Ua ʻike anei ʻoe i kahi puʻupuʻu liʻiliʻi a puʻupuʻu paha ma kekahi wahi o kou kino? Malia paha ʻaʻole ia e hōʻeha, a i ʻole ua pilikia paha ʻoe i nā ʻeha mau loa ma kou lima, wāwae, a i ʻole nā hono. I ka manawa pinepine, hoʻopoina mākou i kēia mau mea. Hoʻomaopopo mākou iā mākou iho, "He puʻupuʻu momona wale nō paha," a i ʻole "Ua kuʻi paha wau iaʻu iho ma kekahi wahi." Eia naʻe, i kekahi manawa ʻo kahi hōʻailona liʻiliʻi e like me kēia hiki ke lilo i hōʻailona o kahi maʻi i kapa ʻia ʻo 'Sarcoma' ( Sarcoma ), he maʻi kanesa kakaʻikahi akā koʻikoʻi e pono ai ʻoe e makaʻala. E ʻoluʻolu, mai hopohopo—e kamaʻilio pū kākou e pili ana i kēia, maʻalahi a mai ka honua aʻe, ma ʻaneʻi ma Nirogi Lanka.
I ka ʻōlelo maʻalahi, he aha ka Sarcoma?
He puʻupuʻu ʻino ka sarcoma e ulu ana i loko o nā iwi o kou kino a i ʻole nā ʻiʻo palupalu . Ke noʻonoʻo nei paha ʻoe he aha nā ʻiʻo palupalu. ʻO kēia nā ʻiʻo e kākoʻo a hoʻohui i nā ʻano like ʻole o kou kino.
ʻo kahi laʻana:
- Nā ʻiʻo
- Momona
- Nā ʻūmiʻi
- ʻO ke iwi ʻili
- Nā ligaments
- Nā kīʻaha koko
- Nā aʻalolo
ʻO kēia nā mea a mākou e kapa nei he mau ʻiʻo palupalu o kou kino, a hiki i kahi sarcoma ke ulu ma kekahi o kēia mau wahi.
He ʻano maʻi kanesa kakaikahi nā Sarcomas. He 1% wale nō o nā maʻi kanesa makua āpau lākou. Eia nō naʻe, he 15% o nā maʻi kanesa i ʻike ʻia i nā keiki lākou. No laila, he mea nui loa ka hoʻomaopopo ʻia e pili ana i kēia maʻi.
Ma hea kahi e loaʻa pinepine ai nā sarcomas?
ʻOiai hiki ke loaʻa kēia maʻi kanesa ma nā wahi āpau mai kou poʻo a i kou mau manamana wāwae, aia nā wahi maʻamau kahi e loaʻa pinepine ai lākou. E noʻonoʻo i kēia: mai kēlā me kēia 100 sarcomas i ʻike ʻia:
- Aia ka 40% ma ke kino haʻahaʻa, e like me kou mau wāwae, nā kuʻekuʻe wāwae, a me nā kapuwaʻi .
- Aia he 15% ma nā ʻaoʻao o luna, e like me kou mau poʻohiwi, nā lima, nā pulima lima, a me nā manamana lima .
- Aia ka 30% i loko o kou kino, umauma, ʻōpū, a i ʻole pelvis .
- ʻO ke koena 15% e loaʻa ana ma ka ʻāpana poʻo a me ka ʻāʻī .
He aha nā ʻano nui o nā sarcomas?
I loko o ka māhele ākea o ka sarcoma, aia ma mua o 70 mau ʻano like ʻole. Eia nō naʻe, hiki iā mākou ke hoʻohui iā lākou i ʻelua mau māhele nui: nā sarcoma iwi a me nā sarcoma ʻiʻo palupalu.
