Iyo abantu benshi bumvise ijambo 'anemia ' , bahita batekereza ku kubura icyuma . Niyo mpamvu bumva bananiwe igihe cyose, bananiwe, bazungera, ndetse rimwe na rimwe ntibashobore gusinzira. Ariko se wari uzi ko mu bihe bimwe na bimwe byo kubura icyuma, ibinyuranye n'ibyo bibaho koko? Aho kubura icyuma, icyuma mu turemangingo tw'amaraso 'kirazamuka'. Ese ibi ntibyumvikana nk'ibitangaje? Uyu munsi turimo kuvuga ku kibazo kimwe kidasanzwe, ariko kidakunze kugaragara cyane, cyitwa sideroblastic anemia.
Mu magambo make, Sideroblastic Anemia ni iki?
Kugira ngo tubisobanukirwe neza, reka tubanze turebe amaraso yacu. Mu mubiri w’uturemangingo dutukura mu maraso yacu harimo poroteyine yitwa hemoglobin . Akazi kayo k’ingenzi ni ugufata ogisijeni iza mu bihaha iyo duhumeka tukayijyana mu mubiri wose. Rero iyi ogisijeni ni ingenzi kugira ngo buri turemangingo two mu mubiri wacu tubeho.
Noneho, kugira ngo umubiri wacu ukore iyi hemoglobine, ukeneye rwose umunyu ngugu wa 'fer'. Muri rusange, kubura amaraso bibaho iyo umubiri udafite fer. Kubwibyo, ntushobora gukora hemoglobine.
Ariko, muri Sideroblastic Anemia, hari ikindi kintu gitandukanye kibaho. Aha, nta feri ibura mu mubiri. Mu by'ukuri, feri iba nyinshi cyane! Ikibazo ni uko bitewe n'inenge iri muri zimwe mu turemangingo dutukura twakorewe mu musemburo w'amagufwa yacu, badashobora gukoresha iyi feri mu gukora hemoglobin.
Tekereza igikoni gifite umuceri, amazi n'umunyu wo guteka umuceri, ariko icyuma giteka umuceri kikaba cyarangiritse. Icyo gihe ntushobora guteka umuceri. Uko ni ko bimeze. Muri iyi ndwara, hari icyuma cyinshi gikenewe kugira ngo hakorwe hemoglobine. Ariko uruganda rukoresha icyo cyuma kugira ngo rukore hemoglobine, uturemangingo tw'amaraso dutukura, ntigikora neza. Bityo icyuma kidakoreshejwe gitangira kwirundanya muri utwo turemangingo tw'amaraso dutukura dufite inenge. Utwo turemangingo tudasanzwe twakusanyije icyuma muri ubu buryo `(Sideroblasts)`.
Ni ibihe bimenyetso by'iyi ndwara?
Ibimenyetso by'iyi ndwara bisa cyane n'ibindi bibazo byo kubura amaraso, bityo rimwe na rimwe bishobora kwitiranywa byoroshye. Kandi kubera ko iyi ndwara ikura buhoro buhoro, ushobora no kutamenya ko uyirwaye. Ibi ni byo bimenyetso by'ingenzi ushobora kubona.
| Ibimenyetso | Ibisobanuro |
|---|---|
| Intege nke z'umubiri n'umunaniro | Kumva unaniwe, kunanirwa vuba nubwo haba hari imirimo mito. |
| Uruhu rwerurutse | Isura yera igaragara iyo amaraso ari make mu mubiri. |
| Guhumeka bigoranye | Asima iterwa no kuba umubiri utabona ogisijeni ikenewe. |
| Umutima utera vuba (Tachycardia) | Ugutera k'umutima cyangwa gutera cyane. |
| Kuribwa umutwe no kurakara | Kubabara umutwe kenshi no kurakara. |
| Kubabara mu gatuza | Mu bihe bimwe na bimwe, ububabare mu gituza bushobora kubaho. |
Ni ubuhe bwoko bw'ingenzi bwa Sideroblastic Anemia?
Iyi ndwara ishobora kugabanywamo ubwoko bubiri.
1. Anemia ya Sideroblastic ikomoka ku ruhu
Iyi ni indwara idakunze kugaragara cyane, iterwa na gene. Ni ukuvuga ko ikwirakwizwa ku mwana binyuze mu ngirabuzimafatizo z'umwe mu babyeyi. Ubwoko bukunze kugaragara cyane ni X-linked Sideroblastic Anemia . Ibi biterwa n'impinduka mu ngirabuzimafatizo igira ingaruka ku ikorwa rya hemoglobine. Kubera iyo mpamvu, umubiri ugerageza kwinjiza icyuma kinini mu biribwa kugira ngo usubize ku ibura rya hemoglobine. Mu bihe bikomeye, ishobora kwangiza ingingo nk'umwijima . Ubu bwoko bw'umubiri bukunze kumenyekana mbere y'imyaka 30.
2. Ubwoko bw'indwara itangira nyuma (Acquired Sideroblastic Anemia)
Ubu ni bwo bwoko bukunze kugaragara cyane. Igice cyiza ni uko akenshi bushobora gukira . Nubwo abaganga rimwe na rimwe batazi impamvu nyayo, hari ibintu byinshi by'ingenzi bigira uruhare muri ubu burwayi:
- Imiti imwe n'imwe: Cyane cyane imiti imwe n'imwe itangwa ku ndwara y'igituntu.
