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ꯑꯂꯄꯔꯁ ꯗꯤꯖꯤꯖꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯈꯪꯖꯤꯅꯒꯗꯕꯥ ꯋꯥꯐꯃꯁꯤꯡ꯫

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📅 Updated: Jul 15, 2026 • ⏱ 8 min read • Editorial Policy
ꯑꯂꯄꯔꯁ ꯗꯤꯖꯤꯖꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯈꯪꯖꯤꯅꯒꯗꯕꯥ ꯋꯥꯐꯃꯁꯤꯡ꯫
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ꯃꯃꯥ ꯅꯠꯠꯔꯒꯥ ꯃꯄꯥ ꯑꯃꯒꯤꯗꯃꯛ ꯃꯈꯣꯌꯒꯤ ꯑꯉꯥꯡ ꯑꯗꯨ ꯃꯈꯣꯌꯒꯤ ꯃꯤꯠꯃꯥꯡꯗꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯁꯣꯟꯊꯔꯀꯄꯥ ꯎꯕꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯆꯥꯎꯕꯥ ꯑꯋꯥꯕꯥ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ꯫ ꯈꯉꯍꯧꯗꯅꯥ ꯂꯥꯟꯊꯦꯡꯅꯗꯨꯅꯥ ꯁꯥꯟꯅꯔꯝꯕꯥ ꯑꯉꯥꯡ ꯑꯃꯅꯥ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯍꯧꯔꯀꯏ, ꯅꯠꯠꯔꯒꯥ ꯃꯍꯥꯛꯀꯤ ꯋꯥꯈꯜ ꯑꯃꯁꯨꯡ ꯇꯝꯕꯗꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯍꯟꯊꯔꯀꯄꯥ ꯎꯕꯗꯥ, ꯅꯍꯥꯛꯅꯥ ꯐꯥꯑꯣꯔꯤꯕꯥ ꯑꯀꯤꯕꯥ ꯑꯃꯁꯨꯡ ꯁꯣꯀꯄꯥ ꯑꯗꯨ ꯋꯥꯍꯩꯁꯤꯡꯗꯥ ꯐꯣꯡꯗꯣꯀꯄꯥ ꯌꯥꯝꯅꯥ ꯂꯨꯏ꯫ ꯃꯗꯨꯅꯤ ꯉꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯋꯥꯔꯤ ꯁꯥꯟꯅꯒꯗꯧꯔꯤꯕꯥ ꯑꯁꯤ ꯈꯅꯕꯗꯥ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯑꯃꯁꯨꯡ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯅꯤ꯫ ꯃꯁꯤꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯑꯂꯄꯔꯁ ꯗꯤꯖꯤꯖ, ꯅꯠꯠꯔꯒꯥ (ꯑꯂꯄꯔꯁ ꯗꯤꯖꯤꯖ)ꯅꯤ꯫

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ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯑꯂꯄꯔꯁ ꯗꯤꯖꯤꯖ ꯍꯥꯌꯕꯁꯤ ꯀꯔꯤꯅꯣ?

ꯑꯂꯄꯔꯁ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯁꯦꯂꯁꯤꯡꯗꯥ ꯄꯥꯋꯔ ꯄꯤꯔꯤꯕꯥ ꯑꯄꯤꯀꯄꯥ ꯄꯥꯋꯔ ꯄ꯭ꯂꯥꯟꯇꯁꯤꯡ ꯑꯣꯏꯔꯤꯕꯥ ꯃꯥꯏꯇꯣꯀꯣꯟꯗ꯭ꯔꯤꯌꯥꯗꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯒꯤ ꯁꯦꯜ ꯈꯨꯗꯤꯡꯃꯛꯀꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯄꯤꯀꯄꯥ ꯕꯦꯠꯇꯔꯤ ꯀꯌꯥ ꯂꯩꯕꯒꯨꯝ ꯈꯅꯕꯤꯌꯨ, ꯑꯃꯁꯨꯡ ꯕꯦꯠꯇꯔꯤꯁꯤꯡ ꯑꯗꯨꯅꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯗꯨꯕꯨ ꯃꯈꯣꯌꯅꯥ ꯊꯕꯛ ꯇꯧꯕꯗꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯏꯅꯔꯖꯤ ꯑꯗꯨ ꯄꯤꯔꯤ꯫ ꯑꯂꯄꯔꯁ ꯂꯥꯌꯅꯥꯗꯥ ꯊꯣꯛꯂꯤꯕꯥ ꯑꯁꯤꯗꯤ ꯍꯥꯌꯔꯤꯕꯥ ꯕꯦꯠꯇꯔꯤꯁꯤꯡ ꯑꯁꯤ ꯃꯥꯏꯇꯣꯀꯣꯟꯗ꯭ꯔꯤꯌꯥ ꯑꯁꯤ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯊꯕꯛ ꯇꯧꯗꯦ꯫

ꯑꯦꯅꯔꯖꯤ ꯃꯥꯡꯈꯤꯕꯥ ꯑꯁꯤꯅꯥ ꯃꯔꯨꯑꯣꯏꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯒꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯣꯔꯒꯥꯟ ꯑꯍꯨꯃꯗꯥ ꯑꯃꯥꯡ-ꯑꯇꯥ ꯊꯣꯀꯍꯜꯂꯤ꯫

