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Ðe gbɔgbɔ sesẽna le viwò suea ŋu alea? Mina míaƒo nu tso "Double Aortic Arch" ŋu!

Ðe gbɔgbɔ sesẽna le viwò suea ŋu alea? Mina míaƒo nu tso "Double Aortic Arch" ŋu!

Ðe viwò suea sena le eɖokui me ɣeaɖewoɣi be gbɔgbɔ le fu ɖem nɛa? Ðe wòtsia nu ne ele nu ɖum alo le no nam? Alo ɖe wòwɔa toɣliɖeɖe wɔnukuwo ne ele gbɔgbɔm? Togbɔ be esiawo ate ŋu anye ɖevimedɔléle siwo bɔ hã la, nɔnɔme aɖe si nu sẽ wu, gake woate ŋu adae, ate ŋu anɔ megbe na esia. Nɔnɔme mawo dometɔ ɖeka si mebɔ o gake wòle vevie be woanya nu tso eŋue nye "Double Aortic Arch." Mina míaƒo nu tso eŋu tsitotsito egbea.

Kpuie ko la, ʋuka vevitɔ si tsɔa ʋu tso viwòa ƒe dzi me yia eƒe ŋutilã ƒe akpa mamlɛae nye aorta . Zi geɖe la, enyea nugo ɖeka si lolo. Woyɔa ʋuka sia ƒe akpa si le gogloe le dzia tame be aortic arch .

Gake le vidzĩ si si "Double Aortic Arch" le me la, "aortic arch" sia dzɔna ɖe eve me. Eyae nye be ʋuka bubu aɖe do ƒome kple "aortic arch" vevi sia, si wɔa aɖaka evelia. Aɖaka eve siawo va kpena, eye wowɔa asigɛ aɖe ƒoa xlã vidzĩa ƒe yaƒoƒomɔ̃ (yagbɔgbɔ) kple nuɖuɖudoƒe (nutome) . Bu eŋu kpɔ, nukae adzɔ ne woxe mɔ na asigɛ sia? Ɣemaɣie vidzĩa dzea dzesi sesẽwo abe gbɔgbɔ sesẽ, toɣliɖeɖe ne ele gbɔgbɔm, kple nuɖuɖu mimi sesẽ ene.

"Aortic arch" sia dzɔna le fufɔfɔ ƒe gɔmedzedze ŋutɔ, le kwasiɖa eve va ɖo adre dome. Le ɣeyiɣi sia me la, dzia kple ʋukawo tsina le mɔ si me kɔ ŋutɔ nu. Akpa aɖewo dzɔna, eye le ɣeyiɣi aɖe megbe la, womegahiãna o eye wobuna. "Double aortic arch" la dzɔna le nane si le abe esia ene ta. Anɔ abe fufɔfɔ ƒe kwasiɖa atɔ̃lia ene la, ʋuka aɖe si wòle be wòabu hafi, le susu aɖe si womenya o ta, mebuna o eye "double aortic arch" sia dzɔna. Esia nye dzidɔ si wodzina , si fia be wodzia vidzĩa kplii.

Nɔnɔme sia si woyɔna be "double aortic arch" la le dzitodzito me dɔléle siwo wodzina ƒe ƒuƒoƒo aɖe si woyɔna be "vascular rings" me. Esiawo nana vidzĩa ƒe yaƒoƒomɔ̃ kple nuɖuɖutome tsina.

Nukae nye "ʋukawo ƒe asigɛ" siawo?

Enyo, "Vascular Rings" nye, abe alesi megblɔe va yi ene la, nɔnɔme siwo me "aortic arch" tsina le mɔ si mesɔ o nu, si ateŋu ana vidzĩa ƒe yaƒoƒomɔ̃ (trachea), nuɖuɖu ƒe pɔmpi (esophagus), alo evea siaa natsi. Esiawo nye dzidɔ siwo wodzina siwo mebɔ kura o . Bu eŋu kpɔ, wodzia vidzĩ siwo ade ɖeka le 100 ɖesiaɖe me kple dzidɔ ƒomevi aɖe si wodzina. Gake vidzĩ ɖeka le 10,000 ɖesiaɖe me koe "ʋukawo ƒe asigɛ" gblẽa nu le. Enye nusi mebɔ nenema gbegbe o.

Nukae nye "Vascular Rings" ƒomevi veviwo?

"Ʋukawo ƒe asigɛ" siawo ƒomevi vevi geɖewo li. Na míakpɔ nusiwo wonye ɖa:

  • Double Aortic Arch: Le esia me la, "aortic arches" eve (miame kple ɖusime) ƒoa xlã yaƒoƒo kple nuɖuɖutome. Esiae nye nyati vevitɔ si ŋu míele nu ƒom tsoe.
  • Right aortic arch with aberrant left subclavian artery and left ligamentum: Aortic arch ɖeka le afisia, gake ele yagbɔgbɔ ƒe ɖusime (zi geɖe la, ele miame). Le go sia me la, miame ƒe asike te ʋuka si naa ʋu yia vidzĩa ƒe abɔwo la dzea egɔme tso ʋuka si me ʋu sina tona me eye wòtoa yagbɔgbɔ kple nuɖuɖutome megbe. Wowua ʋuka ƒe asigɛ sia nu ne ewɔ ɖeka kple miame ligamentum arteriosus, si nye ʋuka aɖe ƒe susɔe si nɔ fugboea ƒe agbenɔɣi eye emegbe wòbuna.
  • Left aortic arch with aberrant right subclavian artery: Le afisia la, ɖusime subclavian artery toa yaƒoƒo kple nuɖuɖutome megbe, eye wòmia wo.
  • Innominate artery compression: Innominate (brachiocephalic) ʋuka nye ʋuka si me ʋu sina tona ƒe alɔdze aɖe. Le go sia me la, edzea egɔme tso yaƒoƒoa ƒe miame, emegbe wòtoa yaƒoƒoa ŋgɔ yia ɖusime. Esia dea nyaƒoɖeamenu ɖe ​​yaƒoƒomɔ̃a dzi.
  • Aklã ƒe ʋuka ƒe ʋuƒo: Miame aklã ƒe ʋuka dzea egɔme tso ɖusime aklã ƒe ʋuka me eye wòtoa yagbɔgbɔ kple nuɖuɖutome dome.

Nusi dzɔna le nusiawo katã mee nye be yaƒoƒomɔ̃ alo nuɖuɖutome ŋu gblẽa nu le eŋu le mɔ aɖe nu.

Ðe "Double Aortic Arch" ƒomevi aɖewo lia?

Ẽ, "double aortic arch" ƒomevi vevi etɔ̃e li. Wodea vovototo esiawo me to aɖaka si lolo wu, kple nenye be aɖaka ma si lolo wu la le yagbɔgbɔ ƒe ɖusime alo miame.

  • Dominant right arch with a small left arch: Esiae nye ƒomevi si bɔ wu, eye wòdzɔna le go siwo ade 80 le alafa me me.
  • Miame ƒe aɖaka si xɔ aƒe ɖe eme si me ɖusime aɖaka sue aɖe le: Wokpɔa esia le nɔnɔme siwo ade 10 le alafa me me.
  • Aɖaka siwo da sɔ: Wokpɔa esia hã le ame siwo ade 10 le alafa me me.

"Ʋukawo ƒe asigɛ" ƒomevi kae wokpɔna wu?

Ðɔktawo susuna tsã be "double aortic arch" ye nye "vascular ring" ƒomevi si bɔ wu. Gake numekuku yeyewo ɖee fia be le nyateƒe me la , "right aortic arch" bɔ wu.

