A châng chuan i rilru, i kawr, a nih loh leh i hmuiah natna i nei em? A nih loh leh thawk harsa tlem, emaw, ei laiin rilru hah lutuk emaw? A tam zawkah chuan heng thilte hi kan theihnghilh a, thil pangngai, gastritis ang chi pawh a ni mai thei tih ngaihtuahin kan theihnghilh thin. Mahse, a châng chuan hengte hi thil engemaw ngaihven tlem a ngai tih chhinchhiahna a ni thei. Chuvangin, vawiin hian kan rilru chhunga thisen kalna bulpui, aorta -a lo awm thei balloon ang maia hring (swelling) chungchang kan sawi dawn a ni. Damdawi lamah chuan hei hi `Thoracic Aortic Aneurysm` kan ti a.
Hei hi eng nge ni `Thoracic Aortic Aneurysm`? A awlsam zawngin...
I in hian tui pekna bulpui ber a nei ang tih han ngaihtuah teh. Chutiang chuan kan taksaa aorta hian hna a thawk a ni. Hei hi thinlung atanga taksa pum puia thisen phurtu thisen kalna kawng lian ber leh pawimawh ber a ni. Tube ang maia siam a ni.
Tunah chuan, he `Thoracic Aortic Aneurysm` hi i rilru chhunga i aorta wall (chuvang chuan `Thorax` emaw chest cavity an tih) chu a chak lo va, hmun khatah balloon ang maia a bulge chhuak a ni. Mi thenkhat chuan hei hi dilation emaw widening of the artery emaw an ti bawk. A tlangpuiin, chu aorta hmun chu a zau zawng pangngai atanga 50% aia zau a nih chuan `Aneurysm`, emaw bulge/bulge emaw ah kan ngai thin. He ``normal width`` hi aorta chhungah hmun hrang hrangah a danglam thei.
Heng bulges te hi aorta khawi hmunah pawh a awm thei. A tam zawkah chuan pum chhungah an awm (`Abdominal Aortic Aneurysm` kan ti a), mahse mi pali zinga pakhat velin he natna hi an rilruah an nei thei a ni.
Aneurysm tenau te hi enkawlna lian tham a ngai lo mai thei. Damdawi leh regular imaging test (scan ang chi) hmanga a hnuaia dinhmun control nan a tawk mai thei. Mahse, i thisen kalna (aneurysm) chu a lian emaw, a lo ṭhang chak emaw a nih chuan, nunna atana hlauhawm harsatna lo thleng tûr ven nân operation neih a ngai mai thei . Doctor-te chuan i tana enkawlna tha ber tur leh engtikah nge i tih tur tih an rel ang, a chhan chu result tha ber i hmuh an duh vang a ni.
Hetiang dinhmun hi engtiang chiahin nge a awm?
He natna hi `Thoracic Aortic Aneurysm` tia koh a ni a, mi 100,000 zingah mi 6 leh 10 inkar a awm tlangpui. Mahse, a zat dik tak sawi a harsa a, a chhan chu a tam zawkah chuan heng aneurysm te hian symptom an nei lo va, chuvang chuan hriat lohvin an awm thin. Tuna damlo hmuhchhuah zinga 20% vel chuan chhungkaw history-ah he natna hi an nei a, hei hian genetic link a awm tihna a ni.
United States-ah ringawt pawh hian kum tin mi 30,000 vel chu aortic dissection emaw rupture emaw vangin an thi nia chhut a nih avangin hei hi thil awlsam tak a ni lo.
Thoracic Aortic Aneurysm natna lan chhuah dan chu engte nge ni?
A tam zawkah chuan he ``aneurysm'' vei te hian an hre lo va, a chhan chu a lan chhuah dan a awm lo fo thin.Mahse, a chang chuan heng ang chhinchhiahnate hi a lantir thei a ni:
- I hmui, i kawr, i rilru, a nih loh leh i hnungzang chunglam natna hriat .
