Koj tus menyuam puas muaj teeb meem nrog cov hlab ntsha lymph hauv nws txoj hnyuv? (Primary Intestinal Lymphangiectasia) Cia peb tham txog qhov no!

Koj puas tau pom tias koj tus me nyuam ob txhais ceg thiab caj npab tsuas yog o qee zaum? Los yog nws puas feem ntau yws txog mob plab? Nws puas poob phaus yam tsis nce phaus? Tej zaum koj yuav xav tias cov no yog cov tsos mob ib txwm muaj uas peb tsis tau them sai sai rau. Txawm li cas los xij, tom qab cov no, tej zaum yuav muaj ib qho mob tsis tshua muaj tab sis yeej txhawj xeeb hu ua 'Primary Intestinal Lymphangiectasia' (PIL) . Lub npe suab me ntsis ntshai, puas yog? Tab sis tsis txhob txhawj. Cia peb tham txog qhov no kom meej thiab yooj yim heev hnub no.

'Primary Intestinal Lymphangiectasia' yog dab tsi?

Hais yooj yim xwb, qhov no yog ib qho teeb meem tsis tshua muaj uas tshwm sim hauv peb cov menyuam txoj kev zom zaub mov, tshwj xeeb yog txoj hnyuv me. Koj paub, feem ntau ntawm cov khoom noj uas peb noj yog zom thiab cov as-ham hauv nws raug nqus mus rau hauv lub cev hauv txoj hnyuv me no.

Tam sim no, nyob rau hauv qhov xwm txheej no (PIL), lub raj me me hu ua 'lymph vessels' hauv koj tus menyuam txoj hnyuv me me raug puas tsuaj thiab lawv tsis ua haujlwm zoo. Cov hlab ntsha lymph no yog ib lub network zoo heev ntawm cov channel uas kis thoob plaws peb lub cev. Nws zoo li lwm lub 'yeeb nkab system' hauv peb lub cev. Lawv lub luag haujlwm tseem ceeb yog sau cov kua dej thiab cov protein uas sib sau ua ke hauv peb cov nqaij (peb hu cov kua dej no 'lymph') thiab xa rov qab mus rau lub cev ncig ntshav.

Tiamsis rau ib tug menyuam uas muaj PIL, cov hlab ntsha lymph no yuav o thiab 'tawg'. Qhov uas tshwm sim yog tias es tsis txhob nqus cov as-ham thiab cov protein los ntawm cov hlab ntsha lymph no rau hauv lub cev, lawv rov qab mus rau hauv txoj hnyuv. Nws zoo li dej ntws los ntawm cov yeeb nkab uas tawg.

Thaum tej yam xau zoo li no, muaj ob qhov teeb meem tseem ceeb tshwm sim:

1. Cov protein tsawg: Cov protein yog ib yam dab tsi uas ua lub luag haujlwm tseem ceeb heev hauv lub cev. Yog li thaum cov no nkag mus rau hauv txoj hnyuv, lub cev tsis tau txais cov protein txaus. Qhov no tuaj yeem ua rau tag nrho lub cev o. Peb kuj hu qhov mob no ua 'protein-losing enteropathy' hauv cov lus kho mob.

2. Kev Tsis Txaus Noj Haus: Nrog rau cov kua dej uas ntws tawm, cov vitamins thiab minerals tseem ceeb kuj ploj mus. Yog tias qhov no tsis tau saib xyuas kom zoo, tus menyuam yuav muaj ntau yam kev tsis txaus noj haus.

(PIL) feem ntau cuam tshuam rau cov menyuam yaus thiab cov hluas. Feem ntau nws raug kuaj pom ua ntej hnub nyoog 3 xyoos. Txawm li cas los xij, nws qee zaum tuaj yeem cuam tshuam rau cov neeg laus thiab txawm tias cov menyuam hauv plab. Tseem tsis tau muaj kev kho rau nws. Txawm li cas los xij, cov kws kho mob tuaj yeem tswj cov tsos mob thiab txo qhov xau thiab o los ntawm kev siv cov phiaj xwm noj zaub mov tshwj xeeb thiab tshuaj. Lawv kuj tseem tuaj yeem muab cov vitamins thiab minerals rau lub cev uas nws xav tau.

