Ni tam tak chhung chu a châng chuan i ruh a na a, i khawsik a, i ruh a na em? I vunah pink rash a awm mai thei. Heng symptoms te hi i neih chuan vawiin a kan sawi tur hi i nei mai thei: Adult-Onset Still’s Disease (AOSD). Hei hi thil awm lo tak a ni a, mahse hriat reng a pawimawh.
Puitling-Onset Still’s Disease (AOSD) hi eng nge ni?
A awlsam zawngin, AOSD hi inflammatory arthritis a ni a, taksa pum pui a nghawng a, ruhkawr a ti na a, a na bawk . Ruh na, taksa ruh na, nitin khawsik lo thleng leh chhuak, vun natna a thlen thei bawk. Chu bakah, systemic symptom dang pawh a awm thei bawk.
He natna hi `AOSD` tia koh a ni a, puitling ang chi natna `Still's disease` emaw `(Juvenile Idiopathic Arthritis - JIA)` naupangte zingah a awm a ni. Kum 16 leh 35 inkar thalai a vei tam ber a, naupang natna ang bawkin a chang chuan kum khat aia rei lovah a bo thei a, a nih loh leh hun kal zelah a lo kal leh thei bawk. Symptoms ``flares`` hi a lo kal leh chhuak fo thei a, a nih loh leh rei tak a lo kal thei bawk. Tin, heng symptoms te hi a chang chuan a na lo thei hle a, a chang chuan a na hle thei bawk. Mahse, symptoms a lo lan hunah control turin damdawi tha tak tak a awm.
He natna chi hrang hrang hi engte nge ni?
AOSD hian mi zawng zawng a nghawng dan a inang lo. Engtin nge a nghawng dawn che tih chiang taka sawi a harsa khawp mai. Mahse doctor-te chuan symptoms hi kawng pathumin a lang tlangpui tih an hmuchhuak a:
AOSD monophasic `(AOSD pakhat)`
"Monophasic" tih hian symptoms chu vawi khat chauh a lang tihna a ni . Hei hi kar engemaw zat emaw thla engemaw zat emaw a daih thei a, mahse kum khat aia rei lo a ni. Hetiang chi hi a intan nghal thei a, a bo nghal vat bawk. Ngaihtuah teh, kan thianpa Kasun hian heng symptoms te hi khawsik leh ruh natna nen a nei a, thla thum vel hnuah damdawi hmangin a dam vek a, a lo kir leh tawh ngai lo. Chu chu he `(Monophasic AOSD)` tih hi a ni.
Polyphasic AOSD `(AOSD chi hrang hrang)`
"Polyphasic" tih hian symptoms vawi tam tak a awm tihna a ni . Chûngte chu a hun laiin a thleng thei a, a châng chuan kar engemaw zât, thla engemaw zât, a nih loh leh kum engemaw zât hnuah pawh a thleng thei a ni. Mahse, hun kal zelah heng symptoms te hi a tawi deuh a, a na lo deuh fo bawk.
Chronic AOSD `(AOSD rei tak)`
"Chronic" tih hian symptoms kal zel i nei tihna a ni a, a nih loh leh condition chu a flare up fo tihna a ni . Rheumatoid Arthritis ang natna ang bawkin he natna (Chronic AOSD) hian i ruhte chu hun rei tak chhung a tichhe thei a ni.
A chi pathumte hi a tam emaw a tlem emaw chuan a inang tlangin hmuh a ni. Mahse, a tir lamah chuan eng chi nge tih chiang taka sawi theih a ni lo. A châng chuan "monophasic" emaw "polyphasic" emaw anga ngaih ni mah se, a hnuah "chronic" `AOSD` a lo ni thei bawk.
AOSD natna lan chhuah dan chu engte nge ni?
He natnaah hian a lan chhuah dan tlangpui bakah hian a lan chhuah dan tlangpui dang a awm bawk.
A lan chhuah dan ber
- Fever: Symptoms active a nih chuan mi tam zawk chuan ni khatah vawi hnih , zing vawi khat leh tlaiah vawi khat an nei thin . He khawsik hi a tlangpuiin 39 degree Celsius (102 degree Fahrenheit) aia sang a ni thei.
- Skin rash: Pink, a châng chuan salmon rawng hring hring hi khawsik a san ber laiin a lang tlangpui . Khawsik a reh chuan a bo mai thei. A tir lamah chuan rilru, kut leh keah a lang tlangpui a, mahse taksa pum puiah a darh thei.
- Joint pain: Mi tam tak chuan joint pain , leh mi tam tak chuan swelling leh stiffness an nei thei bawk. A tirah chuan ruh tlemte chauh a nghawng thei a, mahse hun kal zelah he natna hian taksa pum puia ruh a nghawng thei a ni.
