Ua loaʻa anei iā ʻoe ka ʻū no kekahi manawa? Malia paha ua hele pū me ka phlegm? A i ʻole ke manaʻo nei ʻoe he pōkole iki ka hanu? Hoʻopoina pinepine mākou i kēia mau mea, me ka manaʻo he anu wale nō lākou. Akā, he mea kākaʻikahi loa, aia paha kekahi mea ʻē aʻe ma hope o ia ʻano hōʻailona liʻiliʻi e pono ai mākou e makaʻala. I kēia lā, e kamaʻilio mākou e pili ana i kahi maʻi kanesa kakaʻikahi akā koʻikoʻi loa o nā māmā. ʻO ia hoʻi nā Lung Carcinoid Tumors.
I ka ʻōlelo maʻalahi, he aha kēia mau ʻōpū carcinoid māmā?
Pono kēia i kahi wehewehe iki. Aia kekahi ʻano cell kūikawā i loko o ko kākou kino e pili ana i ka ʻōnaehana nerve a me ka ʻōnaehana hormonal. Kāhea mākou i kēia mau cell neuroendocrine. E noʻonoʻo i kēia mau cell ma ke ʻano he mau mea hoʻonohonoho i loko o ko kākou kino. Ke hele mai kahi leka mai ka ʻōnaehana nerve, ʻo kā lākou hana ka hana ʻana i nā hormones i ka pane ʻana iā ia a kaohi i nā hana like ʻole i loko o ke kino. No ka laʻana, kōkua kēia mau cell i ka kaohi ʻana i ke ala e komo ai ko kākou hanu i loko o nā māmā a me ke ala e neʻe ai ka meaʻai ma o ke ala digestive.
No laila, no kekahi kumu, i ka wā e hoʻomaka ai kēia mau pūnaewele neuroendocrine e māhele a hoʻonui me ke kāohi ʻole ʻia, hoʻokumu ʻia nā puʻupuʻu ma kēlā mau wahi. Kāhea mākou i nā puʻupuʻu carcinoid māmā nā puʻupuʻu kanesa e hoʻomaka ana i loko o kēia mau pūnaewele neuroendocrine i loko o nā māmā.
Akā, mai makaʻu ʻoe ke lohe ʻoe i ka huaʻōlelo "maʻi kanesa." No ka mea, ʻelua ʻano o kēia mau puʻupuʻu carcinoid. ʻOkoʻa loa ke ʻano o nā mea ʻelua.
ʻO nā ʻano nui ʻelua o nā cysts cassinoid
Ua māhele ʻia lākou i ʻelua ʻano nui e pili ana i ko lākou wikiwiki o ka ulu ʻana a me ka hiki ke hoʻolaha.
| ʻAno Puʻupuʻu | Wehewehena |
|---|---|
| Nā Tumor Carcinoid Maʻamau | ʻO kēia ke ʻano maʻamau (90% o nā maʻi i ʻike ʻia no kēia ʻano). Ulu mālie loa lākou. He haʻahaʻa loa hoʻi ko lākou pilikia o ka laha ʻana (metastasizing) i nā ʻāpana ʻē aʻe o ke kino. Hiki ke loaʻa iā lākou ma nā ala ea nui o nā māmā (waena) a i ʻole ma nā ʻaoʻao o waho o nā māmā (peripheral). |
| Nā Tumor Carcinoid Atypical | He mea kākaʻikahi loa kēia ʻano. Loaʻa iā ia ka hiki ke ulu wikiwiki ma mua o ke ʻano maʻamau. Loaʻa iā ia kahi pilikia kiʻekiʻe o ka laha ʻana i nā ʻōpū ʻē aʻe. ʻO kēia ʻano ka mea maʻamau i waena o ka poʻe puhi paka. |
ʻO ka mea nui, ʻaʻole maʻamau loa kēia ʻano. ʻO 1% a 2% wale nō o nā maʻi kanesa māmā a pau i hōʻike ʻia ma ka honua holoʻokoʻa e hāʻule ana i loko o kēia māhele. No laila, ʻaʻohe pono e hopohopo nui ʻia e pili ana i kēia.
He aha nā hōʻailona o kēia maʻi?
