So ɛtɔ mmere bi a wopere wo ho wɔ nantew ho, wo ho yɛ wo yaw anaasɛ wo ho yɛ wo yaw a wuntumi nkyerɛkyerɛ mu, anaasɛ wote nka sɛ wobrɛ bere nyinaa? So woahyɛ no nsow sɛ saa sɛnkyerɛnne ahorow yi fi ase nkakrankakra na ɛyɛ kɛse bere tenten, sen sɛ ɛbɛda adi mpofirim? Sɛ saa a, ɛho hia sɛ wokyerɛkyerɛ wo ho wɔ tebea bi a yɛfrɛ no PPMS ho. Bere a eyi yɛ asɛm a ɛyɛ den no, wɔ Nirogi Lanka no, yɛpɛ sɛ yɛkyekyɛ mu wɔ ɔkwan a ɛnyɛ den na ɛnyɛ den sɛ wobɛte ase so ma wo.
Dɛn ankasa ne PPMS?
Momma yɛmfa mfitiasesɛm no mfi ase. PPMS gyina hɔ ma ‘Primary Progressive Multiple Sclerosis .’ . Ɛyɛ Multiple Sclerosis ( MS ) bi pɔtee bi.
Sɛ yɛbɛka no tiawa a, Multiple Sclerosis (MS) ba bere a wo nipadua mu tumi a ɛko tia nyarewa —a wɔayɛ sɛ ɛbɛbɔ wo ho ban afi nyarewa ho —di mfomso tow hyɛ w’ankasa wo ntini ahorow so no. Eyi sɛe nkitahodi a ɛkɔ w’amemene, akyi berɛmo, ne wo nipadua a aka no ntam.
MS ahorow atitiriw abien na ɛwɔ hɔ:
1. Relapsing-Remitting MS (RRMS): Wɔ saa ɔkwan yi mu no, wunya yare no ho sɛnkyerɛnne ahorow a ɛyɛ hyew mpofirim (a wonim no sɛ ‘remissions’), na ɛno akyi no, mmere a sɛnkyerɛnne ahorow no tu mpɔn anaasɛ ɛyera koraa (‘remission’). Fa no sɛ ahum; osu tɔ denneennen, afei ɛho tew, na osu san tɔ bio.
2. Primary Progressive MS (PPMS): Ɔkwan a yɛreka ho asɛm nnɛ no yɛ soronko koraa. Wɔ PPMS mu no, sɛnkyerɛnne ahorow no nsɔre na afei ɛyera. Mmom no, wo sɛnkyerɛnne ahorow no fi ase fi mfiase na nkakrankakra, bere kɔ so no, ɛyɛ kɛse. Ɛte sɛ osu a ɛtɔ bere nyinaa kɛse; ɛkɔ so, na bere kɔ so no, nea efi mu ba no da adi kɛse. Bere a ɛtɔ mmere bi a ebia wubehu yare no ho sɛnkyerɛnne ahorow a ɛkɔ soro kɛse no, ɛntaa nsi koraa.
Nnipa a wɔwɔ MS no mu bɛyɛ 10% wɔ saa ɔkwan yi, a wɔfrɛ no PPMS.
Dɛn ne PPMS ho sɛnkyerɛnne atitiriw?
Mfiase no, ebia PPMS ho sɛnkyerɛnne no yɛ nea ɛnyɛ anifere. Nanso, sɛnea bere kɔ so no, sɛnea emu yɛ den no taa yɛ kɛse. Saa sɛnkyerɛnne ahorow yi gu ahorow wɔ onipa biara mu. Ma yɛnhwɛ nsɛnkyerɛnne a ɛtaa ba a ebia wubehyia.
