Angiosarcoma tih hming hi i hre tawh em? A ni lo mai thei. A chhan chu hei hi cancer chi khat hmuh tur awm lo, chu chu cancer chi khat hmuh tur awm lo a nih vang a ni. Mahse hetiang thil hi kan hriat chian a pawimawh hle. A chhan chu, hei hi cancer na tak a ni a, a na thei hle a, a darh thuai thei bawk. Chuvangin vawiin hian he thu hi chipchiar tak leh awlsam takin i sawi dawn nia.
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Angiosarcoma hi eng nge ni?
A awlsam zawngin, angiosarcoma hi cancer natna a ni a, i thisen kalna kawng emaw, lymphatic vessel emaw chhungril atanga intan a ni. Kan taksa pum puia heng vessels network ang maiin han ngaihtuah teh. Chuvangin he cancer hi taksa chhunga heng vessels awmna hmun apiangah a lo awm thei a ni.
Mahse, lu, kawr, hnute vunah a lang tam ber. Cutaneous angiosarcoma kan ti a. Hei bakah hian internal organs, heart (cardiac angiosarcoma), liver, leh spleen-ah te pawh a lo awm thei a, mahse a tlem deuh hlek a ni.
Angiosarcoma i vei tih i hriat chuan mangang leh hlauhna i neih hi thil pangngai a ni. Hei hi cancer na tak leh enkawl harsa tak a ni thei. Mahse chu chuan duhthlan tur i nei lo tihna erawh a ni lo. I doctor chuan i dinhmun atana enkawlna tha ber berte a hrilh ang che.
Hetiang dinhmun hi engtiang chiahin nge a awm?
Angiosarcoma hi soft tissue sarcoma chi khat a ni a, a awm lo hle. Soft tissue sarcomas pawh hi tumor chi khat hmuh tur awm lo tak a ni. Ngaihtuah teh, America ang ramah pawh hian kum tin mi maktaduai khat zinga pakhat velin angiosarcoma hi a awm thin. I vunah, a bik takin i lu vunah an lo awm tam ber.
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Angiosarcoma symptoms hi taksa chhunga khawi hmunah nge a awm tih a zirin a danglam thei. Entirnan, angiosarcoma vunah (lu vun, hmai, kawr, leh hnute te pawh huamin) a awm chuan a natna lan chhuah dan te chu:
- They start as small red or blue bumps , chutah chuan zawi zawiin an darh a, an lian a, awlsam takin thisen an chhuak tan thin.
- Vun hmun dum, vun rawng emaw, hliam emaw ang chi. A chung lamah pawh scaly a ni thei bawk.
- Hliam dam lo, a nih loh leh hliam a lian deuh deuh.
I liver ang chi internal organ-a angiosarcoma i neih chuan, chu organ hnathawh tichhe thei tur khawpa tumor a lo lian hma chuan symptoms i hmu lo mai thei. A nih loh leh, tumor hian a bula structure awmte chu a nawr thei bawk. Internal organ-a angiosarcoma symptoms te chu:
- Chauhna nasa tak a awm.
- A natna hmuna natna.
- Malaise, nuam lo tihna a ni.
- Chhan awm lovin taksa rihna tihtlem.
- Thâwk harsa(Hei hi cardiac angiosarcoma natna langsar ber a ni.)
- Jaundice leh pum veilam chunglam natna awm reng (hengte hi hepatic angiosarcoma chhinchhiahna a ni thei).
Angiosarcoma hi a na em?
Angiosarcoma hian natna a thlen thei a, a thlen lo thei bawk. Entirnan, i liver emaw spleen emaw-a angiosarcomas lo awm hian i pum chunglam a ti na thei a ni. Mahse chu chu a tlangpuiin tumor a lo lian a, natna a lo zual zel hnuah chauh a ni. Angiosarcomas vunah lo awm hi a na lo thei lo. Chu ai chuan, dam lo, darh zau thei hliam ang maiin an lang thei.
Engvangin nge Angiosarcoma hi a lo awm?
Angiosarcoma hi i thisen kalna kawng chhunga line siamtu cell te chu cell pangngai atanga cell pangngai lo ah an inthlak vang a ni. Cell pangngai ang lo takin heng cancer cell te hi an thi lo. Chu ai chuan cell tam zawk an siam chhunzawm zel a, a tawpah chuan tumor an siam ta zawk a ni. Heng cancer cell te hi thisen kalna kawng a nghawng atang hian an lo thang lian zel a. Vawi tam tak chu taksa peng dangah an darh zauh zauh thin.
Risk factors te chu engte nge ni?
Researcher-te chuan angiosarcoma vei theihna tipungtu thil engemaw zat an hmuchhuak a. Chungte chu:
- Kum leh mipa leh hmeichhia: Angiosarcoma hi kum eng pawhah a awm thei a, mahse kum 60 chunglam ah a tam zawk a, hmeichhia aiin mipa hian primary angiosarcoma an vei tam zawk.
