Loaʻa iā ʻoe ka maʻi Sickle Cell? No laila, inā loaʻa iā ʻoe ka ʻeha o ka umauma, mai pāʻani a puni! E pili ana kēia i ka Acute Chest Syndrome!

Loaʻa iā ʻoe i kekahi manawa ka ʻeha koke o ka umauma a me ka paʻakikī o ka hanu ʻana? Inā loaʻa iā ʻoe kēia mau hōʻailona me ka ʻū a me ke kuni, ʻoiai inā loaʻa iā ʻoe kahi maʻi i kapa ʻia ʻo Sickle Cell Disease (SCD) , mai lawe māmā. Hiki i kēia mau hōʻailona ke hōʻailona o kahi maʻi koʻikoʻi i kapa ʻia ʻo Acute Chest Syndrome. Mai hopohopo, e kamaʻilio mākou e pili ana i kēia ma ke ʻano maopopo a maʻalahi i kēia lā.

He aha ka Acute Chest Syndrome? I ka ʻōlelo maʻalahi...

ʻAe, e nānā i kēia manawa. ʻO kēia 'Acute Chest Syndrome' kahi pilikia koʻikoʻi o ka maʻi cell sickle ('SCD') . I ka ʻōlelo maʻalahi, ʻo ia ka wā e loaʻa ai iā ʻoe ka ʻeha o ka umauma, ka ʻū, ke kuni, ka haʻahaʻa o ka oxygen i loko o kou koko, a me nā mea ʻē aʻe, ʻo ia hoʻi ka wai, e hoʻomaka e hōʻiliʻili i loko o ka ʻiʻo māmā ('lung infiltrates').

Hiki i kēia maʻi ke lilo i mea koʻikoʻi koke . ʻO ka ʻoiaʻiʻo, ʻo kēia 'Acute Chest Syndrome' ke kumu nui o ka hoʻokipa ʻia ʻana i ka haukapila a i kekahi manawa make no ka poʻe me ka maʻi sickle cell . No laila, he mea nui loa ka makaʻala i kēia.

I kēia manawa, ke noʻonoʻo nei paha ʻoe i ke ʻano o ka maʻi Sickle Cell (SCD). E hoʻomanaʻo iki kākou iā ʻoe e pili ana i ia mea. He maʻi genetic ia. ʻO ia hoʻi, ua hoʻoilina ʻia. Hoʻopilikia ia i ka protein i loko o kā mākou mau ʻulaʻula koko i kapa ʻia ʻo hemoglobin . ʻOiai he poepoe nā ʻulaʻula koko o ke kanaka olakino, ua like ke ʻano o nā ʻulaʻula koko o ke kanaka me SCD me ka sickle (e like me ka crescent). No laila, ʻaʻole hiki i kēia mau ʻulaʻula ʻano sickle ke hele maʻalahi ma o ko mākou mau kīʻaha koko lahilahi. A laila, ʻaʻole hiki i ka hemoglobin ke lawe pono i ka oxygen ma ke kino holoʻokoʻa. ʻO kēia ka pilikia nui me SCD.

Pehea ka maʻamau o ka Acute Chest Syndrome?

ʻO kaʻoiaʻiʻo, ʻo ka `Acute Chest Syndrome` kahi maʻi maʻamau i waena o ka poʻe me ka maʻi sickle cell (`SCD`). Wahi a nā helu helu, ma kahi o ka hapalua o ka poʻe me `SCD` e ʻike i kēia maʻi ma ka liʻiliʻi hoʻokahi i ko lākou ola . ʻOiai ʻo ia ka mea maʻamau i nā keiki ʻōpio ma waena o nā makahiki 2 a me 4 , hiki ke ʻoi aku ka koʻikoʻi i nā pākeke ma mua o nā keiki . Ua ʻike ʻia hoʻi he ʻoi aku ka nui o ka pilikia o ka poʻe i loaʻa i ka `SCD` a me ka hānō i ka hoʻomohala ʻana i ka `Acute Chest Syndrome` ma mua o nā poʻe ʻē aʻe.

