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Yala an bɛna kuma kuru min man ca, n’a bɛ wele ko Feochromocytome bi wa?

Yala an bɛna kuma kuru min man ca, n’a bɛ wele ko Feochromocytome bi wa?

Yala tansiyɔn jiginni barikama bɛ i la tuma dɔw la wa? Walima i bɛ sumaya dɔrɔn wa? Yala i bɛ kungolodimi sɔrɔ ni dusukun bɛ kirin wa? Aw kana teliya kojugu k’a miiri ko nin fɛn damadɔw ye bana jugumanba ye. Nka, ni nin taamasiɲɛ ninnu bɛ to senna, kɛrɛnkɛrɛnnenya la ni tansiyɔn jiginni ye min kunbɛnni ka gɛlɛn, a ka ɲi aw ka hami dɔɔni. Bi an bɛna kuma bana dɔ kan min man ca dɔɔni, nka ni a sɛgɛsɛgɛra ka ɲɛ, a bɛ se ka furakɛ ka ɲɛ kosɛbɛ. O bɛ wele ko feochromocytome.

Feochromocytoma ye mun ye? An k’a faamu cogo nɔgɔman na.

N’an y’a fɔ cogo nɔgɔman na, feochromocytome ye kuru ye min bɛ sɔrɔ sugunɛbara cɛmancɛ yɔrɔ la, n’o ye sugunɛbaralabana ye. O kurukuruw bɛ sɔrɔ farikolokisɛ suguya kɛrɛnkɛrɛnnen dɔ fɛ min bɛ wele ko kuromafini selilu. O farikolokisɛw bɛ ɔrimɔni dɔw Bɔ joli la minnu ka kan an farikolo ka "kɛlɛ walima boli" jaabi la. Aw ye miiri a la, ni aw barika banna walima ni aw ye degun caman sɔrɔ, fɛn minnu bɛ yeli kɛ aw fari la - aw dusukun tantanni bɛ bonya, aw bɛ sumaya, aw farikolo bɛ yɛrɛyɛrɛ - o ɔrimɔni ninnu de bɛ o kɛ.

A ka ca a la, feochromocytoma bɛ sɔrɔ sugunɛbaralabana kelen dɔrɔn de la. Nka, tuma dɔw la, a bɛ se ka kɛ ɲɛgɛnɛsira fila bɛɛ la. A bɛ se ka kɛ ko kuru ka ca ni kelen ye glande kelen kɔnɔ.

Nafa min b’a la, o ye ko feyokɔrɔmositoma fanba tɛ bana jugu ye (u tɛ bana jugu ye) . O kɔrɔ ye k’u tɛ jɛnsɛn farikolo yɔrɔ wɛrɛw la. Nka, 10% ni 15% cɛ bɛ se ka kɛ kansɛri ye. Ni nin ye kansɛribana ye, a ɲɛfɔlen don kuluba caman na, ka kɛɲɛ ni a jɛnsɛnna cogo ye:

  • Feochromocytome localisé : Tumu bɛ sɔrɔ sugunɛbaralabana kelen dɔrɔn de la walima a fila bɛɛ la.
  • Feochromocytome régional : Kansɛri jɛnsɛnna ɲɛgɛnɛsiraw la minnu bɛ sugunɛbaralabana kɛrɛfɛ walima farikolo yɔrɔ wɛrɛw la.
  • Feochromocytome metastatique : Kansɛri jɛnsɛnna farikolo yɔrɔ janw na i n’a fɔ sugunɛ, fogonfogon walima kolo.
  • Feochromocytoma min bɛ segin ka kɛ : Kansɛri seginna ka na furakɛli kɔfɛ. A bɛ se ka kɛ yɔrɔ kelen na a tun bɛ yɔrɔ min na ka kɔn o ɲɛ walima yɔrɔ wɛrɛ la.

O sugunɛbaralabanaw ye mun ye an farikolo la? U ka baara ye mun ye?

An bɛ ni surɔfiyen fila ye. U bɛ sɔrɔ an kɔnɔbara kɔ fɛ, an ka sugunɛ sanfɛ, i n’a fɔ finimugu. U ye an ka endocrine system (banakisɛfagalanw) yɔrɔ dɔ ye. Surɔfiyen kelen-kelen bɛɛ bɛ ni yɔrɔba fila ye. Kɛnɛma yɔrɔ bɛ wele ko surɔfiyen, cɛmancɛ yɔrɔ bɛ wele ko surɔfiyen.

An ka sugunɛbaralabana bɛ ɔrimɔni kulu dɔ dilan min bɛ wele ko katekolaminiw. O ɔrimɔni ninnu bɛ taabolo nafama caman ɲɛnabɔ an farikolo la:

  • Dusukun tantanni
  • Tansiyɔn jiginni
  • Joli sukaro hakɛ `(Joli sukaro)`
  • An farikolo bɛ degun jaabi cogo min na ("kɛlɛ walima boli" jaabi) .

Katekolamini suguya kunbabaw ye:

  • Dopamine (dopamine) ye
  • Epinefirini (Adrenaline) `(Epinephrine / Adrénaline)`
  • Norepinephrine (Noradrenaline) `(Norepinephrine / Noradrénaline)`

Ni feochromocytoma bɛ yen, a bɛ se ka nin ɔrimɔni ninnu caman bɔ joli la, adrénaline ni noradrenaline, ka tɛmɛ a mago kan. O waati de la taamasiɲɛ suguya caman bɛ daminɛ ka bɔ kɛnɛ kan.

Danfara jumɛn bɛ Feochromocytoma ni Paraganglioma cɛ?

Ninnu ye kuru suguya fila ye minnu bɔlen don ɲɔgɔn fɛ kosɛbɛ, minnu man ca. U fila bɛɛ bɛ bɔ kuromafini selilɛri kelenw na, an ye baro kɛ minnu kan ka tɛmɛ. Nka, feochromocytoma bɛ sɔrɔ sugunɛbara cɛmancɛ yɔrɔ la (surénaux medulla), ka sɔrɔ paraganglioma bɛ sɔrɔ yɔrɔ wɛrɛw la surɔfiyen kɔkan .

Jɔn de ka teli ka nin bana in sɔrɔ? A ka ca cogo di?

Feochromocytoma bɛ se ka sɔrɔ si hakɛ bɛɛ la, nka a ka ca mɔgɔw la minnu si bɛ san 30 ni san 50 cɛ.

nin ye kuru ye min man ca kosɛbɛ . A ka gɛlɛn ka a fɔ tigitigi nin bana in bɛ mɔgɔ hakɛ min na. Ikomi mɔgɔ dɔw tɛ taamasiɲɛ foyi jira, a bɛ se ka kɛ bana in ma dɔn. A jateminɛna ko tansiyɔn jiginni bɛ mɔgɔ minnu na, olu hakɛ tɛ se 1% ma.

Feochromocytoma bɛ mɔgɔ min na, o bɛ taamasiɲɛ jumɛnw jira?

Feochromocytome taamasiɲɛw bɛ sɔrɔ ni kuru ye adrénaline (épinephrine) walima noradrenaline (norepinephrine) ɔrimɔni caman bɔ joli la. Nka, kuru dɔw tɛ o ɔrimɔni caman bɔ, wa a bɛ se ka kɛ ko taamasiɲɛ tɛ u la.

