Ke manaʻo nei ʻoe i kekahi manawa ua like ʻoe me ke kaulike ʻole, ke kuʻia nei, a ʻaʻole hana pono kou mau lālā i kou hele ʻana? Ke noʻonoʻo nei paha ʻoe, "He aha ka hewa iaʻu, e hāʻule wale ana au." ʻOiai ʻaʻole mākou e noʻonoʻo nui i ia mea i nā manawa e like me kēia, he hōʻailona paha kēia o kahi pilikia me kā mākou ʻōnaehana nerve. ʻO ia ka mea a mākou e kapa nei he ataxia ma ka lāʻau lapaʻau.
I ka ʻōlelo maʻalahi, he aha ka ataxia?
ʻO Ataxia ka nalowale ʻana o ka hoʻonohonoho ʻana o nā ʻiʻo i loko o kou kino. E noʻonoʻo i kēia ʻano: ʻo kou lolo ke kumu ma hope o nā neʻe ʻana a pau o kou kino. No ka hāpai ʻana i ka lima, e kau i ka wāwae, e ʻōlelo, pono kēia mau mea a pau i nā kuhikuhi mai kou lolo. I ka ataxia, aia kahi pilikia ma kekahi wahi o kēia kaʻina kuhikuhi. ʻO ka hopena, lilo kāu mau neʻe ʻana i mea ʻē, ʻano ʻē, a i kekahi manawa he ʻano ʻē.
ʻO ka mea nui, hiki i ka ataxia ke lilo i hōʻailona o kahi maʻi ʻē aʻe. Eia kekahi, aia kahi hui o nā maʻi i kapa ʻia ʻo ataxia ma ka inoa like.
He aha ka ʻokoʻa ma waena o Ataxia lāua ʻo Apraxia?
ʻOiai ke kani like nei kēia mau huaʻōlelo ʻelua, aia kahi ʻokoʻa maopopo ma waena o kēia mau kūlana ʻelua. ʻO ka hoʻomaopopo ʻana i kēia e hāʻawi iā ʻoe i kahi ʻike nui.
| Kūlana | Ua wehewehe maʻalahi ʻia |
|---|---|
| ʻApaxia | ʻO ka mea e hana ʻia ma kēia , ʻo ia ka poina ʻana o kou lolo i ka hana ʻana i kahi mea āu i ʻike mua ai pehea e hana ai. No ka laʻana, ʻo ka mea ʻike i ke kāhili ʻana i ko lākou lauoho me kahi kāhili, ʻaʻole hiki iā ia ke ʻike pehea e hana ai. Aia kahi pilikia me ke kikowaena 'hana' i loko o ka lolo. |
| ʻAtaxia | I kēia hihia, ʻike ka lolo i ka mea e hana ai, akā ʻaʻole hiki i nā ʻiʻo e pono ai ke hana pēlā ke kūlike pū. ʻIke ka lolo he pono ia e kahili i kona lauoho, akā nele iā ia ka hoʻonohonoho ʻana e paʻa pono ai i ka kahili a neʻe pololei i kona lima i kona poʻo. |
He aha nā ʻano nui o ka ataxia?
Hiki ke hoʻokaʻawale ʻia ʻo Ataxia i ʻekolu mau ʻano nui ma muli o ke ʻano o kona hana ʻana.
- ʻO Cerebellar Ataxia: ʻO kēia ke ʻano maʻamau. Ma ke kua o ko kākou lolo, ma lalo o ka cerebellum , aia kahi ʻāpana liʻiliʻi. ʻO kēia ke kikowaena nui e kaohi ana i ka neʻe ʻana o ko kākou kino, ke kūlana, a me ke kaulike. Hana ʻia kēia ʻano ataxia ke hōʻino ʻia kēia cerebellum.
- ʻO Sensory Ataxia: Ua ʻike anei ʻoe i kahi o kou mau lima a me kou mau wāwae ʻoiai ke pani ʻoe i kou mau maka? Ua kapa ʻia kēia ʻo 'self-positioning sense'. He ʻōnaehana kēia e haʻi mau ana i ka lolo e pili ana i ke kūlana o ko mākou kino. Loaʻa ka sensory ataxia ke hoʻopilikia ʻia kēia ʻike. He paʻakikī i kēia poʻe ke hele wāwae, ʻoiai ke pani ʻia ko lākou mau maka, a i ʻole i ka pōʻeleʻele.
- Vestibular Ataxia: Aia i loko o ko kākou pepeiao i loko kahi ʻōnaehana e pono ai no ke kaulike o ke kino. Ua kapa ʻia kēia ʻo ka ʻōnaehana vestibular. Ke loaʻa kahi pilikia me kēia ʻōnaehana, no ka laʻana, kahi maʻi, ua nalowale loa kou kaulike. Hiki iā ia ke manaʻo e like me ʻoe e lana ana ma luna o kahi waʻa a laila pae ma ka ʻāina.