Gake nu bubu aɖe hã gali. Vidzĩ siwo ŋu "ɖusime aortic arch" le la ate ŋu akpɔ dzi ƒe gbɔdzɔgbɔdzɔ bubuwo si wodzina wu vidzĩ siwo si "double aortic arch" le. Gake anɔ eme be womekpɔa dɔlélea le wo dzi le wo dziɣi o. Esia le alea elabena "right aortic arch" ateŋu mahe dzesiwo vɛ le gɔmedzedzea me o. Eyata ate ŋu ahiã be woawɔ dɔ na ame le kuxi sia ta ne woxɔ ɣleti 6 va ɖo 18.

Nɔnɔme aɖe si woyɔna be ``Double Aortic Arch'' ye nye ʋukawo ƒe asigɛ ƒomevi si bɔ wu . Eyata viwòa ƒe ɖɔkta ate ŋu anya kuxia kaba. Ne wotsɔ vidzĩ siwo ŋu ʋukawo ƒe asigɛ ƒomevi bubuwo le sɔ kple vidzĩ siwo ŋu ``Double Aortic Arch'' le ate ŋu ahiã be woawɔ dɔ na wo le wo dzidzi megbe kpuie.

Nukae nye "Double Aortic Arch" ƒe dzesiwo?

Zi geɖe la, "double aortic arch" ƒe dzesiwo dzena ne wozi vidzĩa ƒe yaƒoƒomɔ̃, nuɖuɖutome, alo evea siaa dzi. Nutete sia ate ŋu akpɔ ŋusẽ ɖe vidzĩa ƒe gbɔgbɔ, nuɖuɖu, alo dzi ƒe dɔwɔwɔ dzi.

Zi geɖe la, dzesi siawo dzena le ɖevime (vevietɔ ne nɔnɔmea nu sẽ), gake ɣeaɖewoɣi la, woate ŋu adze le ƒe etɔ̃ xɔxɔ me ke, alo le ƒewuiwo me gɔ̃ hã.

Woate ŋu abu ɖevi aɖewo vodadatɔe be asrã le wo ŋu elabena dzesiawo sɔ. Ne asrãdɔdada do kpo nu eye wogawɔ dodokpɔ bubuwo ko hafi wokpɔa nɔnɔmea.

Yagbɔgbɔ ƒe dzesiwo

Vidzĩ kple ɖevi siwo ŋu "double aortic arch" le dometɔ siwo ade 91 le alafa me xɔa dzesi siawo siwo do ƒome kple gbɔgbɔ. Woawoe nye:

  • Gbeɖiɖi wɔnuku aɖe ne wole gbɔgbɔm (gbeɖiɖi sesẽ aɖe si woyɔna be `stridor` alo gbeɖiɖi si le ʋuʋum si woyɔna be `wheezing`) .
  • Kɔdzi si ɖi "nutrenu ƒe ɣlidodo." Esia sɔ kple kɔdzidɔ si dzɔna le nɔnɔme aɖe si woyɔna be "croup" me.
  • Yagbɔgbɔ ƒe akpa si le ete ƒe dɔlékuiwo xɔxɔ enuenu .

Dɔgbo kple dɔgbo ƒe dzesiwo

Vidzĩwo kple ɖevi siwo ŋu "double aortic arch" le dometɔ siwo ade 40 le alafa me kpɔa nuɖuɖumeŋusẽ ƒe dzesi siawo. Wo dometɔ aɖewoe nye:

  • Aɖuɖɔtoe ne èle no nam alo le nu nam.
  • Nu mimi sesẽ (nuɖuɖu ƒe kuxi) . Zi geɖe la, esia dzena ne vidzĩa dze nuɖuɖu sesẽwo ɖuɖu gɔme vɔ.
  • Lolo dzi ɖeɖe kpɔtɔ sesẽ .
  • Nuɖuɖu si trɔna yia dzi yia ŋɔti me (`Regurgitation/reflux`) .

Dzi ƒe dzesiwo

Vidzĩwo kple ɖevi siwo ŋu "double aortic arch" le dometɔ siwo ade 30 le alafa me xɔa dzidɔ ƒe dzesiwo. Esiawo dometɔ aɖewoe nye:

  • Akɔtave .
  • Dzi ƒe gbeɖiɖi si mesɔ o (`Dzi ƒe liʋiliʋilili`) .
  • Ŋutilã si le blɔ (cyanosis) .

Nukae hea "Double Aortic Arch" vɛ?

Womeke ɖe nusi tututu gbɔ "double otic arch" tsona ŋu haɖe o . Togbɔ be wokpɔa nɔnɔme sia zi geɖe le vidzĩ siwo wofɔ to "in-vitro fertilization" (IVF) me hã la, womenya nusi tututu gbɔ wòtso o.

Woate ŋu atsɔ double aortic arch hã asɔ kple atikewɔwɔ me nɔnɔme bubuwo. Vidzĩ siwo ƒe aortic arch eve le dometɔ siwo ade 12 le alafa me ƒe dzi ƒe dɔmawɔmawɔ nyuie bubu si wodzina, abe ventricular septal defect (VSD) kple tetralogy of Fallot ene . Tsɔ kpe ɖe eŋu la, domenyiŋusẽfianu ƒe nɔnɔmewo abe chromosome 22q11 deletion kple trisomy 21 (Down syndrome) ene le vidzĩ siwo ƒe aortic arch eve le dometɔ siwo ade 20 le alafa me ŋu .

Aleke woawɔ ade dzesi "Double Aortic Arch"?

Wokpɔa aortic arch eve le vome alo ne dzesiawo dze egɔme. Ɣeaɖewoɣi la, wokpɔnɛ le vo me le fufɔɣi, le vidzidzi megbe, alo le nɔnɔmetatawo dodokpɔ siwo wowɔ le susu bubu aɖe ta me. Tso ƒe 2004 me la, amesiwo wokpɔna be dɔléle sia le wo ŋu to fotoɖeɖe me le fufɔɣi dzi ɖe edzi. Esia ɖea vi ŋutɔ, elabena woate ŋu awɔ ɖoɖo ɖe atikewɔwɔ ŋu ne wonya dzi vidzĩa ko.

Alo, woate ŋu akpɔe ne dzesiawo dze le vidzĩa dzidzi vɔ megbe. Viwòa ƒe ɖɔkta aƒo nu tso dzesiawo ŋu na wò eye emegbe wòawɔ dodokpɔ aɖewo.

Dodokpɔwo be woatsɔ anya "Double Aortic Arch".

Dodokpɔ vevi siwo wozãna tsɔ dea dzesi dɔléle siae nye:

  • Akɔta ƒe X-ray: Zi geɖe la, esiae nye dodokpɔ gbãtɔ si wowɔna.
  • CT-dɔdamɔnu.
  • Echocardiogram (Echo) dodokpɔ: Esia kpena ɖe ame ŋu wu le enyanya me ne dzi ƒe gbɔdzɔgbɔdzɔ bubuwo li hã.
  • MRI (MRI) dodokpɔ.

Ɣeaɖewoɣi la, woate ŋu awɔ aɖuɖɔtoemekpɔmɔ̃ atsɔ ado vidzĩa ƒe yaƒoƒomɔ̃ kpɔ. Woate ŋu awɔ esia le gbɔgbɔtsixe ƒoƒo me hafi woakpɔe be aortic arch eve le eŋu. Alo, woate ŋu awɔe hafi woawɔ dɔ nɛ be wòakpe ɖe amekolaa ŋu wòanya nusi gbɔ kuxia tso.

