Yu smɔl pikin gɛt at prɔblɛm? Lɛ wi tɔk bɔt Hypoplastic Aortic Arch!

Sɔntɛnde, i nɔ kin izi fɔ yu smɔl pikin fɔ gi in bɛlɛ? Yu tink se i kin fil taya pas aw i kin fil we i de blo? Ɔ i kin tan lɛk se i gɛt blɛsin ɛn i de swet? I nɔmal fɔ mek yu as mama ɔ papa fil bad bad wan we dɛn tin ya apin to yu smɔl pikin. Sɔmtɛm di tin wae kin mek dis kin bi wae pɔrsin gɛt dis sik wae dɛn bɔn wit. Tide, wi go tɔk bɔt wan sik we kin apin na di at fɔ pikin dɛn, bɔt i kin mɛn if dɛn no am kwik ɛn trit am fayn.

Wetin na Hypoplastic Aortic Arch?

Fɔ tɔk am simpul wan, Hypoplastic Aortic Arch , we sɔm pipul dɛn kin kɔl Aortic Arch Hypoplasia (AAH) , na wan prɔblɛm we pɔsin kin bɔn we i bɔn we kin apin na wan pat na yu pikin in at , we na di aorta . Tink bɔt dis we, di aorta tan lɛk wan big at we de kɛr blɔd ɔlsay na wi bɔdi. I kin bigin na di at ɛn i kin kɛr blɔd we gɛt ɔksijɛn ɔlsay na di bɔdi. I shep lɛk ken, i kɔba smɔl. di kכv we de tap pan di ken dεn kכl am di aortic arch , we min ‘di arch fכ di aorta.’

di wɔd ‘haypoplastik’ min ‘nɔ de divɛlɔp fayn’, ‘smɔl’. so, pikin we gεt haypoplastik aorta arch gεt aorta arch we nכ de divεlכp. Dat min se di opin ɔ dayamita insay da pat de smɔl pas aw i fɔ smɔl. Jɔs lɛk aw wata paip kin blok, we di aorta arch smɔl, i kin at fɔ mek blɔd kɔmɔt na di at go na di ɔda pat dɛn na di bɔdi, tru di aorta we de kam dɔŋ . Dis kin mek di blɔd we de go na di wan ol bɔdi nɔ bɔku.

Udat dɛn kin afɛkt mɔ pan dis sik? Yu tink se sɔntin de we gɛt fɔ du wit ɔda at sik dɛn?

di aortic arch hypoplasia (AAH) kin apin in wan. Bɔt bɔku tɛm dɛn kin si am wit ɔda at prɔblɛm we dɛn bɔn wit , we dɛn kɔl coarctation of the aorta . dis na di kכndyushכn we wan כda pat pan di aorta, we kin kכl nia di ductus arteriosus, we na spεshal bכdi we nכmal fכ de na di bכdi, kin sכmtεm sכmtεm.

So yu pikin in dɔktɔ kin se, "Yu pikin gɛt coagulopathy na di aorta wit aortic arch hypoplasia." Dat min se di aorta de sכm, nכto jכs na wan ples, bכt along wan lכng sεkshכn.

Apat frɔm dat, pikin dɛn we gɛt AAH kin gɛt ɔda at prɔblɛm dɛn. Fɔ ɛgzampul:

• Atrial Septal Defect (ASD) : Na ol na di wכl bitwin di tu כp chεmba dεm na di at.
• Atrioventricular Septal Defect : Na komplex difεkt na di wכl dεm bitwin di chεmba dεm na di at.
• Bicuspid Aortic Valve εn Aortic Valve Stenosis : difεkt dεm εn di aorta valv de sכmtεm sכmtεm sכmtεm.
• Hypoplastic Left Heart Syndrome (HLHS) : di lεft say na di at nכ de divεlכp fayn.
• Patent Ductus Arteriosus (PDA) : na wan bכdi we dεn kכl ductus arteriosus we fכ klos afta dεn bכn de stil opin.
• Shone’s Syndrome : Na wan kɔmbaynshɔn fɔ sɔm difrɛn difrɛn tin dɛn we de ambɔg di blɔd flɔ na di lɛft say na di at.
• Ventricular Septal Defect (VSD) : Na ol na di wכl bitwin di tu lכw chεmba dεm na di at.

Fɔ gɛt pas wan at sik lɛk dis rili impɔtant we yu de plan fɔ trit yu. Bikɔs dɛn nid fɔ gɛt ɔpreshɔn ɔ tritmɛnt plan we dɛn mek fɔ di kɔmpleks, patikyula tin dɛn we de apin na di pikin in at.

