Xav txog tias koj tsuas yog zaum xwb thiab koj cov leeg nraub qaum ua rau koj lub cev tsis muaj zog li pob zeb, tsis txav tau. Los yog txawm tias lub suab me me lossis ib tug neeg ntaus koj ua rau koj lub cev tshee thiab koj cov leeg nqaij tshee nrog mob hnyav. Tej zaum cov no tsis yog mob nraub qaum lossis mob nqaij ib txwm muaj. Niaj hnub no peb tab tom tham txog ib qho mob tsis tshua muaj uas ntau tus neeg tsis tau hnov txog, tab sis nws tseem ceeb heev uas yuav tsum paub txog. Qhov no hu ua Stiff Person Syndrome , lossis luv luv SPS.
Hais yooj yim xwb, tus mob Stiff Person Syndrome (SPS) yog dab tsi?
Kab mob Stiff Person Syndrome yog ib yam mob uas tsis tshua muaj neeg mob hauv lub hlwb. Nws cuam tshuam rau peb lub hlwb thiab tus txha caj qaum. Hais yooj yim xwb, nws yog ib yam kab mob autoimmune . Qhov no txhais tau tias lub cev tiv thaiv kab mob, uas yuav tsum tiv thaiv peb lub cev ntawm kab mob, pib tawm tsam peb cov hlwb noj qab haus huv tsis raug. Kab mob no tsis tshua muaj neeg mob uas txawm tias nyob hauv lub tebchaws zoo li Tebchaws Meskas, muaj tsawg dua 5,000 tus neeg mob uas kuaj pom tias muaj kab mob no.
Ib tug neeg uas muaj tus kab mob no thawj zaug yuav hnov qhov kev xav ntawm qhov nruj ntawm cov leeg nqaij ntawm nruab nrab ntawm lub cev, uas yog, thaj tsam lub cev . Raws li lub sijhawm dhau mus, qhov kev nruj no tuaj yeem nthuav mus rau caj npab thiab ceg. Ntxiv rau qhov kev nruj no, cov leeg nqaij mob heev kuj tuaj yeem tshwm sim. Vim yog qhov kev nruj no, lub cev txoj kev sawv cev yuav hloov pauv raws li lub sijhawm, nyo hau rau pem hauv ntej me ntsis thiab saib khoov .
Cov leeg nqaij ntswj no tuaj yeem tshwm sim yam tsis tau npaj tseg lossis yog vim muaj qee yam ua rau. Piv txwv li, lub suab nrov nrov tam sim ntawd, ib tug neeg tsoo koj, lossis kev ntxhov siab heev tuaj yeem ua rau cov leeg ntswj no.
Cov tsos mob tseem ceeb ntawm tus kab mob no yog dab tsi?
Txawm hais tias cov teebmeem ntawm tus kab mob no txawv me ntsis ntawm ib tus neeg mus rau ib tus neeg, muaj qee cov tsos mob uas pom tau. Cia peb saib lawv hauv ib daim ntawv teev.
| Cov tsos mob | Ua li cas rau nws? |
|---|---|
| Cov leeg nqaij tawv heev | Nws pib hauv lub cev thiab tom qab ntawd nthuav mus rau ceg. Txawm hais tias qhov mob no tuaj thiab ploj mus thaum xub thawj, nws yuav ruaj khov mus tas li. |
| Mob Nqaij Mob Qaug Zog | Cov kev tshee hnyo no tuaj yeem kav ntev li ntau teev, thiab qee zaum lawv hnyav heev uas lawv tuaj yeem ua rau pob txha tawg . |
| Kev Nyuaj Siab Taug Kev & Kev Ncua | Cov leeg nqaij tawv ua rau nws nyuaj rau taug kev lossis txav mus los. Koj yuav poob koj qhov sib npaug thaum sawv ntsug lossis taug kev thiab ntog. Qhov kev poob no piav qhia tias "zoo li ib tug ntoo poob" vim tias lub cev tawv tag thiab koj tsis tuaj yeem tswj hwm qhov kev poob. |
| Cov teebmeem ntawm lub hlwb | Kab mob no feem ntau ua rau koj ntxhov siab thiab nyuaj siab. Tej zaum koj yuav ntshai tawm hauv tsev vim koj ntshai tsam qaug dab peg. |
Vim tias cov tsos mob no tshwm sim sai sai, cov neeg mob ntshai mus rau cov chaw pej xeem thiab tsav tsheb. Yog li ntawd, lawv sim maj mam txav deb ntawm zej zog.
Vim li cas ho muaj tej yam zoo li no tshwm sim?
Cov kws kho mob tseem tsis tau pom qhov ua rau qhov no, tab sis lub tswv yim tseem ceeb yog tias nws yog teeb meem nrog peb lub cev tiv thaiv kab mob.
Muaj ib qho neurotransmitter hu ua GABA uas pab tswj kev txav ntawm peb cov leeg. Xav txog nws zoo li 'kev hloov' uas xa lub teeb liab mus rau peb cov leeg kom 'so'. Ib qho enzyme hu ua 'glutamic acid decarboxylase (GAD)' yog qhov tseem ceeb rau kev ua GABA no. Hauv feem ntau cov neeg mob SPS, lub cev tsim cov tshuaj tiv thaiv kab mob uas tawm tsam cov enzyme GAD no. Thaum cov tshuaj tiv thaiv kab mob no mus thiab rhuav tshem cov enzyme GAD, GABA tsis raug tsim tawm kom zoo. Tom qab ntawd cov leeg tsis tau txais cov lus kom 'so' kom zoo, thiab lawv pheej nruj thiab co tas li.
