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Ke kahe nui nei hoʻi ʻoe i ke koko mai kahi ʻeha liʻiliʻi? E nānā kākou i ka ITP (Immune Thrombocytopenia)!

Ke kahe nui nei hoʻi ʻoe i ke koko mai kahi ʻeha liʻiliʻi? E nānā kākou i ka ITP (Immune Thrombocytopenia)!

Ke noʻonoʻo nei paha ʻoe i kekahi manawa no ke aha e lilo ai kahi ʻeha liʻiliʻi i ʻeha nui, a no ke aha e pau ʻole ai ke kahe ʻana o ke koko i kahi ʻoki liʻiliʻi? A i ʻole ke ʻike nei ʻoe i nā mea e like me ke kahe ʻana o ka ihu me ke kumu ʻole, a i ʻole ke kahe ʻana o nā ʻāʻī i ka wā e palaki ai i kou mau niho? Inā hana pinepine ʻia kēia mau mea iā ʻoe, he mea nui paha iā ʻoe ke ʻike i ke kūlana a mākou e kamaʻilio nei i kēia lā i kapa ʻia ʻo ITP (Immune Thrombocytopenia). Mai hopohopo, e kamaʻilio maʻalahi kākou e pili ana i kēia.

He aha ka ITP (Immune Thrombocytopenia)?

I ka ʻōlelo maʻalahi, ʻo ITP (Immune Thrombocytopenia) kahi kūlana i loaʻa ai i kou koko kahi helu haʻahaʻa o nā ʻāpana liʻiliʻi i kapa ʻia he platelets . ʻO kēia mau platelets ka mea e kōkua ai i ka hoʻōki ʻana i ke kahe ʻana ke loaʻa iā mākou kahi ʻeha ma kekahi wahi o ko mākou kino. Hoʻokumu lākou i kahi clot a hoʻōki i ke kahe ʻana . No laila, i ka wā e emi ai ka helu o kēia mau platelets, ʻaʻole e maʻalahi ke kāpili ʻana o kou koko. ʻO ia ke kumu hiki i kahi ʻeha liʻiliʻi ke hoʻoulu i ke kahe nui ʻana, a i ʻole hiki iā ʻoe ke ʻeha wale i kou kino.

Ua kapa ʻia kēia ʻo ITP, a ʻo ka huaʻōlelo 'Immune' ke ʻano o kahi mea e pili ana i ka ʻōnaehana pale. ʻO 'Thrombocytopenia' ke ʻano o nā platelets haʻahaʻa. No laila, ʻo ka mea e hana ʻia ma kēia, ʻo kāu ʻōnaehana pale ponoʻī, nā koa e pale iā mākou mai ka maʻi, manaʻo kuhihewa he ʻenemi waho kāu mau cell platelet ponoʻī a hoʻouka a luku iā lākou. Ua like ia me ka hoʻouka ʻana i kekahi i loko o kou hale ponoʻī, me ka manaʻo he ʻaihue lākou.

I kekahi manawa hiki ke mālama ʻia ka ITP me ka lāʻau lapaʻau a i ʻole me ka ʻole o ka lāʻau lapaʻau a lilo i mea maikaʻi i ka hala ʻana o ka manawa. Akā no kekahi poʻe, hiki ke lilo i maʻi mau loa . ʻO ke ʻano kēia, ʻoiai hiki ke kāohi ʻia nā hōʻailona, ​​​​​​he paʻakikī ke ho'ōla loa. I kēlā poʻe, pono paha ka lāʻau lapaʻau no ke koena o ko lākou ola.

He aha nā inoa ʻē aʻe no ITP?

Ke hele ʻoe i ke kauka, hoʻohana paha lākou i nā inoa ʻē aʻe ma waho aʻe o ITP. No laila he manaʻo maikaʻi e hoʻomanaʻo i kēia mau inoa pū kekahi:

  • ʻO ka Purpura Thrombocytopenic Autoimmune
  • ʻO ka Purpura Thrombocytopenic Immune
  • ʻO ka ʻōlelo ʻo `Idiopathic Thrombocytopenic Purpura` (Ua hoʻohana nui ʻia kēia inoa i ka wā ma mua, ʻo ke ʻano o `Idiopathic` ʻaʻole ʻike ʻia ke kumu pololei)
  • ʻO ka maʻi Werlhof
  • ʻO ka Thrombocytopenia Autoimmune

ʻOiai ke ʻano o ka inoa āu e hāʻawi ai, pili pinepine ia i ke ʻano olakino like.

Pehea ka maʻamau o ka ITP?

ʻOiaʻiʻo, he maʻi laha ʻole ka ITP. ʻAʻole ia he maʻi e pili ana i nā kānaka a pau. Ma ke ʻano helu, ma kahi ʻāina e like me ʻAmelika, ma kahi o ʻehā o kēlā me kēia haneli tausani (4/100,000) mau keiki a ʻekolu o kēlā me kēia haneli tausani (3/100,000) mau mākua i ʻike hou ʻia me kēia maʻi i kēlā me kēia makahiki. ʻIke ʻia kēia maʻi ma Sri Lanka, akā he mea paʻakikī iki ka loaʻa ʻana o nā helu kikoʻī e pili ana iā ia. Akā, inā loaʻa i kekahi kēia maʻi, hiki ke lilo i pilikia nui no lākou, ʻeā?

Aia kekahi mau ʻano o ka ITP?

ʻAe, hiki ke hoʻokaʻawale ʻia ka ITP i ʻelua mau ʻano nui:

1. ITP mua:ʻO kēia ka manawa e hoʻouka ai kāu ʻōnaehana pale ponoʻī i kāu mau platelets me ke kumu ʻole. Ma kahi o 80 pakeneka (80%) o nā maʻi ITP i loaʻa i kēia ʻano. He "maʻi autoimmune" ia, ʻo ia hoʻi, ua hana ʻia e ka hana hewa ʻana o ka ʻōnaehana pale.

2. ITP lua: Hana ʻia kēia i ka wā e emi ai ka helu platelet ma ke ʻano he hopena ʻaoʻao o kekahi maʻi lapaʻau ʻē aʻe, ka maʻi, a i ʻole ka lāʻau lapaʻau. Eia kekahi laʻana:

  • ʻO kekahi mau maʻi lōʻihi, e like me ka HIV, Hepatitis C, a i ʻole H. pylori (kahi bacteria e hoʻoulu ai i nā ʻōpū ʻōpū)
  • Nā maʻi ʻaʻai koko
  • Nā 'maʻi autoimmune' ʻē aʻe (e.g. lupus - SLE)
  • Hiki paha ke kumu o kekahi mau lāʻau lapaʻau.

Hoʻokaʻawale pū nā kauka i ka ITP ma muli o ka lōʻihi o kona noho ʻana:

  • ITP ʻoi: E hoʻomaikaʻi pinepine kēia i loko o ʻekolu mahina. ʻO ia ka mea maʻamau i nā keiki.
  • ITP mau loa: Hiki i kēia ke mau mai ʻekolu mahina a i ʻumikūmālua mahina (hoʻokahi makahiki).
  • ITP Mau Loa: ʻOi aku kēia ma mua o hoʻokahi makahiki. ʻO ka mea maʻamau ia i nā pākeke.