- Radiation therapy: A chang chuan angiosarcoma hi cancer pahnihna a ni. Chumi awmzia chu cancer chi dang (a tam zawk chu hnute cancer) avanga radiation therapy hmanga enkawlna hnuah kum engemaw zat (a tlangpuiin kum 8-10 vel) a lo awm tihna a ni.
- Chemical nena inzawmna: Hepatic angiosarcoma hi chemical polyvinyl chloride, arsenic, leh thorium dioxide te nena inzawm a ni. A chang chuan, he exposure atanga kum 10-40 hnuah angiosarcoma hi a lang lo.
- Chronic lymphedema: Angiosarcoma zawng zawng zinga 5% vel hi Stewart-Treves syndrome an tih, chronic (hun rei tak daih) lymphedema chi khat nen a inzawm a ni. Hei hian hmeichhia hnute cancer enkawlna atana mastectomy leh lymph node dissection nei tawhte a nghawng tam ber.
- Genetic disorders: Angiosarcoma zawng zawng zinga 3% vel chu genetic disorders avanga natna nei te zingah a awm thin. Thil awm dan bikte chu bilateral retinoblastoma, Maffucci syndrome, neurofibromatosis, leh Klippel-Trenaunay syndrome te a ni.
Engtin nge hei hi i hriat chian?
Doctor chuan taksa a enfiah hmasa ang che a, i natna lan chhuah dan te a sawi ang. I medical history pawh an zawt ang. Entirnan, a hmain radiation therapy i lo nei tawh emaw, chemical thenkhat nena inhriatthiamna tam tak nei hna i neih chuan doctor chuan angiosarcoma a ringhlel thei a ni.
A dawtah chuan imaging test hmangin tumor lian leh te, a awmna hmun hriat theih a ni. CT scan, MRI, leh PET scan te hi angiosarcoma hriat theihna atana hman tlanglawn ber a ni. I doctor-in hnute angiosarcoma a rinhlelh chuan mammogram emaw ultrasound emaw tih a ngai mai thei. I doctor-in cardiac angiosarcoma a rinhlelh chuan transesophageal echocardiogram neih a ngai mai thei.
A tawp berah chuan biopsy i neih a ngai ang . Hei hian doctor-in i tissue, i tui leh i cell sample te te a laksak a ngai a ni. Heng sample te hi lab-ah thawn a ni a, chutah chuan pathologist chuan cancer cell a awm leh awm loh a enfiah thin. Lab test immunohistochemistry tih hmangin angiosarcoma i vei em tih a chiang thei.
Angiosarcoma natna stage hrang hrang
Cancer staging hian doctor-te chu cancer nasat dan leh a darh zau zia thliar hrang turin a pui a ni. Angiosarcomas hi stage I (pakhat) atanga IV (pali) thlenga scale-a stage-a dah a ni. Stage I tih awmzia chu tumor hi a bul tanna hmun aiin a darh lo tihna a ni. Stage IV tih awmzia chu taksa hmun hla tak takah a darh tawh tihna a ni. Angiosarcomas hi cancer natna khirh tak, a lo thang chak em em a, chuvang chuan an hriat chhuah meuh chuan a darh tawh (chu chu a sang chho tawh tihna a ni) fo thin. Lung lamah an darh tam ber.
I cancer stage hriat hian i doctor chu eng treatment nge i dam rei zawk ang tih a rel thei a ni.
Engtin nge enkawl a nih?
Angiosarcoma enkawlna atana hman tlanglawn ber chu tumor lakchhuahna tur surgery hi a ni. Doctor-te chuan operation hma emaw, operation hnuah emaw radiation therapy emaw chemotherapy emaw hmangin tumor tihtlem emaw, cancer cell la awm zawng zawng tihhlum emaw an rawt thei a ni.
Tunah hian cancer enkawlna thar, targeted therapy drugs leh immunotherapy te chu angiosarcoma dona atan siam chhuah mek a ni. I dinhmun azirin i doctor chuan heng enkawlna zinga pakhat emaw, cancer enkawlna thar test-na clinical trial emaw a rawt thei ang.
Hei hi ven theih a ni em?
Angiosarcoma thlentu zawng zawng hi i veng thei lo. Entirnan, i genetic condition rochun emaw, cancer vanga radiation therapy lak a ngai emaw chu i titawp thei lo. Mahse, angiosarcoma vei theihna thenkhat tihziaawmna tur thil i tih theih a awm a, chu chu chemical tha lo thenkhat i hman lohna tur a ni.
Angiosarcoma ka neih chuan eng nge thleng ang?
Angiosarcomas hi i thisen kalna kawngah a intan avangin a darh chak hle thei a ni. Vawikhat an darh chuan angiosarcomas hi enkawl a harsa hle. Inenkawl zawha kal bo pawh ni se, an lo let leh theihna a sang zawk.
