Yu dɔn ɛva yɛri se sɔm kayn at prɔblɛm dɛn we dɛn kin bɔn wit kin mek yu gɛt siriɔs prɔblɛm dɛn leta na yu layf? Wan pan dɛn kayn kɔmpleks sik ya na di sik we dɛn kɔl Eisenmenger syndrome. Di nem kin bi nyu tin to yu, bɔt i impɔtant fɔ no bɔt am, mɔ if pɔsin na yu famili gɛt at sik we dɛn bɔn wit. Lɛ wi tɔk bɔt dis smɔl smɔl, bikɔs fɔ no dis sik kwik kwik wan ɛn fɔ no bɔt dis sik rili impɔtant.
Wetin rili na di sik we dɛn kɔl Eisenmenger Syndrome?
Fɔ tɔk am simpul wan, Eisenmenger Syndrome na wan sik we kin apin we tumɔs blɔd de pas na di blɔd vesel (arterie) we de kɛr blɔd frɔm yu at to yu lɔng. Tink bɔt am lɛk wata we de flɔ tru pɔt tu kwik. Dis kin mek yu gɛt ay blɔd prɛshɔn na di blɔd vesel dɛn na yu lɔng ɛn na di rayt say na yu at, we na wan sik we dɛn kɔl Pulmonary Hypertension . I tan lɛk se yu de tray fɔ push bɔku bɔku wata tru smɔl paip, ɛn dis kin mek bɔku prɛshɔn insay di paip.
pan tap dat, bכdi de bigin fכ fכlכ fayn fayn wan bitwin di lεft εn rayt say na di at (`blɔd shunting`). dis min se biכs fכ wan abnכmal kכnεkshכn (lεk wan ol we de we dεn bכn am), bכdi we de kכmכt na di lεft say na di at (we gεt כksijεn) de fכlכ to di rayt say (lεk כksijεn we nכ gεt bכku). As tɛm de go, dis sik kin chenj bak, we min se blɔd we nɔ gɛt bɛtɛ ɔksijɛn kin kɔmɔt na di rayt say to di lɛft say.
Dis sik we dɛn kɔl Eisenmenger syndrome kin apin bɔku tɛm we dɛn nɔ trit wan ɔ mɔ pan di at prɔblɛm dɛn we dɛn bɔn wit ɔ we dɛn nɔ no se i gɛt am . If dis sik de fɔ lɔng tɛm, i kin mek di lɔng dɛn pwɛl fɔ ɔltɛm ɛn ɔda prɔblɛm dɛn we kin mek pɔsin in layf de pan denja. Na dat mek dis na tin we pɔsin fɔ pe atɛnshɔn to gud gud wan.
Udat kin gɛt dis sik?
Eisenmenger syndrome na wan kכndyushכn we kin apin pan pikin dεm εn yכng pipul dεm we dεn bכn wit Ventricular Septal Defect (VSD), we na wan ol na di wכl bitwin di tu lכw pכmp chεmba dεm na di at (di lεft εn rayt vεntrikl).
Dɔn bak, Eisenmenger syndrome kin apin we dɛn nɔ trit sɔm ɔda at prɔblɛm dɛn we dɛn bɔn wit fayn fayn wan. Na sɔm ɛgzampul dɛn ya:
- Atrioventrikular kanal difεkt
- Atrial septal difεkt
- Saynotik at sik (we di bɔdi kin tɔn blu) .
- Patent ductus arteriosus (wan blɔd vesel we dɛn se de lɔk afta dɛn bɔn am) .
- Tetralogy of Fallot (na wan kɔmbaynshɔn fɔ 4 at prɔblɛm dɛn) .
- Truncus arteriosus `(Trunkus atεriɔs)`
Wan ɔda tin na, Daun sindrom.Pikin dɛn we gɛt Daun sindrom kin gɛt bɔku risk bak fɔ gɛt at sik we dɛn bɔn wit. Dis kin mek dɛn gɛt mɔ sik bak we dɛn kɔl Eisenmenger syndrome. Infakt, stεdi sho se bitwin 25% εn 50% pan di big pipul dεm we gεt Eisenmenger sεndrכm dεn gεt dכwn sεndrכm bak.