No ke aha e kū mai ai ka Acute Chest Syndrome? He aha nā kumu?

ʻAʻole hiki i nā kānaka ʻepekema ke ʻōlelo maopopo i ke kumu maoli o ka 'Acute Chest Syndrome'. Akā, manaʻoʻiʻo lākou he kumu paha ia o hoʻokahi a ʻoi aku paha. E nānā kākou i ke ʻano o lākou:

• Ka necrosis o ka iwi iwi:Ua ʻike anei ʻoe ʻo ka iwi iwi ka ʻāpana palupalu a palupalu i loko o ko kākou mau iwi nui? Inā make kēia iwi iwi ma kekahi ʻano (i kapa ʻia ʻo 'necrosis'), hiki i nā ʻāpana liʻiliʻi ke haki a komo i ke koko a hele i loko o ke kino. Inā hele kēia mau ʻāpana i nā māmā, hiki iā ia ke hana i ka 'Acute Chest Syndrome'.
• ʻO ka embolism momona: ʻO kekahi kumu paha o ka hāʻule ʻana o ka iwi iwi i ʻōlelo ʻia ma luna nei, ʻo ia ka embolism momona . I ka ʻōlelo maʻalahi, ʻo ia ka wā e paʻa ai kahi ʻāpana momona (e noʻonoʻo iā ia he kulu o ka ʻaila) i loko o kahi kīʻaha koko a ālai i ke kahe o ke koko . Hiki i kēia ke alakaʻi i ka Acute Chest Syndrome.
• Maʻi : ʻO nā maʻi like ʻole, ʻoi aku ka pneumonia i hoʻokumu ʻia e ka bacteria a i ʻole nā ​​​​virus , hiki ke hana i ka acute chest syndrome. ʻO nā maʻi ke kumu nui o kēia ʻano maʻi i nā keiki ʻōpio . Eia nō naʻe, i nā pākeke , ʻoi aku ka nui o ka hana ʻia e ka fat embolism.

He aha nā hōʻailona o kekahi kanaka me ka Acute Chest Syndrome?

Hiki ke ʻokoʻa nā hōʻailona o ka 'Acute Chest Syndrome' mai kēlā kanaka a kēia kanaka. Aia kekahi mau ʻokoʻa, ʻoi aku hoʻi ma waena o nā keiki ʻōpio a me nā pākeke. ʻO nā keiki ʻōpio ka mea maʻamau e hōʻike i ka hapa nui o nā hōʻailona o kahi maʻi:

• Kuke
• kuni
• Hoʻemi ʻia ka nui o ka oxygen i loko o ke koko (hypoxemia)
• Ka wikiwiki o ka hanu ʻana (tachypnea)
• Wheezing (he leo e puka mai ana mai ka umauma i ka wā e hanu ana)

Hiki i nā pākeke ke ʻike i kēia mau hōʻailona. Eia kekahi, e ʻike paha ʻoe:

• Hiki ke hoʻonui ʻia ka ʻeha o ka umauma , ʻoiai i ka wā e hanu ana.
• ʻEha nui a koke hoʻi ma nā lima, nā wāwae, a me ke kua i hoʻokumu ʻia e ke ālai ʻana o ke kahe koko (i kapa ʻia hoʻi he 'vaso-occlusive crisis').
• Ka hōʻiliʻili ʻana o ka wai i loko o nā māmā a me ka umauma (pleural effusion).
• Ka paʻakikī o ka hanu ʻana (dyspnea).

Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​ʻoiai inā he SCD kāu, he mea nui loa ia e ʻimi koke i ke kōkua lapaʻau .