| Nsɛnkyerɛnne a ɛkyerɛ | Nkyerɛkyerɛmu a Ɛnyɛ Den |
|---|---|
| Nsɛnnennen a Ɛwɔ Nantew mu | Eyi ne PPMS ho sɛnkyerɛnne a ɛtaa ba. Nan a ɛyɛ mmerɛw, ɛyɛ den, anaasɛ ɛnkari pɛ betumi ama nantew ayɛ den yiye. |
| Ɔbrɛ a Ɛnkɔ So | Ɔbrɛ a ɛboro so, bere a woada anadwo mũ nyinaa anaasɛ apɔw-mu-teɛteɛ kakraa bi mpo akyi. Eyi kɔ akyiri koraa sen ɔbrɛ a wɔtaa de di dwuma. |
| Ayɛ a ɛyɛ mmerɛw anaasɛ Tingling | Ebia wobɛte nkate te sɛ ‘pin ne nnade,’ wo ho a ɛyɛ wo yaw, anaasɛ wo nipadua no afã horow a ɛyera, titiriw wɔ wo nsa ne wo nan mu. |
| Anisoadehu mu Nsakrae | Nsɛnkyerɛnne no betumi ayɛ aniwa a ɛyɛ kusuu, aniwa mmɔho abien, anaa ɛyaw a ɛba aniwa mu. |
| Ntini a Ɛyɛ Den anaa Mmerewa | Ntini betumi ayɛ den (spasticity), na ɛma ɛyɛ den sɛ wɔbɛkotow anaasɛ wɔbɛtrɛw mu. Bio nso, ebia wubehu sɛ wo ntini mu ahoɔden so atew. |
| Akisikuru ne Dwonku Ho Nsɛm | Ebia wubenya hia a ehia sɛ wotow wo ho mpofirim, ntɛm ara, wuntumi nni akisikuru no so, anaasɛ ɛbɛyɛ den sɛ wobɛma akisikuru no mu ada mpan. |
| Nkate mu Nsɛnnennen (Amemene Mu Nsuonwini) . | Eyi betumi ayɛ ɔhaw wɔ adwene a wɔde besi biribi so, nkae a ɛnyɛ den, anaasɛ ɛyɛ den sɛ wobenya nsɛmfua a ɛfata bere a wɔrebɔ nkɔmmɔ no. |
Nea ɛho hia sen biara no, yɛsrɛ sɛ nsusuw sɛ wowɔ PPMS esiane sɛ wunya saa sɛnkyerɛnne ahorow yi mu biako anaa abien nti. Ayaresa mu tebea afoforo pii nso wɔ saa sɛnkyerɛnne koro yi ara. Sɛ wopɛ sɛ wuhu yare no yiye a, ɛsɛ sɛ wokɔ oduruyɛfo bi nkyɛn.
Dɛn nti na PPMS ba? Dɛn na ɛde ba?
Nokwarem no, wɔda so ara nnim nea ɛde MS anaa PPMS ba ankasa. Nanso, nhwehwɛmufo gye di sɛ efi nneɛma pii a wɔaka abom mu:
- Awosu mu su: Sɛ obi wɔ w’abusua mu wɔ MS a, ebia asiane no bɛkɔ soro kakra, ɛwom sɛ mpɛn pii no asiane yi sua de. Ɛnkyerɛ sɛ akyinnye biara nni ho sɛ wɔde bɛma wo.
- Nneɛma a atwa yɛn ho ahyia: Wogye di sɛ mmoawa anaa mmoawa bi a wɔde wɔn ho hyɛ mu no betumi adi dwuma wɔ MS a ɛba no mu.
- Nkwammoaa a ɛko tia nyarewa no ntumi nyɛ adwuma yiye: Sɛnea yɛaka no, wo nipadua mu tumi a ɛko tia nyarewa no di mfomso sɛe ahobammɔ a atwa wo ntini mu nkwammoaa ho ahyia (‘myelin kotoku’) no. Saa ɔsɛe yi ma ntini mu nsɛnkyerɛnne a wɔde mena no kyɛ na ɛhaw.
Ɔkwan bɛn so na wohu PPMS?
Sɔhwɛ biako biara nni hɔ a wɔde besi PPMS so dua. Oduruyɛfo titiriw bi na ɛkyerɛ sɛnea woahu yare no denam wo yare no ho sɛnkyerɛnne, w’ayaresa ho abakɔsɛm, ne nea efi nhwehwɛmu ahorow mu ba a ɔhwɛ mu yiye so. Ɛyɛ adeyɛ a edi mũ, anammɔn biara a wɔde hwehwɛ yare mu.