A taamasiɲɛ minnu ka teli ka ye, olu ye:

  • Tansiyɔn jiginni (Tansiyɔn jiginni): O de ye a taamasiɲɛba ye. Tuma dɔw la, a ka gɛlɛn ka a kunbɛn.
  • Kungolodimi: A bɛ se ka kɛ kungolodimi jugumanba ye, min bɛ kɛ yɔrɔnin kelen.
  • Sumaya kojugu kun tɛ a la.
  • Dusukun tantanni ye dusukun tantanni teliya ye, min tɛ kɛ tuma bɛɛ, walima min bɛ kɛ ni dusukun tantanni ye.
  • K’a ye ko i farikolo bɛ yɛrɛyɛrɛ.

Taamasiɲɛ minnu ka teli ka sɔrɔ:

  • Disi ni/walima kɔnɔdimi.
  • Fari bɛ barika kɛ ka ɲɛ ka tɛmɛ a cogo kɔrɔ kan.
  • Dusukunnata ni/walima fɔɔnɔ.
  • Kɔnɔboli.
  • Kɔnɔja.
  • Tansiyɔn jiginni orthostatique ye tansiyɔn jiginni barikama ye ni aw wulila. O kɔrɔ ye ko i ɲɛnamini bɛ kɛ ni i wulila yɔrɔnin kelen ka bɔ i sigiyɔrɔ la.
  • Kisɛya dɔgɔyali kun tɛ.

Nin taamasiɲɛ ninnu bɛ se ka bɔ walima ka juguya ko dɔw kɔfɛ. I n'a fo:

  • Farikoloɲɛnajɛ jugumanba.
  • Farikolo jogin walima hakili degun jugumanba.
  • Den bangeli.
  • Anestezi sɔrɔli.
  • Opereli kɛli.
  • Dumuni minnu nafa ka bon tiramini na (misali la, diwɛn bilenman, sokola, foromazi).

Yala a taamasiɲɛw bɛ yen tuma bɛɛ wa? Walima u bɛ na ka taa wa?

Feochromocytoma bɛ mɔgɔ min na , tansiyɔn jiginni bɛ se ka kɛ a la, walima a bɛ se ka na ka taa .

Mɔgɔ dɔw bɛ se ka "paroxysmal attacks" sɔrɔ, walima bana taamasiɲɛw bɛ se ka barika sɔrɔ. O kɔrɔ ye ko tansiyɔn bɛ bonya yɔrɔnin kelen, ka fara a taamasiɲɛw kan i n’a fɔ kungolodimi juguman, dusukun tantanni caya, ani sumaya kojugu. O "bìnkanni" ninnu bɛ Se ka Kɛ siɲɛ caman tile kɔnɔ, walima hali siɲɛ kelen walima siɲɛ fila kalo kɔnɔ.

Nafama: Ni nin taamasiɲɛ ninnu dɔ bɛ aw la, kɛrɛnkɛrɛnnenya la tansiyɔn jiginni barikama, kungolodimi, sumaya, ani dusukun tantanni, a nafa ka bon kosɛbɛ aw ka dɔgɔtɔrɔ ka ladilikan ɲini.

Mun na feochromocytoma bɛ sɔrɔ? O sababu ye mun ye?

A ka ca a la, sababu kɛrɛnkɛrɛnnen tɛ se ka sɔrɔ feyokɔrɔmositoma la. A bɛ kɛ k’a sɔrɔ a ma kɛ cogo si la.

Nka, 25% fo 35% la, o bana in bɛ tali kɛ cɛya banaw la. A kunbaba dɔw ye ninnu ye:

  • Endocrine néoplasie multiple 2 syndrome, suguya A ni B (MEN2A ni MEN2B) .
  • Von Hippel-Lindau (VHL) ka bana
  • Neurofibromatose suguya fɔlɔ (NF1) .
  • Paragangliome héritage (banakisɛfagalan) min bɛ sɔrɔ cɛya la
  • Carney-Stratakis dyad [paraganglioma ani kɔnɔbara basigilen kuru (GIST)].
  • Carney triad (paraganglioma, GIST ani fogonfogonlabana) .

Ka fara o jamu cogoyaw kan, feyokɔrɔmositoma fana bɛ se ka sɔrɔ ka da fɛn caman sɛgɛsɛgɛli kan jamu suguya 10 la dɔgɔmannin.

Nin bana in bɛ dɔn cogo di? (Sɛgɛsɛgɛli) .

Feochromocytoma sɔrɔli bɛ se ka gɛlɛya barisa a ye kuru ye min man teli ka sɔrɔ, wa tuma dɔw la a tɛ taamasiɲɛ foyi lase mɔgɔ ma. Tuma dɔw la, kuru in bɛ sɔrɔ a danma sɛgɛsɛgɛli dɔ senfɛ min kɛra kun wɛrɛ la.

Kun caman bɛ yen minnu b’a to dɔgɔtɔrɔ bɛ se ka siga nin bana in na:

  • Aw ta donFurakɛcogo tariku ɲɛfɔlen, kɛrɛnkɛrɛnnenya la ni denbaya kɔnɔ mɔgɔ dɔ ye feyokɔrɔmositɔmu sɔrɔ ka kɔrɔ.
  • Farikolo ni furakɛli sɛgɛsɛgɛli dafalen.
  • Taamaʃyɛn kɛrɛnkɛrɛnnen dɔw , misali la an kumana "attaques paroxysme" minnu kan ani tansiyɔn jiginni min tɛ kunbɛn furakɛlicogo nɔgɔmanw fɛ.

Sɛgɛsɛgɛli sugu jumɛnw bɛ kɛ?

Aw ka dɔgɔtɔrɔ bɛ se ka nin sɛgɛsɛgɛli ninnu fɔ aw ye walasa ka a dɔn ni feochromocytoma bɛ aw la:

  • Sugunɛ sɛgɛsɛgɛli lɛri 24 kɔnɔ : O ye ka aw ka sugunɛ lajɛ tile bɛɛ kɔnɔ ani ka katekolamini hakɛ jateminɛ a kɔnɔ. A bɛ fɛnw fana suman minnu bɛ bɔ ni o ɔrimɔni ninnu tiɲɛna. Ni o hakɛw cayara ka tɛmɛ a cogo kɔrɔ kan, o bɛ se ka kɛ feyokɔrɔmositɔmu taamasiɲɛ ye.
  • Joli katekolamini sɛgɛsɛgɛliw : Olu bɛ katekolamini hakɛ jateminɛ joli la. I n’a fɔ sugunɛ sɛgɛsɛgɛli, u bɛ fɛnw fana ɲini minnu bɛ sɔrɔ ɔrimɔni tiɲɛni fɛ.
  • CT scan (Computer Tomography scan): O bɛ kɛ ka X-ray kɛ ka tugu ɲɔgɔn na walasa ka ja caman dilan i farikolo kɔnɔna na. Aw ka dɔgɔtɔrɔ bɛ se ka nin fɔ aw ye walasa ka aw ka sugunɛbilenniw lajɛ.
  • MRI scan (MRI - Magnetic Resonance Imaging): O bɛ kɛ ni magɛnni ye, arajo fiɲɛw ani ɔridinatɛri ye walasa ka farikolo kɔnɔna ja caman dilan. A bɛ kɛ fana ka sugunɛbaralabanaw sɛgɛsɛgɛ.

Ni bana in tiɲɛna, sɛgɛsɛgɛli wɛrɛw bɛ se ka kɛ walasa ka a dɔn ni kuru in ye kansɛri ye (bana jugumanba) walima ni bana juguman don (bana jugumanba), ani ni a jɛnsɛnna farikolo yɔrɔ wɛrɛw la.

Mun na jamu sɛgɛsɛgɛli nafa ka bon?