Aw kɔmɔn sik na Eisenmenger syndrome?
Bɔt gud tin na dat, di sik we dɛn kɔl Eisenmenger syndrome na wan sik we nɔ kin apin so ɔltɛm . I kin afɛkt bitwin 1% ɛn 6% pan di big pipul dɛm we dɛn bɔn wit wan at prɔblɛm we dɛn bɔn wit. Bɔt pan ɔl we i nɔ kin bɔku, i impɔtant fɔ no bɔt am bikɔs i siriɔs.
Wetin kin mek pɔsin gɛt di sik we dɛn kɔl Eisenmenger?
Fɔ ɔndastand gud gud wan wetin mek dis kin apin, yu nid fɔ gɛt smɔl aidia bɔt aw blɔd de flɔ na wi at. Imajin se wi at tan lɛk os we gɛt 4 rum.
Blɔd we de go na di at we gɛt wɛlbɔdi kin apin lɛk dis:
1. Rayt atria: di bכdi in yus, diכksijεn bכdi fכs de kam εn kכlekt ya. afta dat dεn de pכmp dis bכdi go na di rayt vεntrikl.
2. Rayt vεntrikl: Dis na di say we di bכdi we nכ gεt כksijεn de sεnd to di lכng dεm fכ gεt nyu כksijεn.
3. Lεft atria: di klin bכdi we dεn bin gεt כksijεn na di lכng dεm de go bak na di at ya. afta dat dεn kin sεnd dis bכdi to di lεft vεntrikl.
4. di lεft vεntrikl: dis na di men pכmp fכ di at. Dis na di say we di blɔd we gɛt ɔksijɛn de sheb ɔlsay na di bɔdi.
naw imajin se wan strכkchכral difεkt de na di at, lεk wan ol na di wכl bitwin di rayt εn lεft vεntrikl (VSD). Wetin kin apin da tɛm de? di blɔd we gɛt bɔku ɔksijɛn (na di lɛft say) ɛn di blɔd we nɔ gɛt bɛtɛ ɔksijɛn (na di rayt say) kin bigin fɔ miks togɛda. Dis kin mek tumɔs blɔd go na di lɔng dɛn. Dis na wetin de mek di pulmonary hypertension we wi bin dɔn tɔk bɔt. Dɔn bak, di blɔd we gɛt ɔksijɛn we nid fɔ go na di ɔda pat dɛn na di bɔdi kin ridyus. Dis na di men prɔblɛm we de wit di sik we dɛn kɔl Eisenmenger syndrome.
Wetin na di sayn dɛm wae de sho se yu gɛt Eisenmenger syndrome?
De sayn dɛm fɔ Eisenmenger syndrome kin difrɛn frɔm wan pɔrsin to ɔda pɔrsin. Dɛn kin dipen pan di kayn at prɔblɛm ɛn di ɔgan dɛm we i afɛkt. Bɔku tɛm, dɛn sayn ya nɔ kin apin wan tɛm. Bɔku tɛm, dɛn kin bigin fɔ apia we dɛn de bɔn pikin ɔ we dɛn yɔŋ. Dɔn, de sik kin wɔs smɔl smɔl.
Dis na sɔm pan de sayn dɛm wae pɔrsin kin si:
- Chest pen ɔ tayt (Angina) .
- di at bit we nכ de bit rεgulεr (Arrhythmias) - Dis min se di at de bit difrεn we dεm insted fכ bit wan we.
- di εnd dεm fכ di fכs nel dεm big εn di kכva fכ di nel dεm (Clubbing) - lεk di tip fכ drumstik.
- Fɔ kɔf blɔd.
- di kכla we de kכl blu כ greysh na di skin (Cyanosis) - dis kin kכz fכ di כksijεn we de na di bכdi we de dכn.
- Diziz ɔ fɔdɔm.
- Di leg, anklɛ, fut, ɔ bɛlɛ kin swel (ɛdima).
- Fɔ fil lɛk se yu at de bit fast, fɔ yɛri di sawnd we yu chɛst de bit (at de bit).
- Taya pasmak ɛn nɔ gɛt ɛnaji (Lethargy).
- Dispnea - I nɔ kin izi fɔ blo ivin if yu tray smɔl.