He aha nā hōʻailona o ka ITP?

Loaʻa paha i kekahi poʻe ka ITP me ka ʻole o nā hōʻailona. Eia nō naʻe, inā loaʻa nā hōʻailona, ​​hiki ke hele mālie a koke paha. ʻO nā hōʻailona nui:

  • Petechiae: ʻO kēia ka wā e ʻike ai ʻoe i nā kiko ʻulaʻula liʻiliʻi a poni paha ma kou ʻili, ʻoi aku hoʻi ma nā wāwae haʻahaʻa. Ua like lākou me ka ʻulaʻula. ʻAʻole e nalo wale kēia mau mea.
  • Purpura: Hoʻohui ʻia nā petechiae i ʻōlelo ʻia ma mua e hana i nā kiko ʻulaʻula, poni, a ʻeleʻele paha. He ʻuʻuku kēia ma mua o kahi palapū, akā ʻoi aku ka nui ma mua o kēlā mau kiko. Hoʻokumu ʻia kēia e kahi liʻiliʻi o ke koko e kahe ana mai nā kīʻaha koko liʻiliʻi ma lalo o ka ʻili.
  • ʻO nā palapū maʻalahi: ʻOiai kahi puʻupuʻu liʻiliʻi ma kekahi wahi hiki ke hana i kahi palapū nui a palapū paha. I kekahi manawa, hiki ke ʻike ʻia nā palapū me ke kumu ʻole.
  • ʻĀʻī koko: Hiki ke koko kou ʻāʻī ke palaki ʻoe i kou mau niho a i ʻole ke kū mālie ʻoe. Hiki ke ʻike ʻia kou ʻāʻī ua pehu.
  • Koko i loko o ka ʻōpala: Inā ʻeleʻele loa ke ʻano o kou ʻōpala, e like me ke kēpau, he koko kūloko paha ia.
  • Koko i loko o ka mimi: Inā he ʻulaʻula a ʻulaʻula paha ka wai i loko o ke pola lua i kou mimi ʻana, aia paha no ka mea he koko i loko o ka mimi.
  • Nā wā menstruation kaumaha i nā wahine: Inā ʻoi aku ka lōʻihi o kou wā mahina ma mua o ʻehiku mau lā, a inā ʻoi aku kou kahe ʻana o ke koko ma mua o ka maʻamau ('Menorrhagia`), hiki i kēlā ke hōʻailona o ITP.
  • Ka kahe pinepine ʻana o ke koko ihu.
  • ʻEha nui (Hematoma): I kekahi manawa hiki ke hana ʻia kahi ʻeha nui a pehu (`Hematoma`) ke hōʻiliʻili ka nui o ke koko ma kahi hoʻokahi.
  • Manaʻo luhi loa (Fatigue).

Mea nui: Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​he mea nui loa e ʻike koke i ke kauka no ka ʻōlelo aʻo.

He aha nā kumu o ka ITP?

E like me kā mākou i kūkākūkā ai ma mua, hana ʻia ka ITP ke hana hewa kāu ʻōnaehana pale i nā antibodies e kūʻē i kāu mau platelets ponoʻī, a laila e haʻi aku i nā cell immune ʻē aʻe e luku iā lākou. Ke hōʻino ʻia kahi kīʻaha koko i loko o kou kino, ʻo nā platelets ka poʻe e hele mai i kahi, e pili pū ana, e hana i kahi clot koko, a hoʻōki i ke kahe ʻana o ke koko. Ua kapa ʻia kēia he "hemostasis mua".

Eia nō naʻe, ʻaʻole maopopo i nā loea ke kumu e hoʻomaka ai kēia ʻōnaehana pale e hoʻouka i kāna mau platelets ponoʻī.

Eia nō naʻe, ua ʻike ʻia kekahi mau noiʻi:

  • No ka poʻe i loaʻa i ka `(HIV)` (Human Immunodeficiency Virus)
  • No nā poʻe me ka maʻi bacteria i kapa ʻia ʻo `(H. pylori)` (Helicobacter pylori) (pili pinepine kēia i nā ʻōpū ʻōpū a me ka gastritis)
  • No nā kānaka me ka maʻi akepaʻa i kapa ʻia ʻo `(Hepatitis C)`

Aia kahi pilikia nui o ka hoʻomohala ʻana i ka ITP. Hiki i kēia ke alakaʻi i ka ITP lua.

Pehea e ʻike ʻia ai ka ITP?

Ma mua o ka hiki ʻana i ke kauka ke hoʻoholo inā loaʻa iā ʻoe ka ITP, e hana mua lākou i kahi hoʻokolokolo kino piha e nānā i nā hōʻailona o ke kahe koko, ka palapū, a me nā kiko e like me ka petechiae a me ka purpura. A laila e nīnau lākou e pili ana i kou mōʻaukala olakino i hala, nā lāʻau lapaʻau āu e lawe nei, a inā paha ua loaʻa i kekahi o kou ʻohana nā pilikia kahe koko.

Ma muli o ka like o nā hōʻailona o ITP me nā maʻi koko ʻē aʻe a i ʻole nā ​​​​maʻi ʻoi aku ka koʻikoʻi e like me ke kanesa koko, e kāpae ke kauka i nā kumu ʻē aʻe a pau (kahi hōʻailona o ka hoʻokaʻawale ʻana) ma mua o ka hana ʻana i ka hōʻoia paʻa o ITP.

He aha nā hoʻokolohua i hoʻohana ʻia e ʻike ai i ka ITP?

Hana pinepine nā kauka i kēia mau hoʻokolohua:

  • Helu Koko Piha (CBC): Nānā kēia i ka helu o nā ʻano ʻano cell like ʻole i loko o kou koko, me nā cell ʻulaʻula, nā cell keʻokeʻo, a me nā platelets . I ka ITP, haʻahaʻa loa paha kēia mau platelets.
  • ʻO ka Smear Koko Peripheral: Ma kēia hoʻokolohua, lawe ʻia kahi kulu koko, hohola ʻia ma luna o kahi slide aniani, a nānā ʻia ma lalo o kahi microscope e ʻike inā he maʻamau ke ʻano a me ka nui o nā platelets, a inā he mau mea ʻē aʻe.

Inā manaʻo kāu kauka ua pilikia ʻoe no ka maʻi HIV, Hepatitis C, a i ʻole H. pylori, hiki iā lākou ke hana i nā hoʻokolohua no kēlā mau maʻi. I kekahi manawa hiki ke hana ʻia kahi biopsy iwi, akā ʻaʻole hana ʻia kēia no nā mea āpau.

He aha nā lāʻau lapaʻau no ITP?

ʻO ka hapa nui o ka manawa,Ke loaʻa i nā keiki ka ITP, inā ʻaʻole koʻikoʻi nā hōʻailona, ​​e hoʻomaikaʻi lākou me ka ʻole o ka lāʻau lapaʻau. Eia nō naʻe, pono pinepine ka lāʻau lapaʻau i nā pākeke, ʻoiai inā haʻahaʻa loa ka helu o ko lākou platelet a inā paha he pilikia o ke kahe ʻana o ke koko.

