Rutivi rwerudyi rwemoyo wemwana wako harusi kukura zvakanaka here? (Hypoplastic Right Heart Syndrome)

Ko kana mwana wako akazvarwa aine dambudziko remwoyo? Fungidzira kuti izvozvo zvingarwadza sei. Vamwe vacheche vanozvarwa vaine rutivi rwerudyi rwemoyo wavo rusingakure zvakanaka. Vanachiremba vanodana izvi kuti Hypoplastic Right Heart Syndrome. Izvi zvinoderedza huwandu hweoxygen hunowanikwa nemwana. Ngatitaurei nezvazvo zvakadzama, handiti?

Chii chinonzi Hypoplastic Right Heart Syndrome?

Zvichitaurwa zviri nyore, Hypoplastic Right Heart Syndrome chirwere chemwoyo chisingawanzoitiki icho vamwe vacheche vanozvarwa nacho . Chinoitika apa ndechekuti zvimwe zvikamu zverutivi rwerudyi rwemoyo wemwana hazvikure zvakakwana. Funga nezvazvo sepombi diki. Rutivi rwerudyi rwemoyo ndirwo runotora ropa risina oxygen mumuviri roritumira kumapapu kuti riwane oxygen. Saka, kana rutivi urwu rwerudyi rusingakure zvakanaka, haruzoiti basa raro nemazvo.

Mumamiriro ezvinhu aya, zvikamu zvinotevera zvemoyo zvinogona kukanganiswa:

• Vharuvhu ine tricuspid: Izvi zvakafanana negedhi riri pakati peatrium yekurudyi neventricle yekurudyi yemoyo. Kana isingashande zvakanaka, inovhara kufamba kweropa.
• Vharuvhu yemapapu: Iyi ndiyo vharuvhu inotangira tsinga yemapapu, inotakura ropa kubva ku ventricle yekurudyi kuenda kumapapu.
• Vhiki rekurudyi: Iyi ndiyo nzvimbo huru yekupomba ropa kurudyi rwemoyo. Kana ikaita diki, inopomba ropa shoma.
• Tsinga yemapapu: Iyi ndiyo tsinga huru inotakura ropa kubva ku right ventricle kuenda kumapapu.

Zvichienderana nekuti chirwere chacho chakanyanya sei kana kuti chakanyanya kuderera, mashandiro ezvikamu izvi zvemoyo anogona kudzikira kana kuwedzera.

Dzimwe nguva, vacheche vane HRHS vanogonawo kuva nezvimwe zvirwere zvemwoyo. Semuenzaniso:

• Atrial septal defect (ASD): Buri riri pamadziro pakati pemakamuri maviri epamusoro (atria) emwoyo.
• Kukanganisika kwetsinga dzemudumbu (VSD): Buri riri pakati pemakamuri maviri epasi (maventricles) emwoyo.
• Kukanganisika kwemugero weAtrioventricular: Buri guru riri pakati pemoyo pamwe chete nezvimwe zvinetso zvakawanda.

Mamiriro ezvinhu aya akakomba zvakadini?

Hypoplastic right heart syndrome (HRHS) inogona kuva yakakomba kune vamwe vanhu kupfuura vamwe . Vanhu vane zvirwere zvakakomba, zvakaita semhepo yakaderera , vanoda kurapwa nekukasika . Zvisinei, vamwe vanhu vangave vasina chirwere ichi chakakomba, vaine matambudziko madiki chete. Vanhu vakadaro vanogona kusaonekwa kusvika vakura.

Dambudziko iri rakajairika zvakadii?

Izvi hazviwanzoitiki zvechokwadi.Vaongorori vanofungidzira kuti vanhu vashoma pane 50,000 muUnited States vane HRHS. Izvi hazviwanzoitiki kupfuura Hypoplastic Left Heart Syndrome, chirwere chekuti divi rekuruboshwe remoyo harikure zvakanaka.

