Yu no bɔt wan sik we nɔ kin apin so ɔltɛm na yu at: Ebstein’s Anomaly?

Wi at na ɔgan we rili wɔndaful, nɔto so? Bɔt sɔmtɛm, bikɔs ɔf sɔm chenj dɛn we kin apin we dɛn bɔn am, smɔl prɔblɛm kin de wit di we aw di at de wok. Tide wi go tɔk bɔt wan kayn at sik we nɔ kin bɔku we nɔto bɔku pipul dɛn gɛt. Dɛn kɔl dis Ebstein’s Anomaly. Pan ɔl we di nem kin tan lɛk se i de mek wi fred smɔl, lɛ wi ɔndastand am simpul wan.

So wetin na Ebstein in Anomaly?

Fɔ tɔk am simpul wan, Ebstein’s Anomaly na wan at sik we kin de we dɛn bɔn am . dεn kכl am bak "congenital," we min se i de de we dεn bכn am. "anomaly" min sɔntin we nɔ kɔmɔn ɔ we dɛn nɔ bin de ɛkspɛkt. insay dis kכndyushכn , di trikuspid valv, we na wan pan di fכ valv dεm na wi at, de mεntal afekt.

Tink bɔt am, tin dɛn de lɛk domɔt dɛn bitwin di chɛmba dɛn na wi at we de ɛp blɔd fɔ flɔ na wan say nɔmɔ. Na dat wi de kɔl valv. Di trikuspid valv na wan pan dɛn. Wan Jaman dɔktɔ we nem Wilhelm Ebstein bin tɔk bɔt dis sik fɔ di fɔstɛm insay 1866. Na dat mek dɛn gi am in nem.

Wetin kin apin to di trikuspid valv na Ebstein anomaly?

yu kin si tu men chenj dεm na di trikuspid valv fכ pכsin we gεt dis kכndyushכn:

1. di valv nכ fכm fayn (difכm): di lif dεm, di flap dεm we de opin εn klos wit εvri bit na di at, nכ de shep nכmal wan. Sɔntɛnde, dɛn kin ivin stik na di wɔl na di at.

2. Di say we di valv de difrɛn: Dis valv de dɔŋ pas aw i fɔ de.

Dɛn prɔblɛm ya kin mek di valv nɔ kin lɔk fayn, we kin mek di blɔd lik bak insay di ɔpa rayt atria. Dɔktɔ dɛn kin kɔl dis rigurgitation. As blɔd de kɔntinyu fɔ flɔ bak, di rayt atria de big smɔl smɔl. As tɛm de go, di rayt say na di at kin wik ɛn mek di at nɔ wok fayn . Dis nɔto at atak, bɔt na we di at nɔ ebul fɔ pɔmp blɔd fayn fayn wan.

Udat dis tin kin afɛkt mɔ?

Bɔrku pipul dɛm wae gɛt Ebstein’s Anomaly gɛt ɔda kayn hat sik. Na lɛk 94 pasɛnt pan di pipul dɛm wae gɛt Ebstein’s Anomaly gɛt ol na di wɔl bitwin di tu ɔpa chɛmba dɛm na di at (atria). Dɛn kɔl dis Atrial Sɛptal Difɛkt (ASD) ɔ Patent Foramen Ovale (PFO).

כlso, yu kin si sכm dεfεkt dεm na di כda valv dεm na di at εn di lεft sayd chεmba dεm.

Aw kɔmɔn tin na Ebstein in Anomaly?

Dis na tin we nɔ kin apin so ɔltɛm . I kin afɛkt lɛk wan pan ɛvri tu ɔndrɛd tawzin pikin dɛn we dɛn jɔs bɔn. pan di hat sik dεm we dεn kin bכn, dεn kin si am pan less dan 1%.

Wetin na di sayn dɛm fɔ Ebstein’s Anomaly?

di sayn dεm fכ dis kכndyushכn kin difrεn frכm pכsin to pכsin, i kin kכmכt frכm sכmtεm to siriכs dipכnt pan di digri we di valv de fכm.

If di sik rili bad, di sayn dɛm kin apin we dɛn bɔn am ɔ insay di fɔs mɔnt dɛm we i de liv . Insay yɔŋ bebi dɛn, sɔntɛnde:

• di skin kin tכn blu biכs di כksijεn nכ de na di bכdi (cyanosis) .
• Di fɔs sayn dɛm fɔ sho se yu at pwɛl kin bi:
• Fɔ blo kwik kwik wan.
• I nɔ kin izi fɔ yu fɔ blo.
• We yu de gɛt bɔku bɔku bɔdi na tin we kin apin we yu de gɛt bɔku bɔku bɔdi.
• Swel (edema) na di leg, bɛlɛ, ɔ rawnd di yay.

