Yu smɔl pikin gɛt dis kayn at prɔblɛm? (Tɔtal Anomalous Pulmonary Venous Return - TAPVR) Lɛ wi tɔk bɔt dis!

We dɛn bɔn yu pikin, sɔntɛnde i kin fil lɛk se i nɔ izi fɔ blo? Sɔntɛnde, i kin tan lɛk se di skin de tɔn blu? Na nɔmal tin fɔ fil bad bad wan we yu si sɔntin lɛk dat. Tide wi go tɔk bɔt wan sik we pɔsin kin bɔn wit in at we kin sho dɛn sayn ya. Dɛn kɔl dis TAPVR (Tɔtal Anomalous Pulmonary Venous Return) . Pan ɔl we i go tan lɛk se di nem kɔmplikt smɔl, lɛ wi ɔndastand am simpul wan.

Wetin na TAPVR? Fɔ put am simpul wan...

Tink bɔt am, wi bɔdi kin gɛt ɔksijɛn frɔm di lɔng, nɔto so? So, frכm dεn lכng dεm ya, di bכdi we gεt כksijεn (lε wi kכl dis "gud bכdi") de kam na di at bay vein dεm , we na wan kayn bכdi vεsεl. nכmal wan, dis "gud bכdi" fכ kam na di lεft atria na di lεft say na di at. Frɔm de, dɛn kin pɔmp di blɔd fɔ gi ɔksijɛn to di wan ol bɔdi.

Bɔt pan pikin we gɛt TAPVR, instead fɔ kɔnɛkt to di lɛft atria na di at, dis pulmonari vein de kɔnɛkt to di rɔng ples, we na di rayt atria . di rayt atria nכmal wan de gεt "bad bכdi" we di bכdi dכn yus כp, we nכ gεt כksijεn. Naw di "gud blɔd" we ful-ɔp wit ɔksijɛn de miks wit dis "bad blɔd." Wetin kin apin da tɛm de? Di ɔksijɛn we de na di blɔd we dɛn se go go na di wan ol bɔdi de go dɔŋ. Dis na tin we rili denja ɛn we kin mek pikin in layf de pan denja . Dis na at sik we dɛn kin bɔn wit .

kכlכsכl כl di pikin dεm we gεt TAPVR gεt sכmכl ol (Atrial Septal Defect - ASD) bitwin di tu chεmba dεm na dεn at, di rayt atria εn di lεft atrium. Dis ol de mek sɔm blɔd we gɛt ɔksijɛn go na di lɛft say na di at ɛn afta dat go na di ɔda pat dɛn na di bɔdi. If nɔto dat, di sik bin fɔ dɔn wɔs pasmak.

Di tin we impɔtant pas ɔl na dat bebi dɛn we gɛt TAPVR rili nid ɔpreshɔn. If dɛn du di ɔpreshɔn kwik, bɔku pikin dɛn kin liv fayn layf te dɛn big. Bɔt sɔntɛnde, tin dɛn lɛk fɔ mek di vein dɛn smɔl leta we dɛn dɔn day, dɛn kin nid fɔ du ɔda ɔpreshɔn ɔ ɔda tritmɛnt dɛn. So, ivin afta dɛn dɔn du TAPVR ɔpreshɔn, yu go nid fɔ mek dɔktɔ we de mɛn yu at de wach yu fɔ di res ɔf yu layf.

Sɔntɛnde, dɔktɔ dɛn kin kɔl dis kɔndishɔn bak TAPVC (Tɔtal Anomalous Pulmonary Venous Connection). Dɛn ɔl tu na di sem kɔndishɔn.

Difrɛn kayn TAPVR dɛn de?

Yes, sɔm men kayn TAPVR dɛn de. dεn kin kכl dεm dεm ya akɔdin to aw di "gud bכdi" we de kכmכt na di lכng dεm nכ kכnekt fayn fayn wan to di rayt atria.

• Supracardiac TAPVR: insay dis, di pulmonari vein dεm de jכyn εn kכnekt to wan big vein we de oba di at (dεn kכl am supεriכr vena cava , we na wan big vein we de kכri bכdi frכm di כp pat dεm na di bכdi to di rayt say na di at).
• di kadyak TAPVR: na ya, di pulmonari vein dεm de fכlכ dεrekt insay di korona sayn na di rayt say na di at.Kɔnekt dɛn. dis korona at na ples we di bכdi we nכ gεt כksijεn kin kכlekt frכm di at mכsul.
• Infracardiac TAPVR: Insay dis kayn we, di pulmonari vein de pas dכn di at, tru di liva, εn i de kכnekt to wan big vein ( inferior vena cava ) we de kכri bכdi frכm di lכw pat dεm na di bכdi to di rayt say na di at.
• Mixed TAPVR: Dis na di kayn we we nɔ bɔku ɛn we at fɔ mek. na ya, mכr dan wan vein frכm di lכng dεm kin kכnεkt, insay wan kכmbaynshכn fכ wan כ mכr pan di tכp dεm we wi bin dכn tכk bכt.

