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Chiratidzo chinoshamisa apo rumwe rutivi rwemuviri rwakatsvuka uye rumwe rutivi rwakachenuruka (Chiratidzo cheHarlequin)

Chiratidzo chinoshamisa apo rumwe rutivi rwemuviri rwakatsvuka uye rumwe rutivi rwakachenuruka (Chiratidzo cheHarlequin)

Fungidzira uchitarisa mugirazi woona mutsetse wakatwasuka pakati pechiso chako, rumwe rutivi rutsvuku uye rwakaita ziya, uye rumwe rutivi rwakaita serwakajairika, pamwe rwakachenuruka zvishoma... Hazvisi zvinotyisa uye zvinoshamisa here izvozvo? Kana kuti ko kana ukaona rumwe rutivi rwemuviri wemwana wako achangoberekwa ruchishanduka kamwe kamwe rutsvuku uye rumwe rutivi rwakaita serwakajairika? Izvi ndizvo zvatinodaidza kuti Harlequin Sign in medicine. Sezvo zita racho risinganzwisisike zvishoma, ngationei zvakawanda nezvazvo uye kana ichi chiri chinhu chekutya zvechokwadi.

Chii chaizvo chinonzi Harlequin Sign ichi?

Zvichitaurwa zviri nyore, Harlequin Sign inguva apo rumwe rutivi rwemuviri wako kana chiso chako runosangana nekuchinja kweruvara rweganda (kutsvuka kana kusviba), nepo rumwe rutivi ruchiramba rwakafanana, dzimwe nguva kutotsvuka. Mativi maviri aya anoita seakaparadzaniswa nemutsetse wakatwasuka, pakati pemuviri.

Pamwe chete nemusiyano uyu muruvara rweganda, zvimwe zvinhu zvinogona kuonekwa kumativi ese.

  • Kutsvuka: Nzvimbo iyi inogona kunge iri hyperhidrosis (kudikitira zvakanyanya). Ganda riri panzvimbo iyoyo rinogonawo kunzwa richidziya zvishoma kana rikabatwa.
  • Rutivi Rwakachenuruka/Rwakajairika: Rutivi urwu harudiki. Ganda rinonzwawo richitonhora kana rikabatwa.

Kunyangwe chiratidzo ichi cheHarlequin dzimwe nguva chingave chiratidzo chechirwere chakadai se'Harlequin syndrome', kazhinji kacho hachina njodzi uye chinongopera.

Ndezvipi zvikonzero zvikuru zveizvi?

Hazviwanzoitiki kuwana chikonzero chaicho cheizvi. Chikonzero chikuru cheizvi idambudziko rekutaurirana muhurongwa hwetsinga hwemuviri wedu. Funga nezveizvi sehurongwa hwe "auto-pilot" hwemuviri wedu. Hurongwa uhwu hunodzora zvinhu zvatisingazive kuti tinazvo, zvakaita sekufema kwedu, kurova kwemoyo, uye kudikitira.

Saka, kana paine kuvharika kana kusashanda zvakanaka kwetsinga dzinotumira mashoko kubva kuuropi (hypothalamus) kuburikidza nemutsipa wemusana kuenda kumeso nepamusoro pemuviri, mashoko acho anogona kusatumirwa zvakanaka kudivi rimwe chete remuviri. Ndokusaka mitsipa yeropa iri kudivi rimwe ichikura uye ichitsvuka, ukuwo rimwe divi risingagamuchire mashoko acho uye richiramba rakajairika.

Izvi zvinoitikawo kuvana vacheche vachangoberekwa here?

Ehe, ichi chinhu chinoonekwa muvana vachangoberekwa. Sekureva kweongororo, vanenge 10% vevana vane hutano vanogona kuva nechiratidzo ichi cheHarlequin. Saka, musazvidya mwoyo kana mwana wenyu aine ichi.

Izvi zvinowanzoitika pakati pemazuva maviri kusvika mashanu mwana aberekwa, asi dzimwe nguva zvinogona kuoneka kusvika mavhiki matatu.

Chinhu chinonyanya kukosha ndicho chiratidzo cheHarlequin icho vana vachangoberekwa vane.Hazvikuvadzi zvachose. Kuchinja kweruvara uku kunonyangarika mumasekonzi makumi matatu chete. Dzimwe nguva kunogona kutora kusvika maminetsi makumi maviri. Kunogona kuonekazve kana mwana akaiswa parutivi.