ʻO ka hapa nui o ka manawa, ʻoiai hoʻi i nā poʻe me nā cysts maʻamau, ʻaʻohe hōʻailona . ʻIke ʻia lākou ma ka hanana, me he mea lā ma kahi X-ray umauma no kekahi kumu ʻē aʻe. Eia nō naʻe, hiki i kekahi poʻe ke ʻike i kēia mau hōʻailona:
- ʻŪhū mau (i kekahi manawa me ke koko a i ʻole ka mucus)
- ʻEha umauma
- Ka paʻakikī o ka hanu ʻana (dyspnea)
- Ke lohe nei i kahi leo ʻūlū iki i ka wā e hanu ana (wheezing)
He kūlana kūikawā i kapa ʻia ʻo Carcinoid Syndrome
ʻAʻole pinepine loa, hoʻomaka kēia mau puʻupuʻu e hana i ka nui o ka hormone serotonin. Hiki i kēia ke hana i nā hormonal imbalances i loko o ke kino, e alakaʻi ana i nā ʻano hōʻailona like ʻole. Ua kapa ʻia kēia he carcinoid syndrome . ʻO kāna mau hōʻailona:
- Ka maʻi pākī nui
- ʻUlaʻula a manaʻo paha o ka mehana ma ka maka a me ka ʻāʻī (flushing)
- Piʻi ke kaumaha me ke kumu ʻole
- Ka paʻakikī o ka hanu ʻana a i ʻole nā hōʻailona like me ka hānō
Inā loaʻa kēia mau hōʻailona, he mea nui e ʻimi koke i ke kōkua lapaʻau.
No ke aha e like ai kēia ʻano me nā puʻupuʻu? Aia kekahi mau mea pilikia?
ʻO ka mea ʻoiaʻiʻo, ʻaʻole i ʻike ʻia ke kumu kikoʻī i hoʻomaka koke ai kēia mau pūnaewele neuroendocrine e māhelehele me ka ʻole o ke kāohi .
Eia nō naʻe, ua ʻike ʻia kekahi poʻe he ʻoi aku ka nui o ka pilikia o ka loaʻa ʻana o kēia maʻi. ʻO kēia mau mea:
- Loaʻa iā ʻoe kahi maʻi hoʻoilina laha ʻole i kapa ʻia ʻo Multiple Endocrine Neoplasia type 1 (MEN1) .
- ʻO ka puhipaka (ʻoi aku hoʻi no ke ʻano atypical)
- ʻOiai he wahine (ʻoi aku ka nui o ka loaʻa ʻana o kēia ʻano i nā wahine)
- Ma waena o 45 a me 55 mau makahiki. ʻOiai ʻo ka maʻi ka mea i ʻike pinepine ʻia i kēia hui makahiki, hiki ke loaʻa i kēlā me kēia makahiki, ʻoiai i nā keiki ʻuʻuku loa.
Pehea e ʻike ai i kēia maʻi?
Inā loaʻa iā ʻoe kekahi o nā hōʻailona i ʻōlelo ʻia ma luna, pono ʻoe e ʻike mua i kāu kauka. E nīnau ʻo ia iā ʻoe e pili ana i kāu mau hōʻailona, e hoʻolohe i kou umauma me kahi stethoscope, a, inā kānalua, e paipai i kekahi mau hoʻokolohua e hōʻoia i ka hōʻailona.
1. Kiʻi: ʻO ka hana mua, ʻo ia ke kiʻi ʻana i kahi X-ray umauma . Inā loaʻa kekahi mau mea ʻē, hiki ke kauoha ʻia kahi CT scan (Computed Tomography scan) . Hiki i kahi CT scan ke hana i nā kiʻi ʻokiʻoki maopopo loa o nā māmā, e ʻae ana i ka nui a me kahi o ka puʻupuʻu e hoʻoholo ʻia.
2. Nā hoʻāʻo koko a me ka mimi: Hana ʻia kēia mau hoʻāʻo e ʻike inā aia kekahi mau hormones i hana ʻia e kēia mau puʻupuʻu i loko o ke koko a i ʻole ka mimi.
