I kal (kidney stone) leh i hnungzang, i pum hnuai lam emaw, i sir lama natna tuar theih loh avangin damdawi inah i awm tawh em? A nih loh leh i hriat mi pakhatin hetiang harsatna tawk hi i hre tawh em? Kidney stone hi thil hrehawm tak a ni tak zet a ni. Heng lungte hi kawng hrang hrangin a lo piang thei a ni. Vawiin hian kidney stone chi khat, tlem a tlem zawk, mahse a enkawl that loh chuan harsatna a thlen thei, a bik takin thalai zingah, cystine stone an tih chungchang kan sawi dawn a ni.
Heng cystine lungte hi engte nge ni?
A awlsam zawngin sawi ila, cystine stone hi kidney stone chi khat a ni. Kidney stone hi hard mass a ni a, i zun chhunga chemical hrang hrang, lung lian lo te ang chi, a lo awm khawm hian a lo awm thin. Cystine lung hi chemical pakhat cystine an tih atanga siam a ni a . He cystine hi kan taksaa awm amino acid a ni. A tlangpuiin thil thleng tur chu he cystine hi kal (kidney) hian taksaah a insiam leh thin a ni. Mahse a chang chuan hetiang thil hi a thleng dik loh chuan cystine chu zun chhungah a awm khawm a, lung a siam thin.
Heng cystine lungte hi a lian hle fo thin . Chuvangin a chang chuan kal emaw zun kawng emaw a chhiat loh nan operation tihchhuah a ngai thin . Thil lungchhiatthlak tak chu, mi tam tak, cystine lung nei te hian an dam chhungin vawi eng emaw zat heng lung hi an nei thei a ni. Mahse lungngai suh, he natna hi surgery tel lova enkawl dan a awm. Entirnan, i ei leh in thlak danglam emaw, i zun pH balance thei damdawi hmang emaw hian he natna hi i control thei a ni.
Chuti a nih chuan Cystinuria chu eng nge ni?
Cystinuria hi natna awm lo, rochun atanga lo chhuak a ni. Hei hi i zun chhungah chemical cystine an tih a lo awm khawm hian a ni. Mi sang sawm zinga pakhat velin he natna hi an nei a ni. Cystinuria i neih chuan i taksain cystine a tihthianghlim harsatna a nei a ni. Hei hi a lo pungkhawm a, cystine lung a siam hun a ni. Cystinuria hian i dam chhungin kal (kidney stone) vawi tam tak a nei thei a.
Hei hi gene chi khat (autosomal recessive gene) tih atanga lo awm a ni. Chumi awmzia chu naupangin he gene hi nu leh pa atanga a rochun chuan naupang chuan cystinuria a nei dawn tihna a ni. Hei hi dam chhung zawnga natna a ni a, tihdam kim theih a ni lo. Mahse, enkawl dan dik tak chuan a thunun tha thei a ni .
Cystine kidney stone hi engtiang chiahin nge a tlem?
Kidney stone chi dang nena khaikhin chuan cystine stone hi 1% atanga 2% chauh a awm a ni. Chu chu a tlem hle. Mahse mak tak maiin naupangte kal (kidney stone) zinga 6% atanga 8% vel chu cystine stone a ni . Dik tak chuan cystine stone nei zinga 80% chuan kum 20 an tlin hmain lung hmasa ber an nei thin.Mahse, heng lung pakhat emaw, a aia tam emaw hi kum eng pawha siam theih a ni.
Cystine stones hi eng symptoms nge ni?
Cystine stones symptoms hi kidney stone dang nen a inang hle. Lung a lo awm chuan symptoms i nei tan chauh a ni.
Hetiang thil hi a thleng thei a ni:
- I taksa sir khatah (back) hliam na tak .
- Groin area emaw, pum hnuai lam emawa natna hriat.
- Zun chhunga thisen hmuh .
- Luak chhuak leh pum na (nausea).
- Zun laiin natna (hei hi lung chu bladder hnaih takah a thleng thin).
A châng chuan, cystine lung chu a tlakbuak thei a, urinary tract infection (UTI) a thlen thei bawk . Lung dang aiin cystine lung hi a lian deuh avangin chutiang harsatna chu a thlen tam zawk a ni.
Engvangin nge heng cystine lungte hi an lo awm?
Kan sawi tawh ang khan cystine lung hi natna hlauhawm tak, cystinuria tih hming pu te zingah a lo awm tam ber a ni. Cystinuria hi gene SLC3A1 leh SLC7A9 a mutations vang a ni a . Hetiang dinhmun hian i taksain amino acid cystine hi a hmang dik thei lo. Chumi hnuah chuan a insiam a, lung a siam ta a ni. Heng lungte hi i zun kawng khawi hmunah pawh a awm thei a, chu chu i zunthlum emaw, i kal emaw-ah te pawh a awm thei.