- Chaw ei harsa emaw, ei laiin natna emaw (aneurysm hian i chaw kawng a press a nih chuan).
- Aw ri bengchheng (he aneurysm hian i aw control tu nerve a compress a nih chuan).
- Khuh emaw thawk harsa (aneurysm hian i thawkna kawng a compress a nih chuan).
Aneurysm rupture (`Rupture`) emaw dissection (`Dissection`) emaw chhinchhiahna - hengte hi emergency a ni!
Mi tam tak chuan symptom an nei lo va, chutah chuan rang takin aneurysm chu a chhe thei a, a chhe thei bawk. Heng pahnih hi medical emergency, enkawl vat ngai an ni! Symptoms hi a intan nghal thei a, a na hle thei bawk. Nangmah emaw midang emaw hian heng symptoms te hi i neih chuan damdawi inah i kal nghal tur a ni :
- Rilru emaw, hnungzang emaw, tuar theih loh khawpa natna. Mi ṭhenkhat chuan hliam tuar, hrual, a nih loh leh puak angin an sawi.
- Luak chhuak emaw, inher chhuah emaw.
- Thâwk harsa.
- Heart rate a sang chho zel.
- Thaw hah lutuk.
- Rilru tibuai.
- Thusawi harsa.
- Mit hmuhna hloh.
- Taksa sir khata chak lohna emaw, rilru hahna emaw.
Hetiang dinhmunah hian , darkar leh minute tin hi a pawimawh. Enkawlna zawng i tihkhawtlai poh leh i nunna i chhanhim theihna a tlem zawk. Chuvangin heng symptoms te hi ngaihthah suh.
`Thoracic Aortic Aneurysm` awm chhan hi engte nge ni?
Thoracic Aortic Aneurysm awm chhan ber chu Atherosclerosis an tih hi a ni. A awlsam zawngin, hei hi kan thisen kalna kawng bang chhungah thau (plaque) a lo awm khawm a, zawi zawiin a ti tawi a ni. Hun a kal zel a, heng thau awmte hian aorta bangte chu a tichak lo va, chu chuan aneurysm a neih theihna a tipung zawk a ni.
A tlangpuiin kan aorta bangte hi a nghet a, thisen a kal laiin a tul angin a zau thei a, a inzawm thei tur a ni. Ngaihtuah teh, he aorta hi thinlung atanga thisen lo chhuahna direct a ni. Chuvangin, thinlungin thisen a pump nasa lutuk hian pressure a siam chu a tuar thei tur a ni.
Aorta hrisel chuan harsatna awm lovin a ti thei a ni. Mahse, aorta bangte a chak lo a nih chuan thinlung atanga pressure lo chhuak chuan aorta section pakhat chu pawn lam hawiin a bulge thei a, aneurysm a siam thei a ni. He bulge hi a pangngai lo a, aorta’s tube pianzia a thlak danglam thin. He bulge kal tlanga thisen a luang chhunzawm zel chuan bang chak lo tawhte chu pressure nasa zawk a siam a, chu chuan a tichak lo zual sauh a ni. Chuvang chuan bangte chu a bulge zual sauh sauh a ni. Aneurysm a lian poh leh a hlauhawm zual thin.
Risk factors te chu engte nge ni?
Eng thil pawh hian aorta bang a tichak lo a nih chuan aneurysm a awm theihna a tipung a ni. Atherosclerosis bakah hian risk factor dang engemaw zat a awm a:
- `Aortitis` tih a ni: Aorta-a awm thin inflammatory condition a ni.
- `Bicuspid aortic valve disease` : Thinlung aortic valve hian leaflet pahnih a nei a (a tlangpuiin pathum a awm tur a ni).
- Coronary artery disease (CAD) : Heart muscle-a thisen pe chhuaktu coronary arteries nena inzawm natna.
- Chhungkaw history-a aneurysm (chhungkaw history) nei .
- Thisen sang sang .
- Loeys-Dietz syndrome : Genetic condition hmuh tur awm lo tak, connective tissue inrawlhna.
