Hliam kan neih chuan thisen a zang a, thisen a chhuah tawh loh hi thil pangngai a ni. A nihna takah chuan kan taksa invenna mechanism a ni. Mahse, chhan awm lova taksa thisen zam (veins)-ah thisen zam a lo awm fo a nih chuan ngaihtuahawm tak a ni. A bik takin naupai laiin nau pai i nei reng a nih chuan a chhan chu he natna Antiphospholipid Syndrome (APS) an tih hi a ni thei a, hei hi vawiinah hian kan sawi dawn a ni.
APS chu eng nge ni mai?
A awlsam zawngin sawi ila, Antiphospholipid Syndrome (APS) hi i taksain a tlangpui aia thisen zam a siam tam zawkna a ni. Doctor-te chuan Antiphospholipid antibody syndrome an ti \hin.
Chûng thisen zamte chuan harsatna lian tak, nunna atana hlauhawm tak tak, stroke ang chite a thlen thei a ni . He natna hian naupai laiin nau pai leh harsatna dang a thlen theihna a tipung bawk.
APS hi a takah chuan autoimmune disease a ni . Ngaihtuah teh, sipai ang maiin kan taksaah hian defence system kan nei a. Immune system kan ti a. A hna chu natna thlentu hrik leh hri kai laka min humhim hi a ni. Mahse he autoimmune natnaah hian thil thleng chu kanmahni defense system hian kan taksa chhunga cell tha tak takte chu a rawn bei sual tan ta a ni.
Hetiang natna lan chhuah dan hi engte nge ni?
APS vei thenkhat chuan an vunah hian net ang maia hnawih dum an nei thei. Hei hi damdawi lam chuan livedo reticulitis an ti a . Mahse, APS vei tam zawk chuan thisen zam an neih hma emaw, naupai laiin harsatna an neih hma loh chuan symptom an nei lo.
Hengte hi thisen zam (blood clot) a lo awm chuan a lo lang thei a ni. Hengte hi i fimkhur hle tur a ni.
| Symptom a ni | Hrilhfiahna |
|---|---|
| A rilru a na | Thinlung emaw, lung emawa thisen zam vang a ni thei. |
| Thâwk harsa (dyspnea) . | A bik takin lung chhunga thisen zam (pulmonary embolism) vang a ni thei. |
| Lu na fo thin | Thluak lam panna thisen kalna kawngah harsatna a awm thei. |
| Natna rapthlak tak | Kut, ke, hnungzang, kawr emaw, hmuiah emaw natna nghal. |
| A hring emaw, a sen emaw | Thisen zam vang a ni thei a, a bik takin kut emaw keah emaw a ni thei. |
| Pum a na | Pum chhung peng hrang hranga thisen pe chhuaktu thisen kalna kawng (vessels)-a thisen zam vang a ni thei. |
A pawimawh ber: Thisen zam hi nunna atana hlauhawm emergency a ni. Thisen zam i neih nia rinhlelhna i neih chuan hospital emergency department (ETU) hnai ber pan nghal rawh.
Heng symptoms bakah hian APS hian symptom thenkhat kan hmuh theih loh leh kan hriat theih loh a thlen thei bawk.
- Thisen platelet level a tlahniam.
- Thisen tlakchhamna (Anaemia).
- Heart valve a dik lo.
Engvangin nge hetiang hi a lo awm?
Antiphospholipid Syndrome hi i immune system-in a tihsual avanga antibody chi danglam tak a siam tan chuan a lo awm thin. A tlangpuiin antibodies hi protein bik, kan taksaa lut hrik leh allergens zawng chhuaktu leh tichhe theitu an ni. Defense robot ang mai an ni.
Mahse APS vei mi pakhatah chuan heng antibodies, immune system siam hian kan cell-a phospholipids (thau chi khat) nena inzawm protein te chu an bei thin. He attack hian phospholipids te chu a tichhia a, chu chuan an inzawm khawm a, thisen zam a siam awlsam zawk a ni.
