Ke manaʻo nei ʻoe ua nui loa ke kaomi o kou mau māmā? E kamaʻilio kākou e pili ana i ka Chronic Thromboembolic Pulmonary Hypertension (CTEPH)!

Ke manaʻo nei ʻoe i kekahi manawa he pōkole iki ka hanu, a i ʻole he manaʻo ʻē i loko o kou umauma? Hiki paha ke kiʻekiʻe iki ke kaomi i loko o nā kīʻaha koko i loko o kou mau māmā. He kūlana kūikawā kēia i kapa ʻia ʻo `(Chronic Thromboembolic Pulmonary Hypertension)` a i ʻole `(CTEPH)`. Mai hopohopo, e kamaʻilio maʻalahi mākou e pili ana i kēia, ma ke ʻano e hiki ai iā ʻoe ke hoʻomaopopo.

He aha kēia `(CTEPH)`? E hoʻomaopopo pono kākou!

I ka ʻōlelo maʻalahi, ʻo CTEPH kahi piʻi ʻana o ke koko i loko o nā kīʻaha koko liʻiliʻi i loko o nā māmā. Ua like ia me ke kaomi i loko o kahi paipu wai. Akā ʻo ke kumu nui o kēia , ua loaʻa iā ʻoe kahi ʻūlū koko i loko o kou mau māmā ma mua (kapa mākou i kēia he Pulmonary Embolism) a ʻaʻole i hoʻoheheʻe pono ʻia ke ʻūlū . ʻO ia ka manawa e piʻi ai kēia kaomi.

ʻO wai ka mea i ʻoi aku ka paʻakikī o ka loaʻa ʻana o CTEPH?

He mea nui loa kēia. Loaʻa wale ka CTEPH i nā poʻe i loaʻa ka mōʻaukala o ka pulmonary embolism . Inā he kiʻekiʻe kou kaomi i loko o kou mau māmā akā ʻaʻohe ʻūpā koko, ʻaʻole paha he CTEPH, akā he ʻano ʻokoʻa. No laila he mea nui e hoʻomaopopo i kēia ʻokoʻa.

Pehea ka maʻamau o kēia ʻano?

He maʻi laha ʻole ka CTEPH. No ka laʻana, ma kahi ʻāina e like me ʻAmelika Hui Pū ʻIa, ma kahi o 5,000 mau hihia hou i hōʻike ʻia i kēlā me kēia makahiki. Eia nō naʻe, ʻoiai ʻaʻole i ʻike pono ʻia i kekahi manawa, ʻoi aku ka nui o ka helu. No laila, he mea nui loa ka makaʻala i nā hōʻailona.

He aha ka hopena o CTEPH i kou olakino?

Ke piʻi aʻe ke kaomi i loko o kou mau māmā, ʻoiai hoʻi i ka hihia o CTEPH, ʻike nui ka ʻaoʻao ʻākau o kou puʻuwai i ke kaomi . E noʻonoʻo, pono kou puʻuwai e hana ikaika e pamu i ke koko i kou mau māmā. ʻO ka mea e hana ʻia, ʻo ia ke paʻa ʻana o kekahi o ke koko nele i ka oxygen i loko o kou puʻuwai a lōʻihi ka manawa e hiki ai i kou mau māmā. Hiki i kēia ke hana i kou kino e loaʻa i nā pae oxygen haʻahaʻa. He kūlana koʻikoʻi loa kēia, ʻeā?

No ke aha e ulu ai kēia `(CTEPH)`? He aha nā kumu?

ʻO ke kumu nui o kēia, ʻo ia ka hoʻoheheʻe pono ʻole ʻana o nā ʻōpū koko i hana ʻia i loko o nā kīʻaha koko liʻiliʻi i loko o nā māmā. Ke hana ʻia kēia , e hana ʻia nā ʻiʻo e like me ka ʻōpala ma kahi i loaʻa ai nā ʻōpū. ʻO kēia ʻōpala ke kumu o ka wili ʻana o nā kīʻaha koko e ololi, e like me ka paipu wai e paʻa ana. I ka piʻi ʻana o kēia wili ʻana, e piʻi pū ana ke kaomi.

He aha nā kumu pilikia no ka hoʻomohala ʻana o CTEPH?

Aia kekahi mau mea pilikia e hiki ke kōkua i ka ulu ʻana o `(CTEPH). E nānā kākou i ko lākou ʻano:

• ʻOkoʻa ke ʻano koko o ka ʻAno O.
• Loaʻa kahi maʻi i nā iwi (Osteomyelitis).
• Kekahi mau ʻano maʻi ʻaʻai.
• Nā maʻi ʻōpū mau loa, no ka laʻana, nā kūlana e like me ka `(Inflammatory Bowel Disease)`.
• ʻOiai he wahine. (ʻOi aku ka nui o ka loaʻa ʻana o kēia maʻi i nā wahine ma mua o nā kāne.)
• ʻO ka maʻi o ka ʻiʻo puʻuwai ma muli o kahi pacemaker.
• Loaʻa iā ʻoe a i ʻole kekahi o kou ʻohana kahi moʻolelo o nā maʻi koko koko, e like me ka Antiphospholipid Syndrome.
• Ma hope o ka wehe ʻana o ka spleen ma mua (Splenectomy).
• Ke lawe nei i ka lāʻau hoʻololi hormone thyroid.

