Esi nèle ŋku lém ɖe viwò si wodzi yeyee ŋu la, ɖe nède dzesii kpɔ be eƒe ŋutilã le ɣie viea? Zi geɖe la, vidzĩ yeye akpa gãtɔ xɔa aɖuɖɔtoe vie le kwasiɖa ɖeka alo eve gbãtɔwo me, eye zi geɖe la, esia nu yina le ŋkeke ʋɛ aɖewo megbe. Gake ɖe nèbu viwòa ƒe aɖuɖɔ ƒe amadede ŋu kpɔa? Ɣeaɖewoɣi la, edzena abe ɖe wòle ɣie alo le ɣie enea? Ne èkpɔ nu siawo evea siaa ɖekae la, mègaflu wò nàsusu be esɔ o. Elabena ate ŋu anye nɔnɔme sesẽ aɖe si woyɔna be Biliary Atresia, si ŋu míele nu ƒom tsoe egbea ƒe dzesi.
Kpuie ko la, nukae nye Biliary Atresia?
Bu aklã si le míaƒe ŋutilã me be enye dɔwɔƒe sue aɖe. Dɔwɔƒe sia wɔa tsi si woyɔna be "bile" abe gbeɖuɖɔ ene. Aɖuɖɔtoe sia tso aklãa me toa mɔ̃ nyui aɖe ŋutɔ me (aɖuɖɔtoewo) eye wòwua enu ɖe míaƒe dɔgbo suea me. Dɔ vevi eve le Bile si. Ðekae nye be woakpe asi ɖe gbeɖuɖɔ siwo míedi o ɖeɖeɖa le ŋutilãa me ŋu. Bubue nye be wòakpe ɖe mía ŋu míaɖu nuɖuɖu siwo míeɖuna, vevietɔ ami, eye míaxɔ nunyiame siwo míaƒe ŋutilã hiã.
Biliary Atresia nye nɔnɔme si me ʋuka si me ʋu sina tona si me ʋu sina tona la xena alo medzɔna nyuie le vidzidzi me o. Esia fia be mɔ aɖeke meli si dzi ʋumenugbagbeviɣidɔ si dona le aklãa me ato ado o, eye wòtsia aklãa me boŋ. Esia le abe gbeɖuɖɔ tsɔtsɔ ƒu gbe ƒe mɔwo katã xexe le dugã aɖe me ene. Gbeɖuɖɔawo katã ƒoa ƒu ɖe dua me, eye wogblẽa du bliboa me. Ne ʋumenugbagbeviɣia ge ɖe aklãa me la, edzea nu gblẽ le aklãa ŋu vevie.
Esia nye nɔnɔme sesẽ aɖe si dzea vidzĩ suewo dzi le woƒe ɣleti ʋɛ gbãtɔwo me. Ne womedae kaba o la, ate ŋu agblẽ nu le aklã ŋu vevie eye aklã nawɔ dɔ nyuie gɔ̃ hã.
Gake mègatsi dzi o. Atikeŋutinunya de ŋgɔ ŋutɔ fifia. Ne wokpɔ nɔnɔme sia kaba la, amekoko ate ŋu ana mɔ yeye aɖe nasu ʋuka me sisi. Esia tae wòle vevie ŋutɔ be nànya dzesi siawo ɖo.
Nukawoe nye Biliary Atresia ƒe dzesi veviwo?
Zi geɖe la, dzesi siawo dzea egɔme le kwasiɖa ʋɛ aɖewo megbe tso esime wodzi vidzĩa. Abe dzilawo ene la, ele be mialé ŋku ɖe esia ŋu vevie.
