Skip to main content

Peb puas yuav tham txog tus mob qog nqaij hlav hu ua Pheochromocytoma hnub no?

Peb puas yuav tham txog tus mob qog nqaij hlav hu ua Pheochromocytoma hnub no?

Koj puas muaj tej lub sij hawm koj muaj ntshav siab tam sim ntawd? Los yog koj tsuas yog hws xwb? Koj puas mob taub hau nrog lub plawv dhia ceev? Tsis txhob xav tias qee yam no yog ib yam kab mob loj heev. Txawm li cas los xij, yog tias cov tsos mob no tseem muaj, tshwj xeeb tshaj yog nrog ntshav siab uas nyuaj rau tswj, nws yog ib lub tswv yim zoo kom txhawj me ntsis. Hnub no peb yuav tham txog ib qho mob uas tsis tshua muaj, tab sis yog tias kuaj pom zoo, tuaj yeem kho tau zoo heev. Qhov ntawd hu ua pheochromocytoma.

Pheochromocytoma yog dab tsi? Cia peb nkag siab yooj yim.

Hais yooj yim xwb, pheochromocytoma yog ib qho mob qog uas loj hlob nyob rau hauv nruab nrab ntawm cov qog adrenal, lub adrenal medulla. Cov qog no yog tsim los ntawm ib hom hlwb tshwj xeeb hu ua chromaffin hlwb. Cov hlwb no tsim thiab tso cov tshuaj hormones rau hauv cov ntshav uas tsim nyog rau peb lub cev "sib ntaus lossis khiav". Xav txog nws, thaum koj ntshai tam sim ntawd lossis ntsib kev ntxhov siab ntau, cov kev hloov pauv uas tshwm sim hauv koj lub cev - koj lub plawv dhia nce ntxiv, koj hws, koj lub cev tshee hnyo - cov tshuaj hormones no yog lub luag haujlwm rau qhov no.

Feem ntau cov mob pheochromocytoma tsuas tshwm sim hauv ib lub qog adrenal xwb. Txawm li cas los xij, qee zaum nws tuaj yeem tshwm sim hauv ob lub qog. Nws muaj peev xwm muaj ntau dua ib lub qog hauv ib lub qog.

Qhov tseem ceeb, feem ntau cov pheochromocytomas yog cov mob tsis muaj teeb meem (tsis yog mob qog) . Qhov no txhais tau tias lawv tsis kis mus rau lwm qhov ntawm lub cev. Txawm li cas los xij, ntawm 10% thiab 15% tuaj yeem yog mob qog noj ntshav. Yog tias qhov no yog mob qog noj ntshav, nws tau piav qhia ua ntau pawg tseem ceeb, nyob ntawm seb nws tau kis mus li cas:

  • Pheochromocytoma Hauv Ib Cheeb Tsam: Lub qog no tsuas nyob hauv ib lossis ob lub qog adrenal xwb.
  • Regional pheochromocytoma: Tus mob qog nqaij hlav tau kis mus rau cov qog ntshav ze ntawm cov qog adrenal lossis lwm cov nqaij.
  • Metastatic pheochromocytoma: Tus mob qog nqaij hlav tau kis mus rau cov kabmob deb xws li lub siab, lub ntsws, lossis pob txha.
  • Mob pheochromocytoma uas rov qab los dua: Tus mob qog noj ntshav tau rov qab los tom qab kho mob lawm. Nws tuaj yeem nyob rau tib qho chaw uas nws tau nyob ua ntej lossis nyob rau lwm qhov chaw.

Cov qog adrenal hauv peb lub cev yog dab tsi? Lawv lub luag haujlwm yog dab tsi?

Peb muaj ob lub qog adrenal. Lawv nyob tom qab ntawm peb lub plab, saum peb lub raum, zoo li lub hau. Lawv yog ib feem ntawm peb lub endocrine system. Txhua lub qog adrenal muaj ob feem tseem ceeb. Txheej sab nraud hu ua adrenal cortex, thiab nruab nrab hu ua adrenal medulla.

Peb lub adrenal medulla tsim ib pawg ntawm cov tshuaj hormones hu ua catecholamines. Cov tshuaj hormones no tswj ntau yam txheej txheem tseem ceeb hauv peb lub cev:

  • Lub plawv dhia ceev
  • Ntshav siab
  • Qib ntshav qab zib (ntshav qab zib)
  • Peb lub cev teb li cas rau kev ntxhov siab (qhov kev teb "sib ntaus lossis khiav")

Cov hom catecholamines tseem ceeb yog:

  • Dopamine
  • Epinephrine (Adrenaline) `(Epinephrine / Adrenaline)`
  • Norepinephrine (Noradrenaline) `(Norepinephrine / Noradrenaline)`

Thaum muaj tus mob pheochromocytoma, nws tuaj yeem tso cov tshuaj hormones no, adrenaline thiab noradrenaline, mus rau hauv cov ntshav ntau dua li qhov tsim nyog. Thaum ntawd yog thaum ntau yam tsos mob pib tshwm sim.

Qhov txawv ntawm Pheochromocytoma thiab Paraganglioma yog dab tsi?

Cov no yog ob hom qog nqaij hlav zoo sib xws, tsis tshua muaj. Ob qho tib si tshwm sim los ntawm tib lub hlwb chromaffin uas peb tau tham ua ntej. Txawm li cas los xij, pheochromocytoma tshwm sim hauv nruab nrab ntawm lub qog adrenal (adrenal medulla), thaum paraganglioma tshwm sim hauv lwm qhov chaw sab nraum lub qog adrenal .

Leej twg yuav muaj tus mob no ntau tshaj? Nws tshwm sim ntau npaum li cas?

Kab mob Pheochromocytoma tuaj yeem tshwm sim rau txhua lub hnub nyoog, tab sis feem ntau tshwm sim rau cov neeg hnub nyoog ntawm 30 thiab 50 xyoo. Kwv yees li 10% ntawm cov neeg mob tau tshaj tawm tias yog menyuam yaus.

Qhov no yog ib qho mob qog nqaij hlav uas tsis tshua muaj . Nws nyuaj rau hais tias muaj pes tsawg tus neeg muaj tus mob no. Vim tias qee tus neeg tsis muaj tsos mob dab tsi, tus kab mob no yuav tsis raug kuaj pom. Kwv yees tias tsawg dua 1% ntawm cov neeg uas muaj ntshav siab muaj pheochromocytoma.

Cov tsos mob ntawm tus neeg uas muaj tus kab mob pheochromocytoma qhia li cas?

Cov tsos mob ntawm tus kab mob Pheochromocytoma tshwm sim thaum lub qog tso cov tshuaj hormones adrenaline (epinephrine) lossis noradrenaline (norepinephrine) ntau dhau rau hauv cov ntshav. Txawm li cas los xij, qee cov qog tsis tsim cov tshuaj hormones no ntau dhau thiab tej zaum yuav tsis muaj tsos mob.

