Mi pakhatin a kut a phar chhuak a, a duh loh zawnga a tlak nghal a, a rawn flick leh mai mai tih i hmu ngai em? Butterfly pakhatin a thla a phar ang mai a ni. Hei hi nangmah ngei pawhin i tawng tawh mai thei. Hei hi tremor pangngai a ni lo; damdawi lamah chuan hei hi Asterxis kan ti a ni. Natna tak tak a ni lo va, a hnuaia damdawi lam dinhmun (underlying medical condition) clinical sign a ni zawk. Chuti a nih chuan, engvangin nge hetiang hi a lo awm a, i lungkham tur em ni? Nirogi Lanka hmangin chiang tak leh awlsam takin i then ang u.
Asterxis hi eng nge ni?
A awlsam zawngin, Asterxis hi i taksa peng pakhat—entir nân, i kut i phar chhuah lai—a duh loh vanga rei lo tê a tih hahdam chuan a lo awm a ni. Hei hi i thluak atanga signal thawn chhuah te chu hun rei lote chhunga a tlakchhiat vang a ni.
Bang chunga nawr ang maiin han ngaihtuah teh. I kut ruhte chu second tlemte chhung a relax a nih chuan i kut chu hmalam panin a tla thla ang a, chutah chuan a awmna hmunah a snap leh ang. Chu chu a bul berah chuan Asterxis-a thil thleng chu a ni. Damdawi lamah chuan negative myoclonus tia hriat a ni bawk. Hemi kawngah hian "negative" tih hian "tha lo" tihna a ni lo va; muscle tone hloh tihna a ni. Typical muscle twitch (positive myoclonus) hian hnathawh tam lutuk a huam avangin hei hi a kalh zawngin kan ti a—hun rei lo te chhunga "drop" emaw, activity hloh emaw a ni.
Hetiang dinhmun hi thluak chhunga direct issue atanga lo chhuak a ni thei a, a nih loh leh systemic problems secondary symptom a ni thei bawk a, chu chu liver emaw kidney dysfunction emaw thluak hnathawh tichhe thei a ni.
Engtin nge hriat chhuah a nih?
Asterxis hian taksa sir lehlamah a nghawng tlangpui a, mahse a chang chuan asymmetrical a ni thei. Mut theih lohna, rilru buai, leh hun emaw hmun emaw chungchanga ngaihtuahna buai te ang chi chhinchhiahna dang a awm fo bawk .
I doctor chuan a awm leh awm loh enfiah nan heng clinical method pahnih zinga pakhat hi a hmang ngei ang:
1. Palms-out method: I doctor chuan i kutphah chu pawn lam hawiin hmalam pan turin a ti ang che, hmuh theih loh bang i nawr ang maiin, i kut zungtang chu zau takin a phar ang. Hetiang dinhmun hi second 30 vel i vawn lai hian i kut chu duh lohvin hnuai lam hawiin "flap" in, a snap leh a nih chuan Asterxis a awm tih a tilang a ni.
2. Grip method: He test-ah hian i doctor chuan an kut chu nghet taka chelh turin a ti ang che. I grip chakna chu a tlahniam emaw, rei lo te chhunga "giving way" emaw a nih chuan an hre thei ang, chu chu he natna clinical hallmark a ni.
Clinical examination neih laiin Asterxis hi a lang nghal lo thei tih hriat reng a pawimawh. I doctor chuan i dinhmun chu minute khat emaw, a aia rei emaw vawng reng tûrin a ti thei che a, chu chu dik taka i enfiah theih nân a ni.
Engvangin nge Asterxis hi a lo awm a, a chhan berte chu engte nge ni?
Asterxis hi thil engemaw zat avanga lo awm thei a ni a, a langsar ber chu i taksaa taksa peng pawimawh tak takte hnathawh dik loh vang a ni. Heng a chhan bulpui berte hi han thlir ila.
| Bithliahna | Hrilhfiahna |
|---|---|
| Liver leh Kidney chungchang | I thisen atanga toxins te chu i liver leh kidney te hian an filter chhuak thin a ni. Heng taksa peng hrang hrangte hi a chhiat chuan toxins a pung khawm thin. I thluak hi a sensitive hle avangin heng toxins te hian thluak hnathawh a tichhe thei a, Asterxis a thlen thei a ni. Liver failure, kidney failure, cirrhosis ang chi natna hi a awm fo thin. |
| Thluak Hliam | Hliam emaw, damdawi lam dinhmun hnuaia awm emaw hian thluak hmun bik takah hliam a siam thei a, chu chuan taksa ruh inzawmna (muscle coordination) a thunun thei a ni. Chutiang hunah chuan taksa sir khatah chauh he natna hi i hmu thei a ni. |
| Damdawi lam thil dang | Thisen chemistry inthlauhna pawh hi a chhan a ni thei bawk. Entirnan, hypoglycemia (thisen sugar hniam), hypokalemia (potassium hniam), hypomagnesemia (magnesium hniam), thinlung chak lohna, leh thawk lama harsatna te hi a ni. Tin, Wilson natna ang chi genetic condition, taksaah copper a awm khawmna hian hetiang hi a thlen thei bawk. |
Damdawi avanga Asterixis lo awm
A chang chuan Asterxis hi damdawi thenkhat avanga hun eng emaw chen atana side effect a ni thei bawk. Liver emaw kidney emaw lama harsatna i neih tawh chuan a hlauhawmna a sang hle.
