Behçet-a Natna hi i hre tawh em? A hming hi a mak deuh mai thei. Mahse a takah chuan kan taksa peng hrang hrang tam tak nghawng thei, complex, mahse manageable condition a ni. Chuvangin, vawiin hian chipchiar takin sawi ila, awlsam takin, ṭhian nena inbiakna ang maiin.
Behçet-a Natna hi eng nge ni?
A awlsam zawngin sawi ila, Behçet natna hi kan taksa chhunga
thisen kalna kawng hrang hranga natna awm reng a ni. Doctor-te chuan ``vasculitis'' an ti bawk.Hei hi thisen kalna kawng a hring, a sen, a na a ni. Thisen kalna kawng lian (arteries) leh thisen kalna kawng te (veins) te pawh a nghawng thei a ni. He natna hi a chang chuan "Silk Road disease" tia sawi a ni a, a chhan chu history-ah Silk Road dung hmun hrang hrangah a hluar hle a ni.
He natna hi tuin nge vei tam zawk?
Behçet natna hian khawvela tu pawh a nghawng thei a ni. Mahse, ram thenkhatah chuan a tam zawk. Entirnan, Turkey hmar lam, Mediterranean tuipui chhehvel ram, Middle East leh East Asia-ah te a tam zawk. United States ang ramah chuan a tam lo hle.
Kum 20 leh 30 inkar atanga a lan chhuah tan tlangpui a, mahse kum eng pawhah a awm thei. A tirah chuan hmeichhia leh mipa te pawh inang tlangin a nghawng nia ngaih ni mah se, zirchianna ṭhenkhat chuan
mipaah hian he natna hi an vei tam deuh niin an sawi .
He natna lan chhuah dan engte nge ni? Engtin nge kan awm?
Hei hi a pawimawh ber a ni. Behçet natna lan chhuah dan hi mi hrang hrangah a inang lo thei. Chumi awmzia chu i symptoms neihte chu mi dang symptoms nen a inang lo thei tihna a ni. Mahse key symptom tlemte a awm a, chu chu a awm fo thin.
Kawngkhar natna
Hei hi
mi tam takin an hriat hmasak ber a ni . Kan kâa kan hmuh ṭhin cancer natna ang mai a ni a, mahse a
lian zawk a, a tam zawk a, a na zawk bawk . Mi thenkhat chuan natna lanchhuahna dang a lan hmain heng hmui natna hi an nei thei a ni. An hmuiah te, leiah te, leh hmui chhungah te an lang thei.
Imagine, you constantly get mouth ulcers , a na lutuk a, ei leh in pawh i ei thei lo va, damdawi i ei hnuah pawh ni engemaw zat hnuah a rawn let leh thin. Chutiang dinhmun chu a ni.
Mipat hmeichhiatna lama hliam
Kawng natna ang bawkin mipat hmeichhiatna lam natna pawh a awm thei bawk. Hengte hi a hrehawm thei bawk. Mipaah pawh scrotum-ah leh hmeichhiaah vulva-ah an awm thei bawk. Amaherawhchu, hmui natna angin an awm lo.
Mit natna a awm
Mit a hring (inflammation) pawh hi he natna chhinchhiahna pawi tak a ni. Hei hian
a ti sen thei a, natna a thlen thei a, mit a ti fiah lo thei a, êng a hriat theih bawk a, mit a ti tui thei bawk . Enkawl that loh chuan
mitdelna tluantling a thlen thei a ni.Chance a awm. Hetiang mit chhiatna hi Middle East leh Japan ang ramah a tam hle niin report a awm bawk.
Vun lama harsatna nei
Vun lama harsatna pawh a awm fo. A châng chuan, pimple ang chi blisters leh red nodules (erythema nodosum) a lo lang thei bawk. Heng bumps te hi khawih a hrehawm hle. Hun dangah chuan vun ulcer a lo awm thei bawk. Chung zinga ṭhenkhat chu a chunglam a ni a, ṭhenkhat erawh chu a thuk thei thung. Thil danglam tak dang chu
vun chu a hrual emaw, a hliam emaw a nih chuan a hmun chu a sen ang a, ni engemaw zat chhungin blister te tak te a lo lang ang Doctor-te chuan hei hi "positive patergy test" tiin an sawi.
Joint natna
Heng damlote zingah hian ruh natna pawh a tam hle. A bik takin
ke ruh, khup, elbow, leh hips te a nghawng a ni . A ruh chu a hring thei a, a sen a, khawih pawhin a na thei bawk. Mahse, a tlangpuiin ruhte chu a tichhe vek lo.