Ni a sɔrɔla ko feochromocytome bɛ aw la, a ka c’a la, aw ka dɔgɔtɔrɔ bɛna a fɔ aw ye ko aw ka ladilikanw ni sɛgɛsɛgɛli kɛ jamu kan walasa ka a dɔn ni bana dɔ bɛ aw la min bɛ sɔrɔ ciyɛn fɛ, o bɛ aw bila farati la ka kansɛri wɛrɛw sɔrɔ.

Jɛnkulu sɛgɛsɛgɛli bɛ se ka kɛ nin ko suguw la:

  • Ni taamasiɲɛw bɛ aw walima aw ka denbaya kɔnɔmɔgɔ dɔ la minnu bɛ tali kɛ feochromocytoma héritage walima paraganglioma syndrome la.
  • Ni kuruw bɛ aw ka sugunɛbaralabana fila bɛɛ la.
  • Ni kuru ka ca ni kelen ye sugunɛbaralabana kelen na.
  • Ni katekolamini hakɛ cayalenba taamasiɲɛw bɛ joli la.
  • Ni feochromocytoma sɔrɔla ka kɔn san 40 ɲɛ.

Ni jamu sɛgɛsɛgɛli y’a ye ko jamu caman yeli ye, jamu ladilikɛla bɛ se k’a fɔ aw ye ko aw ka denbaya kɔnɔmɔgɔ tɔw (minnu taamasiɲɛ tɛ u la nka farati bɛ minnu na) fana ka o sɛgɛsɛgɛli kɛ.

Feochromocytoma furakɛcogo jumɛnw ye?

O furakɛcogo ɲuman ye ka opereli kɛ ka kuru bɔ, ni a bɛ se ka kɛ .

Furakɛli sugandili bɛ bɔ fɛn caman na:

  • Tumu hakɛ.
  • Ni kuru in ye kansɛri ye (a jugumanba) walima a man ɲi (bana jugumanba).
  • Ni taamasiɲɛw bɛ yen ka a sababu kɛ katekolamini ɔrimɔni caya ye.
  • Yala kuru bɛ ​​dan yɔrɔ kelen na wa, walima a jɛnsɛnna farikolo yɔrɔ wɛrɛw la wa? (A bɛ taa yɔrɔ wɛrɛw la) .
  • Ni bana in sɔrɔla a siɲɛ fɔlɔ la, walima ni a seginna ka kɛ furakɛli tɛmɛnen kɔfɛ.

Ni bana taamasiɲɛw bɛ aw la ka a sababu kɛ sugunɛbilenni ɔrimɔni caya ye, aw ka dɔgɔtɔrɔ bɛ se ka furaw di aw ma walasa ka o taamasiɲɛw kunbɛn. I n'a fo:

  • Fura minnu bɛ tansiyɔn to a cogo la, i n’a fɔ alfa-blokantiw.
  • Fura minnu bɛ dusukun tantanni to a cogo la, i n’a fɔ beta-blokantiw.
  • Fura minnu bɛ ɔrimɔni nɔw bali minnu bɛ bɔ ka tɛmɛ sugunɛbaralabana fɛ.

Feochromocytoma furakɛcogo kunbabaw ye:

  • Operelikɛyɔrɔ
  • Furakɛli min bɛ kɛ ni fiɲɛ ye
  • Chimiothérapie (banakisɛfagalanw) furakɛli
  • Ablation furakɛli
  • Embolisasi furakɛli
  • Furakɛli min ɲɛsinnen don a ma

Aw ni aw ka dɔgɔtɔrɔso jɛkulu bɛna fara ɲɔgɔn kan ka furakɛli bolodacogo dɔn min ka fisa aw ma.

Furakɛli fɛɛrɛ kunbabaw

  • Operelikɛyɔrɔ:

Nin ye feyokɔrɔmositɔmu furakɛli kunba ye. kuru 90% ɲɔgɔn bɛ se ka bɔ opereli fɛ ka ɲɛ .

Dɔgɔtɔrɔ bɛ se ka opereli fɔ aw ye walasa ka aw ka sugunɛbaralabana kelen walima u fila bɛɛ bɔ (surénalectomie). Opereli senfɛ, operelikɛla bɛna a lamini yɔrɔw ni ɲɛgɛnɛsiraw sɛgɛsɛgɛ walasa ka a dɔn ni kuru jɛnsɛnna. Ni a y’a sɔrɔ, u bɛna o fɛnɲɛnamafagalan bɔ, ni a bɛ se ka kɛ.

Opereli kɔfɛ, aw joli walima aw ka sugunɛ bɛna sɛgɛsɛgɛ walasa ka katekolamini hakɛ dɔn. Ni a hakɛ seginna a cogo kɔrɔ la, o kɔrɔ ye ko feyokɔrɔmositoma selilɛriw bɛɛ bɔra.

Ni sugunɛbilenni fila bɛɛ bɔra, aw bɛna ɔrimɔni furakɛli kɛ aw ka ɲɛnamaya bɛɛ kɔnɔ walasa ka ɲɛgɛnɛsiralabanaw ka ɔrimɔni minnu bɛ bɔ, olu bila u nɔ na.

  • Furakɛli min bɛ kɛ ni fiɲɛ ye:

Nin ye fura ye min bɛ kɛ ka kansɛribanakisɛw faga walima ka u bali ka bonya. O bɛ kɛ cogo la min tɛ tiɲɛni kɛ farikolo yɔrɔ kɛnɛmanw na ka se a dan na.

Fiɲɛdimi furakɛli suguya fila bɛ yen:

  • Kɛnɛya furakɛli : Fiɲɛ bɛ lase kansɛri yɔrɔ la ka bɔ masin dɔ la min bɛ farikolo kɔkan.
  • Kɔnɔna na furakɛli : Fɛn min bɛ kɛ ni fiɲɛ ye, o bɛ pake pikirijikɛlanw, kisɛw, nɛgɛw walima katetɛriw kɔnɔ ka dɔgɔtɔrɔ dɔ don kansɛri yɔrɔ la walima a kɛrɛfɛ.

Fiɲɛdimi furakɛli suguya bɛ bɔ kansɛri yɔrɔ la, sigida la, a bɛ taa yɔrɔ wɛrɛw la, walima ni a bɛ segin ka kɛ. Feochromocytoma jugumanba bɛ furakɛ ka caya ni kɛnɛyaji ye min bɛ kɛ ni kɛnɛyaji ye ani/walima ni 131I-MIBG furakɛli ye. 131I-MIBG ye fɛnɲɛnamafagalan ye min bɛ nɔrɔ kansɛribana dɔw la ka u faga.

  • Chimiothérapie (banakisɛfagalanw) :

O bɛ furaw kɛ ka kansɛribanakisɛw faga, ka u bali ka tila ka caya, walima ka kansɛri falenni dabila. A ka ca a la, fura ninnu bɛ di jolisira fɛ. Hali ni nin ye furakɛli ɲɛnama ye, a bɛ se ka kɔlɔlɔw lase mɔgɔ ma.

  • Ablation furakɛli:

Nin ye furakɛli ye min tɛ fɛn caman kɛ. A bɛ funteni jugumanba walima nɛnɛba kɛ ka kurukuruw tiɲɛ.

  • Radiofréquence ablation : Radiofrequence ablation bɛ kɛ ni arajo fiɲɛw ye walasa ka kansɛribanakisɛw ni farikolokisɛ minnu tɛ cogoya la, olu sumaya ani ka u tiɲɛ.
  • Cryoablation : A bɛ kɛ ni azote jilama walima gazi ɲuman jilama ye walasa ka kansɛribanakisɛw ni farikolokisɛ minnu tɛ cogoya la, olu sumaya ani ka u tiɲɛ.
  • Embolization furakɛli:

O la, joli sira min bɛ joli lase surɔfiyen ma, o bɛ datugu. O bɛ joli boli dabila ka taa ɲɛgɛnɛsira la, ka kansɛribanakisɛw faga minnu bɛ falen yen.