Cov neeg uas muaj SPS kuj muaj feem yuav muaj lwm yam kab mob autoimmune ntau dua.
- Vitiligo - cov pob dawb ntawm daim tawv nqaij
- Kab mob ntshav qab zib hom 1
- Pernicious anemia - Kab mob ntshav tsis txaus uas tshwm sim los ntawm qhov tsis txaus vitamin B12
- Thyroiditis (kev kis kab mob ntawm cov thyroid caj pas)
Tsis tas li ntawd xwb, cov neeg uas muaj qee hom mob qog noj ntshav muaj feem yuav mob SPS (piv txwv li mob ntsws, mob raum, mob mis, mob qog thyroid, mob qog plab hnyuv).
Tus kws kho mob yuav kuaj mob no li cas kom meej?
Cov tsos mob ntawm SPS feem ntau tshwm sim ntawm hnub nyoog 30 thiab 60 xyoo. Cov poj niam muaj feem yuav mob tus kab mob no ob npaug ntau dua li cov txiv neej.
Vim tias cov tsos mob ntawm tus kab mob no zoo ib yam li lwm cov kab mob uas feem ntau pom, SPS feem ntau raug nkag siab yuam kev tias yog lwm yam kab mob.
- Kab mob Multiple Sclerosis
- Kab mob Parkinson
- Fibromyalgia
- Kev mob nqaij ntshiv dystrophy
- Kev ntxhov siab
Vim li no, nws yuav siv sijhawm me ntsis kom tau txais kev kuaj mob tseeb. Koj tus kws kho mob yuav xub kuaj koj, nug txog koj keeb kwm kev mob nkeeg, thiab tom qab ntawd yuav kom kuaj ntau zaus kom paub tseeb tias puas muaj lwm yam mob.
1. Kuaj ntshav rau cov tshuaj tiv thaiv kab mob GAD: Qhov no yog qhov kev kuaj tseem ceeb tshaj plaws. Cov tshuaj tiv thaiv kab mob GAD no muaj ntau heev nyob rau hauv cov ntshav ntawm 60% - 80% ntawm cov neeg mob SPS.
2. Kev kuaj mob hluav taws xob (EMG): Qhov no ntsuas qhov ua haujlwm hluav taws xob ntawm koj cov leeg thaum lawv so thiab thaum lawv nruj. Cov leeg ntawm cov neeg mob SPS tseem ua haujlwm txawm tias thaum lawv so.
Cov kev kho mob rau qhov no yog dab tsi?
Thawj qhov uas yuav tsum hais yog tias tseem tsis tau muaj kev kho rau tus kab mob no . Txawm li cas los xij, muaj ntau txoj kev kho mob zoo uas tuaj yeem pab tswj cov tsos mob thiab pab koj txuas ntxiv koj cov dej num txhua hnub. Txoj kev npaj kho mob yog tsim rau txhua tus neeg mob, raws li lawv cov tsos mob.
Koj tus kws kho mob yuav sim cov tshuaj sib txawv los tswj qhov mob thiab cov leeg nqaij ntswj. Tsis yog txhua tus neeg lub cev teb rau cov tshuaj tib yam, yog li nws yuav siv sijhawm me ntsis los nrhiav cov tshuaj sib xyaw ua ke rau koj.
- Rau cov leeg nqaij tawv: Benzodiazepines (piv txwv li diazepam, clonazepam) thiab baclofen feem ntau yog siv.
- Rau qhov mob: Cov tshuaj loog mob thiab qee cov tshuaj tiv thaiv kev qaug dab peg tuaj yeem pab tswj qhov mob.
- Kev kho mob Immunoglobulin hauv cov hlab ntsha (IVIG): Qhov no suav nrog kev muab cov tshuaj tua kab mob uas tau los ntawm cov neeg noj qab haus huv hauv cov hlab ntsha. Qhov no kuj tau pom tias yog kev kho mob zoo rau kev tswj cov tsos mob SPS.
Ntxiv nrog rau kev siv tshuaj, kev kho lub cev, kev tawm dag zog ncab, kev zaws, thiab kev siv koob txhaj tshuajTej yam zoo li no yuav pab txo qhov mob thiab ua kom cov leeg nqaij ua haujlwm tau zoo.
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Kab mob Stiff Person Syndrome (SPS) tsis yog tsuas yog mob nqaij xwb, nws yog ib qho kab mob autoimmune neurological uas tsis tshua muaj neeg pom.
- Cov tsos mob tseem ceeb yog cov leeg nqaij tawv heev thiab mob ntswj pib hauv thaj tsam lub cev.
- Vim tias qhov no feem ntau tsis meej pem nrog lwm yam kab mob, kev pab los ntawm tus kws kho mob uas muaj kev paub dhau los yog qhov tseem ceeb rau kev kuaj mob kom raug.
- Txawm hais tias tus kab mob no tsis tuaj yeem kho tau tag nrho los xij, muaj cov kev kho mob zoo uas tuaj yeem pab koj tswj koj cov tsos mob thiab ua neej nyob li qub.
- Yog koj lossis ib tug neeg koj paub muaj cov tsos mob no, tsis txhob tsis quav ntsej lawv, hais tias, "Nws tsuas yog mob nqaij xwb." Mus ntsib koj tus kws kho mob tam sim ntawd thiab nrhiav kev pab kho mob.











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus