I kekahi manawa, i ko kākou noho mālie ʻana, e ʻoni koke ana kekahi ʻiʻo i loko o ko kākou kino, ʻeā? Malia paha e hiamoe ana kākou a ala aʻe me ka ʻoni ʻana. ʻO nā mea e like me kēia ka mea maʻamau e hana ʻia i nā kānaka a pau. Akā inā hoʻomau kēia ʻoni ʻiʻo, inā e hoʻopilikia ia i nā hana o kēlā me kēia lā, hiki ke lilo i hōʻailona o kekahi maʻi. No laila i kēia lā, e kamaʻilio kākou e pili ana i ke ʻano o kēia 'Myoclonus', ke kumu o ia mea, a me ka wā e pono ai kākou e hopohopo no ia mea.
He aha ka Myoclonus?
I ka ʻōlelo maʻalahi, ʻo Myoclonus kahi ʻūlū koke, makemake ʻole ʻia, a pōkole paha o kekahi a ʻoi aku paha mau ʻiʻo. Hiki iā ia ke like me ka haʻalulu uila a mau no kahi hapa o ka kekona. Hiki iā ia ke hoʻopilikia i hoʻokahi wale nō ʻiʻo ma ka lima, ka wāwae, ka poʻohiwi, ka pūhaka, ke kua, a i ʻole ka maka, a i ʻole hiki ke hoʻopilikia i kekahi mau ʻiʻo i ka manawa hoʻokahi.
Hiki i ke kanaka olakino ke ʻike i kēia i kekahi manawa o ko lākou ola. Eia nō naʻe, i kekahi manawa, hiki iā ia ke lilo i hōʻailona o kekahi mau maʻi koʻikoʻi.
Hiki ke loaʻa ka myoclonus ma nā ʻano nui ʻelua:
- ʻO ka myoclonus maikaʻi: ʻO kēia ka manawa e ʻaelike koke ai nā ʻiʻo.
- ʻO ka myoclonus maikaʻi ʻole: He hoʻomaha koke kēia o nā ʻiʻo. I ka lāʻau lapaʻau, ua kapa ʻia hoʻi ʻo "Asterixis". Hōʻike ʻia ia e ka haʻalulu lima.
He aha nā kumu nui o ka Myoclonus?
Nui nā kumu o ka myoclonus. He mea maʻamau loa kekahi a manaʻo ʻia. Akā hiki i nā mea ʻē aʻe ke hana ʻia e nā kūlana olakino e hoʻopilikia i nā ʻōnaehana like ʻole i loko o ko mākou kino. Hoʻokaʻawale nā loea i kēia mau kumu i ʻehā mau māhele nui.
Nā kumu maʻamau, physiological (Physiological Myoclonus)
He mau ʻano myoclonus ʻino ʻole kēia i hoʻokumu ʻia e nā kaʻina hana maʻamau i loko o ko mākou kino. ʻAʻohe kumu e makaʻu ai i kēia.
- Hiccups: He ʻano Myoclonus nō hoʻi kēia. Eia nō naʻe, inā hoʻomau ia no nā lā ʻelua a ʻoi aku, ʻoi aku ka maikaʻi o ke ʻike ʻana i ke kauka.
- ʻO ka myoclonus hiamoe/Hypnic jerks: Ka lī koke ʻana o ke kino, i ka wā e hiamoe ana ʻoe a i ʻole i ka wā e ala ana ʻoe. He mea maʻamau kēia no nā poʻe he nui.
- Nā pane hoʻohoka: Ke makaʻu koke mākou a kāhāhā paha, neʻe ko mākou kino me ka hiki ʻole ke kāohi.
ʻO Myoclonus i hoʻokumu ʻia e ka maʻi epilepsy
Hiki ke loaʻa kēia mau ʻūlū ʻiʻo me kekahi mau maʻi epilepsy. He mea maʻamau kēia ʻano me ka `(myoclonic seizures)`. Hiki ke pili pū me nā kūlana e like me `(Lennox-Gastaut syndrome)` a me `(juvenile myoclonic epilepsy)`.