Inā makemake ʻoe i ka lāʻau lapaʻau, hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e hoʻonui i kāu helu platelet a i ʻole e hoʻōki i kāu ʻōnaehana pale mai ka hoʻouka ʻana i kāu mau platelet. ʻO nā ʻano lāʻau lapaʻau nui i hoʻohana ʻia:

  • ʻO Corticosteroids: (e.g. Prednisolone). Hana kēia ma ka hoʻōki ʻana i ka hana ʻana o nā antibodies e luku ai i nā platelets. He lāʻau lapaʻau laina mua kēia.
  • Immunoglobulin (IVIg): He lāʻau lapaʻau kēia i hāʻawi ʻia ma ke kino. Hoʻololi pū ia i ka hana o ka ʻōnaehana pale a hōʻemi i ka luku ʻia ʻana o nā platelets.
  • ʻO nā agonists receptor Thrombopoietin (TPO-RAs): Kōkua kēia mau lāʻau i ke kino e hana i nā platelets hou aku.
  • Nā lāʻau pale kino: (e.g. Rituximab, Mycophenolate). Hoʻemi kēia i ka hana o ka ʻōnaehana pale kino a hoʻōki i ka luku ʻia ʻana o nā platelets.

Ma waho aʻe o kēia mau lāʻau lapaʻau, hiki i ke kauka ke ʻōlelo i nā hana ʻē aʻe:

  • Ke mālama ʻana i kahi maʻi kumu: I nā hihia o ka ITP lua, hiki ke hoʻi ka helu platelet i ka maʻamau ke mālama ʻia ka maʻi i hoʻokumu ai.
  • Ke hoʻōki nei i kekahi mau lāʻau lapaʻau: Inā ʻoe e lawe ana i kekahi mau mea hoʻokahe koko, e like me ka aspirin, e hoʻonui ai i ka pilikia o ke kahe ʻana o ke koko, hiki i kāu kauka ke noi iā ʻoe e hoʻōki i ka lawe ʻana iā lākou.
  • Ka hoʻoili ʻana o nā platelet: Inā koʻikoʻi loa kou kahe ʻana o ke koko a haʻahaʻa loa kou helu platelet, hiki ke hāʻawi ʻia iā ʻoe nā platelet mai ka hāʻawi ʻana a kekahi. Eia nō naʻe, he hopena manawa pōkole kēia.
  • Splenectomy: ʻO ka spleen kahi ʻāpana o ke kino e wehe ai i nā hunaola koko kahiko a hōʻino ʻia, a me nā platelets i hōʻailona ʻia me nā antibodies. I kekahi poʻe, inā ʻaʻole hiki i nā lāʻau lapaʻau ʻē aʻe ke kāohi i ka maʻi, wehe ʻia ka spleen ma ke ʻoki ʻana. Hiki i kēia ke kāohi nui i ke kūlana o ITP. Eia nō naʻe, ʻo ka wehe ʻana i ka spleen hiki ke hoʻonui i kou pilikia o ka loaʻa ʻana o kekahi mau maʻi.

Nā hopena ʻaoʻao o ka lāʻau lapaʻau

E like me nā lāʻau lapaʻau a i ʻole ka lāʻau lapaʻau, hiki i nā lāʻau lapaʻau ITP ke hana i kekahi mau hopena ʻaoʻao . No ka laʻana, hiki i nā corticosteroids ke hoʻonui i ke kaumaha, ka pehu ʻana o ka maka, ka hiamoe ʻole, a me nā loli o ke ʻano. E wehewehe kāu kauka i kēia mau mea a me ko lākou ʻano iā ʻoe. Ma kēia ala, hiki iā ʻoe ke ʻike iā lākou ma mua a kamaʻilio e pili ana iā lākou inā he mau hopohopo kāu.

He aha ka manaʻo no ka ITP?

ʻOkoʻa ka nānā ʻana/prognosis mai kēlā kanaka a kēia kanaka, ma muli o ke ʻano o ITP.

  • No nā keikiInā ulu ka ITP koʻikoʻi, e ho'ōla loa ka hapa nui o ka poʻe me ka ʻole o ka lāʻau lapaʻau i loko o kekahi mau pule a mau mahina paha.
  • Inā loaʻa i nā pākeke ka ITP mau loa, hiki ke lilo i maʻi no ke ola holoʻokoʻa. Akā, ʻaʻohe pono e hopohopo. Hiki i ka hapa nui o ka poʻe ke hoʻokele maikaʻi i kā lākou mau hōʻailona me ka lāʻau lapaʻau a me nā lāʻau lapaʻau ʻē aʻe a ola i kahi ola maʻamau. ʻOiai ʻaʻole hiki i nā kauka ke ho'ōla piha i ka ITP, nui ka poʻe me ka ITP mau loa e ola maikaʻi me ke ʻano no nā makahiki he ʻumi.

Pehea wau e mālama ai iaʻu iho?

Inā loaʻa iā ʻoe ka ITP, pono paha ʻoe e lawe i ka lāʻau lapaʻau no ke koena o kou ola e hōʻoia i ka hana ʻana o kou kino i nā platelets lawa. Pono nō hoʻi ʻoe e pale i nā hana a me nā ʻano e hoʻoweliweli iā ʻoe i ka ʻeha a me ke kahe ʻana o ke koko. E noʻonoʻo e pili ana i ia mea, ʻoiai he hāʻule liʻiliʻi hiki ke lilo i pilikia nui, ʻeā? No laila e makaʻala i kēia mau mea:

  • E noho mamao aku mai nā haʻuki pili e pili ana i ke kuʻi ʻana, ka hāʻule ʻana, a me ka pili kino ikaika , e like me ka pôpeku, ka rugby, ka mokomoko, karate, ka basketball, a me ka hockey hau, i ka hiki.
  • Inā loaʻa i kāu keiki ka ITP, e hōʻoia e ʻaʻahu lākou i nā mea pale e like me ka mahiole, nā pale kuli, a me nā pale kuʻekuʻe i ka wā e komo ai lākou i kekahi hana, e like me ke kaʻa paikikala, ka holo papa, a i ʻole ka heʻe ʻana i ka wili.
  • I ka wā e holo ana i loko o ke kaʻa a i ʻole ka van, e kau mau i ke kāʻei noho , a mai poina e hoʻopaʻa pono i ke kāʻei noho o kāu keiki a kau paha iā ia i loko o ka noho kaʻa.
  • Inā ʻoe e lawe ana i nā lāʻau lapaʻau a i ʻole nā ​​​​mea hoʻohui lāʻau lapaʻau, e kamaʻilio me kāu kauka e pili ana iā lākou a loaʻa kā lākou ʻae . Hiki i kekahi mau lāʻau ʻeha, e like me ka aspirin a me ka ibuprofen, a me kekahi mau lāʻau lapaʻau lāʻau, ke hoʻonui i ka pilikia o ke kahe ʻana o ke koko.

Āhea wau e ʻike ai i ke kauka?