| ʻAno Sarcoma | Wehewehe Maʻalahi |
|---|---|
| Nā Sarcoma Iwi | Hoʻomaka pololei kēia mai ka ʻiʻo iwi. Ua kapa ʻia kēia mau mea ʻo 'primary bone sarcomas.' ʻOi aku ka maʻamau o lākou i nā keiki a me nā ʻōpio ma lalo o 35 mau makahiki. Eia kekahi mau laʻana:
|
| Nā Sarcomas ʻiʻo palupalu | Hoʻomaka kēia mai nā ʻiʻo palupalu e like me nā ʻiʻo a i ʻole ka momona. ʻOi aku ka maʻamau o kēia i nā pākeke ma mua o nā sarcomas iwi, ʻoiai hiki ke loaʻa kekahi mau ʻano (e like me ka rhabdomyosarcoma) i nā keiki. ʻO kekahi mau laʻana:
|
He Manaʻo Koʻikoʻi: I kekahi manawa, hiki i ka maʻi kanesa e hoʻomaka ana ma kahi ʻāpana ʻē aʻe o ke kino (e like me nā māmā, ka umauma, ka thyroid) ke laha i nā iwi. Ua kapa ʻia kēia ʻo 'metastatic bone cancer.' ʻAʻole kēia he ʻano sarcoma. He maʻi kanesa ʻē aʻe ia i laha i nā iwi.
No ke aha e kū mai ai nā sarcomas? He aha nā kumu pilikia?
E like me nā ʻano maʻi kanesa ʻē aʻe he nui, ʻaʻole maopopo loa ke kumu pololei e lilo koke ai kahi cell olakino i maʻi kanesa. I ka ʻōlelo maʻalahi, ʻo ka mutation i loko o ka DNA o nā cell e kūkulu ana i kou mau iwi a i ʻole nā ʻiʻo palupalu e hoʻoulu ai iā lākou e ulu a māhelehele me ka ʻole o ke kāohi. ʻO ka hopena o ka nui o nā cell ka mea a mākou e ʻike ai he puʻupuʻu. Inā ʻaʻole mālama ʻia, hiki i kēia mau cell cancer ke hele ma ke koko a i ʻole ka ʻōnaehana lymphatic a laha i nā ʻōpū ʻē aʻe o ke kino. Ua kapa ʻia kēia kaʻina hana he metastasis.
Eia nō naʻe, ua ʻike ʻia kekahi mau mea pilikia e hoʻonui ai i ka likelika o ka hoʻomohala ʻana i kahi sarcoma.
| Kumu Hoʻopilikia | Wehewehena |
|---|---|
| Nā Kemika | Ka lōʻihi o ka hoʻopili ʻana i ka arsenic, kekahi mau kemika i hoʻohana ʻia i ka hana plastik (vinyl chloride), nā herbicides, a me nā mea mālama lāʻau. |
| Pāhawewe | ʻO ka radiation therapy kiʻekiʻe ma mua i hoʻohana ʻia e mālama i nā ʻano maʻi ʻē aʻe. |
| ʻO ka lymphedema | ʻO ka pehu lōʻihi ma nā lima a i ʻole nā wāwae i hoʻokumu ʻia e ka hōʻiliʻili ʻana o ka wai lymph. |
| Nā Kūlana Hoʻoilina | Hiki i kekahi mau kūlana hoʻoilina i hoʻoilina ʻia (e like me, Neurofibromatosis type 1, Li-Fraumeni syndrome) ke hoʻonui i kou pilikia. |
He aha nā hōʻailona o ka sarcoma?
ʻO kēia kahi e huikau ai nā kānaka he nui. No ka mea, ʻokoʻa loa nā hōʻailona o ka sarcoma ma muli o kahi i hoʻokumu ʻia ai ka puʻupuʻu. I kekahi manawa, ʻaʻohe hōʻailona iki i nā pae mua.
Eia kekahi o nā hōʻailona maʻamau āu e ʻike ai:
- He puʻupuʻu hou: Hiki i kēia puʻupuʻu ke ʻeha a ʻeha ʻole paha. Hiki ke manaʻo ʻia he puʻupuʻu ma lalo o kou ʻili.
- ʻEha: ʻEha mau ma ka lima, ka wāwae, ka ʻōpū, a i ʻole ka ʻāpana pelvic. No kekahi poʻe, hiki ke ʻoi aku ka ʻeha i ka pō.