Ma ke ʻano he hōʻailona o kekahi maʻi ʻē aʻe (Secondary Myoclonus)
Inā kū mai ka myoclonus ma ke ʻano he hōʻailona o kahi maʻi ʻē aʻe, ua kapa ʻia ʻo 'Secondary Myoclonus'. Nui nā kumu e hiki ai ke hana i kēia. E aʻo hou kākou e pili ana i ia mea mai ka papa ma lalo nei.
| Kumu hoʻokumu | Ka wehewehe a me nā laʻana |
|---|---|
| Nā maʻi autoimmune | Nā maʻi i hoʻouka ai ka ʻōnaehana pale o ke kino i kāna mau hunaola ponoʻī. Eia kekahi laʻana: (Maʻi Celiac) . |
| Nā kūlike ʻole o nā kemika i loko o ke kino | ʻO ka maʻi puʻupaʻa a i ʻole ke akepaʻa, nā pilikia thyroid, ka nele o nā huaora a i ʻole nā mineral, a me nā kaulike ʻole electrolyte . |
| Nā ʻeha o ka lolo | Ka hōʻino ʻana i nā ʻiʻo o ka lolo ma muli o ka nele o ka oxygen (cerebral hypoxia) a i ʻole ka hahau ʻana. |
| Nā maʻi lolo degenerative | Eia kekahi laʻana: ka dementia e pili ana i (ka maʻi Alzheimer) , (ka dementia kino Lewy) , a me (ka maʻi Parkinson) . |
| Nā maʻi hoʻoilina | Nā maʻi i hoʻokumu ʻia e nā hoʻololi DNA i hiki ke hoʻoilina ʻia mai nā mākua. No ka laʻana: (maʻi Krabbe) , (maʻi Wilson) . |
| Nā maʻi | Nā maʻi viral a bacteria paha e hoʻopilikia ana i ka lolo a i ʻole ka ʻōnaehana nerve. No ka laʻana: (Herpes simplex virus) , (Lyme disease). |
| Nā ʻeha o ke aʻalolo a i ʻole ke kaula kuamoʻo | Hoʻopilikia kahi ulia i ke kamaʻilio ʻana ma waena o ka lolo a me nā ʻāpana o ke kino, e hana ana kēlā mau ʻāpana me ka manaʻo ʻole. |
| Nā lāʻau lapaʻau a me nā lāʻau lapaʻau | Hiki ke hana ʻia kēia e nā lāʻau lapaʻau i lawe ʻia me ke kauoha ʻole a ke kauka (e like me ka waiʻona, cocaine, heroin). Hiki nō hoʻi ke hana ʻia e nā lāʻau lapaʻau i kauoha ʻia e ke kauka, e like me nā anti-epileptics, antidepressants , nā lāʻau koko, a me nā antibiotics . |
| Nā mea ʻawahia a me nā mea ʻawahia | Ka ʻai ʻana i nā metala kaumaha e like me ke kēpau, manganese, mercury. Nā mea make e like me nā pesticides (e.g. methyl bromide ). |
ʻO ka Myoclonus koʻikoʻi
He maʻi hoʻoilina kēia i hoʻoili ʻia mai kēlā hanauna a i kēia hanauna. ʻAʻole ia e hōʻeha a ʻaʻole e ʻoi aku ka ʻino i ka hala ʻana o ka manawa. Eia nō naʻe, hiki i ka inu ʻana i ka waiʻona ke hoʻonui i ka ʻike ʻia o kēia mau ʻūlū ʻiʻo.
Hiki ke pale ʻia kēia kūlana?
ʻO Myoclonus kahi mea e hiki koke mai ana, me ka ʻole o ka ʻōlelo aʻo. No laila, ʻaʻole hiki ke pale ʻia nā ʻano myoclonus a mākou i kamaʻilio ai ma mua, i kapa ʻia ʻo physiological a me essential myoclonus.
Eia nō naʻe, hiki iā mākou ke kaohi i nā kūlana myoclonus i hoʻokumu ʻia e nā maʻi ʻē aʻe (lua) a me ka epilepsy (epileptic) i kekahi ʻano.
- E pale i ka hoʻohana ʻana i nā lāʻau lapaʻau: E pale i ka hoʻohana ʻana i nā lāʻau lapaʻau i kuhikuhi ʻole ʻia e ke kauka. Eia kekahi, inā ʻike ʻoe i kēia mau hōʻailona ma hope o ka lawe ʻana i kahi lāʻau lapaʻau i kuhikuhi ʻia e ke kauka, e hoʻomaopopo koke i kāu kauka. Aia lākou ma laila e kōkua iā ʻoe, ʻaʻole e hoʻohewa iā ʻoe. No laila, he mea nui no kou palekana a me ka mālama kūpono e haʻi iā lākou e pili ana i nā mea āpau āu i hoʻohana ai.