ʻAʻole hoʻopilikia kēia mau mea a pau i nā kānaka a pau, akā ua ʻike ʻia lākou he mau mea pilikia.

He aha nā hōʻailona o ka `(CTEPH)`?

Hiki i kekahi kanaka me CTEPH ke ʻike i nā hōʻailona e like me:

• Ka manaʻo o ka ʻeha o ka umauma a i ʻole ka ʻūmiʻi .
• Ke ʻū ʻana i ke koko (he mea laha ʻole kēia).
• ʻO ke kala polū o nā manamana lima a me nā manamana wāwae (Cyanosis).
• Manaʻo puni ke poʻo .
• ʻO ka syncope.
• Manaʻo luhi loa ('Fatigue') .
• ʻO ka manaʻo e like me ke kuʻi ʻana o kou umauma, kapa mākou i kēia ʻo "Heart Palpitations".
• Paʻakikī ka hanu ʻana , ʻoiai i ka wā e hana ai i kekahi mea a i ʻole e hele wāwae ana.
• ʻO ka pehu ʻana o nā wāwae, ma muli o ka hōʻiliʻili ʻana o ka wai i loko o ke kino (edema).

Mai manaʻo he CTEPH kou no ka mea he hoʻokahi a ʻelua paha o kēia mau hōʻailona kou. Akā inā hoʻomau kēia mau hōʻailona, ​​ʻoi aku ka maikaʻi o ke ʻike ʻana i ke kauka.

Pehea e ʻike ʻia ai kēia maʻi `(CTEPH)`?

Ke ʻike ʻoe i ke kauka, hana mua paha ʻo ia i kekahi mau hoʻokolohua e nānā ai no CTEPH, e like me:

• He hoʻokolohua e nānā ana i ka ea a me ka lako koko i nā māmā (`(Lung ventilation-perfusion scan - V/Q scan)`).
• ʻO ka "Pulmonary Angiogram" kahi hoʻokolohua e nānā ai i nā ʻūpā koko a i ʻole ka haiki ʻana o nā kīʻaha koko o nā māmā.
• Nā Hoʻāʻo Hana o ka Puʻuwai.
• Ua like ka Transthoracic Echocardiogram (TTE) me ke kiʻi ultrasound o ka puʻuwai.

Ma hope o kēia mau hoʻokolohua mua, pono paha nā hoʻokolohua hou aʻe e hōʻoia i ka hōʻailona o CTEPH a hoʻoholo i kona koʻikoʻi. Hiki i kēia mau mea ke komo pū me:

• ʻO ke Catheterization o ka Puʻuwai ʻĀkau kahi hoʻokolohua e ana i ke kaomi ma ke hoʻokomo ʻana i kahi ʻōmole liʻiliʻi i loko o ka ʻaoʻao ʻākau o ka puʻuwai.
• E nānā i nā aʻa i loko o nā māmā me ka hoʻohana ʻana i nā ʻano hana kiʻi holomua e like me CT Pulmonary Angiography (CTPA) a i ʻole Digital Subtraction Angiography.
• He kiʻi MRI.
• He "Hoʻāʻo Koʻikoʻi Hoʻoikaika Kino" e nānā ai i ka hana o ka puʻuwai i ka wā e hoʻoikaika kino ana.

ʻO kēia mau hoʻokolohua ka mea e hiki ai i nā kauka ke hoʻoholo pono inā loaʻa iā ʻoe ʻo CTEPH a me ke kahua hea ia.

He aha nā lāʻau lapaʻau no ka `(CTEPH)`?

ʻO ka maʻamau, ʻo ka mālama ʻana no CTEPH e pili ana i ke ʻoki kino a i ʻole kahi hana like. ʻElua mau koho nui:

1. Pulmonary Endarterectomy : He hana ʻoki kino hāmama kēia. Ma kēia kaʻina hana, wehe ʻia nā ʻōpū koko kahiko a me nā ʻiʻo ʻeha i paʻa i loko o nā aʻa o nā māmā ma ke ʻoki kino. Hana ʻia kēia e hoʻāʻo e hoʻihoʻi i ke kahe koko i nā māmā.

