Yu de wɔri bɔt aw yu smɔl pikin in fes shep? Lɛ wi tɔk bɔt Binder Syndrome!

We dɛn bɔn yu smɔl pikin, yu notis se dɛn fes chenj smɔl? Sɔntɛnde, dɛn nos kin luk flat smɔl, ɔ dɛn ɔp lip nɔ kin de na di rayt ples. Na nɔmal tin fɔ mek mama ɔ papa fred smɔl we dɛn si sɔntin lɛk dis. Bɔt nɔr wɔri, tide wi go tɔk bɔt wan sik wae de sho di sem kayn sik, bɔt nɔr kin bɔrku, wae dɛn kɔl Binder Syndrome.

Wetin na di Binder Syndrome? Fɔ tɔk am simpul wan...

Binder syndrome na wan rare , congenital condition wae kin apin wae dɛn bɔn am. di bon dεm we de na di midul pat na di fes, spεshal wan di nos εn di כp jaw, nכ de divεlכp fayn. I tan lɛk di we aw dɛn nɔ de bil sɔm wɔl dɛn na os fayn fayn wan. Dis kin mek di pikin in fes luk difrɛn smɔl.

Tink bɔt am, wi nos ɛn di ɔpa lip shep bikɔs ɔf di bon dɛn we de ɔnda am. So we dɛn bon dɛn de stɔp fɔ gro, di we aw dɛn de luk kin chenj. Sɔm pikin dɛn kin gɛt prɔblɛm fɔ blo bikɔs ɔf dis sik, ɛn dɛn kin gɛt prɔblɛm bak fɔ it, mɔ we dɛn de gi dɛn bɛlɛ . Bɔt di gud nyus na dat, tritmɛnt de fɔ dis. כltεm, we di pikin big sכmtεm, dat na we dεn rich di tεm we dεn rich 15-19 ia), dεn bon dεm ya kin rialayn εn di fכs fכ luk bak tru di fes εn jaw כpεrayshכn (`maxillofacial surgery`) .

Ɔda nem dɛn de fɔ Binder Syndrome?

Yɛs, sɔntɛnde dɔktɔ dɛn kin yuz ɔda nem fɔ dis sik. I fayn fɔ no bikɔs yu kin yɛri dɛn nem ya bak:

• Binder phenotype - Dis na ɔda nem fɔ Binder syndrome.
• Binder tayp nasomaksila displasia
• Displasia na di maksilɔnasal
• Nasomaxillary haypoplasia we pɔsin kin gɛt

Pan ɔl we dɛn nem dɛn ya kin tan lɛk se dɛn kɔmplikt smɔl, dɛn ɔl min di sem tin.

Aw kɔmɔn dis sik we dɛn kɔl Binder Syndrome?

Dis na rili wan sik we nɔ kin apin so ɔltɛm . Sɔm ripɔt dɛn se dis sik kin apin to lɛs wan pan ɛvri 10,000 pikin dɛn we dɛn jɔs bɔn. So nɔ mek yu fred fɔ dis. Bɔt, pan ɔl we i nɔ kin bɔku, i impɔtant fɔ no bɔt am.

Wetin na di sayn dɛm fɔ Binder Syndrome?

di men tin we de sho dis sik na we di fes nכ de gro . Dis kin mek di pikin in fes sho dɛn chenj ya:

• Di nos kin flat, ɛn di ɔp lip kin flat . I kin tan lɛk se di nos dɔn sink insay.
• Di jaw we de dɔŋ de kɔmɔt bifo.I tan lɛk dis. dis apinεns de apin biכs di כp jaw de go insay εn di lכw jaw de kam fכd.
• di כp εn lכw tit dεm nכ de fit tכgeda fayn fayn wan (`malocclusion`) . Dis kin mek i nɔ izi fɔ yu we yu de it ɛn tɔk.
• Di nos dɛn kin gɛt triangul ɔ kres shep .

Dis na di sayn dɛm wae kin kam pan pɔrsin. Bɔt apat frɔm dat, yu kin si dɛn sik ya bak pan sɔm kayn tin dɛn we nɔ kin apin so ɔltɛm :

• Klɛft palata .
• Di at we dɛn bɔn wit .
• Di we aw pɔsin kin yɛri fayn .
• Intɛlektual disabiliti .
• Spinal malfɔmeshɔn dɛn .
• Strabismus ɔ yay we krɔs .

Nɔto ɔl pikin dɛn go gɛt ɔl dɛn sik ya. Sɔm pikin dɛn kin jɔs gɛt di men sayn dɛn.

Wetin mek di Binder Syndrome kin apin? Wetin na di tin dɛn we kin mek i apin?

Fɔ tɔk tru, masta sabi bukman dɛn stil nɔ dɔn no di rayt tin we kin mek dis apin . Bɔrku tɛm, pikin dɛn kin gɛt dis sik fɔ no rizin.