- Marfan syndrome : Genetic condition dang, connective tissue tichhe thei.
- Kum 65 chunglam a nih vang a ni.
- Meizial zu emaw, zuk leh hmuam thil eng pawh hman emaw.
- `Turner syndrome` : Hmeichhia chauh natna nei, genetic condition a ni.
- Vascular Ehlers-Danlos syndrome : Connective tissue natna hmuh tur awm lo tak, thisen kalna kawng a nghawng thin.
Thoracic Aortic Aneurysm hi rochun theih a ni em?
Ni e, Thoracic Aortic Aneurysm hi chhungkaw hrang hrangah a kal thei. Chu chu thlah kal zelah a kal zel thei tihna a ni. Researcher-te chuan genetic mutations engemaw zat an hmuchhuak a, chu chuan a hlauhawmna a tipung a ni. Chung zingah chuan ACTA2 gene-a mutation awm hi a tam ber a ni.
ACTA2 gene hian kan taksa chu kan thisen kalna kawng (arteries walls) ah protein thenkhat siam turin a hrilh a. Heng protein te hian kan thisen kalna kawngte chu a pianzia vawng reng turin a pui a, a chhunga thisen luang chhuak pressure chu a thlawp a ni. ACTA2 gene-ah hian mutation a awm a nih chuan kan thisen kal tlanga thisen a kal chuan kan thisen kalna bangte hi a inzawm lutuk thei a ni.
Mahse, aneurysm i neih vang mai maiin genetic mutation i rochun tih i sawi thei lo. Mahse, a risk a sang zawk. I chhungte hnai ber (biologically related) tu emaw chuan Thoracic Aortic Aneurysm a vei a nih chuan i doctor nen inbiakna neih a tha. Genetic testing pawh a rawt thei bawk .
He `Thoracic Aortic Aneurysm` hi khawiah nge a awm?
Chungte chu aorta bang chak lohna hmunah an siam thin. A hmaa kan sawi tawh `Atherosclerosis` (fatty deposits) ang chi thil te, a nih loh leh connective tissue natna te hian aorta bang a tichak lo va, `Aneurysm` siam a awlsam phah hle.
Aorta hi kan taksaa thisen kalna lian ber a ni tih i hria em? Hmanlai kalna thingpui ang mai a ni. Thinlung atanga tan a, a curve chho a, chutah chuan rilru leh pum kaltlangin a chhuk leh thin. Navel chungah chiah a tawp thin.
A tam zawkah chuan Thoracic Aortic Aneurysm hi ascending aorta emaw descending aorta emaw ah a lo awm thin. A tlem berah chuan aorta arched part-ah pawh a lo thang lian thei bawk – chu chu stick kutkawr ang maia lang a ni.
`Thoracic Aortic Aneurysm` hi engtiang chiahin nge a pawi?
Thoracic Aortic Aneurysm hi damdawi lam natna khirh tak a ni. Harsatna engemaw zat a awm thei a:
- Aneurysm a chhuak.
- Aortic dissection tih a ni .
- Thisen zam chu aneurysm awmna hmunah a lo awm a, taksa hmun dangah a kal (thromboembolism). Heng thisen zam hian natna khirh tak tak a thlen thei a , chu chu stroke emaw mesenteric ischemia emaw a ni thei .
- Aortic valve atanga lo chhuak leh chhuak .
Hengte hi dinhmun pawi tak a ni tak zet a ni. Chuvang chuan he `Aneurysm` hi kan fimkhur a ngai a ni.
He `Thoracic Aortic Aneurysm` hi engtin nge an hriat theih?
A tam zawkah chuan Thoracic Aortic Aneurysm hi accident-in hmuhchhuah a ni . Chumi awmzia chu Doctor ten chhan dang avanga test an tih laiin hmuhchhuah a ni tihna a ni. Entirnan, chest X-ray-ah chuan i rilru chhungril lam (mediastinum) chu a tlangpui aia zau zawk a ni tih a lang thei. Hei hi aneurysm chhinchhiahna a ni thei.