Vein natna (vein inflammation) a awm
Thisen kalna chhunga inflammation hian
thisen a tikhawlo thei a, a tikhawlo thei a , a nih loh leh thisen kalna kawng a tikhawlo vek thei bawk. Hei hian vun hnaih tak, superficial veins leh taksa chhunga thuk tak vein thuk tak takte pawh a nghawng thei a ni. A châng chuan kan taksaa vein lian ber, vena cava chu a nghawng thei a, chu chuan hriselna lama harsatna lian tak a thlen thei a ni. Heng thisen kalna kawng harsatna hi inflammation vang a ni a, thisen zam (blood clotting system) a chhiatna vang a ni lo.
Thluak inrawlhna
A chang chuan he natna hian thluak a nghawng thei bawk. A bik takin thluak khuh tu membrane (meninges) te hi a ni. Tichuan symptoms te
chu khawsik, lu na nasa tak, kawng na tak, kal laiin chetna inrualrem harsa tih te hi a lang thei a ni. A châng chuan
, stroke pawh a awm thei bawk. Hei hi thluaka thisen kalna kawng a inkhar emaw, a puak emaw a nih chuan a ni.
Gastrointestinal (GI) kawng hrang hranga thil awm dan
Digestive system-ah pawh harsatna a awm thei a, chu chu intestines-ah a awm thei bawk.
Pum natna leh thisen chhuahna ang chi thil i hmu mai thei . Hei hi a chhan chu hmui leh mipat hmeichhiatna hmuna hliam te, chubakah intestines chhunga hliam te a awm vang a ni. Heng intestine-a hliam te hi a hlauhawm deuh a, a chhan chu intestine atanga thisen chhuak emaw, rupture emaw a thlen thei a ni.
Organ dangte chunga nghawng a neih dan
A tlem hle nachungin, he natna hian taksa peng dang, lung, kal, leh thisen kalna kawng lian tak tak (aorta) te pawh a nghawng thei bawk.
Engvangin nge Behçet natna hi a lo awm? Eng nge a chhan?
He natna thlen chhan dik tak hi hriat a la ni lo . Scientist ten an la zirchiang mek a ni. Theory pakhat chu ``autoimmune disorder`` a ni thei tihna a
ni.. He attack hi a chunga kan sawi tak inflammatory conditions thlentu a ni. Gene marker thenkhat, `(HLA-B5)` leh `(HLA-B51) te hi he natna vei thenkhatah hian hmuh tur a awm a. Mahse, heng gene marker nei zawng zawng hian Behçet natna hi an vei vek lo. Chuvangin genes chauh hi a chhan nia sawi theih a ni lo. Researcher te pawhin
he natna hi genetically predisposed nei te zingah hian he natna hi infection (bacterial emaw viral emaw) avanga lo awm thei tih ngaihdan a awm niin an ngai bawk Hei hian a awmzia chu genetic leh environmental factor pahnih hian a nghawng thei tihna a ni.
Tute nge he natna vei theihna sang zawk?
Mi thenkhat chuan midang aiin he natna hi an vei theihna a sang zawk:
- He natna vei tamna hmuna chengte (e.g. Turkey, Middle East).
- Kum 20 leh 40 inkar te .
- Genes bik thenkhat (HLA-B5 emaw HLA-B51 emaw) nei te .
- Mipa (hmeichhia aiin mipa hian he natna hi kai an hlauhawm zawk).
Engtin nge he natna hi dik taka hriat theih a nih? (Diagnosis) tih a ni.
Behçet natna hriat theihna tur
laboratory test pakhat mah a awm lo . Doctor-te chuan i natna lan chhuah dan a zirin an enfiah thin. An zawng ber chu:
- Kawngkhar natna lo lang leh fo (a tlangpuiin kum khatah vawi thum aia tam) .
- Chu bakah, a hnuaia mize pahnih tal chu a awm tur a ni :
- Mipat hmeichhiatna hmuna hliam.
- Mit natna (inflammation) a awm .
- Vun lama harsatna nei.
- A positive pathergy test - Hei hian vun a hliam emaw, a hliam emaw a nih hnu ni engemaw zat chhungin a sen, blister ang chi a lo lang tihna a ni. Hei hian immune system hnathawh that dan tur ngaihtuahna a pe a ni.
He natna hi dik taka hriat theih nan chuan
Behçet natna ang chi hmui natna thlentu natna dangte chu paih chhuah a ngai a ni . Entirnan, `(systemic lupus)`, `(Crohn natna)` (intestines-a inflammatory condition), leh `(vasculitis)` chi dang. I doctor chuan heng natna dangte hi a awm loh nan thisen test a ti thei ang.
Hei hi thlahtu natna a ni em?