Pehea e ʻike ʻia ai ka Acute Chest Syndrome? (Diagnosis)

ʻO ka ʻike mua ʻana i ka 'Acute Chest Syndrome' hiki ke hoʻōla i ke ola o ke kanaka.Inā loaʻa iā ʻoe ka SCD a ua hoʻokomo ʻia i ka haukapila, pono ʻoe e nānā mau ʻia a loaʻa nā hoʻokolohua e pono ai. Aia kekahi mau hoʻokolohua e hiki ke kōkua i nā kauka e ʻike i kēia pilikia:

• Ka nānā ʻana i ke kinoea koko arterial: Hiki i kēia ke ana i ka acidity (pH), oxygen, a me nā pae kalapona dioxide o kou koko.
• Nā hoʻāʻo koko: Hiki i ka helu koko piha ke hāʻawi i ka ʻike e pili ana i kāu mau hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a me nā platelets.
• X-ray o ka umauma: Hiki ke hoʻohana ʻia kēia e nānā i nā maʻi māmā a i ʻole ka hōʻiliʻili ʻana o kēlā mau mea ʻē (infiltrates) a mākou i kamaʻilio ai ma mua.
• Nā Moʻomeheu: Kōkua kēia mau hoʻāʻo e ʻike i nā ʻano maʻi like ʻole ma ka nānā ʻana i kou koko, mucus, a i ʻole nā ​​​​wai kino ʻē aʻe.

Ma muli o kēia mau hopena hoʻāʻo a me kāu mau hōʻailona, ​​​​hiki i kāu kauka ke hoʻokaʻawale i ka Acute Chest Syndrome i ke ʻano he ʻoluʻolu, kaulike, a koʻikoʻi paha .

He aha nā lāʻau lapaʻau no ka Acute Chest Syndrome?

I kēia kūlana , ʻo ka hoʻomaka mua ʻana i ka lāʻau lapaʻau ke ala maikaʻi loa e pale aku ai i nā pilikia koʻikoʻi . ʻO nā koho lapaʻau e komo pū me:

• Hoʻoili koko: ʻO kēia ka wehe ʻana i kekahi o kou koko a hāʻawi iā ʻoe i ke koko a i ʻole nā ​​​​​​mea koko mai kahi mea hāʻawi.
• Nā wai IV: Kōkua kēia i ka pale ʻana i ka maloʻo (paʻa ʻana o ka wai), hiki ke hoʻonui i ka maʻi cell sickle a hoʻonui i ka ʻeha.
• Nā lāʻau hoʻopau ʻeha: Hiki ke hāʻawi ʻia nā lāʻau lapaʻau e like me ke 'ketorolac' a i ʻole 'opioids' e kāohi i ka ʻeha.
• He Spirometer Hoʻoikaika: Kōkua kēia mea liʻiliʻi iā ʻoe e hanu hohonu. Kōkua ia i ka mālama ʻana i kou mau māmā i ka maʻemaʻe a me ka hana pono.
• Lapaʻau oxygen pākuʻi: Inā haʻahaʻa ka pae oxygen i loko o ke koko, hāʻawi ʻia ka oxygen.
• Nā lāʻau antibiotic: Inā loaʻa kēia maʻi i kahi maʻi bacteria, hāʻawi ʻia nā lāʻau antibiotic.
• Nā lāʻau antiviral: Inā he maʻi viral ke kumu, hāʻawi ʻia nā lāʻau antiviral kūpono.

Hiki ke hoʻemi ʻia ka pilikia o ka hoʻomohala ʻana i ka Acute Chest Syndrome?

Inā loaʻa iā ʻoe ka maʻi cell sickle (SCD), he mea nui e kamaʻilio me kāu hui lapaʻau e pili ana i nā ala e pale aku ai i ka Acute Chest Syndrome. Hiki iā lākou ke kuhikuhi i nā mea e like me:

• Ke puhi mau nei i loko o kahi ʻōmole: ʻOiai he mea maʻalahi paha ia, kōkua kēia i ka mālama ʻana i kou mau ala ea a hoʻemi i ka hōʻiliʻili ʻana o ka wai pono ʻole a puni kou mau māmā.
• Hoʻoikaika kino mau: Hiki i kēia ke hoʻonui i ka ikaika o kou māmā.
• Nā hoʻoili koko maʻamau: Pono paha kekahi poʻe i kēia.
• ʻO ka lawe ʻana i nā lāʻau lapaʻau e like me 'Hydroxyurea' a i ʻole 'L-glutamine': Hiki i kēia mau lāʻau lapaʻau ke kōkua i ka hōʻemi ʻana i ka ʻeha a me ka hoʻemi ʻana i ka pilikia o ka hoʻokipa pinepine ʻia ʻana i ka haukapila. Eia nō naʻe, pono e lawe ʻia kēia mau mea ma lalo o ke aʻo ʻana a ke kauka.

