Ese umwana wawe afite iminkanyari idasanzwe? (West Syndrome) Reka tubiganireho!

Ese wigeze ubona umwana wawe agwa gitumo, nk'aho yakubiswe n'inkuba? Amaboko n'amaguru bye bihita bihindagurika, cyangwa akikubita inyuma. Nubwo ibi byamara amasegonda make gusa, niba bibaye inshuro nyinshi zikurikiranya, bishobora gutera ubwoba cyane ku mubyeyi wese ubibonye. Tugiye kuvuga ku ndwara iteye ubwoba cyane, ariko ni ngombwa cyane kuyimenya vuba. Iyo ni indwara ya West Syndrome.

Mu magambo make, indwara ya West Syndrome ni iki?

Indwara ya West Syndrome ni indwara idakunze kugaragara ifata abana bato, cyane cyane abari munsi y'umwaka umwe . Yitiriwe umuganga wayivumbuye bwa mbere.

Ibi bifite amazina menshi mu baganga. Ushobora kumva izina Infantile Spasms (IS). Ibyo bisobanura infantile spasms. Binavugwa Epileptic Spasms. Nubwo hari amazina menshi, yose yerekeza ku ndwara imwe.

Ni ibihe bimenyetso by'iyi ndwara?

Ikintu nyamukuru kiranga ibi ni ugukora imibonano mpuzabitsina twavuze mbere. Ibyo byitwa spasms. Ibi bintu bifite imiterere yihariye:

• Uko ibise biza: Umwana ahita yunamira imbere (nk'iyo arwaye igifu) cyangwa agasubira inyuma. Amaboko n'amaguru bihita bikomera kandi bigatitira.
• Igihe: Igitutu kimwe kimara amasegonda make gusa.
• Amatsinda: Uku gutwita ntabwo kuza rimwe gusa ngo bihagarare. Kuza mu buryo bukomeza, bugizwe n'amatsinda . Gutwita kumwe gukurikirwa n'ukundi, hanyuma ukundi, hanyuma ukundi, kugeza ku 150 mu matsinda. Hari abana bafite amatsinda agera kuri 60 nk'ayo ku munsi.
• Igihe: Ubusanzwe ushobora kubona izi ngendo umwana akimara gukanguka avuye mu bitotsi.

Uretse uku gutigita, hari n'ibindi bimenyetso bishobora kugaragara.

Kuki ibi bibaho ku bana bato?

Indwara ya West Syndrome ni indwara idakunze kugaragara cyane. Ifata abana bagera kuri 6 mu 10.000. Ikunze gufata abana bari hagati y'amezi 4 na 8. Nubwo impamvu nyayo idahora izwi, hari impamvu nyinshi z'ingenzi zagaragaye.

• Ibibazo by'imiterere y'ubwonko: Ibitagenda neza bibaho mu gihe ubwonko bukura cyangwa bukora.
• Impinduka mu miterere y'uturemangingo: Iyi ndwara ishobora guterwa n'impinduka zimwe na zimwe mu miterere y'uturemangingo tw'umwana.
• Kwangirika k'ubwonko: Biterwa no kubura umwuka wa ogisijeni mu bwonko mu gihe cyo kuvuka cyangwa mu kindi gihe, nk'impanuka.
• Indwara za metabolike: Biterwa n'ibibazo bimwe na bimwe mu mikorere y'ibinyabutabire mu mubiri.
• Kwandura indwara zo mu bwonko: Indwara zandura zigira ingaruka ku bwonko.
• Ikibyimba cya Tuberous Sclerosis: Indwara y’uturemangingo aho ibibyimba bitari kanseri bikura mu mubiri no mu bwonko.

Isuzuma rikorwa rite?

Niba ubonye umwana wawe afite ubwo bwoko bw'indwara yo gucura, ugomba kujya kwa muganga w'abana vuba bishoboka .

Icy'ingenzi cyane: Mbere yo kujya kwa muganga, ni ingirakamaro cyane niba ushobora gufata videwo ku nda z'umwana wawe. Ibi akenshi bishobora kwitiranywa na colic, bityo ni ingirakamaro cyane kuri muganga kureba videwo kugira ngo agufashe gusuzuma iyo ndwara.