Ndezvipi zviratidzo zve hypoplastic right heart syndrome (HRHS)?

Zviratidzo zvechirwere ichi zvinotevera:

• Kuchinja ruvara rwebhuruu rweganda remaoko netsoka. Izvi zvinonzi cyanosis . Zvinoreva kuti muviri hausi kuwana oxygen yakakwana.
• Kutadza kufema zvakanaka. Izvi zvinonzi dyspnea .
• Kufema nekukurumidza. Izvi zvinonzi tachypnea .
• Mwana haasi kunwa mukaka nemazvo.
• Kukurumidza kuneta, kunzwa hope nguva dzese.

Kana mwana wako aine chimwe chezviratidzo izvi kana kupfuura, zvakanaka kuti uone chiremba nekukasika.

Chii chinokonzera izvi?

Kutaura zvazviri, chikonzero chaicho che hypoplastic right heart syndrome (HRHS) hachisati chawanikwa .

Zvisinei, vaongorori vanotenda kuti majini anogona kunge aripo , sezvo vanhu vakawanda vemumhuri imwe chete vakashumwa kuti vane HRHS pakuzvarwa. Saka, tsvakiridzo yakawanda inodiwa.

Ndezvipi zvimwe zvinetso zvinogona kukonzera izvi?

Hypoplastic Right Heart Syndrome (HRHS) inogona kukonzera matambudziko akadai se:

• Mwero weokisijeni wakaderera mumuviri. Izvi zvinonzi hypoxemia .
• Kukundikana kwemoyo kurudyi.
• Kurova kwemoyo kusina kurongeka. Izvi zvinonzi arrhythmia .

Pazera diki, kunyangwe kune avo vasina kubatwa zvakanyanya neHRHS, kubvisa pamuviri kunogona kuitika nekuda kwekushomeka kweoxygen mumuviri.

Chirwere ichi chinoonekwa sei?

Dzimwe nguva, chiremba anogona kuona HRHS mwana achiri mudumbu (kukura kwemwana asati azvarwa) . Vanoshandisa ultrasound scan kuti vaone moyo wemwana. Kana uchida kunyatsoongorora, unogona zvakare kuita fetal echocardiogram . Miedzo iyi yese haipindi muropa.

Ndezvipi bvunzo dzinoitwa mushure mekuzvarwa kwemwana?

Mushure mekunge mwana azvarwa, bvunzo idzi dzisingapindi mumuviri dzinogona kuitwa kuti uone kana mwana ane HRHS:

• Pulse oximeter (pulse ox): Ichi chishandiso chidiki chakaita seclip chinoyera huwandu hweokisijeni nekuchibatanidza pamunwe wako kana nzeve.
• Electrocardiogram (EKG/ECG): Muedzo unoyera mashandiro emagetsi emwoyo.
• Echocardiogram (Echocardiogram - echo): Iyi bvunzo inoshandisa mafungu eruzha, akafanana neultrasound, kutora mifananidzo yemoyo. Inogona kuratidza chimiro chemoyo, mashandiro anoita mavharuvhu, uye kuti ropa rinoyerera sei.
• MRI yemwoyo (Magnetic Resonance Imaging): Inoshandisa magineti nemasaisai eredhiyo kugadzira mifananidzo yakadzama yemoyo.

Ndezvipi zvinorapwa izvi?

Hypoplastic Right Heart Syndrome (HRHS) inogona kurapwa nemishonga, nzira dzisinganyanyi kupindira mumuviri, kana kuvhiyiwa . Chinangwa chikuru chekurapa uku ndechekubatsira mapapu emwana kuwana ropa neoxygen yakakwana .

Mushonga

• Prostaglandin inoshandiswa kubatsira kuchengetedza ductus arteriosus yemwana yakavhurika. Iyi ductus arteriosus ichubhu inoshandiswa nemwana kugamuchira ropa rine oxygen kubva kuna amai vari mudumbu. Mwana paanotanga kufema nemapapu mushure mekuzvarwa, chubhu iyi inowanzovhara mukati memazuva mashoma. Zvisinei, mumwana ane HRHS, nekuti rutivi rwerudyi rwemoyo harusi kushanda zvakanaka, kuchengetedza chubhu iyi yakavhurika kunobatsira kuti ropa rifambe kuenda kumapapu.

