Ke luhi nei ʻoe a me ka palaualelo i nā manawa a pau? Loaʻa iā ʻoe ke kuni, nā ʻeha waha, a manaʻo ʻoe e maʻi ana ʻoe mai nā mea liʻiliʻi loa? Aia paha kekahi maʻi ma hope o kēia mau mea a mākou e kamaʻilio nui ʻole ai, akā hiki ke koʻikoʻi loa. I kēia lā e kamaʻilio mākou e pili ana i kekahi o ia mau maʻi, ʻo ia hoʻi ʻo Agranulocytosis. Mai hopohopo, e wehewehe kākou i nā mea āpau ma nā ʻōlelo maʻalahi.
He aha ka Agranulocytosis maoli?
I ka ʻōlelo maʻalahi, he emi weliweli kēia o kahi ʻano o nā hunaola koko keʻokeʻo i loko o ko kākou koko. E noʻonoʻo ua like ko kākou kino me kahi ʻāina. A laila ʻo nā huakini e hoʻoulu ai i nā maʻi i loko o ko kākou kino, ʻo ia nā ʻenemi e hoʻouka ana i ka ʻāina. ʻO ka pūʻali koa e hakakā nei i kēia mau ʻenemi, ʻo ia nā hunaola koko keʻokeʻo i loko o ko kākou koko.
ʻO kahi pūʻali koa kūikawā i loko o kēia pūʻali koa koko keʻokeʻo i kapa ʻia he granulocytes . ʻEkolu mau ʻano koa nui i loko o kēia pūʻali koa:
- Nā Neutrophils
- Nā Basophil
- Nā Eosinophils
Aia i loko o kēia mau pūnaewele nā granules liʻiliʻi, nona nā enzymes e luku ai i nā germs e like me nā bacteria e komo i loko o ke kino. Hoʻopuka ʻia kēia mau pūnaewele koʻikoʻi loa i loko o ko kākou iwi iwi.
No laila, ʻo ka agranulocytosis ka wā e emi nui ai kēia mau cell hakakā i kapa ʻia ʻo granulocytes, ʻoiai nā cell neutrophil nui loa, i loko o ke koko. Ke hana ʻia kēlā, aneane pau loa ka ʻōnaehana pale o ko mākou kino. Hoʻomaka mākou e maʻi maʻalahi mai ka germ liʻiliʻi loa.
ʻO ka maʻamau, pono i ke kanaka olakino ke loaʻa ma mua o 1,800 mau keʻokeʻo koko no kēlā me kēia microliter o ke koko. Inā hāʻule kēia helu ma lalo o 500, ua kapa ʻia ʻo Agranulocytosis. He kūlana weliweli loa kēia.
He aha nā kumu o ka agranulocytosis?
ʻElua mau ʻano nui o nā kumu o kēia maʻi: congenital a i loaʻa.
1. ʻO ka Agranulocytosis hānau:
ʻO ke kumu o kēia he kīnā hoʻoilina. Hānau ʻia kekahi mau keiki me ka hiki ke hoʻemi ʻia ke hana ʻana i nā hunaola koko keʻokeʻo i loko o ko lākou iwi iwi. Eia kekahi laʻana, aia kahi maʻi laha ʻole i kapa ʻia ʻo Kostmann syndrome. Loaʻa pinepine i kēlā mau keiki ke kuni, nā maʻi, a me nā pilikia iwi.
2. ʻO ka Agranulocytosis e kū mai ana ma hope:
ʻO kēia ke kūlana maʻamau. Hiki ke hana ma hope o ke ola no nā kumu like ʻole.
| Kumu | Wehewehena |
|---|---|
| Nā lāʻau lapaʻau | ʻO kēia ke kumu nui a maʻamau. Hiki i kekahi mau lāʻau lapaʻau ke kāohi i ka iwi iwi mai ka hana ʻana i nā hunaola koko keʻokeʻo a luku paha i nā hunaola i hana ʻia. |
| Nā maʻi | Hiki i kekahi mau maʻi viral (e like me ka HIV, hepatitis) a me nā maʻi bacteria (e like me ka typhoid, tuberculosis) ke hana i ka hāʻule ʻana o ka iwi. |
| Nā hemahema o ka wikamina | ʻAʻohe pono o ke kino i nā meaolaola e like me ka huaora B12 a i ʻole ka folate. |
| Nā kūlana olakino ʻē aʻe | Nā maʻi iwi ʻiʻo, nā hoʻoili iwi ʻiʻo, nā maʻi autoimmune e like me Systemic Lupus Erythematosus (SLE) a me Rheumatoid Arthritis. |
| Nā kumu ʻē aʻe | ʻO ka inu ʻona nui a me nā maʻi ʻai e like me ka anorexia nervosa. |
Pehea e hoʻoulu ai ka lāʻau lapaʻau i kēia maʻi?