  • Furakɛli min ɲɛsinnen don a ma:

O bɛ kɛ ni furaw walima fɛn wɛrɛw ye minnu bɛ kansɛribanakisɛw dɔrɔn de kɛlɛ kɛrɛnkɛrɛnnenya la k’a sɔrɔ u ma tiɲɛni kɛ farikolokisɛ kɛnɛmanw na. Nin furakɛli in bɛ kɛ feyokɔrɔmositoma (feochromocytome) la min bɛ taa yɔrɔ wɛrɛw la ani min bɛ segin ka kɛ.

Tirosini kinase inhibiteur dɔ min bɛ wele ko sunitinib, o bɛ ka sɛgɛsɛgɛ feochromocytoma metastatique (feochromocytome) la min bɛ taa yɔrɔ wɛrɛw la. O fura ninnu bɛ tumuw falenni bali.

Yala nin bana in bɛ se ka kunbɛn wa?

A fɔ man di nka, fɛɛrɛ si tɛ yen min bɛ se ka feyokɔrɔmositoma bali . Nka, ni farati bɛ aw la ka nin bana in sɔrɔ ka a sababu kɛ ciyɛntalanw ni jamu ye, jamu ladilikanw bɛ se ka dɛmɛ don sɛgɛsɛgɛli ni a dɔnni joona la.

Ni aw ka denbaya kɔnɔmɔgɔ gɛrɛgɛrɛ dɔw (balimakɛw, bangebagaw) ye feyokɔrɔmositɔmu sɔrɔ, walima ni aw ka jamu bana dɔ bɛ aw la i n’a fɔ an ye baro kɛ minnu kan ka tɛmɛ (Multiple endocrine neoplasia 2 syndrome, Von Hippel-Lindau (VHL) bana, Neurofibromatose type 1 (NF1), Hereditary paraganglioma syndrome, Carney-Stratakis dyad, Carney triad), a nafa ka bon kosɛbɛ ka kuma i ka dɔgɔtɔrɔ fɛ o ko la.

Furakɛli kɔfɛ, a bɛ se ka kɛnɛya cogo di? (Pronostic) (Kɔrɔfɔcogo) .

A ka ca a la, feokɔrɔmositoma (pheochromocytome) ɲɛfɔli ka ɲi kosɛbɛ ni a furakɛra.An y’a fɔ kaban ko kuru 90% ɲɔgɔn bɛ se ka bɔ opereli fɛ ka ɲɛ.

Nka, ni o bana ma furakɛ, o bɛ se ka kɛ sababu ye ka gɛlɛyabaw lase mɔgɔ ma, hali minnu bɛ se ka mɔgɔ ka ɲɛnamaya bila farati la . I n'a fo:

  • Dusukun tantanni (Cardiomyopathie).
  • Mikorokaridi (mikorocardite) bɛ sɔrɔ
  • Joli bɔli kunsɛmɛ na min tɛ kunbɛn (Cerebral hemorrhaging) .
  • Ji ka dalajɛ fogonfogon la (Fogonfogon la sɔgɔsɔgɔninjɛ) .

Feochromocytoma banabagatɔ dɔw fana bɛ se ka kirin walima ka dusukun tantanni sɔrɔ.

Tuma jumɛn na ne ka kan ka taa dɔgɔtɔrɔso la?

  • Ni a sɔrɔla ko feyokɔrɔmositoma bɛ aw la ani ni taamasiɲɛ gɛlɛn o taamasiɲɛ bɛ aw la, aw bɛ taa dɔgɔtɔrɔso la joona.
  • Ni feochromocytoma taamasiɲɛw bɛ aw la, i n’a fɔ tansiyɔn jiginni ani kungolodimi, aw bɛ kuma aw ka dɔgɔtɔrɔ fɛ. Hali ni feokɔrɔmositoma man teli ka kɛ, a nafa ka bon ka tansiyɔn jiginni furakɛ.
  • Ni aw b’a dɔn ko aw somɔgɔw dɔ (balimakɛw, bangebagaw) ka jamu bana dɔ bɛ a la i n’a fɔ `Multiple endocrine neoplasia 2 syndrome` walima `Von Hippel-Lindau (VHL) disease`, aw bɛ se ka kɛ fana ko faratiba bɛ aw la ka feochromocytoma sɔrɔ, o la aw bɛ taa dɔgɔtɔrɔso la walasa ka baro kɛ jamu sɛgɛsɛgɛli kan.

Ne ka kan ka ɲininkali jumɛnw kɛ dɔgɔtɔrɔ la?

Ni a sɔrɔla ko feochromocytoma bɛ aw la, a bɛ se ka kɛ ko a bɛ aw dɛmɛ ka nin ɲininkali ninnu kɛ aw ka dɔgɔtɔrɔ la:

  • Mun na ne ye feochromocytoma sɔrɔ?
  • Yala ne denw ni/walima ne somɔgɔw bɛ se ka feochromocytoma sɔrɔ wa?
  • Furakɛli suguya jumɛnw bɛ ne bolo?
  • Furakɛli suguya wɛrɛw kɔlɔlɔ jumɛnw bɛ yen?
  • Ne bɛ se ka ne ka bana taamasiɲɛw kunbɛn cogo di?

A laban na, fɛn minnu nafa ka bon kosɛbɛ an ka kan ka to an hakili la (Take-Home Message) .

O bɛ ɲɛ, o la, hali ni feyokɔrɔmositɔmu ye kuru ye min man teli ka sɔrɔ, a ka ca a la, a man ɲi ani a bɛ se ka furakɛ . Ani fana, a bɛ se ka boli denbayaw kɔnɔ, o la ni nin bana in sɔrɔla aw walima aw ka denbaya kɔnɔmɔgɔ dɔ la, a nafa ka bon aw ka jamu sɛgɛsɛgɛli kɛ. O bɛ se ka dɛmɛ fana ka a dɔn ni farati bɛ aw la kɛnɛyako gɛlɛya wɛrɛw la.

Aw ye aw hakili to a la ko ni ɲininkali dɔw bɛ aw fɛ feyokɔrɔmositoma sɔrɔli farati kan walima nin bana in kan, aw kana siran ka kuma aw ka dɔgɔtɔrɔ fɛ. U bɛ yan walisa k’aw dɛmɛ. Aw ka to kɛnɛya la!


Feochromocytoma , surɔfiyen, katekolamini, tansiyɔn jiginni, kungolodimi, sumaya, kuru, endocrine system

Frequently Asked Questions (FAQ)

Sɛgɛsɛgɛli sugu jumɛnw bɛ kɛ?

Aw ka dɔgɔtɔrɔ bɛ se ka nin sɛgɛsɛgɛli ninnu fɔ aw ye walasa ka a dɔn ni feochromocytoma bɛ aw la:

Mun na jamu sɛgɛsɛgɛli nafa ka bon?

Ni a sɔrɔla ko feochromocytome bɛ aw la, a ka c’a la, aw ka dɔgɔtɔrɔ bɛna a fɔ aw ye ko aw ka ladilikanw ni sɛgɛsɛgɛli kɛ jamu kan walasa ka a dɔn ni bana dɔ bɛ aw la min bɛ sɔrɔ ciyɛn fɛ, o bɛ aw bila farati la ka kansɛri wɛrɛw sɔrɔ.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Yala an bɛna kuma kuru min man ca, n’a bɛ wele ko Feochromocytome bi wa?
Banaw ni cogoyaw5 zuluye 2026

Yala an bɛna kuma kuru min man ca, n’a bɛ wele ko Feochromocytome bi wa?

