Ke luhi mau nei ʻoe a make ke ola? ʻO kekahi kumu o kēia, ʻo ia ka nele o ke koko i loko o ke kino, kahi maʻi i kapa ʻia ʻo anemia ma nā ʻōlelo lapaʻau. Ke loaʻa kēia anemia ma muli o kekahi mau maʻi, pono paha ʻoe e hoʻololi pinepine i ke koko. No laila, i kēia lā e kamaʻilio mākou e pili ana i kahi lāʻau hou i hoʻolauna ʻia i ka honua e mālama i ia mau maʻi. ʻO Reblozyl ka inoa o kēlā lāʻau.
He aha ke ʻano lāʻau lapaʻau ʻo Reblozyl?
He lāʻau lapaʻau ʻo Reblozyl i ʻāpono ʻia i ka makahiki 2019. I ka pololei, no kahi papa lāʻau lapaʻau i kapa ʻia ʻo "erythroid maturation agents (EMA)". ʻAe, ʻae, he paʻakikī iki paha kēlā huaʻōlelo. I ka ʻōlelo maʻalahi, kōkua kēia lāʻau i nā hunaola koko ʻulaʻula i hana ʻia i loko o ko kākou iwi iwi e "ʻōpiopio", ʻo ia hoʻi, e lilo i mau hunaola olakino maikaʻi. Hoʻohana nui ʻia kēia lāʻau lapaʻau no ka mālama ʻana i ka anemia i hoʻokumu ʻia e kekahi mau maʻi koko. ʻOi loa aku i nā pākeke me kēia mau maʻi ʻelua: 1.
Beta-thalassemia: ʻO ka poʻe e pono e loaʻa i nā hoʻoili koko maʻamau ma muli o kēia ʻano. 2.
Myelodysplastic Syndromes (MDS): Ua ʻike ʻia kēia ʻo ka nele o ka
iwi iwi. No laila, hāʻawi ʻia ʻo Reblozyl i ka poʻe e pono e loaʻa i nā hoʻoili koko maʻamau.
E aʻo iki kākou e pili ana i ka beta-thalassemia a me MDS.
Inā maopopo iki ʻoe e pili ana i kēia mau maʻi ʻelua, e maʻalahi ka hoʻomaopopo ʻana i ke ʻano o ka hana ʻana o ka lāʻau Reblozyl.
- Beta-thalassemia: E noʻonoʻo i nā hunaola koko ʻulaʻula i loko o ko kākou koko e like me nā kaʻa e lawe ana i ka oxygen. Hoʻouka ʻia ka oxygen i loko o kēia kaʻa ma luna o kahi protein i kapa ʻia ʻo hemoglobin . ʻAʻole hana ka mea me ka beta-thalassemia i ka lawa o kēia protein hemoglobin. No laila, ʻaʻole loaʻa i nā hunaola i loko o ke kino ka oxygen a lākou e pono ai. ʻO ia ke kumu e kū mai ai nā hōʻailona e like me ka luhi mau a me ka mae .
- ʻO ka maʻi Myelodysplastic (MDS): He ʻano maʻi kanesa kēia e hoʻomaka ana ma ka iwi iwi. ʻO ka iwi iwi ka hale hana e hana ai i kā mākou mau hunaola koko (nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a me nā platelets). I loko o ke kanaka me MDS, ua hoʻopilikia ʻia ka hana ʻana o kēia hale hana. ʻO ia hoʻi, ua emi ka hana ʻana o nā hunaola koko olakino a ulu maikaʻi.
Ma kēia mau kūlana ʻelua, ʻo ka pilikia nui ka emi ʻana o ka helu o nā hunaola koko ʻulaʻula olakino a hana pono, ʻo ia hoʻiLoaʻa ka anemia .
Hana ʻo Reblozyl ma ke kōkua ʻana i nā hunaola koko ʻulaʻula ʻōpiopio e ulu pono ʻole ana e oʻo pono. Hoʻonui kēia i ka nui o nā hunaola koko ʻulaʻula olakino, hoʻonui i nā pae hemoglobin, a hoʻomaikaʻi i ka hiki o ke kino ke lawe i ka oxygen. ʻO ka hopena,
pono paha ʻoe i nā hoʻoili koko pinepine ʻole .
Akā e hoʻomanaʻo i kēia: ʻAʻole pani ʻo Reblozyl no nā hoʻoili koko. He lāʻau lapaʻau wale nō ia e kōkua ai i ka hōʻemi ʻana i ka pono.
Pehea e hāʻawi ʻia ai kēia lāʻau lapaʻau?
ʻAʻole ʻo Reblozyl kahi pila hiki iā ʻoe ke lawe ma ka home. He pana ia e hāʻawi ʻia
i kēlā me kēia 3 pule . Hāʻawi ʻia kēia pana e ke kauka a kahu maʻi paha i aʻo ʻia ma ke keʻena o kāu kauka, keʻena lapaʻau, a i ʻole ka haukapila.
- Ma hea e hāʻawi ai i ka lāʻau pale: Hāʻawi pinepine ʻia kēia lāʻau pale ma lalo o ka ʻili o ka lima, ka ʻūhā, a i ʻole ka ʻōpū, ma lalo o ka poʻohiwi.
- Ka loaʻa ʻana o ka lāʻau pale i ka manawa kūpono: He mea nui loa e hele e loaʻa ka lāʻau pale i ka lā hoʻokahi a ke kauka i hāʻawi ai iā ʻoe. Inā hala ʻoe i ka lā, e kāhea koke i ke kauka a noi i ka ʻōlelo aʻo no ka lā aʻe e hiki mai ana.