Muganga ahanini yerekeza kuri ibi bizamini:

• EEG (Electroencephalogram): Iki ni cyo kizamini cy'ingenzi cyane. Muri make, cyandika imikorere y'amashanyarazi mu bwonko nk'icyitegererezo. Umwana urwaye West Syndrome azagaragaza imiterere idasobanutse neza yitwa Hypsarrhythmia kuri EEG. Iki ni cyo kimenyetso cy'ingenzi cyo gusuzuma iyi ndwara.
• MRI cyangwa CT scan:Izi scan zifasha kureba niba hari ibibazo, ibyangiritse, cyangwa ibitagenda neza mu miterere y'ubwonko.
• Ibipimo by'amaraso, inkari, n'amazi yo mu bwonko (CSF): Ibi bizamini bifasha kumenya niba icyateye gutigita ari ikibazo cy’uturemangingo cyangwa ikibazo cy’imikorere y’umubiri.

Ni ubuhe buryo bwo kuvura ibi?

Ni ngombwa cyane gutangira kuvurwa vuba bishoboka nyuma yo gupimwa indwara ya West Syndrome, kuko kurwanya iyi ndwara bifasha kugabanya kwangirika k'ubwonko bw'umwana.

Umuti

Uburyo bukunze gukoreshwa cyane muri ibi ni imiti.

• ACTH: Iyi ni imisemburo. Itangwa nk'urushinge. Ifite akamaro kanini mu kugenzura umutima.
• Vigabatrin (Sabril): Uyu ni umuti uvura igicuri. Ugira akamaro cyane cyane ku bana barwaye indwara ya West Syndrome, indwara iterwa na Tuberous Sclerosis.
• Steroids: Steroids nka Prednisone nazo zirakoreshwa.

Iyi miti ishobora kugira ingaruka mbi nko kugabanuka k'ubudahangarwa bw'umubiri, kwiyongera k'umuvuduko w'amaraso, ndetse no kutabona neza. Kubwibyo, muganga ahora asuzuma umwana kandi akamuvura akurikije ibyiza n'ingaruka.

Indyo y'ibikomoka kuri Ketogenic

Ku bana bamwe, niba imiti idahagije mu kugabanya impiswi zabo, muganga ashobora kubagira inama yo kurya iyi ndyo yihariye. Iyi ni indyo irimo ibinure byinshi kandi irimo karubohidrati nke cyane .

Umuburo: Ntukagerageze kubikora uri wenyine mu rugo. Ibi bikunze gutangirira mu bitaro, ubifashijwemo na muganga n'inzobere mu mirire/imirire.

Kubaga

Iyo MRI scan igaragaje neza ko stroke iterwa n'igisebe runaka mu bwonko, muganga ashobora gusaba ko icyo gice cy'ubwonko gikurwaho. Ibi si ibintu buri wese ashobora gukora. Bifatwa icyemezo n'itsinda ry'abaganga.

Ni iki wavuga ku byerekeye ahazaza? (Outlook)

Nubwo iki kibazo kigoye kwibaza, ni ngombwa kumenya ukuri. Ahazaza ha West Syndrome hazagenwa n'ibintu byinshi by'ingenzi.

• Impamvu: Ni iyihe mpamvu itera iyi ndwara? Iyo itewe n'igikomere gikomeye mu bwonko, ibisubizo bishobora kuba bibi. Iyo itewe nta mpamvu igaragara (idiopathic), ibisubizo biba byiza.
• Igihe cyo gutangira kuvurwa: Iyo ubuvuzi bushobora gutangira mu kwezi kumwe nyuma yo kuvurwa, imikurire y'umwana ishobora kongera kumera neza.
• Uburyo bwo kuvurwa: Uburyo ifatwa ry'igicuri rishobora kugenzurwa vuba.

Uku kuvuga nabi akenshi kurahagarara ahagana ku myaka 4. Ariko,Abana benshi bashobora kurwara ubundi bwoko bw'igicuri nyuma yaho.

Abana benshi bafite ubumuga bwo mu mutwe cyangwa ibibazo byo mu mutwe. Ariko, iyo habonetse ubuvuzi bwiza hakiri kare, abana bagera kuri 20%-25% bashobora kubaho ubuzima busanzwe bafite ubwenge busanzwe. Kubwibyo, gufata ingamba hakiri kare ni ingenzi.