Inā ua ʻike ʻia ʻoe me ITP a ke loaʻa nei ka lāʻau lapaʻau, e nānā mau kāu kauka iā ʻoe. Eia naʻe, i kēia manawa:

  • Inā ʻike ʻoe i nā palapū hou ,
  • Inā he mau kiko ʻulaʻula liʻiliʻi kou (`petechiae`) ma kou ʻili,
  • Inā manaʻo ʻoe e kahe ana ke koko maʻalahi ma mua o ka maʻamau,

ʻO ke ʻano kēia e ʻoi aku ka ʻino o kou kūlana, a i ʻole e haʻahaʻa paha kāu helu platelet. I kēlā hihia, e ʻike koke i kāu kauka. Hiki iā ia ke nānā hou i kāu mau pae platelet a hoʻoponopono i kāu lāʻau lapaʻau inā pono.

Āhea wau e hele ai i ka ʻOihana Pōpilikia (ETU) ?

He mea kākaʻikahi loa kēia, akā i kekahi manawa hiki i ka ITP ke hoʻohaʻahaʻa i ka helu o kāu platelet a hoʻomaka ʻoe e kahe koko me ke kāohi ʻole. No ka laʻana, inā he kahe koko kou ihu ʻaʻole e pau, he waha kahe koko, he kahe koko nui i ka wā o ka menstruation, a i ʻole kahi ʻeha ʻaʻole e pau ke kahe koko ʻoiai ʻoe e ʻomi iā ia, he pilikia olakino ia.I ia hihia, pono ʻoe e hele koke i ka lumi pilikia o ka haukapila kokoke loa. Eia kekahi, inā paʻi ʻoe i kou poʻo, a inā he mau hōʻailona o ke kahe ʻana o ke koko i loko o ka lolo, e like me ka ʻeha poʻo nui, ka luaʻi ʻana, a i ʻole nā ​​​​loli o ka ʻike, e hele koke i ka haukapila.

He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?

Ke ʻike ʻoe he ITP kou, nui paha kāu mau nīnau. Mai makaʻu a hilahila paha e nīnau i kāu kauka e pili ana iā lākou āpau. Eia kekahi mau nīnau hiki iā ʻoe ke nīnau:

  • He aha ke ʻano o ka ITP iaʻu? (ʻAki, maʻi mau, mua, lua?)
  • He aha ka lāʻau lapaʻau āu e ʻōlelo mai ai noʻu? No ke aha mai?
  • Pehea ka lōʻihi e hiki ai i kēlā mau lāʻau ke hoʻōla/hopena?
  • Pono anei au e lawe i kēia lāʻau lapaʻau i kēlā me kēia lā?
  • Inā ʻaʻole holomua ka lāʻau lapaʻau mua, he aha ka mea e hiki mai ana?
  • He aha nā hopena ʻaoʻao o kēia mau lāʻau lapaʻau? He aha kaʻu e hana ai inā loaʻa lākou?
  • He aha nā hoʻololi e pono iaʻu e hana i kaʻu meaʻai a me ke ʻano o ka nohona?
  • He aha nā hoʻoikaika kino maikaʻi iaʻu e hana ai? He aha nā hoʻoikaika kino maikaʻi ʻole iaʻu e hana ai?

He aha ka mea e hana ai inā hāpai au i ka wā e loaʻa ana iaʻu ka ITP?

Inā hāpai ʻoe a i ʻole e hoʻolālā ana e hāpai, hiki ke hopohopo loa ka ʻike ʻana ua loaʻa iā ʻoe ka ITP. Akā hiki iā ʻoe ke hōʻoluʻolu i ka ʻike ʻana i kēia: ʻAʻole maʻamau ka hopena pololei o ka ITP i kāu pēpē i hānau ʻole ʻia.

Hiki ke haʻahaʻa iki ka helu platelet o ka pēpē i ka wā e hānau ʻia ai, akā he manawa pōkole wale nō kēia a e piʻi aʻe i loko o kekahi mau lā. E nānā nā kauka i nā pae platelet o ka pēpē.

Inā loaʻa iā ʻoe ka ITP ʻoluʻolu i ka wā hāpai, a ʻaʻole koʻikoʻi kāu mau hōʻailona, ​​ʻaʻole paha ʻoe e pono i kekahi lāʻau lapaʻau. Eia nō naʻe, inā haʻahaʻa loa kāu helu platelet a i ʻole ʻoe i ka pilikia o ke kahe ʻana o ke koko, pono paha ʻoe i ka lāʻau lapaʻau. I kēlā mau hihia, e hana pū kāu kauka hānau keiki a me ka hematologist e koho i ka lāʻau lapaʻau palekana loa nou a me kāu pēpē . E mālama pono pū lākou i ka wā hānau.

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

ʻAe, i kēia manawa ua maopopo iā ʻoe ka mea a mākou i kamaʻilio ai, ʻo ITP (Immune Thrombocytopenia). Eia kekahi mau mea nui e hoʻomanaʻo ai:

  • ʻO ka ITP kahi kūlana kahi e hoʻopau ai kāu ʻōnaehana pale i kāu mau platelets ponoʻī, e hoʻemi ana i ke koko.
  • Hiki i nā hōʻailona ke komo pū me ka ʻeha maʻalahi, nā kiko ʻulaʻula ma ka ʻili, a me ke kahe pinepine ʻana o ke koko.
  • Ke hana ʻia kēia i nā keiki, e hoʻomaikaʻi pinepine ia me ka hala ʻana o ka manawa. Pono paha nā pākeke i ka lāʻau lapaʻau lōʻihi.
  • ʻOiai ʻaʻole hiki ke ho'ōla loa ʻia ka ITP, me ka mālama maikaʻi ʻana, hiki ke kaohi ʻia nā hōʻailona a hiki ke hoʻokō ʻia ke ʻano o ke ola.
  • Inā loaʻa iā ʻoe kēia mau hōʻailona, ​​mai kānalua e ʻike i ke kauka. E hāʻawi ʻo ia iā ʻoe i nā ʻōlelo aʻoaʻo a me nā lāʻau lapaʻau e pono ai.
  • E pale iā ʻoe iho mai nā ʻeha, e hahai i nā ʻōlelo aʻoaʻo a ke kauka, a e lawe i kāu mau lāʻau lapaʻau e like me ke kauoha.

Hiki i ka ITP ke lilo i mea weliweli, ʻoiai ke kahe wale nei ke koko. Akā, ʻaʻole ʻoe hoʻokahi. Aia nā kauka e hiki ke kōkua iā ʻoe a mālama iā ʻoe. No laila, e kū i kēia kūlana me ka wiwo ʻole. Inā he mau hopohopo kāu, e kamaʻilio me kāu kauka.


ITP , Immune Thrombocytopenia, platelets, coagulation koko, kahe koko, ʻōnaehana pale, bruising, petechiae, purpura

Frequently Asked Questions (FAQ)

He aha nā hoʻokolohua i hoʻohana ʻia e ʻike ai i ka ITP?

