Kan taksa chhungah hian thil tam tak a thleng a ni lawm ni? Kan ei leh in te hi a digested a, chakna a lo chhuak a, bawlhhlawh pawh a lo chhuak bawk. Chuvangin, he ammonia hi chutiang bawlhhlawh pakhat, kan taksaa lo chhuak a ni. Mahse hei hi a chhuak tha lo a nih chuan harsatna engemaw zat a thlen thei a ni. Vawiin hian he ammonia chungchang te, a hlauhawm theih chhan te, a control dan tur te i sawi dawn nia.
Ammonia chu eng nge ni? A awlsam zawngin...
A awlsam zawngin ammonia emaw (NH3) emaw hi kan ei protein kan ei hian kan intestine-a bacteria-te siam chhuah bawlhhlawh a ni. Chaw ei hmin atanga thil la awm ang maiin ngaihtuah rawh. Chuti a nih chuan, thil thleng tlangpui chu i hria em? He ammonia hi kan liver ah a kal thin . Liver hi kan taksaah factory mak tak ang mai a ni. Chutah chuan he ammonia hi an siam chhuak a, bawlhhlawh dang urea -ah an chantir a ni. Tichuan, he urea hi kan kal (kidney) ah a kal a, chutah chuan zun ah a chhuak thin. Hetiang zawng zawng hi urea cycle an ti a .
Mahse, he urea cycle chhunga hmun eng emaw zatah hian harsatna a awm a nih chuan, chu chu liver emaw, kidney emaw, thil dang emaw pawh ni se, he thil hi a puitu a nih chuan, ammonia chu a process tha lo va, a chhuak lo tih han ngaihtuah teh. Chutiang a nih chuan ammonia chu thisenah a awm khawm tan ta a ni. Vawikhat a khawlkhawm chuan thisen atanga thluak thlengin a kal thei bawk. Kan thisena ammonia awm tur hi a tlem hle . Tlemte pawhin a pung a nih chuan, chu chu hyperammonemia tih natna a lo awm a nih chuan kan central nervous system (CNS) tan a toxic hle tihna a ni. Chu chu a hlauhawm tihna a ni.
Taksaah hian ammonia engzat nge awm tur?
Tunah chuan mi hrisel thisenah ammonia awm tur zat hi kum a zirin a danglam thin. Nausen piang tharte hian puitling aiin tlemin an nei tam zawk. Tin, naute hi term-a piang emaw, a pian hma emaw pawh hian a nghawng bawk.
- Nausen term hrisel : Liter khatah micromoles 45±9 vel / micromol/L. A tlangpuiin a chunglam chu 80 leh 90 micromol/L inkar a ni.
- Nausen piang hma : 71±26 micromol/L vel. Hei hi ni sarih vel hnuah a normal level-ah a tlahniam ta a ni.
- Naupang thla khat aia upa : 50 micromol/L aia tlem.
- Puitling : Micromol/L 30 aia tlem lo.
Mahse thil pakhat hriat reng tur. Heng value te hi lab hrang hrangah a inang lo deuh thei. Chuvangin, i lab report-a value awmte nen khaikhin a tha ber. Harsatna a awm chuan, .I doctor emaw nurse emaw zawt ngei ang che.
Ammonia level hi engtiang chiahin nge a hlauhawm?
Ammonia hi thil tha lo tak a ni . A tlangpuiin puitling hrisel thisena ammonia level hi liter khatah micromoles 50 (micromol/L) aia tlem a ni. Mahse, hei hi litre khatah micromole 100 chauh (100 micromol/L)-ah a pung a nih pawhin, hriatnaah inthlak danglamna a awm tan thei a ni. Chumi awmzia chu ngaihtuahna seng harsa a lo ni ta a, tlem chuan i buai deuh mai thei. Thisena ammonia level 200 micromol/L thlenga a san chuan coma-ah i lut thei a, convulsion i nei thei bawk. Hei hi a hlauhawm hle a, nunna atana hlauhawm tak a ni thei bawk.
Taksa chhunga ammonia awm zat hi engtin nge kan enfiah ang?