Zvakakosha: Chirwere ichi chinonzi Harlequin Sign hachifanirwe kuvhiringidzwa ne `Harlequin ichthyosis`, chirwere chine njodzi zvikuru, chinotyisidzira hupenyu uye chisingawanzoitiki chemajini. `Harlequin ichthyosis` chirwere umo muviri wese wemwana wakafukidzwa nemakwande akakora, akaita seplate, ane mitswe yakadzika pakati. Chinhu chakasiyana zvachose.

Zvimwe zvirwere zvine chekuita nazvo

Chiratidzo cheHarlequin dzimwe nguva chinogona kuonekwa sechiratidzo chemamwe matambudziko ehutano.

Harlequin Syndrome

Ichi chirwere chinokanganisa sisitimu yedu yetsinga inonzwira tsitsi. Sisitimu iyi yetsinga inodzora mhinduro yedu ye "kurwa-kana-kutiza", inova shanduko dzinoitika mumuviri patinofara, tichitya, kana tichiita maekisesaizi. Pose painoshanda sisitimu iyi mumunhu ane Harlequin Syndrome (semuenzaniso, panguva yekurovedza muviri), rumwe rutivi rwechiso nemuviri ruchatsvuka uye ruchadikitira, nepo rumwe rutivi rusingazodaro.

Horner Syndrome

Ichi chirwere chisingawanzoitiki chetsinga. Chinokanganisa ziso nenyama dzakapoteredza kune rumwe rutivi rwechiso. Chinonziwo 'oculosympathetic palsy'. Chinokonzerwa nekuvharika kwenzira yetsinga kubva kuuropi kuenda kuziso nekumeso. Pano zvakare, divi rechiso rakakanganiswa rinogona kutsvuka.

Chinzvimbo Ndiani ari kukanganiswa? Zvinhu zvikuru Zvechokwadi here?
Chiratidzo cheHarlequin (muvana vachangoberekwa) Vacheche vachangoberekwa vane hutano hwakanaka (inenge 10%) Kutsvuka kwenguva pfupi kune rumwe rutivi rwemuviri. Kwete. Hazvikuvadzi zvachose uye zvinongopera zvega.
Harlequin SyndromeKune chero ani zvake wezera ripi zvaro Kutsvuka uye kudikitira kune rumwe rutivi panguva yekurovedza muviri kana kufara. Zvinoenderana nechikonzero chiripo. Kazhinji hazvikuvadzi.
Horner Syndrome Kune chero ani zvake wezera ripi zvaro Maziso ezasi kune rumwe rutivi rwechiso, ziso diki dema, kudikitira kushoma, uye kutsvuka kwechiso. Chikonzero chikuru (semuenzaniso, bundu) chingave chakakomba. Kuongororwa nachiremba kwakakosha.

Inorapwa sei?

Kurapwa kunoenderana nechikonzero cheHarlequin Sign.

  • Kune vacheche: Hapana mushonga unodiwa. Uchapera wega mumasekonzi mashoma kana maminetsi.
  • Kune Harlequin Syndrome: Kurapwa hakusi chinhu chinodiwa nguva dzose. Dzimwe nguva chirwere ichi chinogona kunaya chega. Zvisinei, kana chiremba wako achifunga kuti kurapwa kwakakosha, achakupa mishonga zvichienderana nechikonzero chacho. Izvi zvinosanganisira:
  • Mushonga unonzi `Stellate ganglion block` unoshandiswa kudzora kusviba kweganda.
  • Majekiseni emuchetura weBotulinum kudzora kudikitira.
  • Kana paine bundu riri pasi, rinogona kubviswa nekuvhiyiwa kana kuburikidza nemwaranzi.
  • Mazano ekurapa kuzvidya mwoyo kwepfungwa kunokonzerwa nekuonekwa uku.
  • Kune Horner Syndrome: Kana pasina kurwadziwa, kurapwa kungasave kwakakosha. Muchiitiko ichi, chiremba acharapa chikonzero chacho.

Unofanira kuona chiremba rini?

Kana iwe kana mumwe munhu wemumhuri mako akaona Harlequin Sign, iyo yakatsvuka, ichiita ziya, uye inopisa kune rumwe rutivi rwemuviri, chinhu chakanakisa chekuita kuona chiremba uye kuongororwa.