Domenyiŋusẽfianu dodokpɔ kpena ɖe ame ŋu wòdea dzesi domenyiŋusẽfianu ƒe nɔnɔmewo.

Aleke woawɔ ada "Double Aortic Arch"?

Ele be woawɔ dɔ na ame be woatsɔ aɖɔ "double aortic arch" ƒe nɔnɔmea ɖo. Le vidzĩ siwo me dzesi aɖeke mele o gɔ̃ hã gome la, amekoko nyo wu ne woxɔ tso ɣleti 6 va ɖo 9. Vidzĩ siwo ŋu dzesiwo le, vevietɔ ne dzesiawo nu sẽ la, ate ŋu ahiã be woawɔ dɔ na wo kaba gɔ̃ hã.

Bu eŋu kpɔ ko, wode dzesi nɔnɔme si nye "double aortic arch" zi gbãtɔ le ƒe 1737. Wowɔ amekoko gbãtɔ nɛ le ƒe 1947. Aleke gbegbe míeva ɖo tso ɣemaɣi! Vidzĩ siwo ŋu vidzidzi ƒe gbɔdzɔgbɔdzɔ sia le te ŋu nɔa agbe didi, le lãmesẽ me le amekoko ta.

"Double Aortic Arch" amekoko

"Double Aortic Arch" amekokoa le dedie ŋutɔ, eye emetsonuwo kpɔ dzidzedze ŋutɔ . Mahiã be woatsɔ viwòa aƒo ka na "dzitodzito ƒe mɔxenu" (dzi kple aklã ƒe mɔ̃) o .

Wozãa mɔnu aɖe si woyɔna be "lateral thoracotomy" tsɔ wɔa amekokoa. Esia fia be amekolaa tsoa vidzĩa ƒe akɔta ƒe akpa ɖeka, le akɔta eve dome. Wowɔa esia zi geɖe le miame, elabena afimae vidzĩ akpa gãtɔ ƒe akɔtaƒu sue "si kpe ɖe eŋu" ma le. Nɔnɔmetatawo dodokpɔ siwo wowɔna do ŋgɔ na amekokoa nana amekolaa te ŋu léa ŋku ɖe vidzĩa ƒe ŋutilã ƒe akpa si le eme ŋu nyuie eye wòwɔa ɖoɖo ɖe amekokoa ŋu wòsɔ ɖe enu.

Amekolaa zãa "ligating and dividing" mɔnu . Esia fia be woblaa aɖaka suea be wòatɔ te ʋu si dona to eme. Emegbe wolãnɛ hetsɔa aŋe blanɛ. Wogbugbɔa nu sia wɔna vaseɖe esime aɖakaʋua ma keŋkeŋ eye yaƒoƒomɔ̃a kple nuɖuɖutome ƒe nyaƒoɖeamenu nu nayi.

Viwòa anɔ kɔdzi abe kwasiɖa ɖeka ene, emegbe ahaya eye wòatrɔ ava aƒeme.

"Kommerell diverticulum" (`Kommerell diverticulum - KD`) ƒe atikewɔwɔ

Ƒã hafi nane si woyɔna be "Kommerell diverticulum (KD)" ate ŋu anɔ vidzĩ aɖewo siwo ŋu "double aortic arch" hã si. Esia bɔ ɖe vidzĩ siwo ŋu "ɖusime ʋuka ƒe akɔta" le wu, gake mebɔ ŋutɔ le "ʋuka eve ƒe akɔta" hã gome.

`KD` sia nye `aneurysm`, ʋuka si dona le `aorta` si ɖiɖina me le `aortic arch` gbɔ. Ʋuʋudedi sia ate ŋu axɔ teƒe eye wòate ɖe vidzĩa ƒe yaƒoƒomɔ̃ kple nuɖuɖu ƒe pɔmpi dzi. Ðewohĩ mahe kuxi aɖeke vɛ enumake o. Ke hã, amekolawo lɔ̃a esia hã ɖeɖeɖa ne wole `double aortic arch` wɔm be woaxe mɔ ɖe kuxiwo nu emegbe.

Dzidɔ bubuwo dada

Ne dzidɔ bubu aɖewo le viwòa ŋu si hiã be woawɔ dɔ nɛ la, woate ŋu adae le ɣeyiɣi ɖeka me kple aortic arch eve. Esia ateŋu abia be woawɔ dɔ si woyɔna be ``median sternotomy'' , si bia be woatso akɔta ƒe titina. Viwòa ƒe amekola adzro tiatia nyuitɔ si nàwɔ na wò me, le nya siwo gbɔ wòle be woakpɔ nu.

Kuxi kawoe ate ŋu ado tso amekoko me?

Afɔku si le kuxi siwo dona tso ʋuka eve ƒe dɔwɔwɔ me la le sue ŋutɔ . Ƒã hafi vidzĩa ate ŋu ana nuɖuɖu alo gbɔgbɔtsixe tsia enu. Ne gbɔgbɔmekuxi aɖewo li siwo nɔa anyi ɖaa la, zi geɖe la, wo nu yina le ƒe ɖeka me le amekokoa megbe.

Kuxi siwo dona tso amekoko be woatsɔ aɖɔ ʋuka ƒe akpa eve kple dzi ƒe gbɔdzɔgbɔdzɔ bubuwo ɖo me ate ŋu ato vovo. Dzro afɔku kple kuxi siawo katã me kple viwòa ƒe amekola.

Ðe woate ŋu axe mɔ ɖe "Double Aortic Arch" nua?

Ao, womate ŋu axe mɔ ɖe nɔnɔme si woyɔna be "double aortic arch" nu o . Enye nusi dona le fufɔfɔ ƒe gɔmedzedze eye wònɔa anyi le edziɣi.

Nukae nye amesiwo ŋu "Double Aortic Arch" le ƒe etsɔme?

Vidzĩwo kple ɖevi siwo wowɔ dɔ na "Double Aortic Arch" ƒe etsɔme nyui aɖe ŋutɔ . Woate ŋu anɔ agbe ahaƒo wo ɖokui ɖe nuwɔna siwo sɔ me mɔxeɖenu aɖeke manɔmee.

Le amekokoa megbe la, viwòa ate ŋu ayi edzi anɔ gbɔgbɔm toɣliɖeɖe vaseɖe ƒe ɖeka. Esia le alea elabena vidzĩa ƒe yaƒoƒomɔ̃ metsi bliboe o le "double aortic arch" ta. Eyata, axɔ ɣeyiɣi aɖe hafi yaƒoƒomɔ̃a nasẽ ɖe edzi.

Ƒã ŋutɔ la, gbɔgbɔtsixe ƒe dzesiwo ate ŋu anɔ vidzĩwo kple ɖeviwo ŋu wu ƒe ɖeka le amekokoa megbe.

Nu vevitɔe nye be nàkplɔ viwòa ayi aɖadoe kpɔ edziedzi eye nàgblɔe na wò ɖɔkta ne dzesi aɖewo le ŋuwò si yia edzi. Beléle na ɖevi ɖesiaɖe si wowɔ dɔ na le dzitodzito me ɣeyiɣi didi ƒe beléle le vevie ŋutɔ.

Ɣekaɣie wòle be maƒo ka na vinyea ƒe ɖɔkta?

Ne ède dzesi dzesi yeye aɖewo, alo ne edze abe dzesi siwo li xoxo la le sesẽm ɖe edzi ene la, ƒo nu kple viwòa ƒe ɖɔkta enumake. Vidzĩwo kple ɖevi suewo trɔna ale gbegbe be ate ŋu asesẽ ɣeaɖewoɣi be woanya nusi sɔ kple nusi mesɔ o. Gake ne kɔdzi ma si le abe nutrenu ene alo gbeɖiɖi si le ʋuʋum le viwòa ŋu la, gblɔe na wò ɖɔkta enumake. Ate ŋu anye ɖevimedɔléle si sɔ. Gake ƒã hafi ate ŋu anye dzidɔ si le ŋusẽ kpɔm ɖe viwòa ƒe gbɔgbɔ ƒe ŋutete dzi ƒe dzesi.

