Mi ṭhenkhat, a bîk takin naupang tê tête, rang taka thisen tlakchhamna nasa tak an tawh a, an chau hle a, a châng chuan nunna atana hlauhawm thei dinhmun hi i hmu tawh em, i hre tawh em? Chu chu tûn laia kan sawi tûr dinhmun khirh tak pakhat, aplastic crisis tih chu a ni. He hming hi hlauhawm deuhin a lang thei a, mahse kan hriat chian chuan he dinhmun hi kan tuar thiam thei hle.
He aplastic crisis hi eng nge ni tak tak?
A awlsam zawngin, aplastic crisis chu kan taksaa ruhro (bone marrow) -in thisen sen thar a siam chhuah loh thut mai hi a ni . Tunah chuan, "Chuti a nih chuan red blood cell siam chhuah a tawp chuan eng nge thleng ang?" Heng thisen sen (red blood cells) te hi kan taksa pum puia oxygen phurtu an ni. Chuvângin, an siam chhuah tawh loh chuan taksaa thisen sen zat chu nasa takin a tlahniam a, chu chuan thisen tlakchhamna nasa tak a thlen a ni . Hei hi nunna atana hlauhawm thei dinhmun a ni.
Aplastic crisis hian thisen lama harsatna nei sickle cell anemia ang chi te a nghawng tlangpui . Hei hi a chhan ber chu virus infection tlanglawn tak Parvovirus B19 tih a ni. Mak ti suh u, he virus hian mi tam tak a nghawng nachungin aplastic crisis hi thisen lama harsatna nei te hian he virus hi an kai chauhvin a thleng thin. Hetiang dinhmun hi naupang tê tê, a bik takin nauteah a tam zawk. Mahse thu lawmawm a awm a, hei hi enkawl dan tur a awm a, chu chu thisen pek leh intravenous immunoglobulin (IVIG) te hi a ni.
Hei hi mi zawng zawng tuar thei natna a ni em?
Ni lo, a ni lo tak zet. Ka sawi tawh ang khan Parvovirus B19 hi virus tlanglawn tak a ni. Mahse, he hri kai zawng zawng hian aplastic crisis an nei vek lo. Hei hi thisen natna chi khat nei mi pakhatin Parvovirus B19 a vei chauhvin a thleng thin.
Nau piang thar, nausen leh naupang sickle cell anemia vei te hi an hlauhawm hle. Thisen sen tichhe thei leh hemolytic anemia thlentu natna dang nei te pawhin parvovirus B19 an kai chuan aplastic crisis an vei theihna a sang hle bawk. Chung dinhmun thenkhat chu:
- Hnam dang atanga lo piang Spherocytosis
- Hemoglobin C natna a ni
- Thalassemia natna a ni
- G6PD tlakchhamna a ni
- Pyruvate Kinase tlakchhamna a awm
- Autoimmune Hemolytic Anemia atanga lo chhuak a ni
- Paroxysmal Zan lama Hemoglobinuria a awm thin
- Hereditary Elliptocytosis atanga lo piang chhuak a ni
Nangmah emaw, i fa emaw hian hetiang thisen natna hi i nei a nih chuan hei hi a bik taka enkawl a pawimawh hle.
Aplastic crisis natna lan chhuahna chu engte nge ni?
Puitling bakah naupang leh nausen, aplastic crisis nei te pawhin thisen tlakchhamna nasa tak nena inzawm symptom an nei tlangpui. Naute leh naupang tête chu a hma aia nasain an buai emaw, an thinrim emaw pawh a ni thei. Entirnan, i fa chu a tap nasa hle a, engmah a duh lo emaw, a thinrim reng ang tih emaw a nih chuan hei hi hetiang thil a nihna chhinchhiahna a ni thei.
A lan chhuah dan tlangpui thenkhat chu hetiang hi a ni:
- Chauhna: Chau lutuk, engmah ti thei lo anga inhriatna.