3. Biopsy: ʻO kēia ka hoʻāʻo koʻikoʻi loa e hōʻoia i ka maʻi 100%. Maanei, lawe ʻia kahi ʻāpana liʻiliʻi loa o ka ʻiʻo mai ka puʻupuʻu a nānā ʻia ma lalo o kahi microscope. Hiki i kēia ke hoʻoholo pololei inā he puʻupuʻu carcinoid ka puʻupuʻu, maʻamau a atypical paha. ʻO ke ʻano maʻamau i hoʻohana ʻia e kiʻi i kēia laʻana ʻiʻo ʻo ia ka bronchoscopy . Maanei, hoʻokomo ʻia kahi ʻōmole lahilahi me kahi kāmela liʻiliʻi ma o nā ala ea e nānā ai i ka puʻupuʻu a lawe ʻia kahi ʻāpana liʻiliʻi.
He aha nā koho lapaʻau?
ʻO ke ʻano lapaʻau maikaʻi loa nou e pili ana i ke ʻano, ka nui, kahi o ka puʻupuʻu, a me kou olakino holoʻokoʻa. ʻO ka nūhou maikaʻi , hiki ke ho'ōla loa ʻia ka hapa nui o nā puʻupuʻu carcinoid māmā me ke ʻoki kino wale nō.
Aia kekahi mau koho lapaʻau nui:
- ʻO ke ʻoki kino:
- Lobectomy: Wehe piha ʻana i ka lobe o ka māmā kahi i loaʻa ai ka puʻupuʻu.
- ʻO ka Wedge Resection: Wehe ʻana i ka puʻupuʻu wale nō a me kahi ʻiʻo liʻiliʻi a puni ia.
- Pneumonectomy: He mea kākaʻikahi loa, pono paha e wehe ʻia ka māmā holoʻokoʻa.
- Ka wehe ʻana i nā kīpē lymph: Hiki i ke kauka lapaʻau ke hoʻoholo e wehe i nā kīpē lymph kokoke e ʻike inā ua pālahalaha ke kanesa a pale i ka laha hou ʻana.
- Lapaʻau Radiation: Hāʻawi ʻia kēia lāʻau lapaʻau inā ʻaʻole hiki i ke ʻoki kino ke wehe loa i ka puʻupuʻu a i ʻole inā aia ka mea maʻi i loko o kahi kūlana olakino e hiki ʻole ai ke ʻoki kino. Pili ia i ka radiation kukuna waho a i ʻole ke kau ʻana o nā mea radioactive liʻiliʻi kokoke i ka puʻupuʻu (brachytherapy).
- Kemokalama:Ma muli o ka ulu lohi ʻana o kēia mau puʻupuʻu, ʻaʻole maikaʻi loa ka chemotherapy maʻamau, ka mea e kuhikuhi ana i nā cell e ulu wikiwiki ana. No laila, ʻaʻole hāʻawi pinepine ʻia kēia lāʻau i nā ʻano maʻamau. Eia nō naʻe, pono paha kēia lāʻau no nā ʻano atypical e ulu wikiwiki ana a i ʻole i ka wā i pālahalaha ai lākou i nā ʻōpū ʻē aʻe.
- Nā lāʻau lapaʻau ʻē aʻe:
- Octreotide: Hāʻawi ʻia kēia lāʻau hormonal e kāohi i nā hōʻailona i hoʻokumu ʻia e ka maʻi carcinoid.
- Nā mea hoʻopaʻa MTOR (e like me Everolimus): He ʻano lāʻau lapaʻau e kāohi ai i ka ulu ʻana o ka puʻupuʻu.
He aha ka nui o ka ho'ōla a me ka nānā ʻana?
He pilikia kēia no nā kānaka he nui.
He maikaʻi loa ka wānana no nā ʻōpū carcinoid maʻamau. ʻOi aku ka liʻiliʻi o ka pilikia o ka hoʻi hou ʻana ma hope o ke ʻoki ʻana ma mua o 4%. ʻO ke ʻano kēia he 96 o 100 mau kānaka e ho'ōla piha ʻia.
ʻOi aku ka paʻakikī o ka mālama ʻana i nā ʻōpū carcinoid atypical. ʻOi aku ka kiʻekiʻe o ka pilikia o ka hoʻi hou ʻana. Eia nō naʻe, hiki ke hoʻomalu pono ʻia kēia ʻano ma ka hoʻohana ʻana i ka hui pū ʻana o nā ʻano lāʻau like ʻole.