Qhov xwm txheej (PIL) no muaj ntau lub npe hu ua:

• Kev mob lymphangiectasia hauv plab hnyuv
• Lymphangiectasia
• kab mob Waldmann

Cov tsos mob ntawm tus mob no (PIL) yog dab tsi?

Cov tsos mob tseem ceeb thiab feem ntau ntawm PIL yog o vim yog cov kua dej khaws cia. Cov kws kho mob hu qhov no ua lymphedema . Tej zaum koj yuav pom qhov no thawj zaug ntawm koj tus menyuam ob txhais ceg thiab ko taw. Thaum cov kua dej no sib sau ua ke, koj tus menyuam lub ntsej muag, tes, thiab txawm tias thaj chaw ntawm lub cev kuj yuav pib o.

Xav txog seb, thaum koj tus menyuam sawv thaum sawv ntxov, lawv txhais taw zoo li qub, tab sis thaum nruab hnub dhau mus, thaum yav tsaus ntuj, lawv txhais taw o heev ua rau lawv tsis tuaj yeem hnav khau. Qhov ntawd yog qhov tshwm sim hauv qhov xwm txheej no.

Ntxiv rau qhov ntawd, tus menyuam kuj tseem yuav muaj kua dej nyob ib puag ncig lub plawv (hu ua pericarditis ), kua dej hauv lub hauv siab (hu ua pleural effusion ), lossis kua dej hauv plab (hu ua ascites lossis abdominal effusion) .

Nov yog qee cov tsos mob ntxiv:

• Mob plab
• Xeev siab thiab ntuav
• Mob plab (mob plab )
• Xav tias nkees txhua lub sijhawm (Fatigue)
• Kev poob phaus
• Tsis rog zuj zus txawm koj noj zaub mov ntau npaum li cas los xij (qhov no yog vim lub cev tsis nqus cov as-ham kom zoo, uas hu ua 'malabsorption' )

Yog koj tus menyuam muaj ib lossis ntau yam ntawm cov tsos mob no, nws yog qhov zoo tshaj plaws los nrhiav kev pab kho mob.

Puas muaj teeb meem loj ntawm tus mob (PIL) no?

Yog, txawm hais tias tsis tshua muaj, (PIL) tuaj yeem ua rau tus menyuam lub cev tag nrho o tuaj ntau dhau. Qhov no hu ua 'anasarca' . Qhov no yog ib qho mob hnyav uas tuaj yeem ua rau tuag taus. Yog li ntawd, nws yog ib qho tseem ceeb heev uas yuav tsum paub txog cov tsos mob.

Vim li cas qhov teeb meem no (PIL) thiaj li tshwm sim?

Tus mob no (PIL) yog tshwm sim los ntawm qhov tsis zoo ntawm cov lymphatic channels ntawm tus menyuam. Cov lymphatic channels no, raws li tau hais ua ntej lawm, yog ib lub system ntawm cov raj uas nqa cov khoom xws li rog los ntawm tus menyuam txoj hnyuv me mus rau lub siab thiab lwm qhov ntawm lub cev.

Qhov teeb meem no ua rau cov hlab ntsha lymph raug thaiv. Tom qab ntawd, lawv puv nrog cov kua lymph, cov hlab ntsha o, thiab thaum kawg lawv tawg, thiab cov khoom hauv cov hlab ntsha ntawd sib sau ua ke hauv tus menyuam txoj hnyuv loj (colon).

Txawm li cas los xij, cov kws kho mob tseem tsis tau paub meej tias yog vim li cas qhov mob no tshwm sim. Qhov ntawd yog qhov teeb meem.

Qhov no puas yog noob caj noob ces? (Puas yog noob caj noob ces ntawm txoj hnyuv lymphangiectasia?)

Tsis tshua muaj neeg tshaj tawm tias muaj ntau tus tswv cuab hauv tib tsev neeg raug tus mob no. Txawm li cas los xij, cov kws tshawb fawb tseem tsis tau paub tseeb tias qhov no puas yog mob caj ces. Tab tom tshawb nrhiav ntxiv txog qhov no.