Doctor-te chuan angiosarcoma enkawl dan tur kawng tha zawk an zawng mek a ni. Mahse, damchhuah zat erawh a la hniam hle. Angiosarcoma vei hmuhchhuah zinga 35% vel chauh hi an hmuhchhuah atanga kum nga hnuah an dam a ni.
Hetiang information hriat hian hlauhna neih hi thil pangngai tak a ni. Mahse a pawimawh ber chu thil awmdan hrethiam a, damdawi lam thurawn zawm hi a ni.
Engtin nge ka in enkawl ang?
Angiosarcoma hi cancer thang chak tak a ni. I in enkawl thei a, awlsam takin i la thei a, awlsam takin i la thei bawk. I taksa chunga thil thleng hriatthiam nan hun pe rawh. I enkawlna thlawp tura i tih theih turte chu i doctor nen sawiho rawh. Hetah hian ṭanpui thei tûr rawtna ṭhenkhat chu hetiang hi a ni:
- I stress tihziaawm tum ang che. I diagnosis hnua stress i neih chuan nangmah chauh i ni lo. Cancer hi a stressful hle. Meditation, relaxation exercise, leh thawk thûk tak ang chi thilte hian a ṭanpui thei a ni.
- Chawlh hahdam phal rawh. I cancer enkawlna hnuah i chau hle mai thei, "chau" i ti mai thei. A theih ang anga chawlh hahdam tum ang che.
- Chaw hrisel ei fo tum ang che. I enkawlna hian i ei duhna a nghawng thei a ni. Chaw tha tak tak ei tum ang che (chaw ei khap suh). Chaw ei harsatna i neih chuan dietitian nen inbia ang che.
- Midang nen inzawmna siam rawh. Cancer hmachhawn hian mahni chauhna a awm thei a, a bik takin angiosarcoma ang chi cancer hmuh tur awm lo tak nen chuan. I doctor chu support group-te nena inzawm tir turin hrilh la, chutah chuan i rilru put hmang chu mi hrethiamte hnenah i sawi thei ang.
Engtikah nge Doctor ka hmuh ang?
I vunah (a bik takin i lu vun, i hmai, i kawr a dam lo) i hmuh chuan doctor pan rawh. Tin, a hmaa radiation therapy i neihna hmun ang chi, hliam thar i hmuh chuan i doctor hnenah hrilh bawk ang che.
Angiosarcoma enkawl mek i nih chuan i natna lan chhuah dan a zual zel nia i hriat chuan doctor ko rawh. Tin, i enkawlna avanga beisei loh emaw, a danglam bik taka na tak emaw i neih chuan hriattir bawk ang che.
Engtikah nge emergency room-ah ka kal ang?
Cancer enkawlna thenkhat chuan i taksa hriselna a nghawng thei a, natna kai theihna a tipung thei a ni. Surgery i neih tawh chuan surgery hmunah harsatna i nei thei a ni. Emergency room-ah i kal tur a ni a, chu chu:
- Khawsik 100.4 degree Fahrenheit (38.3 degree Celsius) aia sang i neih chuan khawsik hi natna i vei tih chhinchhiahna a ni thei.
- I natna tidamtu damdawi hmanga thunun theih loh natna i neih chuan.
- I luak tam lutuk emaw, persistent diarrhea i neih chuan.
Doctor hnenah eng zawhna nge ka zawh ang?
Angiosarcoma hi cancer hmuh tur awm lo tak a ni. Engvangin nge he cancer hi i vei tih leh i doctor-in eng nge a puih theih che tih i ngaihtuah mai thei. Chutiang inbiakna nei tûra ṭanpui thei tûr zawhna ṭhenkhat chu hetiang hi a ni:
- Ka angiosarcoma hi eng stage nge ni?
- Eng enkawlna nge i rawt?
- An side effects te chu engte nge ni?
- Enkawlna hnua cancer lo kir leh theihna chance chu engzat nge ni?
- Clinical trial-ah hian ka tel a ngai em?
- Ka natna hi eng prognosis nge ni?
Thil hriat reng tur tawi te tein
Angiosarcoma hi cancer a awm lo hle a, a thang chak hle. Chu chu angiosarcoma i neih chuan cancer na tak i hmachhawn a nih hmel tihna a ni. A hnua thil thleng tûr chu i lungkham hle mai thei. Hmalam hun tur chiang lo anga inhriat hi thil pangngai a ni. Mahse he diagnosis chauh hi i hmachhawn a ngai lo. I ngaihtuahna chu i doctor hnenah hrilh rawh. I enkawl dan tur leh natna hmalam hun tur a hrilhfiah thei che a ni. Tin, i tanpui thei tur program leh service hrang hrang nena inzawm tir turin hrilh bawk ang che. Beiseina chu bansan ngai suh.
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