Kodi nthawi zina mumamva ngati muli ndi chotupa kapena malo olimba pansi pa khungu pafupi ndi malo olumikizirana mafupa monga chigongono, phewa, kapena bondo? Sichingapweteke mukachikanikiza, koma chingakhale chachikulu pang'ono. Ndizachilendo kumva mantha pang'ono mukaona chinthu chonga ichi. Koma si zotupa zonse izi zomwe ndi khansa yoopsa. Lero tikambirana za vuto lomwe limasonyeza zizindikiro izi, koma si khansa, ndipo ndi losowa koma lofunika kudziwa. Ndi 'Tumoral Calcinosis' .
Kodi Tumoral Calcinosis ndi chiyani?
Mwachidule, tumoral calcinosis ndi matenda a majini . Izi zimachitika pamene kuchuluka kwa mankhwala otchedwa phosphate m'magazi mwanu kuli kokwera kwambiri. Phosphate ndi tinthu tamagetsi, kapena ayoni, tomwe tili ndi phosphorous. Chifukwa chake, mwa munthu amene ali ndi tumoral calcinosis, phosphorous ndi calcium zimasonkhana m'thupi, zomwe zimapangitsa kuti ziphuphu zipange pansi pa khungu, makamaka mozungulira mafupa.
Phosphorus ndi calcium ndizofunikira kwambiri kuti matupi athu amange mano ndi mafupa athanzi komanso olimba. Koma akakula kwambiri, zotupa zomwe sizili ndi khansa (zosaopsa), zomwe sizili zoopsa, koma zomwe zimaoneka ngati zotupa, zimayamba kupangika m'minofu. Ichi ndi chomwe timachitcha kuti tumoral calcinosis.
Kodi pali dzina lina la izi?
Inde, dzina lonse lachipatala la vutoli ndi 'Hyperphosphatemic Familyal Tumoral Calcinosis' (HFTC) . Dzina lalitali pang'ono, sichoncho? Madokotala ena amalitchanso kuti 'Teutschlaender disease'. Ndi kukumbukira Otto Teutschlaender, dokotala waku Germany amene anaphunzira za matendawa kuyambira m'ma 1930 mpaka m'ma 1950.
Kodi dzina lalitali lachipatalali limatanthauza chiyani?
Kodi tigawane dzinali m'zigawo zina kuti tilimvetse? Zimenezo zingakhale zosavuta.
- Hyperphosphatemic: Izi zikutanthauza kuti phosphate m'magazi ndi yokwera.
- Zachibale: Izi zikutanthauza kuti ichi ndi chikhalidwe chomwe chimachitika m'mabanja ndipo ndi cholowa.
- Chotupa: Mawuwa amagwiritsidwa ntchito chifukwa zotupa ngati chotupazi zimaoneka ngati zotupa za khansa.
- Calcinosis: Izi zikutanthauza kuti calcium imayikidwa m'maselo a minofu yanu ndi minofu yanu.
Kodi tsopano mwamvetsa tanthauzo la dzina lalitali limenelo?
Kodi Tumoral Calcinosis imakhudza bwanji thupi?
Ziphuphu zimenezi, zotchedwa tumoral calcinosis , nthawi zambiri zimapangika pansi pa khungu, pafupi ndi malo olumikizirana mafupa . Zitha kupangika m'malo olumikizirana mafupa angapo, komanso zimatha kupangika m'malo olumikizirana mafupa angapo. Malo odziwika kwambiri ndi awa:
- Malumikizidwe a m'chiuno
- Zigongono
- Mapewa
- Pansi
- Malumikizidwe a dzanja
- Zokhudzana ndi msana
- Malo a nsagwada
Kodi vutoli ndi lofala bwanji?
Akatswiri azachipatala sakudziwa bwino kuchuluka kwa anthu omwe ali ndi khansa ya calcinosis. Popeza ndi vuto losowa kwambiri , limapezeka kwambiri mwa anthu ochokera ku Africa ndi Middle East. Lingakhudze amuna ndi akazi.
Kodi mitundu ikuluikulu ya Tumoral Calcinosis ndi iti?
Mtundu wofala kwambiri wa izi ndi Hyperphosphatemic Familyal Tumoral Calcinosis, womwe tidakambirana kale. Kuphatikiza apo, palinso mitundu ina yosowa:
- Matenda a Hyperphosphatemia-hyperostosis (HHS): Imeneyi ndi matenda omwe amachititsa kuti mafupa azikula kwambiri komanso kuti mafupa asakhale ndi khansa azikula.
- Normophosphatemic tumoral calcinosis: Mtundu uwu nthawi zambiri umapezeka mwa anthu omwe ali ndi vuto la impso. Ungayambitse matenda otchedwa hyperparathyroidism, omwe ndi parathyroid gland yomwe imagwira ntchito mopitirira muyeso.
Kodi n’chiyani chimayambitsa matenda a Tumoral Calcinosis?
Matenda a khansa ya m'mawere ndi matenda a kagayidwe kachakudya omwe amabadwa nawo . Pafupifupi gawo limodzi mwa magawo atatu a anthu omwe ali ndi vutoli ali ndi kusintha, kapena kusintha, mu jini yawo ya FGF23. Jini ya FGF23 imathandiza maselo athu a mafupa kupanga puloteni yotchedwa fibroblast growth factor (FGF) 23. Anthu ena alinso ndi vutoli chifukwa cha kusintha kwa majini a GALNT3 ndi KL. Majini amenewa amalamulira kupanga FGF23. Anthu omwe ali ndi nomophosphatemic tumor calcinosis ali ndi kusintha kwa majini a SAMD9.
Kawirikawiri, puloteni `FGF23` imauza impso zathu kuchuluka kwa phosphate yoti itengenso kuchokera m'magazi. Koma pakakhala kusintha kwa majini, njirayi imasokonekera. Kenako impso zimayamwanso phosphate yochulukirapo kuposa momwe ziyenera kukhalira. Kawirikawiri, impso zimatulutsa phosphate yochulukirapo mu mkodzo. Koma mu calcinosis yotupa, phosphate iyi imagwirizana ndi calcium ndikupanga zotupa m'minofu yofewa.
Ndani ali pachiwopsezo chotenga matendawa?
Matenda a tumorous calcinosis ndi matenda obwera chifukwa cha autosomal recessive . Izi n'zovuta kumvetsa, koma mwachidule, kuti muthe kudwala matendawa, muyenera kulandira majini osinthika kuchokera kwa makolo anu onse awiri. Makolo anu akhoza kukhala onyamula kusintha kwa majini, koma mwina sangakhale ndi matendawa.
Ngati makolo onse awiri ali ndi kachilomboka, mwana aliyense ali ndi mwayi wotsatira:
- Pali mwayi umodzi mwa anayi wosakhala ndi jini yosinthika (palibe chiopsezo chotenga matendawa).
- Pali mwayi umodzi mwa anayi woti munthu akhale ndi khansa ya calcinosis.
- Pali mwayi umodzi mwa awiri woti munthu mmodzi mwa awiriwa akhale ndi matendawa koma osatenga matendawa.
Kodi zizindikiro za Tumoral Calcinosis ndi ziti?
Vutoli limapangitsa kuti ziphuphu za kukula kosiyanasiyana zipangike pafupi ndi malo amodzi kapena angapo olumikizirana mafupa. Ziphuphu zimenezi nthawi zambiri zimawonekera ali ana kapena achinyamata . Komabe, zimathanso kukula mwa makanda ndi akuluakulu. Nthawi zina, ziphuphu zochepa zokha zimakula m'moyo wonse. Kapena, ziphuphu zambiri zimatha kukula nthawi imodzi.
Mungakhale ndi zizindikiro monga izi:
- Kuvuta kusuntha kapena kupinda bwino malo olumikizirana mafupa.
- Ziphuphu zolimba, zopanda ululu (ziphuphu zina zingakhale zopweteka pang'ono zikakhudza).
- Kupweteka kwa minofu ndi mafupa.
Kodi Tumoral Calcinosis imapezeka bwanji?
Dokotala wa mafupa ndi dokotala amene amagwira ntchito yokhudza mavuto a mafupa ndi mafupa. Iye adzakuyang'anirani ndikufunsani za zizindikiro zanu. Kenako akhoza kuchita X-ray imodzi kapena zingapo zotsatirazi kuti aone zotupa izi ndi mavuto ena a mafupa:
- Kufufuza kwa X-ray `(X-ray)`
- Kujambula kwa CT
- Kujambula kwa MRI `(MRI)`
Ndi matenda ena ati omwe amasonyeza zizindikiro zofanana ndi za Tumoral Calcinosis?