Yuav kuaj mob li cas thiaj paub tias yog tus kab mob (PIL) no? (Kev kuaj mob)

Feem ntau, thawj qhov uas tus kws kho mob yuav ua yog kuaj xyuas koj tus menyuam lub cev thiab nug koj txog cov tsos mob ntawm koj tus menyuam. Qee zaum, kev kuaj ultrasound ua ntej yug menyuam , ua thaum tus menyuam tseem nyob hauv plab, tuaj yeem qhia cov cim ntawm o (edema) hauv tus menyuam ob txhais ceg, uas tuaj yeem qhia koj qee lub tswv yim ntawm yam uas tab tom tshwm sim.

Tom qab tus me nyuam yug los, tus kws kho mob yuav kuaj xyuas PIL los ntawm kev siv cov cuab yeej tshwj xeeb hu ua endoscope los saib sab hauv tus me nyuam txoj hnyuv. Qhov no yog ib lub raj yas uas muaj lub koob yees duab txuas rau nws. Tus me nyuam yuav raug muab tso pw tsaug zog hauv qab tshuaj loog thaum lub sijhawm kuaj no, yog li lawv yuav tsis hnov ​​​​​​mob. Yog li tsis txhob txhawj.

Thaum lub sijhawm kuaj mob no, tus kws kho mob yuav muab cov ntaub so ntswg me me (hu ua biopsy ) los ntawm ntau qhov chaw ntawm tus menyuam txoj hnyuv. Tom qab ntawd, tus kws kho mob pathologist , tus kws kho mob uas tshwj xeeb hauv kev kuaj cov ntaub so ntswg, saib cov qauv ntaub so ntswg no hauv qab lub tshuab microscope kom paub seb puas muaj qhov o ntawm cov hlab ntsha lymph.

Ntxiv mus, kev kuaj ntshav tuaj yeem txiav txim siab seb muaj pes tsawg cov protein nyob hauv lub cev. Kuj tseem tuaj yeem coj cov qauv quav mus saib seb cov kua dej puas ntws los ntawm cov qog ntshav mus rau hauv txoj hnyuv me.

Cov kev kho mob zoo tshaj plaws rau (PIL) yog dab tsi?

Thaum kho tus kab mob PIL, qhov tseem ceeb tshaj plaws yog hloov tus menyuam txoj kev noj haus. Qhov no yog riam phom tseem ceeb tiv thaiv PIL. Xav txog nws zoo li muab 'qhov ntsaws' los tiv thaiv cov khoom noj tsis txhob xau.

Ntau tus kws kho mob tau sau ntawv kom noj zaub mov uas muaj roj tsawg thiab muaj protein ntau.

Rog nyuaj me ntsis rau kev zom. Yog li nws nyuaj rau koj tus menyuam txoj hnyuv kom nqus cov rog kom zoo. Yog li koj cov zaub mov tshiab yuav suav nrog ib hom rog tshwj xeeb hu ua 'medium-chain triglycerides (MCTs).' Cov no (MCTs) yog ib hom rog uas lub cev yooj yim nqus tau. Tsis tas li ntawd, kev ntxiv cov protein ntau rau koj cov zaub mov tuaj yeem ua rau cov as-ham uas koj lub cev nqus tau ntau tshaj plaws.

Vim tias qee cov as-ham ploj mus lawm, tus kws kho mob kuj tseem yuav pom zoo kom noj cov vitamin thiab minerals kom ntseeg tau tias lub cev ntawm tus menyuam tau txais yam nws xav tau.

Ntxiv rau qhov ntawd, tus kws kho mob kuj tseem yuav sau ntawv kom noj cov tshuaj xws li cov no los pab nrog ntau yam ntawm tus mob (PIL):

• Cov tshuaj diuretics (tseem hu ua cov tshuaj ntsiav dej): Cov no ua haujlwm los ntawm kev txo cov kua dej ntxiv uas sib sau ua ke hauv lub cev vim yog cov protein xau.
• Cov tshuaj Somatostatin analogs (xws li octreotide): Cov tshuaj no pab txo qhov kev xau ntawm cov tshuaj los ntawm lub cev lymphatic.