Dis klasification impɔtant fɔ mek dɔktɔ dɛn plan fɔ du ɔpreshɔn ɛn disayd aw fɔ trit am.

Aw kɔmɔn tin na TAPVR?

TAPVR na wan at sik we nɔ kin apin so ɔltɛm . Ivin na kɔntri lɛk Amɛrika, dis sik kin afɛkt wan pan ɛvri 7,500 pikin dɛn we dɛn jɔs bɔn. I nɔ kin bɔku bak na Sri Lanka.

Wetin na di sayn dɛm fɔ TAPVR?

di simptom dεm fכ TAPVR kin bi we dεn bכn am , spεshal wan if di pulmonari vein dεm we dεn kכnεkt to di at sכmtεm sכmtεm sכmtεm. Bɔt sɔm pikin dɛn nɔ kin sho di sik fɔ sɔm wiks.

Di men sayn dɛm na dɛn wan ya:

• Saynosis: Na bluish ɔ greyish kɔlɔ we de chenj di skin, nel, ɛn lip (insay pikin dɛn we gɛt dak skin). Dis kin apin bikɔs ɔksijɛn nɔ de na di blɔd.
• i at fכ sכk: di pikin kin gεt difεlεnt fכ sכk εn i kin taya afta i dכn drink sכmtεm.
• Taya ɛn taya: Di pikin kin taya ɔltɛm ɛn i kin tan lɛk se i taya.
• At grɔmbul: We di dɔktɔ lisin to di pikin in at (wit stetɔskɔp), dɛn kin yɛri wan sawnd we nɔmal.
• Short brith (dyspnea): di pikin de blo kwik kwik wan ɛn i tan lɛk se i nɔ izi fɔ blo.
• I nɔ de gro fayn ɛn i nɔ de gɛt bɔku bɔku wet: Di pikin nɔ de gɛt wet fayn ɛn i nɔ de wok fayn.

If yu pikin gɛt wan ɔ mɔ pan dɛn sik ya, yu fɔ go to dɔktɔ wantɛm wantɛm .

Wetin kin mek pɔsin gɛt TAPVR?

Infakt, dɔktɔ dɛn stil nɔ no di rayt tin we kin mek pɔsin gɛt TAPVR. i kin kכz fכ difεkt na di at εn di bכdi vεsul dεm we di pikin de divεlכp .

Nɔr kin si am as sik wae dɛn kin gɛt frɔm dɛn mama ɛn papa. Bɔt dɛn dɔn ripɔt se di sik kin apin to brɔda ɛn sista dɛn we de insay di sem famili. Sɔm stɔdi dɛn dɔn sho se kin gɛt sɔntin fɔ du wit pikin dɛn we gɛt sɔm sik dɛn ɛn we dɛn de yuz tin dɛn we dɛn kin yuz fɔ pul pent, mɛrɛsin fɔ kil peshɛnt, ɛn lid we dɛn gɛt bɛlɛ. Bɔt, dɛn nɔ pruv dis yet.

Wetin na di pɔsibul kɔmplikeshɔn dɛm fɔ TAPVR?

Bebi we gɛt TAPVR gɛt at pwɛl ɛn pulmonari haypatɛnshɔn.Ivin afta dɛn dɔn du ɔpreshɔn, sɔntɛnde di at nɔ kin rit ɔ i kin blok na di pulmonari veins. Na dat mek i impɔtant fɔ kɔntinyu fɔ chɛk yu mɛrɛsin.

Aw dɛn kin no bɔt TAPVR?

sכmtεm, dεn kin no di kכndyushכn bifo dεn bכn di pikin, wit εchocardiogram (we dεn kin skan di at) we dεn bεlε. Bɔt bɔku tɛm dɛn kin no di sik sɔm wik ɔ mɔnt afta dɛn bɔn di pikin.

We dɛn bɔn di pikin, di dɔktɔ go du in bɔdi ɛgzam ɛn lisin to di pikin in at. dεn kin yuz wan sכmכl tin we dεn k כl puls כksimita (klip we fit rawnd di pikin in big fut) fכ mכsu di כksijεn lεvεl na di bכdi.

