So wowɔ hemophilia B? Momma yɛnka Factor IX ho asɛm! (Ade a Ɛto so IX Nneɛma a Wɔde Yɛ Adwuma) .

So wuhu sɛ wowɔ tebea bi a sɛ wotwa wo ho ketewaa bi mpo a, ɛma mogya tu wo a wuntumi nni so? Ebia wowɔ mogya a ɛtwetwe ho haw te sɛ Hemophilia B. Ɛnnɛ yɛrebɛka aduru titiriw bi a ɛboa yɛn nipadua wɔ nsɛm a ɛtete saa mu ho asɛm. Ɛyɛ aduru a wɔde bɔ nkurɔfo ho ban a wɔfrɛ no Factor IX. Sɛ wote eyi a, mma wo ho nnsuro. Momma yɛnte eyi ho biribiara ase kɛkɛ.

Dɛn ne Factor IX?

Sɛ yɛbɛka no tiawa a, Factor IX yɛ protein a ɛho hia na ama yɛn mogya atɔ. Mpɛn pii no, sɛ obi pira a, mogya no gyae efisɛ saa protein ahorow yi (nneɛma a ɛma mogya tu) bom yɛ adwuma. Nanso, wɔ nnipa a wɔwɔ yare bi a wɔfrɛ no Hemophilia B mu no, wɔnyɛ saa protein a wɔfrɛ no Factor IX yi wɔ abɔde mu anaasɛ wɔyɛ no dodow a ɛba fam koraa.

Enti, saa aduru yi yɛ adwuma de siesie saa sintɔ no. Factor IX a wɔde ma sɛ aduru a wɔde bɔ mogya no boa ma mogya no tu na ɛma mogya tu bere a ɛhyɛn nipadua no mu no. Wɔ hemophilia B akyi no, nnuruyɛfo betumi akyerɛw saa aduru yi nso ama tebea afoforo bi a ɛmma mogya ntumi nkɔ.

Nneɛma a ɛsɛ sɛ woka kyerɛ wo duruyɛfo ansa na woanom nnuru

Okay, afei nneɛma kakraa bi wɔ hɔ a ɛsɛ sɛ woka kyerɛ wo duruyɛfo ansa na woanom saa aduru yi. Mfa saa nneɛma yi nsie, efisɛ ɛho hia paa ma w’ahobammɔ.

• Nyarewa afoforo a wowɔ:
• Mmɛn mu yare
• Ɔhaw afoforo a ɛma mogya tu
• Tebea a ɛma mogya tu wɔ mogya ntini bi mu (thrombosis) .
• Allergies: So woanya aduru, aduan, nnuru a wɔde yɛ nneɛma, anaa nneɛma a wɔde siesie nneɛma biara ho akisikuru pɛn? Hwɛ hu sɛ wobɛka eyi ho asɛm, titiriw sɛ wo ho nyɛ wo hyew wɔ nnipa anaa mmoa protein (e.g., mprako, hamsters) ho a.
• Nyinsɛn ne nufu a wɔde ma: Sɛ wonyinsɛn, worebɔ mmɔden sɛ wubenyinsɛn, anaa worema nufu a, ka kyerɛ wo duruyɛfo.

Wode saa aduru yi di dwuma dɛn?

Eyi yɛ injection a wɔde gu ntini mu (`(injection into a vein)`). Mpɛn pii no, akwahosan ho ɔbenfo a ɔwɔ ayaresabea anaa ayaresabea na ɔde ma.

Nanso ɛtɔ da bi a, ebia ɛho behia sɛ wode saa aduru yi di dwuma wɔ fie. Sɛ ɛba saa a, wɔbɛma wo ntetee a ɛho hia wɔ ayaresabea hɔ. Ɛho hia paa sɛ wubedi saa akwankyerɛ ahorow no akyi pɛpɛɛpɛ.

Sɛ wode redi dwuma wɔ fie a, ma nneɛma yi ntra w’adwenem:

• Ahosiesie: Ma aduru no powder ne ano aduru no mmra dan mu hyew mu kakra.
• Fafrafra: Fa ahwɛyiye fra sɛnea wɔakyerɛ no. Nwosow denneennen na ama woanya ahuru. Fa toa no kyinkyin ma ɛnyɛ hyew.
• Sɛnea wɔde di dwuma: Fa dodow a wɔakyerɛw ama wo no, wɔ bere a wɔakyerɛw ama wo no mu, sɛnea wo duruyɛfo akyerɛ wo no. Tow nea aka biara gu.
• Nnade a wɔtow gu: Eyi ho hia yiye. Mfa nnade anaa syringe a wɔde adi dwuma ngu nwura mu da. Ɛsɛ sɛ wɔde gu ade titiriw bi a wɔde nnam ayɛ mu. Sɛ wunni bi a, bisa wo duruyɛfo ma ɔmma wo bi.

So wobetumi de saa aduru yi ama mmofra?

Yiw, wɔ nsɛm bi a wɔapaw mu no, wɔde saa aduru yi nso ma mmofra. Nanso egye ahwɛyiye soronko. Enti, sɛ wode saa aduru yi rema wo ba a, wo ne wo mmofra oduruyɛfo nkasa wɔ eyi ho yiye.

Sɛ wonom nnuru pii a, dɛn na ɛsɛ sɛ woyɛ?

Sɛ wususuw sɛ woanom aduru yi a ɛboro dodow a wɔakyerɛw ama wo a, frɛ Ɔman Awuduru Ho Amanneɛbɔbea a ɛwɔ Colombo Ɔman Ayaresabea no ntɛm ara . Anaasɛ kɔ Emergency Department (ETU) a ɛwɔ ayaresabea a ɛbɛn wo no. Ntwentwɛn wo nan ase.

Nneɛma afoforo a ebia ɛne aduru no bedi nkitaho

Ebia nnuru bi ne Factor IX bedi nkitaho. Nhwɛsoɔ:

• Aminocaproic acid a ɛwɔ nipadua no mu
• Ade VIIa (ade VIIa) .
• Tranexamic acid a wɔde yɛ aduru

Saa list yi nwie pɛyɛ. Enti, ka nnuru a wonom nyinaa (sɛ́ ebia nnuruyɛfo afoforo akyerɛw ama wo anaasɛ woatɔ wɔ nnurutɔnbea), vitamin ahorow, nhabannuru a wode di dwuma, ne sɛ wonom sigaret, wonom nsa, anaa wode nnuru afoforo di dwuma ho asɛm kyerɛ wo duruyɛfo .

Nneɛma a ɛsɛ sɛ wohwɛ yiye wɔ ho bere a wode aduru no redi dwuma no

• Asiane a ɛwɔ ɔyare mmoawa mu: Wɔde nnipa mogya mu nsu na ɛyɛ Factor IX nneɛma bi. Enti, asiane ketewaa bi wɔ hɔ sɛ wɔde nneɛma te sɛ mmoawa bɛkɔ nnipa mu. Nanso mma ɛnhaw wo, wɔde akwan a ɛkɔ akyiri sen biara na ekum mmoawa ne mmoawa yi mu dodow no ara bere a wɔayɛ saa aduru yi no. Sɛ wowɔ nsɛmmisa bi fa eyi ho a, wo ne wo duruyɛfo nkasa. Sɛ wohu sɛ wowɔ hemophilia foforo a, ɛho hia yiye sɛ wobɛbɔ wo ho ban afi Hepatitis A ne B ho.
• ID: Sɛ wowɔ hemophilia a, fa ID krataa a wo ho nsɛm ka ho bere nyinaa. Ɛsɛ sɛ ɛka wo din, aduru a worenom no din ne dodow a wɔde di dwuma, wo duruyɛfo no din ne telefon nɔma, ne obi a wobɛkɔ no nkyɛn bere a biribi a egye ntɛmpɛ asi no ho nsɛm ka ho. Eyi betumi agye nkwa.

Nsunsuanso bɔne a ebetumi afi aduru no mu aba

Te sɛ aduru biara no, eyi betumi de ɔhaw ahorow aba nnipa binom so. Momma yɛnhwɛ nea wɔyɛ.