- Khawsik: Taksa lumna chu 38 degree Celsius (101 degree Fahrenheit) emaw a aia sang emaw a ni thei.
- Luak chhuak: I lu a inher ang maiin a lang a, i mit pawh a sen thei.
- Thâwk hah / dyspnea: Tlemte chet lai pawhin thawk tawi, stairs chhoh laia chau hle tih hriat.
- Lungphun mumal lo emaw, chak lo emaw: Lungphun chu a hma aia chak zawk a ni thei a, a nih loh leh a mumal lo a, kawng khatah a thawk lo thei bawk.
- Pallor: Vun, hmui, hmui emaw, nail emaw chu a tlangpui aia hring a lo ni ta. Hei hi thisen tlakchhamna a awm laia hmuh theih rawng a ni.
Heng chhinchhiahna pakhat emaw a aia tam emaw i hmuh chuan, a bik takin nangmah emaw, i fa emaw hian thisen lama harsatna i neih chuan, damdawi lam thurawn lak nghal a pawimawh hle .
Engvangin nge he aplastic crisis hi a lo awm? Eng nge a chhan?
"Aplastic" tih thumal hian i taksaa thil pakhatin hna a thawk tawh lo tihna a ni. Chu chu he aplastic crisis-ah hian a thleng thin. I ruhro hian thisen sen hrisel tak a siam thei lo. Chumi chhan chu a hmaa ka sawi tawh Parvovirus B19 kha a ni. He virus hian thisen sen puitling lo, la puitling lote chu direct-in a target a ni. Anmahni a tichhia a ni.
Kan taksa hian ruhro atang hian thisen sen (red blood cells), thisen var thenkhat, leh plasma ang chi thil a dawng thin. Chuvângin, thisen zam siam chhuah chhunzawm zel chu a reh chuan thisen tlakchhamna nasa tak i nei a ni . Ngaihtuah teh, hei hi kan taksa thisen factory-in a hnathawh a chawlhsan thut hian a ni.
Hetiang dinhmun avanga harsatna awm thei te chu engte nge ni?
Aplastic crisis hian harsatna hrang hrang a thlen thei a, a bik takin sickle cell anemia vei te tan chuan . Hengte pawh hi a pawi hle.
- Hun rei tak chhunga Vaso-occlusive crisis (VOC): 1.1.VOC hi natna rang tak, na tak, sickle cell anemia vei te tan a ni. He natna hi aplastic crisis vangin a rei thei hle.
- Myocarditis: Hei hi heart muscle inflammation a ni a, chu chu swelling ang chi a ni.
- Splenetic sequestration: Thisen sen pangngai lo chu spleen-ah a tang a, chu chuan spleen a ti lian a.
- Glomerulonephritis: Hei hi kal natna a ni a, a enkawl that loh chuan kal a tichhe thei a ni.
Chuvang chuan he dinhmun hi hriat chian a pawimawh hle kan ti.
Doctor-te hian engtin nge hei hi an hriat?
Nangmah emaw, i fa emaw hian heng symptoms te hi a lan chhuah hunah, doctor i hmuh hunah, ani chuan i symptoms te chu a zawt hmasa ang che. Tichuan taksa enfiahna a nei ang. Chu bakah, a natna hriat chian nan test eng emaw zat tih theih a ni bawk:
- Complete Blood Count (CBC): Hei hian taksaa thisen sen, thisen var leh platelet awm zat a enfiah thin. Aplastic crisis-ah chuan thisen sen (red blood cells) hi a tlem hle.
- Reticulocyte count: Reticulocyte hi thisen sen puitling lo a ni. He test hian ruhro atanga thisen sen thar engzat nge siam chhuah tih a teh a ni. Aplastic crisis-ah pawh he number hi a tlem hle.
- Parvovirus B19 test: He test hi he virus hi i kai tawh em tih finfiah nan tih a ni.
Heng test te hnuah hian doctor chuan hei hi aplastic crisis dik tak nge thil dang a ni tih chiang takin a hre thei a ni.