Apat frɔm dat, dɛn kin du tɛst dɛn lɛk dɛn wan ya fɔ chɛk aw di at ɛn di blɔd vesel dɛn de:

• X-ray na di chɛst
• CT skan (CT skan - kɔmpyuta tomografi) .
• At MRI (magnɛtik rɛsɔnans imej) .
• Ekokardiogram we dɛn kin du
• EKG (EKG ɔ ECG - Ilɛktrokardiogram) .

sכm pan dεn tεst dεm ya (lεk MRI) kin nid fכ mek di pikin sכdi (put am slip layt wan). Bɔt ɔl dɛn tɛst ya nɔ kin ambɔg pɔsin. Dɛn tɛst ya kin mek dɔktɔ dɛn ebul fɔ gɛt klia pikchɔ dɛn bɔt di pikin in at ɛn in lɔng, si aw blɔd de flɔ, ɛn luk fɔ tin dɛn we nɔ fayn.

Sɔntɛnde, dɛn kin yuz wan tɛst we dɛn kɔl cardiac catheterization bak fɔ no di sik. Bɔt bikɔs bɔku tɛm dɛn kin gɛt di tin dɛn we dɛn nid frɔm di skan dɛn we wi dɔn tɔk bɔt, dɛn nɔ kin du di pikin invayv tɛst.

Aw dɛn kin trit TAPVR?

Klose to ɔl di pikin dɛn we gɛt TAPVR nid ɔpreshɔn fɔ mek dɛn kɔntinyu fɔ liv. Dɔktɔ dɛn kin trit am wit ɔpreshɔn fɔ opin at . Bɔku tɛm, dɛn kin du dis ɔpreshɔn kwik kwik wan afta dɛn dɔn no se i gɛt di sik.

Pan ɔl we i nɔ kin apin so ɔltɛm, dɛn kin no se sɔm pipul dɛn gɛt TAPVR we dɛn dɔn big ɛn dɛn nɔ kin du ɔpreshɔn pan dɛn we dɛn smɔl. Bɔt bay da tɛm de dɛn kin gɛt tin dɛn lɛk pulmonary hypertension we kin mek ɔpreshɔn rili tranga.

Tritmɛnt bifo dɛn du di ɔpreshɔn

We dɛn de wet fɔ mek dɛn du di ɔpreshɔn, dɛn kin nid fɔ gi di pikin ɛkstra ɔksijɛn ɔ kɔnɛkt am to ventilator fɔ ɛp am fɔ blo. Dɛn kin gi yu bak wan kayn mɛrɛsin we dɛn kɔl inotrope , we kin ɛp di at fɔ bit tranga wan.

Aw dɛn kin du di ɔpreshɔn

Afta di pikin dɔn slip kpatakpata ɔnda jenɛral anestezi , di dɔktɔ we de du di ɔpreshɔn go du dɛn tin ya:

1. Dɛn kin kɔt di pikin in chɛst ɛn in at.

2. di pulmonari vein dεm de kכnekt bak to di kכrekt ples, dat na di lεft atrium na di at.

3. di vein dεm we kכnεkt abnכmal wan dεn kin kכlok.

4. If eni blכk de na di pulmonari vein dεm, dεn kin pul am.

5. Bɔku tɛm, di ol bitwin di lɛft ɛn rayt atria ( Atrial Septal Defect - ASD ) kin lɔk.

Pan ɔl we dis na ɔpreshɔn we rili kɔmpleks, di mɛdikal tim dɛn we gɛt ɛkspiriɛns kin du am fayn fayn wan.

Di prɔblɛm dɛn we kin apin we pɔsin de trit am

Dis na sɔm pan di prɔblɛm dɛn we kin apin afta dɛn dɔn du di ɔpreshɔn:

• Di at bit we nɔ de bit ɔltɛm (Arrhythmias) .
• Pulmonari haypatɛyshɔn
• Pulmonary venous obstrukshɔn
• Sɔntɛnde, afta dɛn dɔn yuz at-lɔng mashin (baypas mashin) we dɛn de du ɔpreshɔn, i nɔ kin izi fɔ mek di at bit insɛf.

Dɔktɔ dɛn kin de wach ɔltɛm fɔ tin dɛn lɛk dis.

Yu tink se dɛn kin ebul fɔ stɔp TAPVR?

Bɔt i sɔri fɔ no se, no we nɔ de fɔ mek dɛn nɔ gɛt dis kayn at sik we dɛn kin bɔn wit. If pɔsin na yu famili gɛt at sik we dɛn bɔn wit, ɔ if yu gɛt TAPVR, i fayn fɔ tɔk to yu dɔktɔ bifo yu bigin famili.

If mi pikin gɛt TAPVR, wetin a fɔ ɛkspɛkt?

If dɛn nɔ du ɔpreshɔn, sɔm kayn TAPVR kin kil pɔsin insay sɔm wiks afta dɛn bɔn am. Bɔt if dɛn no di sik kwik ɛn trit am wit ɔpreshɔn, di luk fɔ bebi dɛn we gɛt TAPVR kin rili fayn. di rεt we de liv afta di כpεrayshכn na bכt 97%. Dat na rili ay sakrifays rɛt.