APS thlen thei antibody chi thum a awm a, chungte chu:
- Lupus anticoagulant a ni
- Anticardiolipin hman a ni
- Anti-B2 glycoprotein a awm bawk
APS vei chuan heng antibody pakhat emaw, pahnih emaw, pathum emaw a nei vek thei. Mahse mak zawk chu mi thenkhat chuan heng antibodies te hi nei mahse APS symptoms an nei ngai lo. Mithiamte chuan kan immune system hian heng antibodies dik lo siam turin eng thilin nge a tichak tih chiang takin an la hre lo.
Hetiang dinhmun hi tute nge hlauhawm ber?
Tu pawhin APS an nei thei. Mahse, i risk a sang deuh thei a, chu chu:
- Hmeichhia i nih chuan .
- Kum 30 leh 40 inkar i nih chuan.
- Autoimmune natna dang, lupus emaw rheumatoid arthritis emaw i neih chuan.
- I chhungte hnai ber (nu leh pa, pi leh pu) zinga pakhatin APS a neih chuan.
APS vang hian eng harsatna nge thleng thei?
Antiphospholipid syndrome hian harsatna na tak a thlen thei a, a chang chuan thihna thlen thei a ni. Harsatna lian ber chu thisen zam (blood clots) a lo awm a, i taksa peng pawimawh tak takte hnena thisen petu thisen kalna kawngte a tihkhawtlai hian a thleng thin.
- Thluak: stroke a awm
- Lung lam: Lung natna (thrombosis) .
- Lungs: Lung chhunga thisen kalna kawng a block (pulmonary embolism) .
- Kidney: Kal a chhia
Naupai i nih chuan thisen zam (blood clot) hian nausen (placenta)-a nutrients supply a tikhawlo thei a ni. Naupai laiin thisen sang a awm thin , preeclampsia vei theihna a tipung bawk.
Catastrophic antiphospholipid syndrome (CAPS) hi APS natna avanga harsatna awm lo mahse na tak a ni. Ni engemaw zat chhunga taksa peng hrang hranga thisen zam (blood clots) a lo awm thinna a ni. Hetiang natna vei zinga a chanve vel chu an thi thin. Mahse, CAPS hi APS vei zinga 1% aia tlem loah a awm thung.
APS hian i dam chhung a nghawng lo tlangpui. Mahse, thisen zam hian taksa peng pawimawh tak a tihchhiat chuan, a bik takin CAPS ang dinhmunah chuan thihna a thlen thei a ni.
Engtin nge doctor hian he natna hi dik taka a hriat theih ang?
APS hi thisen zam a lo awm hnuah emaw, nau pai nawn leh hnuah emaw hmuhchhuah a ni fo thin. Mi thenkhat chuan antiphospholipid antibodies nei mahse symptom an nei ngai lo.
Doctor chuan thisen test hmangin APS i neih leh neih loh a finfiah ang . I thisen sample an la ang a, a hmaa kan sawi tawh angin antibody chi thum an awm leh awm loh an enfiah ang. Natna finfiah tur chuan thisen test vawi khat tal chu vawi hnih, thla thum aia inhlat a positive a ngai a ni.
Hei hi eng enkawlna nge ni?
I doctor chuan thisen zam hlauhawmna tihziaawmna tur damdawi a rawn rawt ang che. Enkawlna hman tlanglawn ber chu thisen tithianghlimtu, a nih loh leh anticoagulants .
| Ruihhlo chi hrang hrang | Hman dan leh hnathawh dan |
|---|---|
| Enkawlna tlangpui | |
| Heparin a ni | Hei hi intravenous (IV) damdawi a ni a, damdawi ina i awm chuan thisen zam chu a tithianghlim thei a ni. |
| Warfarin a ni | Hei hi pill i ei thin a ni. Thisen a ti thim a, thisen zam thar siam a veng bawk. |
| Aspirin a ni | I doctor chuan i thisen kalna kawng (arteries)-a thisen zam a awm loh nan aspirin dose tlem ei a rawt mai thei. |
| Naupai laia enkawlna hman dan | |
| Enoxaparin a ni | Hei hi vun hnuaia injection a ni. Nau pai loh nan aspirin dose tlem nen a tha fo thin. |
| Immunoglobulin (IVIG) hmanga thisen kal tlanga hman thin. | He enkawlna hi thisen kal tlanga pek hian immune system hnathawh a control a, nau pai theihna a ti tlem bawk. |
| Corticosteroid hmanga tihdam theih a ni | Heng damdawi te hian taksaa inflammation a tihziaawm bakah immune system overactivity a control bawk. |
Naupai i nih chuan he enkawlna hi nang leh i naute tan a him a, chuvangin ngaihtuah buai a ngai lo.