Hei hi eng enkawlna nge ni?
Aplastic crisis enkawlna ber chu thisen pek hi a ni . Hei hian pawn lam atanga thisen pek tihna a ni. Hei hian taksaa thisen zam (red blood cell count) hniam tak chu rang takin a siam tha leh thei a ni. Hei bakah hian Intravenous Immunoglobulin (IVIG) tih damdawi an pe bawk. Hei hi vein (IV) hmangin taksaah a lut a ni.
Damlo tam zawk chu enkawl tan atanga ni 10 atanga ni 14 chhungin an dam leh thin. Thil tha dang chu mi pakhatin parvovirus B19 a kai tawh chuan dam chhung zawngin he hri laka invenna a nei ta a ni. Chumi awmzia chu virus atanga aplastic crisis lo awm leh theihna chu nasa takin a tlahniam tihna a ni.
Aplastic crisis ven dan tur a awm em?
A nihna takah chuan sawi harsa deuh a ni. A chhan chu, aplastic crisis hi thisen lama harsatna nei mi pakhatin parvovirus B19 a vei hian a thleng thin. Parvovirus B19 hi hri kai a ni a, a laka invenna vaccine a la awm lo.
Mahse, nang leh i fa tanThisen lama harsatna i neih chuan sickle cell anemia ang chi i neih chuan parvovirus B19 i vei theihna tur tihtlem nan eng nge i tih theih tih doctor zawh a pawimawh. Entirnan, thil awlsam tak tak, mipui tamna hmun atanga hla taka awm leh kut sil fo te hian venhimna engemaw chen a pe thei a ni.
Hetiang dinhmun hnu hian eng nge thleng ang? (Prognosis) tih a ni.
Prognosis hi i dinhmun atana beisei tur a ni. Aplastic crisis nei te hi enkawl tan atanga ni 10 atanga ni 14 chhungin an dam tlangpui. Mahse, mi thenkhat chuan aplastic crises recurring an nei thei. Chuvang chuan a natna lan chhuah dan ngaihven a, doctor thupek zawm a pawimawh.
Engtin nge ka in enkawl ang? / Engtin nge ka fa ka enkawl ang?
Aplastic crisis hi thisen natna sickle cell anemia ang chi natna avanga harsatna tam tak awm thei zinga pakhat chauh a ni . Parvovirus B19 hi i veng thei lo mai thei a, mahse i hriselna zawng zawng vawng reng turin thil i tih theih a awm a:
- Checkup neih fo rawh: I primary care physician nena inbiak rengna hmang hian damdawi lama harsatna lian tham tak takte chu a lo thlen hmain i hre thei ang.
- I hri kai theihna tihtlem: I doctor nen influenza leh common cold ang chi natna tlanglawn laka inven dan tur sawipui rawh.
- Chaw hrisel ei: Ei leh in inthlau tak ei la, ni khatah tui glass 8-10 vel in rawh.
- Exercise: Taksa tihchak fo hian i rilru put hmang leh hriselna a titha thei a ni. Mahse, zawi zawiin la la, i hah hunah chawlh la, tui tam tak in tur tih hre reng ang che.
Heng thilte hian i taksa immune system a tichak a, a tlangpuiin hrisel taka awm turin a pui bawk.
Engtikah nge Doctor ka hmuh ang?
Aplastic crisis hi damdawi lam emergency a ni.
Nangmah emaw i fa emaw hian thisen lama harsatna i neih chuan sickle cell anemia , i hriselnaah inthlak danglamna rang tak, chak lohna emaw, chau lutuk emaw i neih chuan , i doctor pan nghal tur a ni a, tihkhawtlai lohvin. Enkawl i tan hma chuan a tha zawk.
Doctor hnenah eng zawhna nge ka zawh ang?
Nang emaw i fa emaw hian aplastic crisis i neih chuan i doctor hnenah hetiang zawhna hi i zawt thei ang:
- Engtikah nge kei/ka fa hi a dam leh ang?