I doctor chuan Thoracic Aortic Aneurysm a rinhlelh chuan X-ray hmang emaw, chhan dang emaw avanga a hnuaia test te hi a ti ang:
- `Computed tomography (CT) angiogram` : Hei hi CT scan bik a ni.
- `Echocardiogram (echo)` : Thinlung ultrasound hmanga enfiah a ni.
- Magnetic resonance angiogram (MRA) : MRI technology hmanga thisen kalna kawng enfiahna scan a ni.
- Abdominal ultrasound : Abdominal aorta-a aneurysm awm leh awm loh enfiahna atana ultrasound test a ni.
Thoracic Aortic Aneurysm hi eng enkawlna nge ni?
Aorta surgery hi Thoracic Aortic Aneurysm enkawlna ber leh awm reng ber a ni. Doctor-te chuan surgery technique hrang hrang an hmang a. Chung zinga ṭhenkhat chu:
- Traditional open surgery : Hei hi rilru lai takah incision rei tak siam a, aorta chhia chu lakchhuah a, artificial tube (graft) hmanga thlak a ni. Hetiang method hi ascending aorta-a aneurysm enkawl nan hman a ni a, chubakah rilru leh pum chhunga complex aneurysm enkawl nan hman a ni bawk.
- Thoracic endovascular aortic repair (TEVAR) : Hei hi surgical procedure a ni a, a invasive lo hle . Hei hian incision lian tak tak siam lovin tih a ni tihna a ni. Descending aorta-a aneurysm enkawlna atan hman a ni. Hetiang tih danah hian surgeon chuan i groin-ah incision te te a siam a, chuta kal tlang artery (femoral artery) a hmang a, catheter (thin tube) hmangin aneurysm chhungah graft a dah a ni.
- Aortic root thlak danglam a ni: He surgery hi aorta leh thinlung inzawmna hmun (`Aortic root`) ah `Aneurysm` tih a ni. Hei hian i aortic valve thlak pawh a huam thei bawk. A dang pawhin `Valve-sparing techniques` hmangin i natural valve chu i vawng reng thei bawk.
A châng chuan, surgeon-te chuan aneurysm awm dân a zirin heng hmanrua pakhat aia tam (entir nân, open surgery leh endovascular treatment) an hmang khawm ṭhin. Aorta center-a enkawlna dawng hian i duhthlan tur a tipung a, i result tha tak neih theihna a tipung bawk.
Engtikah nge operation ka mamawh ang?
Doctor chuan operation i mamawh leh mamawh loh, a nih chuan engtikah nge tih chu, heng thilte hi ngaihtuahin a rel ang:
- Aneurysm lian tham leh awmna hmun.
- Aneurysm hi engtiang chiahin nge a lo thang chak .
- Aneurysm hian symptom a thlen em tih leh a nasat dan .
- Damdawi lam dinhmun hnuaia awm dangte i neih.
Aneurysm a lian emaw, a lan chhuah dan emaw a nih chuan a puak loh nan operation neih a ngai mai thei. Aneurysm lian leh te hi a pawimawh a , a chhan chu a lian poh leh a puak theihna a sang zawk a ni. A tlangpuiin, doctor-te chuan aneurysm chu inches 2 leh 2.2 (centimetre 5 atanga 5.5 vel) inkar a zau a nih chuan, emaw, kum khatah centimetre chanve vel zeta a lo thang lian a nih chuan operation tih an rel ang.
Mahse, a size chauh hi a pawimawh lo. Connective tissue disorder, bicuspid aortic valve emaw, thil dang emaw i neih chuan i rupture emaw rupture emaw hlauhawmna tipungtu i neih chuan i doctor chuan operation tih thuai a tum mai thei. I doctor nen i aneurysm lian tham leh engtikah nge operation a ngai theih ang tih sawipui rawh.