2. ``(Angioplasty Balon Pulmonary)`'Ma kēia, ua hoʻopili ʻia kahi pōpō liʻiliʻi ma ka hopena o kahi ʻōmole lōʻihi (catheter), kahi e hoʻokomo ʻia i loko o ke kīʻaha koko i haiki ʻia i loko o nā māmā. Hoʻopiha ʻia ka pōpō e hoʻokuke i ka ʻiʻo ʻeha i ka ʻaoʻao, e hoʻonui hou ana i ke kīʻaha koko.

ʻO ke koho ʻana i kekahi o kēia mau ʻano hana ʻelua e pili ana i nā kumu he nui, e like me ke kūlana o ka mea maʻi a me kahi o ke koko i hoʻopaʻa ʻia.

Aia kekahi mau koho lapaʻau ʻē aʻe?

ʻAe, ʻaʻole hiki i kekahi poʻe ke hana i kēia ʻoki kino. No kēlā poʻe, a i ʻole no ka poʻe e hoʻomau nei i ke kaomi i loko o ko lākou mau māmā ma hope o ke ʻoki kino, hiki ke hāʻawi ʻia kahi pila i kapa ʻia ʻo `(Riociguat)` . He lāʻau lapaʻau kēia i hāʻawi ʻia no ke koko kiʻekiʻe o ka pulmonary. Kōkua kēia i ka hōʻoluʻolu ʻana i nā hōʻailona.

Hiki ke pale ʻia ka CTEPH?

He pilikia ka CTEPH o nā maʻi olakino ʻē aʻe he nui. ʻO kekahi mau mea hiki ʻole iā mākou ke kaohi. Akā ʻo ka mea nui loa hiki iā ʻoe ke hana, ʻo ia ka mālama pono ʻana i kou mau māmā . ʻO ia hoʻi, he mea nui loa ka haʻalele ʻana i ka paka inā ʻoe e puhipaka.

He aha ka manaʻo no nā maʻi me CTEPH?

ʻO kēia ka nūhou maikaʻi loa! Hiki i ka Pulmonary Endarterectomy a me ka Pulmonary Balloon Angioplasty ke ho'ōla loa i ka CTEPH . Nui ka poʻe e hana nei i kēia mau lāʻau lapaʻau e ʻike i nā hopena maikaʻi loa.

Eia nō naʻe, me kēia mau hopena maikaʻi, hiki i kekahi mau maʻi ke loaʻa i kekahi ʻano o ka pilikia noʻonoʻo, ka hopohopo, a me ke kaumaha. Hiki ke ʻoiaʻiʻo kēia no ka poʻe i kūpono ʻole no nā lāʻau lapaʻau i ʻōlelo ʻia ma luna. Inā ʻoe e ʻike nei i kekahi o kēia mau pilikia noʻonoʻo, e kamaʻilio me kāu kauka. Hiki iā lākou ke hoʻolohe i kāu mau hopohopo a ʻōlelo i nā lāʻau lapaʻau e kōkua iā ʻoe e ʻoluʻolu.

He aha nā mea nui e ʻike ai i ka wā e noho pū ana me ka `(CTEPH)`?

• Pono paha ʻoe e lawe i nā lāʻau hoʻokahe koko no ke koena o kou ola .
• Inā ʻoe e lawe ana i kahi lāʻau lapaʻau e like me Warfarin, pono paha ʻoe e kaupalena i kekahi mau meaʻai (e like me ka soy a me ka broccoli, i waiwai nui i ka wikamina K). E nīnau i kāu kauka e pili ana i kēia.
• Hiki i ka hoʻoikaika kino māmā , e like me ka hele wāwae, ke kōkua i nā poʻe he nui e hoʻihoʻi i ka ikaika a noho olakino. Hiki i kāu kauka ke ʻōlelo aku i kahi papahana hoʻoikaika kino i mālama ʻia (pulmonary rehabilitation).

ʻO ka mea hope loa, e hoʻomanaʻo i kēia.

ʻO ke Chromboembolic Pulmonary Hypertension (CTEPH) kahi maʻi kakaikahi kahi e piʻi ai ke koko i loko o nā kīʻaha koko o nā māmā, akā he maʻi hiki ke mālama ʻia inā ʻike mua ʻia a mālama pono ʻia . Inā loaʻa iā ʻoe kekahi o kēia mau hōʻailona, ​​​​mai kānalua e ʻimi i ke aʻo lapaʻau. E hoʻomanaʻo, me ka mālama kūpono, hiki i ka hapa nui o ka poʻe ke hoʻōla maikaʻi. No laila, mai hopohopo. E hahai pono i nā ʻōlelo a kāu kauka, a e hiki iā ʻoe ke hoʻōla koke!

`CTEPH, Ke koko kiʻekiʻe o ka puʻuwai, Nā ʻūpā koko, Paʻakikī hanu, Maʻi puʻuwai, Pulmonary Embolism, Pulmonary Hypertension