If yu gɛt wan ɔ mɔ pan dɛn sik ya, i rili impɔtant fɔ go to dɔktɔ wantɛm wantɛm.
Wetin na di prɔblɛm dɛn we kin apin we pɔsin gɛt Eisenmenger syndrome?
Bɔt i sɔri fɔ no se, Eisenmenger syndrome nɔto sik we kin de na wan ples. I kin mek yu gɛt difrɛn prɔblɛm dɛn wit yu wɛlbɔdi. Sɔm pan dɛn na:
- Blɔd we de kɔmɔt na di bren.
- Bren abses bikɔs ɔf infɛkshɔn.
- bכdi nכ de gi di bren (Sεribral vaskulεr insufficiency).
- Gout we pɔsin kin gɛt.
- At atak.
- At we nɔ de wok fayn.
- At infεkshכn, fכ egzampl, εndokarditis.
- Blɔd we de tik (Hyperviscosity syndrome).
- Kidni we nɔ de wok fayn.
- di kכmplikεshכn dεm we yu bεlε (dis rili denja).
- Strok.
- Day wantɛm wantɛm.
We yu luk dɛn prɔblɛm ya, yu go si aw dis tin rili siriɔs, nɔto so? Na dat mek wi nid fɔ pe spɛshal atɛnshɔn to dis.
Aw dɛn kin no se pɔsin gɛt di sik we dɛn kɔl Eisenmenger syndrome?
Bɔku tɛm, dɔktɔ go luk fɔ sayn dɛn we de sho se pɔsin gɛt Eisenmenger syndrome we dɛn de chɛk in bɔdi. Fɔ ɛgzampul, if yu skin blu, if yu finga dɛn gɛt klɔb, ɛn if yu de yɛri sawnd dɛn we nɔmal we yu de lisin to yu at.
Dɔn, di dɔktɔ kin ɔda wan ɔ mɔ pan dɛn tɛst ya fɔ no if pɔsin gɛt di sik:
- Fɔ chɛk di ɔksijɛn lɛvɛl na di blɔd.
- Cardiac catheterization: Dis na fɔ put smɔl tiub insay di at fɔ mɛzhɔ prɛshɔn ɛn chɛk aw i tan.
- X-ray na di chɛst.
- Kɔmplit blɔd kɔnt (CBC).
- Echocardiogram (Echocardiogram - echo): Dis na ɔltra saund skan fɔ di at. I kin luk di at in chɛmba dɛm, di valv dɛm, ɛn aw blɔd de flɔ.
- Ilɛktrokardiogram (EKG/ECG): Dis de tɛst di ilɛktrik wok we di at de du.
- Wan at MRI tɛst.
- Tɛst fɔ di wok we di pulmonari de du.
Di dɔktɔ kin no di sik kɔrɛkt wan bay di infɔmeshɔn we i gɛt frɔm dɛn tɛst ya.
Aw dɛn kin trit di sik we dɛn kɔl Eisenmenger syndrome?
Di men gol fɔ trit di sik we dɛn kɔl Eisenmenger syndrome na fɔ kɔntrol di sik dɛn ɛn fɔ mek dɛn nɔ pwɛl di at ɔ di lɔng dɛn mɔ.
Dɛn kin yuz dɛn tin ya as tritmɛnt:
- Antibayɔtik: I de mek baktri nɔ gɛt di sik na di at ɛn di lɔng.
- Antikoagulant: I de ridyus di fכmeshכn fכ blכd kכlכt na di bכdi vεsul dεm.
- Diuretics (wata pills): Ridyus di ekstra wata we de gɛda na di bɔdi.
- Dual endothelin receptor antagonists: Dis na spɛshal kayn mɛrɛsin we dɛn kin gi fɔ ridyus di ay blɔd prɛshɔn na di lכng.
- Iron supliment: Trit anemia we kin kam bikɔs i nɔ gɛt ayɔn.
- Sɔplɛnt ɔksijɛn: Mek i izi fɔ blo ɛn mek di ɔksijɛn lɛvɛl go ɔp na di blɔd.
Di impɔtant tin na dat, wans Eisenmenger syndrome dɔn kam, bɔku tɛm i kin tu let fɔ ɔpreshɔn fɔ mek di at we dɛn bɔn wit, bikɔs da tɛm de di damej na di lɔng dɛn dɔn ɔlrɛdi dɔn.
