If pɔsin sik ɛn put am na ɔspitul bikɔs i nɔ gɛt bɛtɛ wata ɛn sɔl na in bɔdi, dɔktɔ dɛn go gi am salin fɔ mek i nɔ gɛt bɛtɛ wata. Dat na nɔmal tin. Bɔt yu no se sɔntɛnde, if di sodium we nɔ de na di bɔdi go ɔp wantɛm wantɛm ɛn kwik kwik wan, dat kin pwɛl di bren? Na dat wi kin kɔl wan rare bɔt siriɔs kɔndishɔn we dɛn kɔl Central Pontine Myelinolysis. Pan ɔl we di nem kɔmplikt smɔl, lɛ wi tɔk bɔt am simpul wan.
Fɔ tɔk am simpul wan, us kayn tin dis de apin?
Dis na sik we gɛt fɔ du wit di nervɔs sistɛm. di ilektrikal signal dεm we di bכdi nid de travul tru di nεv sεl dεm (nyuron dεm) na wi bren. wan tin de we de kכba rawnd dεn nεv sεl dεm ya we de protεkt. Wi kin kɔl am di maylin sheath . I tan lɛk di plastic sheath we de rawnd ilɛktrik waya. dis maylin sεt na di wan we de alaw di ilektrikal signal dεm fכ travul kwik εn witout nכ tin we de ambɔg am.
sεntri Pכntin Maylinolysis (CPM) de apin we di maylin sεt dεm na wan spεsifi k εria na di bren, spεshal wan di pons, dεn dכn pwεl. Dis damej kin afɛkt di wok we difrɛn pat dɛn na di bɔdi de du.
sכmtεm, insay lεk 10% pan di kes dεm, dis damej kin afekt nכto di pons nכmכ, bכt כda pat dεm na di bren. So, pipul dεn kin no dis kכndyushכn wit כda bכdi nem. Dat na di sik we dɛn kɔl Osmotic Demyelination Syndrome (ODS) .
Dis kɔndishɔn nɔr kin kɔmɔn, bɔt dɛn dɔn si se lɛk 2.5% pan di sik pipul dɛm wae dɛn admit na intensiv kia yunit (ICU) kin gɛt risk fɔ gɛt ODS.
Wetin na di rizin we mek dis kayn tin de apin?
di men rizin fכ dis na dat we di bכdi in sכdiכm lεvεl (we na wetin de insay di sכl we wi de it) rili lכw, i de inkrεs wan wan εn kwik kwik wan . Dis risk kin go ɔp mɔ we di bɔdi in sodium lɛvɛl dɔn smɔl fɔ pas tu dez ɛn dɛn de gi tritmɛnt.
Di impɔtant tin na dat, dis nɔto sɔntin we wi de it ɔ drink. Dis na sɔntin we kin apin na ɔspitul, we dɛn gi sɔdiɔm insay di bɛlɛ , dat na tru salin, as mɛrɛsin.
Tink bɔt am dis we. Pɔsin dɔn de vɔmit bɔku bɔku wan fɔ sɔm dez, ɔ i gɛt dayarɛa. Dɔn, nɔto wata nɔmɔ, bɔt sɔl dɛn lɛk sɔdiɔm kin lɔs na dɛn bɔdi. We dɛn kam na ɔspitul, dɛn sodium lɛvɛl kin rili smɔl. Naw di dɔktɔ dɛn de gi dɛn salin fɔ tray fɔ mek dɛn sodium lɛvɛl kam bak to nɔmal. Bɔt if dɛn nɔ no bɔt di ɔda tin dɛn we kin mek di pɔsin gɛt prɔblɛm, dɛn kin ebul fɔ mek di sodium lɛvɛl go ɔp smɔl kwik kwik wan.
We dat apin, di wata we de insay di bren sɛl dɛn kin lik kɔmɔt na di sɛl dɛn wantɛm wantɛm. Di sɛl dɛn kin smɔl lɛk grep we dɔn dray. Dis chenj we kin apin wantɛm wantɛm na in kin pwɛl di maylin sheath dɛn we wi bin tɔk bɔt.
Udat dɛn de pan big risk?
Nɔto ɔlman kin gɛt dis sik we dɛn sodium lɛvɛl go ɔp tumɔs kwik, bɔt sɔm pipul dɛn kin gɛt mɔ risk.
| Risk grup | Tɔk bɔt |
|---|---|
| Pipul dɛn we gɛt adikshɔn to rɔm | I nɔ kin gɛt bɛtɛ tin fɔ it ɛn di sɔl nɔ kin balans na tin we kin apin to pipul dɛn we kin drink rɔm fɔ lɔng tɛm. |
| Liva transplant pasɛnt dɛn | Dis risk kin bɔku mɔ fɔ di wan dɛn we dɛn dɔn du ɔpreshɔn fɔ transplant dɛn liva. |
| Hyperemesis we uman gɛt bɛlɛ | Hyperemesis Gravidarum, na wan sik we de mek yu nɔ de stɔp fɔ vɔmit we yu gɛt bɛlɛ, kin mek di sɔl we de na di bɔdi go dɔŋ bad bad wan. |
| Sik dɛn we kin de fɔ lɔng tɛm | Ɛni ɔda tin we kin apin to pɔsin fɔ lɔng tɛm we kin mek di bɔdi wik ɔ we kin mek i nɔ gɛt bɛtɛ it, dat kin mek i gɛt mɔ prɔblɛm. |
Wetin na di sayn dɛm fɔ dis sik?
Bɔrku tɛm, di sayn dɛm kin bigin fɔ sho insay tu to tri dez afta dɛn dɔn kɔrɛkt di sodium lɛvɛl na di bɔdi. Sɔm sayn dɛm de wae kin kam kwik, ɛn sɔm kayn sayn dɛm wae kin kam afta sɔm wiks.
| CPM simptom dɛn | |
|---|---|
| Di fɔs sayn dɛm (insay 2-3 dez) . | |
| |
| Di sayn dɛm wae kin kam leta (afta sɔm wik ɔr mɔnt) . | |
|
Bɔt nɔ fred. Pan ɔl we dɛn bin tink fɔs se di nɔmba fɔ pipul dɛn we de day bɔku, dɛn bin no dat bay we dɛn du ɔtopsi. Akɔdin to nyu data, 94% pan di pipul dɛm wae gɛt dis sik kin liv . Dɔn bak, bitwin 25% ɛn 40% pan dɛn kin wɛl kpatakpata . Bɔt bitwin 25% ɛn 30% kin lɛf wit sɔm pɔrmɛnt disabiliti.
Aw dɔktɔ dɛn kin fɛn dis?
Di bɛst we fɔ no dis sik na fɔ du MRI (Magnetic Resonance Imaging) skan . Yu dɔktɔ go luk di MRI pikchɔ dɛn na yu bren ɛn chɛk fɔ patikyula chenj dɛn we de sho se di maylin swɛt dɛn dɔn pwɛl.
Sɔntɛnde dis damej nɔ kin sho pan MRI wantɛm wantɛm, so yu dɔktɔ kin aks yu fɔ du ɔda MRI insay wan ɔ tu wik.
CPM kin luk lεk sεvεra כda kכndishכn dεm pan MRI imej dεm. So, dɔktɔ dɛn kin rili tek tɛm fɔ mek dɛn nɔ kɔnfyus dis sik wit dɛn sik ya we de kam biɛn ya.
- Mɔltipɛl Sklɛrosis
- Awtoimyun ɔ infɛkshɔn ɛnsɛfalaytis (inflameshɔn na di bren) .
- Sɛntral nervɔs sistɛm vaskulaytis
- Sɔm kayn kansa dɛn
If di MRI nɔmɔ nɔ ebul fɔ sho klia wan di damej, di dɔktɔ go du mɔ dip nyurolɔjik ɛgzam. dis kin inklud tεst dεm we de mכsu ilektrikal signal dεm na di bren, lεk EEG (electroencephalography).
Aw fɔ trit am? Prɛvenshɔn na di bɛst!
Infakt, di men tritmɛnt fɔ Sɛntral Pɔntin Maylinɔlaysis na fɔ mek di sik nɔ apin .
I rili impɔtant fɔ mek yu mɛdikal tim no bɔt ɛni risk factor wae yu gɛt (fɔ ɛgzampul, if yu de drink rɔm, if yu gɛt ɔda mɛdikal kɔndishɔn) so dat dɛn go sef ɛn sloslo inkrisayz yu sodium lɛvɛl.
If yu gɛt dis sik, di tritmɛnt go dipen pan di sayn dɛm wae yu de gɛt. Bɔrku tɛm, dɛn go nid fɔ gɛt sɔm mɔnt fɔ gɛt fizik tritmɛnt ɛn ɔda tritmɛnt fɔ rihabiliteshɔn.
If yu gɛt sayn dɛn we fiba di sik we dɛn kɔl Pakinsin, lɛk we yu de shek shek, yu dɔktɔ kin gi yu mɛrɛsin dɛn we gɛt dopaminergic .
We yu de na ɔspitul, fɔ mek yu nɔ gɛt ɔda sɛkɔndari kɔmplikeshɔn na impɔtant pat bak pan tritmɛnt. Di mɛdikal tim go de wach tin dɛn lɛk:
- Dipen pan wan ventilator
- Infεkshכn dεm na di urinary tract
- Nyumonia
- Blɔd we de klɔt na di vein (Dip vein thrombosis) .
- Mɔsul dɛn we de atrofi
Ivin klinik trial dɛn de we dɛn de du fɔ dis sik, ɛn yu dɔktɔ kin tɛl yu fɔ du wan.
Mɛsej we dɛn kin kɛr go na os
- Sεntri Pכntin Maylinכlaysis (CPM) na siriכs kכndyushכn we de kכz fכ damej di maylin sεt dεm na di bren bikoz fכ di lכw sכdiכm (sכlt) lεvεl na di bכdi inkrεs wan wan εn kwik kwik wan.
- Di bɛst tritmɛnt fɔ dis na fɔ mek dɛn nɔ gɛt dis sik . Bifo yu gɛt ɛni tritmɛnt, tɛl yu dɔktɔ yu kɔmplit mɛdikal istri, mɔ bɔt aw yu de drink rɔm ɔ ɔda sik dɛn.
- If dis sik apin, di chans fɔ liv kin bɔku, bɔt fɔ wɛl ful wan kin tek lɔng tɛm, ivin fɔ trit yu bɔdi.
- If yu ɔ pɔsin we yu sabi gɛt dɛn sik ya, mɔ afta dɛn dɔn du sɔdiɔm riplesmɛnt tɛrapi na ɔspitul, tɛl dɔktɔ wantɛm wantɛm.











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