Ɣekaɣie wòle be nàƒo ka na 911 (xexlẽdzesi si le nudzɔdzɔ kpatawo me)?

"Double aortic arch" ate ŋu ade nyaƒoɖeamenu si ate ŋu ade viwòa ƒe yaƒoƒomɔ̃ dzi si ate ŋu ade eƒe agbe afɔku me . Ne viwòa ƒe ŋutigbalẽ dze blɔ (cyanosis) , alo ne gbɔgbɔ le sesẽm na viwòa vevie la , ƒo ka na 911 enumake.

Nya kawoe wòle be mabia vinyea ƒe ɖɔkta?

Ne wokpɔe be "double aortic arch" le viwòa ŋu la, esɔ be nyabiase geɖe nanɔ asiwò. Ele vevie be nànya viwòa ƒe nɔnɔme, si me ɣeyiɣi si me wòhiã be woawɔ dɔ na viwòa hã le, kple nenye be lãmesẽkuxi bubu aɖewo le viwòa ŋu. Àte ŋu abia nyawo abe:

  • Ɣekaɣie wòle be woawɔ dɔ na vinyea?
  • Afikae wowɔa amekokoa le? Amekae le ewɔm?
  • Dzesi kawoe wòle be makpɔ nyuie le aƒeme?
  • Nukae mate ŋu awɔ be wòanɔ bɔbɔe na vinyea be wòanɔ aƒeme?
  • Ðe dzidɔ bubuwo le vinyea ŋua?
  • Ðe wòle be mado domenyiŋusẽfianu kpɔ na vinyea alo nye ƒomea me tɔ mamlɛawoa?
  • Aleke vinyea ƒe etsɔme anɔ?

Nukae nye "Aortic Arch Syndrome"? Ðe wòto vovo tso "Double Aortic Arch" gbɔa?

Ẽ, mègatɔtɔ ame eveawo o. "Aortic Arch Syndrome" nye "Vasculitis" ƒomevi aɖe si mebɔ kura o . Wogayɔnɛ be "Takayasu ƒe ʋukawo ƒe dɔléle" .

"Vasculitis" nye wò ʋukawo ƒe gliwo ƒe dɔdzẽ. Ate ŋu adzɔ le ʋuka ɖesiaɖe me, ʋuka suetɔ kekeake siwo nye ʋuka siwo me ʋu sina tona gɔ̃ hã me. "Takayasu ƒe ʋukawo ƒe dɔléle" nye ʋuka siwo lolo titina kple gãwo ƒe dɔdzẽ. Edzena zi geɖe le "aortic arch" kple eƒe alɔ gãwo me. Esia tae wogayɔnae be "aortic arch syndrome."

Takayasu ƒe ʋuka me dɔléle (si woyɔna hã be "aortic arch syndrome") dzɔna le sɔhɛ tsitsiwo kple sɔhɛ tsitsiwo me . Esia nye kuxi si to vovo kura tso "double aortic arch" si wodzina si ŋu míeƒo nu tsoe va yi gbɔ, eye atikewɔwɔ si hiã la to vovo.

Zi geɖe la, vidzĩ dzidzi nyea dzidzɔ kple azãɖuɖu ƒe ɣeyiɣi. Gake ne èva nya be dzidɔ aɖe le viwòa ŋu, le fufɔɣi alo le edziɣi megbe la, dzimaɖitsitsi kple kakaɖedzimanɔamesi va xɔna ɖe dzidzɔ ma teƒe. Ne ɖeko nèva nya be "double aortic arch" le viwòa ŋu teti koe nye ema la, ke ɖewohĩ èle nusi akplɔe ɖo ŋu bum.

Mega tsi dzi o. Wò atikewɔlawo ƒe ƒuƒoƒoa akpe ɖe ŋuwò le esiawo katã me afɔɖeɖe ɖesiaɖe. Èɖe afɔ gbãtɔ xoxo, si nye be nàsrɔ̃ nu geɖe tso viwòa ƒe nɔnɔmea ŋu. Nya nyuiae nye be aʋala ƒe akɔta eve ƒe dɔwɔwɔ le dedie ŋutɔ eye wòkpɔa dzidzedze. Ne dzidɔ alo domenyiŋusẽfianu ƒe nɔnɔme bubuwo le viwòa ŋu la, atikewɔwɔ ate ŋu asesẽ vie wu. Gake ne wowɔ ŋgɔyiyi le vidzĩ yeyewo dzi kpɔkpɔ me la, àte ŋu akpe ɖe viwòa ŋu wòakpɔ beléle si sɔ si wòhiã, ahaya, eye wòakpɔ dzidzɔ le ɖevime.

Eyata nu vevi kawo dzie wòle be míaɖo ŋkui le nusiwo ŋu míeƒo nu tsoe me? (Gbedasi si Wotsɔ Yi Aƒeme)

Enyo, mina míaƒo nu tso nusiwo wòle be wòanɔ susu me na wò la dometɔ aɖewo ŋu kpuie tso nusiwo ŋu míeƒo nu tsoe ku ɖe "Double Aortic Arch" sia ŋu:

  • "Double aortic arch" nye dzidɔ si wodzina . Vidzĩa ƒe ʋuka si me ʋu sina tona la mã ɖe aɖaka eve me, si wɔnɛ be yaƒoƒomɔ̃ kple nuɖuɖutome la tena ɖe edzi.
  • Dzesi vevitɔwoe nye gbɔgbɔ sesẽ, ʋuʋudedi, nu mimi sesẽ, kple gbɔgbɔtsixe ƒe dɔléle enuenu .
  • Wokpɔa nɔnɔme sia to dodokpɔwo abe `CT scan`, `MRI`, `Echocardiogram` me . Ɣeaɖewoɣi la, woate ŋu akpɔe le fufɔɣi gɔ̃ hã.
  • Atikewɔwɔae nye amekoko . Amekoko sia le dedie ŋutɔ eye wòkpɔa dzidzedze.
  • Na vidzĩa le amekoko vɔ megbeÀte ŋu anɔ agbe si sɔ, si me lãmesẽ le.
  • Ne dzesiwo abe gbɔgbɔ sesẽ alo eƒe ʋuʋu ene le viwòa ŋu la, di atikewɔlawo ƒe aɖaŋuɖoɖo enumake .
  • Mega tsi dzi o . Esi egbegbe atikewɔwɔ va le ŋgɔ yim la, woate ŋu ada dɔléle sia dzidzedzetɔe. Wò atikewɔlawo ƒe ƒuƒoƒoa ana kpekpeɖeŋu si nèhiã la wò.

` Double Aortic Arch, Dzidɔ si Wodzina, Ʋukawo ƒe Kpẽwo, Vidzĩwo ƒe Asphyxia, Vidzĩwo ƒe Lãmesẽ, Dzidɔ

Frequently Asked Questions (FAQ)

Nukae nye "Vascular Rings" ƒomevi veviwo?

"Ʋukawo ƒe asigɛ" siawo ƒomevi vevi geɖewo li. Na míakpɔ nusiwo wonye ɖa:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Womeɖo nya aɖeke ɖe amewo haɖe o. Tsɔ wò nyaŋuɖoɖo kpe ɖe afisia zi gbãtɔ.

