko te karo i ngā 'mea whakaoho' e puta ai ngā tohu. Koinei te rongoā matua.
Me mahi koe i ēnei:
- Kaua e kai rawa i ngā pīni fava.
- Kaua e tango i ngā rongoā whakamamae mamae pērā i te Aspirin me te Acetaminophen (Paracetamol) me te kore he whakaaetanga a tō tākuta.
- Me whakamōhio atu ki tō tākuta kei a koe te ngoikore o te G6PD i mua i te tuku rongoā .
- Rapua tonutia he awhina hauora mēnā ka pāngia koe e tētahi mate.
Mena he ngawari ō tohu, ka tohua pea e tō tākuta he pire waikawa folic me te rino. Mena he kino rawa tō anemia, me kawe pea koe ki te hōhipera, me whiwhi toto whakawhiti, rongoā hāora rānei.
Kia maumahara kāore ngā antioxidants pēnei i te Huaora E e āwhina i tēnei āhuatanga.
Karere Tangohia ki te Kāinga
- He mate ira noa te ngoikore o te G6PD ka tukuna iho i roto i ngā whakatipuranga, ā, ehara i te mea hei wehi.
- He tokomaha te hunga kāore he tohu. Ka puta ngā tohu ina pāngia rātou e ngā 'mea whakaoho' pērā i te pīni fava, ētahi rongoā, ngā mate pāwera rānei.
- Ko te whakahaere matua ko te karo i ēnei mea whakaoho.
- Mena he ngoikore tōu G6PD, he mea nui kia whakamōhio koe ki tētahi tākuta i mua i te rapu maimoatanga.
- Ki te pāngia koe e ngā tohu pēnei i te ngenge rawa ohorere, te kōwhai o te kiri, te mimi pouri rānei, me toro atu tonu ki tō tākuta.











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