Wetin na di sayn dɛm if pikin gɛt dis sik?

di pikin dεm we gεt kכarktashכn pan di aorta εn di aorta arch haypoplasia kin bigin fכ sho di simptom dεm sכm tεm afta dεn bכn dεm . Imajin se yu pikin we yu jɔs bɔn, we dɔn taya afta i dɔn drink sɔm tɛm, i tan lɛk se i nɔ izi fɔ blo. Sɔntɛnde, dɛn kin swet ɛn tɔn bluish-wayt kɔlɔ. Aw i kin mek mama fred fɔ si sɔntin lɛk dis, nɔto so?

De men sayn wae yu kin si na:

• Fast pulse : Di puls rεt tu fast.
• Taya : Di pikin kin fil taya kwik kwik wan, mɔ we i de gi in mama in bɛlɛ.
• Grey ɔ pale skin : Sɔntɛnde di skin kin tan lɛk blu bak.
• We pɔsin kin swet bad bad wan .
• Fɔ kray ɔltɛm, fɔ vɛks .
• Fɔ blo kwik kwik wan ɔ we yu de blo tranga wan .
• Trɔbul wit fɔ it: I nɔ gri fɔ drink milk, ɔ i kin stɔp afta i dɔn drink smɔl.
• wik puls na di lכw pat dεm na di bכdi : εspεshali na di lεg dεm, di puls na di fεmoral at de rili wik we dεn palpat am.

If yu pikin gɛt wan ɔ mɔ pan dɛn sik ya, i rili impɔtant fɔ go to dɔktɔ wantɛm wantɛm .

Wetin mek dis de apin? Wetin na di rizin dɛn?

AAH na wan at prɔblɛm we dɛn bɔn wit . Na sɔntin we kin apin we di pikin stil de na di bɛlɛ. Risach pipul dɛn stil de tray fɔ no wetin rili mek dis kayn at prɔblɛm we dɛn bɔn wit.

Bɔt wetin dɛn no na dat dis sik kin apin if di pikin in aɔta arch nɔ de divɛlɔp fayn fayn wan insay di fɔs wik dɛn we i gɛt bɛlɛ .

Aw yu kin fɛn dis? Wetin na di tɛst dɛn?

Dɔktɔ dɛn kin yuz dis fɔ no di sik.Speshal imej tɛst dɛn. Dɛn kin du dɛn tɛst ya jɔs afta dɛn bɔn di pikin.

Di men tɛst dɛm we dɛn kin yuz fɔ no AAH na:

• Kardiak Kɔmpyuta Tomografi (CT skan) .
• Magnɛtik Rɛsɔnans Angiogram (MRA) .
• Transthoracic Echocardiogram (TTE) : Dis tan lɛk ɔltra saund skan fɔ di at.
• Cardiac Catheterization : Sɔntɛnde, dɛn kin nid fɔ du dis tɛst bak.

dis tεst dεm kin luk di strכkchכ fכ di pikin in at, dat na aw dεn arenj di insay pat dεm, bכku bכku wan. Dɛn kin no bak if di pikin gɛt ɔda at prɔblɛm dɛn. Na we di dɔktɔ dɛn gɛda ɔl dɛn tin ya, dɛn kin plan di tritmɛnt we go fayn fɔ di pikin.

Fɔ no if AAH de, dɔktɔ dɛn kin luk di sayz fɔ di pikin in aɔta arch. Speshali, dɛn kin mɛzhɔ in dayamita , we na di wit we di opin insay. dis mכsul dεn kכmpεr am wit di dayamita fכ כda pat dεm na di pikin in aorta (fכ egzampl, di aorta we de go כp כ di aorta we de dכn). dεn de yuz dεn valyu dεm ya fכ no if di dayamita fכ di aorta arch tu sכm.

Lɛ wi lan smɔl bɔt di difrɛn pat dɛn na di aotic arch.

We yu pikin in dɔktɔ tɔk bɔt dis sik, i kin tɔk bɔt di difrɛn pat dɛn na di aɔta arch. yu kin de wɔnda, "Di aorta arch de sheb to ɔda pat dɛm? nɔto dat pat pan di big aorta?" Yɛs, na tru. di aorta arch na sכmכl, "kεn lεk" pat pan di aorta. bכt, lεk כl di pat dεm na di aorta, di aorta arch gεt bכdi vεsul dεm (atεri dεm) we de branch כf difrεn say dεm. Jɔs lɛk aw men rod gɛt sayd rod dɛn. Dɔktɔ dɛn kin yuz dɛn difrɛn blɔd vesel ya as bɔda, we de mak usay wan patikyula pat pan di aɔta arch bigin ɛn dɔn. Dis "map" kin rili ɛp fɔ no bɔt AAH ɛn fɔ plan tritmɛnt.