Tsɔ wò nyaŋuɖoɖo kpee

Taflatse bu akɔnta be: 2 + 8 =
Ðe gbɔgbɔ sesẽna le viwò suea ŋu alea? Mina míaƒo nu tso "Double Aortic Arch" ŋu!

Ðe gbɔgbɔ sesẽna le viwò suea ŋu alea? Mina míaƒo nu tso "Double Aortic Arch" ŋu!

Ðe viwò suea sena le eɖokui me ɣeaɖewoɣi be gbɔgbɔ le fu ɖem nɛa? Ðe wòtsia nu ne ele nu ɖum alo le no nam? Alo ɖe wòwɔa toɣliɖeɖe wɔnukuwo ne ele gbɔgbɔm? Togbɔ be esiawo ate ŋu anye ɖevimedɔléle siwo bɔ hã la, nɔnɔme aɖe si nu sẽ wu, gake woate ŋu adae, ate ŋu anɔ megbe na esia. Nɔnɔme mawo dometɔ ɖeka si mebɔ o gake wòle vevie be woanya nu tso eŋue nye "Double Aortic Arch." Mina míaƒo nu tso eŋu tsitotsito egbea.

Kpuie ko la, ʋuka vevitɔ si tsɔa ʋu tso viwòa ƒe dzi me yia eƒe ŋutilã ƒe akpa mamlɛae nye aorta . Zi geɖe la, enyea nugo ɖeka si lolo. Woyɔa ʋuka sia ƒe akpa si le gogloe le dzia tame be aortic arch .

Gake le vidzĩ si si "Double Aortic Arch" le me la, "aortic arch" sia dzɔna ɖe eve me. Eyae nye be ʋuka bubu aɖe do ƒome kple "aortic arch" vevi sia, si wɔa aɖaka evelia. Aɖaka eve siawo va kpena, eye wowɔa asigɛ aɖe ƒoa xlã vidzĩa ƒe yaƒoƒomɔ̃ (yagbɔgbɔ) kple nuɖuɖudoƒe (nutome) . Bu eŋu kpɔ, nukae adzɔ ne woxe mɔ na asigɛ sia? Ɣemaɣie vidzĩa dzea dzesi sesẽwo abe gbɔgbɔ sesẽ, toɣliɖeɖe ne ele gbɔgbɔm, kple nuɖuɖu mimi sesẽ ene.

"Aortic arch" sia dzɔna le fufɔfɔ ƒe gɔmedzedze ŋutɔ, le kwasiɖa eve va ɖo adre dome. Le ɣeyiɣi sia me la, dzia kple ʋukawo tsina le mɔ si me kɔ ŋutɔ nu. Akpa aɖewo dzɔna, eye le ɣeyiɣi aɖe megbe la, womegahiãna o eye wobuna. "Double aortic arch" la dzɔna le nane si le abe esia ene ta. Anɔ abe fufɔfɔ ƒe kwasiɖa atɔ̃lia ene la, ʋuka aɖe si wòle be wòabu hafi, le susu aɖe si womenya o ta, mebuna o eye "double aortic arch" sia dzɔna. Esia nye dzidɔ si wodzina , si fia be wodzia vidzĩa kplii.

Nɔnɔme sia si woyɔna be "double aortic arch" la le dzitodzito me dɔléle siwo wodzina ƒe ƒuƒoƒo aɖe si woyɔna be "vascular rings" me. Esiawo nana vidzĩa ƒe yaƒoƒomɔ̃ kple nuɖuɖutome tsina.

Nukae nye "ʋukawo ƒe asigɛ" siawo?

Enyo, "Vascular Rings" nye, abe alesi megblɔe va yi ene la, nɔnɔme siwo me "aortic arch" tsina le mɔ si mesɔ o nu, si ateŋu ana vidzĩa ƒe yaƒoƒomɔ̃ (trachea), nuɖuɖu ƒe pɔmpi (esophagus), alo evea siaa natsi. Esiawo nye dzidɔ siwo wodzina siwo mebɔ kura o . Bu eŋu kpɔ, wodzia vidzĩ siwo ade ɖeka le 100 ɖesiaɖe me kple dzidɔ ƒomevi aɖe si wodzina. Gake vidzĩ ɖeka le 10,000 ɖesiaɖe me koe "ʋukawo ƒe asigɛ" gblẽa nu le. Enye nusi mebɔ nenema gbegbe o.

Nukae nye "Vascular Rings" ƒomevi veviwo?

"Ʋukawo ƒe asigɛ" siawo ƒomevi vevi geɖewo li. Na míakpɔ nusiwo wonye ɖa:

  • Double Aortic Arch: Le esia me la, "aortic arches" eve (miame kple ɖusime) ƒoa xlã yaƒoƒo kple nuɖuɖutome. Esiae nye nyati vevitɔ si ŋu míele nu ƒom tsoe.
  • Right aortic arch with aberrant left subclavian artery and left ligamentum: Aortic arch ɖeka le afisia, gake ele yagbɔgbɔ ƒe ɖusime (zi geɖe la, ele miame). Le go sia me la, miame ƒe asike te ʋuka si naa ʋu yia vidzĩa ƒe abɔwo la dzea egɔme tso ʋuka si me ʋu sina tona me eye wòtoa yagbɔgbɔ kple nuɖuɖutome megbe. Wowua ʋuka ƒe asigɛ sia nu ne ewɔ ɖeka kple miame ligamentum arteriosus, si nye ʋuka aɖe ƒe susɔe si nɔ fugboea ƒe agbenɔɣi eye emegbe wòbuna.
  • Left aortic arch with aberrant right subclavian artery: Le afisia la, ɖusime subclavian artery toa yaƒoƒo kple nuɖuɖutome megbe, eye wòmia wo.
  • Innominate artery compression: Innominate (brachiocephalic) ʋuka nye ʋuka si me ʋu sina tona ƒe alɔdze aɖe. Le go sia me la, edzea egɔme tso yaƒoƒoa ƒe miame, emegbe wòtoa yaƒoƒoa ŋgɔ yia ɖusime. Esia dea nyaƒoɖeamenu ɖe ​​yaƒoƒomɔ̃a dzi.
  • Aklã ƒe ʋuka ƒe ʋuƒo: Miame aklã ƒe ʋuka dzea egɔme tso ɖusime aklã ƒe ʋuka me eye wòtoa yagbɔgbɔ kple nuɖuɖutome dome.

Nusi dzɔna le nusiawo katã mee nye be yaƒoƒomɔ̃ alo nuɖuɖutome ŋu gblẽa nu le eŋu le mɔ aɖe nu.

Ðe "Double Aortic Arch" ƒomevi aɖewo lia?

Ẽ, "double aortic arch" ƒomevi vevi etɔ̃e li. Wodea vovototo esiawo me to aɖaka si lolo wu, kple nenye be aɖaka ma si lolo wu la le yagbɔgbɔ ƒe ɖusime alo miame.

  • Dominant right arch with a small left arch: Esiae nye ƒomevi si bɔ wu, eye wòdzɔna le go siwo ade 80 le alafa me me.
  • Miame ƒe aɖaka si xɔ aƒe ɖe eme si me ɖusime aɖaka sue aɖe le: Wokpɔa esia le nɔnɔme siwo ade 10 le alafa me me.
  • Aɖaka siwo da sɔ: Wokpɔa esia hã le ame siwo ade 10 le alafa me me.

"Ʋukawo ƒe asigɛ" ƒomevi kae wokpɔna wu?