A awlsam zawngin, hei hi genetic problem a ni. Chu chu i sualna a ni lo tihna a ni.
Cysteine lung hi eng atanga siam nge ni?
Cystine lung hi cystine atanga siam a ni . Kan sawi tawh ang khan cystine hi amino acid a ni . Amino acid hi protein chi khat a ni. Kan taksa hian tissue siam that a, taksa ruh a siam a, natna hrik a do theih nan an pui bawk. Cystinuria vei te hian an kal (kidney) hian he amino acid hi a hip lut emaw, a hmang emaw a harsatna an nei thin.
Cystine lung (cystine stone) avanga harsatna awm thei te chu engte nge ni?
Cystinuria hi dam chhung zawnga natna a ni. I doctor chuan damdawi hmangin, ei leh in thlak danglamin, leh operation hmangin i natna chu a enkawl thei che a ni. Mahse, i dam chhung zawngin cystine stone i nei tam zawk. Heng lungte hi an kal pelh lai hian a na thei hle.
Cystine lung hian harsatna a thlen thei a, chungte chu:
- Kidney natna a awm thin .
- Ureter (kidney atanga bladder thlenga zun phurtu tube) blockage.
- Zun kawng natna (UTIs) .
- Kidney a chhiat phah.
Engtin nge cystine lung i nei tih i hriat theih ang?
I doctor chuan i natna lan chhuah dan a ngaihthlak a, i medical history kimchang a lak a, i chhungte zingah heng natna hi tu emaw pawhin an nei tawh em tih te pawh a la a, cystine lung a awm tih a hmuchhuak ang. Chu bâkah, a hnuaia mite hi i ti thei bawk ang:
- Imaging test , ultrasound scan leh CT scan , leh zun test te pawh a awm bawk.
- Lung pakhat chu lab-ah test turin thawn. I theih chuan i zun nena inzawm lung pakhat chu la khawm la, i doctor chuan lab-ah a thawn thei ang a, a zirchiang thei ang. Chutiang chuan lung chu eng chemical nge a siam tih chiang takin an hre thei ang.
Cystinuria hi engtin nge enkawl a nih?
Cystine lung enkawl huna pawimawh ber chu a hmasa berah chuan a lo awm loh nan tum hi a ni . Chutianga tih theih dan tha ber pakhat chu i zun a cystine awm zat tihtlem hi a ni. I doctor chuan damdawi leh ei leh in thlak danglamna hmangin lung i siam zat tihtlem nan a pui mai thei. Damdawi leh ei leh in tihdanglamna hian lung siam a titawp lo a nih chuan, a nih loh leh lung a lian hle a nih chuan surgery hi tih theih dang a ni.
Damdawi ei tur
I doctor chuan tui tam tak in hian lung chu a mah chauhin a kal thei ang tih a ngaihtuah chuan, a natna damdawi over-the-counter (OTC) a pe thei a ni. Nakin lawka lung awm lohna tura pui turin tiopronin leh d-penicillamine ang chi damdawi an pe thei bawk.
Ei leh in tur ruahmanna
I doctor chuan lung a lo awm loh nan i ei leh in dan thlak danglam turin a fuih mai thei che. Chung zinga ṭhenkhat chu:
- Tui tam tak in. Hei hian cystine lungte chu a tithianghlim thei a ni. I doctor chuan ni khatah tui ounces 96 (litre 2.8 vel) in turin a ti thei che a, darkar tin tui glass khat in turin a ti thei che a, zan lama i thawh hunah tui in turin a hrilh thei che a ni.
- Sodium (salt) i ei zat kha tihtlem la. Chumi awmzia chu frozen emaw canned food emaw ei kha i bansan a ngai tihna a ni. Buhfai kan ei chhunga chi kan dah mai ni lovin, thil chi hrang hrang, pickles, pickles, sauce, packaged foods, leh dawr atanga kan lei ei tur teah pawh chi thup a awm bawk. Chuvangin chu lam pawh i fimkhur a ngai a ni.
- Animal protein , chu chu sa ei tlem a, chu ai chuan thlai atanga siam protein ei tihna a ni. Entirnan, sa leh sangha ai chuan chickpeas, lentils, leh soy ang chi thil te i dah thei bawk.
Inzai
Lung lian tak takte chu zun kawng kaltlanga a kal loh chuan a chhe thei hle. Heng lungte hian a na thei hle a, taksa atanga zun luang chhuak tur pawh a tikhawlo thei bawk. Lung lak chhuah nan i doctor-in a hman theih dan hrang hrang a awm a:
- Camera te tak te, flexible tak chu i urethra chung lamah, bladder leh urethra kaltlangin, lung chu zawng chhuakin lakchhuah nan an pass a (ureteroscopy) .