| Dzesi si dzena | Nuɖᴐɖᴐ |
|---|---|
| Ŋutilã kple ŋku ƒe ɣie (Jaundice) . | Esiae nye dzesi vevitɔ kple gbãtɔ. Vidzĩa ƒe ŋutigbalẽ kple ŋku ɣiwo trɔna zua ɣie. Togbɔ be ʋusɔgbɔdɔ sɔ na vidzĩ yeyewo hã la, enye nuxlɔ̃amedzesi ne enɔ anyi wu kwasiɖa eve. |
| Aɖuɖɔ si me kɔ o | Esia hã nye dzesi vevi aɖe ŋutɔ. Zi geɖe la, aɖuɖɔ ƒe amadede nyea ɣi, blɔ, alo amadede dzẽ le ʋumenugbagbeviɣi ta. Esi ʋumenugbagbeviɣi mele dɔgboa me ɖom o ta la, vidzĩa ƒe aɖuɖɔ nyea beige dzẽ, ɣie, alo anyikpe. Ðɔktawo yɔa esiawo be "acholic stools." |
| Aɖuɖɔ doviviti | Ne ʋumenugbagbeviɣi, si ƒoa ƒu ɖe aklã me, gena ɖe ʋukawo me eye wòɖenɛ to ayikuwo me la, vidzĩa ƒe aɖuɖɔ va zua amadede ɣi alo aŋutiɖiɖi. |
Dzesi bubu siwo dzena le ɣeyiɣi aɖe megbe
Kaka viwòa naxɔ abe kwasiɖa 6 va ɖo 10 ene la, dzesi siawo hã ate ŋu adze:
- Ŋutilã si le ʋuʋum: Ʋumenugbagbeviɣidɔ ƒe ƒoƒo ɖe ŋutilãa me ate ŋu ana ŋutigbalẽa naʋuʋu vevie.
- Avifafa enuenu kple dzikudodo: Le ŋutilã ƒe vevesese ta la, vidzĩa ate ŋu ado dziku eye wòafa avi enuenu.
- Dzedzeme: Ne ʋumenugbagbeviɣi mele nuɖuɖua me o la, womeɖua nuɖuɖu nyuie o, eyata ŋutilãa mexɔa nunyiamewo o. Esia wɔe be vidzĩa melolona nyuie o.
- Ƒodo ƒe vuvu: Aklãa gblẽ eye tsi tea yɔyɔ ɖe ƒodoa me, si wɔnɛ be ƒodoa dona ɖe gota hevuvuna.
Nukatae Biliary Atresia dzɔna?
Nyabiasewo le dzila geɖe si abe, "Nukatae nusia dzɔ ɖe mía vi dzi?" "Ðe míewɔ nu gbegblẽ aɖea?" Numekulawo meka ɖe nusi gbɔ esia tsona dzi 100% haɖe o.
Gake susu vevitɔe nye be domenyiŋusẽfianu ƒe tɔtrɔ si dzɔna le ʋumenugbagbeviɣiwo ƒe wɔwɔme me esime vidzĩa le tsitsim le vidadaa ƒe dɔme gbɔe nɔnɔme sia tsona. Nu vevitɔe nye be esia menye nusi ƒe dome wonyi tso dzilawo gbɔ na ɖevia o. Azɔ hã, menye nane si nèwɔ alo gblɔ le fufɔɣi gbɔe nɔnɔme sia tsona o. Eyata mègatsi dzi ɖe eŋu alo abu fɔ ɖokuiwò o.
Kuxi kawoe ate ŋu ado mo ɖa ne womewɔ atike nɛ o?
Biliary atresia nye dɔléle si hiã be woawɔ atike nɛ enumake. Ne wohe atikewɔwɔ ɖe megbe la, ate ŋu ahe kuxi sesẽwo vɛ.
- Aklã ƒe gbegblẽ tegbee (Cirrhosis):Ʋumenugbagbeviɣidɔ atraɖii nana aklãmenugbagbeviwo kuna, aklãa xɔa abi, eye wòzua abe kpe ene. Esia ate ŋu ana aklã ƒe dɔwɔwɔ nabu keŋkeŋ.
- Ʋusɔgbɔdɔ si le agbo nu: Ne aklãa xɔ abi la, ʋu si sina toa eme la xea mɔ, si wɔnɛ be ʋu ƒe sisi le ʋuka siwo tsɔa ʋu yia aklã me la me.
- Ascites: Tsi dzea ƒoƒo ɖe ƒodoa me le aklã ƒe dɔmawɔmawɔ nyuie kple ʋusɔgbɔdɔ si le agbo nu ta.
- Aklã ƒe lolome: Aklã vuvu eye wòlolona le ʋumenugbagbeviɣidɔ kple abixɔxɔ ta.
- Nuɖuɖutome ƒe Vovototo: Ʋusɔgbɔdɔ si le agbo nu ate ŋu ana ʋuka siwo le nuɖuɖutome navuvu eye woagbã. Esia ate ŋu ana ʋu nado le ememe vevie si ate ŋu ade ame ƒe agbe afɔku me.
Esiawo katã ate ŋu ana aklã nawɔ dɔ nyuie o. Gake ne ède dzesi dzesiawo kaba, yi ɖɔkta gbɔ, eye nèdze atikewɔwɔ gɔme la, woate ŋu axe mɔ ɖe kuxi siawo dometɔ geɖe nu.