Ma keʻano holoʻokoʻa, ʻo ka nui o ke ola ʻana o ʻelima makahiki no nā ʻano puʻupuʻu carcinoid māmā āpau he 89% . ʻO ke ʻano kēia, mai loko mai o 100 poʻe i ʻike ʻia me kēia maʻi, 89 e olakino mau ana ma hope o 5 mau makahiki.
Āhea ʻoe e ʻike ai i ke kauka?
Inā loaʻa iā ʻoe nā hōʻailona hou a i ʻole e ʻoi aku ka ʻino, ʻoiai ka pōkole o ka hanu, ka maʻi pākī, a i ʻole ka pohō kaumaha i wehewehe ʻole ʻia, e haʻi i kāu kauka. Mai kānalua e kamaʻilio e pili ana i kekahi mau nīnau a hopohopo paha.
I ka manawa hea e hele koke ai i ka ETU (Emergency Treatment Unit)
Inā loaʻa iā ʻoe nā hōʻailona koʻikoʻi ma lalo nei, e hele koke i ka Emergency Department (ETU) o ka haukapila kokoke loa:
- Manaʻo nui i ka hanu ʻole (ʻoiai i ka wā e hoʻomaha ai).
- Ke ʻū ʻana i ke koko.
- ʻEha hou a ʻeha paha ka ʻeha o ka umauma.
- Ka huikau a i ʻole ka ʻike i loli.
- ʻO ke kala polū o ka ʻili, nā lehelehe, a i ʻole nā kui lima (cyanosis).
Nā nīnau e nīnau aku ai i kāu kauka
He mea maʻamau ka loaʻa ʻana o nā nīnau ke loaʻa iā ʻoe kahi hōʻailona e like me kēia. He mea kōkua paha ka nīnau ʻana i kāu kauka i nā nīnau e like me kēia:
- He mea maʻamau kēia a i ʻole he mea ʻē aʻe?
- Ua laha anei kēia i nā wahi ʻē aʻe?
- He aha ka lāʻau lapaʻau āu e paipai nei?
- He aha ke ʻano o ka nānā ʻana no kēia ʻano puʻupuʻu?
- Pehea e mālama ai i nā hōʻailona ma ka home?
He ʻike paʻakikī ka loaʻa ʻana o kahi hōʻailona o kekahi maʻi kanesa. Akā e hoʻomanaʻo, ʻo ka hapa nui o nā carcinoids māmā he hiki ke mālama ʻia a he haʻahaʻa ka pilikia o ka hoʻi hou ʻana. E kamaʻilio ākea me kāu hui lapaʻau e pili ana i ka mea e manaʻo ai no kou kūlana. E wehewehe lākou i nā koho lapaʻau maikaʻi loa iā ʻoe a pane i nā nīnau āu e loaʻa ai.
Leka Lawe-Home
- ʻO nā ʻōʻō carcinoid pulmonary kahi maʻi kanesa kakaikahi e kū ana i loko o nā māmā.
- ʻO ke ʻano maʻamau, ʻo ia hoʻi ke ʻano 'maʻamau', ulu lohi loa ia a hiki ke ho'ōla loa ʻia me ke ʻoki kino wale nō.
- ʻAʻole ʻike ka hapa nui o ka poʻe i kekahi mau hōʻailona . Inā loaʻa nā hōʻailona, hiki iā lākou ke komo pū me ka ʻū lōʻihi, ka ʻeha o ka umauma, a i ʻole ka paʻakikī o ka hanu ʻana.
- Aia ka lāʻau lapaʻau i ke ʻano a me ka nui o ka puʻupuʻu. ʻO ke ʻoki kino ka lāʻau lapaʻau nui a maikaʻi loa.
- He kiʻekiʻe loa ka nui o ka ho'ōla ʻana no kēia maʻi . No laila, he mea nui loa ka hana ʻana ma ke ʻano he ʻōlelo aʻoaʻo lapaʻau kūpono me ka ʻole o ka hoʻokumu ʻana i ka makaʻu pono ʻole.
- ʻO ka pale ʻana i ka puhipaka ke ala maikaʻi loa e pale aku ai i nā maʻi māmā he nui.











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