Na sɔm pan di pat dɛm na di aural arch we yu pikin in dɔktɔ kin tɔk bɔt:

• Proximal Transverse Arch : dis de bitwin di pikin in Brachiocephalic Artery (sכmtεm dεn kin kכl am Innominate Artery) εn di Left Common Carotid Artery . Dis na di pat we de nia di at pas ɔl.
• Distal Transverse Arch : Dis de bitwin di lεft kכmכn karotid atεri εn di lεft sabklavian atεri .
• Aortic Isthmus : Dis de bitwin di lef sabklavian at ɛn di blɔd vesel we wi bin dɔn tɔk bɔt we dɛn kɔl Ductus Arteriosus .

Yu pikin in dɔktɔ go no ustɛm di smɔl smɔl tin we de na yu pikin in yɛri arch, ɛn bak aw di smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl. Dis infɔmeshɔn go gayd di tritmɛnt plan.

Wetin na di tritmɛnt dɛm fɔ dis?

di pikin dεm we gεt haypoplastik aorta arch go nid at כpεrayshכn fכ kכrekt di kכndyushכn. Di dɔktɔ we de mɛn yu pikin in at go ɛksplen to yu us kayn ɔpreshɔn yu pikin go nid. Di ɔpreshɔn we dɛn kin du kin difrɛn difrɛn wan bay di ɔda tin dɛn we nɔ fayn ɛn di we aw yu pikin in at tan. Yu kin nid fɔ mek dɛn kɔt yu pikin , we na smɔl say we dɛn kɔt na di lɛft say na yu pikin in chɛst, ɔ sternotomy, we na wan say we dɛn kɔt dɔŋ di midul pat na di chɛst.

Wan kɔmɔn ɔpreshɔn we dɛn kin kɔl rɛsekshɔn wit ɛkstend ɛnd-to-ɛnd anastomosis . dis כpεrayshכn kin rili εp fכ bebi dεm we gεt kכarktashכn na di aorta εn aorta arch haypoplasia. insay dis prosidur, di sajin de pul di pat we sכmtεm na di aorta, tek di lכw pat pan di aorta (di aorta we de dכn), εn ataya am pan wan say we lכng sכmtεm na di aorta arch.

Di op fɔ dis ɔpreshɔn na fɔ mek di blɔd flɔ fayn fayn wan tru di pikin in aorta, ɛn mek shɔ se di pikin in ɔgan ɛn tisu dɛn gɛt inof blɔd we gɛt ɔksijɛn.

Wetin na di op fɔ mek mi pikin wɛl?

Di bɛst ansa to dis kwɛstyɔn na yu pikin in dɔktɔ. Na bikɔs di pikin in wɛlbɔdi kin dipen pan bɔku tin dɛn. Na mɔ, if ɔda at prɔblɛm dɛn de we pɔsin kin bɔn wit, dat kin rili afɛkt am.

in jεnarכl, pikin dεm we dεn dכn trit fכ wan kכndyushכn we dεn kכl aotic arch hypoplasia gεt hכy chans fכ gεt dεn prכblεm ya leta na layf:

• Dɛn aorta kin smɔl bak bak .
• Ay blɔd prɛshɔn (Hypertension) .
• I nɔ izi fɔ it ɔ swɛla : Dis kin apin if wan nerve dɔn pwɛl we dɛn de du ɔpreshɔn (dis nɔ kin apin so ɔltɛm).

Tɔk to yu pikin in dɔktɔ bɔt dɛn prɔblɛm ya ɛn aw fɔ kɔntrol dɛn.

Yu tink se dɛn go ebul fɔ mek dis tin nɔ apin?

di hat dεfεkt dεm we dεn bכn wit lεk haypoplastik aorta arch kin nכ kin kכmplit fכ avεnt . Bɔt if yu fala yu dɔktɔ in advays fɔ gɛt bɛlɛ we gɛt wɛlbɔdi, dat kin ɛp fɔ mek yu nɔ gɛt dis sik ɔ ɔda tin dɛn we nɔ fayn.

in jεnarכl, dεn tin ya fכ rili av כyd we uman bεlε:

• Rum .
• Nɔ smok, vaping ɛn ɔl di tin dɛn we dɛn kin mek wit tabak . Dɔn bak, nɔ smok sɛkɔn-han smok .
• Drug dɛn we nɔ rayt, mɔ di kɔkɛyn .