Hana pinepine nā kauka i kēia mau hoʻokolohua:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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E ʻoluʻolu e helu: 1 + 4 =
Ke kahe nui nei hoʻi ʻoe i ke koko mai kahi ʻeha liʻiliʻi? E nānā kākou i ka ITP (Immune Thrombocytopenia)!

Ke kahe nui nei hoʻi ʻoe i ke koko mai kahi ʻeha liʻiliʻi? E nānā kākou i ka ITP (Immune Thrombocytopenia)!

Ke noʻonoʻo nei paha ʻoe i kekahi manawa no ke aha e lilo ai kahi ʻeha liʻiliʻi i ʻeha nui, a no ke aha e pau ʻole ai ke kahe ʻana o ke koko i kahi ʻoki liʻiliʻi? A i ʻole ke ʻike nei ʻoe i nā mea e like me ke kahe ʻana o ka ihu me ke kumu ʻole, a i ʻole ke kahe ʻana o nā ʻāʻī i ka wā e palaki ai i kou mau niho? Inā hana pinepine ʻia kēia mau mea iā ʻoe, he mea nui paha iā ʻoe ke ʻike i ke kūlana a mākou e kamaʻilio nei i kēia lā i kapa ʻia ʻo ITP (Immune Thrombocytopenia). Mai hopohopo, e kamaʻilio maʻalahi kākou e pili ana i kēia.

He aha ka ITP (Immune Thrombocytopenia)?

I ka ʻōlelo maʻalahi, ʻo ITP (Immune Thrombocytopenia) kahi kūlana i loaʻa ai i kou koko kahi helu haʻahaʻa o nā ʻāpana liʻiliʻi i kapa ʻia he platelets . ʻO kēia mau platelets ka mea e kōkua ai i ka hoʻōki ʻana i ke kahe ʻana ke loaʻa iā mākou kahi ʻeha ma kekahi wahi o ko mākou kino. Hoʻokumu lākou i kahi clot a hoʻōki i ke kahe ʻana . No laila, i ka wā e emi ai ka helu o kēia mau platelets, ʻaʻole e maʻalahi ke kāpili ʻana o kou koko. ʻO ia ke kumu hiki i kahi ʻeha liʻiliʻi ke hoʻoulu i ke kahe nui ʻana, a i ʻole hiki iā ʻoe ke ʻeha wale i kou kino.

Ua kapa ʻia kēia ʻo ITP, a ʻo ka huaʻōlelo 'Immune' ke ʻano o kahi mea e pili ana i ka ʻōnaehana pale. ʻO 'Thrombocytopenia' ke ʻano o nā platelets haʻahaʻa. No laila, ʻo ka mea e hana ʻia ma kēia, ʻo kāu ʻōnaehana pale ponoʻī, nā koa e pale iā mākou mai ka maʻi, manaʻo kuhihewa he ʻenemi waho kāu mau cell platelet ponoʻī a hoʻouka a luku iā lākou. Ua like ia me ka hoʻouka ʻana i kekahi i loko o kou hale ponoʻī, me ka manaʻo he ʻaihue lākou.

I kekahi manawa hiki ke mālama ʻia ka ITP me ka lāʻau lapaʻau a i ʻole me ka ʻole o ka lāʻau lapaʻau a lilo i mea maikaʻi i ka hala ʻana o ka manawa. Akā no kekahi poʻe, hiki ke lilo i maʻi mau loa . ʻO ke ʻano kēia, ʻoiai hiki ke kāohi ʻia nā hōʻailona, ​​​​​​he paʻakikī ke ho'ōla loa. I kēlā poʻe, pono paha ka lāʻau lapaʻau no ke koena o ko lākou ola.

He aha nā inoa ʻē aʻe no ITP?

Ke hele ʻoe i ke kauka, hoʻohana paha lākou i nā inoa ʻē aʻe ma waho aʻe o ITP. No laila he manaʻo maikaʻi e hoʻomanaʻo i kēia mau inoa pū kekahi:

  • ʻO ka Purpura Thrombocytopenic Autoimmune
  • ʻO ka Purpura Thrombocytopenic Immune
  • ʻO ka ʻōlelo ʻo `Idiopathic Thrombocytopenic Purpura` (Ua hoʻohana nui ʻia kēia inoa i ka wā ma mua, ʻo ke ʻano o `Idiopathic` ʻaʻole ʻike ʻia ke kumu pololei)
  • ʻO ka maʻi Werlhof
  • ʻO ka Thrombocytopenia Autoimmune

ʻOiai ke ʻano o ka inoa āu e hāʻawi ai, pili pinepine ia i ke ʻano olakino like.

Pehea ka maʻamau o ka ITP?

ʻOiaʻiʻo, he maʻi laha ʻole ka ITP. ʻAʻole ia he maʻi e pili ana i nā kānaka a pau. Ma ke ʻano helu, ma kahi ʻāina e like me ʻAmelika, ma kahi o ʻehā o kēlā me kēia haneli tausani (4/100,000) mau keiki a ʻekolu o kēlā me kēia haneli tausani (3/100,000) mau mākua i ʻike hou ʻia me kēia maʻi i kēlā me kēia makahiki. ʻIke ʻia kēia maʻi ma Sri Lanka, akā he mea paʻakikī iki ka loaʻa ʻana o nā helu kikoʻī e pili ana iā ia. Akā, inā loaʻa i kekahi kēia maʻi, hiki ke lilo i pilikia nui no lākou, ʻeā?

Aia kekahi mau ʻano o ka ITP?

ʻAe, hiki ke hoʻokaʻawale ʻia ka ITP i ʻelua mau ʻano nui:

1. ITP mua:ʻO kēia ka manawa e hoʻouka ai kāu ʻōnaehana pale ponoʻī i kāu mau platelets me ke kumu ʻole. Ma kahi o 80 pakeneka (80%) o nā maʻi ITP i loaʻa i kēia ʻano. He "maʻi autoimmune" ia, ʻo ia hoʻi, ua hana ʻia e ka hana hewa ʻana o ka ʻōnaehana pale.

2. ITP lua: Hana ʻia kēia i ka wā e emi ai ka helu platelet ma ke ʻano he hopena ʻaoʻao o kekahi maʻi lapaʻau ʻē aʻe, ka maʻi, a i ʻole ka lāʻau lapaʻau. Eia kekahi laʻana:

  • ʻO kekahi mau maʻi lōʻihi, e like me ka HIV, Hepatitis C, a i ʻole H. pylori (kahi bacteria e hoʻoulu ai i nā ʻōpū ʻōpū)
  • Nā maʻi ʻaʻai koko
  • Nā 'maʻi autoimmune' ʻē aʻe (e.g. lupus - SLE)
  • Hiki paha ke kumu o kekahi mau lāʻau lapaʻau.

Hoʻokaʻawale pū nā kauka i ka ITP ma muli o ka lōʻihi o kona noho ʻana:

  • ITP ʻoi: E hoʻomaikaʻi pinepine kēia i loko o ʻekolu mahina. ʻO ia ka mea maʻamau i nā keiki.
  • ITP mau loa: Hiki i kēia ke mau mai ʻekolu mahina a i ʻumikūmālua mahina (hoʻokahi makahiki).
  • ITP Mau Loa: ʻOi aku kēia ma mua o hoʻokahi makahiki. ʻO ka mea maʻamau ia i nā pākeke.

