Wake waphawula ukuthi amehlo engane yakho aqhelelene kancane kunokujwayelekile? Noma ingabe udokotela ukutshelile ngakho? Ngokwezokwelapha, lesi simo sibizwa ngokuthi i-Orbital Hypertelorism . Ngezinye izikhathi sibizwa nangokuthi i-Ocular Hypertelorism. Nakuba la mazwi engase esabise, lokhu akukubi njengoba sicabanga. Namuhla, sizokhuluma ngalokhu kalula, ngendlela ongayiqonda.
Kuyini ngempela i-Orbital Hypertelorism?
Kalula nje, i-Orbital Hypertelorism ayisona isifo esihlukile. Ngokuvamile ivela njengophawu lwesinye isici sokuzalwa noma ukuphazamiseka kofuzo.
Cabanga ngakho, lapho umntwana esesiswini, amathambo obuso bakhe aqala ukuma kancane kancane. Ngalesi sikhathi, izimbobo ezimbili zamehlo ezigcina amehlo akhe zibekwe kude kancane kunokujwayelekile. Ngakho-ke, igebe eliphakathi kwamehlo libonakala kakhulu kunasenganeni evamile. Lesi sikhala esandisiwe sigcwele ithambo elengeziwe.
Into ebalulekile ukuthi iningi lezingane ezinamahlo aqhelelene kangaka ngeke zibe nezinkinga zokubona. Ukuthi umbono uyathinteka yini kuncike ekutheni amehlo aqhelelene kangakanani nokuthi yiziphi ezinye izimpawu ingane enazo.
Odokotela bakuthola kanjani lokhu ngqo?
Ngokuvamile, udokotela uxilonga lesi simo ngokushesha nje lapho umntwana ezalwa. Ngezinye izikhathi, singabonakala ngisho nangesikhathi sokuhlolwa kwe-ultrasound ngesikhathi umntwana esesesibelethweni.
Akukho banga elibekiwe phakathi kwamehlo, kodwa odokotela basebenzisa izilinganiso ezimbili eziyinhloko ukuze bathole lokhu.
| Indlela yokulinganisa | Kuchazwe kalula |
|---|---|
| Ibanga Langaphakathi Le-Canthal | Ibanga ukusuka ekhoneni leso elilodwa eliseduze nekhala kuya ekhoneni lelinye iso eliseduze nekhala. |
| Ibanga Lomfundi | Ibanga ukusuka enkabeni yempuphu yeso elilodwa kuya enkabeni yempuphu yeso lelinye. |
Zombili lezi zilinganiso ziphakeme kunezivamile ezinganeni ezine-orbital hypertelorism.
Kungani lokhu kwenzeka? Yiziphi izizathu eziyinhloko?
Odokotela bakholelwa ukuthi isisekelo salesi simo sibekwa phakathi kwesonto lesine nelesishiyagalombili lokukhula komntwana. Cabanga ngamathambo ekhanda lomntwana njengezingcezu zephazili enobukhulu obuthathu (3D) ezihlangana. Uma kukhona ukuphazamiseka noma ushintsho ezinyathelweni ezihilelekile ekuhlanganiseni lezi zingcezu, amasokhethi amabili amehlo angaphazamiseka futhi aqhelelane kakhulu.
Izizathu ezimbili eziyinhloko zalokhu yilezi:
1. Ukukhubazeka kokuzalwa
2. Izinkinga zofuzo
1. Izimo zokuzalwa
Iphutha lokuzalwa liwukungajwayelekile ekubukekeni, ezithweni zangaphakathi, noma ezinqubweni zamakhemikhali zomzimba womntwana lapho ezalwa. Lokhu kungabangelwa yi:
- Izici zofuzo kanye nefa.
- Ezinye izifo ezitholwa ngumama ngesikhathi sokukhulelwa.
- Ukuchayeka emisebeni.
- Ukusetshenziswa kwezidakamizwa noma utshwala ngesikhathi sokukhulelwa.
Ngezinye izikhathi ukukhubazeka kokuzalwa kungenzeka ngaphandle kwesizathu esicacile, ngisho noma kungahleliwe. I-Craniosynostosis ingenye yalezi zinkinga zokuzalwa. Okwenzekayo lapha ukuthi izicubu ezixhumanisa amathambo ekhanda lomntwana ziyahlangana. Lokhu kungabangela ne-Orbital Hypertelorism.
2. Izinkinga zofuzo
Izakhi zofuzo ziyiyunithi ezincane ze-DNA ezinikeza imiyalelo kumaseli emzimbeni wethu. Ukuguquka kwezakhi zofuzo kulezi zakhi zofuzo kungabangela izifo zofuzo. Ezinye zezifo zofuzo ezingabangela i-orbital hypertelorism yilezi:
- I-Apert syndrome
- I-DiGeorge syndrome
- Isifo sika-Edwards
- I-Crouzon syndrome
- I-Noonan syndrome
- Uhlobo 1 lwe-Neurofibromatosis
Uma ingane yakho inalesi simo, udokotela wakho angakuthumela ukuze uthole ukwelulekwa ngofuzo, okungakusiza ukuthi uqonde kabanzi ngengozi yomndeni wakho yokuthola izifo zofuzo.
Yiziphi izindlela zokwelapha lokhu?
Izingane ezinalesi simo zingabuyiswa amehlo azo ngokuhlinzwa. Lokhu kubizwa ngokuthi ukuhlinzwa okuvuselelayo . Lokhu kuhlinzwa kuvame ukwenziwa lapho ingane ineminyaka ephakathi kwemi-5 neyi-7 ubudala. Lokhu kuhlinzwa kunikeza ingane ukubukeka okuvamile futhi kunciphisa ibanga phakathi kwamehlo.