Ɛn bak, yu yon.I rili impɔtant bak fɔ atɛnd chɛk-ap bifo yu bɔn ɔltɛm. If yu gɛt ɛni ɔda wɛlbɔdi prɔblɛm, go to dɔktɔ fɔ advays yu fɔ kɔntrol dɛn sik dɛn de bifo yu gɛt bɛlɛ ɛn we yu gɛt bɛlɛ.

Aw fɔ kia fɔ di pikin afta dɛn dɔn du di ɔpreshɔn?

di tin dεm we εvri pikin nid kin difrεn afta dεn du di כpεrayshכn, so i bεst fכ aks yu pikin in mεdikal tim aw fכ kia fכ yu pikin fכ sכt εn lכng tεm.

Na sɔm kwɛstyɔn dɛn we yu kin aks yu dɔktɔ:

• Aw a fɔ kia fɔ mi pikin we a go na os?
• Us mɛrɛsin a fɔ gi mi pikin? Aw lɔng a fɔ gi am?
• Dɛn nid ɛni tritmɛnt fɔ ɛp di pikin in bɔdi ɔ in nyurolɔjik wok?
• Ɛnitin de we de stɔp di pikin fɔ du tin?
• Ustɛm i sef fɔ sɛn mi pikin na daycare? Us spɛshal instrɔkshɔn dɛn a fɔ gi dɛn?
• Yu tink se mi pikin go nid fɔ gɛt ɔda tritmɛnt ɔ ɔpreshɔn?

Fɔ bi mama ɔ papa nɔ kin izi ɔltɛm. Bɔt fɔ liv wit pikin we gɛt at sik lɛk hypoplastic aortic arch (AAH) kin briŋ nyu chalenj ɛvride. Sɔm pan di wɔd dɛn we dɔktɔ dɛn kin tɔk ɛn di tritmɛnt plan dɛn kin tan lɛk se i nɔ izi fɔ ɔndastand. Dat na nɔmal tin, ɛn nɔto yu wan de. Aks yu pikin in dɔktɔ bɔt tin dɛn ɛn sɔpɔt grup dɛn we go ɛp yu. Fɔ bil kɔmyuniti fɔ sɔpɔt yu ɛn yu famili kin ɛp fɔ ridyus strɛs ɛn gi yu trɛnk fɔ go bifo wit wetin yu pikin nid.

Mek wi jos memba wetin wi tok abaut (Take-Home Message)

• Hypoplastic Aortic Arch (AAH) na wan sik we di arch na di aorta, we na wan big bכdi we de na di pikin in at, nכ de divεlכp fayn fayn wan, we de mek di arch sכmtεm sכmtεm.
• Dis kin mek i nɔ izi fɔ lɛ blɔd kɔmɔt na di at to ɔda pat dɛn na di bɔdi.
• Bɔku tɛm dɛn kin si dis sik togɛda wit ɔda at sik we dɛn kɔl Coarctation of the Aorta .
• di sayn dεm lεk fכ taya, i at fכ brith, εn di skin we de fכm kin ali na di pikin in layf.
• Dɛn kin no dis sik wit spɛshal skan.
• Di tritmɛnt na ɔpreshɔn na di at .
• Fɔ fala di mɛdikal instrɔkshɔn dɛn ɛksaktɔli ɛn fɔ fala fɔ lɔng tɛm afta dɛn dɔn du di ɔpreshɔn rili impɔtant.
• If yu fala di fayn fayn abit dɛn we yu gɛt bɛlɛ, dat kin mek yu nɔ gɛt sɔm prɔblɛm dɛn we yu bɔn wit.
• Nɔto yu wan de. Gɛt ɛp frɔm dɔktɔ ɛn sɔpɔt grup dɛn.

Wi op se dis infɔmeshɔn go ɛp yu. Wi de wish yu smɔl pikin fɔ wɛl kwik kwik wan!

` Hypoplastic Aortic Arch, Aortic Arch Hypoplasia, we dɛn bɔn wit at prɔblɛm, pikin in at ɔpreshɔn, kɔt kɔt di aorta, pikin at sik, at ɔpreshɔn