- Kunywa inzoga nyinshi: Kunywa inzoga nyinshi igihe kirekire ni ikintu gikomeye gishobora gutera ingaruka mbi.
- Ibinyabutabire by'uburozi : Guhura n'ibintu bimwe na bimwe by'uburozi igihe kirekire, nka lisansi.
- Izindi ndwara: Iyi ndwara ishobora guterwa n'izindi ndwara nk'indwara z'ubudahangarwa bw'umubiri, ibibyimba, cyangwa indwara z'imikorere y'umubiri.
Hari ikintu tugomba kwitaho cyane hano. Abantu bagera kuri 10% bafite iyi ndwara bashobora kurwara kanseri y'amaraso yitwa Leukemia. Kubwibyo, ni ngombwa cyane gusuzuma iyi ndwara neza, kumenya icyayiteye no kuyivura.
Byongeye kandi, ubwo bwoko bwombi bushobora kugira indi ndwara yitwa hemochromatosis , ituma icyuma cyiyongera mu mubiri.
Ni gute wasuzuma iyi ndwara neza?
Kubera ko ibimenyetso bisa n'ibindi bibazo byo kubura amaraso, bishobora kugorana kubisuzuma. Rero ni ngombwa gutega amatwi umubiri wawe. Niba ufite kimwe cyangwa byinshi mu bimenyetso byavuzwe haruguru, nyamuneka reba muganga wawe.
Muganga azakubaza witonze ibimenyetso byawe, agusuzume, hanyuma agutegeke ibipimo byinshi kugira ngo yemeze niba ufite iyi ndwara.
- Gupima amaraso: Gupima amaraso yose n'inyigo z'icyuma ni ingenzi.
- Gusiga amaraso mu gice cyo hanze: Hano, icyitegererezo cy'amaraso gisuzumwa hifashishijwe mikorosikopi kugira ngo harebwe niba hari uturemangingo tudasanzwe twibumbiramo icyuma (Sideroblasts) twavuze mbere.
- Isuzuma ry'amagufwa: Hari igihe hashobora kuba ngombwa ko hafatwa icyitegererezo gito cy'amagufwa no gupimwa kugira ngo hemezwe ko indwara ari yo.
- Ibindi bipimo: Iyo bibaye ngombwa, muganga ashobora no kukugira inama yo gupima MRI cyangwa gupima imiterere y’umubiri.
Ivurwa ite?
Uburyo bwo kuvura buterwa n'uko ufite ubwoko bw'indwara wavukanye cyangwa warabuvuwe.
- Kuvura Impamvu: Niba ufite ubwoko bw'indwara, intambwe ya mbere ni ukuvanaho impamvu. Urugero, niba hari umuti utera iyo ndwara, muganga wawe azahagarika uwo muti maze akwandikire undi. Niba unywa inzoga nyinshi, uzakenera kureka kunywa inzoga burundu.
- Vitamine B6: Ubushakashatsi bwagaragaje ko vitamine B6, cyangwa pyridoxine, ishobora kuba ingirakamaro mu kuvura ubwoko bwombi bw'indwara. Muganga wawe ashobora kukwandikira iyi vitamine nk'inyongera.
- Gukuraho icyuma gikabije: Hari imiti ishobora gutangwa kugira ngo ikure icyuma gikabije mu mubiri. Deferoxamine itangwa nk'urushinge munsi y'uruhu, naho Deferasirox itangwa nk'ikinini. Ariko, iyi miti ishobora kugira ingaruka ku mpyiko, bityo ikwiye gukoreshwa ikurikiranwe na muganga.
- Guterwa amaraso: Niba umubiri wawe utitabiriye ubuvuzi bwa Vitamine B6, muganga wawe ashobora kukugira inama yo guterwa amaraso. Ariko, ibi bifite ingaruka mbi. Iyo ukomeje guterwa amaraso, urugero rwa feri mu mubiri wawe ruziyongera, bikongera ibyago byo kwangirika k'umwijima.
- Gutera Umwobo w'Amagufwa: Ubu ni bwo buryo bwa nyuma bwo kuvura. Bufatwa mu bihe bikomeye aho nta bundi buryo bwo kuvura bwatanze umuti.
Ubutumwa bwo kujyana mu rugo
- Kubura amaraso mu maraso (Sideroblastic anemia) ntabwo ari nk'amaraso asanzwe. Ikigaragara hano ni uko urugero rw'icyuma mu turemangingo tw'amaraso rwiyongera, ntabwo rugabanuka.
- Nubwo waba ufite ibimenyetso nko kunanirwa kenshi no kutagira ubwiza, ntugafate icyemezo ubwawe ko ari ukubura icyuma gusa.
- Iyi ndwara ishobora kuvukanwa cyangwa ikavuka nyuma bitewe n'ibintu nk'inzoga cyangwa imiti imwe n'imwe.
- Niba ufite ibimenyetso, shaka ubufasha kwa muganga. Kwisuzuma no kwivura bishobora guteza akaga gakomeye.
- Hari uburyo bwiza bwo kuvura, nka vitamine B6 n'imiti ikuraho icyuma. Muganga wawe ni we uzaguhitiramo uburyo bwiza bwo kuvura.











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Kwipimisha kanseri y'ibere, kwisuzuma no kwirinda byakozwe byoroshye. Kanseri y'ibihaha
Ishyirireho intego ya calorie hanyuma ubare itariki yo kugabanya ibiro.