- He puke moʻolelo hōʻailona: He manaʻo maikaʻi e kākau i kāu mau hōʻailona (e like me ka luhi a me ka poniuniu ) i loko o kahi puke liʻiliʻi a i ʻole ma kāu kelepona i kēlā me kēia lā. E maʻalahi kēia i ka wehewehe ʻana i kāu kauka pehea e hoʻopilikia ai ka lāʻau lapaʻau iā ʻoe.
E hoʻoholo ʻia ka nui o ka lāʻau lapaʻau e hāʻawi ʻia iā ʻoe e kāu kauka ma muli o kou kaumaha a me ka pane a kou kino i ka lāʻau lapaʻau.
He aha nā hopena ʻaoʻao e hiki mai ana? Pehea e hana ai me lākou?
E like me nā lāʻau lapaʻau āpau, hiki iā Reblozyl ke hana i kekahi mau hopena ʻaoʻao. ʻAʻole loaʻa i nā kānaka a pau, akā he mea nui e makaʻala iā lākou. Hōʻike ka papa ma lalo nei i kekahi o nā hopena ʻaoʻao maʻamau a pehea e mālama ai iā lākou.
| Hopena ʻaoʻao | Pehea e hoʻokele ai |
|---|
| Luhi nui, poniuniu, nalowale ke kaohi o ke kino | E pale i ka hoʻokele kaʻa a i ʻole ka hoʻohana ʻana i nā mīkini kaumaha a hiki i kou ʻike pono ʻana i ke ʻano o ka hopena o kēia lāʻau lapaʻau iā ʻoe. |
| ʻEha poʻo, ʻeha ʻiʻo a hui paha | E nīnau i kāu kauka e pili ana i nā lāʻau ʻeha e hiki ke kōkua i ka hōʻoluʻolu ʻana i kēia mau hōʻailona. E haʻi i kāu kauka inā ʻaʻole e hoʻomaikaʻi a i ʻole e ʻoi aku ka ʻino o kāu mau hōʻailona. |
| Ka luaʻi, ʻeha ʻōpū, diarrhea (flatulence) | E hoʻāʻo e ʻai i nā meaʻai liʻiliʻi ma mua o nā meaʻai nui. E ʻai i nā meaʻai palalulu e like me ka berena, nā kuki, a me ka laiki. E inu i ka wai he nui. Inā ʻoi aku ka ʻino o kēia mau hōʻailona a i ʻole ʻaʻole hoʻi e hoʻomaikaʻi, e haʻi i kāu kauka. |
| Ke koko kiʻekiʻe | He mea nui e hoʻoikaika kino a lawe i kahi meaʻai olakino e like me DASH. E nānā mau i kou koko. Inā ʻoi aku ke kiʻekiʻe o kou koko ma mua o 180/120 mmHg, e hele koke i ka Emergency Department (ETU) . |
| Paʻakikī ka hanu ʻana, ka hopena allergies | E nīnau mua i kāu kauka e pili ana i nā hōʻailona o kahi maʻi ʻaleka (e laʻa, ka ʻulaʻula o ka ʻili, ka maneʻo, ka pehu ʻana o ka maka, ka pōkole o ka hanu). Inā ʻike ʻoe i kekahi o kēia mau hōʻailona, e kāhea koke aku i kāu kauka a i ʻole e hele i ka Emergency Department (ETU) kokoke loa . |
| Ka hōʻiliʻili ʻana o ka wai i loko o ke kino (edema) | Inā ʻike ʻoe i kekahi pehu ma kou mau lima, nā wāwae, a i ʻole ke kino, e haʻi i kāu kauka. Na ia e hāʻawi i ka lāʻau e pono ai. |
Hiki paha nā pilikia me nā lāʻau lapaʻau ʻē aʻe?
ʻAe. Hiki i ka lawe ʻana iā Reblozyl ke hoʻopilikia inā ʻoe e lawe i kekahi mau lāʻau lapaʻau ʻē aʻe. ʻOi aku hoʻi, inā ʻoe e lawe ana i ka lāʻau hoʻololi hormone no ka menopause a i ʻole nā lāʻau hoʻomalu hānau, hiki ke piʻi aʻe ka pilikia o nā ʻōpū koko.
No laila, e hōʻoia e haʻi aku i kāu kauka e pili ana i nā lāʻau lapaʻau āpau āu e lawe ai, me nā mea i kuhikuhi ʻia e nā kauka, nā lāʻau lapaʻau ma luna o ke kauka, nā huaora, nā lāʻau lapaʻau kuʻuna, a me nā huahana lāʻau .
Leka Lawe-Home
- He lāʻau hou ʻo Reblozyl i hāʻawi ʻia ma ke ʻano he pana e mālama ai i ka anemia i hoʻokumu ʻia e nā kūlana i kapa ʻia ʻo beta-thalassemia a me MDS.
- Kōkua nui kēia i nā hunaola koko ʻulaʻula ʻōpiopio e ulu pono.
- Hiki i kēia lāʻau lapaʻau ke hōʻemi i ka pono no ke kahe koko pinepine ʻana, akā, ʻaʻole ia he pani no ka hāʻawi koko ʻana.
- Hāʻawi ʻia kēia lāʻau pale e ke kauka a kahu maʻi paha i kēlā me kēia 3 pule.
- Hiki ke loaʻa nā hopena ʻaoʻao e like me ke poʻo ʻeha, ka luhi, a me ka ʻeha ʻiʻo. E kamaʻilio me kāu kauka e pili ana i kekahi mau hōʻailona ʻē.
- He mea nui e hoʻomaopopo i kāu kauka e pili ana i nā lāʻau lapaʻau ʻē aʻe āu e lawe nei.
ʻO Reblozyl, Anemia, Beta-Thalassemia, Myelodysplastic Syndromes, MDS, hoʻoili koko, Luspatercept, hemoglobin
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