Entirna tlanglawn tak takte chu:
- Anti-seizure damdawi: A bik takin phenytoin, "phenytoin flap" tia sawi fo thin. Damdawi dang gabapentin, valproate, carbamazepine te pawhin a thlen thei bawk.
- Barbiturates a ni
- Benzodiazepines te pawh a awm
- Antibiotics thenkhat
- Lithium (mood tidanglam theitu) .
- Metoclopramide (rilru natna dona damdawi) .
Hei hi engtin nge enkawl a nih?
Asterxis tan chauh damdawi bik a awm lo. Doctor-te chuan a chhan bulpui hriatchhuah leh chu natna enkawl chu an ngaih pawimawh ber a ni.
Entir nan:
- Liver natna avanga lo awm a nih chuan liver condition kan enkawl thin.
- Renal issues avanga lo awm a nih chuan kidney function kan address thin.
- Damdawi pakhat chu a mawhphurtu a nih chuan i doctor chuan a dose a siamrem ang a, a nih loh leh enkawlna dang a hmang ang che.
Chuvangin, Asterxis i vei a nih chuan, a pawimawh ber chu enkawlna dik tak i tan theih nan diagnosis dik tak neih hi a ni. Hei hi in lama enkawl tum tur dinhmun a ni ngai lo.
Enkawl loha dah mai mai chuan eng hlauhawmna nge a neih?
Asterxis ngaihthah theihna hlauhawm ber chu a thlentu damdawi lam dinhmun khirh tak hmachhawn loh hi a ni. Heng natna hnuaia awmte hi nunna atana hlauhawm tak a ni thei. Enkawlna tel lo chuan neurological damage permanent i hlauhawm thei a, i cognition, gait, leh fine motor skills te a nghawng thei a ni.
Asterxis hian i ke emaw, i ke ruh emaw a nghawng chuan i tlu nghal thei a, a hnuah hliam na tak i tuar thei bawk.
Engtikah nge damdawi lam pan nghal tur?
Asterxis chhinchhiahna i neih nia i rinhlelh chuan doctor i pan vat a ngai a ni.
Chubakah, a hnuaia mite hi medical emergency angin en ve bawk ang che :
- Asterxis hi buainain a zui a nih chuan.
- I chhehvêl, i hun hriat loh, i nihna hriat loh ang chi disorientation i neih chuan.
- Sudden mental status change dang i lantir chuan.
Heng symptoms te hian thluak hnathawhnaah nghawng lian tak a nei tih a tilang. Chutiang dinhmunah chuan emergency department hnai ber pan nghal mai tur a ni.
Take-Home Thuchah a ni
👩🏽 ⚕️ Zawhna tam tak (FAQs) .
💬 Damdawi bik Macitentan (Opsumit) hi eng atan nge hman?
Hei hi therapy specialized tak a ni. ‘Pulmonary Arterial Hypertension (PAH) enkawl nan hman a ni a, chu chu i thinlung atanga i lung thlenga thisen phurtu thisen kalna kawngte a zim a, a nghet a, thisen sang hlauhawm tak a thlen thin. ‘Endothelin Receptor Antagonist’ anga a thawh avangin he damdawi hi natna zual zel tur tikhawtlai tur leh i dam rei theihna tura siam a ni.
💬 Pulmonary blood vessels a inkharkhip chhoh lai hian engtin nge Macitentan hian a puih?
I taksaa thil tha lo tak ‘Endothelin-1’ an tih hian heng thisen kalna kawngte hi a ti tawi a, a fibrosis (stiffening) a tichhuak thin. He damdawi hi i thisenah a luh veleh Endothelin-1-in chhiatna a thlenna atana a hman receptor (ETA leh ETB - dual block) te chu a block tha hle. Tin, damdawi hian lung tissue-ah a lut a, chu chuan vessel walls a thim lehzual loh nan a pui bawk.
💬 Opsumit ka ei hmaa ka hriat tur pawimawh tak tak ‘Black Box Warnings’ te chu engte nge ni?
Vaukhânna pawi ber chu naupai laiin he damdawi hi khap tlat a ni a; piansualna nasa tak emaw, nausen thihna emaw a thlen thei. Hmeichhia te hian REMS himna programme bik an zawm a ngai a ni. Chubakah, mipaah chuan he damdawi hian sperm count a tihhniam bakah nau pai theih lohna a thlen tih hriat a ni bawk. Damlo thenkhat chuan thisen tlakchhamna (hemoglobin level hniam) nasa tak an nei thei bawk.