- Paʻakikī ke neʻe: Inā ulu kahi ʻōpū a kaomi ma luna o kahi hono a ʻiʻo paha, paʻakikī paha iā ʻoe ke kūlou a hoʻopololei paha i kou mau lālā i ke kūpono.
- Ka pohō kaumaha i wehewehe ʻole ʻia.
- ʻEha hope.
He mea maʻamau kēia mau hōʻailona i nā kūlana olakino ʻē aʻe he nui. No laila, mai makaʻu ʻoe he sarcoma maoli nō ia no ka mea he kekahi o kēia mau hōʻailona kāu. Eia nō naʻe, inā ʻike ʻoe i kahi mea e like me kēia, he mea nui e pale ʻole iā ia a e ʻike i kāu kauka no ka hoʻokolokolo ʻana.
Pehea e ʻike ai ke kauka i ka sarcoma?
Ke kipa aku ʻoe i kāu kauka, e nīnau mua lākou e pili ana i kāu mau hōʻailona a hana i kahi hoʻokolokolo kino. Inā loaʻa kahi puʻupuʻu, e nānā lākou i kona nui a me kona ʻano. Ma hope iho, hiki ke kuhikuhi ʻia ʻoe no kekahi mau hoʻokolohua e hōʻoia i ka hōʻailona.
- X-ray: He hoʻāʻo mua e nānā i nā ʻano ʻē i nā iwi a me nā ʻiʻo palupalu.
- CT scan (Computed Tomography scan): Hoʻohana i kahi kamepiula e hoʻohui i nā kiʻi X-ray e hana i nā hiʻohiʻona ʻāpana o kou kino, e hāʻawi ana i kahi kiʻi maopopo o ka puʻupuʻu.
- MRI scan (Magnetic Resonance Imaging): Hoʻohana i nā kahua magnetic a me nā nalu lekiō e hana i nā kiʻi kikoʻī a maopopo o loko o kou kino, he mea nui loa ia no ka nānā ʻana i nā puʻupuʻu palupalu.
- Biopsy: ʻO kēia ka hoʻāʻo koʻikoʻi a paʻa loa. Hōʻiliʻili ʻia kahi hāpana ʻiʻo liʻiliʻi mai ka puʻupuʻu ma o kahi ʻoki liʻiliʻi a i ʻole kahi nila kūikawā a nānā ʻia ma lalo o kahi microscope i loko o kahi keʻena hoʻokolohua. Penei ke ʻano o ka hōʻoia ʻia ʻana o ke ʻano o ka maʻi kanesa—a i ʻole ke ʻano o ka sarcoma.
Hiki ke ʻōlelo ʻia kekahi mau hoʻokolohua ʻē aʻe, e like me nā scan PET a i ʻole nā scan iwi.
He aha nā lāʻau lapaʻau no ka sarcoma?
He hana hui pū ka mālama ʻana i ka sarcoma. E hana pū kahi hui o nā loea, me nā kauka ʻokiʻoki, nā kauka oncologists, a me nā mea hoʻōla radiation, e hoʻoholo i ka hoʻolālā lapaʻau maikaʻi loa nāu.
Hoʻoholo ʻia ke ʻano o ka mālama ʻana ma muli o:
- ʻO ke ʻano o ka sarcoma.
- Ka nui a me ka wahi o ka puʻupuʻu.
- Kou kūlana olakino holoʻokoʻa.
- Inā ua pālahalaha ke kanesa i nā ʻāpana ʻē aʻe o kou kino.
Aia kekahi mau ʻano lapaʻau nui.
ʻoki kino
No ka hapa nui o nā sarcomas, ʻo ke ʻoki kino ke ʻano lapaʻau mua. ʻO ka pahuhopu ka wehe ʻana i ka puʻupuʻu holoʻokoʻa me kahi liʻiliʻi o nā ʻiʻo olakino e hoʻopuni ana iā ia e hōʻoia ʻaʻohe mau hunaola kanesa microscopic i koe. I kekahi mau hihia, hana ʻia nā ʻoki hoʻopakele lālā e hoʻopakele i kahi lālā. I nā hihia kakaikahi loa kahi hiki ʻole ke hoʻopakele ʻia ka lālā, pono paha ke ʻoki ʻia.