Chiremba wako achakuongorora, obvunza nezvezviratidzo zvako, uye kana zvichidikanwa, oita mimwe miedzo kuti aone kana paine zvimwe zvirwere. Kunyangwe zvisingawanzoitiki, zvakakosha kuti uzive kana paine bundu kana chimwe chirwere, sezvo ichi chingave chiri chikonzero.

Kana zviratidzo izvi zvikangoerekana zvauya nezvimwe zviratidzo zvakakomba (semuenzaniso musoro wakakomba, kuchinja kwekuona, kurasikirwa nepfungwa), zvakakosha zvikuru kuenda kuEmergency Department (ETU) yechipatara chiri pedyo nekukurumidza .

Mharidzo Yekuenda Nayo Kumba

  • Chiratidzo cheHarlequin chirwere apo rumwe rutivi rwemuviri kana chiso rutsvuku uye rumwe rutivi ruchena. Izvi hazviwanzo kuva nengozi.
  • Izvi zvinowanzoitika kuvana vachangoberekwa. Zvinopera zvega, mukati memaminitsi mashoma, pasina kurapwa, uye hazvina basa. Yeuka kuti ichi hachisi chirwere chine njodzi che 'Harlequin ichthyosis'.
  • Kana izvi zvikaitika kuvanhu vakuru, zvinogona kunge zviri chiratidzo chedambudziko retsinga dzakadai se'Harlequin syndrome' kana 'Horner syndrome'.
  • Kana iwe kana mwana wako mukaona chiratidzo ichi, kuchenjera kusatya, asi kuona chiremba wenyu kuti aone chikonzero chaicho uye kuona kuti hapana zvimwe zvirwere zvakakomba.

Harlequin Sign, kuchinja kweruvara rweganda, Harlequin Sign, mwana achangoberekwa, Harlequin Syndrome, Horner Syndrome, system yetsinga, system yetsinga inozvimiririra
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Wedzera zvaunofunga

Ndokumbira uverenge: 3 + 7 =
Chiratidzo chinoshamisa apo rumwe rutivi rwemuviri rwakatsvuka uye rumwe rutivi rwakachenuruka (Chiratidzo cheHarlequin)
Zviratidzo2026 Chikunguru 15

Chiratidzo chinoshamisa apo rumwe rutivi rwemuviri rwakatsvuka uye rumwe rutivi rwakachenuruka (Chiratidzo cheHarlequin)

Fungidzira uchitarisa mugirazi woona mutsetse wakatwasuka pakati pechiso chako, rumwe rutivi rutsvuku uye rwakaita ziya, uye rumwe rutivi rwakaita serwakajairika, pamwe rwakachenuruka zvishoma... Hazvisi zvinotyisa uye zvinoshamisa here izvozvo? Kana kuti ko kana ukaona rumwe rutivi rwemuviri wemwana wako achangoberekwa ruchishanduka kamwe kamwe rutsvuku uye rumwe rutivi rwakaita serwakajairika? Izvi ndizvo zvatinodaidza kuti Harlequin Sign in medicine. Sezvo zita racho risinganzwisisike zvishoma, ngationei zvakawanda nezvazvo uye kana ichi chiri chinhu chekutya zvechokwadi.

Chii chaizvo chinonzi Harlequin Sign ichi?

Zvichitaurwa zviri nyore, Harlequin Sign inguva apo rumwe rutivi rwemuviri wako kana chiso chako runosangana nekuchinja kweruvara rweganda (kutsvuka kana kusviba), nepo rumwe rutivi ruchiramba rwakafanana, dzimwe nguva kutotsvuka. Mativi maviri aya anoita seakaparadzaniswa nemutsetse wakatwasuka, pakati pemuviri.

Pamwe chete nemusiyano uyu muruvara rweganda, zvimwe zvinhu zvinogona kuonekwa kumativi ese.

  • Kutsvuka: Nzvimbo iyi inogona kunge iri hyperhidrosis (kudikitira zvakanyanya). Ganda riri panzvimbo iyoyo rinogonawo kunzwa richidziya zvishoma kana rikabatwa.
  • Rutivi Rwakachenuruka/Rwakajairika: Rutivi urwu harudiki. Ganda rinonzwawo richitonhora kana rikabatwa.