Lwm cov kev xaiv kho mob:

• Kev Phais Mob: Yog tias lwm yam kev kho mob tsis pab tau, thiab tsis tshua muaj, cov kws kho mob yuav pom zoo kom phais mob kom tshem tawm qhov mob ntawm koj tus menyuam txoj hnyuv.
• Lwm yam kev kho mob uas yuav muaj tau: Kev tshawb nrhiav txog qhov no tseem tab tom ua mus. Muaj ntau yam tshuaj tshiab, xws li sirolimus, tab tom raug sim rau PIL. Cov no yuav pab tau rau qee kis, tab sis lawv tseem tsis tau siv dav.

Yuav ua li cas thiaj li paub tias qhov teeb meem (PIL) yuav zoo li cas?

Raws li tau hais ua ntej lawm, (PIL) tsis yog ib yam kab mob uas kho tau tag nrho. Txawm li cas los xij, cov protein hauv cov ntshav ntawm tus menyuam yuav tsum nce ntxiv hauv ob peb lub lis piam tom qab pib kho. Txawm li cas los xij, tus menyuam yuav tsum noj zaub mov uas tsis muaj roj ntau thiab noj cov tshuaj ntxiv rau nws lub neej.

Txawm hais tias qhov no yog ib qho teeb meem los xij, yog tias tswj tau zoo, tus menyuam yuav muaj peev xwm ua neej nyob li qub. Qhov tseem ceeb tshaj plaws yog ua raws li tus kws kho mob cov lus qhia thiab saib xyuas tus menyuam txoj kev noj haus.

Puas tiv thaiv tau qhov teeb meem (PIL) no?

Vim tias cov kws tshawb fawb tseem tsis tau paub tias dab tsi ua rau muaj tus mob no (PIL), tam sim no tsis muaj txoj hauv kev los tiv thaiv tus mob no.

Thaum twg kuv tus menyuam yuav tsum mus ntsib kws kho mob?

Yog koj pom koj tus menyuam ob txhais ceg, ko taw, lossis ib qho ntawm cov tsos mob ntawm PIL uas tau hais los saum toj no, nws yog qhov zoo tshaj plaws coj koj tus menyuam mus rau kws kho mob tam sim ntawd. Thaum ntxov pom nws, kev kho mob sai dua tuaj yeem pib.

Kuv yuav tsum nug kuv tus menyuam tus kws kho mob li cas?

Yog koj tus menyuam muaj mob PIL, tej zaum koj yuav muaj ntau lo lus nug los nug koj tus kws kho mob. Nov yog qee cov lus nug:

• Kev noj zaub mov twg zoo tshaj plaws rau tus mob no (PIL)?
• Kuv yuav tsum muab cov tshuaj dab tsi rau kuv tus menyuam?
• Kuv ua tau dab tsi ntxiv los tswj kuv tus menyuam cov tsos mob kom zoo dua?
• Qhov teeb meem (PIL) no puas loj heev?
• Kuv yuav tsum ceev faj txog tej teeb meem twg?

Tsis txhob ntshai nug cov lus nug no. Tham txog tej yam koj txhawj xeeb nrog koj tus kws kho mob.

Thaum kawg, tej yam yuav tsum nco ntsoov (Cov Lus Coj Mus Tsev)

Thaum koj thawj zaug pib muaj cov tsos mob ntawm Primary Intestinal Lymphangiectasia, nws yuav nyuaj rau koj thiab koj cov kws kho mob kom nkag siab txog qhov xwm txheej. Nws tuaj yeem yog qhov kev paub tsis meej thiab tsis meej pem heev. Txawm li cas los xij, koj cov kws kho mob tuaj yeem ua haujlwm nrog koj los pab koj txiav txim siab seb dab tsi ua rau nws.

Zoo hmoo, nrog kev noj zaub mov uas tsis muaj roj ntau thiab cov tshuaj noj qab haus huv, koj tus menyuam cov tsos mob tuaj yeem tswj tau raws sijhawm. Nug koj tus menyuam tus kws kho mob seb koj tuaj yeem ua dab tsi ntxiv los pab koj tus menyuam tswj hwm qhov mob no. Koj txoj kev hlub, kev txhawb nqa, thiab kev saib xyuas yog qhov tseem ceeb rau koj tus menyuam thaum lub sijhawm no.

`Primary intestinal lymphangiectasia, PIL, lymphatic obstruction, plab hnyuv kab mob rau cov menyuam yaus, ceg o, tsis muaj protein txaus, plab hnyuv kab mob