- E pale i kāu ʻōnaehana nerve: ʻO ka hoʻohana ʻana i nā lako palekana e like me nā mahiole a me nā kāʻei noho e hiki ke pale i nā ʻeha i kou lolo a me ke kaula spinal.
- E hoʻokele i nā maʻi maʻi mau loa: Inā loaʻa iā ʻoe nā maʻi maʻi e like me ka maʻi epilepsy a i ʻole ka maʻi thyroid, ʻo ka hahai pono ʻana i nā ʻōlelo a kāu kauka hiki ke kōkua i ka pale ʻana a i ʻole ka hōʻemi ʻana i ka hanana o myoclonus.
Āhea mākou e ʻike ai i ke kauka?
ʻAʻole pono ka lāʻau lapaʻau no ka spasticity maʻamau. Eia nō naʻe, inā hoʻomau kēia mau spasms ʻiʻo, ʻoiai inā hoʻopilikia lākou i kāu mau hana o kēlā me kēia lā a i ʻole ka hiamoe, pono ʻoe e ʻike i ke kauka.
E hoʻomanaʻo, ʻaʻohe pono e hopohopo e pili ana i kahi mea e like me ka ʻulaʻula maʻamau. Akā inā hoʻomau kēia mau ʻulaʻula, hiki ke lilo i hōʻailona o kahi mea koʻikoʻi, no laila he mea naʻauao ke ʻimi i ke kōkua lapaʻau.
Inā manaʻo ʻoe ua ale ʻoe i kahi mea make, e hele koke i ka Emergency Treatment Unit (ETU) o ka haukapila. Hiki iā ʻoe ke kelepona i ke National Poisons Information Centre ma ka Colombo National Hospital no ka ʻōlelo aʻoaʻo.
Nā ʻano kikoʻī ʻē aʻe o ka myoclonus
Aia kekahi mau ʻano kikoʻī ʻē aʻe o ka myoclonus, kahi e kū wale ana i kekahi mau makahiki a i ʻole ma nā ʻano kikoʻī.
ʻO ka myoclonus hiamoe hānau hou maikaʻi
He ʻano maʻi kēia e hoʻopilikia ai i nā pēpē hānau hou. Loaʻa i kēia mau pēpē nā ʻūlū koke o ko lākou mau lālā a i ʻole ke kino i ka wā e hiamoe ana lākou. ʻOiai ke ʻano like kēia me ka maʻi epilepsy i ka nānā mua ʻana, ʻaʻole hōʻike kahi electroencephalogram (EEG) i kekahi hana epileptic. ʻAʻole kēia e hōʻeha i ka pēpē a nalowale loa i ka piha ʻana o 6 mahina.
ʻO ka myoclonus pepeiao waena
ʻO kēia ka manawa e ʻūlū ai kahi ʻiʻo i kapa ʻia ʻo ka tensor tympani i loko o kou pepeiao me ke kāohi ʻole ʻia. ʻO ka maʻamau, ʻūlū kēia ʻiʻo i ka wā e kamaʻilio ai, ʻai ai, a ʻakaʻaka paha e pale i ka pepeiao o loko. Akā i kēia hihia, ʻūlū kēia ʻiʻo i ka manawa kūpono ʻole, e hana ana i kahi kani kaomi mau a i ʻole ka pahū ʻana i loko o ka pepeiao. He mea hoʻonāukiuki kēia, akā ʻaʻole weliweli. Hiki ke mālama ʻia me ke ʻoki kino a i ʻole nā ʻano hana ʻē aʻe.
ʻO ka maʻi Opsoclonus-myoclonus (OMS)
ʻO ka Opsoclonus kahi neʻe ʻana o nā ʻiʻo e kāohi ana i ke kuhikuhi o nā maka. He ʻano laha ʻole ka OMS kahi e hui pū ai ka ʻūlū ʻana o nā maka a me ka ʻūlū ʻana o nā ʻiʻo o ke kino. I kekahi manawa hana ia i ka wā e hoʻouka hewa ai kā mākou ʻōnaehana pale i kā mākou ʻōnaehana nerve ponoʻī. I nā keiki, hiki ke hana ʻia kēia pane pale e kahi ʻano maʻi ʻaʻai lolo i kapa ʻia ʻo neuroblastoma. I nā pākeke, hiki ke pili kēia ʻano me ka maʻi ʻaʻai māmā, umauma, a i ʻole ovarian.