Kunyangwe chiratidzo ichi cheHarlequin dzimwe nguva chingave chiratidzo chechirwere chakadai se'Harlequin syndrome', kazhinji kacho hachina njodzi uye chinongopera.

Ndezvipi zvikonzero zvikuru zveizvi?

Hazviwanzoitiki kuwana chikonzero chaicho cheizvi. Chikonzero chikuru cheizvi idambudziko rekutaurirana muhurongwa hwetsinga hwemuviri wedu. Funga nezveizvi sehurongwa hwe "auto-pilot" hwemuviri wedu. Hurongwa uhwu hunodzora zvinhu zvatisingazive kuti tinazvo, zvakaita sekufema kwedu, kurova kwemoyo, uye kudikitira.

Saka, kana paine kuvharika kana kusashanda zvakanaka kwetsinga dzinotumira mashoko kubva kuuropi (hypothalamus) kuburikidza nemutsipa wemusana kuenda kumeso nepamusoro pemuviri, mashoko acho anogona kusatumirwa zvakanaka kudivi rimwe chete remuviri. Ndokusaka mitsipa yeropa iri kudivi rimwe ichikura uye ichitsvuka, ukuwo rimwe divi risingagamuchire mashoko acho uye richiramba rakajairika.

Izvi zvinoitikawo kuvana vacheche vachangoberekwa here?

Ehe, ichi chinhu chinoonekwa muvana vachangoberekwa. Sekureva kweongororo, vanenge 10% vevana vane hutano vanogona kuva nechiratidzo ichi cheHarlequin. Saka, musazvidya mwoyo kana mwana wenyu aine ichi.

Izvi zvinowanzoitika pakati pemazuva maviri kusvika mashanu mwana aberekwa, asi dzimwe nguva zvinogona kuoneka kusvika mavhiki matatu.

Chinhu chinonyanya kukosha ndicho chiratidzo cheHarlequin icho vana vachangoberekwa vane.Hazvikuvadzi zvachose. Kuchinja kweruvara uku kunonyangarika mumasekonzi makumi matatu chete. Dzimwe nguva kunogona kutora kusvika maminetsi makumi maviri. Kunogona kuonekazve kana mwana akaiswa parutivi.

Zvakakosha: Chirwere ichi chinonzi Harlequin Sign hachifanirwe kuvhiringidzwa ne `Harlequin ichthyosis`, chirwere chine njodzi zvikuru, chinotyisidzira hupenyu uye chisingawanzoitiki chemajini. `Harlequin ichthyosis` chirwere umo muviri wese wemwana wakafukidzwa nemakwande akakora, akaita seplate, ane mitswe yakadzika pakati. Chinhu chakasiyana zvachose.

Zvimwe zvirwere zvine chekuita nazvo

Chiratidzo cheHarlequin dzimwe nguva chinogona kuonekwa sechiratidzo chemamwe matambudziko ehutano.

Harlequin Syndrome

Ichi chirwere chinokanganisa sisitimu yedu yetsinga inonzwira tsitsi. Sisitimu iyi yetsinga inodzora mhinduro yedu ye "kurwa-kana-kutiza", inova shanduko dzinoitika mumuviri patinofara, tichitya, kana tichiita maekisesaizi. Pose painoshanda sisitimu iyi mumunhu ane Harlequin Syndrome (semuenzaniso, panguva yekurovedza muviri), rumwe rutivi rwechiso nemuviri ruchatsvuka uye ruchadikitira, nepo rumwe rutivi rusingazodaro.

Horner Syndrome

Ichi chirwere chisingawanzoitiki chetsinga. Chinokanganisa ziso nenyama dzakapoteredza kune rumwe rutivi rwechiso. Chinonziwo 'oculosympathetic palsy'. Chinokonzerwa nekuvharika kwenzira yetsinga kubva kuuropi kuenda kuziso nekumeso. Pano zvakare, divi rechiso rakakanganiswa rinogona kutsvuka.