Cov tsos mob feem ntau pom yog:

  • Ntshav Siab (Tshuaj Ntshav Siab): Qhov no yog cov tsos mob tseem ceeb. Qee zaum nws nyuaj rau tswj.
  • Mob taub hau: Nws tuaj yeem yog mob taub hau hnyav, tam sim ntawd.
  • Hws ntau dhau tsis muaj laj thawj.
  • Palpitations yog ib qho kev xav ntawm lub plawv dhia ceev, tsis sib xws, lossis pounding.
  • Zoo li koj lub cev tshee hnyo.

Cov tsos mob uas tsis tshua muaj:

  • Mob hauv siab thiab/lossis mob plab.
  • Daim tawv nqaij mam li daj dua li niaj zaus.
  • Xeev siab thiab/lossis ntuav.
  • Mob raws plab.
  • Cem quav.
  • Orthostatic hypotension yog qhov ntshav siab poob qis tam sim ntawd thaum koj sawv ntsug. Qhov no txhais tau tias koj yuav kiv taub hau thaum koj sawv ntsug tam sim ntawd los ntawm qhov chaw zaum.
  • Poob phaus tsis muaj laj thawj.

Cov tsos mob no yuav tshwm sim lossis hnyav zuj zus tom qab muaj tej yam xwm txheej. Piv txwv li:

  • Kev tawm dag zog lub cev hnyav heev.
  • Kev raug mob lub cev lossis kev ntxhov siab hnyav rau lub hlwb.
  • Yug me nyuam.
  • Tau txais tshuaj loog.
  • Ua kev phais mob.
  • Noj cov khoom noj uas muaj tyramine ntau (piv txwv li cawv liab, chocolate, cheese).

Puas muaj cov tsos mob tas li? Los yog lawv tuaj thiab mus?

Ib tug neeg uas muaj mob pheochromocytoma yuav muaj ntshav siab tas li, lossis nws yuav tuaj thiab mus .

Tej tus neeg yuav muaj "paroxysmal attacks," lossis cov tsos mob tshwm sim sai sai. Qhov no txhais tau tias muaj ntshav siab nce sai sai, nrog rau cov tsos mob xws li mob taub hau hnyav, lub plawv dhia ceev ceev, thiab tawm hws ntau dhau. Cov "kev tawm tsam" no tuaj yeem tshwm sim ntau zaus hauv ib hnub, lossis ib lossis ob zaug hauv ib hlis.

Tseem Ceeb: Yog tias koj muaj ib qho ntawm cov tsos mob no, tshwj xeeb tshaj yog ntshav siab tam sim ntawd, mob taub hau, tawm hws, thiab lub plawv dhia ceev ceev, nws yog ib qho tseem ceeb heev uas yuav tsum nrhiav kev pab kho mob.

Vim li cas thiaj muaj tus mob pheochromocytoma? Dab tsi yog cov ua rau muaj tus mob no?

Feem ntau, tsis muaj qhov ua rau mob pheochromocytoma tshwm sim . Nws tshwm sim yam tsis muaj laj thawj.

Txawm li cas los xij, nyob rau hauv 25% txog 35% ntawm cov rooj plaub, qhov mob no yog cuam tshuam nrog cov mob uas tau txais los ntawm noob caj noob ces. Qee qhov tseem ceeb yog:

  • Mob qog nqaij hlav endocrine ntau yam 2, hom A thiab B (MEN2A thiab MEN2B)
  • Kab mob Von Hippel-Lindau (VHL)
  • Kab mob Neurofibromatosis hom 1 (NF1)
  • Kab mob paraganglioma uas muaj keeb kwm los ntawm noob caj noob ces
  • Carney-Stratakis dyad [paraganglioma thiab gastrointestinal stromal tumor (GIST)]
  • Carney triad (paraganglioma, GIST thiab pulmonary chondroma)

Ntxiv rau cov mob caj ces no, pheochromocytoma kuj tseem tuaj yeem tshwm sim vim muaj kev hloov pauv hauv tsawg kawg 10 lub noob sib txawv.

Yuav kuaj mob li cas? (Kev kuaj mob)

Kab mob Pheochromocytoma nyuaj rau kuaj mob vim nws yog ib hom qog nqaij hlav uas tsis tshua muaj thiab qee zaum tsis muaj tsos mob dab tsi li. Qee zaum, cov qog nqaij hlav raug pom tsis tau thaum lub sijhawm kuaj mob vim lwm yam laj thawj.

Muaj ntau yam ua rau tus kws kho mob xav tias muaj tus kab mob no:

  • Koj liKeeb kwm kev kho mob kom ntxaws, tshwj xeeb yog seb puas muaj leej twg hauv tsev neeg tau muaj mob pheochromocytoma ua ntej.
  • Kev kuaj mob thiab lub cev tag nrho.
  • Qee cov tsos mob tshwj xeeb , piv txwv li cov "paroxysmal attacks" uas peb tau tham txog thiab ntshav siab uas tsis raug tswj los ntawm kev kho mob ib txwm muaj.

Yuav ua li cas thiaj kuaj tau?

Koj tus kws kho mob yuav pom zoo kom kuaj cov kev kuaj no kom paub tseeb tias koj puas muaj mob pheochromocytoma:

  • Kev kuaj zis 24 teev: Qhov no suav nrog kev sau koj cov zis thoob plaws hnub thiab ntsuas qhov ntau ntawm catecholamines hauv nws. Nws kuj ntsuas cov tshuaj uas tsim tawm thaum cov tshuaj hormones no tawg. Yog tias cov qib no siab dua li qub, nws yuav yog ib qho cim ntawm pheochromocytoma.
  • Kev kuaj ntshav catecholamine: Cov no ntsuas cov catecholamines hauv cov ntshav. Ib yam li kev kuaj zis, lawv kuj nrhiav cov tshuaj uas tsim los ntawm kev rhuav tshem cov tshuaj hormones.
  • CT scan (Computer Tomography scan): Qhov no siv ntau cov duab X-rays los tsim cov duab ntxaws ntxaws ntawm sab hauv koj lub cev. Koj tus kws kho mob yuav pom zoo kom ua qhov no los saib koj cov qog adrenal.
  • Kev kuaj MRI (MRI - Magnetic Resonance Imaging): Qhov no siv lub hlau nplaum, cov nthwv dej xov tooj cua, thiab lub khoos phis tawj los ua cov duab ntxaws ntxaws ntawm sab hauv lub cev. Nws kuj tseem siv los kuaj xyuas cov qog adrenal.

Thaum tus kab mob tau paub tseeb lawm, yuav muaj kev kuaj ntxiv kom paub seb qhov qog puas yog mob qog (malignant) lossis mob qog tsis muaj mob (benign), thiab seb nws puas tau kis mus rau lwm qhov ntawm lub cev.

Vim li cas kev kuaj noob caj noob ces thiaj tseem ceeb?

Yog tias koj raug kuaj pom tias muaj mob pheochromocytoma, koj tus kws kho mob yuav pom zoo kom koj sab laj thiab kuaj mob caj ces kom paub seb koj puas muaj tus kab mob uas tau txais los ntawm noob caj ces uas ua rau koj muaj feem yuav mob qog noj ntshav lwm yam.