Imajin, if pikin we dɛn jɔs bɔn kɔntinyu fɔ tɔn blu ɛn i nɔ izi fɔ blo, dɔktɔ dɛn go dawt if dis kayn sik de.

If de sik nɔr kin pasmak, yu nɔr kin gɛt ɛni sayn at ɔl, ɔr de sayn kin kam wae yu dɔn big. We di sayn dɛn kin sho pan big pipul dɛn, yu kin notis tin dɛn lɛk:

• Blu di kɔlɔ we di skin kin chenj (espɛshali di lip ɛn finga nel).
• Di at we nɔ de bit ɔltɛm (arithmia).
• If at pwɛl hat:
• Chɛst de pen.
• Diziz ɔ fɔdɔm.
• Fɔ fil taya ɔltɛm.
• I nɔ kin izi fɔ yu fɔ blo, mɔ we yu de du ɛksɛsayz.
• Di leg ɔ bɛlɛ kin swel.

Wetin kin mek pɔsin gɛt Ebstein’s Anomaly?

Fɔ tɔk tru, dɔktɔ dɛn stil nɔ ebul fɔ tɔk klia wan wetin mek dis sik kin apin . dεn biliv se i de kכz fכ wan kכmbaynshכn fכ jεnεtik (i.e. inhεrit) εn invayroment fכktכ dεm. Bɔt dɛn nɔ dɔn no fɔ tru wetin na dɛn tin dɛn de.

Aw dɛn kin no dis sik? (Diagnosis) .

We yu go to dɔktɔ, dɛn go aks yu bɔt yu sik ɛn chɛk yu puls rit ɛn blɔd prɛshɔn. Dɛn kin du sɔm tɛst dɛn bak fɔ no aw yu at de wok fayn, lɛk:

• Imej fɔ di kadyak:
• Chɛst X-ray: Dis kin chɛk fɔ si if di at dɔn big.
• Cardiac MRI: Dis kin mek klia, mɔ ditayli pikchɔ dɛn bɔt di at in valv ɛn chɛmba dɛn.
• Echocardiogram: Dis tan lɛk ɔltra saund fɔ di at. I de mek di dɔktɔ si di shep we di at in valv ɛn chɛmba dɛn gɛt, ɛn aw dɛn de wok. i kin sho klia wan di valv abnכmaliti dεm na Ebstein anomaly.
• Ilɛktrokardiogram (ECG): Dis de mɛzhɔ di ilɛktrik wok we di at de du. I kin no ɛni at bit we nɔ de bit ɔltɛm (arrhythmias).
• Ɛksesaiz strɛs tɛst:Insay dis, dɛn go put yu pan tredmil ɔ bayk ɛn dɛn go tek ECG. Dɛn kin du dis fɔ si aw yu at de wok we yu strɛs.
• Holter monitor: Dis na smɔl tin we yu kin wɛr fɔ 24 to 48 awa. Insay dis tɛm, i kin rayt ɛvri at bit. Dis kin gi yu dɔktɔ gud aidia bɔt aw yu at rit ɛn ritm de chenj ɔl di de.

Aw dɛn kin trit di sik we dɛn kɔl Ebstein’s Anomaly?

Di tritmɛnt dipen pan aw yu sik dɛn kin tranga.

• If di sayn dɛm nɔr de ɔr nɔr de: Yu dɔktɔ go de wach yu at ɔltɛm fɔ si if ɛni chenj de. Sɔntɛm yu nɔ go nid ɛni tritmɛnt.
• If yu gɛt sayn dɛn we de sho se yu at nɔ de wok fayn ɔ yu at nɔ de bit ɔltɛm (arrhythmia):
• Dɛn kin gi mɛrɛsin fɔ kɔntrol dɛn sik dɛn de.
• If yu at dɔn big ɔ yu gɛt istri we yu at nɔ de bit ɔltɛm, dɛn kin aks yu fɔ lɛ yu nɔ du bɔku tin fɔ du . Yu fɔ fala yu dɔktɔ in instrɔkshɔn dɛn di rayt we.

• If di sayn dɛn rili bad: Tricuspid valv ɔpreshɔn na di bɛst opshɔn. dis kin mek di valv wok fayn fכ lכng tεm.
• Fɔ tray fɔ ripɛnt am yuz yu yon valv tisu na di tritmɛnt we fit pas ɔl.
• If di damej tu bad fɔ mek dɛn ebul fɔ mek am, dɛn kin nid fɔ chenj di valv . dis kin bi wit mεkanikal valv כ bayolojikal tisu valv. Bɔt if dɛn put mɛkanikal valv, yu go nid fɔ tek mɛrɛsin we de mek yu blɔd tan lɛk yu layf.