Yala tansiyɔn jiginni barikama bɛ i la tuma dɔw la wa? Walima i bɛ sumaya dɔrɔn wa? Yala i bɛ kungolodimi sɔrɔ ni dusukun bɛ kirin wa? Aw kana teliya kojugu k’a miiri ko nin fɛn damadɔw ye bana jugumanba ye. Nka, ni nin taamasiɲɛ ninnu bɛ to senna, kɛrɛnkɛrɛnnenya la ni tansiyɔn jiginni ye min kunbɛnni ka gɛlɛn, a ka ɲi aw ka hami dɔɔni. Bi an bɛna kuma bana dɔ kan min man ca dɔɔni, nka ni a sɛgɛsɛgɛra ka ɲɛ, a bɛ se ka furakɛ ka ɲɛ kosɛbɛ. O bɛ wele ko feochromocytome.

Feochromocytoma ye mun ye? An k’a faamu cogo nɔgɔman na.

N’an y’a fɔ cogo nɔgɔman na, feochromocytome ye kuru ye min bɛ sɔrɔ sugunɛbara cɛmancɛ yɔrɔ la, n’o ye sugunɛbaralabana ye. O kurukuruw bɛ sɔrɔ farikolokisɛ suguya kɛrɛnkɛrɛnnen dɔ fɛ min bɛ wele ko kuromafini selilu. O farikolokisɛw bɛ ɔrimɔni dɔw Bɔ joli la minnu ka kan an farikolo ka "kɛlɛ walima boli" jaabi la. Aw ye miiri a la, ni aw barika banna walima ni aw ye degun caman sɔrɔ, fɛn minnu bɛ yeli kɛ aw fari la - aw dusukun tantanni bɛ bonya, aw bɛ sumaya, aw farikolo bɛ yɛrɛyɛrɛ - o ɔrimɔni ninnu de bɛ o kɛ.

A ka ca a la, feochromocytoma bɛ sɔrɔ sugunɛbaralabana kelen dɔrɔn de la. Nka, tuma dɔw la, a bɛ se ka kɛ ɲɛgɛnɛsira fila bɛɛ la. A bɛ se ka kɛ ko kuru ka ca ni kelen ye glande kelen kɔnɔ.

Nafa min b’a la, o ye ko feyokɔrɔmositoma fanba tɛ bana jugu ye (u tɛ bana jugu ye) . O kɔrɔ ye k’u tɛ jɛnsɛn farikolo yɔrɔ wɛrɛw la. Nka, 10% ni 15% cɛ bɛ se ka kɛ kansɛri ye. Ni nin ye kansɛribana ye, a ɲɛfɔlen don kuluba caman na, ka kɛɲɛ ni a jɛnsɛnna cogo ye:

  • Feochromocytome localisé : Tumu bɛ sɔrɔ sugunɛbaralabana kelen dɔrɔn de la walima a fila bɛɛ la.
  • Feochromocytome régional : Kansɛri jɛnsɛnna ɲɛgɛnɛsiraw la minnu bɛ sugunɛbaralabana kɛrɛfɛ walima farikolo yɔrɔ wɛrɛw la.
  • Feochromocytome metastatique : Kansɛri jɛnsɛnna farikolo yɔrɔ janw na i n’a fɔ sugunɛ, fogonfogon walima kolo.
  • Feochromocytoma min bɛ segin ka kɛ : Kansɛri seginna ka na furakɛli kɔfɛ. A bɛ se ka kɛ yɔrɔ kelen na a tun bɛ yɔrɔ min na ka kɔn o ɲɛ walima yɔrɔ wɛrɛ la.

O sugunɛbaralabanaw ye mun ye an farikolo la? U ka baara ye mun ye?

An bɛ ni surɔfiyen fila ye. U bɛ sɔrɔ an kɔnɔbara kɔ fɛ, an ka sugunɛ sanfɛ, i n’a fɔ finimugu. U ye an ka endocrine system (banakisɛfagalanw) yɔrɔ dɔ ye. Surɔfiyen kelen-kelen bɛɛ bɛ ni yɔrɔba fila ye. Kɛnɛma yɔrɔ bɛ wele ko surɔfiyen, cɛmancɛ yɔrɔ bɛ wele ko surɔfiyen.

An ka sugunɛbaralabana bɛ ɔrimɔni kulu dɔ dilan min bɛ wele ko katekolaminiw. O ɔrimɔni ninnu bɛ taabolo nafama caman ɲɛnabɔ an farikolo la:

  • Dusukun tantanni
  • Tansiyɔn jiginni
  • Joli sukaro hakɛ `(Joli sukaro)`
  • An farikolo bɛ degun jaabi cogo min na ("kɛlɛ walima boli" jaabi) .

Katekolamini suguya kunbabaw ye:

  • Dopamine (dopamine) ye
  • Epinefirini (Adrenaline) `(Epinephrine / Adrénaline)`
  • Norepinephrine (Noradrenaline) `(Norepinephrine / Noradrénaline)`

Ni feochromocytoma bɛ yen, a bɛ se ka nin ɔrimɔni ninnu caman bɔ joli la, adrénaline ni noradrenaline, ka tɛmɛ a mago kan. O waati de la taamasiɲɛ suguya caman bɛ daminɛ ka bɔ kɛnɛ kan.

Danfara jumɛn bɛ Feochromocytoma ni Paraganglioma cɛ?

Ninnu ye kuru suguya fila ye minnu bɔlen don ɲɔgɔn fɛ kosɛbɛ, minnu man ca. U fila bɛɛ bɛ bɔ kuromafini selilɛri kelenw na, an ye baro kɛ minnu kan ka tɛmɛ. Nka, feochromocytoma bɛ sɔrɔ sugunɛbara cɛmancɛ yɔrɔ la (surénaux medulla), ka sɔrɔ paraganglioma bɛ sɔrɔ yɔrɔ wɛrɛw la surɔfiyen kɔkan .

Jɔn de ka teli ka nin bana in sɔrɔ? A ka ca cogo di?

Feochromocytoma bɛ se ka sɔrɔ si hakɛ bɛɛ la, nka a ka ca mɔgɔw la minnu si bɛ san 30 ni san 50 cɛ.

nin ye kuru ye min man ca kosɛbɛ . A ka gɛlɛn ka a fɔ tigitigi nin bana in bɛ mɔgɔ hakɛ min na. Ikomi mɔgɔ dɔw tɛ taamasiɲɛ foyi jira, a bɛ se ka kɛ bana in ma dɔn. A jateminɛna ko tansiyɔn jiginni bɛ mɔgɔ minnu na, olu hakɛ tɛ se 1% ma.

Feochromocytoma bɛ mɔgɔ min na, o bɛ taamasiɲɛ jumɛnw jira?

Feochromocytome taamasiɲɛw bɛ sɔrɔ ni kuru ye adrénaline (épinephrine) walima noradrenaline (norepinephrine) ɔrimɔni caman bɔ joli la. Nka, kuru dɔw tɛ o ɔrimɔni caman bɔ, wa a bɛ se ka kɛ ko taamasiɲɛ tɛ u la.