- Muscle pain: I muscles pawh a na thei , a bik takin khawsik a san ber lai hian.
Symptoms langsar dangte
- Hrawk thip.
- Pum a na.
- Chauhna nasa tak neia inhriatna.
- Malaise hi malaise tih hriatna, hrisel lohna hriatna a ni.
AOSD neih hi engtin nge a awm?
Dik tak chuan, a tir lamah chuan AOSD hi virus natna emaw, common cold emaw ang maiin a lang . Khawsik, taksa na, leh ril na ang chi symptoms te hi natna tlanglawn dang tam tak nen a inang hle. Kar hnih atanga kar thum hnuah pawh heng symptoms te hi a reh loh chuan nang leh i doctor te hian rinhlelhna tlem in nei tan mai thei.
Engvangin nge he AOSD natna hi a lo awm?
I taksaa inflammation hi AOSD symptoms thlentu a ni . A tlangpuiin kan immune system hian he inflammation hi infection do nan leh hliam tihdam nan a siam thin. Hun eng emaw chen atan a ni tur a ni tak zet. But in some diseases, like AOSD, your immune system has a problem with something , chu chuan he inflammation hi a thlen reng a, infection do tur emaw, hliam dam tur emaw a awm loh pawhin.
Hetiang thil a thlen chhan hi zirchiangtute chuan an la hre chiang lo. Juvenile Idiopathic Arthritis ang bawkin Adult Still's Disease hi " idiopathic " an ti a. Chu chu a chhan dik tak hriat a ni lo tihna a ni . Genetic a ni lo niin a lang.
Engtin nge AOSD hi hriat chhuah a nih?
AOSD natna lan chhuah dan hi natna dang tam tak nen a inang hle. Tin, natna hlauhawm tak a nih avangin doctor-te chuan a tir lamah chuan an ringhlel lo mai thei bawk. Chuvangin diagnosis dik tak hmuh theih nan hun engemaw chen a ngai thei .
I natna lan chhuah dan leh i damdawi lam chanchin a enfiah hnuah i doctor chuan i dinhmun hriat chian nan thisen test leh imaging test a ti ang. X-ray emaw ultrasound scan ang chi test hian i ruhroah inflammation leh swelling a awm tih i hmu thei a ni. Thisen test hian natna dang a awm lo thei. I thisen test-naah ferritin level sang tak a awm a, chubakah white blood cell count sang tak a awm bawk a nih chuan , heng symptoms te hian AOSD a tilang thei a ni.
AOSD enkawlna tur engte nge ni?
Doctor te chuan AOSD hi anti- inflammatory drugs chi hrang hrang hmangin an enkawl thin . Mi tin tana tha ber damdawi chi hrang hrang a inang lo. I natna lan chhuahna atana tha ber tur zawn nan experiment engemaw zat a ngai mai thei. A dik tak i hmuh hnuah chuan damdawi hi rei tak i ei chhunzawm a ngai mai thei a, symptom i neih loh lai pawhin. Chumi hnuah chauh chuan inflammation chu a na zual zel tur chu i titawp thei ang.
Damdawi thenkhat chu rei tak hman a nih chuan side effect a nei thei. Chutiang damdawi i ei a nih chuan i doctor chuan side effect a awm loh nan a chang chuan a thlak danglam thin.
Enkawlna atana hman tur damdawi thenkhat chu:
- Nonsteroidal anti-inflammatory drugs (NSAIDs) te pawh a awm bawk.
- Corticosteroids (Synthetic steroids) `(Corticosteroids - steroid siam chhuah)`.
- Natna tidanglam thei anti-rheumatic drugs (DMARDs) te.
- Biological damdawi `(Biologics)` tih a ni.
AOSD hi engtiang chiahin nge a serious?
A tam zawkah chuan AOSD hian hun rei tak chhunga i hriselna aiin i nunphung a nghawng nasa zawk . Chu chu, lungawi lohna a thlen thei a, nitin hnathawhna a tibuai thei a, mahse hun rei tak chhung chu i taksa tan a tichhe hauh lo.
Mahse, mi ṭhenkhat chuan arthritis , a zual zel a, a chhe thei hle a ni . Hei hi chronic AOSD-ah hian chi dang aiin a thleng tam zawk. I ruh natna chu a na tawk a, rei tak a awm chuan zawi zawiin a chhe thei a ni. I ruh vel cushioning chu inflammation vangin a chhe zel a, i ruh chu a hmun atanga chhuakin a kal tan thei a ni. Hetianga swelling leh joint degeneration hian i joint ah deformities na tak a thlen thei a ni.