1. ꯕ꯭ꯔꯦꯟ: ꯕ꯭ꯔꯦꯅꯒꯤ ꯐꯉ꯭ꯀꯁꯟ ꯁꯣꯟꯊꯔꯀꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯗꯤꯃꯦꯅꯁꯤꯌꯥ ꯊꯣꯀꯄꯥ ꯌꯥꯏ, ꯃꯗꯨꯅꯥ ꯃꯦꯃꯣꯔꯤ ꯂꯣꯁ ꯊꯣꯀꯍꯜꯂꯤ꯫

2. ꯂꯤꯚꯔ: ꯂꯤꯚꯔꯒꯤ ꯐꯉ꯭ꯀꯁꯟ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯊꯤꯡꯖꯤꯅꯕꯥ ꯌꯥꯏ, ꯃꯗꯨꯅꯥ ꯂꯤꯚꯔ ꯐꯦꯜ ꯑꯣꯏꯍꯅꯕꯥ ꯌꯥꯏ꯫

3. ꯃꯁꯂꯁꯤꯡ (muscles): ꯕ꯭ꯔꯦꯅꯗꯥ ꯂꯩꯕꯥ ꯏꯂꯦꯛꯠꯔꯤꯀꯦꯜ ꯑꯦꯛꯇꯤꯚꯤꯇꯤꯒꯤ ꯃꯑꯣꯡ-ꯃꯇꯧ (abnormal electrical activity)ꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯁꯤꯖ꯭ꯌꯨꯔ (seizures) ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫

ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯆꯍꯤ ꯑꯃꯍꯦꯛꯇꯗꯥ, ꯊꯥ ꯑꯃꯗꯒꯤ ꯆꯍꯤ 36 ꯐꯥꯎꯕꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯁꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯌꯥꯝꯅꯥ ꯑꯉꯥꯡ ꯑꯣꯏꯔꯤꯉꯩꯗꯥ ꯎꯕꯥ ꯐꯪꯏ, ꯃꯔꯨꯑꯣꯏꯅꯥ ꯆꯍꯤ 2 ꯑꯃꯁꯨꯡ 4ꯒꯤ ꯃꯔꯛꯇꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ, ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯅꯍꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯆꯍꯤꯗꯥ, ꯍꯥꯌꯕꯗꯤ ꯆꯍꯤ 17 ꯑꯃꯁꯨꯡ 24ꯒꯤ ꯃꯔꯛꯇꯥ ꯊꯣꯀꯄꯥ ꯌꯥꯏ, ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯥ, ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ, ꯑꯃꯁꯨꯡ ꯃꯁꯤ ꯑꯌꯥꯝꯕꯅꯥ ꯁꯤꯕꯗꯥ ꯂꯣꯌꯁꯤꯜꯂꯤ꯫

ꯃꯁꯤꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯄꯣꯀꯄꯗꯒꯤ ꯂꯧꯅꯔꯀꯄꯥ ꯖꯤꯅꯦꯇꯤꯛ ꯗꯤꯐꯦꯛꯇ ꯑꯃꯅꯥ ꯊꯣꯀꯍꯅꯕꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯄꯣꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯃꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯖꯤꯅꯁꯤꯡ ꯂꯩꯔꯕꯁꯨ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯂꯥꯀꯁꯤꯅꯕꯗꯥ ꯅꯨꯃꯤꯠ ꯀꯌꯥꯅꯤ, ꯊꯥ ꯀꯌꯥ ꯅꯠꯠꯔꯒꯥ ꯆꯍꯤ ꯀꯌꯥ ꯐꯥꯎꯕꯥ ꯆꯪꯂꯝꯕꯥ ꯌꯥꯏ꯫

ꯑꯂꯄꯔꯇꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯑꯇꯩ ꯃꯃꯤꯡ ꯀꯌꯥꯅꯥ ꯈꯪꯅꯩ:

  • ꯑꯂꯄꯔꯁ-ꯍꯨꯇꯦꯅꯂꯣꯆꯦꯔ ꯁꯤꯟꯗꯣꯝ꯫
  • ꯑꯂꯄꯔꯁ ꯁꯤꯟꯗꯣꯝ꯫
  • ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁꯤꯚ ꯏꯅꯐꯦꯟꯇꯥꯏꯜ ꯄꯣꯂꯤꯑꯣꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ꯫

ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯀꯅꯥꯅꯥ ꯅꯥꯔꯤ? ꯃꯁꯤ ꯀꯌꯥ ꯌꯥꯝꯅꯥ ꯀꯃꯟ ꯑꯣꯏꯕꯒꯦ?