He aha nā kumu o ka ataxia?
Nui nā kumu hiki ke loaʻa i ka ataxia. Hiki ke hoʻokaʻawale nui ʻia lākou penei:
- Nā kumu i loaʻa: Nā kūlana a i ʻole nā kumu ʻē aʻe e ulu ana i kekahi manawa o ke ola. He manawa pōkole kekahi o kēia a hiki ke ho'ōla ʻia.
- Hoʻoilina: Nā kūlana i hoʻoilina ʻia mai nā mākua ma o nā genes. ʻO nā hiʻohiʻona o kēia mau maʻi e like me `Friedreich's ataxia` a me `ataxia-telangiectasia`.
- Nā kumu sporadic: Hoʻokumu ʻia kēia e nā loli kaulele ʻole i loko o nā genes (DNA) e hana ʻia ana i ka wā e ulu ana kahi fetus i loko o ka ʻōpū. ʻAʻole kēia i hoʻoilina ʻia mai nā mākua mai.
ʻO kekahi o nā kumu maʻamau o ka ataxia:
- Ka inu nui ʻana i ka waiʻona: ʻO kēia ke kumu e hina ai ʻoe ke inu nui ʻoe a ʻona.
- Hahau a me nā Hoʻouka Ischemic Kuikilana (TIAs) .
- Nā puʻupuʻu lolo a i ʻole nā maʻi ʻē aʻe.
- Nā ulia poʻo a me nā ʻeha.
- Nā maʻi o ka ʻōnaehana nerve e like me ka Multiple Sclerosis (MS) .
- Nā nele o ka wikamina e like me ka wikamina B12 a me ka wikamina E.
- Ma ke ʻano he hopena ʻaoʻao o kekahi mau lāʻau lapaʻau, ʻoi aku hoʻi nā lāʻau lapaʻau no ka maʻi epilepsy a me ke kaumaha.
- Ka emi ʻana o ka hana thyroid (Hypothyroidism).
- Nā maʻi i hoʻokumu ʻia e ka bacteria, nā virus, a i ʻole ka fungi, ʻoiai hoʻi nā mea e hoʻopilikia ana i ka lolo a i ʻole nā pepeiao.
- Maʻi Celiac.
- Ka ʻike ʻia ʻana i nā mea ʻawahia e like me nā kemika a me nā metala kaumaha (e.g. mercury).
- Ka hōʻino ʻana o nā aʻalolo i hoʻokumu ʻia e ka honi ʻana/huffing (huffing) i nā mea e like me ka gum, ka gasoline, ka pena, a pēlā aku.
- Ka luhi nui a me ke kaumaha.
Pehea e mālama ʻia ai kēia maʻi?
ʻO ke ʻano o ka mālama ʻana no ka ataxia ma muli o ke kumu, no laila he nui nā ʻano lapaʻau e loaʻa ana.
Eia kekahi laʻana, ʻaʻohe lāʻau lapaʻau e pono ai ka ataxia i hoʻoulu ʻia e ka waiʻona koe wale nō ke ala. Hiki ke ho'ōla loa ʻia ka hemahema o ka Vitamin B12 me nā pila vitamina a i ʻole nā inikini. Inā he maʻi ia, pono nā lāʻau antibiotic.
ʻO ka mea nui loa, mai ho'āʻo e mālama iā ʻoe iho me ka ʻike mua ʻole i ke kumu pololei. ʻO kāu kauka wale nō ke haʻi iā ʻoe i ka lāʻau lapaʻau kūpono loa iā ʻoe, ma muli o kāu mau hōʻailona a me nā hoʻokolohua e pono ai.
Āhea ʻoe e ʻike ai i ke kauka?
I kekahi manawa, hiki i ka ataxia ke lilo i hōʻailona hōʻailona o kahi maʻi koʻikoʻi. No laila, i nā hihia aʻe, e ʻimi koke i ka ʻōlelo aʻoaʻo lapaʻau.