Thisen tithianghlimtu (Blood thinners) hian a side effects te pawh i hrechiang ang u.
Blood thinners i ei hian i taksaah thisen a chhuak tam zawk. Chuvangin heng symptoms te hi i fimkhur hle a ngai a ni. If you have any of these , i doctor nen inbia nghal rawh.
- Chhan awm lovin gum emaw hnar atanga thisen chhuak .
- Thlasik laiin a pangngai aia tam thisen chhuak .
- Vomiting chu a sen hring emaw, coffee grounds-colored emaw a ni .
- Stool-a thisen sen hring hring emaw, stool dum, tarry emaw .
- Pum natna nasa tak emaw lu na tak emaw .
- Mit hmuhna lama inthlak danglamna rang tak .
- Kut emaw ke emaw a hriatna hloh nghal .
APS nena kan khawsak huna ngaihtuah tur thil
APS nena kan khawsak lai hian a pawimawh ber chu thisen zam ven hi a ni. Chumi atan chuan thisen tihthianghlimna damdawi dik taka ei a pawimawh hle.
Tin, thisen zam i neih theihna tipungtu hriselna lama harsatna dangte pawh control a pawimawh bawk. Heng zinga pakhat tal i neih chuan i doctor nen inbia la, thunun rawh:
- Zunthlum
- Thisen sang a sang
- Cholesterol sang tak a ni
- Thau lutuk
- Autoimmune natna dangte
Meizial in hian thisen zam a tipung a, a bik takin APS ang natna nei tan chuan thisen zam a tipung a ni.
Ei leh in lamah fimkhur a ngai em?
APS vei te hian ei leh in bik an zawm a ngai lo tlangpui. Mahse, damdawi Warfarin i ei a nih chuan vitamin K tamna ei tur (dark green vegetables like spinach) te hi i fimkhur tur a ni. Vawi khata vitamin K tamna ei hian thisen zam a tipung thei a ni. Chuvangin i doctor hnenah thurawn dil rawh.
Tin, i doctor hnenah zu in chungchang zawt bawk ang che. Zu hian thisen a ti thim a, chuvangin thisen tithianghlimtu damdawi nena inkawp chuan a nghawng a tipung thei a ni.
Engtikah nge Doctor ka hmuh ang?
Thisen tithianghlimtu i ei a nih chuan i thisen zam zat chu a remchan dan angin a awm em tih enfiah turin doctor i pan fo tur a ni.
Naupai i beisei a nih chuan i doctor nen sawi lawk a, thurawn lak a pawimawh hle.
Engtikah nge Emergency Department (ETU) ah ka kal ang?
Hospital-a Emergency Department (ETU)-ah kal nghal rawh:
- Thisen zam i nei tih ka ring.A lo thleng a nih chuan.
- Thisen zam chhinchhiahna eng emaw a awm chuan.
- Thunun theih loh khawpa thisen chhuak i nih chuan .
Take-Home Thuchah a ni
- Antiphospholipid Syndrome (APS) hi thisen zam theihna a tipung a, a chhan chu nangmah ngeiin i immune system hian i taksa a bei a ni.
- Hei hi hlauh tur a ni lo va, enkawl dan dik (a bik takin thisen tithianghlimtu) hmanga thunun theih a ni.
- Naupai lai hian nau pai leh harsatna dang a awm thei a, mahse damdawi lam enkawlna mumal hnuaiah naupang hrisel tak tak hrin theih a ni.
- Thisen zawrh chhinchhiahna, rilru na, thawk harsa, ke ruh natna i neih chuan emergency-ah ngai la, damdawi in pan nghal rawh.
- Doctor thupek dik taka zawm a, checkup neih fo a pawimawh hle.











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