- I hnungzang vunah hian incision te tak te siam a ni a, chuta tang chuan tube chu kidney-ah dahin, lung chu lakchhuah a ni.(percutaneous nephrolithotomy hmanga tih a ni) .
Engtin nge enkawlna a hlawhtlin leh hlawhtlin loh i hriat theih ang?
I doctor chuan i cystine level enfiah nan a hun hunah urinalysis a ti thei ang. He test hian i enkawlna ruahmanna chu a thawk tha em tih a hriat theih nan a pui ang.
Cystine lungte hi a hmin thei em?
Ni e, cystine lung chu a paltlang thei. Mahse uluk taka enkawl leh enkawl chhunzawm zel a ngai a ni . A hmin vek ai chuan a te zawk leh awlsam zawka siam theih a ni.
Eng eitur nge cystinuria vei tanpui?
Research atanga a lan dan chuan cystinuria vei te hian ei leh in thlak danglam hian hlawkna an hmu thei a ni. Chung zinga ṭhenkhat chu tui in tam te, thei leh thlai ei tam te, chi tlemna ei leh in ei te hi a ni. Citrus thei chi hrang hrang, orange leh lemon, thlai hring, leh hnah hring (leafy greens) te hi a tha hle.
Cystine lung hi ven theih a ni em?
Cystinuria hi inherited condition a nih avangin ven theih a ni lo. Mahse, i doctor-in a pek che treatment plan zawm chuan cystine stones lo awm tur chu i veng thei a ni . Chu chu lung siam dan i thunun thei tihna a ni.
Cystinuria hian nunna a tichhe thei em?
Hei hi nunna atana hlauhawm a ni lo tlangpui . Mi tam zawk chuan kal (kidney failure) ang chi natna khirh tak tak an nei lo. A pawimawh ber chu i doctor nen thawk hovin i tana tha tur damdawi zawn hi a ni. Mi tam zawk chuan enkawlna an dawng tha hle. Kidney, bladder, urinary tract tichhe lo damdawi hmuh theih a ni bawk.
Sistine lungte hmalam hun tur chu eng nge ni?
Cystine lung hi i dam chhungin vawi tam tak a lo awm thei a. Cystinuria i neih chuan ei leh in thlak danglam zel a ngai ang a, cystine lung a lo awm loh nan damdawi i ei a ngai bawk ang. I doctor chuan a enkawl ang che a, cystine lung thar lo awm apiang chu uluk taka enkawl i nih leh nih loh a enfiah ang. Hei hi i zun kawng, i kal leh i zun kawng a chhiat loh nan a ni.
Engtikah nge Doctor ka hmuh ang?
Kidney stone symptoms i neih chuan doctor pan ngei ngei tur a ni . Heng a lan chhuah dan tlangpui thenkhat chu hetiang hi a ni:
- Pum, hnungzang sir emaw, groin emaw a na.
- Nausea leh luak chhuak.
- Zun laiin natna.
Cystinuria hi dam chhung zawnga natna a ni a, cystine lung a siam thin. Lung a lo awm loh nan enkawl dan tur ruahmanna siam turin i doctor nen thawk ho rawh. He natna hi genetic a nih avangin cystinuria vei te hian chhungkaw din an ngaihtuah a nih chuan genetic counselling hi ngaihtuah an duh mai thei.A hmuh theih nan pawh a \angkai thei bawk. Thu lawmawm tak chu he natna hi enkawlna hmanga control theih a ni tlangpui a, kal (kidney failure) emaw, zun kawng tichhe nasa tak emaw a thlen lo.
Hriat reng tur pawimawh ber berte (Take-Home Message) .
Okay, chuvangin kan sawi tawh atang khan i hriat reng tur thenkhat chu khaikhawm ila:
- Cystine stones hi kidney stone chi khat a ni a , chu chu genetic condition cystinuria an tih avanga lo awm a ni .
- Chungte chu a lian hle thei a, dam chhungin vawi tam tak a thleng thei bawk.
- A lan chhuah dan chu natna nasa tak, zun chhunga thisen chhuak, leh luak chhuak te a ni thei .
- Enkawlnaah chuan tui tam tak in te, chi leh rannung protein tihtlem te, a tul chuan damdawi leh operation te a tel a ni .
- Cystinuria hi tihdam kim theih ni lo mah se, uluk taka enkawl a nih chuan lung siam hi thunun theih a ni a, nun pangngai a awm thei bawk.
- If you have symptoms of kidney stones , hun khawhral suh la, doctor pan rawh.
He thu hi hriattirna atan chauh a ni a, damdawi lam thurawn anga ngaih tur a ni lo tih hre reng ang che. Hriselna lama harsatna awm apiang doctor rawn hmasak hi a tha ber fo.
` Kidney stone, cystine stone, cystinuria, urinary stone, kidney natna, genetic natna, urinary tract infection











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