- Kei/ka fa hian hetiang crisis hi kan neih leh theihna chance engzat nge awm?
- Hetiang dinhmun nena kan nun lai hian eng thil nge ka fimkhur bik tur?
Hetiang zawhna hi zawh a, i rinhlelhna te tihfai a pawimawh hle.
Aplastic crisis leh aplastic anemia hi thil inang an ni em?
Ni e, heng natna pahnih hi thisen zam (red blood cell count) tlahniam nen inzawm mah se, an pahnih hian danglamna a awm a ni.
Aplastic crisis hi thisen sen (red blood cells) tlahniam nghal, rang taka tihhniam a ni.
Aplastic anemia hi hun kal zelah a lo awm zauh zauh thin a ni. Hemiah hian thisen sen (red blood cells) chauh ni lovin thisen chi dang (white blood cells, platelets) te pawh a tlahniam thei a ni.
A awlsam zawngin sawi ila, Aplastic Crisis hi hun eng emaw chen atana buaina, acute problem a ni. Aplastic Anemia hi hun rei tak chhung, ruhro (bone marrow)-a awm thin a ni.
A tawp berah chuan take-home message
Okay, chuvangin tunah chuan vawiin a kan sawi tawh, Aplastic Crisis hi in hriatthiam ka beisei. Hei hi harsatna lian tak a ni a , thisen natna Sickle Cell Anemia ang chi nei te pawh a nghawng thei a ni . Thil thleng chu i emaw i fa emaw ruhro hian thisen sen (red blood cells) a siam chhuak nghal a, chu chuan thisen tlakchhamna nasa tak a thlen a, chu chuan nunna a tichhe thei a ni.
Aplastic crises hi thil hlauhawm tak a ni thei a, a chhan chu a symptoms chu a lo lang nghal thei a, a na hle thei bawk. Vanneihthlak takin Doctor ten thisen pek leh damdawi hmangin an enkawl thei a ni.
Nangmah emaw, i fa emaw hian thisen lama harsatna i neih a, chu chuan nangmah emaw, i fa emaw chu aplastic crisis vei theihna hlauhawm takah a siam a nih chuan, i doctor hnenah eng symptoms nge harsatna a awm tih tilang thei tih zawt rawh. Aplastic crisis hi i veng thei lo mai thei, mahse a lo thlen chuan eng nge i tih tur tih i hre mai ang. Chu awareness chu a pawimawh ber a ni.
👩🏽 ⚕️ Zawhna dang (FAQ)
💬 Aplastic Crisis hi eng nge ni?
Kan taksa thisen sen (red blood cells) te hi ruhro (bone marrow) ah siam a ni. Eng emaw chhan vangin, a bik takin virus infection (Parvovirus B19 ang chi) hnua kan ruhroah ni engemaw zat chhunga thisen sen siam chhuah a tawp nghal mai chu ‘aplastic crisis’ an ti a.
💬 Taksain thisen a siam chhuah a chawlhsan thut chuan damlo chu engtin nge a awm?
Thisen sen (red blood cells) hian taksa pum puiah oxygen a phur a. An chawlhsan chuan damlo chuan thisen tlakchhamna nasa tak a nei a. A hmui, nail leh vun te chu a var (pale) vek a, heart rate a sang a, a nih loh leh damlo chuan thawk harsatna avangin a hriatna a hloh nghal bawk.
💬 Hetiang mite, a bikin naupangte tan eng enkawl dan nge ni?
Hetiang dinhmun hi naupang sickle cell natna vei tan chuan a hlauhawm ber a ni. Hetiang natna avanga damdawi ina dah i nih chuan damdawi inah thisen pek nghal a ni ang. A tlangpuiin he thisen pek hnuah hian ruhro hian ni 10 atanga ni 14 vel chhungin thisen chu a pangngaiin a siam leh tan thin.
` Aplastic Crisis, Thisen sen, Ruhro, thisen tlakchham, Parvovirus B19, Sickle Cell Anemia











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