I doctor chuan thisen test hmangin i ammonia level a teh thei ang . Puitling tan chuan hei hi i kut vein atanga thisen tlemte lak atanga tih a ni tlangpui. Nausen piang thar tan chuan Doctor chuan naute kekawrte chu a tifai ang a, zungbun te tak te hmangin a chil ang a, thisen tlemte a la ang. Tichuan, a chungah chuan bandage te tak te an dah a. Hei hi thisen test pangngai ang mai a ni.
Ammonia level sang lutuk hian eng symptoms nge a neih?
I thisena ammonia level a san chuan symptoms i nei thei a, chungte chu:
- Buaina leh ngaihtuahna buai (disorientation) a awm
- Mutthilh lutuk, harh harsa
- Hriatna inthlak danglamna, a chang chuan hriatna hloh pawh
- Mood swings, thinrimna leh mood swings te
- Kut a nghing, a bik takin kut hmalam pan chuan
- Coma - Hriat lohna leh chhanna nei lo dinhmun
Hei hi a pawimawh hle: nangmah emaw, i hnaih ber emaw pawhin heng symptoms hi an neih chuan hun khawhral suh la, ambulance service 1990 call la, a rang thei ang bera damdawi in hnai ber emergency department-ah kal rawh. Ammonia level sang hian nunna a tichhe thei a, chuvangin damdawi lam pan vat a ngai a ni.
Nausen piang thar natna lan chhuah dan
Nausen piang tharin a pian hnu ni engemaw zat chhungin heng natna lan chhuahna zinga pakhat tal a lan chuan doctor chuan ammonia level a test thei ang:
- Hahdam lo reng reng, tap fo, leh hnute tui in duh lohna (Irritability) .
- Luak chhuak
- Mutthilh, chau lutuk, harh harsa
- Seizures a awm thin
Naute hian heng symptoms te hi a neih chuan ngaihthah suh. Doctor pan nghal rawh.
Engvangin nge taksaa ammonia level hi a san em em?
Thisenah ammonia level a san theih chhan hrang hrang a awm a. Eng nge an nih hi han thlir ila:
- Liver natna: 1.1.Hei hi a chhan ber a ni . I liver a chhiat chuan, cirrhosis ang chi, liver hian ammonia a clear tha thei lo. Hei hi thin natna khirh tak takah chuan a thleng fo thin. Mahse, a chang chuan thin natna hi a nghet hle a nih pawhin, chaw kawng emaw, chaw kawng emawa thil thleng, chaw kawng thisen chhuak emaw, electrolyte inthlauhna emaw a awm chuan ammonia level a sang nghal thei a ni.
- Liver-a thisen kal tlem: Liver-in thisen a hmuh tlem chuan ammonia hian liver-a luh theihna tur leh tihfai theihna tur kawng a nei lo. Tichuan, ammonia chu thisenah a lo pungkhawm ta a ni.
- Hepatic encephalopathy: Hei hi a buaithlak deuh. A awlsam zawngin sawi ila, thin natna emaw, a chhiat emaw a, ammonia a tihfai that theih loh chuan ammonia chu thisenah a pungkhawm a, thluak lamah a kal thin. Hei hian disorientation, confusion, leh coma a thlen thei a ni. A chang chuan thihna thlen thei a ni.
- Reye’s syndrome: Hei hi natna awm lo mahse na tak a ni a, thisen, thluak leh thin te a nghawng a ni. A tlangpuiin thisenah ammonia level sang leh thisen glucose level hniam a thlen thin. Naupang leh puitling tleirawl, virus natna chickenpox emaw influenza (flu) atanga dam leh laiin symptoms neia aspirin ei tawhte zingah a awm tam ber. Reye’s syndrome hi a chhan dik tak hriat a la ni lo. Mahse, he hlauhawmna avang hian naupang leh puitling naupangte chuan doctor-in a bik taka a rawt loh chuan aspirin ei loh tur a ni.
- Kidney / renal failure: I kal (kidney) a thawk tha lo a nih chuan, a fail tihna a ni a, urea hi a paih chhuak tha thei lo tihna a ni. Hei hian thisenah ammonia a tipung a ni.