Chinzvimbo Ndiani ari kukanganiswa? Zvinhu zvikuru Zvechokwadi here?
Chiratidzo cheHarlequin (muvana vachangoberekwa) Vacheche vachangoberekwa vane hutano hwakanaka (inenge 10%) Kutsvuka kwenguva pfupi kune rumwe rutivi rwemuviri. Kwete. Hazvikuvadzi zvachose uye zvinongopera zvega.
Harlequin SyndromeKune chero ani zvake wezera ripi zvaro Kutsvuka uye kudikitira kune rumwe rutivi panguva yekurovedza muviri kana kufara. Zvinoenderana nechikonzero chiripo. Kazhinji hazvikuvadzi.
Horner Syndrome Kune chero ani zvake wezera ripi zvaro Maziso ezasi kune rumwe rutivi rwechiso, ziso diki dema, kudikitira kushoma, uye kutsvuka kwechiso. Chikonzero chikuru (semuenzaniso, bundu) chingave chakakomba. Kuongororwa nachiremba kwakakosha.

Inorapwa sei?

Kurapwa kunoenderana nechikonzero cheHarlequin Sign.

  • Kune vacheche: Hapana mushonga unodiwa. Uchapera wega mumasekonzi mashoma kana maminetsi.
  • Kune Harlequin Syndrome: Kurapwa hakusi chinhu chinodiwa nguva dzose. Dzimwe nguva chirwere ichi chinogona kunaya chega. Zvisinei, kana chiremba wako achifunga kuti kurapwa kwakakosha, achakupa mishonga zvichienderana nechikonzero chacho. Izvi zvinosanganisira:
  • Mushonga unonzi `Stellate ganglion block` unoshandiswa kudzora kusviba kweganda.
  • Majekiseni emuchetura weBotulinum kudzora kudikitira.
  • Kana paine bundu riri pasi, rinogona kubviswa nekuvhiyiwa kana kuburikidza nemwaranzi.
  • Mazano ekurapa kuzvidya mwoyo kwepfungwa kunokonzerwa nekuonekwa uku.
  • Kune Horner Syndrome: Kana pasina kurwadziwa, kurapwa kungasave kwakakosha. Muchiitiko ichi, chiremba acharapa chikonzero chacho.

Unofanira kuona chiremba rini?

Kana iwe kana mumwe munhu wemumhuri mako akaona Harlequin Sign, iyo yakatsvuka, ichiita ziya, uye inopisa kune rumwe rutivi rwemuviri, chinhu chakanakisa chekuita kuona chiremba uye kuongororwa.

Chiremba wako achakuongorora, obvunza nezvezviratidzo zvako, uye kana zvichidikanwa, oita mimwe miedzo kuti aone kana paine zvimwe zvirwere. Kunyangwe zvisingawanzoitiki, zvakakosha kuti uzive kana paine bundu kana chimwe chirwere, sezvo ichi chingave chiri chikonzero.

Kana zviratidzo izvi zvikangoerekana zvauya nezvimwe zviratidzo zvakakomba (semuenzaniso musoro wakakomba, kuchinja kwekuona, kurasikirwa nepfungwa), zvakakosha zvikuru kuenda kuEmergency Department (ETU) yechipatara chiri pedyo nekukurumidza .

Mharidzo Yekuenda Nayo Kumba

  • Chiratidzo cheHarlequin chirwere apo rumwe rutivi rwemuviri kana chiso rutsvuku uye rumwe rutivi ruchena. Izvi hazviwanzo kuva nengozi.
  • Izvi zvinowanzoitika kuvana vachangoberekwa. Zvinopera zvega, mukati memaminitsi mashoma, pasina kurapwa, uye hazvina basa. Yeuka kuti ichi hachisi chirwere chine njodzi che 'Harlequin ichthyosis'.
  • Kana izvi zvikaitika kuvanhu vakuru, zvinogona kunge zviri chiratidzo chedambudziko retsinga dzakadai se'Harlequin syndrome' kana 'Horner syndrome'.
  • Kana iwe kana mwana wako mukaona chiratidzo ichi, kuchenjera kusatya, asi kuona chiremba wenyu kuti aone chikonzero chaicho uye kuona kuti hapana zvimwe zvirwere zvakakomba.

Harlequin Sign, kuchinja kweruvara rweganda, Harlequin Sign, mwana achangoberekwa, Harlequin Syndrome, Horner Syndrome, system yetsinga, system yetsinga inozvimiririra
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Hapana zvakataurwa parizvino. Isa mhinduro yako pano kekutanga.

Wedzera zvaunofunga

Ndokumbira uverenge: 3 + 7 =