Ʋusɔgbɔdɔ, gake iron sɔ gbɔ akpa le ŋutilãa mea? Mina míaƒo nu tso Sideroblastic Anemia ŋu

Ne ame akpa gãtɔ se nya ‘ʋusɔgbɔdɔ ’ , la, iron ƒe anyimanɔmanɔ va susu me na wo enumake. Esia tae ɖeɖi tea wo ŋu ɣesiaɣi, kuviawɔwɔ, taɖuame, eye ɣeaɖewoɣi la, womete ŋu dɔa alɔ̃ o. Gake ènya be le ʋusɔgbɔdɔ ƒe nɔnɔme aɖewo me la, nusi to vovo na ema ŋutɔŋutɔ dzɔnaa? Le esi teƒe be iron ƒe anyimanɔmanɔ nanɔ anyi la, iron si le ʋumenugbagbeviwo me ‘dzina ɖe edzi’. Ðe esia meɖi nusi wɔ nuku vie oa? Egbea míele nu ƒom tso ʋusɔgbɔdɔ ƒe nɔnɔme tɔxɛ mawo dometɔ ɖeka si woyɔna be sideroblastic anemia ŋu.

Kpuie ko la, nukae nye Sideroblastic Anemia?

Be míase esia gɔme la, mina míalé ŋku ɖe míaƒe ʋu ŋu gbã. Protein aɖe si woyɔna be hemoglobin le ʋumenugbagbevi dzĩ siwo le míaƒe ʋu me la me . Eƒe dɔ vevitɔe nye be wòalé ɔksidzin si gena ɖe lãkusi me ne míele gbɔgbɔm eye wòtsɔe yi ŋutilã bliboa me. Eyata oxygen sia hiã vevie hafi lãmenugbagbevi ɖesiaɖe si le míaƒe ŋutilã me nate ŋu anɔ agbe.

Fifia, be míawɔ hemoglobin sia la, míaƒe ŋutilã hiã mineral ‘iron’ godoo. Zi geɖe la, ʋusɔgbɔdɔ dzɔna ne iron mele ŋutilãa me o. Eyata mete ŋu wɔa ʋumenugbagbeviɣidɔ o.

Kpɔe ɖa le susu me be nuɖaƒe aɖe si me bli, tsi, kple dze le be woatsɔ aɖa bli, gake bliɖaka la gbã. Ekema màte ŋu aɖa bli o. Aleae wòle. Le dɔléle sia me la, iron, si nye nusi hiã be woatsɔ awɔ ʋumenugbagbeviɣidɔ, sɔ gbɔ ɖe eme. Gake dɔwɔƒe si zãa gayibɔ ma tsɔ wɔa hemoglobin, si nye míaƒe ʋumenugbagbevi dzĩwo, mewɔa dɔ nyuie o. Eyata gayibɔ si womezã o la dzea ƒoƒo ƒu ɖe ʋumenugbagbevi dzĩ siawo siwo gblẽ la me. Míeyɔa lãmenugbagbevi siawo siwo mesɔ o siwo ƒo iron nu ƒu le mɔ sia nu be `(Sideroblasts)`.

Nukae nye nɔnɔme sia ƒe dzesiwo?

Dɔléle sia ƒe dzesiwo ɖi ʋusɔgbɔdɔ ƒe nɔnɔme bubuwo ŋutɔ, eyata woate ŋu atɔtɔe bɔbɔe ɣeaɖewoɣi. Eye esi dɔlélea doa mo ɖa vivivi ta la, ɖewohĩ mànya gɔ̃ hã be ele ye ŋu o. Esiawoe nye dzesi vevi siwo nàte ŋu akpɔ.

Nukawoe nye Sideroblastic Anemia ƒomevi veviwo?

Woate ŋu ama dɔléle sia ɖe hatsotso eve me koŋ.

1. Sideroblastic Anemia si ƒe dome wonyi

Esia nye domenyiŋusẽfianu ƒe nɔnɔme si mebɔ kura o. Eyae nye be wotoa domenyiŋusẽfianu siwo tso dzilawo dometɔ ɖeka gbɔ dzi naa ɖevi. Esia ƒomevi si bɔ wue nye X-linked Sideroblastic Anemia . Esia tsoa domenyiŋusẽfianu ƒe tɔtrɔ si kpɔa ŋusẽ ɖe hemoglobin ƒe wɔwɔ dzi gbɔ. Esia wɔe be ŋutilãa dzea agbagba be yeaxɔ iron geɖe tso nuɖuɖu me be yeatsɔ aɖo ʋumenugbagbeviɣidɔa teƒe. Le nɔnɔme sesẽwo me la, ate ŋu agblẽ nu le ŋutinuwo abe aklã ene ŋu . Zi geɖe la, wokpɔa dɔléle sia si wodzina hafi xɔa ƒe 30.

2. Ƒomevi si dzea egɔme emegbe (Acquired Sideroblastic Anemia) .

