Wakambonzwa nezverudzi rwegomarara rusingawanzoitiki uye rwakakomba runokura muitsvo here, kunyanya muvechidiki? Pamwe kwete. Iyi iRenal Medullary Carcinoma, kana kuti RMC muchidimbu. Kunyangwe zvisiri zvakajairika, zvinogona kukosha kuziva nezvazvo, kunyanya kune vamwe vanhu. Kunyangwe iyi iri nyaya yakakomba, musatya. Ngatitaurei nezvazvo nenzira iri nyore uye inonzwisisika nhasi.
Chii chaizvo chinonzi RMC?
Zvichitaurwa zviri nyore, Renal Medullary Carcinoma (RMC) imhando yegomarara reitsvo. Asi hariwanzoitiki, rine simba, uye rinopararira nekukurumidza. Rinonyanya kuitika muvechidiki, kunyanya avo vane chirwere cheropa chinonzi `sickle cell disease` kana `sickle cell trait`.
Kana tichitaura nezvegomarara reitsvo, rudzi rwakanyanya kuwanda ndi'renal cell carcinoma'. RMC iboka re'renal cell carcinoma'. Asi hapana kana mumwe chete pavanhu zana vane gomarara reitsvo anova nechirwere ichi cheRMC. Hazviwanzoitiki.
Chii chinokonzera gomarara iri?
Masayendisiti nevanachiremba havasati vawana chikonzero chaicho cheizvi, asi pane chinhu chimwe chete chikuru chakawanikwa.
Itsvo dzedu dzine chikamu chinonzi `renal medulla`. Munhu ane chirwere che`sickle cell` dzimwe nguva ane masero matsvuku eropa anoshanduka kuita chimiro chesickle. Kana izvi zvikaitika, masero anogona kunamatirana pamwe chete ovhara tsinga dzeropa dziri muchikamu che`renal medulla` cheitsvo.
Kuvharika kweropa uku kunokuvadza masero ari munzvimbo iyoyo. Kunyanya, jini rinonzi `INI1` (rinonziwo `SMARCB1`) riri mumasero iwayo rinokuvadzwa. Iri jini re`INI1` rinoshanda se`muchengeti` anomisa masero kuti asave nekenza. Kana masero ekenza eRMC akaongororwa, jini iri re`INI1` hariwanikwe maari. Saka vanachiremba vanoongorora kuvapo kwejini iri re`INI1` kuti vaone kana bundu riri reRMC kana kwete.
Ndiri panjodzi yekubatwa neRMC here?
Zvakaoma kutaura kuti ndiani achazviwana. Kuva nemumwe munhu mumhuri yako ane RMC hakuwedzeri njodzi yekuzviwana. Izvi zvinoreva kuti hazvisi zvinhu zvinoitika mumhuri.
Chinhu chikuru chinokonzera njodzi chirwere cheropa chinonzi `sickle hemoglobinopathy`. Kureva kuti, vane `sickle cell disease` kana `sickle cell trait`. Asi kashoma , vanhu vasina zvirwere izvi vanogonawo kuva neRMC. Inonzi "renal cell carcinoma, isina kuiswa muzvikamu zvine medullary phenotype" (RCCU-MP).
Kana ukatarisa nhamba:
- Zvinowanzoitika muvarume kupfuura vakadzi.
- Kazhinji zvinokanganisa itsvo chaiyo.
- Chirwere ichi chinowanzoonekwa pazera diki, pakati pemakore gumi nerimwe nemakumi matatu nemapfumbamwe.
Zvakakosha kuti vechidiki, kunyanya avo vane chirwere chesickle cell kana kuti sickle cell trait, vazive nezvezviratidzo izvi, sezvo kuonekwa nekukurumidza kunogona kuita kuti kurapwa kuve nyore. Kana zviratidzo zvikaonekwa, enda kuna chiremba nekukasika.
Ndezvipi zviratidzo zveRMC?
Kune zviratidzo zvakawanda zvechirwere ichi. Kana uine chimwe kana zvimwe zvezviratidzo izvi, zvakanaka kutsvaga rubatsiro rwechiremba nekukurumidza.
| Chiratidzo | Tsananguro |
|---|---|
| Marwadzo munzvimbo yeitsvo | Kurwadziwa kunogara kuchinzwika kumativi ese edumbu nemusana wepazasi (pamusoro pegumbo). |
| Ropa muweti | Weti yepingi, tsvuku, kana shava. Dzimwe nguva panogona kunge paine ropa risingaonekwe nemaziso. |
| Bundu remudumbu | Chibundu kana kuti bundu rinoita sebundu riri kudivi rimwe redumbu. |
| Kuderedza uremu pasina chikonzero | Kudzikira uremu nekukurumidza munguva pfupi, pasina kuedza. |
| Kugara uchidziya uye kudikitira husiku | Kana uchigara uchirwara nefivha pasina chimwe chikonzero uye uchizvidya ziya zvakanyanya husiku zvekuti machira ako anonyorova. |
Chiremba anoongorora sei izvi?