Kev kuaj noob caj ces yuav raug pom zoo rau cov xwm txheej zoo li no:

  • Yog tias koj lossis ib tug neeg hauv koj tsev neeg muaj cov tsos mob cuam tshuam nrog tus kab mob pheochromocytoma lossis paraganglioma syndrome uas tau txais los ntawm noob caj noob ces.
  • Yog tias koj muaj qog nqaij hlav hauv koj ob lub qog adrenal.
  • Yog tias muaj ntau tshaj ib lub qog hauv ib lub qog adrenal.
  • Yog tias muaj cov tsos mob ntawm cov qib catecholamines ntau ntxiv hauv cov ntshav.
  • Yog tias kuaj pom tias muaj tus kab mob pheochromocytoma ua ntej hnub nyoog 40 xyoo.

Yog tias kev kuaj noob caj noob ces pom muaj kev hloov pauv ntawm noob caj noob ces, tus kws pab tswv yim txog noob caj noob ces yuav pom zoo kom lwm tus tswv cuab hauv koj tsev neeg (cov neeg uas tsis muaj tsos mob tab sis muaj kev pheej hmoo) kuj yuav tsum kuaj qhov no thiab.

Cov kev kho mob rau Pheochromocytoma yog dab tsi?

Txoj kev kho mob zoo tshaj plaws rau qhov no yog phais tshem tawm qhov qog, yog tias ua tau .

Kev xaiv kev kho mob nyob ntawm ntau yam:

  • Qhov loj ntawm lub qog.
  • Seb qhov mob qog yog mob qog (malignant) los yog mob qog benign (benign).
  • Seb puas muaj cov tsos mob vim yog kev nce ntxiv ntawm cov tshuaj hormones catecholamine.
  • Puas yog lub qog tsuas yog nyob rau ib qho chaw xwb, lossis nws puas tau kis mus rau lwm qhov ntawm lub cev? (Metastasised)
  • Seb tus kab mob puas tau kuaj pom thawj zaug, lossis seb nws puas tau rov tshwm sim dua tom qab kev kho mob yav dhau los.

Yog tias koj muaj cov tsos mob vim yog cov tshuaj hormones adrenal ntau ntxiv, koj tus kws kho mob yuav sau ntawv kom tswj cov tsos mob ntawd. Piv txwv li:

  • Cov tshuaj siv los tswj cov ntshav siab kom nyob rau theem ib txwm, xws li alpha-blockers.
  • Cov tshuaj siv los ua kom lub plawv dhia ceev li qub, xws li beta-blockers.
  • Cov tshuaj uas thaiv cov teebmeem ntawm cov tshuaj hormones uas tso tawm ntau dhau los ntawm cov qog adrenal.

Cov kev kho mob tseem ceeb rau pheochromocytoma yog:

  • Kev phais mob
  • Kev kho mob hluav taws xob
  • Kev kho mob qog noj ntshav
  • Kev kho mob ablation
  • Kev kho mob embolization
  • Kev kho mob tsom mus rau

Ua ke, koj thiab koj pab neeg kho mob yuav txiav txim siab txog txoj kev npaj kho mob uas zoo tshaj plaws rau koj.

Cov kev kho mob tseem ceeb

  • Kev phais:

Qhov no yog kev kho mob tseem ceeb rau pheochromocytoma. Kwv yees li ntawm 90% ntawm cov qog nqaij hlav tuaj yeem raug phais tshem tawm .

Koj tus kws kho mob yuav pom zoo kom phais ib lossis ob qho ntawm koj cov qog adrenal (adrenalectomy). Thaum lub sijhawm phais, tus kws phais yuav kuaj cov nqaij thiab cov qog lymph nyob ib puag ncig kom pom tias qhov qog puas tau kis mus rau lwm qhov. Yog tias nws tau kis mus rau lwm qhov, lawv yuav tshem cov nqaij ntawd tawm, yog tias ua tau.

Tom qab phais lawm, koj cov ntshav lossis zis yuav raug kuaj seb puas muaj cov catecholamine ntau ntau. Yog tias cov qib rov qab mus rau qhov qub, nws txhais tau tias tag nrho cov hlwb pheochromocytoma tau raug tshem tawm lawm.

Yog tias ob lub qog adrenal raug tshem tawm, koj yuav tsum tau noj tshuaj hormones rau tas koj lub neej kom hloov cov tshuaj hormones uas cov qog adrenal tsim tawm.

  • Kev kho mob hluav taws xob:

Qhov no yog kev kho mob uas siv los tua cov hlwb qog noj ntshav lossis tiv thaiv lawv kom tsis txhob loj hlob. Qhov no ua tiav rau hauv txoj kev uas tsis ua rau cov nqaij noj qab haus huv puas tsuaj ntau li ntau tau.

Muaj ob hom kev kho mob hluav taws xob:

  • Kev kho mob hluav taws xob sab nraud: Kev kho mob hluav taws xob raug xa mus rau qhov chaw mob qog noj ntshav los ntawm lub tshuab sab nraud lub cev.
  • Kev kho mob hluav taws xob sab hauv: Cov tshuaj radioactive raug ntim rau hauv cov koob, noob, xov hlau, lossis catheters thiab tus kws kho mob ntxig rau hauv lossis ze ntawm qhov chaw mob qog noj ntshav.

Hom kev kho mob hluav taws xob nyob ntawm seb tus mob qog noj ntshav puas yog nyob ib qho chaw, ib cheeb tsam, kis mus rau lwm qhov, lossis rov tshwm sim dua. Feem ntau, tus mob pheochromocytoma uas muaj teeb meem loj raug kho nrog kev kho mob hluav taws xob sab nraud thiab/lossis kev kho mob 131I-MIBG. 131I-MIBG yog ib yam khoom uas muaj hluav taws xob uas lo rau qee cov hlwb qog noj ntshav thiab tua lawv.

  • Kev Kho Mob Siv Tshuaj:

Qhov no siv cov tshuaj los tua cov hlwb qog noj ntshav, tiv thaiv lawv kom tsis txhob faib thiab loj hlob, lossis tiv thaiv kev loj hlob ntawm cov qog noj ntshav. Cov tshuaj no feem ntau yog muab rau hauv cov hlab ntsha. Txawm hais tias qhov no yog kev kho mob zoo, nws tuaj yeem muaj cov kev mob tshwm sim.

  • Kev kho mob ablation:

Qhov no yog kev kho mob uas tsis tas phais ntau. Nws siv cua sov heev lossis txias heev los rhuav tshem cov qog nqaij hlav.