A taamasiɲɛ minnu ka teli ka ye, olu ye:

  • Tansiyɔn jiginni (Tansiyɔn jiginni): O de ye a taamasiɲɛba ye. Tuma dɔw la, a ka gɛlɛn ka a kunbɛn.
  • Kungolodimi: A bɛ se ka kɛ kungolodimi jugumanba ye, min bɛ kɛ yɔrɔnin kelen.
  • Sumaya kojugu kun tɛ a la.
  • Dusukun tantanni ye dusukun tantanni teliya ye, min tɛ kɛ tuma bɛɛ, walima min bɛ kɛ ni dusukun tantanni ye.
  • K’a ye ko i farikolo bɛ yɛrɛyɛrɛ.

Taamasiɲɛ minnu ka teli ka sɔrɔ:

  • Disi ni/walima kɔnɔdimi.
  • Fari bɛ barika kɛ ka ɲɛ ka tɛmɛ a cogo kɔrɔ kan.
  • Dusukunnata ni/walima fɔɔnɔ.
  • Kɔnɔboli.
  • Kɔnɔja.
  • Tansiyɔn jiginni orthostatique ye tansiyɔn jiginni barikama ye ni aw wulila. O kɔrɔ ye ko i ɲɛnamini bɛ kɛ ni i wulila yɔrɔnin kelen ka bɔ i sigiyɔrɔ la.
  • Kisɛya dɔgɔyali kun tɛ.

Nin taamasiɲɛ ninnu bɛ se ka bɔ walima ka juguya ko dɔw kɔfɛ. I n'a fo:

  • Farikoloɲɛnajɛ jugumanba.
  • Farikolo jogin walima hakili degun jugumanba.
  • Den bangeli.
  • Anestezi sɔrɔli.
  • Opereli kɛli.
  • Dumuni minnu nafa ka bon tiramini na (misali la, diwɛn bilenman, sokola, foromazi).

Yala a taamasiɲɛw bɛ yen tuma bɛɛ wa? Walima u bɛ na ka taa wa?

Feochromocytoma bɛ mɔgɔ min na , tansiyɔn jiginni bɛ se ka kɛ a la, walima a bɛ se ka na ka taa .

Mɔgɔ dɔw bɛ se ka "paroxysmal attacks" sɔrɔ, walima bana taamasiɲɛw bɛ se ka barika sɔrɔ. O kɔrɔ ye ko tansiyɔn bɛ bonya yɔrɔnin kelen, ka fara a taamasiɲɛw kan i n’a fɔ kungolodimi juguman, dusukun tantanni caya, ani sumaya kojugu. O "bìnkanni" ninnu bɛ Se ka Kɛ siɲɛ caman tile kɔnɔ, walima hali siɲɛ kelen walima siɲɛ fila kalo kɔnɔ.

Nafama: Ni nin taamasiɲɛ ninnu dɔ bɛ aw la, kɛrɛnkɛrɛnnenya la tansiyɔn jiginni barikama, kungolodimi, sumaya, ani dusukun tantanni, a nafa ka bon kosɛbɛ aw ka dɔgɔtɔrɔ ka ladilikan ɲini.

Mun na feochromocytoma bɛ sɔrɔ? O sababu ye mun ye?

A ka ca a la, sababu kɛrɛnkɛrɛnnen tɛ se ka sɔrɔ feyokɔrɔmositoma la. A bɛ kɛ k’a sɔrɔ a ma kɛ cogo si la.

Nka, 25% fo 35% la, o bana in bɛ tali kɛ cɛya banaw la. A kunbaba dɔw ye ninnu ye:

  • Endocrine néoplasie multiple 2 syndrome, suguya A ni B (MEN2A ni MEN2B) .
  • Von Hippel-Lindau (VHL) ka bana
  • Neurofibromatose suguya fɔlɔ (NF1) .
  • Paragangliome héritage (banakisɛfagalan) min bɛ sɔrɔ cɛya la
  • Carney-Stratakis dyad [paraganglioma ani kɔnɔbara basigilen kuru (GIST)].
  • Carney triad (paraganglioma, GIST ani fogonfogonlabana) .

Ka fara o jamu cogoyaw kan, feyokɔrɔmositoma fana bɛ se ka sɔrɔ ka da fɛn caman sɛgɛsɛgɛli kan jamu suguya 10 la dɔgɔmannin.

Nin bana in bɛ dɔn cogo di? (Sɛgɛsɛgɛli) .

Feochromocytoma sɔrɔli bɛ se ka gɛlɛya barisa a ye kuru ye min man teli ka sɔrɔ, wa tuma dɔw la a tɛ taamasiɲɛ foyi lase mɔgɔ ma. Tuma dɔw la, kuru in bɛ sɔrɔ a danma sɛgɛsɛgɛli dɔ senfɛ min kɛra kun wɛrɛ la.

Kun caman bɛ yen minnu b’a to dɔgɔtɔrɔ bɛ se ka siga nin bana in na:

  • Aw ta donFurakɛcogo tariku ɲɛfɔlen, kɛrɛnkɛrɛnnenya la ni denbaya kɔnɔ mɔgɔ dɔ ye feyokɔrɔmositɔmu sɔrɔ ka kɔrɔ.
  • Farikolo ni furakɛli sɛgɛsɛgɛli dafalen.
  • Taamaʃyɛn kɛrɛnkɛrɛnnen dɔw , misali la an kumana "attaques paroxysme" minnu kan ani tansiyɔn jiginni min tɛ kunbɛn furakɛlicogo nɔgɔmanw fɛ.

Sɛgɛsɛgɛli sugu jumɛnw bɛ kɛ?

Aw ka dɔgɔtɔrɔ bɛ se ka nin sɛgɛsɛgɛli ninnu fɔ aw ye walasa ka a dɔn ni feochromocytoma bɛ aw la:

  • Sugunɛ sɛgɛsɛgɛli lɛri 24 kɔnɔ : O ye ka aw ka sugunɛ lajɛ tile bɛɛ kɔnɔ ani ka katekolamini hakɛ jateminɛ a kɔnɔ. A bɛ fɛnw fana suman minnu bɛ bɔ ni o ɔrimɔni ninnu tiɲɛna. Ni o hakɛw cayara ka tɛmɛ a cogo kɔrɔ kan, o bɛ se ka kɛ feyokɔrɔmositɔmu taamasiɲɛ ye.
  • Joli katekolamini sɛgɛsɛgɛliw : Olu bɛ katekolamini hakɛ jateminɛ joli la. I n’a fɔ sugunɛ sɛgɛsɛgɛli, u bɛ fɛnw fana ɲini minnu bɛ sɔrɔ ɔrimɔni tiɲɛni fɛ.
  • CT scan (Computer Tomography scan): O bɛ kɛ ka X-ray kɛ ka tugu ɲɔgɔn na walasa ka ja caman dilan i farikolo kɔnɔna na. Aw ka dɔgɔtɔrɔ bɛ se ka nin fɔ aw ye walasa ka aw ka sugunɛbilenniw lajɛ.
  • MRI scan (MRI - Magnetic Resonance Imaging): O bɛ kɛ ni magɛnni ye, arajo fiɲɛw ani ɔridinatɛri ye walasa ka farikolo kɔnɔna ja caman dilan. A bɛ kɛ fana ka sugunɛbaralabanaw sɛgɛsɛgɛ.

Ni bana in tiɲɛna, sɛgɛsɛgɛli wɛrɛw bɛ se ka kɛ walasa ka a dɔn ni kuru in ye kansɛri ye (bana jugumanba) walima ni bana juguman don (bana jugumanba), ani ni a jɛnsɛnna farikolo yɔrɔ wɛrɛw la.

Mun na jamu sɛgɛsɛgɛli nafa ka bon?