Behçet natna hi thlahtute atanga lo chhuak a ni tih finfiahna chiang tak a awm lo . A tam zawk hi chu random takin a thleng a, chhungkaw history engmah a awm lo. Chhungkaw pakhata mi engemaw zatah hian za zela tlemte chauh hmuhchhuah ni mah se, thlahtute atanga lo piang chhuak chiang tak a awm lo.
Hei hi eng enkawlna nge ni? (Tihdamna)
He natna hi damdawi a la awm lo . Mahse, natna lan chhuahna enkawlna atana pui thei damdawi engemaw zat a awm a:
- Corticosteroids (e.g., prednisone): Hengte hi a enkawlna ber a ni. Heng damdawi te hian inflammation leh immune system overactivity a tiziaawm a ni.
- Colchicine (Colcrys®): Hei hian hmui natna, serh natna leh a chang chuan ruh natna te a pui thin.
- Immunosuppressant damdawi dang : Entirnan, methotrexate (Trexall®, Rasuvo®), azathioprine (Imuran®, Azasan®), cyclophosphamide (Cytoxan®, Neosar®), leh cyclosporine (Gengraf®, Neoral®, Sandimmune®) te hi a ni. A na zawkah chuan anti-TNF (Tumor Necrosis Factor) biologics infliximab (Remicade®), etanercept (Enbrel®), leh tocilizumab (Actemra®) te pawh hman a ni bawk.
Pawimawh: Heng immunosuppressant damdawi te hian i taksain natna a do theihna a ti tlem thei a, chu chuan natna dang i vei theihna a tipung a ni.
- Apremilast (Otezla®) : Hei hi ei tur tablet a ni. Behçet natna vei te hmui natna enkawlna atana pawm a ni.
I dinhmun a nasat dan azirin, i doctor chuan heng damdawi te hi i hman hmain mittui tlakna, hmui silna, leh vun hriak chi hrang hrang hmangin a natna lan chhuah dan control a tum thei a ni.
He natna nen hian eng ang beiseina nge i neih theih ang?
Behçet's hi
natna khirh tak a ni . Chumi awmzia chu, enkawl ni mahse, a chang chuan a bo thei a, a lo lang leh thei tihna a ni. Hei hian enkawlna a hlawhtlin zia chiang taka sawi a harsa hle. Damlo tam tak chuan an dam chhungin a chang chuan heng symptoms te hi an hmachhawn a ngai dawn a ni. Mahse,
mi tam zawk chuan nun pangngai, famkim an hmang thei a ni .
He natna hi engtin nge hlawhtling taka kan hmachhawn theih ang?
He natna vei lai hian tanpui theih dan kawng hrang hrang a awm a:
- Chawlh hahdam leh thiltih inthlauhna : Exercise regimen mumal tak neih hian i taksa a ti nuam ang a, ruh natna leh harsatna hmun dangte a tiziaawm ang. Tin, natna lanchhuahna a nasat laiin chawlh hahdamna hun engemaw chen hman hi i rilru hriselna atan a tha a, natna lanchhuahnain nghawng a neih pawh a ti tlem thei bawk.
- Shared experience and community : Hei hian mi dangte dinhmun inang nei zawng chhuak leh biak tihna a ni. Hei hi a harsa thei hle a, a chhan chu a dinhmun hi a tlem hle. Mahse i doctor chuan chutiang thil tawn tawhte zawng turin a pui thei che a ni.
He natna hian thihna a thlen thei em?
He natna avanga thihna
hi 5% vel a ni.Thihna thlentu ber chu intestinal perforation, stroke, leh rupture of aneurysms te hi a ni. Behçet natna hi direct-a thihna thlentu ni lo mah se, taksa pum puiah hriselna lama harsatna leh damdawi lam harsatna hrang hrang a thlen thei a, chung zinga tam tak chu a na hle. Mahse,
natna hi hlawhtling taka enkawl a, nun pangngaia nun theih a ni . A bîk takin exercise i neih fo a, i chawlh a, chutiang bawka thil tawn ve tho mi dangte i biak chuan.
A tawp berah chuan heng thilte hi hre reng ang che!
Behçet natna hi thil buaithlak leh nuam lo tak a ni thei. Mahse hei hi hre reng ang che:
- Hei hi enkawl theih natna a ni.
- Heng symptoms te hi i neih chuan doctor thurawn zawng nghal rawh .
- Enkawlna dik leh nunphung thlak danglamin nun pangngai nun i tum thei a ni .
- Nangmah chauhin hrehawm tuar suh la, support group emaw damlo dang emaw nen inzawm rawh .
He thu hi i tan a tangkai ngei ka beisei. Hrisel takin awm rawh!
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