ꯑꯂꯄꯔꯁ ꯂꯥꯌꯅꯥ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯑꯁꯣꯌꯕꯥ ꯖꯤꯟ ꯑꯁꯤ ꯏꯅꯍꯦꯔꯤ ꯇꯧꯔꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯅꯥ ꯖꯦꯟꯗꯔꯒꯤ ꯃꯇꯨꯡ ꯏꯟꯅꯥ ꯁꯦꯛꯁ ꯑꯅꯤꯃꯛꯇꯥ ꯆꯞ ꯃꯥꯟꯅꯅꯥ ꯁꯣꯀꯍꯜꯂꯤ꯫

ꯑꯗꯨꯕꯨ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏ, ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫ ꯆꯥꯡꯆꯠꯇꯥ ꯃꯤꯑꯣꯏ ꯂꯥꯈ ꯑꯃꯗꯥ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯱ . ꯃꯁꯤ ꯅꯣꯡꯄꯣꯛ ꯌꯨꯔꯣꯄꯀꯤ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯃꯔꯛꯇꯥ ꯈꯔꯥ ꯍꯦꯟꯅꯥ ꯀꯃꯟ ꯑꯣꯏ ꯍꯥꯌꯕꯁꯨ ꯌꯥꯏ꯫

ꯑꯂꯄꯔꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯀꯔꯤꯒꯤ ꯊꯣꯛꯂꯤꯕꯅꯣ? ꯃꯁꯤꯒꯤ ꯃꯔꯝ ꯀꯔꯤꯅꯣ?

ꯃꯁꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯔꯃꯗꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ POLG1 ꯀꯧꯕꯥ ꯖꯤꯟ ꯑꯃꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯥ, ꯅꯠꯠꯔꯒꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯁꯤꯅꯤ꯫ ꯃꯁꯤ ꯃꯤꯔꯣꯜ ꯑꯃꯗꯒꯤ ꯃꯤꯔꯣꯜ ꯑꯃꯗꯥ ꯆꯠꯊꯔꯀꯄꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯤ꯫

ꯏꯆꯝ ꯆꯝꯕꯥ ꯋꯥꯍꯟꯊꯣꯛ ꯑꯃꯗꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯃꯁꯤ ꯑꯁꯤꯒꯨꯝꯅꯥ ꯑꯣꯏꯔꯤ꯫ ꯑꯉꯥꯡ ꯑꯃꯥ ꯁꯦꯝꯅꯕꯒꯤꯗꯃꯛ ꯅꯍꯥꯛꯀꯤ ꯃꯃꯥꯗꯒꯤ ꯖꯤꯟ ꯑꯃꯥ ꯑꯃꯁꯨꯡ ꯃꯄꯥꯗꯒꯤ ꯖꯤꯟ ꯑꯃꯥ ꯂꯧꯕꯥ ꯃꯊꯧ ꯇꯥꯏ꯫ ꯑꯂꯄꯔꯁ ꯂꯥꯌꯅꯥ ꯂꯥꯛꯅꯕꯒꯤꯗꯃꯛ, ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯃꯃꯥ ꯑꯃꯁꯨꯡ ꯃꯄꯥ ꯑꯅꯤꯃꯛꯇꯒꯤ ꯑꯁꯣꯀꯄꯥ POLG1 ꯖꯤꯟ ꯑꯗꯨ ꯂꯧꯁꯤꯅꯒꯗꯕꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯃꯥ-ꯃꯄꯥ ꯑꯅꯤꯃꯛ ꯑꯁꯣꯀꯄꯥ ꯖꯤꯟ ꯑꯗꯨꯒꯤ ꯀꯦꯔꯤꯌꯔ ꯑꯣꯏꯔꯕꯁꯨ ꯃꯈꯣꯌꯗꯥ ꯂꯥꯏꯑꯣꯡ ꯂꯩꯇꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯕꯨ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯃꯈꯣꯌ ꯑꯅꯤꯃꯛꯇꯒꯤ ꯑꯁꯣꯀꯄꯥ ꯖꯤꯟ ꯑꯅꯤꯃꯛ ꯏꯅꯍꯦꯔꯤ ꯇꯧꯔꯕꯗꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯗꯥ ꯑꯂꯄꯔꯁ ꯂꯥꯌꯅꯥ ꯂꯥꯛꯀꯅꯤ꯫

ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯈꯟꯅꯈꯤꯕꯒꯨꯝꯅꯥ, POLG1 ꯖꯤꯅꯒꯤ ꯑꯁꯣꯏꯕꯥ ꯑꯁꯤꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯏꯅꯔꯖꯤ ꯁꯦꯟꯇꯔ ꯑꯣꯏꯔꯤꯕꯥ ꯃꯥꯏꯇꯣꯀꯣꯟꯗ꯭ꯔꯤꯌꯥꯗꯥ ꯂꯩꯕꯥ ꯗꯤ.ꯑꯦꯟ.ꯑꯦ. ꯃꯁꯤꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯕ꯭ꯔꯦꯟ, ꯂꯤꯚꯔ ꯑꯃꯁꯨꯡ ꯃꯁꯂꯁꯤꯡꯒꯨꯝꯕꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯑꯦꯅꯔꯖꯤ ꯃꯊꯧ ꯇꯥꯕꯥ ꯑꯣꯔꯒꯥꯅꯁꯤꯡꯗꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯁꯣꯀꯍꯜꯂꯤ꯫

ꯔꯤꯁꯔꯆꯔ ꯈꯔꯅꯥ ꯊꯥꯖꯩ ꯃꯗꯨꯗꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯚꯥꯏꯔꯁꯒꯨꯝꯕꯥ ꯑꯀꯣꯌꯕꯒꯤ ꯐꯤꯕꯃꯒꯤ ꯐꯦꯛꯇꯔ ꯑꯃꯅꯥ ꯑꯁꯣꯏ-ꯑꯉꯥꯝ ꯌꯥꯑꯣꯗꯕꯥ ꯖꯤꯅꯁꯤꯡ ꯑꯁꯤ ꯏꯅꯍꯦꯔꯤ ꯇꯧꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯥ ꯁꯣꯀꯍꯜꯂꯕꯗꯤ ꯃꯁꯤꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯊꯣꯀꯍꯅꯕꯁꯨ ꯌꯥꯏ꯫

ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯀꯔꯤꯅꯣ?

ꯑꯂꯄꯔꯇꯀꯤ ꯂꯥꯌꯅꯥꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯈꯦꯠꯅꯕꯥ ꯌꯥꯏ꯫ ꯃꯈꯣꯌ ꯑꯁꯤ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯍꯦꯅꯒꯠꯂꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯂꯥꯀꯄꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯗꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯌꯥꯏ꯫

ꯃꯍꯧꯁꯥꯅꯥ ꯎꯕꯥ ꯐꯪꯂꯤꯕꯥ ꯑꯍꯥꯅꯕꯥ ꯂꯥꯏꯑꯣꯡ ꯑꯁꯤ ꯔꯤꯐ꯭ꯔꯦꯛꯇꯔꯤ ꯏꯄꯤꯂꯦꯄꯁꯤꯅꯤ, ꯃꯁꯤ ꯂꯥꯏꯌꯦꯡꯕꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯑꯋꯥꯕꯥ ꯑꯣꯏ꯫

ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯇꯦꯕꯜ ꯑꯁꯤꯗꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯍꯦꯟꯅꯥ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯈꯪꯖꯤꯅꯁꯤ꯫

ꯂꯥꯏꯑꯣꯡꯒꯤ ꯃꯈꯜ꯫ ꯌꯦꯡꯅꯤꯡꯉꯥꯏ ꯑꯣꯏꯕꯥ ꯋꯥꯐꯃꯁꯤꯡ꯫
ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯍꯥꯅꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ꯫
  • ꯂꯤꯚꯔꯒꯤ ꯂꯥꯌꯅꯥ꯫
  • ꯋꯥꯈꯜ ꯈꯅꯕꯥ ꯉꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯆꯠꯊꯣꯛ-ꯆꯠꯁꯤꯟ ꯇꯧꯕꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯍꯟꯊꯔꯀꯄꯥ (ꯃꯥꯏꯜꯗ ꯀꯣꯒꯅꯤꯇꯤꯚ ꯏꯝꯄꯥꯌꯔꯃꯦꯟꯇ)
  • ꯀꯟꯗꯤꯁꯟ ꯑꯅꯤꯁꯤꯕꯨ ꯄꯨꯟꯅꯥ ꯁꯥꯏꯀꯣꯃꯣꯇꯣꯔ ꯔꯤꯒ꯭ꯔꯦꯁꯟ ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫
ꯑꯇꯣꯞꯄꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ꯫
  • ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯑꯃꯁꯨꯡ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ꯫
  • ꯕ꯭ꯔꯦꯅꯒꯤ ꯂꯥꯌꯅꯥꯁꯤꯡ (ꯑꯦꯅꯁꯦꯐꯦꯂꯣꯄꯦꯊꯤ) .
  • ꯕ꯭ꯂꯗ ꯁꯨꯒꯔ ꯅꯦꯝꯕꯥ (ꯍꯥꯏꯄꯣꯒ꯭ꯂꯥꯏꯁꯦꯃꯤꯌꯥ) .
  • ꯍꯤꯡꯕꯗꯥ ꯃꯥꯌ ꯄꯥꯀꯄꯥ ꯉꯃꯗꯕꯥ꯫
  • ꯍ꯭ꯌꯥꯂꯨꯁꯤꯅꯦꯁꯅꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯃꯥꯏꯒ꯭ꯔꯦꯟ꯫
  • ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯁꯣꯟꯊꯕꯥ (spasticity)
  • ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ꯫
  • ꯂꯥꯌꯅꯥ ꯑꯁꯤꯅꯥ ꯍꯦꯟꯅꯥ ꯁꯣꯀꯆꯤꯜꯂꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ꯫
  • ꯑꯣꯄꯇꯤꯛ ꯅꯔꯚ ꯁꯣꯟꯊꯔꯀꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯃꯤꯠ ꯎꯗꯕꯥ (optic atrophy)
  • ꯆꯥꯅꯕꯥ ꯆꯤꯟꯖꯥꯛ ꯊꯀꯄꯗꯥ ꯑꯋꯥꯕꯥ (dysphagia) .
  • ꯃꯦꯃꯣꯔꯤ ꯑꯃꯁꯨꯡ ꯏꯟꯇꯦꯂꯤꯖꯦꯟꯁ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯃꯥꯡꯈꯤꯕꯥ (ꯗꯤꯃꯦꯅꯁꯤꯌꯥ)
  • ꯍꯥꯔꯇꯀꯤ ꯃꯁꯂꯒꯤ ꯂꯥꯌꯅꯥꯁꯤꯡ (cardiomyopathy) .
  • ꯍꯀꯆꯥꯡꯒꯤ ꯕꯦꯂꯦꯟꯁ ꯑꯃꯁꯨꯡ ꯃꯨꯚꯃꯦꯟꯇ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯃꯗꯕꯥ (ataxia)
  • ꯁ꯭ꯇꯣꯃꯥꯛ ꯑꯃꯁꯨꯡ ꯏꯟꯇꯦꯁ꯭ꯇꯥꯏꯅꯒꯤ ꯂꯥꯌꯅꯥꯁꯤꯡ꯫
  • ꯂꯤꯝꯕꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯃꯗꯕꯥ (spastic quadriplegia, ꯁꯦꯔꯤꯕ꯭ꯔꯦꯜ ꯄꯥꯂꯁꯤꯒꯤ ꯃꯑꯣꯡ ꯑꯃꯥ)
  • ꯂꯤꯚꯔ ꯁꯤꯔꯣꯁꯤꯁ ꯅꯠꯠꯔꯒꯥ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯁꯣꯀꯍꯜꯂꯀꯄꯥ꯫
  • ꯗꯣꯛꯇꯔꯁꯤꯡꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯈꯪꯗꯣꯀꯄꯒꯦ?

    ꯃꯍꯧꯁꯥꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯆꯦꯀꯁꯤꯟꯅꯥ ꯌꯦꯡꯁꯤꯅꯒꯅꯤ, ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯈꯟꯅꯈꯤꯕꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡ ꯑꯍꯨꯝ ꯑꯗꯨꯗꯥ ꯑꯈꯟꯅꯅꯥ ꯃꯤꯠꯌꯦꯡ ꯆꯪꯒꯅꯤ : ꯃꯦꯃꯣꯔꯤ ꯂꯣꯁ, ꯂꯤꯚꯔꯒꯤ ꯂꯥꯌꯅꯥ, ꯑꯃꯁꯨꯡ ꯏꯄꯤꯂꯦꯄꯁꯤ .

    ꯃꯁꯤꯒꯤ ꯃꯊꯛꯇꯥ, ꯗꯥꯏꯑꯦꯒ꯭ꯅꯣꯁꯤꯁ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯅꯕꯥ ꯑꯇꯣꯞꯄꯥ ꯇꯦꯁ꯭ꯠ ꯀꯌꯥ ꯑꯃꯁꯨ ꯄꯥꯡꯊꯣꯀꯏ꯫

    ꯆꯥꯡꯌꯦꯡ ꯀꯔꯝꯅꯥ ꯇꯧꯒꯅꯤ ꯑꯃꯁꯨꯡ ꯀꯔꯤ ꯈꯉꯒꯗꯒꯦ꯫
    ꯁꯦꯔꯤꯕ꯭ꯔꯣꯁ꯭ꯄꯥꯏꯅꯦꯜ ꯐ꯭ꯂꯨꯏꯗ ꯑꯦꯅꯥꯂꯥꯏꯁꯤꯁ ꯇꯧꯕꯥ꯫ ꯁ꯭ꯄꯥꯏꯅꯦꯜ ꯇꯦꯞ ꯑꯃꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯃꯈꯥ ꯊꯪꯕꯥ ꯁꯔꯨꯛꯇꯥ ꯌꯥꯝꯅꯥ ꯄꯤꯀꯄꯥ ꯅꯤꯗꯜ ꯑꯃꯥ ꯊꯥꯗꯨꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯕ꯭ꯔꯦꯅꯒꯤ ꯑꯀꯣꯌꯕꯗꯥ ꯂꯩꯕꯥ ꯐ꯭ꯂꯨꯏꯗ ꯑꯗꯨꯒꯤ ꯑꯄꯤꯀꯄꯥ ꯁꯔꯨꯛ ꯑꯃꯥ ꯂꯧꯊꯣꯀꯄꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯎꯏ꯫ ꯃꯁꯤꯒꯤ ꯐ꯭ꯂꯨꯏꯗ ꯑꯁꯤ ꯑꯀꯛꯅꯕꯥ ꯕ꯭ꯔꯦꯅꯒꯤ ꯀꯦꯃꯤꯀꯦꯜ ꯈꯔꯗꯥ ꯑꯋꯥꯠꯄꯥ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯅꯥ ꯇꯦꯁ꯭ꯠ ꯇꯧꯏ꯫
    ꯏ.ꯏ.ꯖꯤ.ꯒꯤ ꯇꯦꯁ꯭ꯠ (ꯏꯂꯦꯛꯠꯔꯣꯑꯦꯅꯁꯦꯐꯦꯂꯣꯒ꯭ꯔꯥꯐꯤ)꯫ꯕ꯭ꯔꯦꯅꯒꯤ ꯏꯂꯦꯛꯠꯔꯤꯀꯦꯜ ꯑꯦꯛꯇꯤꯚꯤꯇꯤ ꯑꯗꯨ ꯌꯦꯡꯁꯤꯟꯅꯕꯥ ꯁ꯭ꯀꯨꯂꯗꯥ ꯑꯄꯤꯀꯄꯥ ꯙꯥꯇꯨꯒꯤ ꯄ꯭ꯂꯦꯇꯁꯤꯡ (electrodes) ꯊꯥꯏ꯫ ꯏ.ꯏ.ꯖꯤ.
    ꯖꯦꯅꯦꯇꯤꯛ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯥ꯫ ꯏꯒꯤ ꯁꯦꯝꯄꯜ ꯑꯃꯥ ꯂꯧꯗꯨꯅꯥ ꯖꯤꯅꯁꯤꯡꯒꯤ ꯁꯤꯛꯕꯦꯟꯁ ꯑꯗꯨ ꯇꯦꯁ꯭ꯠ ꯇꯧꯏ꯫ ꯃꯁꯤꯅꯥ POLG1 ꯖꯤꯅꯗꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯑꯆꯨꯝꯕꯥ ꯃꯑꯣꯡꯗꯥ ꯈꯪꯗꯣꯀꯄꯥ ꯉꯃꯒꯅꯤ꯫
    ꯑꯦꯝ.ꯑꯥꯔ.ꯑꯥꯏ.ꯒꯤ ꯁ꯭ꯀꯦꯟ (ꯃꯦꯒ꯭ꯅꯦꯇꯤꯛ ꯔꯤꯖꯣꯅꯦꯟꯁ ꯏꯃꯦꯖꯤꯡ)꯫ ꯕ꯭ꯔꯦꯅꯒꯤ MRI ꯁ꯭ꯀꯦꯟ ꯑꯃꯅꯥ ꯑꯂꯄꯔꯁ ꯂꯥꯌꯅꯥ ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯒꯤ ꯕ꯭ꯔꯦꯅꯗꯥ ꯒ꯭ꯔꯦ ꯃꯦꯇꯔ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯎꯕꯥ ꯐꯪꯏ꯫

