Nhengo dzemudumbu dzemwana wako dzabuda here? Ngatidzidzei nezveizvi zvinonzi cloacal exstrophy!

Amai kana baba vangatya sei kana vakaona kuti dumbu remwana achangoberekwa harina kuumbwa zvakanaka uye dzimwe nhengo dzinofanira kunge dziri mukati dzabuda? Zvakaoma kufungidzira. Asi musazvidya mwoyo. Kunyange zvazvo ichi chiri chirwere chisingawanzoitiki, pane mushonga wacho. Ngatitaurei nezvechirwere ichi chinonzi Cloacal Exstrophy nenzira iri nyore yaunogona kunzwisisa.

Chii chinonzi cloacal exstrophy iyi?

Zvichitaurwa zviri nyore, Cloacal Exstrophy chirwere chekuzvarwa nacho chinoitika kana madziro edumbu remwana asingaumbike zvakanaka pavanenge vachikura mudumbu. Fungidzira, nekuti chikamu chepazasi chedumbu hachivharike zvakanaka, dundira remwana nechikamu cheura, kana dzimwe nhengo, zvakafukidzwa nekamuviri kadiki uye zvinobuda kunze kwemuviri. Izvi zvakaoma kuona. Dambudziko iri rinokanganisawo nhengo dzemuviri dzemwana.

Izvi zvinozivikanwawo sekuzvarwa nemwana asina kunaka . Izvi zvinoreva kuti idambudziko rinoitika mwana achiri mudumbu. Asi musazvidya mwoyo, mushure mekuvhiyiwa kashoma, kutanga pakuzvarwa uye kwenguva yakati, vana vazhinji vane chirwere ichi vanoenderera mberi nekurarama hupenyu hwakajairika, hunofadza.

Izvi zvinokanganisa sei mwana? Chii chinonzi OEIS complex?

Cloacal Exstrophy inozivikanwawo seOEIS complex kana kuti OEIS syndrome nekuti inosangana nemamwe matambudziko akati wandei. Ngationei kuti ndeapi:

Chii chinonzi Omphalocele?

Izvi zvinoitika kana tsandanyama dzemudumbu dzemwana, dziri pedyo nedumbu, dzisina kubatana zvakanaka, zvichiita kuti pave neburi. Nepaburi iri, dundira, ura hukuru, uye dzimwe nguva dzimwe nhengo, dzakadai sechiropa, dzinobuda. Asi nhengo idzi hadzingobudi chete, dzinofukidzwa neganda rinodzivirira.

Chii chinonzi exstrophy?

Apa ndipo panotenderera madziro edundira remwana kunze kwete mukati. Izvi zvinonzi dundira rekunze . Dundira rakati sandara panzvimbo pedenderedzwa, uye rinogona kutopatsanurwa kuita maviri. Uyewo, tsandanyama dzemudumbu nemapfupa echiuno, kana mapfupa akatenderedza chiuno, haabatani zvakanaka. Nekuda kweizvozvo, dundira rinopararira kumativi ese, sebhuku rakavhurwa zvakanyanya.

Chii chinonzi imperforate anus?

Muchiitiko ichi, huro yemwana, gomba ratinopinda naro tsvina, harina kuumbwa zvakanaka. Rinogona kunge rakavharika, kana kuti pangave pasina gomba rakadaro zvachose. Hura hupfupi zvikuru, uye hunogona kunge hwakabatana nedundira.

Zvikanganiso zvemusana chii?

Vanenge vatatu pavana vana vane cloacal exstrophyPanogonawo kuva nechirwere chinonzi spina bifida, apo mapfupa emusana haavharike zvakanaka, zvichiita kuti saga rine mvura rakatenderedza musana (zvichida netsinga) ribude nepaburi.

Zvakakosha: Mwana anogona kunge aine zvese izvi, kana kuti zvimwe chete. Vanachiremba vachanyatsoongorora zvese izvi.

Izvi zvine zvazvinoita here panhengo dzepabonde?

Ehe, Cloacal Exstrophy inokanganisawo nhengo dzesikarudzi dzemwana.