Ðɔktawo susuna tsã be "double aortic arch" ye nye "vascular ring" ƒomevi si bɔ wu. Gake numekuku yeyewo ɖee fia be le nyateƒe me la , "right aortic arch" bɔ wu.

Gake nu bubu aɖe hã gali. Vidzĩ siwo ŋu "ɖusime aortic arch" le la ate ŋu akpɔ dzi ƒe gbɔdzɔgbɔdzɔ bubuwo si wodzina wu vidzĩ siwo si "double aortic arch" le. Gake anɔ eme be womekpɔa dɔlélea le wo dzi le wo dziɣi o. Esia le alea elabena "right aortic arch" ateŋu mahe dzesiwo vɛ le gɔmedzedzea me o. Eyata ate ŋu ahiã be woawɔ dɔ na ame le kuxi sia ta ne woxɔ ɣleti 6 va ɖo 18.

Nɔnɔme aɖe si woyɔna be ``Double Aortic Arch'' ye nye ʋukawo ƒe asigɛ ƒomevi si bɔ wu . Eyata viwòa ƒe ɖɔkta ate ŋu anya kuxia kaba. Ne wotsɔ vidzĩ siwo ŋu ʋukawo ƒe asigɛ ƒomevi bubuwo le sɔ kple vidzĩ siwo ŋu ``Double Aortic Arch'' le ate ŋu ahiã be woawɔ dɔ na wo le wo dzidzi megbe kpuie.

Nukae nye "Double Aortic Arch" ƒe dzesiwo?

Zi geɖe la, "double aortic arch" ƒe dzesiwo dzena ne wozi vidzĩa ƒe yaƒoƒomɔ̃, nuɖuɖutome, alo evea siaa dzi. Nutete sia ate ŋu akpɔ ŋusẽ ɖe vidzĩa ƒe gbɔgbɔ, nuɖuɖu, alo dzi ƒe dɔwɔwɔ dzi.

Zi geɖe la, dzesi siawo dzena le ɖevime (vevietɔ ne nɔnɔmea nu sẽ), gake ɣeaɖewoɣi la, woate ŋu adze le ƒe etɔ̃ xɔxɔ me ke, alo le ƒewuiwo me gɔ̃ hã.

Woate ŋu abu ɖevi aɖewo vodadatɔe be asrã le wo ŋu elabena dzesiawo sɔ. Ne asrãdɔdada do kpo nu eye wogawɔ dodokpɔ bubuwo ko hafi wokpɔa nɔnɔmea.

Yagbɔgbɔ ƒe dzesiwo

Vidzĩ kple ɖevi siwo ŋu "double aortic arch" le dometɔ siwo ade 91 le alafa me xɔa dzesi siawo siwo do ƒome kple gbɔgbɔ. Woawoe nye:

  • Gbeɖiɖi wɔnuku aɖe ne wole gbɔgbɔm (gbeɖiɖi sesẽ aɖe si woyɔna be `stridor` alo gbeɖiɖi si le ʋuʋum si woyɔna be `wheezing`) .
  • Kɔdzi si ɖi "nutrenu ƒe ɣlidodo." Esia sɔ kple kɔdzidɔ si dzɔna le nɔnɔme aɖe si woyɔna be "croup" me.
  • Yagbɔgbɔ ƒe akpa si le ete ƒe dɔlékuiwo xɔxɔ enuenu .

Dɔgbo kple dɔgbo ƒe dzesiwo

Vidzĩwo kple ɖevi siwo ŋu "double aortic arch" le dometɔ siwo ade 40 le alafa me kpɔa nuɖuɖumeŋusẽ ƒe dzesi siawo. Wo dometɔ aɖewoe nye:

  • Aɖuɖɔtoe ne èle no nam alo le nu nam.
  • Nu mimi sesẽ (nuɖuɖu ƒe kuxi) . Zi geɖe la, esia dzena ne vidzĩa dze nuɖuɖu sesẽwo ɖuɖu gɔme vɔ.
  • Lolo dzi ɖeɖe kpɔtɔ sesẽ .
  • Nuɖuɖu si trɔna yia dzi yia ŋɔti me (`Regurgitation/reflux`) .

Dzi ƒe dzesiwo

Vidzĩwo kple ɖevi siwo ŋu "double aortic arch" le dometɔ siwo ade 30 le alafa me xɔa dzidɔ ƒe dzesiwo. Esiawo dometɔ aɖewoe nye:

  • Akɔtave .
  • Dzi ƒe gbeɖiɖi si mesɔ o (`Dzi ƒe liʋiliʋilili`) .
  • Ŋutilã si le blɔ (cyanosis) .

Nukae hea "Double Aortic Arch" vɛ?

Womeke ɖe nusi tututu gbɔ "double otic arch" tsona ŋu haɖe o . Togbɔ be wokpɔa nɔnɔme sia zi geɖe le vidzĩ siwo wofɔ to "in-vitro fertilization" (IVF) me hã la, womenya nusi tututu gbɔ wòtso o.

Woate ŋu atsɔ double aortic arch hã asɔ kple atikewɔwɔ me nɔnɔme bubuwo. Vidzĩ siwo ƒe aortic arch eve le dometɔ siwo ade 12 le alafa me ƒe dzi ƒe dɔmawɔmawɔ nyuie bubu si wodzina, abe ventricular septal defect (VSD) kple tetralogy of Fallot ene . Tsɔ kpe ɖe eŋu la, domenyiŋusẽfianu ƒe nɔnɔmewo abe chromosome 22q11 deletion kple trisomy 21 (Down syndrome) ene le vidzĩ siwo ƒe aortic arch eve le dometɔ siwo ade 20 le alafa me ŋu .

Aleke woawɔ ade dzesi "Double Aortic Arch"?

Wokpɔa aortic arch eve le vome alo ne dzesiawo dze egɔme. Ɣeaɖewoɣi la, wokpɔnɛ le vo me le fufɔɣi, le vidzidzi megbe, alo le nɔnɔmetatawo dodokpɔ siwo wowɔ le susu bubu aɖe ta me. Tso ƒe 2004 me la, amesiwo wokpɔna be dɔléle sia le wo ŋu to fotoɖeɖe me le fufɔɣi dzi ɖe edzi. Esia ɖea vi ŋutɔ, elabena woate ŋu awɔ ɖoɖo ɖe atikewɔwɔ ŋu ne wonya dzi vidzĩa ko.

Alo, woate ŋu akpɔe ne dzesiawo dze le vidzĩa dzidzi vɔ megbe. Viwòa ƒe ɖɔkta aƒo nu tso dzesiawo ŋu na wò eye emegbe wòawɔ dodokpɔ aɖewo.

Dodokpɔwo be woatsɔ anya "Double Aortic Arch".

Dodokpɔ vevi siwo wozãna tsɔ dea dzesi dɔléle siae nye:

  • Akɔta ƒe X-ray: Zi geɖe la, esiae nye dodokpɔ gbãtɔ si wowɔna.
  • CT-dɔdamɔnu.
  • Echocardiogram (Echo) dodokpɔ: Esia kpena ɖe ame ŋu wu le enyanya me ne dzi ƒe gbɔdzɔgbɔdzɔ bubuwo li hã.
  • MRI (MRI) dodokpɔ.

Ɣeaɖewoɣi la, woate ŋu awɔ aɖuɖɔtoemekpɔmɔ̃ atsɔ ado vidzĩa ƒe yaƒoƒomɔ̃ kpɔ. Woate ŋu awɔ esia le gbɔgbɔtsixe ƒoƒo me hafi woakpɔe be aortic arch eve le eŋu. Alo, woate ŋu awɔe hafi woawɔ dɔ nɛ be wòakpe ɖe amekolaa ŋu wòanya nusi gbɔ kuxia tso.