"Watchful nghak a ni".
Aneurysm a te a, symptom a awm loh chuan operation i mamawh nghal lo mai thei. Chu ai chuan i doctor chuan i dinhmun a enfiah ang (hei hi watchful waiting an ti a). Tin, harsatna awm thei tihziaawmna turin damdawi an pe thei bawk.
Entirnan, thla 6 atanga thla 12 danah imaging scan order theih a ni a, chu chuan aneurysm a inthlak danglam leh awm loh enfiah a ni. I thisen sang tihhniam nan leh i aorta chak lo zawka pressure tihhniam nan damdawi pek i ni thei bawk. I doctor chuan operation hlawknain a hlauhawmna a hneh chuan operation tih a rawt thei ang .
Thoracic Aortic Aneurysm hi a veng thei ang em?
Hetiang dinhmun hi ven dan tur bik a awm lo. Mahse, atherosclerosis (aneurysm thlentu lian ber) i vei theihna chu i tihtlem thei a ni. I tih theih ṭhenkhat chu hetiang hi a ni:
- I thisen sang leh cholesterol level control rawh.
- Thinlung hriselna atana tha ei tur (e.g., Mediterranean Diet ) zawm tur a ni.
- Zuk leh hmuam siam zawng zawng hi pumpelh rawh.
- Kar khatah minute 150 tal moderate-intensity exercise nei la (mahse exercise plan thar i tan hmain i doctor nen inbia ang che).
- Kum tin medical check-up nei la, follow-up appointment ruahman zawng zawngah tel vek rawh.
Thoracic Aortic Aneurysm nei hian eng chen nge i dam theih ang?
Damchhuah hun chhung hi thil tam takah a innghat a, chung zingah chuan aneurysm lian tham leh harsatna a thlen leh awm loh te pawh a tel. Aneurysm lian tak tak hi a hlauhawm thei hle. Aneurysm lian tak, enkawl loh nei zinga 65% vel chu an hmuhchhuah atanga kum khat hnuah an dam chhuak thin. Kum nga chhung chu 20% chauh an dam.
Amaherawhchu, uluk taka enkawl chuan i dam rei zawng chu nasa takin a tipung thei a, dam rei tak, hrisel takin i nung thei bawk. Chuvangin Thoracic Aortic Aneurysm vei theihna hlauhawma i awm leh awm loh hriat a pawimawh a, i doctor nen thawk hovin i natna hi i enkawl a pawimawh hle.
Engtin nge ka in enkawl ang?
Aneurysm i neih chuan i doctor chuan i in enkawl dan tur thurawn a pe ang che. A sawi thei ang:
- Exercise hahthlak lutuk hi pumpelh rawh. Heavy weightlifting emaw high-intensity interval training (HIIT) ang chi thilte hian i thisen kalna kawng (arteries)-ah harsatna a siam belh thei a ni. I doctor hnenah eng exercise chi nge i tan a him tih zawt rawh.
- Zuk leh hmuam hman loh tur. Zuk leh hmuam hian rilru lam natna tam tak a thlen theihna a tipung a ni. Zuk leh hmuam i zuk emaw, zuk leh hmuam dang i hman emaw chuan, zuk leh hmuam bânsan tûrin ṭanpuina zawng rawh.
- I ei leh inah inthlak danglamna siam rawh. Salt i ei tlem emaw, i artery hriselna atana tha tur tihdanglamna dang emaw i siam a ngai mai thei.
- I damdawi ei tur chu a tih angin ei thin ang che. Damdawi lam dinhmun hnuaia awmte control turin damdawi i mamawh mai thei. Heng damdawi ei dan tur chungchanga zawhna i neih chuan doctor zawt rawh.
- Heart rate tisang thei thilte chu pumpelh rawh. Entirnan, cocaine, amphetamines, leh herbal supplement thenkhat te hi a ni.
Engtikah nge ka doctor ka hmuh ang?