• Kana ari mukomana: Nhengo yemurume inogona kunge yakati sandara, pfupi, kana kuti yakakamurwa kuita mativi ekurudyi nekuruboshwe.
• Kana ari musikana: Clitoris inogona kupatsanurwa kuita zvikamu zviviri, chimwe kurudyi uye chimwe kuruboshwe. Panogonawo kuva nemazino maviri echikadzi.

Dambudziko iri rakajairika zvakadii?

Ichi chirwere chisingawanzoitiki . Zvichitaurwa zviri nyore, chinokanganisa mwana mumwe chete pavana 250,000 kusvika mumwe chete pavana 400,000 vanoberekwa. Uyewo, vakomana vane mukana wekuva nechirwere ichi kaviri kana katatu kupfuura vasikana.

Ndeapi marudzi e exstrophy-epispadius complex (EEC)?

Kubuda kwemasero eropa muropa (cloacal exstrophy) ndeimwe yemapoka ezvirwere zvekuzvarwa nazvo zvinonzi Exstrophy-Epispadias Complex (EEC) . Kutaura zvazviri, ndiyo mhando yakanyanya kuipa yeboka iri. Mwana anogona kuva nechirwere chimwe chete muboka iri, kana kuti anogona kuva nezvimwe zvakawanda pamwe chete.

Mamwe mamiriro ezvinhu ari muchikamu cheEEC ndeaya:

• Epispadias: Mumamiriro ezvinhu aya, urethra yemwana, iyo chubhu inotakura weti kubva mumuviri, haina kuumbwa zvakanaka.
• Dundira rinobuda: Mumamiriro ezvinhu aya, dundira remwana rinobuda mukati.

Chii chinokonzera cloacal exstrophy?

Vanachiremba havazivi kuti sei vamwe vacheche vachiva nechirwere ichi, asi vanotenda kuti chinoitika kana nyama inonzi cloacal membrane ikabvaruka kana kuputika panguva yekutanga yekuzvitakura.

Cloaca inzvimbo iyo sisitimu yekubereka yemwana, sisitimu yekugaya chikafu, uye sisitimu yeweti zvinosangana. Kazhinji, nhengo dzesisitimu idzi dzinoparadzaniswa kubva kune imwe neimwe neiyi membrane yecloacal. Saka kana membrane iyi yabvaruka, madziro edumbu haanyatsoumbwa. Nhengo hadzikure zvakanaka, uye dzinogona kutobatanidzwa zvisiri izvo. Pakupedzisira, dzimwe nhengo dzinobuda nepaburi riri mudumbu.

Ndezvipi zviratidzo zvechirwere ichi?

Zviratidzo zve cloacal exstrophy zvinogona kuonekwa pakarepo mushure mekuzvarwa. Mwana wako anogona kusangana nezvinotevera:

• Nhengo dzemuviri dzakabuda muburi riri mudumbu, mukati mechinhu chakaita sebhegi.
• Chimiro chakaita sebhegi chinobuda paburi riri kumashure kwemusana (uyu ndiwo Spina Bifida).
• Nhengo yemurume kana kuti nhengo yemukadzi inoita kunge yakakamurwa nepakati.

Vanachiremba vanoona sei izvi?

Kubuda kweropa mudumbu kunogona kuonekwa panguva yekuongorora mwana asati aberekwa panguva yekuzvitakura. Chiremba wako anogonawo kukurudzira kuti mwana apihwe MRI . Izvi zvinogona kupa mifananidzo yakajeka yenhengo dzemuviri dzemwana wako. Kuongororwa uku kunogona kuratidza zvinhu zvakaita se:

• Weti haibude zvakanaka kubva mudundira.
• Mapfupa epahuro akaparadzaniswa.
• Zvidiki pane saizi yakajairika yenhengo dzesikarudzi.
• Omphalocele zvinoreva kuti tambo yemwana yakabatirira pasi zvakanyanya mudumbu remwana.

Mushure mekunge mwana wenyu azvarwa, chiremba wenyu anogona kuraira kuti mwana wenyu apihwe MRI scan , abdominal ultrasound , kana zvimwewo zvinoongororwa . Izvi zvinogona kuongorora mashandiro enhengo uye kuoma kwechirwere. Achishandisa ruzivo urwu rwese, chiremba wenyu achagadzira hurongwa hwakanakisisa hwekurapa mwana wenyu.

Cloacal Exstrophy inorapwa sei?