Maitiro asinganyanyi kupindira

• Chiremba anogona kushandisa chubhu diki inonzi catheter kuisa stent (chubhu diki yakaita sesimbi) mu ductus arteriosus yemwana. Izvi zvinoita kuti ductus arteriosus irambe yakavhurika uye zvinoita kuti ropa rifambe zvakanaka kuenda kumapapu.
• Chimwe chinhu chekuboorwa kwevharuvhu remapapu . Muizvi, catheter inopfuudzwa nemutsinga weropa ichipinda muvharuvhu remapapu risingavhurike zvakanaka, zvichiita kuti pave neburi muvharuvhu. Izvi zvinoita kuti ropa rifambe richipinda mutsinga dzemapapu. Vamwe vanachiremba vanoshandisawo nzira inonzi ablation .

Kuvhiya

Nyaya dzakakomba dzeHRHS dzinoda kuvhiyiwa kuti dzirapwe. Izvi zvinowanzoitwa muzvikamu zvakasiyana-siyana.

• Blalock-Taussig-Thomas (BTT) shunt: Iyi inoshandiswa kudzorera kuyerera kweropa mumapapu emwana ane HRHS. Inoshandisa jira rekugadzira kugadzira kubatana pakati pe subclavian artery (tsinga iri mucollarbone) nepulmonary artery.
• Mushure memwedzi mishoma kana makore, chiremba anogona kuita chirongwa cheGlenn uye/kana chirongwa cheFontan . Imwe neimwe yeiyi nzira inogadzira nzira itsva yekuti ropa riyerere richitenderedza ventricle yekurudyi isina kushanda zvakanaka. Kazhinji, ventricle yekurudyi inopomba ropa mutsinga dzemapapu.

Maitiro aGlenn naFontan anobvumira ropa kuti riyerere zvakananga kubva mutsinga huru kuenda mutsinga yemapapu, kubva kwarinoenda kumapapu kunotora okisijeni.

Pane matambudziko aripo here pakurapwa?

Sekunge kune mamwe maoparesheni, pane zvimwe zvinetso zvinogona kuitika pakurapa uku. Matambudziko anogona kusiyana zvichienderana nekurapwa. Semuenzaniso:

• Stent inogona kufamba kubva panzvimbo yayo yekutanga.
• Kuvhiyiwa kweBTT shunt kunogona kukonzera kuti mitsipa yeropa itetepe kana kukuvadza tsinga.
• Kuboorwa kwevharuvhu yemapupa kunogona kukonzera kurova kwemoyo kusina kurongeka (arrhythmia) kana kukanganisa tsinga yeropa.
• Kuvhiyiwa kukuru kunogona kukonzera BP yakakwira, kubuda kweropa muropa, kumira kwemoyo, chirwere cheitsvo kana chechiropa, kana kurova kwemoyo kusina kurongeka.

Asi musazvidya moyo. Vanachiremba vachakuzivisai nezve zvese izvi uye vachatora matanho anodiwa.

Zvinotora nguva yakareba sei kuti upore?

Nguva yekupora inosiyana zvichienderana nekurapwa. Kuvhiyiwa kukuru kunotora nguva yakareba. Mwana wako anogona kugara muchipatara kwemazuva akati wandei, zvichida anopfuura vhiki. Achafanira kutariswa zvakanyanya mushure mekunge adzokera kumba.

Chii chandingatarisira kana mwana wangu ari mudambudziko iri?