Kum tin i doctor hmu la, i follow-up appointment zawng zawng chu vawng reng rawh. I doctor chu ko nghal rawh:
- Symptom thar emaw symptom awm tawha inthlak danglamna emaw i hmuh chuan .
- Damdawi hian beisei loh takin side effect a thlen a nih chuan .
- I enkawlna tur ruahmanna chungchangah zawhna emaw, ngaihtuahna emaw i neih chuan.
Engtikah nge emergency room (ER) ah ka kal ang?
Aneurysm ruptured emaw ruptured emaw symptomsChutiang a nih chuan 911 (Sri Lanka-ah 1990) call emaw, emergency room hnai ber pan nghal emaw rawh. Hengte hi medical emergency a ni a, nunna chhanhim nan enkawl vat a ngai a ni.
Doctor hnenah eng zawhna nge ka zawh ang?
I doctor-in Thoracic Aortic Aneurysm i nei tih a hrilh che chuan zawh hmasak tur i hre lo mai thei. I bul tanna tur zawhna thenkhat chu hetiang hi a ni:
- Ka aneurysm hi engtiang chiahin nge a lian?
- Hetiang zat hi ngaihtuah tur a ni em?
- Eng thilin nge he `aneurysm` hi a thlen theih ang?
- Eng ang enkawlna nge min rawt?
- Ka nunphungah eng inthlak danglamna nge ka neih?
- Follow-up test atan engzat nge ka lo kal ang?
Hei hi eng nge ni `Thoracoabdominal aneurysm`?
Hei hi `Aneurysm` chi khat a ni bawk. Hei hi i rilru (`Thorax`) leh i pum (`Abdomen`) pahnih kaltlanga `Aneurysm` a ni. Hetiang chi hi aorta-a `Aneurysms` lo awm zawng zawng zinga 15% vel a ni.
I rilruah aneurysm i nei tih hriat chu thil hlauhawm tak a ni thei. I thisen kalna kawng hriselna leh an hnathawh dan hi i ngaihtuah ngai lo mai thei. A nih loh leh, connective tissue natna neia piang i nih avangin i taksa chhungril hnathawh dan i hre chiang hle mai thei bawk. Eng pawh hre la, tunah hian i dinhmun hriat belh a, harsatna i tawh theihna tur tihziaawmna tura hmalak hun a ni.
I dinhmun a zirin i beisei theih turte chu i doctor nen sawiho rawh. I mamawh ang zela enkawlna ruahmanna a siam thei ang a, i zawhnate chu a chhang thei ang a, hmalam pan tura i mamawh hriatna a pe thei bawk ang che.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Thoracic Aortic Aneurysm hi natna khirh tak a ni. Mahse, a hmaa hriatna, damdawi lam thurawn dik tak, leh enkawlna dik tak i neih chuan hrisel tak, dam rei tak i neih theihna chance ropui tak i nei a ni.
- Symptoms ngaihven rawh: Sudden, na tak tak, rilru natna emaw, hnungzang na emaw ang chi hi ngaihthah suh.
- Risk factors i neih chuan test rawh: I chhungkuaa mi tu emaw chuan he natna hi a lo vei tawh a nih chuan, emaw, thisen sang emaw, meizuk emaw i neih chuan doctor hnenah thurawn la rawh.
- I doctor thupek dik takin zawm rawh: i damdawi pekte chu ei la, exercise leh ei leh in chungchanga thupekte chu zawm la, test leh appointment ruat saah pawh tel ve rawh.
- Meizial zu hi pumpelh vek rawh: Hei hi i tih theih pawimawh ber pakhat a ni.
Lungngai suh, nangmah chauh i ni lo. I medical team te chuan tanpui turin an inpeih reng a ni. A pawimawh ber chu he dinhmun hi hriat chian a, i hriselna pawh active taka enkawl hi a ni.
` Thoracic Aortic Aneurysm, aorta, rilru natna, thinlung natna, thisen kalna kawng, thisen kalna kawng, surgery











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