Ingabe uvame ukuba nomkhuhlane, ukukhwehlela, noma okunye ukungakhululeki esiswini? Ngezinye izikhathi sicabanga ukuthi "kungenye nje inkinga." Kodwa kwabanye abantu, uma lezi zinto zenzeka njalo, sidinga ukucabanga ngembangela eyinhloko. Namuhla sizokhuluma ngesimo esikhethekile kancane, kodwa abantu abaningi abazi ngaso. Lokho ukuntuleka kwe-IgA okukhethiwe, noma `(Ukuntuleka kwe-IgA okukhethiwe)`.
Kuyini ukuntuleka kwe-IgA okukhethiwe?
Kalula nje, imizimba yethu inesimiso somzimba sokuzivikela ezifweni. Isosha elibalulekile kulesi simiso yiprotheni ebizwa ngokuthi i-immunoglobulin A, noma i-IgA. Le phrotheni ihlala ezithweni zethu zomoya, amehlo, umlomo, kanye nomgudu wokugaya ukudla (njengamathumbu), isivikela kumagciwane azama ukungena.
Manje, uma umuntu ene-protein ye-IgA encane kakhulu noma engenayo nhlobo emzimbeni wakhe, khona-ke leso simo sisibiza ngokuthi i-Selective IgA Deficiency. Igama elithi "selective" lisetshenziswa ngoba lithinta i-IgA kuphela. Lokhu kubhekwa njengesifo sokuntuleka kwamasosha omzimba. Ngezinye izikhathi uzosibona sifinyeziwe njenge-SIgAD.
Kungani lokhu kwenzeka? Iyini imbangela?
Esikhathini esiningi, lesi simo esibizwa ngokuthi i-Selective IgA Deficiency sizuzwa njengefa . Lokho kusho ukuthi, uma othile emndenini enalesi simo sokuntuleka kwe-`(IgA)`, noma enenye inkinga yesistimu yomzimba, kunethuba lokuthi nabanye bazosithola. Cabanga nje, uma umama noma ubaba enalesi simo, nezingane zingasithola.
Ziyini izimpawu zalesi simo?
Nansi into emangalisayo! Abantu abaningi banalokhu `(Selective IgA Deficiency)`, kodwa ababonisi zimpawu. Ngezinye izikhathi kutholakala ngengozi lapho behlolwa esinye isifo.
Kodwa-ke, phakathi kuka-25% no-50% wabantu bangase babe nezinkinga ezithile. Abanye balaba bantu bangase babe nokutheleleka okuvamile. Izindawo ezivame kakhulu zokutheleleka yilezi:
- Umgudu wokuphefumula (izindlela zokuphefumula emaphashini) - izinto ezifana ne-phlegm evame ukuvela, ukukhwehlela, i-bronchitis.
- Ama-sinuses - i-sinusitis evame ukwenzeka.
- Izindlebe - njengezifo zendlebe.
- Izilonda zomlomo, isifo sezinsini.
- Amehlo - Amehlo abomvu, izifo.
- Isistimu yokugaya ukudla (isisu) - izinto ezifana nokuphazamiseka kwesisu, uhudo.
Cabanga nje, unomngane ohlushwa umphimbo obuhlungu noma ikhala eligobhozayo cishe kanye ngenyanga. Noma ubelokhu enenkinga yokuzwa kusukela ebuntwaneni. Mhlawumbe lokhu kuntuleka kwe-`(IgA)` kuyimbangela yezinto ezinjalo.
Sivame kangakanani lesi simo?
Ukuntuleka kwe-IgA okukhethiwe kuvame kakhulu kubantu bomdabu baseYurophu (abaseCaucasus). Ngokwezinye izifundo, cishe umuntu oyedwa kwabangu-500 angaba nalesi simo. Kodwa-ke, lokhu kungahluka kuye ngezindawo nangobuzwe. Kunolwazi oluncane lokuthi kuvame kangakanani ezweni lethu.
Ubani osengozini enkulu yalokhu?