He aha nā hōʻailona o ka ITP?

Loaʻa paha i kekahi poʻe ka ITP me ka ʻole o nā hōʻailona. Eia nō naʻe, inā loaʻa nā hōʻailona, ​​hiki ke hele mālie a koke paha. ʻO nā hōʻailona nui:

  • Petechiae: ʻO kēia ka wā e ʻike ai ʻoe i nā kiko ʻulaʻula liʻiliʻi a poni paha ma kou ʻili, ʻoi aku hoʻi ma nā wāwae haʻahaʻa. Ua like lākou me ka ʻulaʻula. ʻAʻole e nalo wale kēia mau mea.
  • Purpura: Hoʻohui ʻia nā petechiae i ʻōlelo ʻia ma mua e hana i nā kiko ʻulaʻula, poni, a ʻeleʻele paha. He ʻuʻuku kēia ma mua o kahi palapū, akā ʻoi aku ka nui ma mua o kēlā mau kiko. Hoʻokumu ʻia kēia e kahi liʻiliʻi o ke koko e kahe ana mai nā kīʻaha koko liʻiliʻi ma lalo o ka ʻili.
  • ʻO nā palapū maʻalahi: ʻOiai kahi puʻupuʻu liʻiliʻi ma kekahi wahi hiki ke hana i kahi palapū nui a palapū paha. I kekahi manawa, hiki ke ʻike ʻia nā palapū me ke kumu ʻole.
  • ʻĀʻī koko: Hiki ke koko kou ʻāʻī ke palaki ʻoe i kou mau niho a i ʻole ke kū mālie ʻoe. Hiki ke ʻike ʻia kou ʻāʻī ua pehu.
  • Koko i loko o ka ʻōpala: Inā ʻeleʻele loa ke ʻano o kou ʻōpala, e like me ke kēpau, he koko kūloko paha ia.
  • Koko i loko o ka mimi: Inā he ʻulaʻula a ʻulaʻula paha ka wai i loko o ke pola lua i kou mimi ʻana, aia paha no ka mea he koko i loko o ka mimi.
  • Nā wā menstruation kaumaha i nā wahine: Inā ʻoi aku ka lōʻihi o kou wā mahina ma mua o ʻehiku mau lā, a inā ʻoi aku kou kahe ʻana o ke koko ma mua o ka maʻamau ('Menorrhagia`), hiki i kēlā ke hōʻailona o ITP.
  • Ka kahe pinepine ʻana o ke koko ihu.
  • ʻEha nui (Hematoma): I kekahi manawa hiki ke hana ʻia kahi ʻeha nui a pehu (`Hematoma`) ke hōʻiliʻili ka nui o ke koko ma kahi hoʻokahi.
  • Manaʻo luhi loa (Fatigue).

Mea nui: Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​he mea nui loa e ʻike koke i ke kauka no ka ʻōlelo aʻo.

He aha nā kumu o ka ITP?

E like me kā mākou i kūkākūkā ai ma mua, hana ʻia ka ITP ke hana hewa kāu ʻōnaehana pale i nā antibodies e kūʻē i kāu mau platelets ponoʻī, a laila e haʻi aku i nā cell immune ʻē aʻe e luku iā lākou. Ke hōʻino ʻia kahi kīʻaha koko i loko o kou kino, ʻo nā platelets ka poʻe e hele mai i kahi, e pili pū ana, e hana i kahi clot koko, a hoʻōki i ke kahe ʻana o ke koko. Ua kapa ʻia kēia he "hemostasis mua".

Eia nō naʻe, ʻaʻole maopopo i nā loea ke kumu e hoʻomaka ai kēia ʻōnaehana pale e hoʻouka i kāna mau platelets ponoʻī.

Eia nō naʻe, ua ʻike ʻia kekahi mau noiʻi:

  • No ka poʻe i loaʻa i ka `(HIV)` (Human Immunodeficiency Virus)
  • No nā poʻe me ka maʻi bacteria i kapa ʻia ʻo `(H. pylori)` (Helicobacter pylori) (pili pinepine kēia i nā ʻōpū ʻōpū a me ka gastritis)
  • No nā kānaka me ka maʻi akepaʻa i kapa ʻia ʻo `(Hepatitis C)`

Aia kahi pilikia nui o ka hoʻomohala ʻana i ka ITP. Hiki i kēia ke alakaʻi i ka ITP lua.

Pehea e ʻike ʻia ai ka ITP?

Ma mua o ka hiki ʻana i ke kauka ke hoʻoholo inā loaʻa iā ʻoe ka ITP, e hana mua lākou i kahi hoʻokolokolo kino piha e nānā i nā hōʻailona o ke kahe koko, ka palapū, a me nā kiko e like me ka petechiae a me ka purpura. A laila e nīnau lākou e pili ana i kou mōʻaukala olakino i hala, nā lāʻau lapaʻau āu e lawe nei, a inā paha ua loaʻa i kekahi o kou ʻohana nā pilikia kahe koko.

Ma muli o ka like o nā hōʻailona o ITP me nā maʻi koko ʻē aʻe a i ʻole nā ​​​​maʻi ʻoi aku ka koʻikoʻi e like me ke kanesa koko, e kāpae ke kauka i nā kumu ʻē aʻe a pau (kahi hōʻailona o ka hoʻokaʻawale ʻana) ma mua o ka hana ʻana i ka hōʻoia paʻa o ITP.

He aha nā hoʻokolohua i hoʻohana ʻia e ʻike ai i ka ITP?

Hana pinepine nā kauka i kēia mau hoʻokolohua:

  • Helu Koko Piha (CBC): Nānā kēia i ka helu o nā ʻano ʻano cell like ʻole i loko o kou koko, me nā cell ʻulaʻula, nā cell keʻokeʻo, a me nā platelets . I ka ITP, haʻahaʻa loa paha kēia mau platelets.
  • ʻO ka Smear Koko Peripheral: Ma kēia hoʻokolohua, lawe ʻia kahi kulu koko, hohola ʻia ma luna o kahi slide aniani, a nānā ʻia ma lalo o kahi microscope e ʻike inā he maʻamau ke ʻano a me ka nui o nā platelets, a inā he mau mea ʻē aʻe.

Inā manaʻo kāu kauka ua pilikia ʻoe no ka maʻi HIV, Hepatitis C, a i ʻole H. pylori, hiki iā lākou ke hana i nā hoʻokolohua no kēlā mau maʻi. I kekahi manawa hiki ke hana ʻia kahi biopsy iwi, akā ʻaʻole hana ʻia kēia no nā mea āpau.

He aha nā lāʻau lapaʻau no ITP?

ʻO ka hapa nui o ka manawa,Ke loaʻa i nā keiki ka ITP, inā ʻaʻole koʻikoʻi nā hōʻailona, ​​e hoʻomaikaʻi lākou me ka ʻole o ka lāʻau lapaʻau. Eia nō naʻe, pono pinepine ka lāʻau lapaʻau i nā pākeke, ʻoiai inā haʻahaʻa loa ka helu o ko lākou platelet a inā paha he pilikia o ke kahe ʻana o ke koko.