Aleke woawɔ anya dɔlélea? (Dɔléle ƒe dzesi) .
Ne viwòa ƒe aɖuɖɔtoedɔ wu kwasiɖa eve, alo ne èsusu be woƒe aɖuɖɔwo le ɣie la, yi ɖeviwo ƒe dɔdala gbɔ enumake. Ðɔktaa ado viwòa kpɔ gbã.
- Eléa ŋku ɖe ŋutigbalẽ kple ŋkuwo ƒe ɣie hã ŋu.
- Woatsɔ asi alé ŋku ɖe eŋu be dɔgboa vuvu alo aklãa lolo hã.
Le ema megbe la, woɖea gbe be woawɔ dodokpɔ geɖe atsɔ aɖo kpe dɔlélea dzi.
| Dodokpɔ | Woɖe eme kpuie |
|---|---|
| Ʋudodokpɔwo | Wowɔa dodokpɔ siawo tsɔ léa ŋku ɖe aklã ƒe dɔwɔwɔ ŋu, bilirubin agbɔsɔsɔme si le ʋua me (nusi gbɔ ʋusɔgbɔdɔ tsona), kple nenye be aklãa gblẽ hã. |
| Ƒodo ƒe ultrasound scan | Esia kpena ɖe ame ŋu wòkpɔa aklã, aɖuɖɔtoe, kple ʋumenugbagbeviɣimɔ̃wo ƒe nɔnɔme tso gota. |
| HIDA ƒe scan dodokpɔ | Esia nye scan tɔxɛ aɖe. Le afisia la, wodoa tsi tɔxɛ aɖe (tracer) ɖe ŋutilãa me eye wozãa fotoɖemɔ̃ tsɔ léa ŋku ɖe alesi wòzɔna kple ʋumenugbagbeviɣi si tso aklãa me ŋu. Ne ʋumenugbagbeviɣia mele sisim ɖe dɔgboa me o la, ate ŋu aɖo kpe edzi be ʋukaa xe. |
| Liver biopsy (aklã ƒe akpa sue aɖe dodokpɔ) . | Ne ehiã la, wozãa aŋe sue aɖe ŋutɔ ɖea lãkusi sue aɖe ŋutɔ le aklãa me eye wodoa wo kpɔna le nusuekpɔmɔ̃ me. Esia ate ŋu akpe ɖe ame ŋu wòanya ne tɔtrɔ aɖewo koŋ le aklãmenugbagbevi siwo do ƒome kple biliary atresia ŋu. |
| Cholangiogram si wowɔna le dɔwɔwɔ na ame me | Esia nye dodokpɔ si wowɔna le amekoko me. Amekolaa doa amadede tɔxɛ aɖe ɖe aɖuɖɔtoea me eye wòtsɔa X-ray léa ŋku ɖe eŋu. Ne amadedea meto dɔgboa me o la, kakaɖedzi li 100% be ʋumenugbagbeviɣia xe. Ne nenemae la, wowɔa atike nɛ le amekokoa wɔɣi. |
Atikewɔwɔ ƒe mɔnu: Kasai ƒe Dɔwɔwɔ
Atike vevitɔ kple gbãtɔ si wozãna na Biliary Atresia enye Kasai ƒe Dɔwɔna . Esia menye dɔléle si woate ŋu atsɔ atike adae o.
Kpuie ko la, le amekoko sia me la, amekolaa ɖea ʋuka si xe la ɖa, tsɔa vidzĩa ŋutɔ ƒe dɔgbo sue ƒe akpa sue aɖe, eye wòtsɔnɛ doa ka kple aklãa tẽ. Esia le abe mɔ gbagbã aɖe ɖeɖe ɖa eye woawɔ ‘mɔ si dzi woato’ yeyee ɖe eteƒe ene. To mɔ yeye sia dzi la, ʋumenugbagbeviɣidɔ si dona le aklã me la dzea sisi gɔme yia dɔgboa me tẽ.
Zi alesi wowɔ amekoko sia kaba la, zi nenemae emetsonuwo kpɔa dzidzedzee. Vevietɔ ne woate ŋu awɔ dɔ sia hafi vidzĩa naxɔ ɣleti 3 , eye ne anya wɔ le ɣleti gbãtɔ me la, mɔnukpɔkpɔ si li be woaɖe aklãa ƒe gbegblẽ dzi akpɔtɔ eye woakpɔ dzidzedze la lolo wu sã.