Njengoba kushiwo ngaphambili, uma othile emndenini wakho enalesi simo sokuntuleka kwe-`(IgA)` noma inkinga efanayo yesimiso somzimba sokuzivikela, usengozini enkulu yokuthola lesi simo. Yingakho kubalulekile ukwazi umlando wezokwelapha womndeni wakho.
Odokotela bakuthola kanjani lokhu? (Ukuxilongwa)
Odokotela bezifo zomzimba ngokuvamile yibo abahlola lokhu. Uma unezifo ezivame ukutheleleka noma usola ukuthi unesifo sokuzivikela komzimba, udokotela wakho angase akucele ukuba uhlolwe igazi. Uma ukuhlolwa kubonisa amazinga aphansi e-IgA, ungase utholakale une-Selective IgA Deficiency.
Ngokuvamile, lapho kuhlolwa igazi ukuze kutholakale esinye isifo, njengesifo se-celiac, le IgA ephansi itholakala ngengozi.
Yiziphi izindlela zokwelapha lokhu?
Into ebalulekile lapha ukuthi i-Selective IgA Deficiency ayikwazi ukwelapheka ngokuphelele. Kodwa ungakhathazeki! Lesi simo singalawulwa. Odokotela belapha ezinye izimo ezibangelwa yilokhu kuntuleka kwe-`(IgA)`. Isibonelo, uma uthola ukutheleleka ngamagciwane, bangakunikeza ama-antibiotic.
Kunezindaba ezinhle! Ezinye izingane ezincane zingakhula zidlule kulesi simo eminyakeni embalwa yokuqala yokuphila, okusho ukuthi amazinga azo e-IgA angabuyela esimweni esijwayelekile. Ngakho-ke uma lokhu kutholakala kusenesikhathi, odokotela bazobe beqaphile.
Yiziphi ezinye izinkinga ezingabangelwa yilokhu?
Iningi labantu abanesifo sokuntuleka kwe-IgA esikhethiwe baphilile ngaphandle kwezinkinga ezinkulu. Kodwa-ke, abanye abantu bangase babe nezifo ezivame kakhulu noma ezinzima. Abantu abanalesi simo nabo basengozini enkulu yokungezwani komzimba , okuyimiphumela engavamile ezintweni ezisendaweni noma ekudleni, kanye ne-asthma , okuwukuvuvukala kwemigudu yomoya emaphashini.
Ngaphezu kwalokho, abanye abantu bangase babe nezinkinga zokuzivikela komzimba . Lokhu kusho ukuthi amasosha omzimba ahlasela amangqamuzana awo aphilile. Ezinye zalezi zifo zifaka:
- Isifo se-Celiac: Lokhu kwenzeka uma udla ukudla okuqukethe i-gluten (iphrotheni etholakala kokusanhlamvu okufana nokolweni nebhali), elimaza amathumbu akho amancane. Kunjengokungathi amathumbu akho azwela lokho kudla.
- Isifo samathumbu esivuvukalayo (IBD): Lokhu kubangela ukuvuvukala kanye nomonakalo ohlelweni lokugaya ukudla, ikakhulukazi amathumbu. Izibonelo zifaka phakathi i-ulcerative colitis kanye nesifo sikaCrohn.
- I-rheumatoid arthritis: Lokhu kubangela ukuvuvukala kwamalunga, okusho ukuvuvukala nobuhlungu.
- I-Lupus: Lesi yisimo lapho amasosha omzimba ehlasela khona izicubu ezinempilo. Singathinta izindawo eziningi, okuhlanganisa isikhumba, amalunga nezinso.
Akuvamile kakhulu, umuntu onesifo sokuntuleka kwe-IgA esikhethiwe angaba nokusabela okubi kakhulu okusongela impilo okubizwa ngokuthi i-anaphylaxis uma enikwa igazi noma imikhiqizo yegazi equkethe i-IgA. Nakuba lokhu kungavamile kakhulu, kubalulekile ukukuqaphela. Ngakho-ke uma unalesi simo, kubaluleke kakhulu ukutshela umhlinzeki wakho wezempilo.