  • Kev siv hluav taws xob ntau zaus (radiofrequency ablation): Kev siv hluav taws xob ntau zaus (radiofrequency ablation) siv cov nthwv dej xov tooj cua los ua kom sov thiab rhuav tshem cov hlwb qog nqaij hlav thiab cov hlwb tsis zoo.
  • Kev Kho Mob Nkeeg: Siv cov kua nitrogen lossis cov pa roj carbon dioxide los khov thiab rhuav tshem cov hlwb qog noj ntshav thiab cov hlwb tsis zoo.
  • Kev kho mob embolization:

Hauv qhov no, cov hlab ntsha uas xa cov ntshav mus rau lub qog adrenal raug thaiv. Qhov no ua rau cov ntshav tsis ntws mus rau lub qog, tua cov hlwb qog nqaij hlav uas loj hlob nyob ntawd.

  • Kev kho mob rau lub hom phiaj:

Qhov no siv cov tshuaj lossis lwm yam tshuaj uas tsuas yog tawm tsam cov hlwb qog nqaij hlav xwb yam tsis ua rau cov hlwb zoo puas tsuaj. Kev kho mob no yog siv rau cov qog nqaij hlav uas kis mus rau lwm qhov thiab rov tshwm sim dua.

Muaj ib hom tshuaj tyrosine kinase inhibitor hu ua sunitinib uas tab tom raug kawm txog rau kev kho mob qog nqaij hlav uas kis mus rau lwm qhov (metastatic pheochromocytoma). Cov tshuaj no tiv thaiv kev loj hlob ntawm qog nqaij hlav.

Puas tiv thaiv tau tus kab mob no?

Tu siab kawg li, tsis muaj ib txoj kev twg los tiv thaiv tau tus kab mob pheochromocytoma. Txawm li cas los xij, yog tias koj muaj feem yuav mob no vim yog cov tsos mob uas los ntawm noob caj noob ces thiab cov noob caj noob ces, kev qhia txog noob caj noob ces tuaj yeem pab tau koj kuaj mob thiab nrhiav tau tus kab mob thaum ntxov.

Yog tias koj cov neeg hauv tsev neeg ze (cov kwv tij neej tsa, niam txiv) tau muaj mob pheochromocytoma, lossis yog tias koj muaj mob caj ces zoo li cov uas peb tau tham ua ntej (Multiple endocrine neoplasia 2 syndrome, Von Hippel-Lindau (VHL) disease, Neurofibromatosis type 1 (NF1), Hereditary paraganglioma syndrome, Carney-Stratakis dyad, Carney triad), nws yog ib qho tseem ceeb heev uas yuav tsum nrog koj tus kws kho mob tham txog qhov no.

Muaj feem yuav rov zoo tom qab kho mob li cas? (Kev kwv yees)

Feem ntau, kev cia siab rau tus kab mob pheochromocytoma yuav zoo heev yog tias kho tau.Peb twb tau hais lawm tias kwv yees li 90% ntawm cov qog nqaij hlav tuaj yeem raug tshem tawm los ntawm kev phais.

Txawm li cas los xij, yog tias tsis kho, qhov mob no tuaj yeem ua rau muaj teeb meem loj heev, txawm tias ua rau tuag taus . Piv txwv li:

  • Kab mob plawv
  • Mob plawv
  • Kev los ntshav hauv lub hlwb uas tsis tswj tau (Cerebral hemorrhaging)
  • Cov kua dej sib sau ua ke hauv lub ntsws (Pulmonary edema)

Qee cov neeg mob pheochromocytoma kuj muaj feem yuav mob stroke lossis myocardial infarction.

Kuv yuav tsum mus ntsib kws kho mob thaum twg?

  • Yog tias koj raug kuaj pom tias muaj tus kab mob pheochromocytoma thiab muaj cov tsos mob uas ua rau koj txhawj xeeb, mus ntsib koj tus kws kho mob tam sim ntawd.
  • Yog koj muaj cov tsos mob ntawm tus kab mob pheochromocytoma, xws li ntshav siab thiab mob taub hau, nrog koj tus kws kho mob tham. Txawm hais tias tus kab mob pheochromocytoma tsis tshua muaj, nws yog ib qho tseem ceeb uas yuav tsum kho tus kab mob ntshav siab.
  • Yog koj paub tias ib tug ntawm koj cov txheeb ze ze (cov kwv tij neej tsa, niam txiv) muaj mob caj ces xws li 'Multiple endocrine neoplasia 2 syndrome' lossis 'Von Hippel-Lindau (VHL) disease', koj kuj tseem yuav muaj feem yuav mob pheochromocytoma ntau dua, yog li mus ntsib kws kho mob kom tham txog kev kuaj caj ces.

Kuv yuav tsum nug tus kws kho mob li cas?

Yog tias koj raug kuaj pom tias muaj tus kab mob pheochromocytoma, nws yuav pab tau yog tias koj nug koj tus kws kho mob cov lus nug no:

  • Vim li cas kuv thiaj muaj tus mob pheochromocytoma?
  • Kuv cov menyuam thiab/lossis cov txheeb ze puas tuaj yeem muaj mob pheochromocytoma?
  • Kuv muaj cov kev kho mob twg?
  • Cov kev mob tshwm sim ntawm ntau yam kev kho mob sib txawv yog dab tsi?
  • Kuv yuav tswj kuv cov tsos mob li cas?

Thaum kawg, tej yam tseem ceeb tshaj plaws uas yuav tsum nco ntsoov (Cov Lus Coj Mus Tsev)

Zoo, yog li ntawd, txawm hais tias pheochromocytoma yog ib qho mob qog nqaij hlav uas tsis tshua muaj, nws feem ntau yog mob qog nqaij hlav tsis muaj teeb meem thiab kho tau . Tsis tas li ntawd, nws tuaj yeem tshwm sim hauv tsev neeg, yog li ntawd yog tias koj lossis ib tus neeg hauv koj tsev neeg raug kuaj pom tias muaj tus mob no, nws yog ib qho tseem ceeb kom tau txais kev kuaj mob caj ces. Qhov no kuj tseem tuaj yeem pab txiav txim siab seb koj puas muaj kev pheej hmoo rau lwm yam teeb meem kev noj qab haus huv.

Nco ntsoov, yog tias koj muaj lus nug txog koj qhov kev pheej hmoo ntawm kev mob pheochromocytoma lossis txog tus kab mob no, tsis txhob ntshai tham nrog koj tus kws kho mob. Lawv nyob ntawm no los pab koj. Nyob kom noj qab nyob zoo!


Pheochromocytoma , adrenal gland, catecholamines, ntshav siab, mob taub hau, tawm hws, qog, endocrine system

Frequently Asked Questions (FAQ)

Yuav ua li cas thiaj kuaj tau?

Koj tus kws kho mob yuav pom zoo kom kuaj cov kev kuaj no kom paub tseeb tias koj puas muaj mob pheochromocytoma:

Vim li cas kev kuaj noob caj noob ces thiaj tseem ceeb?

Yog tias koj raug kuaj pom tias muaj mob pheochromocytoma, koj tus kws kho mob yuav pom zoo kom koj sab laj thiab kuaj mob caj ces kom paub seb koj puas muaj tus kab mob uas tau txais los ntawm noob caj ces uas ua rau koj muaj feem yuav mob qog noj ntshav lwm yam.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.