Esiae nye ƒomevi si bɔ wu. Akpa nyuitɔ kekeakee nye be woate ŋu adae zi geɖe . Togbɔ be ɣeaɖewoɣi la, ɖɔktawo menya nusi tututu gbɔ wòtso o hã la, nu vevi geɖewo li siwo gbɔ dɔléle sia tsona:

• Atike aɖewo: Vevietɔ atike aɖewo siwo wonana na yɔmekpe.
• Ahanono fũu akpa: Ahanono fũu akpa ɣeyiɣi didi nye afɔku gã aɖe.
• Atike siwo me aɖi le : Atike aɖewo siwo me aɖi le, abe lifi ene, zazã ɣeyiɣi didi.
• Dɔléle bubuwo: Nɔnɔme sia ate ŋu atso dɔléle bubuwo abe dɔlélenutsiŋutete ƒe dɔmawɔmawɔ nyuie, dɔdzẽ, alo lãmenugbagbeviwo ƒe dɔwɔwɔ ƒe dɔlélewo hã gbɔ.

Tsɔ kpe ɖe eŋu la, nɔnɔme bubu si woyɔna be hemochromatosis , si nana iron si sɔ gbɔ la ƒoa ƒu ɖe ŋutilãa me, ƒomevi evea siaa ate ŋu adze wo dzi.

Aleke tututu woawɔ anya dɔléle sia?

Esi wònye be dzesiawo sɔ kple ʋusɔgbɔdɔ bubuwo ta la, ate ŋu asesẽ vie be woakpɔ dɔlélea. Eyata ele vevie be nàɖo to wò ŋutilã. Ne dzesi siwo míeyɔ ɖe etame la dometɔ ɖeka alo esi wu nenema le ŋuwò la, taflatse yi ɖɔkta gbɔ.

Ðɔktaa abia wò dzesiwo nyuie, ado wò kpɔ, eye emegbe wòaɖe gbe be woawɔ dodokpɔ geɖe atsɔ akpɔe ɖa be dɔléle sia le ŋuwò hã.

• Ʋudodokpɔ: Ʋu ƒe xexlẽme blibo kple iron ŋuti numekuku nye nu vevitɔ.
• Ʋu ƒe Ʋuʋu le Gome: Le afisia la, wodoa ʋu aɖe kpɔ le nusuekpɔmɔ̃ me be woakpɔe ɖa be lãmenugbagbevi siwo me iron ƒoa ƒu ɖo (Sideroblasts) siwo mesɔ o siwo ŋu míeƒo nu tsoe va yi la li hã.
• Ƒumeŋuɖui Ŋuti Nusɔsrɔ̃: Le go aɖewo me la, ahiã be woaɖe ƒumeŋuɖui sue aɖe adoe akpɔ be dɔlélea le ame ŋu.
• Dodokpɔ bubuwo: Ne ehiã la, ɖɔkta ate ŋu aɖo aɖaŋu hã be woawɔ MRI scan alo domenyiŋusẽfianu ƒe dodokpɔ.

Aleke wowɔa atike nɛ?

Atikewɔwɔ ƒe tiatia nɔ te ɖe nenye be ƒomevi si wodzi na wò alo esi nèxɔ dzi.

• Nusi gbɔ wòtso la dada: Ne ƒomevi si nèxɔ la le asiwò la, afɔɖeɖe gbãtɔe nye be nàɖe nusi gbɔ wòtso la ɖa. Le kpɔɖeŋu me, ne atike aɖee le dɔlélea hem vɛ la, wò ɖɔkta adzudzɔ atike ma zazã eye wòaŋlɔ bubu na wò. Ne ahatsunolae nènye la, ahiã be nàdzudzɔ ahanono keŋkeŋ.
• Vitamin B6: Numekukuwo ɖee fia be vitamin B6, alo pyridoxine, ate ŋu akpe ɖe ame ŋu le dɔlélea ƒomevi evea siaa dada me. Ðewohĩ wò ɖɔkta aŋlɔ vitamin sia na wò be wòanye kpeɖeŋutɔ.
• Iron si sɔ gbɔ ɖe lãme na ame ɖeɖeɖa: Atike aɖewo li siwo woate ŋu ana atsɔ aɖe iron si sɔ gbɔ ɖe ŋutilã me ɖa. Wodoa deferoxamine abe atike si wodona ɖe ŋutigbalẽa te ene, eye wodoa Deferasirox abe atikekui ene. Gake atike siawo ate ŋu agblẽ nu le ayikuwo ŋu, eyata ele be woazã wo le ɖɔkta ƒe dzikpɔkpɔ te.
• Ʋudodo: Ne wò ŋutilã mewɔa nu ɖe ​​vitamin B6 zazã ŋu o la, wò ɖɔkta ate ŋu aɖo aɖaŋu be woado ʋu na wò. Gake nu gbegblẽ aɖe le esia ŋu. Ne èyi edzi do ʋu na wò la, iron ƒe agbɔsɔsɔ si le wò ŋutilã me adzi ɖe edzi, si ana aklã ƒe gbegblẽ ƒe afɔkua nadzi ɖe edzi.
• Ƒumeŋuɖui Dodo: Esiae nye atikewɔwɔ mamlɛtɔ. Wobua eŋu le nɔnɔme sesẽ siwo me atikewɔwɔ bubu aɖeke meɖe atike aɖeke le o me.