Domenyiŋusẽfianu dodokpɔ kpena ɖe ame ŋu wòdea dzesi domenyiŋusẽfianu ƒe nɔnɔmewo.

Aleke woawɔ ada "Double Aortic Arch"?

Ele be woawɔ dɔ na ame be woatsɔ aɖɔ "double aortic arch" ƒe nɔnɔmea ɖo. Le vidzĩ siwo me dzesi aɖeke mele o gɔ̃ hã gome la, amekoko nyo wu ne woxɔ tso ɣleti 6 va ɖo 9. Vidzĩ siwo ŋu dzesiwo le, vevietɔ ne dzesiawo nu sẽ la, ate ŋu ahiã be woawɔ dɔ na wo kaba gɔ̃ hã.

Bu eŋu kpɔ ko, wode dzesi nɔnɔme si nye "double aortic arch" zi gbãtɔ le ƒe 1737. Wowɔ amekoko gbãtɔ nɛ le ƒe 1947. Aleke gbegbe míeva ɖo tso ɣemaɣi! Vidzĩ siwo ŋu vidzidzi ƒe gbɔdzɔgbɔdzɔ sia le te ŋu nɔa agbe didi, le lãmesẽ me le amekoko ta.

"Double Aortic Arch" amekoko

"Double Aortic Arch" amekokoa le dedie ŋutɔ, eye emetsonuwo kpɔ dzidzedze ŋutɔ . Mahiã be woatsɔ viwòa aƒo ka na "dzitodzito ƒe mɔxenu" (dzi kple aklã ƒe mɔ̃) o .

Wozãa mɔnu aɖe si woyɔna be "lateral thoracotomy" tsɔ wɔa amekokoa. Esia fia be amekolaa tsoa vidzĩa ƒe akɔta ƒe akpa ɖeka, le akɔta eve dome. Wowɔa esia zi geɖe le miame, elabena afimae vidzĩ akpa gãtɔ ƒe akɔtaƒu sue "si kpe ɖe eŋu" ma le. Nɔnɔmetatawo dodokpɔ siwo wowɔna do ŋgɔ na amekokoa nana amekolaa te ŋu léa ŋku ɖe vidzĩa ƒe ŋutilã ƒe akpa si le eme ŋu nyuie eye wòwɔa ɖoɖo ɖe amekokoa ŋu wòsɔ ɖe enu.

Amekolaa zãa "ligating and dividing" mɔnu . Esia fia be woblaa aɖaka suea be wòatɔ te ʋu si dona to eme. Emegbe wolãnɛ hetsɔa aŋe blanɛ. Wogbugbɔa nu sia wɔna vaseɖe esime aɖakaʋua ma keŋkeŋ eye yaƒoƒomɔ̃a kple nuɖuɖutome ƒe nyaƒoɖeamenu nu nayi.

Viwòa anɔ kɔdzi abe kwasiɖa ɖeka ene, emegbe ahaya eye wòatrɔ ava aƒeme.

"Kommerell diverticulum" (`Kommerell diverticulum - KD`) ƒe atikewɔwɔ

Ƒã hafi nane si woyɔna be "Kommerell diverticulum (KD)" ate ŋu anɔ vidzĩ aɖewo siwo ŋu "double aortic arch" hã si. Esia bɔ ɖe vidzĩ siwo ŋu "ɖusime ʋuka ƒe akɔta" le wu, gake mebɔ ŋutɔ le "ʋuka eve ƒe akɔta" hã gome.

`KD` sia nye `aneurysm`, ʋuka si dona le `aorta` si ɖiɖina me le `aortic arch` gbɔ. Ʋuʋudedi sia ate ŋu axɔ teƒe eye wòate ɖe vidzĩa ƒe yaƒoƒomɔ̃ kple nuɖuɖu ƒe pɔmpi dzi. Ðewohĩ mahe kuxi aɖeke vɛ enumake o. Ke hã, amekolawo lɔ̃a esia hã ɖeɖeɖa ne wole `double aortic arch` wɔm be woaxe mɔ ɖe kuxiwo nu emegbe.

Dzidɔ bubuwo dada

Ne dzidɔ bubu aɖewo le viwòa ŋu si hiã be woawɔ dɔ nɛ la, woate ŋu adae le ɣeyiɣi ɖeka me kple aortic arch eve. Esia ateŋu abia be woawɔ dɔ si woyɔna be ``median sternotomy'' , si bia be woatso akɔta ƒe titina. Viwòa ƒe amekola adzro tiatia nyuitɔ si nàwɔ na wò me, le nya siwo gbɔ wòle be woakpɔ nu.

Kuxi kawoe ate ŋu ado tso amekoko me?

Afɔku si le kuxi siwo dona tso ʋuka eve ƒe dɔwɔwɔ me la le sue ŋutɔ . Ƒã hafi vidzĩa ate ŋu ana nuɖuɖu alo gbɔgbɔtsixe tsia enu. Ne gbɔgbɔmekuxi aɖewo li siwo nɔa anyi ɖaa la, zi geɖe la, wo nu yina le ƒe ɖeka me le amekokoa megbe.

Kuxi siwo dona tso amekoko be woatsɔ aɖɔ ʋuka ƒe akpa eve kple dzi ƒe gbɔdzɔgbɔdzɔ bubuwo ɖo me ate ŋu ato vovo. Dzro afɔku kple kuxi siawo katã me kple viwòa ƒe amekola.

Ðe woate ŋu axe mɔ ɖe "Double Aortic Arch" nua?

Ao, womate ŋu axe mɔ ɖe nɔnɔme si woyɔna be "double aortic arch" nu o . Enye nusi dona le fufɔfɔ ƒe gɔmedzedze eye wònɔa anyi le edziɣi.

Nukae nye amesiwo ŋu "Double Aortic Arch" le ƒe etsɔme?

Vidzĩwo kple ɖevi siwo wowɔ dɔ na "Double Aortic Arch" ƒe etsɔme nyui aɖe ŋutɔ . Woate ŋu anɔ agbe ahaƒo wo ɖokui ɖe nuwɔna siwo sɔ me mɔxeɖenu aɖeke manɔmee.

Le amekokoa megbe la, viwòa ate ŋu ayi edzi anɔ gbɔgbɔm toɣliɖeɖe vaseɖe ƒe ɖeka. Esia le alea elabena vidzĩa ƒe yaƒoƒomɔ̃ metsi bliboe o le "double aortic arch" ta. Eyata, axɔ ɣeyiɣi aɖe hafi yaƒoƒomɔ̃a nasẽ ɖe edzi.

Ƒã ŋutɔ la, gbɔgbɔtsixe ƒe dzesiwo ate ŋu anɔ vidzĩwo kple ɖeviwo ŋu wu ƒe ɖeka le amekokoa megbe.

Nu vevitɔe nye be nàkplɔ viwòa ayi aɖadoe kpɔ edziedzi eye nàgblɔe na wò ɖɔkta ne dzesi aɖewo le ŋuwò si yia edzi. Beléle na ɖevi ɖesiaɖe si wowɔ dɔ na le dzitodzito me ɣeyiɣi didi ƒe beléle le vevie ŋutɔ.

Ɣekaɣie wòle be maƒo ka na vinyea ƒe ɖɔkta?

