E noʻonoʻo, ua wiwi loa ʻoe, hoʻoikaika kino maikaʻi, a akahele loa i kāu mea e ʻai ai a inu ai. He 40 paha kou mau makahiki. ʻO wai ka mea e manaʻo e loaʻa i kekahi kanaka e like me ia ka maʻi puʻuwai? He mea hiki ʻole ke manaʻoʻiʻo ʻia, ʻeā? Akā, he mea maoli kēia. I kēia lā, ke kamaʻilio nei mākou e pili ana i kahi maʻi olakino ʻike ʻole ʻia, akā he mea weliweli loa. He mea kēia a ka poʻe he nui i ʻike ʻole ai, akā pono kākou a pau e ʻike.
He aha kēia maʻi cholesterol hoʻoilina? (Familial Hypercholesterolemia)
I ka ʻōlelo maʻalahi, he maʻi hoʻoilina kēia. ʻO ia hoʻi, he mea ia a mākou e hoʻoilina ai mai ko mākou mau mākua mai. ʻO ke kanaka me kēia maʻi he kiʻekiʻe loa kona mau pae o ka LDL (Low-Density Lipoprotein) cholesterol, a mākou e kapa nei he "cholesterol maikaʻi ʻole", i loko o ko lākou kino mai ka hānau ʻana mai.
ʻO ka maʻamau, ke kamaʻilio mākou e pili ana i ka cholesterol, manaʻo mākou e piʻi wale kēia i ka poʻe e ʻai ana i nā meaʻai ʻaila a momona, ʻaʻole hoʻoikaika kino, a momona hoʻi. He ʻoiaʻiʻo kēlā i kekahi ʻano. Akā i kēia kūlana i kapa ʻia ʻo Familial Hypercholesterolemia (FH) , ʻaʻohe mea pehea kou wīwī a pehea ke olakino o kou nohona, piʻi koke ka pae o ka cholesterol maikaʻi ʻole i loko o kou kino. No ka mea, ʻo ke kumu o kēia ʻaʻole kou nohona, akā he kīnā i loko o kou mau genes.
Ma muli o kēia, ʻoiai ke kanaka ʻōpio e manaʻo nei he olakino maikaʻi loa lākou, hiki koke iā ia ke loaʻa i ka hōʻeha puʻuwai a i ʻole ka hahau ʻana me ka ʻole o ka hōʻike mua ʻana .
I kekahi mau makahiki i hala aku nei, ua kaʻana like kekahi wahine he 40 ona makahiki i kāna ʻike. He wīwī loa ʻo ia a he olakino maikaʻi hoʻi. I kekahi lā, ʻoiai ʻo ia ma kahi hale ʻaina, ua manaʻo ʻo ia i ke kaumaha hiki ʻole ke hoʻomanawanui ʻia ma kona umauma a ua hou nui ʻo ia. I kona hele koke ʻana e ʻike i ke kauka, ma hope o ka ECG, ua ʻōlelo ke kauka, "Ua loaʻa iā ʻoe kahi hāʻule puʻuwai." ʻAʻole hiki iā ia ke manaʻoʻiʻo.
Ma hope mai, ua ʻike ʻia ma kahi hoʻokolohua kūikawā i kapa ʻia ʻo "Heart Catheterization" ua ālai ʻia he 90% o nā kīʻaha koko nui e hoʻolako ana i ke koko i kona puʻuwai. I loko o ʻelua pule, ua hoʻokomo ʻia ʻelima mau ʻōmole liʻiliʻi, i kapa ʻia ʻo "Stents", e mālama i kēlā mau kīʻaha koko i ka wehe. Ua ʻike hope ʻia he maʻi kona i kapa ʻia ʻo Familial Hypercholesterolemia (FH).
Aia pū kekahi i ka pilikia o kā kākou mau keiki?
ʻO kēia ka mea nui loa e pono ai kākou e kālele aku. ʻOiai he maʻi hoʻoilina ka FH, inā loaʻa i kekahi o nā mākua ka maʻi, aia he 50% ka manawa e hoʻoilina ai nā keiki . ʻO ke ʻano kēia, inā he ʻelua keiki, aia kahi manawa kiʻekiʻe e loaʻa ai i kekahi o lākou ka maʻi.
ʻO ka pōʻino o kēia, no ka mea, ʻaʻole ʻike ʻia nā hōʻailona, ʻaʻole paha mākou e ʻike he maʻi kēia i ke keiki. Akā, i loko o ke kino o kēlā keiki, hoʻomaka mālie ka cholesterol maikaʻi ʻole e hōʻiliʻili i loko o nā kīʻaha koko. Ma muli o kēia, ua hoʻomaka kēlā keiki eʻOiai i ka wā ʻōpiopio, ʻo ia hoʻi, i kou mau makahiki 20 a me 30, aia kahi pilikia kiʻekiʻe loa o ka loaʻa ʻana o ka hōʻeha puʻuwai a i ʻole ka hahau ʻana.
No laila, inā ua loaʻa i kekahi o kou ʻohana nā hōʻeha puʻuwai i ka wā ʻōpiopio, a inā he moʻolelo ʻohana o ka cholesterol kiʻekiʻe, he mea nui loa ia e hoʻāʻo ʻia kāu mau keiki no ka cholesterol. Paipai pū ka American Academy of Pediatrics i nā keiki āpau ma waena o 9 a me 11 mau makahiki e hoʻāʻo ʻia ko lākou cholesterol.