Ntxiv koj cov lus

Thov xam: 7 + 2 =
Peb puas yuav tham txog tus mob qog nqaij hlav hu ua Pheochromocytoma hnub no?

Peb puas yuav tham txog tus mob qog nqaij hlav hu ua Pheochromocytoma hnub no?

Koj puas muaj tej lub sij hawm koj muaj ntshav siab tam sim ntawd? Los yog koj tsuas yog hws xwb? Koj puas mob taub hau nrog lub plawv dhia ceev? Tsis txhob xav tias qee yam no yog ib yam kab mob loj heev. Txawm li cas los xij, yog tias cov tsos mob no tseem muaj, tshwj xeeb tshaj yog nrog ntshav siab uas nyuaj rau tswj, nws yog ib lub tswv yim zoo kom txhawj me ntsis. Hnub no peb yuav tham txog ib qho mob uas tsis tshua muaj, tab sis yog tias kuaj pom zoo, tuaj yeem kho tau zoo heev. Qhov ntawd hu ua pheochromocytoma.

Pheochromocytoma yog dab tsi? Cia peb nkag siab yooj yim.

Hais yooj yim xwb, pheochromocytoma yog ib qho mob qog uas loj hlob nyob rau hauv nruab nrab ntawm cov qog adrenal, lub adrenal medulla. Cov qog no yog tsim los ntawm ib hom hlwb tshwj xeeb hu ua chromaffin hlwb. Cov hlwb no tsim thiab tso cov tshuaj hormones rau hauv cov ntshav uas tsim nyog rau peb lub cev "sib ntaus lossis khiav". Xav txog nws, thaum koj ntshai tam sim ntawd lossis ntsib kev ntxhov siab ntau, cov kev hloov pauv uas tshwm sim hauv koj lub cev - koj lub plawv dhia nce ntxiv, koj hws, koj lub cev tshee hnyo - cov tshuaj hormones no yog lub luag haujlwm rau qhov no.

Feem ntau cov mob pheochromocytoma tsuas tshwm sim hauv ib lub qog adrenal xwb. Txawm li cas los xij, qee zaum nws tuaj yeem tshwm sim hauv ob lub qog. Nws muaj peev xwm muaj ntau dua ib lub qog hauv ib lub qog.

Qhov tseem ceeb, feem ntau cov pheochromocytomas yog cov mob tsis muaj teeb meem (tsis yog mob qog) . Qhov no txhais tau tias lawv tsis kis mus rau lwm qhov ntawm lub cev. Txawm li cas los xij, ntawm 10% thiab 15% tuaj yeem yog mob qog noj ntshav. Yog tias qhov no yog mob qog noj ntshav, nws tau piav qhia ua ntau pawg tseem ceeb, nyob ntawm seb nws tau kis mus li cas:

  • Pheochromocytoma Hauv Ib Cheeb Tsam: Lub qog no tsuas nyob hauv ib lossis ob lub qog adrenal xwb.
  • Regional pheochromocytoma: Tus mob qog nqaij hlav tau kis mus rau cov qog ntshav ze ntawm cov qog adrenal lossis lwm cov nqaij.
  • Metastatic pheochromocytoma: Tus mob qog nqaij hlav tau kis mus rau cov kabmob deb xws li lub siab, lub ntsws, lossis pob txha.
  • Mob pheochromocytoma uas rov qab los dua: Tus mob qog noj ntshav tau rov qab los tom qab kho mob lawm. Nws tuaj yeem nyob rau tib qho chaw uas nws tau nyob ua ntej lossis nyob rau lwm qhov chaw.

Cov qog adrenal hauv peb lub cev yog dab tsi? Lawv lub luag haujlwm yog dab tsi?

Peb muaj ob lub qog adrenal. Lawv nyob tom qab ntawm peb lub plab, saum peb lub raum, zoo li lub hau. Lawv yog ib feem ntawm peb lub endocrine system. Txhua lub qog adrenal muaj ob feem tseem ceeb. Txheej sab nraud hu ua adrenal cortex, thiab nruab nrab hu ua adrenal medulla.

Peb lub adrenal medulla tsim ib pawg ntawm cov tshuaj hormones hu ua catecholamines. Cov tshuaj hormones no tswj ntau yam txheej txheem tseem ceeb hauv peb lub cev:

  • Lub plawv dhia ceev
  • Ntshav siab
  • Qib ntshav qab zib (ntshav qab zib)
  • Peb lub cev teb li cas rau kev ntxhov siab (qhov kev teb "sib ntaus lossis khiav")

Cov hom catecholamines tseem ceeb yog:

  • Dopamine
  • Epinephrine (Adrenaline) `(Epinephrine / Adrenaline)`
  • Norepinephrine (Noradrenaline) `(Norepinephrine / Noradrenaline)`

Thaum muaj tus mob pheochromocytoma, nws tuaj yeem tso cov tshuaj hormones no, adrenaline thiab noradrenaline, mus rau hauv cov ntshav ntau dua li qhov tsim nyog. Thaum ntawd yog thaum ntau yam tsos mob pib tshwm sim.

Qhov txawv ntawm Pheochromocytoma thiab Paraganglioma yog dab tsi?

Cov no yog ob hom qog nqaij hlav zoo sib xws, tsis tshua muaj. Ob qho tib si tshwm sim los ntawm tib lub hlwb chromaffin uas peb tau tham ua ntej. Txawm li cas los xij, pheochromocytoma tshwm sim hauv nruab nrab ntawm lub qog adrenal (adrenal medulla), thaum paraganglioma tshwm sim hauv lwm qhov chaw sab nraum lub qog adrenal .

Leej twg yuav muaj tus mob no ntau tshaj? Nws tshwm sim ntau npaum li cas?

Kab mob Pheochromocytoma tuaj yeem tshwm sim rau txhua lub hnub nyoog, tab sis feem ntau tshwm sim rau cov neeg hnub nyoog ntawm 30 thiab 50 xyoo. Kwv yees li 10% ntawm cov neeg mob tau tshaj tawm tias yog menyuam yaus.

Qhov no yog ib qho mob qog nqaij hlav uas tsis tshua muaj . Nws nyuaj rau hais tias muaj pes tsawg tus neeg muaj tus mob no. Vim tias qee tus neeg tsis muaj tsos mob dab tsi, tus kab mob no yuav tsis raug kuaj pom. Kwv yees tias tsawg dua 1% ntawm cov neeg uas muaj ntshav siab muaj pheochromocytoma.

Cov tsos mob ntawm tus neeg uas muaj tus kab mob pheochromocytoma qhia li cas?

Cov tsos mob ntawm tus kab mob Pheochromocytoma tshwm sim thaum lub qog tso cov tshuaj hormones adrenaline (epinephrine) lossis noradrenaline (norepinephrine) ntau dhau rau hauv cov ntshav. Txawm li cas los xij, qee cov qog tsis tsim cov tshuaj hormones no ntau dhau thiab tej zaum yuav tsis muaj tsos mob.

