Ibintu ukeneye kumenya kuri hemophilia

Iyo ukomeretse gato, kuva amaraso kurahagarara nyuma y'igihe runaka, si byo se? Ibi biterwa n'uburyo butangaje umubiri wacu ukora. Ariko kuri bamwe, kuva amaraso ntibihagarika ibi byoroshye. Ndetse no gukomereka gato bishobora gutuma kuva amaraso gukomeza. Uyu munsi, tugiye kuvuga ku ndwara yitwa hemophilia, abantu benshi bumvise ariko ntibayimenye neza. Mbere yuko tuyitinya, reka dusobanukirwe neza icyo ari cyo.

Wamenya ute ko ufite hemophilia?

Mu magambo make, aho amaraso ava mu mubiri wacu, ikintu kimeze nk'agakingirizo ka 'plug' kigamije guhagarika kuva amaraso. Ibi tubyita fibrin clot. Kugira ngo habeho aka gakingirizo, poroteyine nyinshi zidasanzwe mu maraso yacu zigomba gukorana. Ibyo ni byo twita "ibintu bigabanya amaraso."

Hemophilia ni indwara aho kimwe muri ibi bintu bituma amaraso adakora neza, cyane cyane factor VIII cyangwa factor IX, kidakora cyangwa kikagabanuka kuva umwana avutse. Hanyuma, amaraso adakora neza, maze amaraso agakomeza kuva nta guhagarara.

Muganga wawe niba akeka ko ufite iyi ndwara, azagukorera ibizamini byinshi ku maraso yawe.

• Intambwe ya mbere: Hafatwa icyitegererezo cy'amaraso yawe hanyuma laboratwari igapima igihe bifata kugira ngo agire ubwonko buziba.
• Intambwe ya 2: Niba ibyo bizamini bigaragaza ko hari ibitagenda neza, hazakorwa ibizamini byihariye kugira ngo harebwe ingano ya factor VIII na factor IX mu maraso yawe.

Ni ubuhe buryo bwo kuvura hemophilia?

Uburyo bwo kuvura hemophilia buratandukanye bitewe n'ubwoko n'uburemere bw'indwara ufite. Urugero, niba ufite hemophilia yoroheje , ushobora gukenera kuvurwa gusa nyuma y'imvune cyangwa mbere yo kubagwa.

Ariko, niba ufite hemophilia ikomeye , aho uva amaraso kenshi, uzakenera gukomeza gufata imiti buri gihe kugira ngo wirinde kuva amaraso no gukumira ingingo zawe kwangirika no gucika intege.

Hari uburyo bwinshi bw'ingenzi bwo kuvura:

• Gusimbuza ikintu cyagabanutse mu maraso (Replacement therapy)
• Indi miti yihariye
• Kuvura ingaruka mbi nko kuva amaraso mu ngingo

Gutanga ikibazo cyo kugabanya amaraso mu mubiri (clotting factor) kidahagije

Ubu ni bwo buryo bw'ingenzi bwo kuvura. Ibi bikubiyemo guha umubiri wawe igipimo cy'ibintu bituma amaraso agwa mu mubiri kibura mu mitsi (mu mitsi cyangwa mu mitsi).

• Igipimo cya VIII ku bantu barwaye hemophilia ATanga.
• Factor IX ihabwa abantu bafite hemophilia B.

Ibi bintu bikorwa mu buryo bubiri. Kimwe ni plasma y'amaraso yatanzwe . Ikindi ni ADN ikorwa mu buryo bwa sintetike cyangwa recombinant ikorwa muri laboratwari . Ubwoko bushya bw'ibintu biboneka muri iki gihe bwagenewe kumara igihe kirekire mu mubiri. Kubwibyo, ntibikenewe guterwa inshinge kenshi nkuko byahoze.

Indi miti yihariye

Uretse kuvura indwara zifata amaraso menshi, hari n'indi miti igezweho ishobora gufasha mu kugabanya kuva amaraso. Muganga wawe azagusobanurira.

Menya neza ko amaraso ava mu ngingo n'ibindi bibazo.

Ikimenyetso gikunze kugaragara cya hemophilia ni ukuva amaraso mu ngingo . Ibi bishobora kubaho ahantu nko mu mavi, mu nkokora no mu tuguru. Iyo ibi bibaye, ingingo irabyimba kandi ikagira ububabare.

• Uburyo bwo kuvura: Ni ngombwa guhita ubona uburyo bwo kuvurwa n'ingingo yawe. Bitabaye ibyo, ingingo ishobora kwangirika burundu. Byongeye kandi, muganga wawe azakugira inama yo kuruhuka ingingo no kuyisiga barafu . Ibi bizagabanya ububabare no kubyimba.
• Nyuma: Nyuma y'uko ububabare bugabanutse, ubuvuzi bw'umubiri bushobora no kugirwa inama yo gufasha kugarura imbaraga n'ubushobozi bw'ingingo.

Nanone, ugomba kwitondera imyitozo ngororamubiri ukora. Siporo zose ntizikwiriye umuntu urwaye hemophilia. Siporo ziteje akaga zishobora gutera kuva amaraso imbere mu mubiri. Vugana na muganga wawe kugira ngo agufashe guhitamo imyitozo ngororamubiri ikubereye n'itakubereye.

Ese ubuvuzi bushobora gutera ingorane?

Nubwo uburyo bwo kuvura butekanye cyane muri iki gihe, hari ibintu bibiri ugomba kumenya.

1. Indwara ziterwa n'amaraso

Mu gihe cyashize, ahagana mu myaka ya za 1980, hari ibyago byinshi byo kwandura virusi nka virusi itera SIDA na hepatite biturutse ku bintu bishingiye ku maraso. Ariko ubu ntugomba guhangayikishwa nabyo. Muri iki gihe, abatanga amaraso basuzumwa cyane, kandi amaraso yose atangwa apimwa virusi kandi agasukurwa hakoreshejwe uburyo bwihariye. Rero ubu ibyago byo kwandura indwara bivuye mu kuvurwa ni bike cyane. Ariko, abaganga basaba ko urukingo rwa hepatite A na B rukingirwa.

2. Impinduka mu mikorere y'ubudahangarwa bw'umubiri (Inhibitors)

Ibi biragoye gato, ariko ni ngombwa kubyumva. Hari igihe ubudahangarwa bw'umubiri wacu, ari na bwo buryo bwo kwirinda bw'umubiri wacu, bumenya iyi factor ituma amaraso agwa nk''umwanzi''. Hanyuma, butangira gusenya iyo factor. Ibi tubyita "inhibitors" . Ibi nibibaho, ubuvuzi ufata bushobora kudakora neza. Kubwibyo, muganga wawe azasuzuma amaraso yawe buri gihe kugira ngo arebe niba ibi bibaho.