I ka manawa hea e kānalua ai i ke kūlana FH
ʻAʻole nā kolesterol kiʻekiʻe a pau he FH. Akā, aia kekahi mau hōʻailona e pono e noʻonoʻo ʻia he mea kānalua loa. E wehewehe au i kēia mau mea ma kahi papa.
| Mea kānalua | Wehewehena |
|---|---|
| Nā pae cholesterol LDL kiʻekiʻe loa | Inā ʻoi aku ka nui o ka LDL o kahi pākeke ma mua o 190 mg/dL a i ʻole ʻoi aku ka nui o ka LDL o kahi keiki ma mua o 160 mg/dL (hiki ke ʻokoʻa iki kēia mau waiwai mai kēlā ʻāina a kēia ʻāina). |
| Moʻolelo ʻohana | Inā ua loaʻa i kahi lālā o ka ʻohana (kāne ma lalo o 55 mau makahiki, wahine ma lalo o 65 mau makahiki) kahi hōʻeha puʻuwai a i ʻole ka maʻi puʻuwai. |
| Nā ʻano kino (ʻaʻole i loaʻa i nā kānaka a pau) | Nā waihona momona melemele ma ka ʻili a puni nā maka (Xanthelasmas), nā puʻu momona ma nā ʻāpana ʻiʻo o nā lima, nā kuʻekuʻe lima, a i ʻole nā kuli (Tendon Xanthomas). |
ʻAʻole anei lawa ka hoʻololi wale ʻana i kou nohona?
He nīnau kēia a ka poʻe he nui e nīnau ai. "ʻAʻole anei hiki iaʻu ke hoʻohaʻahaʻa i kaʻu cholesterol inā ʻai maikaʻi wau a hoʻoikaika kino?" I nā hihia o nā pae cholesterol maʻamau, hiki i nā hoʻololi ʻana i ke ʻano o ka nohona ke hana i kahi ʻokoʻa nui.
Akā i ke ʻano o FH, ʻaʻole lawa nā hoʻololi ʻana i ke ʻano o ka nohona wale nō . No ka mea, ʻo ka pilikia he kīnā genetic i loko o ka ʻōnaehana e hana a wehe i ka cholesterol i loko o kou kino. No laila, ʻoiai he mea nui ka ʻai olakino a me ka hoʻoikaika kino, pono maoli ka lāʻau lapaʻau e kaohi i nā pae cholesterol LDL keu i loko o ke koko.
Hoʻomaʻamaʻa pinepine nā kauka i nā lāʻau hoʻohaʻahaʻa cholesterol, e like me nā statins. ʻO kēia mau lāʻau lapaʻau, i hāʻawi ʻia i nā keiki ma nā dosis haʻahaʻa, hiki ke hōʻemi nui i ko lākou pilikia o ka maʻi puʻuwai i ka wā e hiki mai ana.
Nā mea e nīnau aku ai i kāu kauka
Inā he kiʻekiʻe ko ʻoe a i ʻole kekahi o kou ʻohana i ka cholesterol, he mea nui loa e ʻike i kāu kauka a nīnau i kēia mau nīnau.
- He aha nā hoʻāʻo kolesterol e pono iaʻu e hana? (e.g. Lipid Profile)
- ʻEhia pinepine e pono ai iaʻu ke hana i kēia mau hoʻokolohua?
- Pehea e hiki ai i ka ʻai a me ka hoʻoikaika kino ke kōkua i ka kaohi ʻana i koʻu mau pae cholesterol?
- He aha koʻu pilikia o ka maʻi puʻuwai?
- He aha nā hōʻailona e pono iaʻu e hopohopo nui ai? (e laʻa me ka ʻeha o ka umauma, ka paʻakikī o ka hanu ʻana)
ʻO ka ʻike ʻana i kēia ʻike e kōkua nui i ka pale ʻana iā ʻoe iho a me kāu poʻe aloha mai nā maʻi koʻikoʻi. E hoʻomanaʻo, ʻo ka ʻike ka pale maikaʻi loa.
Leka Lawe-Home
- He maʻi hoʻoilina ka Familial Hypercholesterolemia (FH) i hoʻoili ʻia mai nā hanauna aku. Hiki i kēia ke hoʻoulu i nā pae cholesterol kiʻekiʻe loa i loko o ka poʻe wiwi a olakino.
- Inā ua loaʻa i kekahi o kou ʻohana ka maʻi puʻuwai i kona wā ʻōpiopio (nā kāne < 55, nā wahine < 65), he mea nui loa iā ʻoe a me kāu mau keiki ke nānā ʻia ko lākou cholesterol.
- I ke ʻano o FH, ʻoiai he mea nui e ola i kahi nohona olakino, pono pinepine ka lawe ʻana i nā lāʻau lapaʻau i kauoha ʻia e ke kauka e kaohi i nā pae cholesterol.
- ʻO ka ʻike mua ʻana a me ka mālama kūpono ʻana e hiki ke hōʻemi nui i ka pilikia o nā pilikia koʻikoʻi e like me ka hōʻeha puʻuwai a me ka hahau.
- Inā he mau hopohopo kāu e pili ana i kāu pae cholesterol a i ʻole ka mōʻaukala ʻohana, e kamaʻilio me kāu kauka .
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