Bɔt sɔm pipul dɛn we gɛt siriɔs sik ɛn we gɛt siriɔs ɔgan dɛn we dɔn pwɛl kin nid fɔ transplant dɛn at ɔ lɔng. Bɔt dat na tin bak we rili kɔmpleks ɛn we kin mek pɔsin gɛt prɔblɛm.
Yu tink se dɛn go ebul fɔ protɛkt di sik we dɛn kɔl Eisenmenger syndrome?
Yɛs, di wangren we fɔ mek dɛn nɔ gɛt di sik we dɛn kɔl Eisenmenger syndrome na fɔ no di at prɔblɛm dɛn we dɛn bɔn wit kwik kwik wan, we dɛn jɔs dɔn, ɛn trit dɛn fayn, ɛn if nid de, dɛn fɔ du ɔpreshɔn pan dɛn. If dɛn no ɛn trit dɛn prɔblɛm ya we dɛn smɔl, chans de fɔ mek dɛn nɔ gɛt siriɔs sik lɛk Eisenmenger syndrome.
Wetin na di layf we pipul dɛn we gɛt Eisenmenger syndrome kin liv?
Pipul wae gɛt Eisenmenger syndrome kin gɛt shɔt layf pas di jenɛral pipul dɛm. Dis kin bi bikɔs ɔf de kɔmplikeshɔn wae kin kam wit de sik. Bɔt sɔm pipul dɛn kin liv te to midul ej. De lɔng tɛm wae dɛn kin liv kin dipen pan tin dɛm lɛk aw dɛn kin gɛt dis sik, aw dɛn kin gɛt di sik we dɛn bɔn wit, ɛn aw dɛn kin ansa fayn we dɛn de gi dɛn tritmɛnt. So, i impɔtant fɔ fala yu dɔktɔ in advays ɛn tek kia ɔf yu wɛlbɔdi.
If a gɛt Eisenmenger syndrome, a kin gɛt bɛlɛ?
Dis na kwɛstyɔn we rili impɔtant. Bɛlɛ kin rili denja fɔ pɔsin we gɛt Eisenmenger syndrome. I kin mek yu gɛt siriɔs prɔblɛm dɛn lɛk at pwɛl, blɔd kin rɔtin, ɛn day wantɛm wantɛm. If yu gɛt dis sik ɛn yu de tink bɔt fɔ gɛt bɛlɛ, yu fɔ rili go to spɛshal pɔsin we de tɔk bɔt di at we dɛn bɔn wit big pipul dɛn (`(spɛshal pɔsin pan di at kɔndishɔn we dɛn bɔn wit big pipul dɛn)`) fɔ tɔk bɔt dɛn risk ya. Na in go bi di wan we go gi yu di bɛst advays.
Aw a go tek kia ɔf misɛf wit Eisenmenger syndrome?
If yu gɛt Eisenmenger syndrome, sɔm tin dɛn de we yu kin du fɔ ridyus yu risk fɔ gɛt prɔblɛm dɛn. If yu fala dɛn step ya, dat go ɛp fɔ mek yu liv bɛtɛ layf ɛn yu layf bɛtɛ.
Tin dɛn fɔ du:
- It di it we gɛt sɔdiɔm: If yu it bɔku sɔl, i kin mek yu nɔ gɛt wata ɛn i kin mek yu blɔd prɛshɔn go ɔp.
- Gɛt di rayt vaysin: Protɛkt yusɛf frɔm infɛkshɔn lɛk nyumonia ɛn influenza.
- Drink bɔku wata ɛn nɔ mek yu bɔdi nɔ gɛt wata (`(Staying hydrated)`) : Bɔt na di mɔnt nɔmɔ we yu dɔktɔ advays yu.
- Fɔ fala ɔl di mɛrɛsin ɛn ɔda tritmɛnt dɛn we yu dɔktɔ we de mɛn yu at dɔn tɛl yu fɔ du. Nɔ mis wan doz.
- Tek antibayɔtik bifo yu trit yu tit ɔ ɔpreshɔn: Dis kin ɛp fɔ mek yu nɔ gɛt at infɛkshɔn. Aks yu dɔktɔ bɔt dis.