ʻO nā lāʻau lapaʻau ke kumu nui o kēia. Ke lawe ʻoe i nā mea e like me kekahi mau lāʻau anti-cancer, emi iho nā hunaola koko keʻokeʻo o kēlā me kēia kanaka. Akā aia kekahi mau lāʻau lapaʻau, ʻoiai ʻaʻole ia e hoʻopilikia i ka hapa nui o ka poʻe, hiki ke hoʻoulu i ka agranulocytosis i kahi poʻe liʻiliʻi.
- Nā lāʻau lapaʻau e hana ana ma o ka ʻōnaehana pale kino: Hoʻoulu kekahi mau lāʻau i ko mākou kino e hana i nā antibodies e hoʻouka i kā mākou mau hunaola koko keʻokeʻo ponoʻī.
- Nā lāʻau hoʻopau iwi: Hoʻōki kekahi mau lāʻau (e like me ka valproic acid, carbamazepine, kekahi mau lāʻau antibiotic e like me amoxicillin) i ka hana ʻana o nā hunaola koko keʻokeʻo i loko o ka iwi.
- Nā lāʻau lapaʻau anticancer a me kekahi mau lāʻau lapaʻau no ka maʻi noʻonoʻo: ʻO kēia kekahi kumu nui o ka helu haʻahaʻa o nā cell koko keʻokeʻo.
ʻO ka mea nui loa, mai hoʻōki a hoʻomaka paha i kekahi lāʻau lapaʻau me ka ʻole o ke aʻo ʻana a kāu kauka . Inā manaʻo ʻoe he lāʻau lapaʻau ke kumu o kēia, e hoʻomaopopo koke i kāu kauka.
He aha nā hōʻailona o kēia maʻi?
ʻO ka hapa nui o ka manawa, ʻaʻohe hōʻailona kikoʻī no kēia maʻi. ʻIke ʻia ia ma ka hanana ke hana ʻia kahi hoʻāʻo koko no kekahi kumu ʻē aʻe. Eia nō naʻe, ʻike ʻia nā hōʻailona ma o nā maʻi i hoʻokumu ʻia e ka pale ʻana haʻahaʻa.
- kuni kiʻekiʻe koke
- Ke anu nei a me ka haʻalulu
- Nā ʻeha waha
- ʻEha poʻo
- Ka hou ʻana
- Nā ʻōpū lymph pehu
- Ka pehu ʻana o ke akepaʻa a i ʻole ka spleen
- Luhi mau a me ka luhi
ʻO ka mea weliweli loa e pili ana i kēia kūlana, ʻoiai he maʻi liʻiliʻi wale nō hiki ke ulu koke i kahi kūlana koʻikoʻi a hoʻoweliweli i ke ola i kapa ʻia ʻo sepsis . ʻO Sepsis kahi kūlana kahi e laha ai kahi maʻi ma ke kino holoʻokoʻa, hāʻule nui ke koko, a hiki i nā ʻōpū o loko o ke kino ke hāʻule. He kūlana kēia e pono ai ka mālama olakino ulia pōpilikia.
ʻO ka poʻe ma luna o 65 mau makahiki, ʻo ka poʻe me nā maʻi ʻē aʻe e like me ka maʻi puʻupaʻa a i ʻole ka maʻi puʻuwai, ʻoi aku ka nui o ka pilikia o nā pilikia inā loaʻa iā lākou kahi maʻi me ka agranulocytosis.
Pehea e mālama ʻia ai?
ʻO ka hana mua a koʻikoʻi loa i ka mālama ʻana i kēia, ʻo ia ke ʻike i ke kumu .
- Ke mālama ʻana i ke kumu: Inā loaʻa kēia ʻano ma muli o ka lāʻau lapaʻau, hoʻomaikaʻi pinepine ke ʻano i loko o 2-3 mau pule ma hope o ka hoʻōki ʻana i ka lāʻau lapaʻau e like me ke kuhikuhi a kāu kauka. Inā he maʻi ka maʻi, pono e mālama ʻia.