Izi ndizofunikira kwambiri. Chifukwa ndikofunikira kupeza matenda oyenera . Chifukwa chake ndi chakuti pali matenda ena omwe amasonyeza zizindikiro zofanana, koma ndi oopsa kwambiri. Zina mwa matenda awa ndi:
- Zotupa zofewa za minofu yofewa ndi zotupa zofewa za minofu yofewa
- Calcific myonecrosis (chotupa cha calcium yomwe imayikidwa m'minofu ya miyendo)
- Calcific tendonitis (calcium yomwe ili ndi tendonitis)
- Calcinosis circumscripta (calcium yomwe imayikidwa pakhungu ndi minofu ya manja ndi mapazi)
- Calcinosis ya kulephera kwa impso (impso) kosatha (kuchuluka kwa calcium mwa anthu omwe akulandira dialysis)
- Calcinosis universalis (kuchuluka kwa mchere wa calcium m'khungu, minofu, minyewa, ndi minofu)
- Matenda a minofu yolumikizana
- Matenda a m'mimba
- Myositis ossificans (minofu yomwe imasanduka fupa)
- Osteosarcoma ndi sarcoma (khansa ya mafupa)
- Synovial chondromatosis (matuza a cartilage m'malo olumikizirana mafupa)
Mukuona? Ngakhale zizindikiro zake zili zofanana, chifukwa chake chingakhale chosiyana kwambiri. Ndicho chifukwa chake ndikofunikira kudziwa zomwe zikuchitika.
Kodi mankhwala osagwiritsa ntchito opaleshoni ndi ati?
Dokotala wanu angachepetse kuchuluka kwa phosphate m'magazi anu.Mankhwala omangira phosphate angapatsidwe. Mankhwala omangira phosphate awa akaphatikizidwa ndi mankhwala otchedwa acetazolamide (omwe amagwiritsidwa ntchito kwambiri pa matenda a khunyu ndi glaucoma), amatha kulepheretsa thupi kuyamwa phosphorous. Mungafunikenso kudya zakudya zopanda phosphorous .
Kodi zakudya zokhala ndi phosphorous yochepa ndi ziti?
Ngati muli ndi chotupa cha calcinosis, dokotala wanu angakulangizeni kuti mudye zakudya zokhala ndi phosphorous yochepa. Phosphorus imapezeka mwachibadwa mu nyama, nsomba, ndi mkaka. Phosphorus imawonjezedwanso ku zakudya zina ngati chosungira kapena chokometsera.
Yesetsani kuchepetsa zakudya ndi zakumwa zomwe zili ndi phosphorous yambiri, monga:
- Mowa, makola, tiyi wozizira ndi zakumwa za chokoleti.
- Mitundu ya chokoleti ndi caramel.
- Zakudya za mkaka (mkaka, tchizi, ayisikilimu, yogati yosakhala yachi Greek, supu zonona).
- Zakudya zam'madzi monga oyster ndi sardine, ndi ziwalo zamkati monga ng'ombe ndi chiwindi cha nkhuku.
- Nyama yokonzedwa (hot dog, nyama ya nkhomaliro, nyama yankhumba, soseji).
- Zinthu zopangidwa ndi oat bran.
Ndi bwino kulankhula ndi dokotala wanu kapena katswiri wa zakudya zamtunduwu kuti mudziwe zambiri.
Kodi chithandizo cha opaleshoni ndi chiyani?
Mungafunike opaleshoni kuti muchotse zotupa zomwe ndi zazikulu kwambiri moti sizingagwire ntchito bwino. Komabe, zotupazi zimatha kubwereranso kukula . Dokotala wanu angatengenso chitsanzo cha minofu yomwe yachotsedwa ndikujambula kuti atsimikizire kuti matendawa ndi otani.
Kodi ndi mavuto ati omwe angayambitse Tumoral Calcinosis?
Kawirikawiri, vutoli lingakhudze mitsempha yamagazi kapena ubongo wanu, zomwe zimawonjezera chiopsezo chanu cha matenda aakulu monga matenda a mtima ndi sitiroko.
Kuphatikiza apo, vutoli lingayambitsenso zotsatirazi:
- Kuchuluka kwa ma calcification a corneal kapena mikwingwirima ya angioid (mikwingwirima yofiira) mu cornea ya maso.
- Mavuto a mano.
- Kukula kwambiri kwa mafupa (hyperostosis).
- Kutupa m'mafupa aatali (diaphysis) m'miyendo kapena m'manja mwanu.
Kodi Tumoral Calcinosis ingapewedwe?