Ni a sɔrɔla ko feochromocytome bɛ aw la, a ka c’a la, aw ka dɔgɔtɔrɔ bɛna a fɔ aw ye ko aw ka ladilikanw ni sɛgɛsɛgɛli kɛ jamu kan walasa ka a dɔn ni bana dɔ bɛ aw la min bɛ sɔrɔ ciyɛn fɛ, o bɛ aw bila farati la ka kansɛri wɛrɛw sɔrɔ.

Jɛnkulu sɛgɛsɛgɛli bɛ se ka kɛ nin ko suguw la:

  • Ni taamasiɲɛw bɛ aw walima aw ka denbaya kɔnɔmɔgɔ dɔ la minnu bɛ tali kɛ feochromocytoma héritage walima paraganglioma syndrome la.
  • Ni kuruw bɛ aw ka sugunɛbaralabana fila bɛɛ la.
  • Ni kuru ka ca ni kelen ye sugunɛbaralabana kelen na.
  • Ni katekolamini hakɛ cayalenba taamasiɲɛw bɛ joli la.
  • Ni feochromocytoma sɔrɔla ka kɔn san 40 ɲɛ.

Ni jamu sɛgɛsɛgɛli y’a ye ko jamu caman yeli ye, jamu ladilikɛla bɛ se k’a fɔ aw ye ko aw ka denbaya kɔnɔmɔgɔ tɔw (minnu taamasiɲɛ tɛ u la nka farati bɛ minnu na) fana ka o sɛgɛsɛgɛli kɛ.

Feochromocytoma furakɛcogo jumɛnw ye?

O furakɛcogo ɲuman ye ka opereli kɛ ka kuru bɔ, ni a bɛ se ka kɛ .

Furakɛli sugandili bɛ bɔ fɛn caman na:

  • Tumu hakɛ.
  • Ni kuru in ye kansɛri ye (a jugumanba) walima a man ɲi (bana jugumanba).
  • Ni taamasiɲɛw bɛ yen ka a sababu kɛ katekolamini ɔrimɔni caya ye.
  • Yala kuru bɛ ​​dan yɔrɔ kelen na wa, walima a jɛnsɛnna farikolo yɔrɔ wɛrɛw la wa? (A bɛ taa yɔrɔ wɛrɛw la) .
  • Ni bana in sɔrɔla a siɲɛ fɔlɔ la, walima ni a seginna ka kɛ furakɛli tɛmɛnen kɔfɛ.

Ni bana taamasiɲɛw bɛ aw la ka a sababu kɛ sugunɛbilenni ɔrimɔni caya ye, aw ka dɔgɔtɔrɔ bɛ se ka furaw di aw ma walasa ka o taamasiɲɛw kunbɛn. I n'a fo:

  • Fura minnu bɛ tansiyɔn to a cogo la, i n’a fɔ alfa-blokantiw.
  • Fura minnu bɛ dusukun tantanni to a cogo la, i n’a fɔ beta-blokantiw.
  • Fura minnu bɛ ɔrimɔni nɔw bali minnu bɛ bɔ ka tɛmɛ sugunɛbaralabana fɛ.

Feochromocytoma furakɛcogo kunbabaw ye:

  • Operelikɛyɔrɔ
  • Furakɛli min bɛ kɛ ni fiɲɛ ye
  • Chimiothérapie (banakisɛfagalanw) furakɛli
  • Ablation furakɛli
  • Embolisasi furakɛli
  • Furakɛli min ɲɛsinnen don a ma

Aw ni aw ka dɔgɔtɔrɔso jɛkulu bɛna fara ɲɔgɔn kan ka furakɛli bolodacogo dɔn min ka fisa aw ma.

Furakɛli fɛɛrɛ kunbabaw

  • Operelikɛyɔrɔ:

Nin ye feyokɔrɔmositɔmu furakɛli kunba ye. kuru 90% ɲɔgɔn bɛ se ka bɔ opereli fɛ ka ɲɛ .

Dɔgɔtɔrɔ bɛ se ka opereli fɔ aw ye walasa ka aw ka sugunɛbaralabana kelen walima u fila bɛɛ bɔ (surénalectomie). Opereli senfɛ, operelikɛla bɛna a lamini yɔrɔw ni ɲɛgɛnɛsiraw sɛgɛsɛgɛ walasa ka a dɔn ni kuru jɛnsɛnna. Ni a y’a sɔrɔ, u bɛna o fɛnɲɛnamafagalan bɔ, ni a bɛ se ka kɛ.

Opereli kɔfɛ, aw joli walima aw ka sugunɛ bɛna sɛgɛsɛgɛ walasa ka katekolamini hakɛ dɔn. Ni a hakɛ seginna a cogo kɔrɔ la, o kɔrɔ ye ko feyokɔrɔmositoma selilɛriw bɛɛ bɔra.

Ni sugunɛbilenni fila bɛɛ bɔra, aw bɛna ɔrimɔni furakɛli kɛ aw ka ɲɛnamaya bɛɛ kɔnɔ walasa ka ɲɛgɛnɛsiralabanaw ka ɔrimɔni minnu bɛ bɔ, olu bila u nɔ na.

  • Furakɛli min bɛ kɛ ni fiɲɛ ye:

Nin ye fura ye min bɛ kɛ ka kansɛribanakisɛw faga walima ka u bali ka bonya. O bɛ kɛ cogo la min tɛ tiɲɛni kɛ farikolo yɔrɔ kɛnɛmanw na ka se a dan na.

Fiɲɛdimi furakɛli suguya fila bɛ yen:

  • Kɛnɛya furakɛli : Fiɲɛ bɛ lase kansɛri yɔrɔ la ka bɔ masin dɔ la min bɛ farikolo kɔkan.
  • Kɔnɔna na furakɛli : Fɛn min bɛ kɛ ni fiɲɛ ye, o bɛ pake pikirijikɛlanw, kisɛw, nɛgɛw walima katetɛriw kɔnɔ ka dɔgɔtɔrɔ dɔ don kansɛri yɔrɔ la walima a kɛrɛfɛ.

Fiɲɛdimi furakɛli suguya bɛ bɔ kansɛri yɔrɔ la, sigida la, a bɛ taa yɔrɔ wɛrɛw la, walima ni a bɛ segin ka kɛ. Feochromocytoma jugumanba bɛ furakɛ ka caya ni kɛnɛyaji ye min bɛ kɛ ni kɛnɛyaji ye ani/walima ni 131I-MIBG furakɛli ye. 131I-MIBG ye fɛnɲɛnamafagalan ye min bɛ nɔrɔ kansɛribana dɔw la ka u faga.

  • Chimiothérapie (banakisɛfagalanw) :

O bɛ furaw kɛ ka kansɛribanakisɛw faga, ka u bali ka tila ka caya, walima ka kansɛri falenni dabila. A ka ca a la, fura ninnu bɛ di jolisira fɛ. Hali ni nin ye furakɛli ɲɛnama ye, a bɛ se ka kɔlɔlɔw lase mɔgɔ ma.

  • Ablation furakɛli:

Nin ye furakɛli ye min tɛ fɛn caman kɛ. A bɛ funteni jugumanba walima nɛnɛba kɛ ka kurukuruw tiɲɛ.

  • Radiofréquence ablation : Radiofrequence ablation bɛ kɛ ni arajo fiɲɛw ye walasa ka kansɛribanakisɛw ni farikolokisɛ minnu tɛ cogoya la, olu sumaya ani ka u tiɲɛ.
  • Cryoablation : A bɛ kɛ ni azote jilama walima gazi ɲuman jilama ye walasa ka kansɛribanakisɛw ni farikolokisɛ minnu tɛ cogoya la, olu sumaya ani ka u tiɲɛ.
  • Embolization furakɛli:

O la, joli sira min bɛ joli lase surɔfiyen ma, o bɛ datugu. O bɛ joli boli dabila ka taa ɲɛgɛnɛsira la, ka kansɛribanakisɛw faga minnu bɛ falen yen.