A tlem hle a, AOSD nena inzawm inflammatory conditions hian i chhungril taksa peng hrang hrang, i thinlung leh lung te pawh a nghawng thei bawk. Hei hian harsatna lian zawk a thlen thei a ni. AOSD ngei pawh hian i dam chhung a nghawng lo mai thei a, mahse heng secondary conditions te hian thihna a thlen thei lo.
Eng harsatna lian tak nge thleng thei?
Harsatna awm lo mahse na tak tak te chu:
- Pericarditis natna (Pericarditis) a ni.
- Myocarditis natna (Myocarditis) a ni.
- Disseminated intravascular coagulopathy (DIC) a awm bawk.
- Pulmonary arterial-a thisen sang lutuk.
- Pleural effusion a awm thin.
- Interstitial lung natna a awm.
- Hemophagocytic lymphohistiocytosis (HLH) hmanga tihdam theih a ni.
AOSD hi a dam kim thei ang em?
Damdawi hian AOSD a tidam thei lo a , mahse a natna lan chhuah dan tihtawp nan a pui thei a ni. Mi thenkhat tan chuan symptoms hi hun kal zelah a bo vek thei a, a lo let leh tawh ngai lo. Hei hi "remission"-a luh emaw, natna chu a reh lutuk emaw an ti a ni. "Remission"-ah i lut a nih chuan i damdawi ei kha i chawlhsan thei a ni. Mahse mi thenkhat tan chuan AOSD hi a bo tak tak ngai lo. An inflammation control nan hun tiam nei lovin damdawi an ei a ngai mai thei.
Eng ang dinhmun nge i beisei theih ang tih chiang taka sawi a harsa khawp mai. Mahse, doctor ṭhenkhat chuan i natna lan chhuah hmasak berte chuan clue a pe thei che niin an ngai . I ruh ruh na leh hliam i neih chuan rei tak a daih a rinawm.
AOSD nena kan awm chhung hian engtin nge kan in enkawl ang?
AOSD vei tam tak chuan damdawi dik tak hmangin nun pangngai, nuam tak an hmang thei a ni . Mi dangte tan chuan a chang chuan natna khirh tak leh hahna rei tak an tawk a, chu chuan an nitin nun a nghawng thei a ni. AOSD symptoms hian a tibuai chhunzawm zel che emaw, tibuai lo emaw pawh nise, i damdawi ei atang hian side effects i nei thei a, chu chu i taksa rihna sang leh mood swing te hi a ni.
I thunun theih loh thil avanga nun a buai reng hian, mahni invenna bulpui (basic self-care) ngaihtuah a pawimawh zawk . Mut tha, ei leh in tha tak, leh exercise neih fo, low-impact exercise te hian a pumpuiah i rilru a hahdam thei a ni.
AOSD hi thil mak tak a ni a, a chhan hriat lohvin a lo thleng nghal vek a ni. A lo awm hmasak ber ṭumin hun rei tak chhung chu natna danglam takin i inhria thei a ni. I doctor chuan eng thil nge thleng tih hriat theih nan hun leh tha engemaw zat a mamawh mai thei. Vanneihthlak takin i natna hmuhchhuah a nih veleh enkawlna i tan thei a, zawi zawiin i dam tan thei bawk.
I tâna ṭha ber tûr enkawlna zawng tûr chuan trial and error engemaw zât a ngai thei a, mahse mi tam zâwk chuan an natna lan chhuah dân chu an enkawl thei a, damdawi hmangin harsatna lian tak tak an veng thei bawk AOSD hi eng chen pawh nei mah la, i doctor chu a enkawlna kawngah i thawhpui tha ber a ni ang.
A tawp berah chuan take-home message
- AOSD hi inflammatory joint disease hmuh tur awm lo tak a ni a, taksa pum a nghawng a, puitlingah a awm thin.
- Khawsik fo, vun vun na, ruh leh ruh natna te hi a lan chhuah dan ber a ni.
- Hei hi a chhan dik tak hriat a ni lo a, mahse a chhan ber chu immune system hnathawh dan inthlak danglam avanga inflammation vang a ni.
- A hriat theih nan hun rei tak a la ngai thei a, a chhan chu a natna lan chhuah dan hi natna dang nen a inang reng a ni.
- Damdawi hian natna lan chhuah dan a thunun thei a, , thenkhat tan chuan natna chu a tidam vek thei bawk.
- Enkawlna dik leh mahni inenkawlna tha tak nen chuan mi tam zawk chuan nun pangngaiin an khawsa thei a ni.
- Heng symptoms te hi i neih chuan doctor pan ngei ngei tur a ni a, thurawn la rawh . Ngaihtuah buai suh, engkim chinfelna a awm.
Hriselna tha neih duhsakna kan hlan e!
` Puitling Still natna, AOSD, ruh natna, khawsik, vun rawng, autoimmune natna, enkawlna











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