Cov tsos mob feem ntau pom yog:

  • Ntshav Siab (Tshuaj Ntshav Siab): Qhov no yog cov tsos mob tseem ceeb. Qee zaum nws nyuaj rau tswj.
  • Mob taub hau: Nws tuaj yeem yog mob taub hau hnyav, tam sim ntawd.
  • Hws ntau dhau tsis muaj laj thawj.
  • Palpitations yog ib qho kev xav ntawm lub plawv dhia ceev, tsis sib xws, lossis pounding.
  • Zoo li koj lub cev tshee hnyo.

Cov tsos mob uas tsis tshua muaj:

  • Mob hauv siab thiab/lossis mob plab.
  • Daim tawv nqaij mam li daj dua li niaj zaus.
  • Xeev siab thiab/lossis ntuav.
  • Mob raws plab.
  • Cem quav.
  • Orthostatic hypotension yog qhov ntshav siab poob qis tam sim ntawd thaum koj sawv ntsug. Qhov no txhais tau tias koj yuav kiv taub hau thaum koj sawv ntsug tam sim ntawd los ntawm qhov chaw zaum.
  • Poob phaus tsis muaj laj thawj.

Cov tsos mob no yuav tshwm sim lossis hnyav zuj zus tom qab muaj tej yam xwm txheej. Piv txwv li:

  • Kev tawm dag zog lub cev hnyav heev.
  • Kev raug mob lub cev lossis kev ntxhov siab hnyav rau lub hlwb.
  • Yug me nyuam.
  • Tau txais tshuaj loog.
  • Ua kev phais mob.
  • Noj cov khoom noj uas muaj tyramine ntau (piv txwv li cawv liab, chocolate, cheese).

Puas muaj cov tsos mob tas li? Los yog lawv tuaj thiab mus?

Ib tug neeg uas muaj mob pheochromocytoma yuav muaj ntshav siab tas li, lossis nws yuav tuaj thiab mus .

Tej tus neeg yuav muaj "paroxysmal attacks," lossis cov tsos mob tshwm sim sai sai. Qhov no txhais tau tias muaj ntshav siab nce sai sai, nrog rau cov tsos mob xws li mob taub hau hnyav, lub plawv dhia ceev ceev, thiab tawm hws ntau dhau. Cov "kev tawm tsam" no tuaj yeem tshwm sim ntau zaus hauv ib hnub, lossis ib lossis ob zaug hauv ib hlis.

Tseem Ceeb: Yog tias koj muaj ib qho ntawm cov tsos mob no, tshwj xeeb tshaj yog ntshav siab tam sim ntawd, mob taub hau, tawm hws, thiab lub plawv dhia ceev ceev, nws yog ib qho tseem ceeb heev uas yuav tsum nrhiav kev pab kho mob.

Vim li cas thiaj muaj tus mob pheochromocytoma? Dab tsi yog cov ua rau muaj tus mob no?

Feem ntau, tsis muaj qhov ua rau mob pheochromocytoma tshwm sim . Nws tshwm sim yam tsis muaj laj thawj.

Txawm li cas los xij, nyob rau hauv 25% txog 35% ntawm cov rooj plaub, qhov mob no yog cuam tshuam nrog cov mob uas tau txais los ntawm noob caj noob ces. Qee qhov tseem ceeb yog:

  • Mob qog nqaij hlav endocrine ntau yam 2, hom A thiab B (MEN2A thiab MEN2B)
  • Kab mob Von Hippel-Lindau (VHL)
  • Kab mob Neurofibromatosis hom 1 (NF1)
  • Kab mob paraganglioma uas muaj keeb kwm los ntawm noob caj noob ces
  • Carney-Stratakis dyad [paraganglioma thiab gastrointestinal stromal tumor (GIST)]
  • Carney triad (paraganglioma, GIST thiab pulmonary chondroma)

Ntxiv rau cov mob caj ces no, pheochromocytoma kuj tseem tuaj yeem tshwm sim vim muaj kev hloov pauv hauv tsawg kawg 10 lub noob sib txawv.

Yuav kuaj mob li cas? (Kev kuaj mob)

Kab mob Pheochromocytoma nyuaj rau kuaj mob vim nws yog ib hom qog nqaij hlav uas tsis tshua muaj thiab qee zaum tsis muaj tsos mob dab tsi li. Qee zaum, cov qog nqaij hlav raug pom tsis tau thaum lub sijhawm kuaj mob vim lwm yam laj thawj.

Muaj ntau yam ua rau tus kws kho mob xav tias muaj tus kab mob no:

  • Koj liKeeb kwm kev kho mob kom ntxaws, tshwj xeeb yog seb puas muaj leej twg hauv tsev neeg tau muaj mob pheochromocytoma ua ntej.
  • Kev kuaj mob thiab lub cev tag nrho.
  • Qee cov tsos mob tshwj xeeb , piv txwv li cov "paroxysmal attacks" uas peb tau tham txog thiab ntshav siab uas tsis raug tswj los ntawm kev kho mob ib txwm muaj.

Yuav ua li cas thiaj kuaj tau?

Koj tus kws kho mob yuav pom zoo kom kuaj cov kev kuaj no kom paub tseeb tias koj puas muaj mob pheochromocytoma:

  • Kev kuaj zis 24 teev: Qhov no suav nrog kev sau koj cov zis thoob plaws hnub thiab ntsuas qhov ntau ntawm catecholamines hauv nws. Nws kuj ntsuas cov tshuaj uas tsim tawm thaum cov tshuaj hormones no tawg. Yog tias cov qib no siab dua li qub, nws yuav yog ib qho cim ntawm pheochromocytoma.
  • Kev kuaj ntshav catecholamine: Cov no ntsuas cov catecholamines hauv cov ntshav. Ib yam li kev kuaj zis, lawv kuj nrhiav cov tshuaj uas tsim los ntawm kev rhuav tshem cov tshuaj hormones.
  • CT scan (Computer Tomography scan): Qhov no siv ntau cov duab X-rays los tsim cov duab ntxaws ntxaws ntawm sab hauv koj lub cev. Koj tus kws kho mob yuav pom zoo kom ua qhov no los saib koj cov qog adrenal.
  • Kev kuaj MRI (MRI - Magnetic Resonance Imaging): Qhov no siv lub hlau nplaum, cov nthwv dej xov tooj cua, thiab lub khoos phis tawj los ua cov duab ntxaws ntxaws ntawm sab hauv lub cev. Nws kuj tseem siv los kuaj xyuas cov qog adrenal.

Thaum tus kab mob tau paub tseeb lawm, yuav muaj kev kuaj ntxiv kom paub seb qhov qog puas yog mob qog (malignant) lossis mob qog tsis muaj mob (benign), thiab seb nws puas tau kis mus rau lwm qhov ntawm lub cev.

Vim li cas kev kuaj noob caj noob ces thiaj tseem ceeb?

Yog tias koj raug kuaj pom tias muaj mob pheochromocytoma, koj tus kws kho mob yuav pom zoo kom koj sab laj thiab kuaj mob caj ces kom paub seb koj puas muaj tus kab mob uas tau txais los ntawm noob caj ces uas ua rau koj muaj feem yuav mob qog noj ntshav lwm yam.