Ingane yakho izodinga ukuhlolwa kwamehlo njalo ngaphambi nangemva kokuhlinzwa ukuze kuqashwe izinguquko emehlweni nasembonweni.
Odokotela abahlinzayo basebenzisa kakhulu izindlela ezimbili zokuhlinzwa kulokhu.
| Uhlobo lokuhlinzwa | Kwenzekani? |
|---|---|
| I-Box Osteotomy | Lapha, udokotela ohlinzayo ususa ithambo nesikhumba esingaphezulu kwekhala bese elungisa kabusha amasokhethi amehlo ukuze angene kuleso sikhala. Cabanga usika ingxenye eyisikwele emashiya nangaphezu kwekhala, bese uletha amasokhethi amehlo kuleso sikwele. |
| Ukuhlukanisa Ubuso | Lokhu ukuhlinzwa okuyinkimbinkimbi kancane. Kwenziwa ezinganeni ezine-orbital hypertelorism kanye nezinye izinkinga zamathambo obuso (isb., umhlathi, amathambo ezihlathi). Kuhilela ukubumba kabusha amasokhethi amehlo, impumulo, namathambo ezihlathi ukuze kuhlanganiswe amehlo, kuyilapho kulungiswa nezinkinga zomhlathi namazinyo. |
Izinkinga ezingaba khona ngemva kokuhlinzwa
Njenganoma yikuphi ukuhlinzwa, kunezingozi ezincane kakhulu ezihilelekile. Lezi zifaka:
- Ukopha
- Izifo
- Izibazi
- Ijwabu leso eligobile ( i-Ptosis )
- I-Diplopia (ukubona okuphindwe kabili)
- Ukulahlekelwa umbono noma ubumpumputhe (lokhu akuvamile kakhulu)
Udokotela wakho ohlinzayo uzochaza lezi zingozi ngokuningiliziwe.
Kufanele ubonane nini nodokotela?
Uma ubona noma yiziphi izinguquko emehlweni noma embonweni wengane yakho, bonana nodokotela wakho ngokushesha.
Futhi, uma ingane yakho ithola noma yiziphi izimpawu ezilandelayo, shesha uye eMnyangweni Wezimo Eziphuthumayo (ETU) wesibhedlela esiseduze.
- Ukulahlekelwa noma ukuncipha kombono ngokuzumayo.
- Ubuhlungu obukhulu emehlweni.
- Ukubona ukukhanya okusha noma ukuntanta phambi kwamehlo.
Khumbula, ukuthi nje ingane izalwa ine-Orbital Hypertelorism akusho ukuthi ngeke ikhule iphilile futhi iphile kahle njengabanye abantwana. Kuye ngesimo esiyisisekelo esibangele lokhu, ingane yakho ingadinga ukwelashwa isikhashana. Khuluma nodokotela wakho ngakho.
Umlayezo Wokuya Nawe Ekhaya
- I-Orbital Hypertelorism ayisona isifo esihlukile. Kuwuphawu lwesinye isici sokuzalwa noma isimo sofuzo.
- Izingane eziningi ezinalesi simo azinazo izinkinga zokubona.
- Uma ingane isineminyaka engaba ngu-5-7 ubudala, ukuhlinzwa kungenziwa ukuze amehlo abuyele esikhaleni sawo esijwayelekile.
- Uma ingane yakho inalesi simo, ungesabi ukukhuluma ngokukhululekile nodokotela wakho futhi uthole iseluleko nokwelashwa okudingekayo.
- Kubaluleke kakhulu ukubonana nodokotela ngesikhathi futhi uhlolwe amehlo.
👩🏽⚕️ Imibuzo eyengeziwe (ama-FAQ)
💬 Uhlobo luni lwesimo i-Orbital Hypertelorism?
Lokhu akulona ushintsho olujwayelekile ekubukekeni! 'I-Orbital Hypertelorism' iyisici sofuzo/sokuzalwa esenzeka lapho ugebhezi lomntwana kanye namathambo azungeze amehlo (ama-orbits) kukhula esibelethweni, okwenza ibanga phakathi kwamehlo libe kude kakhulu/ngokungavamile. Lokhu akusona isifo samehlo, kodwa inkinga ngohlaka lobuso!
💬 Yiziphi izimbangela eziyinhloko zokuthi amehlo engane aqhelelene kakhulu (i-Orbital Hypertelorism)?
Lokhu akusona isifo esivame ukwenzeka sodwa, kodwa kuyisici esiyinhloko se-'Genetic Syndromes' eyingozi kakhulu! Ezifweni ezinzima njenge-'Apert Syndrome', 'Crouzon Syndrome' kanye ne-'DiGeorge Syndrome', la mathambo ayaqhuma ngenxa yezinkinga ekhanda. Ngezinye izikhathi, isimila esikhula ebusweni ngesikhathi sisesibelethweni (encephalocele) singabangela nokuthi amehlo aqhuma.
💬 Yiziphi ezinye izimpawu eziyingozi izingane ezinamehlo akude ezibhekana nazo futhi yikuphi ukuhlinzwa okungenziwa ukuze kuphulukiswe lokhu?
Ngokuvamile, laba bantwana banezinkinga zokubona, ukukhubazeka kwengqondo, ukukhubazeka kwenhliziyo, kanye nezifo ezibulalayo ezifana ne-cleft palate. Ukuze belaphe lokhu, lapho ingane ineminyaka engaba ngu-5-8 ubudala, kufanele ihlinzwe kakhulu futhi iyinkimbinkimbi (Craniofacial reconstruction / Facial Bipartition) lapho kunqunywa khona ugebhezi, ubuchopho bugcinwa, iso liyanqunywa futhi lisondezwe eduze, bese ubuso bakhiwa kabusha.











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