Inā makemake ʻoe i ka lāʻau lapaʻau, hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e hoʻonui i kāu helu platelet a i ʻole e hoʻōki i kāu ʻōnaehana pale mai ka hoʻouka ʻana i kāu mau platelet. ʻO nā ʻano lāʻau lapaʻau nui i hoʻohana ʻia:

  • ʻO Corticosteroids: (e.g. Prednisolone). Hana kēia ma ka hoʻōki ʻana i ka hana ʻana o nā antibodies e luku ai i nā platelets. He lāʻau lapaʻau laina mua kēia.
  • Immunoglobulin (IVIg): He lāʻau lapaʻau kēia i hāʻawi ʻia ma ke kino. Hoʻololi pū ia i ka hana o ka ʻōnaehana pale a hōʻemi i ka luku ʻia ʻana o nā platelets.
  • ʻO nā agonists receptor Thrombopoietin (TPO-RAs): Kōkua kēia mau lāʻau i ke kino e hana i nā platelets hou aku.
  • Nā lāʻau pale kino: (e.g. Rituximab, Mycophenolate). Hoʻemi kēia i ka hana o ka ʻōnaehana pale kino a hoʻōki i ka luku ʻia ʻana o nā platelets.

Ma waho aʻe o kēia mau lāʻau lapaʻau, hiki i ke kauka ke ʻōlelo i nā hana ʻē aʻe:

  • Ke mālama ʻana i kahi maʻi kumu: I nā hihia o ka ITP lua, hiki ke hoʻi ka helu platelet i ka maʻamau ke mālama ʻia ka maʻi i hoʻokumu ai.
  • Ke hoʻōki nei i kekahi mau lāʻau lapaʻau: Inā ʻoe e lawe ana i kekahi mau mea hoʻokahe koko, e like me ka aspirin, e hoʻonui ai i ka pilikia o ke kahe ʻana o ke koko, hiki i kāu kauka ke noi iā ʻoe e hoʻōki i ka lawe ʻana iā lākou.
  • Ka hoʻoili ʻana o nā platelet: Inā koʻikoʻi loa kou kahe ʻana o ke koko a haʻahaʻa loa kou helu platelet, hiki ke hāʻawi ʻia iā ʻoe nā platelet mai ka hāʻawi ʻana a kekahi. Eia nō naʻe, he hopena manawa pōkole kēia.
  • Splenectomy: ʻO ka spleen kahi ʻāpana o ke kino e wehe ai i nā hunaola koko kahiko a hōʻino ʻia, a me nā platelets i hōʻailona ʻia me nā antibodies. I kekahi poʻe, inā ʻaʻole hiki i nā lāʻau lapaʻau ʻē aʻe ke kāohi i ka maʻi, wehe ʻia ka spleen ma ke ʻoki ʻana. Hiki i kēia ke kāohi nui i ke kūlana o ITP. Eia nō naʻe, ʻo ka wehe ʻana i ka spleen hiki ke hoʻonui i kou pilikia o ka loaʻa ʻana o kekahi mau maʻi.

Nā hopena ʻaoʻao o ka lāʻau lapaʻau

E like me nā lāʻau lapaʻau a i ʻole ka lāʻau lapaʻau, hiki i nā lāʻau lapaʻau ITP ke hana i kekahi mau hopena ʻaoʻao . No ka laʻana, hiki i nā corticosteroids ke hoʻonui i ke kaumaha, ka pehu ʻana o ka maka, ka hiamoe ʻole, a me nā loli o ke ʻano. E wehewehe kāu kauka i kēia mau mea a me ko lākou ʻano iā ʻoe. Ma kēia ala, hiki iā ʻoe ke ʻike iā lākou ma mua a kamaʻilio e pili ana iā lākou inā he mau hopohopo kāu.

He aha ka manaʻo no ka ITP?

ʻOkoʻa ka nānā ʻana/prognosis mai kēlā kanaka a kēia kanaka, ma muli o ke ʻano o ITP.

  • No nā keikiInā ulu ka ITP koʻikoʻi, e ho'ōla loa ka hapa nui o ka poʻe me ka ʻole o ka lāʻau lapaʻau i loko o kekahi mau pule a mau mahina paha.
  • Inā loaʻa i nā pākeke ka ITP mau loa, hiki ke lilo i maʻi no ke ola holoʻokoʻa. Akā, ʻaʻohe pono e hopohopo. Hiki i ka hapa nui o ka poʻe ke hoʻokele maikaʻi i kā lākou mau hōʻailona me ka lāʻau lapaʻau a me nā lāʻau lapaʻau ʻē aʻe a ola i kahi ola maʻamau. ʻOiai ʻaʻole hiki i nā kauka ke ho'ōla piha i ka ITP, nui ka poʻe me ka ITP mau loa e ola maikaʻi me ke ʻano no nā makahiki he ʻumi.

Pehea wau e mālama ai iaʻu iho?

Inā loaʻa iā ʻoe ka ITP, pono paha ʻoe e lawe i ka lāʻau lapaʻau no ke koena o kou ola e hōʻoia i ka hana ʻana o kou kino i nā platelets lawa. Pono nō hoʻi ʻoe e pale i nā hana a me nā ʻano e hoʻoweliweli iā ʻoe i ka ʻeha a me ke kahe ʻana o ke koko. E noʻonoʻo e pili ana i ia mea, ʻoiai he hāʻule liʻiliʻi hiki ke lilo i pilikia nui, ʻeā? No laila e makaʻala i kēia mau mea:

  • E noho mamao aku mai nā haʻuki pili e pili ana i ke kuʻi ʻana, ka hāʻule ʻana, a me ka pili kino ikaika , e like me ka pôpeku, ka rugby, ka mokomoko, karate, ka basketball, a me ka hockey hau, i ka hiki.
  • Inā loaʻa i kāu keiki ka ITP, e hōʻoia e ʻaʻahu lākou i nā mea pale e like me ka mahiole, nā pale kuli, a me nā pale kuʻekuʻe i ka wā e komo ai lākou i kekahi hana, e like me ke kaʻa paikikala, ka holo papa, a i ʻole ka heʻe ʻana i ka wili.
  • I ka wā e holo ana i loko o ke kaʻa a i ʻole ka van, e kau mau i ke kāʻei noho , a mai poina e hoʻopaʻa pono i ke kāʻei noho o kāu keiki a kau paha iā ia i loko o ka noho kaʻa.
  • Inā ʻoe e lawe ana i nā lāʻau lapaʻau a i ʻole nā ​​​​mea hoʻohui lāʻau lapaʻau, e kamaʻilio me kāu kauka e pili ana iā lākou a loaʻa kā lākou ʻae . Hiki i kekahi mau lāʻau ʻeha, e like me ka aspirin a me ka ibuprofen, a me kekahi mau lāʻau lapaʻau lāʻau, ke hoʻonui i ka pilikia o ke kahe ʻana o ke koko.