Sɔntɛnde dɛn kin du ɔda ɔpreshɔn fɔ di at di sem tɛm we dɛn kin du trikuspid valv ɔpreshɔn. fכ egzampl, fכ klos di ol bitwin di כp chεmba dεm na di at (ASD ripa) כ trit di at bit we nכ de bit (tritmεnt fכ aritmia). Di tritmɛnt fɔ di at bit we nɔ de bit ɔltɛm na fɔ pul kateshɔn ɔ fɔ put pesmɛka insay pɔsin in bɔdi.

Na smɔl tɛm nɔmɔ, i kin nid fɔ transplant at if ɔl di ɔda tritmɛnt dɛn nɔ wok.

Yu tink se dɛn kin ebul fɔ stɔp Ebstein in Anomaly?

Bikɔs dɔktɔ dɛn nɔ no di rayt we aw dis sik kin apin, naw, no we nɔ de fɔ mek i nɔ gɛt am .

Aw layf go go bifo wit dis sityueshɔn? (Autluk) .

De luk fɔ pipul dɛm wae gɛt Ebstein’s Anomaly kin difrɛn frɔm pɔrsin to ɔda pɔrsin.Sɔm bebi dɛn nɔ kin liv dis sik. Bɔt ɔda pipul dɛn kin liv lɔng, nɔmal layf ɛn dɛn nɔ kin gɛt ɛni tritmɛnt. In jɛnɛral, de lukin-grɔn kin bɛtɛ fɔ di wan dɛm wae gɛt di kayn sik wae nɔr kin pasmak.

Ivin afta dɛn dɔn du di ɔpreshɔn, sɔm at prɔblɛm dɛn kin kɔntinyu fɔ de. Stɔdi dɔn sho se di layf we pɔsin kin liv kin ridyus smɔl afta dɛn dɔn du di ɔpreshɔn. Wan stɔdi (we bin luk pan pipul dɛm wae gɛt ɔpreshɔn bitwin 1972 ɛn 2006) sho se 20 ia afta dɛn du ɔpreshɔn, 65% pan pipul dɛm bin dɔn go ɔspitul fɔ at sik at le wan tɛm, ɛn 76% bin stil de alayv.

Bɔt dis impɔtant: Bikɔs ɔf di advans we fɔ du ɔpreshɔn ɛn di kia we dɛn de kia fɔ di wan dɛn we de du ɔpreshɔn tide, i go mɔs bi se di tin dɛn we go apin to di wan dɛn we dɛn de du ɔpreshɔn tide go bɛtɛ pasmak.

Ustɛm a fɔ go to dɔktɔ?

If yu gɛt Ebstein’s Anomaly, yu fɔ tɛl yu dɔktɔ wantɛm wantɛm if yu sik de wɔs ɔ if yu gɛt nyu sik . Una fɔ no bɔt dɛn tin ya:

• If di skin de blush mɔ ɛn mɔ.
• If yu fil se yu bɔdi de lɔs trɛnk.
• If yu fil se yu bɔdi de ful-ɔp wit wata (swelling).
• If di at bit fast.

Di mɛsej we impɔtant pas ɔl fɔ kɛr go na os

Ebstein’s Anomaly na wan sik wae nɔr kin bɔrku, wae dɛn kin bɔn wit at. Di tin dɛm wae dis sik kin du kin difrɛn frɔm pɔrsin to ɔda pɔrsin. If dɛn no se i gɛt di sik we i smɔl, bɔku tɛm di sik nɔ kin izi. Bɔrku tɛm, di wan dɛm wae kin liv te dɛn big kin gɛt dis sik wae nɔr kin pasmak. Bɔt dɛn kin gɛt prɔblɛm dɛn bak lɛk at bit we nɔ de bit ɔltɛm (arrhythmia) ɛn at we nɔ de wok fayn as tɛm de go. If dis apin, dɛn kin nid fɔ du ɔpreshɔn fɔ mek ɔ chenj di trikuspid valv, ɛn fɔ trit ɔda at prɔblɛm dɛn we gɛt fɔ du wit am.

Di tin we impɔtant pas ɔl na fɔ de chɛk yu at ɔltɛm fɔ no if yu at chenj ɛn gɛt fayn tritmɛnt kwik kwik wan if nid de. Nɔ wɔri, dɔktɔ dɛn de fɔ ɛp yu.

` Ebstein in Anomaly, At sik, Tricuspid Valve, Kɔnjɛnital At Difɛkt, At Fɛil, At Ɔpreshɔn, Simptom dɛm