Mwana wese achangoberekwa ane cloacal exstrophy achada kuvhiyiwa . Kuvhiyiwa uku kunosanganisira kudzosa nhengo dzakabuda mumuviri uye kuvhara mipata iri mudumbu nemusana. Mwana wako angangove achivhiyiwa kakawanda mumakore akati wandei. Izvi zvinonzi staged reconstruction .

Kurapa kwekufamba panguva yekuzvarwa

Kurapa kwakadai kunotanga mwana achangoberekwa:

• Kuvaka patsva dundira, kudzosera nhengo dziri mudumbu, uye kuvhara nzvimbo iri mudumbu.
• Kugadzira stoma . Iri iburi riri mudumbu rinobvumira tsvina kuti ipfuure ichibva muura hukuru. Tsvina iyi inounganidzwa mubhegi riri kunze (colostomy pouch). Chikwama ichi checolostomy chinogona kuva chenguva pfupi, kusvika mamwe maoparesheni aitwa.
• Kuvhara mukaha uri mumusana.

Kurapa muhudiki

Kana mwana akura zvishoma, kureva kuti, achiri mudiki, kurapwa kunoitwa seizvi:

• Kuvhiyiwa kwemapfupa (osteotomy) kunoitwa kucheka mapfupa echiuno. Izvi zvinoita kuti chiuno chivhare zviri nyore uye zvinopa rutsigiro rwakanaka kudundira mwana paanokura.
• Nhengo dzekubereka nedzemudumbu dziri kurongwa patsva.
• Panobva pagadzirwa buri rekumashure. Kana ura hwakareba zvakakwana, chiremba anogona kuita oparesheni yekudhonza kuti ibatanidze ura neanus. Stoma inobva yavharwa. Mwana haazodi colostomy homwe.

Ndezvipi zvinetso zvinogona kuitika kubva muchirwere ichi?

Mushure mekuvhiyiwa, vana vazhinji vane cloacal exstrophy vanorarama hupenyu huzere uye hune simba . Vamwe vana vangada kuvhiyiwa kakawanda sezvavanokura.

Cloacal exstrophy inogona kukonzera njodzi dzinotevera:

• Kusabereka.
• Zvirwere zveitsvo, hutachiona hweitsvo, matombo eitsvo, uye kutadza kushanda kweitsvo.
• Kusashanda zvakanaka pabonde, kusashanda zvakanaka kwepabonde, nezvimwewo.
• Kutadza kudzora weti uye kusagona kudzora tsvina.

Zvinhu zvekubvunza chiremba wako

Unogona kubvunza chiremba wemwana wako zvinhu zvakaita seizvi:

• Mwana wangu ari panjodzi yakakura yekubatwa nezvimwe zvirwere here?
• Ndeipi nzira yakanakisisa yekurapa Cloacal Exstrophy?
• Mwana wangu achada kuvhiyiwa kangani?
• Ndezvipi zvinetso zvandinofanira kutarisa mushure mekuvhiyiwa?
• Mikana yekuti mwana wangu anotevera achavawo neCloacal Exstrophy ndeipi?

Zvakajairika kuti unzwe kutya uye kunetseka kana ukaona kuti mwana wako ane Cloacal Exstrophy, kana kuti OEIS syndrome. Asi yeuka, hausi wega.

Chinhu chinonyanya kukosha chekurangarira

Zvingori zvechisikigo kuti unzwe wakaremerwa uye uchitya paunoona kuti mwana wako ane Cloacal Exstrophy. Asi usazvidya mwoyo . Vanachiremba vako nechikwata chekurapa vakagadzirira kukubatsira iwe nemwana wako. Mwana wako achada kuvhiyiwa kakawanda mushure mekuzvarwa, uye zvimwe zvekuvhiyiwa kuti agadzire nhengo dzemuviri.

Asi chinhu chakanakisa ndechekuti, kana vakarapwa zvakanaka, vana vazhinji vanoberekwa vane chirwere ichi vanorarama hupenyu hwakajairika uye hunofadza . Taura nachiremba wako nezvemibvunzo kana zvinokunetsa. Vachakutsanangurira zvese.

Kubuda kweCloacal , Zvirwere zvekuzvarwa, OEIS Complex, Omphalocele, Kubuda kweDundira, Kuvhiyiwa kwevana