ʻO ka myoclonus palatal
He ʻano myoclonus kēia e hoʻopilikia ai i nā ʻiʻo o ka palale palupalu i loko o ko kākou waha. Hiki i kēia ke hana i kahi leo 'kāomi' ʻano ʻē i loko o ka pepeiao. Hiki i kēia ke hoʻoilina a i ʻole he hōʻailona o kekahi ʻano hōʻino o ka lolo. Hiki ke hoʻomalu pinepine ʻia kēia ʻano me ka lāʻau lapaʻau.
Leka Lawe-Home
- He ʻūmiʻi koke ka myoclonus i nā ʻiʻo. He mea maʻamau a ʻaʻole pilikia nā mea e like me ka ʻūmiʻi ʻana a me ka hiamoe ʻana.
- Akā inā hoʻomau kēia ʻūlū ʻana o nā ʻiʻo, hana pinepine, koʻikoʻi, a hoʻopilikia paha i kou ola o kēlā me kēia lā, he hōʻailona paha ia o kahi maʻi ʻē aʻe.
- I kēlā kūlana, mai hoʻowahāwahā iā ia, a e ʻike pono i kāu kauka.
- Hoʻoholo wale ʻia ke kumu o ka lāʻau lapaʻau, hiki i kāu kauka ke hoʻoholo.
- He mea nui loa ke kamaʻilio pololei me kāu kauka e pili ana i nā lāʻau lapaʻau a i ʻole nā mea ʻē aʻe āu e lawe nei no ka ʻike pololei a me ka mālama palekana.
👩🏽⚕️ Nā nīnau hou aku (FAQs)
💬 He aha ka maʻi i kuhikuhi ʻia ai nā papa Metoprolol Tartrate / Lopressor?
ʻO kēia ka 'pila puʻuwai' holomua loa a ikaika loa, hana wikiwiki hoʻi ma ka honua (Cardioselective Beta-blocker)! ʻO 'Tartrate' ia, no laila ua komo koke ia i loko o ke kino ke lawe ʻia. Hoʻohana nā kauka iā ia e kāohi i ke 'Kikokikona Koko Kiʻekiʻe' koʻikoʻi, angina, a ʻoi aku hoʻi ma ke ʻano he lāʻau lapaʻau laina mua e hoʻopakele i ke ola o ka mea maʻi i nā manawa ma hope o ka 'Heart Attack'.
💬 Pehea e hoʻohaʻahaʻa ai kēia pila puʻuwai koke (Metoprolol Tartrate) i ke koko a me ka luhi o ka puʻuwai?
Ke loaʻa ka hōʻeha puʻuwai, e kuʻi wikiwiki ka puʻuwai ma muli o ka leka 'adrenaline (Epinephrine)' i hoʻouna ʻia mai ka lolo. I ka wā e komo ai kēia pila i loko o ke kino, hele pololei ia i ka puʻuwai e kokoke ana e make me ka ʻole o ka oxygen, a ua ālai ʻia/pani ʻia ka 100% o nā puka e hele mai ai ka adrenaline (Beta-1 Receptors), a ua laka ikaika ʻia. No ka mea, ʻaʻohe ala e hele ai ka leka, lohi wale ka puʻuwai a hoʻomaka e kuʻi i ka wā hoʻomaha. A laila emi ka ukana ma ka puʻuwai a hoʻopakele ʻia ka mea maʻi mai ka make.
💬 No ke aha i ʻōlelo ʻia ai ʻaʻole e hoʻōki koke i ka lawe ʻana i kēia lāʻau lapaʻau (Lopressor)? He aha nā pilikia (ʻŌlelo Aʻo Pahu ʻEleʻele)?
Inā ʻoe e lawe i kēia pila no nā mahina a laila 'kū koke', e wehe koke ʻia kēlā mau mea loaʻa adrenaline āpau i ālai ʻia me ka ʻole o ka mana! A laila, i loko o nā minuke, e loaʻa iā ʻoe kahi hōʻeha puʻuwai koʻikoʻi a e kū kou puʻuwai (Angina Exacerbation / Myocardial Infarction / Severe Tachycardia) he mea make loa ia a hiki iā ʻoe ke make! Eia kekahi, hiki i kēia pila ke hoʻolohi i kou puʻuwai nui a hoʻoulu i ka dizziness/nui loa ka hiamoe/insomnia/luhi.











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