- Hoʻoulu i ka hana ʻana o nā keʻokeʻo koko: Hāʻawi ʻia nā inikini kūikawā e like me Filgrastim e hoʻonui i ka helu o nā keʻokeʻo koko. Hoʻoulu kēia i ka iwi iwi a hoʻonui i ka hana ʻana o nā neutrophil.
- Ka mālama ʻana i nā maʻi: Inā loaʻa iā ʻoe kahi maʻi bacteria, e kuhikuhi kāu kauka i nā antibiotics. No nā maʻi viral a fungal paha, e hāʻawi lākou iā ʻoe i nā lāʻau lapaʻau kikoʻī. Inā koʻikoʻi ka maʻi, pono paha ʻoe e hoʻokomo ʻia i ka haukapila a hāʻawi ʻia i ka lāʻau intravenous (IV).
- Hoʻoili iwi iwi: Inā ʻaʻohe lāʻau ʻē aʻe e kūpono ana, hiki ke manaʻo ʻia kahi hoʻoili iwi iwi mai kahi mea hāʻawi kūpono ma ke ʻano he koho hope loa.
Pehea e mālama ai kekahi me ka agranulocytosis?
Inā loaʻa iā ʻoe kēia maʻi, ua nāwaliwali loa kou ʻōnaehana pale kino, no laila pono ʻoe e akahele loa e pale iā ʻoe iho mai nā maʻi.
E hoʻomanaʻo, inā hāʻule kāu helu neutrophil ma lalo o 100 no 3-4 mau pule, aia kahi manawa kūpono 100% e loaʻa ai kahi maʻi. No laila e mālama pono i kēia mau hana palekana.
| Nā hana e hana ai e pale iā ʻoe iho mai nā maʻi | |
|---|---|
| Meaʻai | E ʻai wale i nā meaʻai i moʻa maikaʻi ʻia. E pale i ka ʻai ʻana i nā salakeke maka, nā mea ʻono, ka ʻiʻo i moʻa ʻole ʻia, ka iʻa, nā hua manu, a pēlā aku. E holoi a ʻili i nā huaʻai a me nā mea kanu ma mua o ka ʻai ʻana. |
| Hoʻomaʻemaʻe pilikino | E holoi pono i kou mau lima me ke kopa a me ka wai i nā manawa a pau. E hoʻohana i ka mea ʻumiʻumi uila ma kahi o ka pahi ʻumiʻumi. |
| Kaiapuni | Mai hele i nā wahi i piha i nā kānaka (nā kaʻa ʻōhua, nā kaʻaahi, nā hale kiʻiʻoniʻoni). Mai hana me ka lepo, e hoʻopā aku i nā holoholona. Mai ʻauʻau i loko o nā loko a me nā muliwai. |
| Nā pilina me nā poʻe ʻē aʻe | E pale i ka launa pū ʻana me ka poʻe maʻi (e like me ka poʻe me ke kuni a i ʻole ke anu). |
ʻOiai he maʻi koʻikoʻi ka agranulocytosis, hiki ke ho'ōla pinepine ʻia inā ʻike ʻia ke kumu a mālama pono ʻia. ʻO ka mea nui loa, ʻo ia ke ʻike koke i kāu kauka ke ʻike ʻoe i ka hōʻailona liʻiliʻi o ka maʻi (kuni, ʻeha kino). ʻO ka hana wikiwiki ʻana e hiki ke kōkua i ka pale ʻana i nā pilikia koʻikoʻi.
Leka Lawe-Home
- ʻO ka Agranulocytosis kahi emi weliweli o kahi ʻano o ke koko keʻokeʻo (ʻo ia hoʻi nā neutrophils) e hakakā nei i nā germs i loko o ko mākou koko.
- Hiki i kēia ke hoʻonāwaliwali i ka ʻōnaehana pale o ke kino a lilo i mea koʻikoʻi loa nā maʻi liʻiliʻi.
- ʻO ke kumu nui o kēia ma muli o ka lawe ʻana i nā lāʻau lapaʻau, nā maʻi like ʻole, a me kekahi mau kūlana olakino.
- Inā loaʻa iā ʻoe nā hōʻailona e like me ke kuni koke, ka ʻūlū, a i ʻole ka ʻeha waha, e ʻike koke i kāu kauka.
- Inā ua ʻike ʻia ʻoe me kēia maʻi, he mea nui e mālama pono e pale aku i nā maʻi.











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