    ꯃꯁꯤꯒꯤ ꯂꯥꯏꯌꯦꯡ ꯑꯃꯥ ꯂꯩꯕ꯭ꯔꯥ?

    ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯥ ꯉꯁꯤ ꯐꯥꯑꯣꯕꯗꯥ ꯑꯂꯄꯔꯇꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯐꯍꯅꯕꯥ ꯅꯠꯔꯒꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯊꯤꯡꯅꯕꯥ ꯂꯥꯌꯦꯡ ꯑꯃꯠꯇꯥ ꯐꯪꯗ꯭ꯔꯤ꯫

    ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯃꯦꯅꯦꯖ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ, ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯍꯟꯊꯍꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯐꯒꯠꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯃꯈꯜ ꯀꯌꯥꯒꯤ ꯁꯄꯣꯔꯇꯤꯚ ꯇ꯭ꯔꯤꯇꯃꯦꯟꯇꯁꯤꯡ ꯂꯩ꯫ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯑꯁꯤ ꯔꯤꯀꯃꯦꯟꯗ ꯇꯧꯕꯥ ꯌꯥꯏ:

    • ꯏꯄꯤꯂꯦꯄꯁꯤꯒꯤ ꯀꯟꯗꯤꯁꯅꯁꯤꯡ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯅꯕꯥ ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯀꯁꯤꯡ: ꯑꯦꯟꯇꯤꯀꯣꯅꯚꯂꯁꯦꯟꯇ ꯍꯤꯗꯥꯀꯁꯤꯡ ꯑꯁꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ (seizure) ꯊꯣꯀꯄꯥ ꯍꯟꯊꯍꯟꯅꯕꯥ ꯄꯤ꯫
    • ꯅ꯭ꯌꯨꯠꯔꯤꯁꯟ ꯑꯃꯁꯨꯡ ꯍꯥꯏꯗ꯭ꯔꯦꯁꯅꯒꯤꯗꯃꯛꯇꯥ: ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯆꯤꯟꯖꯥꯛ ꯊꯀꯄꯗꯥ ꯑꯋꯥꯕꯥ ꯇꯥꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯈꯣꯡꯗꯥ ꯇꯤꯎꯕ (percutaneous endoscopic gastrostomy) ꯑꯃꯥ ꯊꯥꯗꯨꯅꯥ ꯆꯤꯟꯖꯥꯛ ꯑꯃꯁꯨꯡ ꯐ꯭ꯂꯨꯏꯗ ꯄꯤꯖꯕꯥ ꯌꯥꯏ꯫
    • ꯗꯥꯏꯠ: ꯄ꯭ꯔꯣꯇꯤꯟ ꯅꯦꯝꯕꯥ, ꯑꯄꯤꯀꯄꯥ ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯆꯥꯕꯥ꯫
    • ꯐꯤꯖꯤꯀꯦꯜ ꯊꯦꯔꯥꯄꯤ: ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯍꯟꯊꯍꯟꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯃꯁꯂꯁꯤꯡ ꯃꯄꯥꯉ꯭ꯒꯜ ꯀꯅꯈꯠꯍꯟꯅꯕꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ꯫
    • ꯑꯣꯛꯌꯨꯄꯦꯁꯅꯦꯜ ꯊꯦꯔꯥꯄꯤ: ꯅꯨꯃꯤꯠ ꯈꯨꯗꯤꯡꯒꯤ ꯇꯧꯒꯗꯕꯥ ꯊꯕꯀꯁꯤꯡ ꯃꯁꯥ ꯃꯊꯟꯇꯥ ꯄꯥꯡꯊꯣꯛꯅꯕꯥ ꯇ꯭ꯔꯦꯅꯤꯡ ꯄꯤꯕꯥ꯫
    • ꯁ꯭ꯄꯤꯆ ꯊꯦꯔꯥꯄꯤ: ꯋꯥ ꯉꯥꯡꯕꯗꯥ ꯑꯋꯥꯕꯥ ꯄꯤꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
    • ꯄꯦꯏꯅꯀꯤꯂꯥꯔ ꯑꯃꯁꯨꯡ ꯃꯁꯜ ꯔꯤꯂꯥꯛꯁꯦꯟꯇꯁꯤꯡ: ꯑꯅꯥꯕꯥ ꯑꯃꯁꯨꯡ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯍꯟꯊꯍꯟꯅꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡ ꯄꯤ꯫
    • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯒꯤ ꯁꯄꯣꯔꯠ: ꯀꯔꯤꯒꯨꯝꯕꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯑꯋꯥꯕꯥ ꯊꯣꯛꯂꯕꯗꯤ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ CPAP ꯅꯠꯠꯔꯒꯥ BiPAP®ꯒꯨꯝꯕꯥ ꯃꯦꯁꯤꯅꯁꯤꯡꯅꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ, ꯅꯠꯠꯔꯒꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯊꯧ ꯇꯥꯔꯕꯗꯤ (tracheostomy).ꯅꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫

    ꯃꯁꯤꯗꯁꯨ ꯅꯠꯇꯅꯥ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯄꯦꯁꯦꯟꯇ ꯑꯗꯨꯒꯤ ꯀꯟꯗꯤꯁꯟ ꯑꯗꯨ ꯌꯦꯡꯁꯤꯟꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯃꯊꯧ ꯇꯥꯕꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯗꯨ ꯁꯦꯃꯗꯣꯛ-ꯁꯦꯃꯖꯤꯟ ꯇꯧꯅꯕꯥ ꯊꯥ ꯈꯔꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯇꯣꯉꯥꯟ-ꯇꯣꯉꯥꯅꯕꯥ ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯇꯁꯤꯡ (ꯈꯨꯗꯝ ꯑꯣꯏꯅꯥ ꯀꯝꯞꯂꯤꯠ ꯕ꯭ꯂꯗ ꯀꯥꯎꯟꯇ - CBC, ꯂꯤꯚꯔ ꯐꯉ꯭ꯀꯁꯟ ꯇꯦꯁ꯭ꯠ) ꯄꯥꯡꯊꯣꯛꯀꯅꯤ꯫

    ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯑꯅꯥꯕꯥ ꯑꯉꯥꯡ ꯑꯃꯥ ꯌꯦꯡꯁꯤꯅꯕꯤꯔꯕꯗꯤ...

    ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯤꯡꯅꯕꯥ ꯈꯣꯡꯆꯠ ꯑꯃꯅꯤ ꯍꯥꯌꯕꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯈꯉꯏ꯫ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯅꯥ ꯍꯦꯟꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯃꯑꯣꯡꯗꯥ, ꯅꯍꯥꯛ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯑꯍꯦꯅꯕꯥ ꯁꯄꯣꯔꯠ ꯃꯊꯧ ꯇꯥꯕꯥ ꯌꯥꯏ꯫ ꯈꯣꯡꯆꯠ ꯑꯁꯤꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯉꯝꯕꯥ ꯁ꯭ꯄꯦꯁꯤꯑꯦꯂꯤꯁ꯭ꯠ ꯑꯃꯁꯨꯡ ꯁꯔꯕꯤꯁ ꯀꯌꯥ ꯂꯩꯔꯤ꯫

    • ꯁ꯭ꯄꯦꯁꯤꯑꯦꯂꯤꯁ꯭ꯇꯁꯤꯡ: ꯅꯍꯥꯛꯅꯥ ꯒꯦꯁ꯭ꯠꯔꯣꯏꯟꯇꯦꯔꯣꯂꯣꯖꯤꯁ꯭ꯇꯁꯤꯡ, ꯅ꯭ꯌꯨꯠꯔꯤꯁꯅꯒꯤ ꯃꯤꯑꯣꯏꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯁꯥꯏꯀꯤꯌꯥꯠꯔꯤꯀꯁꯤꯡꯗꯒꯤ ꯃꯇꯦꯡ ꯂꯧꯕꯥ ꯌꯥꯏ꯫
    • ꯍꯣꯝ ꯅꯔꯁꯤꯡ ꯁꯔꯚꯤꯁ: ꯑꯀꯅꯕꯥ ꯑꯅꯥꯕꯒꯤ ꯀꯦꯁꯁꯤꯡꯗꯥ, ꯇ꯭ꯔꯦꯟ ꯇꯧꯔꯕꯥ ꯅꯔꯁꯤꯡ ꯁ꯭ꯇꯥꯐꯁꯤꯡꯕꯨ ꯅꯍꯥꯛꯀꯤ ꯌꯨꯃꯗꯥ ꯂꯥꯛꯇꯨꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯌꯦꯡꯁꯤꯅꯕꯤꯅꯕꯥ ꯀꯧꯕꯥ ꯌꯥꯏ꯫
    • ꯄꯦꯂꯤꯑꯣꯇꯤꯛ ꯀꯦꯌꯔ ꯇꯤꯃꯁꯤꯡ: ꯇꯤꯃꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯑꯔꯣꯏꯕꯥ ꯇꯥꯉ꯭ꯀꯀꯁꯤꯡꯗꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯅꯨꯡꯉꯥꯏꯅꯥ ꯂꯩꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯅꯥꯕꯥ ꯂꯩꯍꯟꯗꯅꯕꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯁꯄꯣꯔꯠ ꯑꯃꯁꯨꯡ ꯃꯦꯟꯇꯦꯜ ꯁ꯭ꯠꯔꯦꯡꯊ ꯄꯤꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫

    ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ, ꯅꯍꯥꯛ ꯈꯛꯇꯅꯥ ꯅꯠꯇꯦ꯫ ꯑꯂꯄꯔꯁ ꯗꯤꯖꯤꯖ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯃꯥꯏꯇꯣꯀꯣꯟꯗ꯭ꯔꯤꯑꯦꯜ ꯗꯤꯖꯤꯖ ꯂꯩꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯒꯤ ꯃꯃꯥ-ꯃꯄꯥꯁꯤꯡꯒꯤꯗꯃꯛ ꯁꯄꯣꯔꯠ ꯒ꯭ꯔꯨꯄꯁꯤꯡ ꯂꯩ꯫ ꯅꯍꯥꯛꯅꯥ ꯑꯦꯛꯁꯄꯔꯤꯌꯦꯟꯁꯁꯤꯡ ꯁꯦꯌꯔ ꯇꯧꯕꯥ ꯌꯥꯏ, ꯔꯤꯁꯣꯔꯁꯁꯤꯡ ꯁꯦꯌꯔ ꯇꯧꯕꯥ ꯌꯥꯏ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯅꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯄꯥꯎꯇꯥꯀꯁꯤꯡ ꯂꯧꯕꯥ ꯌꯥꯏ꯫

    ꯑꯂꯄꯔꯇꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯍꯧꯔꯀꯄꯒꯤ ꯆꯍꯤ 4 ꯑꯃꯁꯨꯡ 10ꯒꯤ ꯃꯔꯛꯇꯥ ꯊꯣꯀꯄꯥ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁꯤꯚ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫

    ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯖꯤꯟ ꯑꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯏꯃꯨꯡꯗꯥ ꯆꯠꯂꯤ ꯍꯥꯌꯕꯥ ꯈꯪꯂꯕꯗꯤ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯅꯥ ꯑꯉꯥꯡ ꯑꯃꯥ ꯄꯣꯛꯂꯤ ꯍꯥꯌꯕꯥ ꯈꯪꯂꯕꯗꯤ, ꯖꯦꯅꯦꯇꯤꯛ ꯀꯥꯎꯟꯁꯦꯂꯔ ꯑꯃꯒꯥ ꯎꯅꯗꯨꯅꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯕꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫ ꯃꯈꯣꯌꯅꯥ ꯑꯗꯣꯃꯗꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯄꯥꯎꯇꯥꯛ ꯑꯃꯁꯨꯡ ꯃꯇꯦꯡ ꯄꯤꯒꯅꯤ꯫

    ꯇꯦꯛ-ꯍꯣꯝ ꯃꯦꯁꯦꯖ ꯇꯧꯕꯥ꯫

    • ꯑꯂꯄꯔꯁ ꯗꯤꯖꯤꯖ ꯑꯁꯤ ꯃꯥꯏꯇꯣꯀꯣꯟꯗ꯭ꯔꯤꯌꯥꯗꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ, ꯁꯥꯊꯤꯕꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫
    • ꯃꯁꯤꯅꯥ ꯃꯔꯨꯑꯣꯏꯅꯥ ꯕ꯭ꯔꯦꯟ, ꯂꯤꯚꯔ ꯑꯃꯁꯨꯡ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ ꯑꯃꯁꯨꯡ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯗꯤ ꯏꯄꯤꯂꯦꯄꯁꯤ, ꯂꯤꯚꯔ ꯐꯦꯜ ꯑꯣꯏꯕꯥ, ꯑꯃꯁꯨꯡ ꯃꯦꯃꯣꯔꯤ ꯂꯣꯁ ꯑꯁꯤꯅꯤ꯫
    • ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯍꯤꯗꯥꯛ ꯂꯥꯡꯊꯛ ꯂꯩꯇꯕꯁꯨ, ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯃꯦꯅꯦꯖ ꯇꯧꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯅꯥꯕꯥ ꯑꯗꯨꯗꯥ ꯅꯨꯡꯉꯥꯏꯕꯥ ꯄꯤꯅꯕꯥ ꯁꯄꯣꯔꯠ ꯇꯧꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯀꯌꯥ ꯂꯩ꯫
    • ꯃꯁꯤ ꯖꯦꯅꯦꯇꯤꯛ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯔꯤꯁ꯭ꯛ ꯍꯟꯊꯍꯟꯅꯕꯒꯤ ꯄꯥꯝꯕꯩ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯐꯦꯃꯤꯂꯤ ꯍꯤꯁ꯭ꯇꯔꯤ ꯂꯩꯔꯕꯗꯤ ꯖꯦꯅꯦꯇꯤꯛ ꯀꯥꯎꯟꯁꯦꯂꯤꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫
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