Kev kuaj noob caj ces yuav raug pom zoo rau cov xwm txheej zoo li no:

  • Yog tias koj lossis ib tug neeg hauv koj tsev neeg muaj cov tsos mob cuam tshuam nrog tus kab mob pheochromocytoma lossis paraganglioma syndrome uas tau txais los ntawm noob caj noob ces.
  • Yog tias koj muaj qog nqaij hlav hauv koj ob lub qog adrenal.
  • Yog tias muaj ntau tshaj ib lub qog hauv ib lub qog adrenal.
  • Yog tias muaj cov tsos mob ntawm cov qib catecholamines ntau ntxiv hauv cov ntshav.
  • Yog tias kuaj pom tias muaj tus kab mob pheochromocytoma ua ntej hnub nyoog 40 xyoo.

Yog tias kev kuaj noob caj noob ces pom muaj kev hloov pauv ntawm noob caj noob ces, tus kws pab tswv yim txog noob caj noob ces yuav pom zoo kom lwm tus tswv cuab hauv koj tsev neeg (cov neeg uas tsis muaj tsos mob tab sis muaj kev pheej hmoo) kuj yuav tsum kuaj qhov no thiab.

Cov kev kho mob rau Pheochromocytoma yog dab tsi?

Txoj kev kho mob zoo tshaj plaws rau qhov no yog phais tshem tawm qhov qog, yog tias ua tau .

Kev xaiv kev kho mob nyob ntawm ntau yam:

  • Qhov loj ntawm lub qog.
  • Seb qhov mob qog yog mob qog (malignant) los yog mob qog benign (benign).
  • Seb puas muaj cov tsos mob vim yog kev nce ntxiv ntawm cov tshuaj hormones catecholamine.
  • Puas yog lub qog tsuas yog nyob rau ib qho chaw xwb, lossis nws puas tau kis mus rau lwm qhov ntawm lub cev? (Metastasised)
  • Seb tus kab mob puas tau kuaj pom thawj zaug, lossis seb nws puas tau rov tshwm sim dua tom qab kev kho mob yav dhau los.

Yog tias koj muaj cov tsos mob vim yog cov tshuaj hormones adrenal ntau ntxiv, koj tus kws kho mob yuav sau ntawv kom tswj cov tsos mob ntawd. Piv txwv li:

  • Cov tshuaj siv los tswj cov ntshav siab kom nyob rau theem ib txwm, xws li alpha-blockers.
  • Cov tshuaj siv los ua kom lub plawv dhia ceev li qub, xws li beta-blockers.
  • Cov tshuaj uas thaiv cov teebmeem ntawm cov tshuaj hormones uas tso tawm ntau dhau los ntawm cov qog adrenal.

Cov kev kho mob tseem ceeb rau pheochromocytoma yog:

  • Kev phais mob
  • Kev kho mob hluav taws xob
  • Kev kho mob qog noj ntshav
  • Kev kho mob ablation
  • Kev kho mob embolization
  • Kev kho mob tsom mus rau

Ua ke, koj thiab koj pab neeg kho mob yuav txiav txim siab txog txoj kev npaj kho mob uas zoo tshaj plaws rau koj.

Cov kev kho mob tseem ceeb

  • Kev phais:

Qhov no yog kev kho mob tseem ceeb rau pheochromocytoma. Kwv yees li ntawm 90% ntawm cov qog nqaij hlav tuaj yeem raug phais tshem tawm .

Koj tus kws kho mob yuav pom zoo kom phais ib lossis ob qho ntawm koj cov qog adrenal (adrenalectomy). Thaum lub sijhawm phais, tus kws phais yuav kuaj cov nqaij thiab cov qog lymph nyob ib puag ncig kom pom tias qhov qog puas tau kis mus rau lwm qhov. Yog tias nws tau kis mus rau lwm qhov, lawv yuav tshem cov nqaij ntawd tawm, yog tias ua tau.

Tom qab phais lawm, koj cov ntshav lossis zis yuav raug kuaj seb puas muaj cov catecholamine ntau ntau. Yog tias cov qib rov qab mus rau qhov qub, nws txhais tau tias tag nrho cov hlwb pheochromocytoma tau raug tshem tawm lawm.

Yog tias ob lub qog adrenal raug tshem tawm, koj yuav tsum tau noj tshuaj hormones rau tas koj lub neej kom hloov cov tshuaj hormones uas cov qog adrenal tsim tawm.

  • Kev kho mob hluav taws xob:

Qhov no yog kev kho mob uas siv los tua cov hlwb qog noj ntshav lossis tiv thaiv lawv kom tsis txhob loj hlob. Qhov no ua tiav rau hauv txoj kev uas tsis ua rau cov nqaij noj qab haus huv puas tsuaj ntau li ntau tau.

Muaj ob hom kev kho mob hluav taws xob:

  • Kev kho mob hluav taws xob sab nraud: Kev kho mob hluav taws xob raug xa mus rau qhov chaw mob qog noj ntshav los ntawm lub tshuab sab nraud lub cev.
  • Kev kho mob hluav taws xob sab hauv: Cov tshuaj radioactive raug ntim rau hauv cov koob, noob, xov hlau, lossis catheters thiab tus kws kho mob ntxig rau hauv lossis ze ntawm qhov chaw mob qog noj ntshav.

Hom kev kho mob hluav taws xob nyob ntawm seb tus mob qog noj ntshav puas yog nyob ib qho chaw, ib cheeb tsam, kis mus rau lwm qhov, lossis rov tshwm sim dua. Feem ntau, tus mob pheochromocytoma uas muaj teeb meem loj raug kho nrog kev kho mob hluav taws xob sab nraud thiab/lossis kev kho mob 131I-MIBG. 131I-MIBG yog ib yam khoom uas muaj hluav taws xob uas lo rau qee cov hlwb qog noj ntshav thiab tua lawv.

  • Kev Kho Mob Siv Tshuaj:

Qhov no siv cov tshuaj los tua cov hlwb qog noj ntshav, tiv thaiv lawv kom tsis txhob faib thiab loj hlob, lossis tiv thaiv kev loj hlob ntawm cov qog noj ntshav. Cov tshuaj no feem ntau yog muab rau hauv cov hlab ntsha. Txawm hais tias qhov no yog kev kho mob zoo, nws tuaj yeem muaj cov kev mob tshwm sim.

  • Kev kho mob ablation:

Qhov no yog kev kho mob uas tsis tas phais ntau. Nws siv cua sov heev lossis txias heev los rhuav tshem cov qog nqaij hlav.