Hoʻōla Pāhawewe
Hoʻohana kēia i nā kukuna X-ikehu kiʻekiʻe e luku i nā hunaola kanesa. Hiki ke hāʻawi ʻia ka radiation ma mua o ke ʻoki ʻana e hoʻēmi i ka puʻupuʻu a i ʻole ma hope o ke ʻoki ʻana e pepehi i nā hunaola kanesa i koe.
Kemoterapia
Pili kēia i ka hoʻohana ʻana i nā lāʻau lapaʻau kūikawā e pepehi a hoʻōki paha i ka ulu ʻana o nā hunaola kanesa e māhele wikiwiki ana. Hiki ke hāʻawi ʻia kēia mau lāʻau lapaʻau ma ke ʻano intravenous a i ʻole he mau pila waha.
Nā Lapaʻau ʻē aʻe
Eia kekahi, ua loaʻa i kēia manawa nā lāʻau lapaʻau hou e like me Targeted Therapy , kahi e hoʻouka ai i nā nāwaliwali kikoʻī i nā hunaola kanesa, a me Immunotherapy , kahi e hoʻoikaika ai i ka ʻōnaehana pale o kou kino e hakakā i ka kanesa.
Āhea ʻoe e ʻike ai i ke kauka?
He maʻalahi ka mālama ʻana iā Sarcoma i ka wā e ʻike mua ʻia ai. No laila, mai hoʻokaʻulua—e ʻike koke i kāu kauka inā ʻike ʻoe i kēia mau mea.
Inā he puʻupuʻu hou kou ma kou kino, inā he ʻeha a ʻaʻole paha, ʻoiai inā ʻoi aku ka nui ma mua o ka pōpō kolepa (ma kahi o 5 cm) a i ʻole e hoʻomau ana i ka ulu ʻana, pono ʻoe e ʻike i ke kauka.
Eia kekahi, mai hoʻowahāwahā i ka ʻeha mau loa a wehewehe ʻole ʻia ma ka lima, ka wāwae, a i ʻole ka iwi, ʻoiai inā ua hana ʻia me ka ʻole o ka ʻeha.
ʻAʻole hoʻokahi wale nō maʻi kanesa ʻo Sarcoma, akā he hui o nā maʻi kanesa. No laila, ʻokoʻa loa nā hoʻolālā lapaʻau a me ka wānana ma muli o ke kanaka, ke ʻano, a me ke kahua o ke kanesa. Inā he mau nīnau kāu a i ʻole kekahi āu i ʻike ai e pili ana i kēia, ʻo ke ala maikaʻi loa e kūkākūkā me kahi loea.
Leka Lawe-Home
- He ʻano maʻi kanesa kakaikahi ʻo Sarcoma e kū mai ana i loko o nā iwi a me nā ʻiʻo palupalu.
- He mea nui loa e hōʻike i kekahi puʻupuʻu hou, e ulu ana, a i ʻole puʻupuʻu nui (ma luna o 5cm) i ke kauka. Mai hoʻowahāwahā iā ia, ʻoiai inā ʻaʻole ia he ʻeha.
- ʻO ka hoʻokolohua koʻikoʻi no ka ʻike pololei ʻana he biopsy.
- Hoʻopilikino ʻia nā lāʻau lapaʻau (ʻoki kino, radiation, chemotherapy) no kēlā me kēia mea maʻi a me ke ʻano o ko lākou maʻi kanesa.
- He mea nui ka ʻike mua ʻana a me ka mālama koke ʻana no nā hopena maikaʻi loa.
ʻO Sarcoma, maʻi ʻaʻai, nā puʻupuʻu kino, maʻi ʻaʻai iwi, maʻi ʻaʻai palupalu, nā hōʻailona maʻi ʻaʻai, Nirogi Lanka