- Urea cycle-a genetic diseases: Genetic natna hi a tlem hle. Hengte hi urea cycle atana enzyme mamawh zinga pakhat pianpui tlakchham vang a ni. Hei hi pian tirh atangin hmuhchhuah a ni tlangpui.
- Hemolytic disease of the newborn: Hei hi nu naupaiin a naute thisen cell laka antibody a siam hian a thleng thin. Hetiang dinhmun hi ven theih a ni. Rh-negative i nih a, a hmaa sensitized i nih loh chuan i naute Rh-positive cells nena i antibody te inrem lohna tur damdawi i ei thei ang.
Ammonia level sang zawka enkawl dan tur chu engte nge ni?
Ammonia level sang enkawlna chu a chhan a zirin a ni. Entirnan, puitlingah chuan liver disease emaw hepatic encephalopathy emaw vang a ni thei a, nausen piang tharah chuan urea cycle tibuaitu congenital condition vang pawh a ni thei.
Acute hyperammonemia enkawlnaah hian ammonia level tihhniam leh cerebral edema leh intracranial hypertension ang chi complication control hi ngaih pawimawh ber a ni.
Nausen piang tharte ammonia level a san chuan doctor ten protein pek an chawlhsan (a chhan chu protein an ei chhuah hian ammonia a siam chhuak thin a ni). Chu ai chuan chakna pe turin glucose solution an pe zawk a ni. Naute thisen atanga ammonia paih chhuah nan hemodialysis tih damdawi an hmang bawk. Hei hian thisen chu machine bik, dialysis machine an tih leh filter, artificial kidney ang chi hmanga tihfai a huam a ni .
Hepatic encephalopathy enkawl hian a tum ber chu intestine-a ammonia siam chhuah tihtlem a ni. Enkawlna hmasa ber chu damdawi ei lactulose leh lactitol tih a ni . Heng sugar te hian intestine-a ammonia siam leh lakluh a ti tlem a ni.
Engtikah nge ka ammonia level chungchangah doctor ka hmuh ang?
Hei hi a chiang hle mai. Nangmah emaw, i hnaih ber tu emaw chuan thisenah ammonia level sang tak, a hmaa kan sawi tawh ang khan ngaihtuahna buai, mutthilh reng, leh hriatna inthlak danglam ang chi i neih chuan 911 call nghal la, a nih loh leh damdawi in hnai ber emergency room-ah a rang thei ang bera kal rawh. Hei hi tihkhawtlai tur thil a ni lo.
Liver natna i neih chuan i liver hian ammonia a clear tha em tih enfiah turin doctor i pan fo tur a ni. Hei hian harsatna eng pawh i hriat hmasak theih nan a pui ang che.
Chuti a nih chuan, he thawnthu atang hian eng thil nge kan hriat reng tur pawimawh ber?
Bawlhhlawh anga kan taksain ammonia a siam chhuah hi thil pangngai ni mah se, thisenah a tam lutuk a awm chuan a hlauhawm hle thei a ni.
Nangmah emaw, i hnaih ber tu emaw hian ammonia level sang tak symptoms (entir nan, buai, mut tam lutuk, nungchang thlak danglam) a neih chuan, a rang thei ang bera damdawi in hnai ber pan la, a rang thei ang bera kal rawh. Hei hi nunna emaw thihna emaw dinhmun a ni thei.
A bik takin liver natna i neih chuan heng symptoms te hi hriat a pawimawh hle a , hei hian ammonia level sang tak a thlen theihna a tipung thei a ni.
Ammonia level sang lutuk chungchanga zawhna i neih chuan, emaw, thil dang hriat duh i neih chuan doctor nen inbiakna neih hreh suh. I tanpui tur leh i zawhnate chhang turin an awm reng a ni. Hrisel taka awm hi a pawimawh ber!
` Ammonia, Ammonia Level, Liver, Kidney, Urea Cycle, Hepatic Encephalopathy, Reye’s Syndrome, Thisen Test, Hyperammonemia











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