As yu pikin de gro ɛn big, i fɔ go to dɔktɔ we de mɛn in at ɔltɛm . Dɛn chɛk-ap ya we dɛn kin du ɔltɛm ɔlsay na yu layf kin ɛp fɔ no ɛn trit prɔblɛm dɛn lɛk we di at nɔ de rit ɔltɛm ɛn we di blɔd vesel de blok. Sɔntɛnde, if pɔsin blok, i kin nid fɔ du mɔ ɔpreshɔn ɛn i nɔ kin izi fɔ trit am. Na dat mek i impɔtant fɔ kɔntinyu fɔ fala wetin yu dɔktɔ tɛl yu fɔ du.

Yu pikin kin nid fɔ kɔntinyu fɔ tek mɛrɛsin ɔ fɔ gɛt tritmɛnt dɛn lɛk fɔ put kateshɔn na in at .

Aw a go kia fɔ mi pikin?

Pikin dεm we gεt TAPVR kin gεt difεlεnt sכmtεm wit nכmal divεlכpmεnt maylston dεm, lεk fayn mכtalman fכnshכn. Yu kin wach yu pikin in divɛlɔpmɛnt maylston dɛm ɛn rifer am to pɔsin we go ɛp am fɔ gɛt dɛn skil dɛm de if nid de.

Tɔk to yu pikin in dɔktɔ bɔt if yu pikin go ebul fɔ tek pat pan spɔt ɛn fɔ du bɔdi wok. Yu go nid fɔ stɔp fɔ du ɛksɛsayz we yu de tray tranga wan .

Ustɛm mi pikin fɔ go to dɔktɔ?

Afta di ɔpreshɔn, dɛn go si yu pikin ɛvri 6 to 12 mɔnt.Di chɛk-ap dɛn we dɛn kin du fɔ mɛn pipul dɛn. Yu fɔ kɔntinyu fɔ go to yu dɔktɔ ɔltɛm we yu big. Yu pikin in dɔktɔ kin want fɔ du tɛst dɛn lɛk EKG, ɛksesaiz strɛs tɛst, ɔ ɛkokardiogram .

Ustɛm yu nid fɔ go na di Imejɛnsi Rum (ETU) ?

Go to dɔktɔ wantɛm wantɛm (go to di ER) if yu pikin gɛt ɛni wan pan dɛn sayn ya:

• If di skin, di nel, ɔ di lip dɛn tɔn blu/grey.
• If yu gɛt prɔblɛm fɔ blo ɔ it/drink milk.
• If yu tan lɛk se yu de slip bad bad wan ɔ yu nɔ gɛt layf.

Us kwɛstyɔn dɛn a fɔ aks mi dɔktɔ?

Na sɔm impɔtant kwɛstyɔn dɛn we yu fɔ aks yu pikin in dɔktɔ:

• Us kayn TAPVR mi pikin gɛt?
• Yu tink se mi pikin go nid fɔ gɛt ɔpreshɔn fɔ di sɛkɔn tɛm?
• Ɔmɔs ɔpreshɔn yu dɔn gɛt fɔ mek TAPVR fayn?

Wan impɔtant mɛsej we pɔsin kin kɛr go na os

Yu go dɔn fala yu dɔktɔ in advays fɔ gɛt wɛlbɔdi we yu gɛt bɛlɛ. Bɔt sɔntɛnde, pikin we dɛn jɔs bɔn kin gɛt at prɔblɛm. Nɔto ɛnibɔdi in fɔlt. Wit di advans mεdikal sayɛns tide, yu pikin kin εkspεkt fכ bεtεh pas di pikin dεm fכ di jεnereshכn dεm we bin de bifo. Ɔspitul tritmɛnt kin rili wok.

Mɛmba se pan ɔl we TAPVR na siriɔs sik, if dɛn no di sik kwik kwik wan ɛn du di rayt ɔpreshɔn, pikin dɛn gɛt bɔku chans fɔ liv gud layf. Afta dɛn dɔn du di ɔpreshɔn, i rili impɔtant fɔ kɛr yu pikin go fɔ mek dɛn go chɛk am ɔltɛm. Dis na fɔ mek dɛn go ebul fɔ wach yu pikin in wɛlbɔdi ɛn dɛn go ebul fɔ trit ɛni prɔblɛm we go apin kwik kwik wan. Nɔto yu wan, dɔktɔ ɛn wɛlbɔdi wokman dɛn de fɔ ɛp yu ɛn yu pikin.

` TAPVR, hat sik, pikin, ɔpreshɔn, pulmonari vein, saynosis, sik dɛn we dɛn bɔn wit