He aha ka nānā ʻana (ho'ōla ʻana) no kekahi me kēia maʻi?

He mea nui e ʻimi koke i ka lāʻau lapaʻau ke kū mai ka `Acute Chest Syndrome`. ʻO ka hana ʻole ʻana pēlā e alakaʻi ai i nā pilikia koʻikoʻi e like me:

• ʻO ka Acute Respiratory Distress Syndrome (ARDS): He maʻi koʻikoʻi kēia o ka māmā e hiki ke hoʻoweliweli i ke ola.
• Ke kūlana noʻonoʻo i hoʻololi ʻia.
• ʻEha puʻupaʻa.
• Ka hana pono ʻole o ke akepaʻa.
• Ka hāʻule ʻana o nā ʻōkana he nui.
• Ka hāʻule piha ʻana o ka hanu.
• ʻEha nui loa.
• ʻO ka mea pōʻino, hiki nō ke make.

Wahi a nā helu helu, ʻo ka nui o ka make no ka 'Acute Chest Syndrome' i waena o nā pākeke ma kahi o 4% . I waena o nā keiki, ʻo kēia helu ma kahi o 1% . ʻO ke ʻano kēia, hiki ke hoʻōla ʻia nā ola he nui me ka mālama mua ʻana.

Eia kekahi, e hoʻomanaʻo ʻoiai inā ua mālama pono ʻia a ho'ōla ʻia ka 'Acute Chest Syndrome', hiki i ke kanaka me 'SCD' ke ʻike hou i kēia maʻi i ka wā e hiki mai ana .

He maʻi ʻeha koʻu. He aha kaʻu e hana ai inā loaʻa iaʻu nā hōʻailona o ka Acute Chest Syndrome?

ʻO kēia ka mea nui loa. Inā loaʻa iā ʻoe ka SCD a hoʻomaka e ʻike i kekahi o nā hōʻailona o ka Acute Chest Syndrome (ʻeha umauma, pōkole o ka hanu, ʻū, kuni), mai hoʻokaʻulua no hoʻokahi minute a e ʻimi koke i ke kōkua lapaʻau .

• E haʻi i nā kauka he maʻi cell sickle kou ke hele ʻoe i ka lumi pilikia a i ʻole kekahi keʻena lapaʻau ʻē aʻe.
• E noi koke i kahi X-ray umauma . Hiki i kēia ke hōʻoia koke inā he Acute Chest Syndrome kou a hoʻomaka koke i ka mālama ʻana.

E hoʻomanaʻo, ʻo ka hana wikiwiki ʻana i kahi manawa e like me kēia hiki ke kōkua nui i ka hoʻopakele ʻana i kou ola.

Leka Lawe-Home

Ua ʻike ʻoe i kēia manawa ʻo ka 'Acute Chest Syndrome', a mākou i kamaʻilio ai, he pilikia koʻikoʻi paha ia o ka maʻi sickle cell. ʻO nā hōʻailona nui ka ʻeha o ka umauma, ka pōkole o ka hanu, ka ʻū, a me ke kuni . Inā loaʻa iā ʻoe ka maʻi sickle cell, e ʻimi koke i ke kōkua lapaʻau inā loaʻa iā ʻoe kekahi o kēia mau hōʻailona.Mai poina e hoʻomaopopo i kāu mau kauka he maʻi cell sickle kou. ʻO ka ʻike mua ʻana a me ka mālama koke ʻana nā ala maikaʻi loa e pale aku ai iā ʻoe iho mai kēia ʻano. E noho olakino! Acute Chest Syndrome, Sickle Cell Disease, ʻEha Umauma, Paʻakikī Hanu, Acute Chest Syndrome, Sickle Cell Disease, Nā Maʻi ʻAkemāmā