Ngati inu ndi mnzanu muli ndi kusintha kwa majini komwe kumayambitsa khansa ya calcinosis, mutha kulankhula ndi mlangizi wa majini za njira zochepetsera chiopsezo cha ana anu kulandira kusintha kwa majini. Anthu ena amasankha njira yotchedwa Preimplantation Genetic Diagnosis (PGD) . Izi zimaphatikizapo kuzindikira mazira omwe alibe kusintha kwa majini. Kenako dokotala wanu amagwiritsa ntchito njira yotchedwa In Vitro Fertilization (IVF) kuti asamutsire mazira athanzi ku ziwalo zoberekera za mayi. Ndi njirayi, mwana wanu sadzalandira kusintha kwa majini komwe kumayambitsa matendawa.
Kodi chiyembekezo cha munthu amene ali ndi Tumoral Calcinosis ndi chotani?
Anthu ambiri omwe ali ndi khansa ya calcinosis amakhala ndi moyo wathanzi komanso wokangalika . Matendawa nthawi zambiri samayambitsa mavuto aakulu azaumoyo. Komabe, muyenera kuwona dokotala nthawi zonse kuti muwone ngati matendawa abwereranso.
Kodi ndiyenera kupita kwa dokotala liti?
Pitani kwa dokotala ngati muli ndi zizindikiro izi:
- Kuchepa kwa kuyenda kwa mafupa m'malo olumikizirana mafupa.
- Kupweteka kwa mafupa, kupweteka kwa mafupa, kapena kupweteka kwa minofu.
- Kuoneka kwa chotupa kapena chotupa pansi pa khungu.
Kodi ndifunse dokotala wanga chiyani?
Mungathe kufunsa dokotala mafunso monga awa:
- Nchifukwa chiyani ndinayamba khansa ya calcinosis?
- Kodi chithandizo chabwino kwambiri kwa ine ndi chiti?
- Kodi ndikufunika opaleshoni?
- Ndi zakudya zamtundu wanji zomwe ndiyenera kuchepetsa?
- Kodi ndiyenera kuda nkhawa ndi zovuta?
- Kodi banja langa lonse liyenera kuyesedwa majini?
Kodi Tumoral Calcinosis Ingakhale Khansa?
Ngakhale kuti dzinalo limagwiritsa ntchito mawu oti "chotupa", zotupa zomwe zimayamba chifukwa cha khansa sizimayambitsa khansa kwenikweni . Palibe chiopsezo chakuti zotupazi zikhale zotupa. Choncho musadandaule nazo.
N’zoona kuti zotupa zomwe zili pansi pa khungu chifukwa cha khansa ya calcinosis zingakhale zosasangalatsa komanso zoopsa pang’ono. Koma kwa anthu ambiri, zotupazi sizimayambitsa mavuto aakulu. Mankhwala amatha kuchepetsa phosphorous m’magazi. Dokotala wanu angakulangizeninso kuti mukaone katswiri wa zakudya kuti akuthandizeni kudya zakudya zopanda phosphorous. Ngati mukuvutika m’mafupa anu, mafupa, kapena minofu zomwe zimakulepheretsani kuyenda bwino, uzani dokotala wanu. Ngakhale kuti zotupazo zingachotsedwe ndi opaleshoni, kumbukirani kuti zingabwererenso.
Uthenga Wopita Nawo Kunyumba (Zinthu Zoti Muzikumbukira)
Chabwino, tiyeni tikambirane mfundo zofunika kwambiri zomwe takambirana lero zokhudza Tumoral Calcinosis:
- Imeneyi ndi vuto losowa kwambiri, lobadwa nalo. Kuchuluka kwa phosphate m'magazi kumapangitsa kuti asakanikizidwe ndi calcium kuti apange ziphuphu pafupi ndi malo olumikizirana mafupa.
- Zotupa izi si khansa .
- Izi nthawi zambiri sizipweteka, koma zimatha kusokoneza kuyenda kwa mafupa.
- Chithandizo chimaphatikizapo mankhwala ochepetsa phosphate, zakudya zopanda phosphorus, komanso, ngati pakufunika, opaleshoni.
- Ngati muwona chotupa chonga ichi, musachite mantha ndipo funsani upangiri kwa dokotala. Kuzindikira matenda molondola ndikofunikira kwambiri.
- Anthu ambiri amakhala ndi moyo wabwinobwino komanso wotanganidwa ndi vutoli.
Choncho, ngati inu kapena munthu amene mumamudziwa ali ndi zizindikiro izi, ndi bwino kupita kwa dokotala kuti akakupatseni upangiri.
Calcinosis yotupa , ma cysts olumikizana, phosphate, calcium, matenda a majini, ma nodule a pakhungu, matenda a mafupa











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