Ingabe lokhu kungavinjelwa?
Ngenxa yokuthi kuyifa, ukuntuleka kwe-IgA okukhethiwe akunakuvinjelwa.
Iyini inkomba yokubikezela kubantu abanalesi simo?
Umbono wabantu abane-Selective IgA Deficiency uyahlukahluka kuye ngomuntu, kodwa ngokuvamile muhle. Iningi labantu liphila impilo evamile.
Nokho, njengoba kushiwo ngaphambili, abanye abantu bangaba nezinye izifo ezinkulu ngenxa yalesi simo. Ezimweni eziningi, lesi yisimo sokuphila konke. Kodwa-ke, njengoba kushiwo ngaphambili, ezinye izingane ezincane zingasinqoba ngokuphelele lesi simo eminyakeni embalwa yokuqala.
Kufanele ngimbone nini udokotela ngalokhu?
Uma unezifo ezivame ukwenzeka noma eziphindaphindayo (isibonelo, i-pneumonia njalo ezinyangeni ezimbalwa, izifo ze-sinus izikhathi eziningana ngonyaka), tshela udokotela wakho. Angenza ukuhlolwa kwegazi ukuze abone ukuthi unesifo sokuntuleka kwe-IgA esikhethiwe noma enye inkinga yesistimu yomzimba.
Yimiphi imibuzo okufanele uyibuze udokotela ngalokhu?
Uma kutholakale ukuthi une-Selective IgA Deficiency, ungase ufune ukubuza udokotela wakho imibuzo efana nalokhu:
- Sibi kangakanani lesi simo esibizwa ngokuthi i-Selective IgA Deficiency?
- Yiziphi izinkinga okufanele ngikhathazeke ngazo kakhulu?
- Ingabe kufanele ngigqoke into efana nesongo "se-Medic Alert" ukuze ngiqaphelise ngalesi simo? (Ikakhulukazi uma kucatshangelwa ingozi ye-anaphylaxis).
Ngingaqhubeka nomsebenzi wami njengenjwayelo?
Ezimweni eziningi, i-Selective IgA Deficiency ayiphazamisi impilo yansuku zonke. Uma uthola ukutheleleka, udokotela wakho uzokutshela ukuthi kufanele ugweme isikhathi esingakanani imisebenzi ethile ngemva kokwelashwa.
Masikhumbule izinto ezibaluleke kakhulu (Umyalezo Wokuya Ekhaya)
Kulungile, ake siphinde sixoxe ngezinto ezibaluleke kakhulu esikhulume ngazo mayelana nokuntuleka kwe-IgA okukhethiwe:
- Abantu abaningi abanazo izimpawu: Abantu abaningi abanalesi simo bahlala bephilile bengazi.
- Qaphela izifo ezivame ukwenzeka: Uma ugula njalo, khuluma nodokotela.
- Nakuba ingelapheki, ingalawulwa: Ingalawulwa ngokwelapha izifo nokuqapha izinkinga.
- Ezinye izinkinga zingase zibe khona: Qaphela ukungezwani komzimba, i-asthma, kanye nezifo ezihlasela amasosha omzimba.
- Izingane ezincane zingalulama: Ezinye izingane zikhula zidlule kulesi simo njengoba zikhula.
- Kubalulekile ukuqaphela lapho unikela ngegazi: Uma unalesi simo, yazisa odokotela bakho.
Ngakho-ke, ngithemba ukuthi lolu lwazi luwusizo kuwe. Ukuqaphela izinto ezinjengalezi kusisiza ukuthi sinakekele impilo yethu kanye nempilo yabathandekayo bethu, akunjalo?
Ukuntuleka kwe - IgA okukhethiwe, ukuntuleka kwe-IgA, amasosha omzimba, izifo, izifo zokuzivikela komzimba, izakhi zofuzo, ukuhlolwa kwegazi

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