Tin dɛn we yu nɔ fɔ du:
- Nɔ go na ples dɛn we rili ay pas di si (`(High altitudes)`): Di prɔblɛm fɔ blo kin bɔku bikɔs ɔksijɛn nɔ de na ay ay ples.
- Nɔ yuz sawna, stim rum, ɔ hot tub: Dɛn tin ya kin mek yu blɔd prɛshɔn go dɔŋ wantɛm wantɛm.
- Nɔ smok ɔ yuz tin dɛn we dɛn kin yuz fɔ smok ɔltogɛda.
- Nɔ ɛksesaiz tranga wan: Na layt ɛksesaiz nɔmɔ yu fɔ du na di lɛvul we yu dɔktɔ gri fɔ.
Mɛsej we dɛn kin kɛr go na os
Eisenmenger syndrome na wan sik wae de mek yu gɛt ay blɔd prɛshɔn na di blɔd vesel dɛm na di lɔng ɛn di rayt say na di at. Bɔrku tɛm, na bikɔs ɔf di at pwɛl hat we dɛn bɔn wit we dɛn nɔ trit. Bɔrku tɛm, di sayn dɛm kin bigin fɔ sho na di yɔŋ pipul dɛm ɔr yɔŋ pipul dɛm. Di sayn dɛm na blu skin (cyanosis), yu nɔ kin blo fayn we yu de du ɛksɛsayz, ɛn yu at nɔ kin bit ɔltɛm.
Di tritmɛnt fɔ dis sik na fɔ mek dɛn nɔ gɛt di sik ɛn fɔ mek di at ɛn di lɔng dɛn nɔ pwɛl bɛtɛ. I dɔn tu let fɔ mɛn dis sik wit ɔpreshɔn. So, i bɛtɛ fɔ no ɛn trit di at prɔblɛm dɛn we dɛn bɔn wit kwik kwik wan.
If yu gɛt ɛni ɔda kwɛstyɔn bɔt dis, nɔ fred fɔ tɔk to yu dɔktɔ. Dɛn go ɛp yu.
👩🏽 ⚕️ Ɔda kwɛstyɔn dɛn (FAQ dɛn)
💬 Yu tink se Eisenmenger Syndrome na nyu at sik?
Dis nɔto nyu tin we de apin. Dis na di las, denja rizɔlt fɔ pikin we dɛn bɔn wit ol na in at (lɛk VSD) ɛn nɔ gɛt ɛni tritmɛnt fɔ am fɔ lɔng lɔng tɛm. dis na di say we di bכdi de fכlכ de rivεs, we de mek blu (deoxygenated) bכdi fכ fכlכ כlsay na di bכdi.
💬 Dis de mek yu bodi tɔn blu?
Yɛs! Di men sayn fɔ dis sik na we di pɔsin in lip, in tɔŋ, ɛn in nel dɛn kin tɔn blu (cyanosis) bikɔs ɔksijɛn nɔ de na in bɔdi. Dɔn bak, di finga dɛn kin bi klɔb (klɔb). Ivin we yu du smɔl tin, dat kin mek yu fil so taya dat yu nɔ kin ebul fɔ blo.
💬 I go fayn fɔ mek dɛn du ɔpreshɔn fɔ lɔk di ol na di at ivin naw?
Nɔ! Na ɔnfɔni, wans yu rich dis ‘Eisenmenger’ stej, if di ol na di at klos, di pɔsin go day rayt de. Bikɔs naw ɔl di blɔd vesel dɛn we de go na di lɔng dɛn dɔn pwɛl ɛn di prɛshɔn dɔn ay. Di wangren tin we dɛn kin du naw na fɔ tek mɛrɛsin ɛn kɔntrol di sik, ɔ fɔ du at-lɔng transplant.
` Eisenmenger sindrom, hat sik, pulmonary hypertension, cyanosis, hat difεkt we dεn bכn wit, difεlεns fכ brith, at hεlth











💬 Comments (0)
No kɔmɛnt nɔ de yet. Ad yu kɔmɛnt ya fɔ di fɔs tɛm.
Ad yu kɔmɛnt