Ka yi tunanin abin da zai faru idan rundunarmu, wato tsarin garkuwar jikinmu, wanda ake tsammanin zai kare jikinmu daga cututtuka , ta fara fahimtar rashin fahimta ba zato ba tsammani ta fara kai hari ga gabobinmu masu kyau? Wannan wata cuta ce mai matuƙar wahala amma mai tsanani da ake kira Goodpasture Syndrome. A cikin wannan cuta, tsarin garkuwar jikinmu galibi yana lalata manyan gabobi guda biyu a jikinmu, huhu da koda . Yana da matuƙar muhimmanci a san da wannan domin yana iya zama barazana ga rayuwa idan ba a gane shi ba kuma a yi masa magani da sauri.
Menene ainihin cutar Goodpasture?
A taƙaice dai, Goodpasture Syndrome cuta ce da ke shafar garkuwar jiki . Wato, tsarin tsaron jikinmu, wato tsarin garkuwar jiki, yana shiga cikin matsala kuma yana kai hari ga ƙwayoyin halittarmu da kyallen jikinmu.
A cikin wannan cuta, tsarin garkuwar jiki yana samar da garkuwar jiki ga wani furotin na musamman da ake kira collagen , wanda ake samu a cikin huhu da koda. Ka yi tunanin wannan collagen a matsayin manne da ke haɗa sassan jikinmu wuri ɗaya. Don haka lokacin da waɗannan garkuwar jiki suka kai hari ga wannan collagen, huhu da koda za su fara lalacewa sosai.
Duk da cewa wannan cuta ce da ba kasafai ake samunta ba, yana da muhimmanci a gane kuma a fara magani da zarar alamun sun bayyana, in ba haka ba sakamakon na iya zama mai tsanani sosai.
Me ke haifar da wannan yanayi?
Likitoci har yanzu ba su fahimci cikakken dalilin da yasa garkuwar jikinmu ke kai hari ga gabobinta ta wannan hanyar ba. Duk da haka, akwai abubuwa da dama da ake ganin suna taka rawa.
- Tasirin Halitta : Tunda wannan cuta tana yaduwa a wasu iyalai, ana kyautata zaton akwai yiwuwar kamuwa da ita ta hanyar kwayoyin halitta.
- Abubuwan da suka shafi muhalli: Fuskantar wasu sinadarai , kamar su sinadarin hydrocarbon da magungunan kashe kwari kamar paraquat.
- Ƙurar ƙarfe: Kullum tana fuskantar ƙurar ƙarfe.
- Magani: Amfani da kwayoyi kamar hodar iblis.
- Shan taba: Shan taba sigari babban abin da ke haifar da hakan.
- Cututtukan ƙwayoyin cuta: Wannan yanayin na iya faruwa bayan wasu kamuwa da ƙwayoyin cuta.
Wannan cuta ta fi yawa a cikin samari, musamman waɗanda ke tsakanin shekaru 20 zuwa 30 da waɗanda suka haura shekaru 60.
Menene alamomin? Ta yaya za ku gane hakan?
Matakan farko na wannan cutar suna nuna alamun gaba ɗaya, marasa ma'ana. Don haka wani lokacin yana iya zama kamar ba wani abu mai tsanani ba ne. Amma wannan yanayin yana ci gaba da sauri.
Duba teburin da ke ƙasa don ganin menene waɗannan alamun.
| Nau'in Halayya | Alamomin da za a iya gani |
|---|---|
| Sifofin farko da na gama gari |
|
| Lokacin da huhu ya kamu da cutar | |
| Lokacin da kodan suka kamu da cutar |
Duk da cewa wannan cuta na iya haifar da zubar jini mai barazana ga rayuwa daga huhu, lalacewar huhu na dogon lokaci yawanci ba ta da yawa. Duk da haka, mafi munin sakamakon wannan cutar shine gazawar koda . Idan haka ta faru, kuna iya buƙatar dialysis na tsawon rai ko dashen koda.
Ta yaya likita zai gano wannan cuta?
Idan ka fuskanci ɗaya ko fiye daga cikin alamomin da muka tattauna, kada ka yi jinkiri . Ka ga likita da wuri-wuri. Musamman idan kana tari da jini, kana fuskantar wahalar numfashi, ko kuma kana fitar da jini a cikin fitsarinka, to gaggawa ce.