Āhea wau e ʻike ai i ke kauka?

Inā ua ʻike ʻia ʻoe me ITP a ke loaʻa nei ka lāʻau lapaʻau, e nānā mau kāu kauka iā ʻoe. Eia naʻe, i kēia manawa:

  • Inā ʻike ʻoe i nā palapū hou ,
  • Inā he mau kiko ʻulaʻula liʻiliʻi kou (`petechiae`) ma kou ʻili,
  • Inā manaʻo ʻoe e kahe ana ke koko maʻalahi ma mua o ka maʻamau,

ʻO ke ʻano kēia e ʻoi aku ka ʻino o kou kūlana, a i ʻole e haʻahaʻa paha kāu helu platelet. I kēlā hihia, e ʻike koke i kāu kauka. Hiki iā ia ke nānā hou i kāu mau pae platelet a hoʻoponopono i kāu lāʻau lapaʻau inā pono.

Āhea wau e hele ai i ka ʻOihana Pōpilikia (ETU) ?

He mea kākaʻikahi loa kēia, akā i kekahi manawa hiki i ka ITP ke hoʻohaʻahaʻa i ka helu o kāu platelet a hoʻomaka ʻoe e kahe koko me ke kāohi ʻole. No ka laʻana, inā he kahe koko kou ihu ʻaʻole e pau, he waha kahe koko, he kahe koko nui i ka wā o ka menstruation, a i ʻole kahi ʻeha ʻaʻole e pau ke kahe koko ʻoiai ʻoe e ʻomi iā ia, he pilikia olakino ia.I ia hihia, pono ʻoe e hele koke i ka lumi pilikia o ka haukapila kokoke loa. Eia kekahi, inā paʻi ʻoe i kou poʻo, a inā he mau hōʻailona o ke kahe ʻana o ke koko i loko o ka lolo, e like me ka ʻeha poʻo nui, ka luaʻi ʻana, a i ʻole nā ​​​​loli o ka ʻike, e hele koke i ka haukapila.

He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?

Ke ʻike ʻoe he ITP kou, nui paha kāu mau nīnau. Mai makaʻu a hilahila paha e nīnau i kāu kauka e pili ana iā lākou āpau. Eia kekahi mau nīnau hiki iā ʻoe ke nīnau:

  • He aha ke ʻano o ka ITP iaʻu? (ʻAki, maʻi mau, mua, lua?)
  • He aha ka lāʻau lapaʻau āu e ʻōlelo mai ai noʻu? No ke aha mai?
  • Pehea ka lōʻihi e hiki ai i kēlā mau lāʻau ke hoʻōla/hopena?
  • Pono anei au e lawe i kēia lāʻau lapaʻau i kēlā me kēia lā?
  • Inā ʻaʻole holomua ka lāʻau lapaʻau mua, he aha ka mea e hiki mai ana?
  • He aha nā hopena ʻaoʻao o kēia mau lāʻau lapaʻau? He aha kaʻu e hana ai inā loaʻa lākou?
  • He aha nā hoʻololi e pono iaʻu e hana i kaʻu meaʻai a me ke ʻano o ka nohona?
  • He aha nā hoʻoikaika kino maikaʻi iaʻu e hana ai? He aha nā hoʻoikaika kino maikaʻi ʻole iaʻu e hana ai?

He aha ka mea e hana ai inā hāpai au i ka wā e loaʻa ana iaʻu ka ITP?

Inā hāpai ʻoe a i ʻole e hoʻolālā ana e hāpai, hiki ke hopohopo loa ka ʻike ʻana ua loaʻa iā ʻoe ka ITP. Akā hiki iā ʻoe ke hōʻoluʻolu i ka ʻike ʻana i kēia: ʻAʻole maʻamau ka hopena pololei o ka ITP i kāu pēpē i hānau ʻole ʻia.

Hiki ke haʻahaʻa iki ka helu platelet o ka pēpē i ka wā e hānau ʻia ai, akā he manawa pōkole wale nō kēia a e piʻi aʻe i loko o kekahi mau lā. E nānā nā kauka i nā pae platelet o ka pēpē.

Inā loaʻa iā ʻoe ka ITP ʻoluʻolu i ka wā hāpai, a ʻaʻole koʻikoʻi kāu mau hōʻailona, ​​ʻaʻole paha ʻoe e pono i kekahi lāʻau lapaʻau. Eia nō naʻe, inā haʻahaʻa loa kāu helu platelet a i ʻole ʻoe i ka pilikia o ke kahe ʻana o ke koko, pono paha ʻoe i ka lāʻau lapaʻau. I kēlā mau hihia, e hana pū kāu kauka hānau keiki a me ka hematologist e koho i ka lāʻau lapaʻau palekana loa nou a me kāu pēpē . E mālama pono pū lākou i ka wā hānau.

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

ʻAe, i kēia manawa ua maopopo iā ʻoe ka mea a mākou i kamaʻilio ai, ʻo ITP (Immune Thrombocytopenia). Eia kekahi mau mea nui e hoʻomanaʻo ai:

  • ʻO ka ITP kahi kūlana kahi e hoʻopau ai kāu ʻōnaehana pale i kāu mau platelets ponoʻī, e hoʻemi ana i ke koko.
  • Hiki i nā hōʻailona ke komo pū me ka ʻeha maʻalahi, nā kiko ʻulaʻula ma ka ʻili, a me ke kahe pinepine ʻana o ke koko.
  • Ke hana ʻia kēia i nā keiki, e hoʻomaikaʻi pinepine ia me ka hala ʻana o ka manawa. Pono paha nā pākeke i ka lāʻau lapaʻau lōʻihi.
  • ʻOiai ʻaʻole hiki ke ho'ōla loa ʻia ka ITP, me ka mālama maikaʻi ʻana, hiki ke kaohi ʻia nā hōʻailona a hiki ke hoʻokō ʻia ke ʻano o ke ola.
  • Inā loaʻa iā ʻoe kēia mau hōʻailona, ​​mai kānalua e ʻike i ke kauka. E hāʻawi ʻo ia iā ʻoe i nā ʻōlelo aʻoaʻo a me nā lāʻau lapaʻau e pono ai.
  • E pale iā ʻoe iho mai nā ʻeha, e hahai i nā ʻōlelo aʻoaʻo a ke kauka, a e lawe i kāu mau lāʻau lapaʻau e like me ke kauoha.

Hiki i ka ITP ke lilo i mea weliweli, ʻoiai ke kahe wale nei ke koko. Akā, ʻaʻole ʻoe hoʻokahi. Aia nā kauka e hiki ke kōkua iā ʻoe a mālama iā ʻoe. No laila, e kū i kēia kūlana me ka wiwo ʻole. Inā he mau hopohopo kāu, e kamaʻilio me kāu kauka.


ITP , Immune Thrombocytopenia, platelets, coagulation koko, kahe koko, ʻōnaehana pale, bruising, petechiae, purpura

Frequently Asked Questions (FAQ)

He aha nā hoʻokolohua i hoʻohana ʻia e ʻike ai i ka ITP?

Hana pinepine nā kauka i kēia mau hoʻokolohua:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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