Sɔhwɛ atitiriw a ebia wɔbɛyɛ no bi ni:
| Sɔhwɛ | Nea ɛhwehwɛ |
|---|---|
| MRI Scan a Wɔde Yɛ Adwuma | Eyi boa ma wohu ntini a asɛe (akuru) wɔ w’amemene ne w’akyi berɛmo mu. Ɛyɛ sɔhwɛ a ɛho hia wɔ PPMS a wobehu mu. |
| Lumbar Puncture a Wɔde Tow Nnipa Mu | Wo duruyɛfo de ade ketewaa bi di dwuma de boaboa amemene mu nsu bi ano. Yɛsɔ eyi hwɛ ma protein pɔtee bi a wɔfrɛ no ‘oligoclonal bands,’ a wɔtaa hu wɔ MS mu. |
| Mogya mu Nhwehwɛmu | Eyinom boa ma woyi tebea afoforo—te sɛ vitamin a wonnya nni anaa nyarewa afoforo a nipadua no tumi ko tia nyarewa—a ebetumi asuasua wo sɛnkyerɛnne ahorow no afi hɔ. |
| Tomography a Wɔde Aniwa Nhyiam (OCT) . | Eyi yɛ mfonini a ɛyaw nnim a wɔde susuw aniwa ntini a ɛwɔ w’ani akyi a asɛe, a MS betumi aka no. |
Bere a wɔtaa hu PPMS bere a wɔadi mfe 40 kosi 50 no, ebetumi aba wɔ mfe biara mu.
Dɛn ne ayaresa ahorow a wɔde sa PPMS?
Mprempren, wonni aduru biara a wɔde sa PPMS. Nanso, akwan a etu mpɔn wɔ hɔ a wobɛfa so ama yare no akɔ so brɛoo na woadi wo sɛnkyerɛnne ahorow ho dwuma na ama w’asetra atu mpɔn.
Wɔakyekyɛ ayaresa ahorow mu ayɛ no akuw atitiriw abien:
1. Ayaresa a Ɛsakra Nyarewa (DMTs) .
Saa nnuru yi boa ma ntini a ɛsɛe no so tew na ɛma yare no mu yɛ den brɛoo. DMT titiriw a wɔapene so ama PPMS ne ocrelizumab (Ocrevus®) , a ebetumi aboa ma woadi wo sɛnkyerɛnne ahorow no nkɔso ho dwuma.
2. Nsɛnkyerɛnne a Wɔde Di Dwuma
Eyi ho hia kɛse ma wo da biara da ahotɔ ne ahofadi:
- Apɔw-mu-teɛteɛ : Ɛboa ma wodi ntini a ɛyɛ den, mmerɛwyɛ, ne kari pɛ ho nsɛm so denam apɔw-mu-teɛteɛ a wɔde wɔn ani asi so so.
- Adwumayɛ mu Ayaresa: Ɛkyerɛkyerɛ wo akwan a mfaso wɔ so na ɛde nnwinnade a ɛbɛma da biara da nnwuma (te sɛ ntadehyɛ anaa aduannoa) ayɛ mmerɛw ba.
- Nnuru: Ebia wo duruyɛfo bɛkyerɛw nnuru ama wo de adi nsɛm pɔtee bi te sɛ akisikuru ano aduru, ɛyaw, ɔbrɛ, ne adwenemhaw ho dwuma .
Wo duruyɛfo no bɛyɛ ayaresa nhyehyɛe bi ama wo nkutoo. Ansa na wubefi ayaresa biara ase no, munsusuw nneɛma bɔne a ebetumi afi mu aba ho pefee bere nyinaa.
Nea ɛsɛ sɛ yɛhwɛ kwan bere a wo ne PPMS te
PPMS yɛ tebea a ɛka wo da biara da asetra kɛse. Bere a wo yare no ho sɛnkyerɛnne resakra no, ebia ebehia sɛ woyɛ nsakrae na ama woanya ahobammɔ na asiw akwanhyia ano.
Sɛ nhwɛso no, ebia awiei koraa no wubehia obi a ɔnam fam anaa mmubuafo akongua. Kae: saa mmoa yi a wode bedi dwuma no nyɛ nkogudi; wɔyɛ nnwinnade a wode bɛkora w’ahofadi so na woakɔ so ayɛ nnam.
Sɛ wo ne tebea bi a enni sabea tra ase a, ebetumi aka wo nkate fam yiyedi. Ɛyɛ ade a ɛfata sɛ wobɛte nka sɛ woayɛ basaa anaasɛ wo ho yeraw wo. Sɛ wo ne adwenemyare ho ɔfotufo bɛkasa anaasɛ wobɛka wo nkate ho asɛm akyerɛ obi a wowɔ mu ahotoso a, ebetumi ayɛ ayaresa a ɛyɛ nwonwa.
PPMS nnya wo nkwa nna so nkɛntɛnso tẽẽ, nanso nsɛnnennen a wubedi ho dwuma no yɛ ade titiriw a ɛbɛma woakura asetra pa mu.
Bere bɛn na ɛsɛ sɛ wokɔ wo duruyɛfo nkyɛn?