  • Kev siv hluav taws xob ntau zaus (radiofrequency ablation): Kev siv hluav taws xob ntau zaus (radiofrequency ablation) siv cov nthwv dej xov tooj cua los ua kom sov thiab rhuav tshem cov hlwb qog nqaij hlav thiab cov hlwb tsis zoo.
  • Kev Kho Mob Nkeeg: Siv cov kua nitrogen lossis cov pa roj carbon dioxide los khov thiab rhuav tshem cov hlwb qog noj ntshav thiab cov hlwb tsis zoo.
  • Kev kho mob embolization:

Hauv qhov no, cov hlab ntsha uas xa cov ntshav mus rau lub qog adrenal raug thaiv. Qhov no ua rau cov ntshav tsis ntws mus rau lub qog, tua cov hlwb qog nqaij hlav uas loj hlob nyob ntawd.

  • Kev kho mob rau lub hom phiaj:

Qhov no siv cov tshuaj lossis lwm yam tshuaj uas tsuas yog tawm tsam cov hlwb qog nqaij hlav xwb yam tsis ua rau cov hlwb zoo puas tsuaj. Kev kho mob no yog siv rau cov qog nqaij hlav uas kis mus rau lwm qhov thiab rov tshwm sim dua.

Muaj ib hom tshuaj tyrosine kinase inhibitor hu ua sunitinib uas tab tom raug kawm txog rau kev kho mob qog nqaij hlav uas kis mus rau lwm qhov (metastatic pheochromocytoma). Cov tshuaj no tiv thaiv kev loj hlob ntawm qog nqaij hlav.

Puas tiv thaiv tau tus kab mob no?

Tu siab kawg li, tsis muaj ib txoj kev twg los tiv thaiv tau tus kab mob pheochromocytoma. Txawm li cas los xij, yog tias koj muaj feem yuav mob no vim yog cov tsos mob uas los ntawm noob caj noob ces thiab cov noob caj noob ces, kev qhia txog noob caj noob ces tuaj yeem pab tau koj kuaj mob thiab nrhiav tau tus kab mob thaum ntxov.

Yog tias koj cov neeg hauv tsev neeg ze (cov kwv tij neej tsa, niam txiv) tau muaj mob pheochromocytoma, lossis yog tias koj muaj mob caj ces zoo li cov uas peb tau tham ua ntej (Multiple endocrine neoplasia 2 syndrome, Von Hippel-Lindau (VHL) disease, Neurofibromatosis type 1 (NF1), Hereditary paraganglioma syndrome, Carney-Stratakis dyad, Carney triad), nws yog ib qho tseem ceeb heev uas yuav tsum nrog koj tus kws kho mob tham txog qhov no.

Muaj feem yuav rov zoo tom qab kho mob li cas? (Kev kwv yees)

Feem ntau, kev cia siab rau tus kab mob pheochromocytoma yuav zoo heev yog tias kho tau.Peb twb tau hais lawm tias kwv yees li 90% ntawm cov qog nqaij hlav tuaj yeem raug tshem tawm los ntawm kev phais.

Txawm li cas los xij, yog tias tsis kho, qhov mob no tuaj yeem ua rau muaj teeb meem loj heev, txawm tias ua rau tuag taus . Piv txwv li:

  • Kab mob plawv
  • Mob plawv
  • Kev los ntshav hauv lub hlwb uas tsis tswj tau (Cerebral hemorrhaging)
  • Cov kua dej sib sau ua ke hauv lub ntsws (Pulmonary edema)

Qee cov neeg mob pheochromocytoma kuj muaj feem yuav mob stroke lossis myocardial infarction.

Kuv yuav tsum mus ntsib kws kho mob thaum twg?

  • Yog tias koj raug kuaj pom tias muaj tus kab mob pheochromocytoma thiab muaj cov tsos mob uas ua rau koj txhawj xeeb, mus ntsib koj tus kws kho mob tam sim ntawd.
  • Yog koj muaj cov tsos mob ntawm tus kab mob pheochromocytoma, xws li ntshav siab thiab mob taub hau, nrog koj tus kws kho mob tham. Txawm hais tias tus kab mob pheochromocytoma tsis tshua muaj, nws yog ib qho tseem ceeb uas yuav tsum kho tus kab mob ntshav siab.
  • Yog koj paub tias ib tug ntawm koj cov txheeb ze ze (cov kwv tij neej tsa, niam txiv) muaj mob caj ces xws li 'Multiple endocrine neoplasia 2 syndrome' lossis 'Von Hippel-Lindau (VHL) disease', koj kuj tseem yuav muaj feem yuav mob pheochromocytoma ntau dua, yog li mus ntsib kws kho mob kom tham txog kev kuaj caj ces.

Kuv yuav tsum nug tus kws kho mob li cas?

Yog tias koj raug kuaj pom tias muaj tus kab mob pheochromocytoma, nws yuav pab tau yog tias koj nug koj tus kws kho mob cov lus nug no:

  • Vim li cas kuv thiaj muaj tus mob pheochromocytoma?
  • Kuv cov menyuam thiab/lossis cov txheeb ze puas tuaj yeem muaj mob pheochromocytoma?
  • Kuv muaj cov kev kho mob twg?
  • Cov kev mob tshwm sim ntawm ntau yam kev kho mob sib txawv yog dab tsi?
  • Kuv yuav tswj kuv cov tsos mob li cas?

Thaum kawg, tej yam tseem ceeb tshaj plaws uas yuav tsum nco ntsoov (Cov Lus Coj Mus Tsev)

Zoo, yog li ntawd, txawm hais tias pheochromocytoma yog ib qho mob qog nqaij hlav uas tsis tshua muaj, nws feem ntau yog mob qog nqaij hlav tsis muaj teeb meem thiab kho tau . Tsis tas li ntawd, nws tuaj yeem tshwm sim hauv tsev neeg, yog li ntawd yog tias koj lossis ib tus neeg hauv koj tsev neeg raug kuaj pom tias muaj tus mob no, nws yog ib qho tseem ceeb kom tau txais kev kuaj mob caj ces. Qhov no kuj tseem tuaj yeem pab txiav txim siab seb koj puas muaj kev pheej hmoo rau lwm yam teeb meem kev noj qab haus huv.

Nco ntsoov, yog tias koj muaj lus nug txog koj qhov kev pheej hmoo ntawm kev mob pheochromocytoma lossis txog tus kab mob no, tsis txhob ntshai tham nrog koj tus kws kho mob. Lawv nyob ntawm no los pab koj. Nyob kom noj qab nyob zoo!


Pheochromocytoma , adrenal gland, catecholamines, ntshav siab, mob taub hau, tawm hws, qog, endocrine system

Frequently Asked Questions (FAQ)

Yuav ua li cas thiaj kuaj tau?

Koj tus kws kho mob yuav pom zoo kom kuaj cov kev kuaj no kom paub tseeb tias koj puas muaj mob pheochromocytoma:

Vim li cas kev kuaj noob caj noob ces thiaj tseem ceeb?

Yog tias koj raug kuaj pom tias muaj mob pheochromocytoma, koj tus kws kho mob yuav pom zoo kom koj sab laj thiab kuaj mob caj ces kom paub seb koj puas muaj tus kab mob uas tau txais los ntawm noob caj ces uas ua rau koj muaj feem yuav mob qog noj ntshav lwm yam.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.

Ntxiv koj cov lus

Thov xam: 7 + 2 =