| Inā loaʻa iā ʻoe kēia mau hōʻailona, e ʻike koke i ke kauka! | |
|---|---|
| Hoʻomaka koke | Inā hoʻomaka koke ka ataxia a piʻi mālie paha. |
| Nā hōʻailona ʻē aʻe | Inā hele mai ka ataxia me ka ʻeha poʻo nui, ka nausea, a me ka luaʻi. |
| Nā pilikia ʻē aʻe | Inā loaʻa iā ʻoe nā hōʻailona e like me ka paʻakikī i ka ale ʻana (dysphagia), ka paʻakikī i ka ʻōlelo ʻana (aphasia), a i ʻole ka neʻe wikiwiki ʻana o nā maka i kāohi ʻole ʻia (nystagmus). |
| Nā hōʻailona o ka hahau ʻana | Inā ʻike ʻoe i nā hōʻailona o ka hahau ʻana, e like me ka mae ʻole, ka nāwaliwali, a i ʻole ka ʻōlelo ʻole ma kekahi ʻaoʻao o ka maka, ka lima, a i ʻole ka wāwae, e hele koke i ka Emergency Department (ETU) o ka haukapila. |
| Manawa | Inā hoʻomau kēia kūlana no nā lā he nui. |
Aia kekahi mau ala e pale aku ai i kēia?
ʻAʻole hiki iā mākou ke pale aku i nā kumu āpau o ka ataxia, ʻoiai nā kūlana hoʻoilina. Eia nō naʻe, hiki ke kāohi ʻia kekahi mau kumu e pili ana i ko mākou nohona.
- Kaohi ʻana i ka waiʻona: Ke kaupalena ʻana a i ʻole ka hoʻōki loa ʻana i ka inu ʻana i ka waiʻona.
- ʻAi olakino: He mea nui loa ka ʻai ʻana i ka meaʻai kaulike e pale aku ai i nā hemahema o nā wikamina.
- Palekana: Ke komo ʻana i nā lako pale e like me nā mahiole i ka wā e pāʻani ai i nā haʻuki a i ʻole e hana ana i nā hana e hōʻeha ai ke poʻo.
- Ka mālama ʻana i nā maʻi: E ʻimi koke i ka ʻōlelo aʻoaʻo lapaʻau a me ka mālama ʻana, ʻoiai inā loaʻa iā ʻoe nā maʻi pepeiao, ma kahi o ka hoʻokuʻu wale ʻana iā lākou.
- Ke pale ʻana i nā mea ʻawahia: E hahai i nā hana palekana i ka wā e hana ana me nā kemika. Inā manaʻo ʻoe ua ale ʻoe i kahi mea ʻawahia, hiki iā ʻoe ke kelepona i ke Kikowaena ʻIke ʻAi ʻawahia Lahui ma ka Halemai Lahui ʻo Colombo no ka ʻōlelo aʻoaʻo.
- E makaʻala me nā lāʻau lapaʻau: Inā manaʻo ʻoe e loaʻa ana kēia mau hōʻailona ma muli o kahi lāʻau lapaʻau āu e lawe nei, mai hoʻōki i ka lawe ʻana me ka ʻole o ke kamaʻilio mua ʻana me kāu kauka. Hiki i kekahi mau lāʻau lapaʻau ke hana i nā hopena ʻino inā ʻoe e hoʻōki koke i ka lawe ʻana iā lākou.
Pehea ka hopena o ka ataxia i kou ola a inā paha e pili ana i kou ola e hilinaʻi wale ʻia ma ke kumu kumu. ʻAʻole pili ka ataxia i hoʻokumu ʻia e nā kumu manawa pōkole i kou ola. Eia nō naʻe, hiki i kekahi mau kūlana hoʻoilina a i ʻole neurological ke loaʻa nā hopena lōʻihi. No laila, ʻo kāu kauka wale nō ke hāʻawi iā ʻoe i ka ʻike maikaʻi loa a me ka ʻōlelo aʻoaʻo e pili ana i kou kūlana. Mai makaʻu a kānalua paha e kamaʻilio me kāu kauka e pili ana i kou pilikia.
Leka Lawe-Home
- ʻAʻole wale ʻo Ataxia he mea e kū ai i ka pilikia a i ʻole ka ʻoluʻolu ʻole, he pilikia ia me ka hoʻonohonoho ʻana o nā mākala o ke kino.
- Hiki ke hana ʻia kēia e nā kumu maʻalahi e like me ka ʻona waiʻona a me ka nele o nā huaora, a me nā kumu koʻikoʻi e like me ka hahau ʻana a me nā puʻupuʻu lolo.
- Inā hiki koke mai ka ataxia, a i ʻole e hele pū me nā hōʻailona e like me ke poʻo ʻeha, ka paʻakikī i ka ʻōlelo ʻana, a i ʻole ka nāwaliwali ma kekahi ʻaoʻao o ke kino, e noʻonoʻo he pilikia ia a e ʻimi koke i ke kōkua lapaʻau.
- Mai hoʻowahāwahā i kēia mau hōʻailona. E ʻike mau i kāu kauka e hoʻoholo i ke kumu pololei.











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