Bɔt bikɔs bɔku pikin dɛn na sɔm famili dɛn gɛt dis sik, dɛn kin tink se sɔm tin dɛn kin de we dɛn gɛt frɔm dɛn jɛnɛtiks, dat na sɔntin we kin mek dɛn gɛt dis sik . Bɔt dɛn nɔ dɔn pruv dis klia wan yet.

Apat frɔm dat, sɔm pipul dɛn we de stɔdi bɔt dis biliv se bɔku tin dɛn we de apin na di envayrɔmɛnt kin ɛp bak. Dɛn kayn tin ya na:

• Di we aw di mama de drink rɔm we i gɛt bɛlɛ.
• Fɔ gɛt sɔm mɛrɛsin dɛn we yu gɛt bɛlɛ. εgzampl dεm na di anti-εpileptik fεnitoin (Dilantin®, Phenytek®) εn di blɔd tina wכfarin (Coumadin®, Jantoven®). (Dɛn fɔ tek dɛn mɛrɛsin ya ɔnda dɔktɔ in sɔpɔtishɔn if nid de, bɔt dɛn fɔ tek spɛshal kia we uman gɛt bɛlɛ.)
• Vitamin K we nɔ de we i gɛt bɛlɛ.
• Trauma na di ed ɔ fes we dɛn de bɔn pikin.

Dis na di risk factor dɛm wae dɛn dɔn no naw.

Aw dɔktɔ dɛn kin no se pɔsin gɛt di sik we dɛn kɔl Binder Syndrome?

Dɔktɔ dɛn kin tink se dis sik fɔs bay we dɛn de luk di pikin in fes . Dɔn fɔ mek dɛn no se dɛn nɔ biliv se dɛn de tink, dɛn kin du spɛshal tɛst dɛn we go ebul fɔ si klia wan di bon dɛn we de na di fes . Dɛn kɔl dɛn tin ya:

• CT skan dɛn we dɛn kin du
• MRI Skan (`MRI`) .
• Ultrasound skan (`ultrasound`) .

tru dεn skan dεm ya, wi kin kכrekt fכ no εni divεlכpmεnt dεfichεns na di fes bon dεm.

Wetin na di tritmɛnt dɛm fɔ Binder Syndrome?

Di tritmɛnt fɔ dis kin difrɛn frɔm wan pikin to ɔda pikin, ɛn i kin dipen bak pan aw di sik kin tranga.I kin difrɛn. Tu men we dɛn de fɔ trit pɔsin:

1. Ɔtodɔnt kia:

• dis involv fכ put waya (`braces`) na di mכt fכ alayne di jaw εn di tit dεm fayn fayn wan .
• Sɔntɛnde, if di sik nɔr tu tranga, dis tritmɛnt fɔ dɛn tit nɔmɔ kin du fɔ yu.
• Ɔda tɛm dɛn, dɛn kin nid fɔ du dis tritmɛnt bifo ɔ afta dɛn du di ɔpreshɔn.

2. Ɔpreshɔn:

• Dis na di men we fɔ trit pɔsin. Wan kraniofacial surgeon (dɔktɔ we spɛshal pan di skel ɛn fes) kin du dɛn ɔpreshɔn ya.
• insay dis, dεn kin chenj di shep fכ di nos bay we dεn de yuz bon, katilej, כ sεntetik mεtirial we dεn tek frכm di pikin in כwn bכdi . Dɛn kin kɔl dis bak raynoplasti .
• Dɔn bak, dɛn kin du wan kayn ɔpreshɔn we dɛn kɔl Le Fort I ɔ II ɔsteotomy fɔ mek di ɔpa jaw go na di rayt pozishɔn. Dɛn ɔpreshɔn ya na sɔm kɔmpleks ɔpreshɔn dɛn, bɔt dɔktɔ dɛn we gɛt ɛkspiriɛns kin du dɛn fayn fayn wan.
• Dɔktɔ dɛn kin se i fɔ wet te di pikin in fes bon dɛn dɔn stɔp fɔ gro kpatakpata bifo dɛn du dis ɔpreshɔn, we kin apin bitwin 15 ɛn 19. Dis na bikɔs if dɛn du am bifo da tɛm de, prɔblɛm kin kam bak as di bon dɛn de kɔntinyu fɔ gro.

Impɔtant: Nɔto ɔl pikin dɛn go nid ɔl tu di tritmɛnt dɛn. Sɔm pikin dɛn kin nid fɔ gɛt wan tritmɛnt nɔmɔ. Na di mɛdikal tim go disayd dis afta dɛn dɔn chɛk di pikin.

Dɛn kin ebul fɔ avɔyd dis sik wae dɛn kɔl Binder Syndrome?

Bikɔs wi nɔ no di rayt tin we kin mek dis apin, i nɔ pɔsibul fɔ gi garanti se dɛn go ebul fɔ avɔyd am kpatakpata .