Sɛ wowɔ PPMS a, abusuabɔ a emu yɛ den a wo ne w’aduruyɛfo kuw no benya no ho hia. Yɛsrɛ sɛ, kɔ wo duruyɛfo nkyɛn sɛ:
- Wo yare no ho sɛnkyerɛnne no mu yɛ den kɛse, na ɛka wo da biara da dwumadi.
- Wohu obubuafo mpofirim, wote ɛyaw a ɛkɔ so daa, anaasɛ wo ho yɛ wo yaw.
- Wohwe ase anaasɛ wupira esiane nsɛm a ɛfa kari pɛ ho nti; yɛsrɛ sɛ kɔ Emergency Department (ED) ntɛm ara.
- Wunya nsunsuanso bɔne a emu yɛ den fi wo nnuru no mu.
Nsɛmmisa a ɛsɛ sɛ wubisa wo duruyɛfo:
- So wɔasi so dua sɛ me yare no yɛ PPMS, anaasɛ MS foforo?
- Ɔkwan bɛn na eye sen biara a mɛfa so adi me yare no ho sɛnkyerɛnne pɔtee no ho dwuma?
- So apɔw-mu-teɛteɛ anaa adwuma mu ayaresa so benya so mfaso?
- Asiane ne nsunsuanso bɔne bɛn na ɛwɔ nnuru a wɔakyerɛw ama me no mu?
- So ɛsɛ sɛ misusuw nneɛma a wɔde boa ma obi nantew te sɛ mmubuafo akongua ho wɔ saa bere yi mu?
Nkrasɛm a Wɔde Kɔ Fie
- PPMS yɛ MS bi a ɛda adi sɛ yare no ho sɛnkyerɛnne kɔ so nkakrankakra sen sɛ ɛbɛba mpofirim.
- Bere a wonnim nea ɛde ba anaa ayaresa biara de besi nnɛ no, ayaresa ahorow a etu mpɔn kɛse wɔ hɔ a ɛbɛma woanya nkɔso brɛoo na wɔadi wo sɛnkyerɛnne ahorow no ho dwuma.
- Nea ɛka nhwehwɛmu pɔtee bi te sɛ MRI mfonini ne akyi berɛmo a wɔtow ho hwehwɛ sɛ wohu yare no.
- Sɛ wosa wo yare yiye na wosakra w’asetra mu a, wubetumi akɔ so atra ase a edi mũ na mfaso wɔ so.
- Sɛ wuhu nsakrae titiriw biara anaasɛ wowɔ biribi a ɛhaw wo a, yɛsrɛ wo, kɔ wo duruyɛfo nkyɛn ntɛm ara.
👩🏽 ⚕️ Nsɛmmisa a Wɔtaa Bisa (FAQs) .
💬 Dɛn ne Mfitiaseɛ Nkɔsoɔ Multiple Sclerosis (PPMS)?
PPMS yɛ Multiple Sclerosis a ɛyɛ den a w’ankasa nipadua mu ahoɔden a ɛko tia nyarewa no di mfomso tow hyɛ ntini a ɛwɔ w’amemene ne w’akyi berɛmo mu a ɛbɔ wo ho ban (myelin) so. Nea ɛnte sɛ MS ahorow afoforo no, mpɛn pii no, PPMS nya nkɔso nkakrankakra bere tenten, na ɛka wo nantew ne sɛnea wubetumi ayɛ da biara da dwumadi ahorow no nkakrankakra.
💬 Dɛn ne PPMS ho nsɛnkyerɛnne a edi kan?
Wɔ mfiase no, ebia wubehu sɛ wo nan mu yɛ duru bere nyinaa, wo ho yɛ wo yaw, anaasɛ wobrɛ a ɛyɛ soronko. Mpɛn pii no, ebia wubehu sɛ wo kari pɛ no ka wo, na ɛde hintidua anaa ɛyɛ den sɛ wobɛnantew. Nea ɛho hia no, saa sɛnkyerɛnne ahorow yi taa mu yɛ den nkakrankakra bere a bere kɔ so no sen sɛ ɛbɛsakrasakra anaasɛ ɛbɛyera.
💬 So wobetumi asa PPMS koraa?
Bere a mprempren wonni PPMS aduru biara no, wɔ Nirogi Lanka no yɛpɛ sɛ wuhu sɛ aduruyɛ mu nkɔso ma wonya anidaso. Yɛnam nnɛyi ayaresa te sɛ Ocrelizumab ne nipadua mu ayaresa a wɔatu ho ama so no, yebetumi adi yare no nkɔso ho dwuma yiye na ama w’asetra atu mpɔn kɛse.