  • Furakɛli min ɲɛsinnen don a ma:

O bɛ kɛ ni furaw walima fɛn wɛrɛw ye minnu bɛ kansɛribanakisɛw dɔrɔn de kɛlɛ kɛrɛnkɛrɛnnenya la k’a sɔrɔ u ma tiɲɛni kɛ farikolokisɛ kɛnɛmanw na. Nin furakɛli in bɛ kɛ feyokɔrɔmositoma (feochromocytome) la min bɛ taa yɔrɔ wɛrɛw la ani min bɛ segin ka kɛ.

Tirosini kinase inhibiteur dɔ min bɛ wele ko sunitinib, o bɛ ka sɛgɛsɛgɛ feochromocytoma metastatique (feochromocytome) la min bɛ taa yɔrɔ wɛrɛw la. O fura ninnu bɛ tumuw falenni bali.

Yala nin bana in bɛ se ka kunbɛn wa?

A fɔ man di nka, fɛɛrɛ si tɛ yen min bɛ se ka feyokɔrɔmositoma bali . Nka, ni farati bɛ aw la ka nin bana in sɔrɔ ka a sababu kɛ ciyɛntalanw ni jamu ye, jamu ladilikanw bɛ se ka dɛmɛ don sɛgɛsɛgɛli ni a dɔnni joona la.

Ni aw ka denbaya kɔnɔmɔgɔ gɛrɛgɛrɛ dɔw (balimakɛw, bangebagaw) ye feyokɔrɔmositɔmu sɔrɔ, walima ni aw ka jamu bana dɔ bɛ aw la i n’a fɔ an ye baro kɛ minnu kan ka tɛmɛ (Multiple endocrine neoplasia 2 syndrome, Von Hippel-Lindau (VHL) bana, Neurofibromatose type 1 (NF1), Hereditary paraganglioma syndrome, Carney-Stratakis dyad, Carney triad), a nafa ka bon kosɛbɛ ka kuma i ka dɔgɔtɔrɔ fɛ o ko la.

Furakɛli kɔfɛ, a bɛ se ka kɛnɛya cogo di? (Pronostic) (Kɔrɔfɔcogo) .

A ka ca a la, feokɔrɔmositoma (pheochromocytome) ɲɛfɔli ka ɲi kosɛbɛ ni a furakɛra.An y’a fɔ kaban ko kuru 90% ɲɔgɔn bɛ se ka bɔ opereli fɛ ka ɲɛ.

Nka, ni o bana ma furakɛ, o bɛ se ka kɛ sababu ye ka gɛlɛyabaw lase mɔgɔ ma, hali minnu bɛ se ka mɔgɔ ka ɲɛnamaya bila farati la . I n'a fo:

  • Dusukun tantanni (Cardiomyopathie).
  • Mikorokaridi (mikorocardite) bɛ sɔrɔ
  • Joli bɔli kunsɛmɛ na min tɛ kunbɛn (Cerebral hemorrhaging) .
  • Ji ka dalajɛ fogonfogon la (Fogonfogon la sɔgɔsɔgɔninjɛ) .

Feochromocytoma banabagatɔ dɔw fana bɛ se ka kirin walima ka dusukun tantanni sɔrɔ.

Tuma jumɛn na ne ka kan ka taa dɔgɔtɔrɔso la?

  • Ni a sɔrɔla ko feyokɔrɔmositoma bɛ aw la ani ni taamasiɲɛ gɛlɛn o taamasiɲɛ bɛ aw la, aw bɛ taa dɔgɔtɔrɔso la joona.
  • Ni feochromocytoma taamasiɲɛw bɛ aw la, i n’a fɔ tansiyɔn jiginni ani kungolodimi, aw bɛ kuma aw ka dɔgɔtɔrɔ fɛ. Hali ni feokɔrɔmositoma man teli ka kɛ, a nafa ka bon ka tansiyɔn jiginni furakɛ.
  • Ni aw b’a dɔn ko aw somɔgɔw dɔ (balimakɛw, bangebagaw) ka jamu bana dɔ bɛ a la i n’a fɔ `Multiple endocrine neoplasia 2 syndrome` walima `Von Hippel-Lindau (VHL) disease`, aw bɛ se ka kɛ fana ko faratiba bɛ aw la ka feochromocytoma sɔrɔ, o la aw bɛ taa dɔgɔtɔrɔso la walasa ka baro kɛ jamu sɛgɛsɛgɛli kan.

Ne ka kan ka ɲininkali jumɛnw kɛ dɔgɔtɔrɔ la?

Ni a sɔrɔla ko feochromocytoma bɛ aw la, a bɛ se ka kɛ ko a bɛ aw dɛmɛ ka nin ɲininkali ninnu kɛ aw ka dɔgɔtɔrɔ la:

  • Mun na ne ye feochromocytoma sɔrɔ?
  • Yala ne denw ni/walima ne somɔgɔw bɛ se ka feochromocytoma sɔrɔ wa?
  • Furakɛli suguya jumɛnw bɛ ne bolo?
  • Furakɛli suguya wɛrɛw kɔlɔlɔ jumɛnw bɛ yen?
  • Ne bɛ se ka ne ka bana taamasiɲɛw kunbɛn cogo di?

A laban na, fɛn minnu nafa ka bon kosɛbɛ an ka kan ka to an hakili la (Take-Home Message) .

O bɛ ɲɛ, o la, hali ni feyokɔrɔmositɔmu ye kuru ye min man teli ka sɔrɔ, a ka ca a la, a man ɲi ani a bɛ se ka furakɛ . Ani fana, a bɛ se ka boli denbayaw kɔnɔ, o la ni nin bana in sɔrɔla aw walima aw ka denbaya kɔnɔmɔgɔ dɔ la, a nafa ka bon aw ka jamu sɛgɛsɛgɛli kɛ. O bɛ se ka dɛmɛ fana ka a dɔn ni farati bɛ aw la kɛnɛyako gɛlɛya wɛrɛw la.

Aw ye aw hakili to a la ko ni ɲininkali dɔw bɛ aw fɛ feyokɔrɔmositoma sɔrɔli farati kan walima nin bana in kan, aw kana siran ka kuma aw ka dɔgɔtɔrɔ fɛ. U bɛ yan walisa k’aw dɛmɛ. Aw ka to kɛnɛya la!


Feochromocytoma , surɔfiyen, katekolamini, tansiyɔn jiginni, kungolodimi, sumaya, kuru, endocrine system

Frequently Asked Questions (FAQ)

Sɛgɛsɛgɛli sugu jumɛnw bɛ kɛ?

Aw ka dɔgɔtɔrɔ bɛ se ka nin sɛgɛsɛgɛli ninnu fɔ aw ye walasa ka a dɔn ni feochromocytoma bɛ aw la:

Mun na jamu sɛgɛsɛgɛli nafa ka bon?

Ni a sɔrɔla ko feochromocytome bɛ aw la, a ka c’a la, aw ka dɔgɔtɔrɔ bɛna a fɔ aw ye ko aw ka ladilikanw ni sɛgɛsɛgɛli kɛ jamu kan walasa ka a dɔn ni bana dɔ bɛ aw la min bɛ sɔrɔ ciyɛn fɛ, o bɛ aw bila farati la ka kansɛri wɛrɛw sɔrɔ.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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