Le amekokoa megbe la, vidzĩa ƒe aɖuɖɔtoea nu fa vivivi, aɖuɖɔ ƒe amadede gatrɔna va nɔa abe tsã ene, eye vidzĩa ƒe kpekpeme tea dzidziɖedzi ne nuɖuɖumeŋusẽ le nyonyom ɖe edzi.
Gake, ɖe Kasai amekoko nye egbɔkpɔnu si anɔ anyi ɖaa?
Zi geɖe la, Kasai ƒe amekoko menye agbemeŋkekewo katã ƒe egbɔkpɔnu o. Elabena ate ŋu agblẽ nu le aklãa ŋu xoxo hafi woawɔ dɔ nɛ. Nusiwo gblẽ ma ate ŋu adzi ɖe edzi vivivi le ɣeyiɣi aɖe megbe.
Ðevi geɖe siwo wowɔ dɔ na le Kasai la ahiã be woado aklã na wo le woƒe ɖevime alo woƒe ƒewuiwo me. Gake esia menye nusi wòle be woavɔ̃ na o. Egbea la, aklã dodo na ame kpɔa dzidzedze ŋutɔ. To esia dzi la, mɔnukpɔkpɔ sua ɖevia si be wòanɔ agbe si me lãmesẽ blibo le, si anɔ anyi eteƒe nadidi.
Aleke mi, abe dzilawo ene, mieléa be na mia vi?
Ne èva nya be Biliary Atresia le viwòa ŋu la, ate ŋu ase le eɖokui me abe wò xexeame katã le tɔtrɔm ene. Ɣeyiɣi sesẽ aɖe ŋutɔe wònye. Gake menye wò ɖeka koe o. Atikewɔlawo ƒe ƒuƒoƒoa aɖe nusianu me na wò eye woakpe ɖe ŋuwò.
- Nuɖuɖu Tɔxɛ: Be ɖɔktaa nakpɔ egbɔ be vidzĩa le nunyiame nyuitɔ xɔm la, ana notsi tɔxɛwo, vitaminwo, kple nunyiame bubuwo.
- Atikewɔwɔ ƒe ŋkuléle ɖe vidzĩa ŋu ɣeyiɣi didi: Ele be woakplɔ vidzĩa ayi atikewɔƒea le ŋkeke siwo woɖo ɖi dzi. Ðɔktaa alé ŋku ɖe vidzĩa ƒe tsitsi kple aklã ƒe dɔwɔwɔ ŋu edziedzi.
- Dzesi siwo ŋu wòle be nàlé ŋku ɖo le amekoko vɔ megbe: Ne èkplɔ viwòa va aƒeme le vidzidɔ ƒe dɔwɔwɔ vɔ megbe la, lé ŋku ɖe dzesi siawo ŋu.
- Asrã
- Ne ŋutilãa gazu ɣie (jaundice) .
- Ne aɖuɖɔa gazu ɣie alo aɖuɖɔa do viviti
Ne èkpɔ nane si le abe esia ene la, yɔ wò ɖɔkta enumake.
- Bu ɖokuiwò hã ŋu kpɔ: Ðeɖi te ŋuwò ŋutɔ le susu kple ŋutilã siaa me le nusiawo katã ta. Bia kpekpeɖeŋu tso ƒometɔwo kple xɔlɔ̃wo gbɔ. Di ɣeyiɣi na ɖokuiwò nàɖi ɖe eme ahadɔ alɔ̃. Azɔ hã, nuƒoƒo kple dzila bubu siwo si vi le la anye ŋusẽtsoƒe gã aɖe na wò.
Gbedasi si Wotsɔ Yi Aƒeme
- Ne vidzĩ si wodzi yeyee ƒe jaundice (yellowing) nɔa anyi wu kwasiɖa eve , mègabui be esɔ o.
- Ne viwòa ƒe aɖuɖɔ le ɣie, ɣie, alo le abe anyi ene la , ke enye dzesi sesẽ aɖe.
- Ne ède dzesi dzesi siwo le etame dometɔ ɖeka alo evea siaa la, mègahe ɖe megbe o eye nàyi ɖeviwo ƒe dɔdala gbɔ enumake.
- Le Biliary Atresia gome la, dɔlélea didi kaba kple eɖoɖo kaba be woawɔ dɔ nɛ (Kasai Procedure) le vevie ŋutɔ na ɖevia ƒe etsɔme.
- Menye wò vodada aɖeke gbɔe nɔnɔme sia tso o. Menye dɔléle si ƒe dome wonyi tso dzilawo gbɔ na ɖeviwo o.

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