Nekuda kwekudzikira kweoxygen mumuviri, vanhu vane hypoplastic right heart syndrome (HRHS) vanogona kusangana nematambudziko akadai se:

• Nyaya dzemutauro.
• Matambudziko ekurangarira.
• Kuwanda kwenjodzi yekurwara nemwoyo, chiropa, kana itsvo kana munhu akwegura.
• Matambudziko epfungwa kana matambudziko ekuzvidya mwoyo.
• Kuomerwa nekuronga chimwe chinhu kana kugadzirisa dambudziko.

Asi, kune nyanzvi dzekubatsira pane zvese izvi. Saka musazvidya mwoyo.

Chii chinonzi fungidziro yechirwere ichi?

Kashoma kuti vanhu vane chirwere chemwoyo chinonzi hypoplastic right heart syndrome (HRHS) vararame kusvika vakura vasina kuvhiyiwa . Zvisinei, vanhu vane chirwere ichi vasinganyanyi kurwara vanogona kusaziva kuti vane chirwere ichi kusvika vakura.

Unotarisira sei mwana ane HRHS?

Kutarisirwa kunodiwa nemwana wako kunoenderana nekuti chirwere chake chakanyanya sei . Kana akavhiyiwa mushure mekusununguka, anofanira kutariswa zvakanyanya mushure mekunge asvika kumba. Chiremba wako kana nyamukuta achakupa mazano akanaka ekuti ungachengeta sei mwana wako.

Unofanira kuona chiremba rini?

Mwana akavhiyiwa anofanira kuona chiremba kuti aonekwe nguva yekutevera . Vachakuudza zvekungwarira uye zvekutaurira chiremba nekukurumidza kana ukaona chero chinhu. Kana uine mibvunzo kana zvinokunetsa nezvemamiriro emwana wako, fonera chiremba nekukurumidza.

Kana mwana wako aine matambudziko ekudzidza kana kudzora manzwiro ake, unogona zvakare kuwana dzimwe nyanzvi dzinogona kubatsira munzvimbo idzodzo. Chiremba wako ndiye achapa gwara rinodiwa.

Mibvunzo ipi yandinofanira kubvunza chiremba?

Heano mimwe mibvunzo yaunogona kubvunza chiremba wemwana wako:

• Mwana wangu anofanira kuvhiyiwa here?
• Unofanira kuvhiyiwa kwenguva yakareba sei?
• Kuvhiyiwa kungani kuchadiwa, uye kuchaitwa riini?
• Mwana wangu ane tarisiro ipi nedambudziko iri?

Ndinonzwisisa kuti zvakaoma sei kuziva kuti mwana wako ane chirwere chemwoyo. Zvisinei, vana vanozvarwa nhasi vane mishonga yaisawanikwa kuzvizvarwa zvakapfuura. Ndiwe munhu akasimba kwazvo waunogona kuva mwana wako panguva ino. Dzidza nezveHRHS. Bvunza chiremba wako nezvechero chinhu chisina kujeka. Taura nachiremba wako kuti usarudze chakanakira mwana wako.

Chekupedzisira, yeuka izvi (Mharidzo Yekuenda Kumba)

Hypoplastic Right Heart Syndrome (HRHS) chirwere chisingawanzoitika chinoberekwa vana, uko rutivi rwerudyi rwemoyo rusingakure zvakanaka. Izvi zvinoderedza huwandu hweokisijeni hunogamuchirwa nemuviri. Kuongororwa nekukurumidza uye kurapwa kwakakodzera (mishonga, kuvhiyiwa kudiki, kana kuvhiyiwa kukuru) zvinogona kuvandudza hupenyu hwemwana . Mumamiriro ezvinhu akadaro, zvakakosha kuti iwe semubereki uzive uye ushande pamwe chete navanachiremba vako. Yeuka, hausi wega. Unogona kuwana rubatsiro rwaunoda.

` Hypoplastic Right Heart Syndrome, HRHS, Chirwere cheMwoyo cheVacheche, Zvirwere zveMwoyo zveVacheche, Cyanosis, Kuoma Kwekufema, Kuvhiyiwa kweMwoyo