Likitan zai iya yin odar gwaje-gwaje da dama don tabbatar da ganewar cutar:
- Binciken fitsari: Wannan gwajin yana duba yawan furotin da ƙwayoyin jinin ja a cikin fitsari. Wannan zai iya taimakawa wajen tantance ko kodan sun lalace.
- Gwajin jini: Ana duba jininka don gano takamaiman ƙwayoyin rigakafi waɗanda ke kai hari ga huhu da kodan.
- X-ray na ƙirji: Wannan na iya neman lalacewa ga huhu, kamar fararen tabo marasa kyau da zubar jini ke haifarwa.
- Binciken Halitta: Wani lokaci ana ɗaukar ƙaramin yanki na nama daga koda ko huhu a duba shi ta hanyar na'urar hangen nesa. Wannan zai iya tabbatar da ko akwai ƙwayoyin rigakafi na Goodpasture Syndrome da kuma yawan lalacewar da aka samu ga koda.
Menene hanyoyin magance wannan?
Da zarar an gano wannan cuta, ya kamata a fara magani cikin sauri da kuma sosai. Manyan manufofin magani sune:
- Yaƙi da ƙwayoyin cuta masu cutarwa.
- Kula da tarin ruwa mai yawa a jiki.
- Sarrafa hawan jini.
- Dakatar da lalacewar huhu da koda.
Maganin yawanci ya ƙunshi waɗannan abubuwa:
1. Magungunan rage ƙarfin garkuwar jiki: Ana ba da magunguna kamar cyclophosphamide da corticosteroids. Waɗannan magunguna suna aiki ta hanyar rage ayyukan garkuwar jikinmu da kuma dakatar da samar da ƙwayoyin rigakafi masu cutarwa. Wani lokaci ana iya ba da yawan maganin steroids ta hanyar jijiya don sarrafa zubar jini a cikin huhu.
2. Plasmapheresis: Wannan tsari ne mai ɗan rikitarwa. A taƙaice dai, ya ƙunshi ɗaukar ƙaramin adadin jininka, saka shi a cikin wata na'ura ta musamman, da kuma raba ɓangaren ruwa, wanda ake kira plasma, wanda ke ɗauke da ƙwayoyin rigakafi masu cutarwa. Sannan, sauran sassan jini masu kyau (ƙwayoyin jini ja da fari) za a haɗa su da wani madadin plasma sannan a mayar da su cikin jikinka. Wannan yana cire ƙwayoyin rigakafi masu haɗari daga jinin. Wannan magani yana iya buƙatar a yi shi kowace rana na tsawon makonni da yawa.
Wannan maganin na iya ɗaukar watanni 6 zuwa 12. Yana iya ɗaukar daga makonni kaɗan zuwa shekaru biyu kafin ya warke gaba ɗaya. A wannan lokacin, wasu marasa lafiya na iya buƙatar ƙarin iskar oxygen ko ma na'urar numfashi. Hakanan ana iya buƙatar ƙarin jini.
Saƙon Ɗauka Gida
- Ciwon Goodpasture cuta ce mai matuƙar wahala amma mai matuƙar tsanani wadda tsarin garkuwar jikinmu ke kai hari ga huhu da kodan.
- Alamomin kamar tari da jini, wahalar numfashi, jini a cikin fitsari, da kumburin jiki alamu ne masu matuƙar muhimmanci na gargaɗi.
- Idan kana da ɗaya daga cikin waɗannan alamun, kada ka jinkirta ka je wurin likita nan da nan . Da zarar an fara magani da wuri, sakamakon zai fi kyau.
- Maganin ya haɗa da magunguna da ke kula da tsarin garkuwar jiki da kuma hanyoyin da ake amfani da su kamar plasmapheresis, waɗanda ke tsarkake jini.
- Idan kai ko wani da ka sani yana da wata shakka ko tambayoyi game da wannan, yi magana a fili da likitanka game da shi.
Ciwon Goodpasture Sinhala, cutar huhu, cutar koda, tsarin garkuwar jiki, cutar autoimmune sinuhala, tari da jini, jini a cikin fitsari











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