Ne ède dzesi dzesi yeye aɖewo, alo ne edze abe dzesi siwo li xoxo la le sesẽm ɖe edzi ene la, ƒo nu kple viwòa ƒe ɖɔkta enumake. Vidzĩwo kple ɖevi suewo trɔna ale gbegbe be ate ŋu asesẽ ɣeaɖewoɣi be woanya nusi sɔ kple nusi mesɔ o. Gake ne kɔdzi ma si le abe nutrenu ene alo gbeɖiɖi si le ʋuʋum le viwòa ŋu la, gblɔe na wò ɖɔkta enumake. Ate ŋu anye ɖevimedɔléle si sɔ. Gake ƒã hafi ate ŋu anye dzidɔ si le ŋusẽ kpɔm ɖe viwòa ƒe gbɔgbɔ ƒe ŋutete dzi ƒe dzesi.

Ɣekaɣie wòle be nàƒo ka na 911 (xexlẽdzesi si le nudzɔdzɔ kpatawo me)?

"Double aortic arch" ate ŋu ade nyaƒoɖeamenu si ate ŋu ade viwòa ƒe yaƒoƒomɔ̃ dzi si ate ŋu ade eƒe agbe afɔku me . Ne viwòa ƒe ŋutigbalẽ dze blɔ (cyanosis) , alo ne gbɔgbɔ le sesẽm na viwòa vevie la , ƒo ka na 911 enumake.

Nya kawoe wòle be mabia vinyea ƒe ɖɔkta?

Ne wokpɔe be "double aortic arch" le viwòa ŋu la, esɔ be nyabiase geɖe nanɔ asiwò. Ele vevie be nànya viwòa ƒe nɔnɔme, si me ɣeyiɣi si me wòhiã be woawɔ dɔ na viwòa hã le, kple nenye be lãmesẽkuxi bubu aɖewo le viwòa ŋu. Àte ŋu abia nyawo abe:

  • Ɣekaɣie wòle be woawɔ dɔ na vinyea?
  • Afikae wowɔa amekokoa le? Amekae le ewɔm?
  • Dzesi kawoe wòle be makpɔ nyuie le aƒeme?
  • Nukae mate ŋu awɔ be wòanɔ bɔbɔe na vinyea be wòanɔ aƒeme?
  • Ðe dzidɔ bubuwo le vinyea ŋua?
  • Ðe wòle be mado domenyiŋusẽfianu kpɔ na vinyea alo nye ƒomea me tɔ mamlɛawoa?
  • Aleke vinyea ƒe etsɔme anɔ?

Nukae nye "Aortic Arch Syndrome"? Ðe wòto vovo tso "Double Aortic Arch" gbɔa?

Ẽ, mègatɔtɔ ame eveawo o. "Aortic Arch Syndrome" nye "Vasculitis" ƒomevi aɖe si mebɔ kura o . Wogayɔnɛ be "Takayasu ƒe ʋukawo ƒe dɔléle" .

"Vasculitis" nye wò ʋukawo ƒe gliwo ƒe dɔdzẽ. Ate ŋu adzɔ le ʋuka ɖesiaɖe me, ʋuka suetɔ kekeake siwo nye ʋuka siwo me ʋu sina tona gɔ̃ hã me. "Takayasu ƒe ʋukawo ƒe dɔléle" nye ʋuka siwo lolo titina kple gãwo ƒe dɔdzẽ. Edzena zi geɖe le "aortic arch" kple eƒe alɔ gãwo me. Esia tae wogayɔnae be "aortic arch syndrome."

Takayasu ƒe ʋuka me dɔléle (si woyɔna hã be "aortic arch syndrome") dzɔna le sɔhɛ tsitsiwo kple sɔhɛ tsitsiwo me . Esia nye kuxi si to vovo kura tso "double aortic arch" si wodzina si ŋu míeƒo nu tsoe va yi gbɔ, eye atikewɔwɔ si hiã la to vovo.

Zi geɖe la, vidzĩ dzidzi nyea dzidzɔ kple azãɖuɖu ƒe ɣeyiɣi. Gake ne èva nya be dzidɔ aɖe le viwòa ŋu, le fufɔɣi alo le edziɣi megbe la, dzimaɖitsitsi kple kakaɖedzimanɔamesi va xɔna ɖe dzidzɔ ma teƒe. Ne ɖeko nèva nya be "double aortic arch" le viwòa ŋu teti koe nye ema la, ke ɖewohĩ èle nusi akplɔe ɖo ŋu bum.

Mega tsi dzi o. Wò atikewɔlawo ƒe ƒuƒoƒoa akpe ɖe ŋuwò le esiawo katã me afɔɖeɖe ɖesiaɖe. Èɖe afɔ gbãtɔ xoxo, si nye be nàsrɔ̃ nu geɖe tso viwòa ƒe nɔnɔmea ŋu. Nya nyuiae nye be aʋala ƒe akɔta eve ƒe dɔwɔwɔ le dedie ŋutɔ eye wòkpɔa dzidzedze. Ne dzidɔ alo domenyiŋusẽfianu ƒe nɔnɔme bubuwo le viwòa ŋu la, atikewɔwɔ ate ŋu asesẽ vie wu. Gake ne wowɔ ŋgɔyiyi le vidzĩ yeyewo dzi kpɔkpɔ me la, àte ŋu akpe ɖe viwòa ŋu wòakpɔ beléle si sɔ si wòhiã, ahaya, eye wòakpɔ dzidzɔ le ɖevime.

Eyata nu vevi kawo dzie wòle be míaɖo ŋkui le nusiwo ŋu míeƒo nu tsoe me? (Gbedasi si Wotsɔ Yi Aƒeme)

Enyo, mina míaƒo nu tso nusiwo wòle be wòanɔ susu me na wò la dometɔ aɖewo ŋu kpuie tso nusiwo ŋu míeƒo nu tsoe ku ɖe "Double Aortic Arch" sia ŋu:

  • "Double aortic arch" nye dzidɔ si wodzina . Vidzĩa ƒe ʋuka si me ʋu sina tona la mã ɖe aɖaka eve me, si wɔnɛ be yaƒoƒomɔ̃ kple nuɖuɖutome la tena ɖe edzi.
  • Dzesi vevitɔwoe nye gbɔgbɔ sesẽ, ʋuʋudedi, nu mimi sesẽ, kple gbɔgbɔtsixe ƒe dɔléle enuenu .
  • Wokpɔa nɔnɔme sia to dodokpɔwo abe `CT scan`, `MRI`, `Echocardiogram` me . Ɣeaɖewoɣi la, woate ŋu akpɔe le fufɔɣi gɔ̃ hã.
  • Atikewɔwɔae nye amekoko . Amekoko sia le dedie ŋutɔ eye wòkpɔa dzidzedze.
  • Na vidzĩa le amekoko vɔ megbeÀte ŋu anɔ agbe si sɔ, si me lãmesẽ le.
  • Ne dzesiwo abe gbɔgbɔ sesẽ alo eƒe ʋuʋu ene le viwòa ŋu la, di atikewɔlawo ƒe aɖaŋuɖoɖo enumake .
  • Mega tsi dzi o . Esi egbegbe atikewɔwɔ va le ŋgɔ yim la, woate ŋu ada dɔléle sia dzidzedzetɔe. Wò atikewɔlawo ƒe ƒuƒoƒoa ana kpekpeɖeŋu si nèhiã la wò.

` Double Aortic Arch, Dzidɔ si Wodzina, Ʋukawo ƒe Kpẽwo, Vidzĩwo ƒe Asphyxia, Vidzĩwo ƒe Lãmesẽ, Dzidɔ

Frequently Asked Questions (FAQ)

Nukae nye "Vascular Rings" ƒomevi veviwo?

"Ʋukawo ƒe asigɛ" siawo ƒomevi vevi geɖewo li. Na míakpɔ nusiwo wonye ɖa:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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