Kana ukatiudza nezvezviratidzo zvako, chinhu chekutanga chinoitwa nachiremba ndechekukuongorora. Wobva watevera matanho aya.
1.Kuongororwa kweUltrasound: Izvi zvinogona kupa pfungwa isina kujeka yekuti pane chimwe chinhu chakaita sebundu muitsvo here.
2. CT kana MRI scan: Kana paine chifungidziro chekuti pane bundu, CT scan kana MRI inogona kurairwa kuti ionekwe zvakajeka nezvebundu iri. Zvichibva pamifananidzo iyi, chiremba anogona kuona kuti rinogona kunge riri kenza.
3. Kuongororwa kwemuviri: Kana kenza ichifungidzirwa zvakanyanya, bvunzo iyi inoitirwa kusimbisa. Izvi zvinosanganisira kuisa tsono diki munzvimbo yebundu reitsvo, kutora chidimbu chidiki chenyama wochiongorora pasi pemaikorosikopu.
4. Kuongororwa kwemajini: Masero anotorwa kubva mu biopsy anoongororwa kuti aonekwe kuti ane jini re `INI1` rinorwisa kenza ratakataura nezvaro kare.
- Kana jini rekuti `INI1` risipo , rinozivikanwa seRMC.
- Kana jini rekuti `INI1` risipo uye murwere asina chirwere che`sickle cell`, anoonekwa se`RCCU-MP`.
- Kana jini rekuti `INI1` riripo , harisi RMC, asi rudzi rwakasiyana rwebundu.
Ndezvipi zvinorapwa izvi?
Nekuti RMC igomarara rinopararira nekukurumidza uye rinotyisa, kurapwa kunofanira kuitwa nekukurumidza uye nehasha zvakaenzana.
- Kurapa nemakemikari: Uku ndiko kurapwa kwekutanga kunonyanya kushandiswa. Kunosanganisira kupa muviri mishonga inouraya masero ekenza.
- Kuvhiyiwa: Kubviswa kwegomarara uye pamwe itsvo yakakanganiswa.
- Kurapa Nemwaranzi: Kuparadza masero egomarara uchishandisa mwaranzi ine simba.
Nekuda kwekuti chirwere ichi hachiwanzoitiki, tsvakiridzo ichiri kuenderera mberi. Masayendisiti anogara achitsvaga mishonga mitsva uye inoshanda yeRMC.
Pane nzira yekudzivirira RMC here?
Zvinosuwisa kuti pari zvino hapana nzira inozivikanwa yekudzivirira RMC kuti isatange, uye hapana bvunzo yekuona zviratidzo zvisati zvaonekwa.
Chinhu chakanakisa chaungaita ndechekuziva . Kana uchiziva kuti une chirwere chesickle cell kana hunhu hwesickle cell, chenjerera zviratidzo zvataurwa pamusoro apa. Kana uine zvinokunetsa, enda kuna chiremba wako nekukasika.
Kazhinji, panguva iyo chirwere ichi chinoonekwa, kenza inenge yatopararira kumasero eropa kana dzimwe nhengo dzakadai semapapu, chiropa, nemapfupa. Saka, kuongororwa nekukurumidza ndiyo nzira yakanakisisa yekuwana mhedzisiro yakanaka.
Mharidzo Yekuenda Nayo Kumba
- Renal Medullary Carcinoma (RMC) igomarara reitsvo risingawanzoitiki asi rakakomba zvikuru rinonyanya kubata vechidiki.
- Chinhu chikuru chinokonzera izvi kuva nechirwere cheropa chinonzi
sickle cell diseasekana kutisickle cell trait. - Kurwadziwa nemusana/mudumbu, ropa muweti, bundu mudumbu, uye kudzikira kwehuremu kusingatsananguriki ndizvo zviratidzo zvikuru.
- Kana uine chirwere chesickle cell uye ukaona chimwe chezviratidzo zvataurwa pamusoro apa, enda kuna chiremba wako nekukasika.
- Muchirwere ichi, kuongororwa nekukurumidza uye kutanga kurapwa ndiyo mukana wakanakisa wekuponesa hupenyu.











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