Bɔt if yu gɛt bɛlɛ, yu kin ridyus yu risk fɔ gɛt dis sik to sɔm mak bay we yu nɔ de pan sɔm pan di tin dɛn we de apin na di envayrɔmɛnt we wi bin dɔn tɔk bɔt. Yu kin tɔk to yu dɔktɔ bɔt dis:

• Di sef fɔ di mɛrɛsin dɛn we yu gɛt bɛlɛ , mɔ di phenytoin ɛn warfarin (nɔ tek ɛni mɛrɛsin pas dɔktɔ tɛl yu, ɛn if dɛn gi yu, tɔk to yu dɔktɔ bɔt am).
• Bɔt di vaytamɛn dɛn we nɔ gɛt bɛtɛ vaytamɛn, mɔ we pɔsin nɔ gɛt vaytamɛn K . I rili impɔtant fɔ gɛt di rayt it we yu gɛt bɛlɛ.

Wetin na de luk fɔ pikin we gɛt Binder Syndrome?

Dis na di bɛst nyus. Jɛnɛral wan fayn tin de fɔ si dis sityueshɔn .

Bɔku pikin dɛn nɔ nid ɛni ɔda tritmɛnt afta dɛn dɔn du raynoplasty. Dɛn kin ebul fɔ blo nɔmal wan, it nɔmal wan, ɛn dɛn fes kin fayn afta dɛn dɔn du dɛn ɔpreshɔn.I pɔsibul. So natin nɔ de fɔ wɔri bɔt, bɔt di tin we impɔtant pas ɔl na fɔ go to dɔktɔ kwik kwik wan.

Us kwɛstyɔn dɛn a fɔ aks mi dɔktɔ?

If yu kam fɔ no se yu ɔ yu pikin gɛt Binder Syndrome, yu kin aks yu dɔktɔ kwɛstyɔn dɛn lɛk dis. Dɛn tin ya go ɛp yu fɔ ɔndastand di sik:

• "Dɔkta, wetin kin bi di tin we go mek mi pikin gɛt di sik? "
• " Us tɛst dɛn kin du fɔ no dis Binder Syndrome kɔndishɔn kɔrɛkt wan? "
• " Wetin na di tritmɛnt opshɔn dɛm fɔ dis? Wetin bɛtɛ fɔ mi pikin?"
• " Wetin na di chans fɔ nid tritmɛnt bak leta na layf? "
• "If a get oda pikin, wetin bi di chans se im go get dis kondishon tu? "

Apat frɔm dɛn kwɛstyɔn ya, aks yu dɔktɔ ɛnitin we yu gɛt na yu maynd.

Us ɔda tin dɛn wae gɛt di sem kayn sayn wae gɛt di sem kayn sik wae de kam wit Binder Syndrome?

כda kכndyushכn dεm de we de afekt di fes bon dεm we de gro εn i de luk lεk di Binder syndrome. Dɔktɔ dɛn bak kin wɔri bɔt dɛn tin ya. Sɔm ɛgzampul dɛn na:

• Akrodaysostosis we dɛn kɔl
• Di sik we dɛn kɔl Apert syndrome
• Chondrodysplasia punctata, rayzomɛlik tayp (CDPR) .
• Fetal warfarin syndrome (na wan kכndyushכn we kin kכmכt we i de gεt warfarin we i bεlε) .
• Keutel sindrom we gɛt di sik
• Stiklɔr sindrom

Jɔs no bɔt dɛn nem ya. Dɔktɔ dɛn go disayd ustɛm yu pikin gɛt di sik.

Fɔ dɔn, tin dɛn fɔ mɛmba (Take-Home Message) .

Okay, so lɛ wi sɔma wetin wi dɔn tɔk bɔt:

• Binder Syndrome na wan sik we nɔ kin apin so ɔltɛm, we dɛn bɔn wit .
• Dis kin mek di bon dɛn we de gro na di midul pat na di fes, mɔ di nos ɛn di ɔpa jaw . dis kin mek tin dεm lεk wan flat nos εn wan lכw jaw we de kכmכt.
• Wi nɔ no di rayt tin we kin mek dis apin , bɔt di tin dɛn we kin mek pɔsin gɛt jɛnɛtiks ɛn di tin dɛn we de apin na di say we i de, kin ɛp fɔ du sɔntin.
• Dɛn kin trit dis sik fayn fayn wan wit ɔtodɔnt tritmɛnt ɛn/ɔ ɔpreshɔn .
• Bɔrku pikin dɛn kin gɛt bɔrku gud rizulyt afta dɛn dɔn trit dɛn ɛn dɛn kin liv nɔrmal layf.

If yu gɛt ɛnitin fɔ wɔri ɔ wɔri bɔt aw yu pikin in fes tan, duya go to dɔktɔ we sabi du di wok kwik kwik wan . Di tin we impɔtant pas ɔl na fɔ nɔ panik, bɔt fɔ gɛt di rayt infɔmeshɔn ɛn gayd. Dɔktɔ dɛn de fɔ ɛp yu.

A op se dis infɔmeshɔn go yusful to yu. A de wish yu ɛn yu famili gud wɛlbɔdi!

` Binder Syndrome, Binder Syndrome, fes difכmiti, sik dεm we dεn bכn wit, pikin dεm hεlth, maksilofacial כpεrayshכn, kraniofacial כpεrayshכn